Sarah Ballantyne, PhD 1717

The Spectrum of Autoimmune The following is a that are either confirmed autoimmune diseases or for which there is very strong scientific evidence for autoimmune origins:

Acute brachial neuropathy (also Atrophic polychondritis (also known Besnier-Boeck (also known A known as acute brachial radiculitis, as systemic chondromalacia and as ) neuralgic amyotrophy, brachial ) Bickerstaff’s encephalitis neuritis, brachial plexus neuropathy, Autoimmune angioedema Bladder pain syndrome (also known brachial plexitis, and Parsonage- Autoimmune aplastic (also as interstitial cystitis) Turner syndrome) known as ) Brachial neuritis (also known as Acute disseminated Autoimmune cardiomyopathy brachial plexus neuropathy, brachial encephalomyelitis (ADEM) Autoimmune dysautonomia plexitis, Parsonage-Turner syndrome, Acute necrotizing hemorrhagic acute brachial neuropathy, acute Autoimmune hemolytic anemia leukoencephalitis brachial radiculitis, and neuralgic Acute (also known as amyotrophy) acute guttate parapsoriasis, acute Autoimmune hyperlipidemia Bullous pemphigoid pityriasis lichenoides, parapsoriasis Autoimmune immunodeficiency Castleman’s disease (also varioliformis, Mucha-Habermann C known as giant lymph node disease, and parapsoriasis or Autoimmune inner ear disease hyperplasia, lymphoid hamartoma, pityriasis lichenoides et varioliformis (AIED) and angiofollicular lymph node acuta) Autoimmune myocarditis hyperplasia) Addison’s disease (also Autoimmune pancreatitis Celiac disease (also known as known as chronic adrenal Autoimmune coeliac disease and celiac sprue) insufficiency, hypocortisolism, and (also known as peripheral hypoadrenalism) neuropathy) Chagas disease (also known as American trypanosomiasis) Adult linear IgA disease (also known Autoimmune polyendocrine as linear IgA disease) syndrome (APS) Chorea minor (also known as Sydenham’s chorea) Agammaglobulinemia Autoimmune polyglandular Chronic Allergic granulomatosis (also known syndrome, Types 1, 2, and 3 (also known as hypocortisolism, as Churg-Strauss syndrome) Autoimmune progesterone hypoadrenalism, and Addison’s (AA; also known as dermatitis disease) spot baldness) Autoimmune retinopathy Chronic focal encephalitis (CFE; American trypanosomiasis (also Autoimmune thrombocytopenic also known as Rasmussen’s known as Chagas disease) (ATP; also known as encephalitis) Amyloidosis thrombotic thrombocytopenic Chronic inflammatory demyelinating Anaphylactoid purpura (also known purpura and idiopathic polyneuropathy (CIDP) thrombocytopenic purpura) as purpura rheumatica and Henoch- Chronic lymphocytic thyroiditis (also Schönlein purpura) Autoimmune thyroid disease known as Hashimoto’s thyroiditis) Angiofollicular lymph node Autoimmune urticaria Chronic recurrent multifocal hyperplasia (also known as Autoimmune (also known as ostomyelitis (CRMO) Castleman’s disease, giant lymph uveitis) Chronic urticaria as a manifestation node hyperplasia, and lymphoid Axonal and neuronal neuropathies of venulitis (also known as urticarial hamartoma) Balo disease (also known as Balo vasculitis) (AS; also B concentric sclerosis) Churg-Strauss syndrome (also known as Bekhterev’s disease and known as allergic granulomatosis) Marie-Strümpell disease) Behçet’s disease (also known as Silk Road disease) Cicatricial pemphigoid (also known Anti-GBM or anti-TBM nephritis Bekhterev’s disease (also known as as benign mucosal pemphigoid) Antiphospholipid syndrome (APS ankylosing spondylitis and Marie- Cogan’s syndrome or APLS; also known as Hughes Strümpell disease) syndrome) Cold agglutinin disease Benign mucosal pemphigoid (also Aplastic anemia (also known as Congenital heart block known as cicatricial pemphigoid, autoimmune aplastic anemia) benign mucous membrane Coxsackie viral myocarditis psoriatica (also known as pemphigoid, scarring pemphigoid, Cranial (also known as arthropathic and psoriatic and ocular cicatricial pemphigoid) Horton disease, giant cell arteritis, arthritis) Berger’s disease (also known as and temporal arteritis) Arthropathic psoriasis (also known IgA nephropathy and synpharyngitic CREST syndrome (also known as arthritis psoriatica and psoriatic glomerulonephritis) as limited systemic sclerosis or arthritis) ) 1818 The Paleo Approach

Crohn’s disease H Hashimoto’s thyroiditis (also known Landry’s paralysis (also known as Crow-Fukase syndrome (also as chronic lymphocytic thyroiditis) Miller Fisher syndrome and Guillain- known as Takatsuki disease, PEP Hashimoto’s encephalitis or Barré syndrome) syndrome, and POEMS syndrome) encephalopathy Leukocytoclastic vasculitis Cryptogenic fibrosing alveolitis Henoch-Schönlein purpura (also (CFA; also known as idiopathic known as anaphylactoid purpura Lichen sclerosus pulmonary fibrosis and fibrosing and purpura rheumatica) Ligneous conjunctivitis alveolitis) Herpes gestationis (also known as Limited systemic sclerosis (also Demyelinating neuropathies (also gestational pemphigoid) known as limited systemic D known as idiopathic inflammatory Horton disease (also known as giant scleroderma and CREST syndrome) demyelinating diseases) cell arteritis, temporal arteritis, and Linear IgA disease (LAD; also Dermatomyositis (DM) cranial arteritis) known as adult linear IgA disease) Devic’s disease (also known as Hughes syndrome (also known as (also known as systemic neuromyelitis optica) antiphospholipid syndrome) lupus erythematosus) Diabetes mellitus type 1 (also known Hypocortisolism (also known as , chronic as insulin-dependent diabetes and hypoadrenalism, Addison’s disease, type 1 diabetes) and chronic adrenal insufficiency) Lymph node syndrome (also known as mucocutaneous lymph node Discoid lupus erythematosus (DLE) syndrome and Kawasaki disease) Dressler’s syndrome (also known as Idiopathic inflammatory bowel Lymphoid hamartoma (also known postmyocardial infarction syndrome) I disease (includes both Crohn’s as angiofollicular lymph node disease and ulcerative colitis) Duhring’s disease (also known as hyperplasia, Castleman’s disease, dermatitis herpetiformis) Idiopathic inflammatory and giant lymph node hyperplasia) demyelinating diseases (also known Endocarditis lenta (also known as Marchiafava-Micheli syndrome (also as demyelinating neuropathies) E subacute bacterial endocarditis) M known as paroxysmal nocturnal Endometriosis Idiopathic pulmonary fibrosis (IPF; hemoglobinuria) also known as cryptogenic fibrosing Eosinophilic esophagitis or Marie-Strümpell disease (also alveolitis and fibrosing alveolitis) gastroenteritis known as ankylosing spondylitis Idiopathic thrombocytopenic Eosinophilic fasciitis and Bekhterev’s disease) purpura (ITP; also known as Ménière’s disease Erythema nodosum thrombocytopenic purpura and Erythroblastopenia (also known as autoimmune thrombocytopenic Microscopic polyangiitis (also ) purpura) known as microscopic polyarteritis) Essential mixed cryoglobulinemia IgA nephropathy (also known as Miller Fisher syndrome (also known as Guillain-Barré syndrome and Evans syndrome synpharyngitic glomerulonephritis and Berger’s disease) Landry’s paralysis) Experimental allergic Mixed connective tissue disease encephalomyelitis (EAE) IgG4-related sclerosing disease (MCTD; also known as Sharp’s Inclusion body myositis Fibrosingalveolitis (also known as syndrome) F idiopathic pulmonary fibrosis and Insulin-dependent diabetes (also Moersch-Woltman condition (also cryptogenic fibrosing alveolitis) known as type 1 diabetes and known as stiff person syndrome) Gestational pemphigoid (also known diabetes mellitus type 1) Mooren’s ulcer G as herpes gestationis) Interstitial cystitis (also known as Mucha-Habermann disease Giant cell arteritis (also known as bladder pain syndrome) (also known as acute guttate temporal arteritis, cranial arteritis, Juvenile diabetes (also known as parapsoriasis, acute parapsoriasis, and Horton disease) J diabetes mellitus type 1, insulin- acute pityriasis lichenoides, dependent diabetes, and type 1 Giant lymph node hyperplasia (also and parapsoriasis or pityriasis diabetes) known as lymphoid hamartoma, lichenoides et varioliformis acuta) angiofollicular lymph node Juvenile rheumatoid arthritis (also Mucocutaneous lymph node hyperplasia, and Castleman’s known as juvenile idiopathic arthritis syndrome (also known as lymph disease) and Still’s disease) node syndrome and Kawasaki Glomerulonephritis Kawasaki syndrome (also known disease) K as Kawasaki disease, lymph node Goodpasture’s syndrome Multiple sclerosis syndrome, and mucocutaneous Granulomatosis with polyangiitis lymph node syndrome) Myasthenia gravis (GPA; also known as Wegener’s Myositis granulomatosis) Kussmaul-Maier disease (also known as polyarteritis nodosa) Narcolepsy Graves’ disease N Lambert-Eaton syndrome Neuromyelitis optica (also known as Guillain-Barré syndrome (also L (also known as Lambert-Eaton Devic’s disease) known as Landry’s paralysis and myasthenic syndrome) Miller Fisher syndrome) Neutropenia Sarah Ballantyne, PhD 1919

Ocular cicatricial pemphigoid Progressive hemifacial Stiff person syndrome (also known O (also known as benign mucous (also known as Parry Romberg as Moersch-Woltman condition) membrane pemphigoid and scarring syndrome) Still’s disease (also known as pemphigoid) Psoriasis juvenile rheumatoid arthritis and Optic neuritis Psoriatic arthritis (also known as juvenile idiopathic arthritis) Ord’s thyroiditis arthritis psoriatica and arthropathic Subacute bacterial endocarditis Ormond’s disease (also known as psoriasis) (SBE; also known as endocarditis retroperitoneal fibrosis) Pure red cell aplasia (also known as lenta) Palindromic rheumatism erythroblastopenia) Susac’s syndrome (also known as P retinocochleocerebral vasculopathy) Paraneoplastic cerebellar Purpura rheumatic (also known as degeneration Henoch-Schönlein purpura and Sydenham’s chorea (also known as anaphylactoid purpura) chorea minor) Parapsoriasis varioliformis (also known as Mucha-Habermann Pyoderma gangrenosum Sympathetic ophthalmia (SO) disease acute guttate parapsoriasis, Rasmussen’s encephalitis (also Synpharyngitic glomerulonephritis acute parapsoriasis, acute pityriasis R known as chronic focal encephalitis) (also known as Berger’s disease lichenoides, parapsoriasis or Raynaud’s phenomenon, disease, and IgA nephropathy) pityriasis lichenoides et varioliformis or syndrome Systemic chondromalacia (also acuta) Reactive arthritis (also known as known as relapsing polychondritis Paroxysmal nocturnal Reiter’s syndrome) and atrophic polychondritis) hemoglobinuria (PNH; also known Reflex sympathetic dystrophy Systemic lupus erythematosus as Marchiafava-Micheli syndrome) (SLE; also known as lupus) Reiter’s syndrome (also known as Parry-Romberg syndrome (also reactive arthritis) Takatsuki disease (also known as known as progressive hemifacial T PEP syndrome, POEMS syndrome, Relapsing polychondritis (also atrophy) and Crow-Fukase syndrome) known as atrophic polychondritis Pars planitis (also known as and systemic chondromalacia) Takayasu’s arteritis or disease peripheral uveitis) Restless legs syndrome (also known Temporal arteritis (also known as Parsonage-Turner syndrome as Willis-Ekbom disease) giant cell arteritis, cranial arteritis, (also known as acute brachial and Horton disease) neuropathy, acute brachial Retinocochleocerebral vasculopathy Thrombocytopenic purpura radiculitis, neuralgic amyotrophy, (also known as Susac’s syndrome) (TTP; also known as idiopathic brachial neuritis, brachial plexus Retroperitoneal fibrosis (also known thrombocytopenic purpura and neuropathy, and brachial plexitis) as Ormond’s disease) autoimmune thrombocytopenic Pediatric autoimmune purpura) neuropsychiatric disorders Rheumatoid arthritis Tolosa-Hunt syndrome associated with streptococcus (PANDAS) Sarcoidosis (also known as Besnier- Transverse myelitis S Boeck disease) vulgaris Type I diabetes (also known as Scarring pemphigoid (also known diabetes mellitus type 1 and insulin- PEP syndrome (also known as as ocular cicatricial pemphigoid dependent diabetes) POEMS syndrome, Crow-Fukase and benign mucous membrane Types 1, 2, and 3 autoimmune syndrome, and Takatsuki disease) pemphigoid) polyglandular syndrome Peripheral neuropathy (also Schmidt’s syndrome (also known Ulcerative colitis known as autoimmune peripheral as autoimmune polyendocrine U neuropathy) syndrome type 2) Undifferentiated connective tissue disease (UCTD) Perivenous encephalomyelitis Schnitzler syndrome Urticarial vasculitis (also known as Pernicious anemia Scleritis chronic urticaria as a manifestation POEMS syndrome (also known as Scleroderma of venulitis) Crow-Fukase syndrome, Takatsuki disease, and PEP syndrome) Sharp’s syndrome (also known as Uveitis (also known as autoimmune mixed connective tissue disease) uveitis) Polyarteritis nodosa (also known as Kussmaul-Maier disease) Sicca syndrome (also known as Vasculitis Sjögren’s syndrome) V Polymyalgia rheumatica Vesiculobullous dermatosis Silk Road disease (also known as Vitiligo Polymyositis (PM) Behçet’s disease) Wegener’s granulomatosis (also Postmyocardial infarction syndrome Sjögren’s syndrome (also known as W known as granulomatosis with (also known as Dressler’s syndrome) Sicca syndrome) polyangiitis) Postpericardiotomy syndrome Sperm and testicular autoimmunity Willis-Ekbom disease (also known Primary biliary (PBC) Spot baldness (also known as as restless leg syndrome) Primary sclerosing cholangitis (PSC) alopecia areata)