ICD-9 Code ICD-10 Code Condition/Diagnosis 042 B20 Human immunodeficiency virus [HIV] disease
046.2 A81.1 Subacute Sclerosing Panencephalitis Malignant neoplasm of right 190.5 C69.01 conjunctiva (Retinoblastoma)
Malignant neoplasm of left conjunctiva 190.5 C69.02 (Retinoblastoma) Malignant neoplasm of central nervous 192.9 C72.9 system, unspecified 225.0 D33.2 Benign Neoplasm of Brain, Unspecified 237.71 Q85.01 Other Neurofibromatosis Congenital iodine-deficiency syndrome, 243 E00.9 unspecified Other disorders of amino-acid transport 270 E72.09 (Fanconi (-de Toni) (-Debre) Syndrome)
270.1 E70.0 Classical phenylketonuria 270.2 E70.20 Disorder of tyrosine metabolism, unspecified
270.2 E70.21 Tyrosinemia, (Type I (Tyrosinosisa) and Type II (Richner-Hanhart Syndrome)
270.2 E70.29 Disorder of tyrosine metabolism, unspecified
270.2 E70.30 Albinism, unspecified
E70.8 Other disorders of aromatic amino-acid 270.2 metabolism Waardenburg's Syndrome, Type I E70.9 Disorder of aromatic amino-acid 270.2 metabolism, unspecified
270.3 E71.0 Maple Syrup Urine Disease 270.3 E71.110 Isovaleric Acidemia 270.3 E71.121 Methylmalonic Aciduria 270.4 E72.11 Homocystinuria 270.6 E72.22 Argininosuccinic Aciduria 270.7 E72.51 Non-ketotic hyperglycinemia Lowe's Syndrome or (Oculocerebrorenal 270.8 E72.03 Syndrome) 271.0 E74.02 Pompe's Disease 271.1 E74.21 Galactosemia 272.7 E75.11 Mucolipidosis IV 272.7 E75.22 Gaucher’s Disease 272.7 E75.240 Niemann-Pick disease type A 272.7 E75.3 Sphingolipidosis, unspecified
272.7 E77.1 Defects in Glycoprotein Degradation (Mannosidosis)
272.7 E77.9 Disorder of glycoprotein metabolism, unspecified
272.7 E77.9 Other disorders of glycoprotein metabolism
Disorder of copper metabolism, 275.1 E83.00 unspecified Menkes' Syndrome (Kinky Hair Disease) 275.1 E83.01 Wilson's Disease 277.00 E84.9 Cystic fibrosis, unspecified
277.00 E84.9 Cystic fibrosis, unspecified
277.2 E79.1 Lesch-Nyhan Syndrome Disorder of bilirubin metabolism, 277.4 E80.7 unspecified 277.5 E760.1 Hurler Syndrome
277.5 E760.2 Hurler-Scheie syndrome
277.5 E760.3 Scheie's syndrome
Carnitine deficiency due to inborn 277.82 E71.42 errors of metabolism
Disorder of fatty-acid metabolism, 277.85 E71.30 unspecified
Long Chain Hydroxy Acyl-CoA 277.85 E71.310 Dehydrogenase Deficiency
Medium Chain Acyl-CoA 277.85 E71.311 Dehydrogenase Deficiency (MCAD)
277.86 E71.522 Adrenomyeloneuropathy 279.11 D82.1 Di George's Syndrome 280.9 D50.9 Iron deficiency anemia, unspecified
282.49 D56.8 Other thalassemias
282.60 D57.1 Sickle-cell disease without crisis
282.7 D58.2 Other hemoglobinopathies Other psychoactive substance use, 292 F19.939 unspecified with withdrawal, unspecified
Major Depressive Affective Disorder 296.2 F32.0 Single Episode Unspecified (DC 0-3 R: 231 Type I Major Depression) Episodic Mood Disorder Unspecified 296.9 F39 (DC 0-3 R: 231 Type II Depressive Disorder) Autistic Disorder (DC 0-3 R: 710 299.00 F84.0 Multisystem Development Disorder) Other Specified Pervasive 299.8 F84.8 Developmental Disorder (DC 0-3 R: 710 Multisystem Development Disorder) Pervasive Development Disorder (PDD), 299.90 F84.9 Unspecified Anxiety Disorder, unspecified (DC 0-3 300 F41.9 R: 225 Anxiety Disorder NOS) Generalized Anxiety Disorder (DC 0-3 300.02 F41.1 R: 220's Anxiety Disorder Disorder) Social Phobia, Unspecified (DC 0-3 R: 300.23 F40.10 220's Anxiety Disorder Disorder) Other Phobic Anxiety Disorders (DC 0-3 300.29 F40.8 R: 220's Anxiety Disorder Disorder) Anorexia Nervosa, Unspecified (DC 0-3 307.1 F50.00 R: 600's Feeding Behavior Disorder) Adjustiment Insominia (DC 0-3 R: 500's 307.41 F51.02 Sleep Behavior Disorder) Other insomnia not due to a substance 307.42 F51.09 or known physiological condition (DC 0-3 R: 500's Sleep Behavior Disorder)
307.3 F98.4 Spasmus Nutans Eating disorder, unspecified (DC 0-3 R: 307.5 F50.9 600's Feeding Behavior Disorder) Bulimia Nervosa (DC 0-3 R: 600's 307.51 F50.2 Feeding Behavior Disorder) PICA of Infancy and Childhood (DC 0-3 307.52 F98.3 R: 600's Feeding Behavior Disorder) Rumination Disorder of Infancy (DC 0-3 307.53 F98.21 R: 600's Feeding Behavior Disorder) Other feeding disorders of infancy and 307.59 F98.29 early childhood (DC 0-3 R: 600's Feeding Behavior Disorder) Adjustment disorder with depressed 309.1 F43.21 mood (DC 0-3 R: 210 Prolonged Bereavement/Grief Reaction)
Separation anxiety disorder of 309.21 F93.0 childhood (DC 0-3 R: 220's Anxiety Disorder Disorder) Adjustment disorder with anxiety (DC 309.24 F43.22 0-3 R: 300 Adjustment Disorder) Adjustment disorder with mixed anxiety 309.28 F43.23 and depressed mood (DC 0-3 R: 300 Adjustment Disorder)
Other childhood disorders of social 309.29 F43.29 functioning (DC 0-3 R: 300 Adjustment Disorder) Adjustment disorder with disturbance 309.3 F43.24 of conduct (DC 0-3 R: 400's Regulation Disorder of Sensory Processing) Adjustment disorder with mixed disturbance of emotions and conduct 309.4 F43.25 (DC 0-3 R: 150 Deprivation /Maltreatment Disorder or DC 0-3 R: 900 Relationship Disorder If PIR-GAS of 40 or below)
Post-traumatic stress disorder, 309.81 F43.10 unspecified (DC 0-3 R: 100 Post Traumatic Stress Disorder) Adjustment disorder, unspecified (DC 0- 309.9 F43.20 3 R: 300 Adjustment Disorder) Childhood emotional disorder, 313.9 F93.9 unspecified (DC 0-3 R: 240 Mixed Disorder of Emotional Expressiveness) 315.31 F80.1 Expressive Language Disorder Mixed Receptive-Expressive Language 315.32 F80.2 Disorder 315.35 F80.81 Childhood Onset Fluency Disorder Other developmental disorders of 315.39 F80.89 speech and language Specific Developmental Disorder of 315.4 F82 Motor Functions Specific Developmental Disorder of 315.5 F82 Motor Functions (Mixed Development Disorder) Other disorders of psychological 315.8 F88 development Other Specified Delays in Development Developmental Disorder of Scholastic 315.9 F81.9 Skills (Mixed Development Disorder) 317.0 F70 Mild Intellectual Disabilities 318.0 F71 Moderate Intellectual Disabilities 318.1 F72 Severe Intellectual Disabilities 318.2 F73 Profound Intellectual Disabilities 319.0 F79 Unspecified Intellectual Disabilities 322.9 G03.9 Meningitis Unspecified 324.9 G06.2 Extradural and Subdural Abscess, Unspecified (Hemiplegia (Hemiparesis) 330 E75.25 Metachromatic Leukodystrophy 330.0 E75.23 Krabbe's Disease 330.0 E75.29 Other sphingolipidosis (Canavan Disease)
330.1 E75.02 Tay-Sachs disease 330.1 E75.19 Other gangliosidosis 330.1 E75.4 Neuronal Ceroid Lipofuscinoses 330.1 E7501 Sandhoff disease 330.8 F84.2 Rett’s Syndrome 330.8 G31.81 Alper's Disease 330.8 G31.82 Leigh’s Disease
331.4 G91.1 Obstructive Hydrocephalus Other Specified Degenerative Diseases 331.89 G31.89 of Nervous System 333.2 G25.3 Myoclonus Genetic Torsion Dystonia (Dystonia 333.6 G24.1 Musculorum Deformans) Cerebellar ataxia with defective DNA 334.8 G11.3 repair Hereditary Ataxia, Unspecified 334.9 G11.9 (Spinocerebellar Disorders) Infantile Spinal Muscular Atrophy 335 G12.0 Werdnig-Hoffman Disease, 336 G95.0 Syringomyelia and syringobulbia 336.6 G95.89 Other specified diseases of spinal cord 343.0 G80.1 Spastic diplegic cerebral palsy (Congenital Diplegia, Paraplegia) 343.1 G80.2 Cerebral Palsy, Infantile, Hemiplegic (Congenital Hemiplegia)
343.1 G80.2 Spastic hemiplegic cerebral palsy Hemiplegia, Congenital (Spastic Infantile Paralysis)
Generalized idiopathic epilepsy and 343.2 G40.301 epileptic syndromes, not intractable, with status epilepticus 343.2 G80.0 Spastic quadriplegic cerebral palsy
343.3 G80.8 Other cerebral palsy Cerebral Palsy, Infantile, Monoplegic
343.4 G80.2 Hemiplegia, Infantile (Postnatal), NOS
343.8 G80.8 Cerebral Palsy, Infantile, Other Specified
343.9 G80.9 Cerebral Palsy, Infantile, Unspecified
Quadriplegia, unspecified Paralysis of 344.0 G82.50 All Four Limbs (Quadriplegia, Quadriparesis,) Paraplegia, unspecified Paralysis of 344.1 G82.20 Both Lower Limbs (Paraplegia) Diplegia of upper limbs Paralysis of 344.2 G83.0 Both Upper Limbs (Diplegia) Monoplegia of lower limb affecting 344.3 G83.10 unspecified side Paralysis of One Lower Limb (Monoplegia) Monoplegia of upper limb affecting 344.4 G83.20 unspecified side Paralysis of One Upper Limb (Monoplegia) 344.89 G83.89 Other Specified Paralytic Syndromes 344.9 G83.9 Paralytic syndrome, unspecified Generalized idiopathic epilepsy and 345.00 G40.309 epileptic syndromes, not intractable, without status epilepticus
Generalized idiopathic epilepsy and 345.01 G40.319 epileptic syndromes, intractable, without status epilepticus
Generalized idiopathic epilepsy and 345.5 G40.311 epileptic syndromes, intractable, with status epilepticus
Localization-related (focal) (partial) idiopathic epilepsy and epileptic
345.50 G40.001 syndromes with seizures of localized onset, not intractable, with status epilepticus
Localization-related (focal) (partial) idiopathic epilepsy and epileptic
345.50 G40.009 syndromes with seizures of localized onset, not intractable, without status epilepticus
Localization-related (focal) (partial) symptomatic epilepsy and epileptic 345.50 G40.011 syndromes with complex partial seizures, not intractable, without status epilepticus Localization-related (focal) (partial) symptomatic epilepsy and epileptic 345.50 G40.119 syndromes with simple partial seizures, intractable, without status epilepticus
Localization-related (focal) (partial) symptomatic epilepsy and epileptic 345.50 G40.219 syndromes with complex partial seizures, intractable, without status epilepticus
Localization-related (focal) (partial) symptomatic epilepsy and epileptic
345.50 G40.A19 syndromes with simple partial seizures, not intractable, without status epilepticus
Localization-related (focal) (partial) symptomatic epilepsy and epileptic 345.51 G40.011 syndromes with complex partial seizures, not intractable, with status epilepticus
Localization-related (focal) (partial) symptomatic epilepsy and epileptic 345.51 G40.019 syndromes with complex partial seizures, intractable, with status epilepticus
Localization-related (focal) (partial) 345.51 G40.101 symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus
Localization-related (focal) (partial) idiopathic epilepsy and epileptic 345.51 G40.111 syndromes with seizures of localized onset, intractable, with status epilepticus
Localization-related (focal) (partial) idiopathic epilepsy and epileptic
345.51 G40.119 syndromes with seizures of localized onset, intractable, without status epilepticus
Localization-related (focal) (partial) symptomatic epilepsy and epileptic 345.51 G40.A11 syndromes with simple partial seizures, intractable, with status epilepticus
Other generalized epilepsy and epileptic 345.60 G40.821 syndromes, not intractable, with status epilepticus
Other generalized epilepsy and epileptic 345.60 G40.822 syndromes, not intractable, without status epilepticus
Other generalized epilepsy and epileptic 345.61 G40.823 syndromes, intractable, with status epilepticus Other generalized epilepsy and epileptic 345.61 G40.824 syndromes, intractable, without status epilepticus
Other epilepsy, not intractable, with 345.80 G40.801 status epilepticus
Other epilepsy, not intractable, without 345.80 G40.802 status epilepticus
Juvenile myoclonic epilepsy, not 345.80 G40.B01 intractable, with status epilepticus
Juvenile myoclonic epilepsy, not 345.80 G40.B09 intractable, without status epilepticus
Other epilepsy, intractable, with status 345.81 G40.803 epilepticus
Other epilepsy, intractable, without 345.81 G40.804 status epilepticus
Juvenile myoclonic epilepsy, intractable, 345.81 G40.B11 with status epilepticus
Juvenile myoclonic epilepsy, intractable, 345.81 G40.B19 without status epilepticus
Epilepsy, unspecified, not intractable, 345.90 G40.901 with status epilepticus
Epilepsy, unspecified, not intractable, 345.90 G40.909 without status epilepticus Epilepsy, unspecified, intractable, with 345.91 G40.911 status epilepticus
Epilepsy, unspecified, intractable, 345.91 G40.919 without status epilepticus
348 G93.0 Congenital cerebral cysts 348.0 G93.0 Cerebral Cysts 348.39 G93.49 Other encephalopathy 348.8 G93.89 Other Conditions of the Brain Hereditary and Idiopathic Neuropathy, 356.9 G60.9 Unspecified 356.9 G60.9 Hypertrophic Interstitial Neuritis Myasthenia Gravis, without (acute) 358.00 G70.00 exacerbation (Familial Infantile) 359.0 G71.2 Congenital Myopathies 359.0 G71.2 Congenital Myopathies 359.1 G71.0 Muscular Dystrophy 359.21 G71.11 Myotonic Muscular Dystrophy Myotonia Congenita (Thomsen's 359.22 G71.12 Disease) 359.9 G72.9 Myopathy Unspecified 361.0 Unspecified retinal detachment with H33.001 retinal break, right eye
361.0 Unspecified retinal detachment with H33.002 retinal break, left eye
361.0 Unspecified retinal detachment with H33.003 retinal break, bilateral
Unspecified Retinal Detachment with 361.0 H33.009 Retinal Break, Unspecified eye 362.21 H35.179 Retrolental Fibroplasia, Unspecified Eye 362.21 Retrolental fibroplasia, right eye H35171
362.21 Retrolental fibroplasia, left eye H35172
362.21 Retrolental fibroplasia, bilateral H35173
362.12 Retinopathy, Exudative H35.02
362.22 Retonpathy of Prematurity, stage 0 H35.11
362.23 Retonpathy of Prematurity, stage 1 H35.12
362.24 Retonpathy of Prematurity, stage 2 H35.13
362.25 Retonpathy of Prematurity, stage 3 H35.14
362.26 Retonpathy of Prematurity, stage 4 H35.15
362.27 Retonpathy of Prematurity, stage 5 H35.16
362.74 H35.52 Pigmentary retinal dystrophy Dystrophies Primarily Involving the 362.76 H35.54 Retinal Pigment Epithelium (Leber’s Congenital Amaurosis) 366 Unspecified infantile and juvenile H26.001 cataract, right eye
366 Unspecified infantile and juvenile H26.002 cataract, left eye
366 Unspecified infantile and juvenile H26.003 cataract, bilateral Unspecified Infantile and Juvenile 366 H26.009 Cataract, Unspecified Eye 367 H52.00 Hypermetropia, unspecified eye
367 H52.01 Hypermetropia, right eye
367 H52.02 Hypermetropia, left eye 367 H52.03 Hypermetropia, bilateral 367.1 H52.10 Myopia, unspecified eye
367.1 H52.11 Myopia, right eye
367.1 H52.12 Myopia, left eye 367.1 H52.13 Myopia, Bilateral 368.0 H53.001 Unspecified amblyopia, right eye
368.0 H53.002 Unspecified amblyopia, left eye
368.0 H53.003 Unspecified amblyopia, bilateral 368.0 H53.009 Unspecified Amblyopia 368.4 H53.40 Unspecified Visual Field Defects 368.46 Homonymous bilateral field defects, H53.461 right side
368.46 Homonymous bilateral field defects, left H53.462 side
Homonomymous Bilateral Field Defects, 368.46 H53.469 Unspecified Side 368.47 H53.47 Heteronymous Bilateral Field Defects 368.54 H53.51 Achromatopsia 368.8 H53.8 Other visual disturbances 368.8 H53.8 Unspecified Visual Disturbance unspecified visual loss (Delayed Visual 368.9 H53.9 Maturation) 369.4 H54.8 Legal blindness, as defined in USA 369.9 H02.315.403 Unspecified ptosis of bilateral eyelids
369.9 H02.401 Unspecified ptosis of right eyelid
369.9 H02.402 Unspecified ptosis of left eyelid 369.9 H54.7 Unspecified Visual Loss 377.1 H47.20 Unspecified Optic Atrophy 377.43 H47.031 Optic nerve hypoplasia, right eye
377.43 H47.032 Optic nerve hypoplasia, left eye
377.43 H47.033 Optic nerve hypoplasia, bilateral Optic Nerve Hypoplasia, Unspecified 377.43 H47.039 Eye 377.75 H47.611 Cortical blindness, right side of brain
377.75 H47.612 Cortical blindness, left side of brain Cortical Blindness, Unspecified Side of 377.75 H47.619 the Brain 378 H50.10 Exotropia Unspecified 378.00 H50.00 Esotropia Unspecified 378.71 H50.811 Duane’s Syndrome, Right Eye 378.71 H50.812 Duane’s Syndrome, Left Eye 378.73 H50.89 Other Specified Strabismus Unspecified disorder of binocular 378.9 H51.9 movement 379.31 H27.03 Aphakia Bilateral 379.5 H55.00 Unspecified nystagmus 379.5 H55.01 Congenital nystagmus Chronic serous otitis media, unspecified 381.10 H65.20 ear 381.10 H6521 Chronic serous otitis media, right ear
381.10 H6522 Chronic serous otitis media, left ear
381.10 H6523 Chronic serous otitis media, bilateral 389 H90.2 Conductive hearing loss, unspecified 389.14 H90.5 Unspecified Sensorineural Hearing Loss Sensorineural Hearing Loss, Unilateral, 389.15 H90.41 Right Ear, with Unrestricted Hearing on the Contralateral Side Sensorineural Hearing Loss, Unilateral, 389.15 H90.42 Left Ear, with Unrestricted Hearing on the Contralateral Side 389.18 H90.3 Sensorineural Hearing Loss, Bilateral 389.2 Mixed conductive and sensorineural H90.6 hearing loss, bilateral
389.2 Mixed conductive and sensorineural hearing loss, unilateral, right ear, with H90.71 unrestricted hearing on the contralateral side
389.2 Mixed conductive and sensorineural hearing loss, unilateral, left ear, with H90.72 unrestricted hearing on the contralateral side
Mixed Conductive and Sensorineural 389.20 H90.8 Hearing Loss, Unspecified Unspecified Hearing Loss, Unspecified 389.9 H91.90 Ear 389.9 H91.91 Unspecified hearing loss, right ear
389.9 H91.92 Unspecified hearing loss, left ear
389.9 H91.93 Unspecified hearing loss, bilateral Nontraumatic intracerebral hemorrhage, 431 I61.9 unspecified 437.9 I67.9 Cerebrovascular Disease, Unspecified 47.9 A87.9 Viral meningitis, unspecified 536.49 K94.29 Other complications of gastrostomy
Triplet pregnancy, unspecified number 651.1 O30.109 of placenta and unspecified number of amniotic sacs, unspecified trimester 714.0 M06.9 Rheumatoid arthritis, unspecified 736.06 M21.511 Acquired clawhand, right hand
736.06 M21.511 Acquired clawhand, right hand
736.06 M21.512 Acquired clawhand, left hand
736.06 M21.519 Acquired clawhand, unspecified hand
736.07 M21.521 Acquired clubhand, right hand
736.07 M21.522 Acquired clubhand, left hand
736.07 M21.529 Acquired clubhand, unspecified hand
736.71 M21.541 Acquired clubfoot, right foot 736.71 M21.542 Acquired clubfoot, left foot
736.71 M21.549 Acquired clubfoot, unspecified foot 736.74 M21.531 Acquired clawfoot, right foot
736.74 M21.532 Acquired clawfoot, left foot
736.74 M21.539 Acquired clawfoot, unspecified foot
Other idiopathic scoliosis, site 737.30 M41.20 unspecified Arnold-Chiari syndrome with spina 741.00 Q07.03 bifida and hydrocephalus 741.00 Q07.03 Arnold-Chiari syndrome with spina bifida and hydrocephalus
741.00 Q0701 Arnold-Chiari syndrome with spina bifida
741.00 Q0702 Arnold-Chiari syndrome with hydrocephalus
Sacral spina bifida without 741.9 Q05.8 hydrocephalus (Meningomyelocele, Meningocele) 741.90 Q05.9 Spina Bifida, Unspecified
742.0 Q01.9 Encephalocele, Unspecified 742.1 Q02 Microcephaly Congenital malformations of corpus 742.2 Q04.0 callosum 742.2 Q04.2 Holoprosencephaly Other Reduction Deformities of Brain 742.2 Q04.3 (Polymicrogyria) Other reduction deformities of brain 742.2 Q04.3 Lissencephaly Atresia of foramina of Magendie and 742.3 Q03.1 Luschka Dandy Walker Syndrome 742.3 Q03.8 Other congenital hydrocephalus 742.3 Q03.9 Congenital hydrocephalus, unspecified Congenital cerebral cysts Cortical 742.4 Q04.6 Dysplasia 742.4 Q04.6 schizencephaly
Other Specified Congenital 742.4 Q04.8 malformations of brain 742.51 Q06.2 Diastematomyelia Familial Dysautonomia (Riley-Day 742.8 G90.1 Syndrome, HSAN III) 742.9 G93.40 Encephalopathy, unspecified 743.0 Q11.1 Other Anophthalmos 743.1 Q11.2 Microphthalmia 743.20 Q15.0 Congenital Glaucoma 743.45 Q13.1 Absence of Iris (Aniridia) Other congenital malformations of 743.49 Q13.89 anterior segment of eye 743.61 Q10.0 Congenital ptosis Congenital Malformations of Ear 744 Q16.9 Causing Impairment of hearing, Unspecified Congenital absence, atresia and stricture 744.02 Q16.1 of auditory canal (external) 744.23 Q17.2 Microtia Other specified congenital anomalies of 744.29 Q17.8 ear Congenital malformation of ear, 744.3 Q17.9 unspecified Other Congenital Malformations of 746.89 Q23.8 Aortic and Mitral Valves Total anomalous pulmonary venous Q26.2 connection 747.41 749.00 Q35.9 Cleft palate, unspecified 749.10 Q36.0 Cleft lip, bilateral 749.10 Q36.9 Cleft Lip, unilateral 749.2 Q37.9 Cleft Palate with Cleft Lip 754.1 Q68.0 Congenital Torticollis 754.89 Q67.8 Other congenital deformities of chest 754.89 Q74.3 Arthrogryposis multiplex congenita Phocomelia, unspecified limb(s) 755.33 Q73.10
Congenital Absence of Unspecified 755.4 Q73.0 limbs Other Reduction Defects of Unspecified 755.4 Q73.8 Limbs Unspecified Congenital Malformation 755.5 Q74.9 of Limb(s) Unspecified Congenital Malformation 755.50 Q74.9 of Limb(s) 755.58 Q71.60 Lobster-claw hand, unspecified hand 755.58 Q71.61 Lobster-claw right hand
755.58 Q71.62 Lobster-claw left hand
755.58 Q71.63 Lobster-claw hand, bilateral Other specified congenital 755.8 Q74.8 malformations of limb(s) Larsen's Syndrome Congenital malformation syndromes 756 Q87.0 predominantly affecting facial appearance Robin’s Syndrome 756.0 Q75.0 Craniosynostosis Mandibulofacial Dysostosis 756.0 Q75.4 (Franschetti-Klein Syndrome) Congenital Anomalies of Skull and Face 756.0 Q75.9 Bone, unspecified (Goldenhar) Congenital malformation syndromes predominantly affecting facial 756.0 Q87.0 appearance Apert's Syndrome (Acrocephalosyndactyly I, ACS I) Congenital malformation syndromes predominantly affecting facial 756.0 Q87.0 appearance Saethre-Chotzen Syndrome (Chotzen's, Acrocephalosyndactyly III) Congenital malformation syndromes predominantly affecting facial 756.0 Q87.0 appearance Goldenhar's Syndrome (Oculoauriculovertebral Dysplasia) Other congenital malformations of 756.13 Q76.49 spine, not associated with scoliosis (Sacral Agenesis) 756.4 Q77.0 Achondrogenesis 756.4 Q77.4 Achondroplasia 756.4 Q77.5 Diastrophic Dysplasia 756.5 Q78.9 Osteochondrodysplasia, unspecified 756.51 Q78.0 Osteogenesis Imperfecta Other Specified Osteochondrodysplasia 756.59 Q78.8 (Acrodysplasia I) 756.6 Q79.0 Congenital Diaphragmatic Hernia 756.71 Q79.4 Prune Belly Syndrome 756.73 Q79.3 Gastroschisis 756.83 Q79.6 Cutis laxa senilis 756.83 Q79.6 Ehlers-Danlos Syndrome Other congenital malformations of 756.9 Q79.8 musculoskeletal system Poland's Syndrome Congenital Malformations of 756.9 Q79.9 Musculoskeletal System, Unspecified Other congenital ichthyosis Sjogren- 757.1 Q80.8 Larsson Syndrome Congenita Ichthyosis, Unspecified 757.1 Q80.9 (Harlequin Fetus) 757.33 Q82.1 Xeroderma Pigmentosum 758.0 Q90.0 Trisomy 21, nonmosaicism (meiotic nondisjunction) 758.0 Q90.1 Trisomy 21, mosaicism (mitotic nondisjunction)
758.0 Q90.2 Trisomy 21, translocation
758.0 Q90.9 Down Syndrome, Unspecified
758.1 Q91.4 Trisomy 13, nonmosaicism (meiotic nondisjunction)
758.1 Q91.5 Trisomy 13, mosaicism (mitotic nondisjunction)
758.1 Q91.6 Trisomy 13, translocation
758.1 Q91.7 Trisomy 13, Unspecified (Patau's, D1)
758.2 Q91.0 Trisomy 18, nonmosaicism (meiotic nondisjunction)
758.2 Q91.1 Trisomy 18, mosaicism (mitotic nondisjunction)
758.2 Q91.2 Trisomy 18, translocation
758.2 Q91.3 Trisomy 18, Unspecified (Edward's, E3)
Deletion of short arm of chromosome 758.31 Q93.4 5(Cri Du Chat or Cat's Cry)
758.32 Q93.81 Velo-cardio-facial Syndrome Deletions with other complex 758.39 Q93.7 rearrangements Other specified trisomies and partial 758.5 Q92.8 trisomies of autosomes 758.6 Q96.9 Turner's syndrome, unspecified 758.7 Q98.4 Klinefelter syndrome, unspecified Other Specified Chromosomal 758.8 Q99.8 Anomalies Other specified sex chromosome 758.81 Q97.8 abnormalities, female phenotype Other specified sex chromosome 758.81 Q98.8 abnormalities, male phenotype Chromosomal Abnormality, 758.9 Q99.9 Unspecified, (Coffin-Lowry Syndrome) Other deletions of part of a chromosome 759.39 Q93.5 (Angelman's Syndrome)
759.5 Q85.1 Tuberous Sclerosis Other Phakomatosis, not elsewhere 759.6 Q85.8 classified (Sturge-Weber Syndrome)
Congenital malformation syndromes 759.81 Q87.1 predominantly associated with short stature (Prader-Willi Syndrome) Other specified congenital 759.82 Q68.8 musculoskeletal deformities (Beals-Hecht Syndrome) 759.82 Q87.40 Marfan's Syndrome, Unspecified 759.83 Q99.2 Fragile X Syndrome For Boys 759.83 Q99.2 Fragile X Syndrome For Girls Congenital malformation syndromes 759.89 E78.72 predominantly associated with short stature Smith-Lemli-Opitz Syndrome 759.89 L94.0 Morphea 759.89 Q00.0 Anencephaly Congenital malformation syndromes predominantly affecting facial 759.89 Q87.0 appearance Oral-Facial-Digital Syndrome Congenital malformation syndromes 759.89 predominantly associated with short Q87.1 stature Congenital malformation syndromes 759.89 Q87.1 predominantly associated with short stature Noonan's Syndrome Congenital malformation syndromes 759.89 Q87.1 predominantly associated with short stature Russell (-Silver) Syndrome Congenital malformation syndromes 759.89 Q87.2 predominantly involving limbs Klippel-Trenaunay-Weber Syndrome Congenital malformation syndromes 759.89 Q87.2 predominantly involving limbs -Caudal Regression Syndrome (Sirenomelia) Congenital malformation syndromes 759.89 Q87.2 predominantly involving limbs Otopalatodigital Syndrome Congenital malformation syndromes 759.89 Q87.2 predominantly involving limbs Rubinstein-Taybi Syndrome Congenital malformation syndromes 759.89 Q87.2 predominantly involving limbs VATER Syndrome Congenital malformation syndromes 759.89 Q87.3 involving early overgrowth (Beckwith- Wiedemann Syndrome) Congenital malformation syndromes 759.89 Q87.3 involving early overgrowth Cerebral Gigantism (Soto's Syndrome) Congenital malformation syndromes 759.89 Q87.89 predominantly associated with short stature Dubowitz Syndrome Other specified congenital malformation syndromes, not elsewhere classified 759.89 Q87.89 Zellweger/Cerebrohepatorenal Syndrome Other specified congenital malformation 759.89 Q87.89 syndromes, not elsewhere classified (Biedl-Bardet Syndrome)
Other specified congenital malformation syndromes, not elsewhere classified 759.89 Q87.89 Langer-Giedion Syndrome (Acrodysplasia V, Klingmuller's) Spondyloepiphyseal dysplasia Dyggve- 759.89 Q87.89 Melchior-Clausen Syndrome (D-M-C Dwarfism) Other Specified Congenital 759.89 Q89.8 Malformations CHARGE Syndrome (CHARGE Association) Other deletions from the autosomes 759.89 Q93.89 Williams Syndrome
Newborn (suspected to be) affected by 760.70 P04.9 maternal noxious substance, unspecified Newborn (suspected to be) affected by 760.71 P04.3 maternal use of alcohol 760.71 Q86.0 Fetal alcohol syndrome (dysmorphic)
Newborn (suspected to be) affected by 760.72 P04.49 maternal use of other drugs of addiction Newborn (suspected to be) affected by 760.75 P04.41 maternal use of cocaine Newborn (suspected to be) affected by 760.79 P04.8 other abnormalities of membranes 760.79 Q86.1 Fetal hydantoin syndrome Newborn light for gestational age, 764.0 P05.00 unspecified weight Extremely low birth weight newborn, 765.01 P07.01 less than 500 grams Extremely low birth weight newborn, 765.02 P07.02 500-749 grams Extremely low birth weight newborn, 765.03 P07.03 750-999 grams Other low birth weight newborn, 765.10 P07.10 unspecified weight Other low birth weight newborn, 1000- 765.14 P07.14 1249 grams Other low birth weight newborn, 1250- 765.15 P07.15 1499 grams Other low birth weight newborn, 1500- 765.16 P07.16 1749 grams Extreme immaturity of newborn, 765.21 P07.21 gestational age less than 23 completed weeks Extreme immaturity of newborn, 765.21 P07.22 gestational age 23 completed weeks Extreme immaturity of newborn, 765.22 P07.23 gestational age 24 completed weeks Extreme immaturity of newborn, 765.23 P07.24 gestational age 25 completed weeks Extreme immaturity of newborn, 765.23 P07.25 gestational age 26 completed weeks
Extreme immaturity of newborn, 765.24 P07.26 gestational age 27 completed weeks Preterm newborn, gestational age 28 765.24 P07.31 completed weeks Preterm newborn, gestational age 29 765.25 P07.32 completed weeks Preterm newborn, gestational age 30 765.25 P07.33 completed weeks
Preterm newborn, gestational age 31 765.26 P07.34 completed weeks Preterm newborn, gestational age 32 765.26 P07.35 completed weeks Preterm newborn, gestational age 33 765.27 P07.36 completed weeks Preterm newborn, gestational age 34 765.27 P07.37 completed weeks 767.6 P14.0 Erb’s Paralysis due to Birth Injury Other Problems with Newborns (birth 768.6 P84 asphyxia NOS, Severe) Hypoxic ischemic encephalopathy [HIE], 768.70 P91.60 unspecified Other problems with newborn 770.88 P84 Intrauterine hypoxia 771.0 P35.0 Congenital rubella syndrome 771.1 P35.1 Congenital cytomegalovirus infection Infection specific to the perinatal period, 771.2 P39.9 unspecified 771.3 A33 Tetanus neonatorum Unspecified intraventricular 772.10 P52.3 (nontraumatic) hemorrhage of newborn Intraventricular (nontraumatic) 772.11 P52.0 hemorrhage, grade 1, of newborn Intraventricular (nontraumatic) 772.12 P52.1 hemorrhage, grade 2, of newborn Intraventricular (nontraumatic) 772.13 P52.21 hemorrhage, grade 3, of newborn Intraventricular (nontraumatic) 772.14 P52.22 hemorrhage, grade 4, of newborn Subarachnoid (nontraumatic) 772.2 P52.5 hemorrhage of newborn 772.8 P54.8 Other specified neonatal hemorrhages
775.6 P70.4 Other neonatal hypoglycemia Perinatal hematological disorder, 776.9 P61.9 unspecified 779.0 P90 Convulsions in newborn 779.2 Neonatal cerebral ischemia P91.0 779.2 Acquired periventricular cysts of P91.1 newborn
779.2 P91.2 Neonatal cerebral leukomalacia 779.2 P91.4 Neonatal Cerebral Depression 779.2 P91.5 Neonatal Coma Feeding problem of newborn, 779.31 P92.9 unspecified Other reactions and intoxications due to 779.4 P93.8 drugs administered to newborn Neonatal withdrawal symptoms from 779.5 P96.1 maternal use of drugs of addiction 779.85 P29.81 Cardiac arrest of newborn 780.39 R56.9 Unspecified convulsions 781.3 P94.2 Congenital hypotonia 783.81 R62.7 Failure to thrive (child) 784.3 R47.01 Aphasia Abnormal findings on neonatal 796.6 P09 screening 806.0 P11.5 Birth injury to spine and spinal cord Toxic Effects of Lead and Its 907.3 T56.0X1A Compounds, accidental (unintentional), Initial Encounter 909.9 T74.4XXS Shaken infant syndrome, sequela Injury of Brachial Plexus, Initial 953.4 S14.3XXA Encounter Toxic Effects of Lead and Its 984.9 T56.0X15 Compounds, accidental (Sequela), Initial Encounter Shaken infant syndrome, initial 995.55 T74.4XXA encounter Other specified problems related to psychosocial circumstances V11.3 Z65.8 (Interpersonal problems, not elsewhere classified) Personal history of adult physical and V15.41 Z91.410 sexual abuse (e.g., sexual abuse or rape) Personal history of adult neglect (e.g., V15.42 Z91.412 neglect) Other personal history of psychological V15.49 Z91.49 trauma, not elsewhere classified Contact with and (suspected) exposure V15.86 Z77.011 to lead Other contact with and (suspected) V15.89 Z77.9 exposures hazardous to health Other specified personal risk factors, not V15.9 Z91.89 elsewhere classified Family history of other mental and V17.0 Z81.8 behavioral disorders Family history of epilepsy and other V17.2 Z82.0 diseases of the nervous system Family history of other diseases of the V17.89 Z82.69 musculoskeletal system and connective tissue Family History of Intellectual Z81.0 V18.4 Disabilities Family history of blindness and visual V19.0 Z82.1 loss Family history of deafness and hearing V19.2 Z82.2 loss Family history of other congenital V19.5 Z82.79 malformations, deformations and chromosomal abnormalities Family history of other specified V19.8 Z84.89 conditions Encounter for health supervision and care of other healthy infant and child Z76.2 (e.g., supervision of healthy infant in cases of socioeconomic adverse V20.1 condition at home) Newborn (suspected to be) affected by V29.9 P00.9 unspecified maternal condition V58.89 Injury of Brachial Plexus, Subsequent S14.3XXD Encounter Shaken infant syndrome, subsequent V58.89 T74.4XXD encounter Homelessness (e.g., Social migrants, V60.0 Z59.0 Transients) Inadequate housing (e.g., Lack of V60.1 Z59.1 heating, Restriction of space) Low income (e.g., Economic problem, V60.2 Z59.6 Poverty) Need for assistance at home and no V60.4 Z74.2 other household member able to render care Other problems related to housing and V60.89 Z59.8 economic circumstances Unspecified housing or economic V60.9 Z59.9 circumstance Encounter for mental health services for victim of spousal or partner abuse V61.11 Z69.11 (Counseling for victim of spousal and partner abuse) Encounter for mental health services for V61.12 Z69.12 perpetrator of spousal or partner abuse (Counseling for perpetrator of spousal and partner abuse)
Encounter for mental health services for perpetrator of parental child abuse V61.21 Z69.010 Counseling for parent-child problem, unspecified Encounter for mental health services for V61.21 Z69.020 victim of parental child abuse Counseling for victim of child abuse Other specified problems related to V61.29 Z62.898 upbringing (e.g., Problem concerning adopted or foster child)
Alcoholism and drug addiction in V61.41 Z63.72 family Dependent relative needing care at V61.49 Z63.6 home (e.g., Care of sick or handicapped person in family or household) Other specified problems related to V61.8 Z69.891 primary support group Problem related to primary support V61.9 Z63.9 group, unspecified
Acculturation difficulty (e.g., Cultural V62.4 Z60.3 deprivation, Social isolation or persecution) Problems related to other legal V62.5 Z65.3 circumstances (e.g., Imprisonment) Other specified problems related to V62.89 Z64.4 psychosocial circumstances (e.g., Life circumstance problems) Problem related to unspecified V62.9 Z65.9 psychosocial circumstances Other specified counseling (Counseling V65.49 Z71.89 for marital and partner problems, unspecified) Problems related to lifestyle, V69.9 Z72.9 unspecified Encounter for screening for certain V79.8 Z13.4 developmental disorders in childhood V907.3 Injury of Brachial Plexus, Sequela S14.3XXS Encounter V91.12 Triplet pregnancy with two or more O30.129 monoamniotic fetuses, unspecified trimester V91.19 Triplet pregnancy, unable to determine O30.199 number of placenta and number of amniotic sacs, unspecified trimester