453

General disease finder 455

This overview will help to find neuromuscular disease patterns in the different sections

Cushing‘s disease: steroid Adrenal dysfunction Addison’s disease: general muscle weakness

Periodic paralysis Aldosteronism Tetanic muscles

CN: VII AIDS : inflammatory, immune mediated, treatment related : inflammatory, treatment related Neoplastic: Lymphoma (direct invasion) Opportunistic infections: CMV, Toxoplasmosis, Cryptococcus, HSV, Candida, Varicella, Histoplasma, TBC, Aspergillus CMV polyradiculomyelopathy Herpes zoster radiculitis Syphilitic Treatment related: /myopathy Ddl, ddC, Foscarnet, Isoniazid Zidovudine

Polyneuropathy (distal, rarely proximal, rare ulcers) Alcoholism Mononeuropathy- (compression) Myopathy Acute necrotizing myopathy and myoglobinuria Chronic proximal weakness Hypokalemic paralysis Myoglobinuria Compartment syndromes (prolonged compression)

Familial amyloid polyneuropathies Amyloid Transthyretin Sensorimotor neuropathy Autonomic involvement Apolipoprotein A-1 Polyneuropathy, painful, hearing loss Gelsolin type V, VII and other CN Mild polyneuropathy Primary amyloidosis (AL) Deposition of immunoglobulin light chains in tissue 456

Painful neuropathy Autonomic involvement Muscle amyloid Amyloidoma (trigeminal root) Secondary or reactive amyloidosis (AA) Chronic inflammatory diseases, rheumatoid diseases, osteomyelitis Deposition of acute phase plasma protein, serum amyloid A: polyneuropathy not significant

Anemia Cobalamin deficiency, polyneuropathy Lead poisoning polyneuropathy Thalassemia: muscle cramps, , muscle atrophy Pure red cell anemia: autoimmune disease associated with myasthenia gravis

Anesthesia Regional: Epidural or spinal anesthesia may cause cauda equina lesions Malpositioning Upper extremity (70%): Mononeuropathies of brachial, radial, ulnar, or median nerves Lower extremity (30%): Mononeuropathies of peroneal, sciatic, or femoral nerves Cardiac bypass operations: nerve stretch, hypothermia, phrenic nerve lesions Tourniquet palsy Neuromuscular transmission disorders induced by muscle relaxants

Angiography Peripheral: Axillary or femoral artery puncture (brachial plexus and femoral nerve) Brachial artery: Cerebral angiography: femoral nerve lesions

Anorexia nervosa Myopathy Polyneuropahty

Asthma Acute ICU steroid myopathy (status asthmaticus) Steroid myopathy Entrapment neuropathies and compression (ulnar, peroneal nerves) Churg Strauss syndrome

Auditory nerve Hearing loss: Refsum’s disease, , mitochondrial disorders, vasculitis, some types of amyloidosis and hereditary neuropathies

Bone marrow CIDP transplantation Inflammatory myopathies MG Polyneuropathy 457

Facial nerve lower branch Carotid surgery Hypoglossal nerve Vagal recurrent nerve

Cranial nerves (meningeal carcinomatosis, base of the skull metastasis) Cancer Mononeuropathies (pressure, toxic, following operations) (meningeal carcinomatosis, compression or infiltration of roots, multiple spinal metastasis), cauda equina syndrome Polyneuropathies (treatment related and paraneoplastic, rarely infiltrative) Myopathies: cachexia, dermatomyositis/polymyositis, necrotizing, neuromyo- tonia Neuromuscular transmission: MG and thymoma, LEMS and () cancer Antineoplastic treatment associated polyneuropathy: Cisplatinum (Carboplatin, Oxaliplatin) Podophyllin derivatives Procarbazine Taxanes Suramin Vinca alkaloids Radiation: Plexopathies (brachial, lumbar, sacral) Paraneoplastic disease Cranial nerve: Optic nerve Polyneuropathies (all types) LEMS Muscle: inflammatory and necrotizing myopathies

Aortic disease: Circulatory disorders – Left recurrent laryngeal nerve palsy – Femoral nerve lesion (ruptured aneurysm, aortic surgery) – Obturator nerve: hematoma in psoas muscle – Radiculopathies: compression of L4,5 and S1, 2 by terminal aorta – Ischemic monomelic: predominately sensory with causaglia like pain

Cholesterol lowering drugs: Myopathy, cramps (Fenofibrate, benzafibrate, clofibrate, gemfibrozil, nico- tinic acid lovastatin, simvastatin, pravastatin) Embolism-compartment syndrome Intermittent claudication Ischemic neuropathy, angiopathic neuropathies Muscle hemorrhage: hemophiliacs, anticoagulants: retroperitoneal, buttock, arm, calf Neuropathy by fistula- hemodialysis Monomelic neuropathy Nerve compression by hematoma (femoral nerve, lumbar plexus, ) 458

Temporary aortic occlusion (surgery) Venous occlusion-phlegmasia cerulea dolens

Coma Cranial nerve lesions Critical illness myopathies Critical illness neuropathy Mononeuropathies (malpositioning) Steroid myopathy Thick filament myopathy

Complications of medical Hip and joint surgery: sciatic, femoral nerve lesions and surgical treatment Hypothermia: polyneuropathy Injection into nerves: Mononeuropathies Nerve blockade Intramuscular injections Knee surgery: peroneal nerve, ramus infrapatellaris Mononeuropathies due to body position: plexus, radial, ulnar, median, pero- neal, femoral nerve lesions Muscle: Drug induced myopathy: acute hypokalemic paralysis, necrotizing myopathy, subacute and chronic myopathies, ischemic injury during surgery Neuromuscular transmission: drug induced MG Neuromuscular blocking agents Postoperatively: GBS, postoperative apnea, malignant hyperthermia Radiation: Spinal cord and nerve plexus (brachial, lumbar and sacral plexus) mononeuro- pathies Spinal anesthesia: nerve roots, epidural hemorrhage, paraplegia, sensory loss, adhesive arachnoiditis Surgical trauma: neck surgery, mastectomy, (thoracodorsal, long thoracic, axil- lary nerve), median sternotomy, pelvic surgery (sciatic, obturator, femoral, ilioinguinal, iliohypogastric nerve) Tourniquet paralysis

Diabetes mellitus Autonomic neuropathy Cranial mononeuropathies Mononeuropathies Muscle infarction Polyneuropathy; several distinct types Thoracic (truncal) radicular lesions

Immobilization Disuse myopathy Mononeuropathies: pressure palsies 459

Heroin: nerve compression (coma), trauma from injection, brachial and lum- Drugs and addiction bosacral plexopathies Phenylcyclidine: Cocaine: rhabdomyolysis

Hypercalcemia: muscle weakness Electrolyte disorders Hypocalcemia: tetany Hypokalemic paralysis Hypokalemic myopathy Hyperkalemia: potassium retaining diuretics Hypermagnesemia muscle weakness Hypomagnesemia muscle weakness Hypernatremia: muscle weakness

Churg Strauss syndrome Eosinophilic syndromes Eosinophilic Eosinophilic polymyositis Eosinophilia myalgia syndromes

Acute abdomen: porphyria, lead poisoning-polyneuropathy Gastrointestinal disorders Chronic : malabsorption neuropathies, Whipple’s disease, celiac dis- ease Celiac disease: myopathy Crohn’s disease: polymyositis

Compartment syndromes Ischemia/peripheral Polyneuropathy vascular occlusive Hepatic disease GBS Hepatitis Primary biliary cirrhosis: myopathy, neuropathy Polymyositis Polyneuropathy (hepatitis B, C) Panarteritis nodosa (hepatitis B) Demyelinating polyneuropathy Biliary cirrhosis Sensory polyneuropathy Hepatic myelopathy Acquired hepatocerebral degeneration Polyneuropathy Chronic liver disease

Hemophilia: Hematologic diseases Nerve compression (femoral nerve, hemorrhage into iliac muscle) compression Median nerve, radial nerve, sciatic nerve, peroneal nerve Thrombocytopenia: Rarely affects peripheral nerves 460

Complications of anticoagulation: Brachial plexus lesions Median nerve Femoral nerve Obturator nerve Sciatic nerve

Polyneuropathy: POEMS syndrome Castleman’s syndrome Waldenstrom’s Lymphoma, HIV

Hyperuricemia Median nerve mononeuropathy Polyneuropathy Radiculopathy

Hypnotic drugs Polyneuropathies: Amitryptiline Gluthethimide Imipramine Li+ carbonate Metaqualone Perazine Phenelzine

Immunization Influenza, swine flu: GBS Mumps: sensorineural deafness Oral polio: GBS Macrophagic microfasciitis (hepatitis A,B, tetanus) Toxoids: Diphtheria/tetanus: GBS Hemophilus influenzae: GBS Plasma derived hepatitis B: GBS

Infections Bacterial meningitis: cranial nerve lesions Hepatitis: A: GBS B: GBS, periarteritis nodosa C: Polyneuropathy (vasculitis)

Herpes zoster: Cranial nerves: ophthalmic, trigeminal, Ramsay Hunt syndrome Postherpetic Leprosy: Leprous Lepromatous leprosy: Skin, superficial nerves 461

Sensory loss (cool areas) Ulnar: proximal to ulnar groove Median: proximal to carpal tunnel Peroneal nerve Tuberculoid: Mixed nerve near the tubercle Ulnar, median, peroneal, facial nerve Enlarged superficial cutaneous, radial nerve Digital, sural nerves Lyme disease: Cranial nerves: VII (possibly bilateral) Radiculoneuritis (Garin-Bujadoux-Bannwarth syndrome) Polyneuropathy (unclear) Root involvement Truncal muscle weakness Neurosyphilis: Cranial nerves: pupillary abnormality Tabes dorsalis (“Lightning pain”) Posterior nerve root, , bladder and sexual dysfunction Tuberculosis: Cranial nerves (meningitis): VI, III, IV Retrobulbar with Myelitis Tuberculous arachnoiditis: radiculomyelopathy Tuberculomas Typhoid : multifocal neuropathy Parasitic infections: Amebic meningoencephalitis: olfactory nerve, smell Angiostrongyliasis: radiculomyeloneuritis Eosinophilic meningitis: cranial neuropathies, Onchocerciasis: blindness Paragonimus: optic atrophy Poliomyelitis: Muscle weakness Laryngeal and pharyngeal Facial diplegia “Postpolio syndrome” Trichinosis-muscle, respiration, and cardial and skeletal muscles Viral meningitis: Enterovirus: poliomyelitis GBS Mumps: deafness Viral: Myopathy Herpes Rabies 462

Postviral complications: Optic neuritis: measles, rubella, mumps, varicella zoster, infectious hepatitis, mononucleosis, rabies vaccine Cranial nerves: mumps GBS: CMV, enterovirus, Epstein Barr, herpes simplex, hepatitis B, HIV, influenza A and B, measles, rabies, rubella, smallpox vaccination Deafness and vertigo: mumps, measles, varicella, influenza, HSV Antimicrobial therapy: Emetine induced myopathy Isoniazide neuropathy Ethambutol neuropathy Nitrofurantoin neuropathy Streptomycin-ototoxicity Sulfonamide vasculitis Metronidazole neuropathy Inflammatory and Infection and immunization: brachial neuritis immune diseases Cranial nerves: VI, VII, vagus Mononeuropathies: serum sickness, acute mononeuropathies: long thoracic, radial, suprascapular, musculocutaneous, femoral, sciatic, anterior interosseus nerve, intercostal, phrenic nerve Polyneuropathy: Migratory recurrent polyneuropathy GBS CIDP Postinfectious and allergic neuropathies Chronic idiopatic neuritis Collagen vascular disease Myopathies: Dermato- and polymyositis Lupus Multiplex neuropathy-vasculitis Periarteritis nodosa Rheumatoid arthritis Miscellaneous: Sarcoid Behcet‘s disease Lyme disease Lipid metabolism Alpha 1 lipoprotein deficiency: polyneuropathy A-betalipoproteinemia: polyneuropathy Hyperlipidemia: polyneuropathy

Lung disease Lung cancer: paraneoplastic disease Sarcoid-polyneuropathy Pneumonia: phrenic neuropathy 463

Cranial nerves: trigeminal Lupus, SLE Mononeuropathies (median, ulnar) Polyneuropathy (sensorimotor) (see rheumatoid disease) see cancer Lymphoma

Malnutrition induced myopathy Malnutrition Polyneuropathy Posterolateral cord degeneration Vitamin B12 deficiency

Susceptibility in several diseases: Malignant hyperpyrexia Central core disease Duchenne’s dystrophy Myotonia congenita Myotonic dystrophy

Muscle weakness in: Mineral and electrolyte Potassium: hypokalemia, hyperkalemia disorders Tetany, hypocalcemia Hypomagnesemia

Fabry’s: corneal clouding Ophthalmologic Retinal microaneurysms: diabetes mellitus complications “Beaded retinal vasculature”: vasculitis Myotonic dystrophy : Refsum’s disease, Cockayne syndrome, Bassen-Kornweig disease Sicca syndrome: Sjögren’s syndrome Xerophthalmia: Sjögren’s syndrome, LEMS Optic disk : POEMS syndrome, CIDP, GBS

Myopathy Osteomalacia

Cranial nerves: Paraneoplastic Paraneoplastic retinal degeneration neuromuscular syndromes “Numb chin syndrome”

Polyneuropathy: Distal sensorimotor Sensory, subacute sensory neuronopathy Vasculitic neuropathy

Paraproteinemic neuropathies: of uncertain significance (MGUS) Anti-MAG IgM POEMS 464

Neuromuscular transmission: LEMS MG (thymoma) Neuromyotonia Myopathy: Dermatomyositis Necrotizing myopathy Type 2 Fiber atrophy “cachectic myopathy” Parathyroid disease Myopathy, bulbar and respiratory weakness Thyrotoxic periodic paralysis Polyneuropathy Ocular myopathy Hypoparathyroid Tetanic muscular reaction Pituitary disease Acromegaly: median, Proximal myopathy Porphyria Polyneuropathy (proximal) Ascending polyradiculopathy Pregnancy Optic neuritis Cranial nerves: Bell’s palsy Median neuropathy Lumbosacral plexus-labor Lumbosacral plexus: fetal head, forceps Mononeuropathies: Lateral femoral cutaneous nerve Obturator nerve Saphenous nerve Sciatic nerve Common peroneal nerve Innervation of sphincter muscle of the pelvic floor Myotonia and myotonic dystrophy, weakness may worsen (uterus contraction, labor) MG (relapse and remission) Arthrogryposis Polyneuropathy-malnutrition-developing countries GBS Relapse of CIDP Psoriasis Psoriatic myopathy Pulmonary disease Asthma: Churg-Strauss syndrome COPD: polyneuropathy Renal disorders Polyneuropathy: Distal symmetric, sensory, motor Cramps, myokymia Restless leg syndrome Compressive neuropathies: Ischemic myopathy related to shunt 465

Amyoloid deposition Multiplex mononeuropathies Neuromuscular junction: Aminoglycoside toxicity Myopathy: (type 2 fiber atrophy) Cachexia, inanition, electrolyte disturbances, rhabdomyolysis

Ethanol intoxication Rhabdomyolysis Drug induced coma General anesthesia Heroin Multiple organ failure Narcotics Secondary entrapment – compartment syndromes

Raynaud’s syndrome Rheumatoid and Polyneuropathy: connective tissue Systemic lupus erythematosus Scleroderma (rare) Eosinophilia myalgia syndrome Mixed connective tissue disease (“Sharp syndrome“) Rheumatoid arthritis Sjögren’s syndrome with sensory ganglionopathy Relapsing polychondritis Trigeminal neuropathy Muscle: Dermatomyositis Polymyositis RA, scleroderma, penicillamine induced Eosinophilic myositis/fasciitis Eosinophilia myalgia syndrome Bechterew: cauda equina syndrome, thoracal radiculopathies Giant cell arteritis: cranial neuropathies, optic nerve, infarction of tongue, claudication when chewing Polymyalgia rheumatica: muscle pain Wegener‘s disesease: cranial neuropathies, neuropathy, vasculitis Osteopetrosis: , optic nerve, atrophy, optomotor, trigeminal nerve, facial nerve, otosclerosis Paget‘s disease: anosmia, optic nerve, trigeminal, deafness, caudal and cranial nerves Therapy induced: Gold therapy: polyneuropathy, myokymia D penicillamine: MG, myositis : myopathy Chloroquine: myopathy Facial nerve (bilateral) Neurosarcoidosis Hypercalcemia 466

Myositis: proximal muscle atrophy Polyneuropathy (distal sensorimotor, small fiber and autonomic) Mononeuropathy Radiculopathy GBS Sepsis Cachexia Critical care myopathy Critical illness neuropathy Malnutrition and avitaminosis Neuromuscular transmission disorders by: Anesthetic drugs, aminoglycosides Septic myopathy Thick filament myopathy Therapy induced: steroid myopathy Skin changes Angiokeratoma: Fabry’s disease Cheilosis/glossitis: vitamin B and folate deficiency Dupytren’s : alcoholic liver disease, diabetes mellitus Hair loss: thallium, alopecia areata (in autoimmune disease, also in MG), , thallium, Lupus Erythema nodosum: leprosy, sarcoidosis, inflammatory bowel disease : POEMS syndrome, adrenomyeloneuropathy, adreno- Hypopigmentation: POEMS syndrome, leprosy (patchy) : POEMS syndrome Skin rash: dermatomyositis Purpura: vasculitis, cryoglobulinemia, amyloidosis : Refsum’s disease Macroglossia: amyloidosis Mees’ lines (nails): arsenic, thallium intoxication Photosensitivity: Lupus, porphyria Raynaud’s syndrome Collagenosis, autoimmune disease Vitiligo: vitamin B deficiency Starvation Anorexia nervosa Myopathy Strachan’s syndrome Wernicke’s disease

Steroid medication Chronic myopathy, type two fiber atrophy Acute myopathy in status asthmaticus Critical illness myopathy Subarachnoid hemorrhage Epsilon aminocaproic acid-myopathy Thyroid disease Hyperthyroidism Basedow’s disease 467

Entrapment mononeuropathy (CTS) Graves ophthalmopathy Hyperthryroid periodic paralysis (Asian, Chinese) MG and hyperthyrosis Thyroid myopathy Hypothyroidism Median neuropathy Myopathy (pseudomyotonia – Hoffman‘s sign) Polyneuropathy

Polyneuropathies: Toxine exposure/ Acrylamide (monomer): sensory working conditions Heavy metals: Lead: motor neuropathy (UE > LE) Wrist and finger extensors Arsenic: distal axonopathy (GBS-like) Mercury: Cranial nerves II, VIII, sensory Thallium: Polyneuropathy, autonomic Tin: Organic solvents (n-hexane, methyl n-butyl ketone, carbon disulfide) Organophosphates: Acetylcholinesterase inhibition: fasciculations, weakness, respiration Nicotinic effects: inhibition of neuropathy target esterase: Distal axonopathy (TOCP) triorthocresyl phosphate gasoline Trichlorethylene: cranial neuropathies

Optic neuropathy Uremia Mononeuropathies Polyneuropathy Shunt monomelic neuropathies

Color vision changes: sulfonamides, streptomycin, methaqualone, barbiturates, Visual disorders digitalis, thiazide diuretics, antihelmintic drugs, nalidixic acid, troxidone Optic neuropathy: chloramphenicol, isoniazid, streptomycin, ethambutol, sul- fas, dapsone, chlorpropamide, chlorambucil, penicillamine, indomethacin, ibuprofen, morphine, MAO-inhibitors, barbiturates

Vitamin B1 (Thiamine): polyneuropathy, myopathy Vitamin deficiency Vitamin B6: isoniazid neuropathy, median neuropathy Pyridoxine high dose: sensory neuropathy Vitamin B12 deficiency: polyneuropathy, posterior column degeneration Vitamin D: muscle weakness, osteomalacia Vitamin E: myopathy, lordosis 469

Subject index 471

A wave 19 Calcaneal nerve 241 Abducens nerve 53 Calpain-3 389 Accessory deep peroneal nerve 228 Campylobacter jejuni 288 Accessory nerve 74 Cancer associated LEMS 349 Acid maltase deficiency (GSD II) 414 Carbon disulfide neuropathy 305 Acoustic nerve 62 Carboplatin 317 Acromegaly 426 Carcinoma associated myopathy 425 Acrylamide neuropathy 304 Carcinomatous myopathy 426 Activity at rest 20 Carnitine palmitoyl transferase 2 deficiency (CPT2) 417 Acute brachial neuritis 97 Carpal tunnel syndrome (CTS) 158 Acute central disc protrusion 138 Cauda equina 137 Acute inflammatory demyelinating polyneuropathy 290 Caveolin-3 389 Acute motor and sensory axonal neuropathy (AMSAN) 289 Cavernous sinus 40 Acute motor axonal neuropathy (AMAN) 288 Cavernous sinus lesions 51 AIDP 290 Central core disease (CCD) 404 Alcohol polyneuropathy 308 Centronuclear myopathy (CNM) 404 Alpha-sarcoglycan 389 Cephalic tetanus 355 AMAN 288 Cervical plexus 89 Amiodarone neuropathy 310 Cervical radiculopathy 119, 122 AMSAN 288 Cervical spinal nerves 89 Amyloidosis 269 Cervical spondylosis 123 Amyotrophic lateral sclerosis 441 Charcot-Marie-Tooth disease type 1, CMT-1 324 Andersen’s syndrome 434 Charcot-Marie-Tooth disease type 2, CMT-2 327 Anosmia 34 Chemotherapy and neuropathy 315 Anterior interosseus syndrome 158 Chloramphenicol neuropathy 311 Anterior 236 Chronic external ophthalmoplegia syndrome (CPEO) 410 Anti-Hu 276 Chronic inflammatory demyelinating polyneuropathy 292 Anti-MAG antibodies 267 Chronic Neuralgic Amyotrophy (HNA2) 99 Anti-striatal antibodies 338 CMT-3 333 Anti-titin antibodies 338 CMT-4 333 negative myasthenia 341 Cobalamin neuropathy 297 Arsenic neuropathy 320 Cocaine-induced myopathy 420, 422 Autonomic findings 16 Colchicine myopathy 421 Autonomic testing 22 Colchicine neuropathy 312 Autosomal recessive with ophthalmople- Coma 81 gia 410 Coma, cranial nerve examination 81 Axillary nerve 147 Combined cranial nerve palsies 84 Azathioprine 343 Congenital fiber type disproportion 404 Congenital myopathies 403 Bacterial and parasitic neuropathies 284 Connective tissue diseases and myophathies 372 Bannwarth’s syndrome 284 Contracture 60 Becker muscular dystrophy (BMD) 383 Corticosteroid atrophy 426 Bell’s palsy 58 Corynebacterium diphtheriae (Diphtheria) 285 Beriberi 302 Cranial nerves 81 Beta-sarcoglycan 389 CRDs 20 Bethlem myopathy 389, 404 Critical illness myopathy 423 Bilateral facial paralysis 60 CSF studies 24 BMRC scale 10 Cushing syndrome 426 Borrelia Burgdorferi 284 Cutaneous femoris lateral nerve 219 Botulism 352 Cutaneous femoris posterior nerve 221 Brachial plexopathy: metastasis 101 Cyclophosphamide 344 Brachial Plexus 91 Cyclosporin A 343 Brancher deficiency (GSD IV) 414 Bruns Garland Syndrome 110 Dapsone neuropathy 313 Bulbospinal muscular atrophy 451 Debrancher deficiency (GSD III) 414 “Burner” syndrome 101 Deep peroneal lesions 228 Defects of fatty acid metabolism 417 C5 122 Delta-sarcoglycan 389 C6 122 Demyelinating neuropathy associated with anti-MAG 295 C7 122 Dermatomyositis 365 C8 122 Diabetes 426 472

Diabetic amyotrophy 110, 258 Hereditary Sensory Neuropathy (HSN) 333 Diabetic autonomic neuropathy 256 Herpes 128 Diabetic distal symmetric polyneuropathy 253 Herpes neuropathy 281 Diabetic mononeuritis multiplex 258 Hexacarbon neuropathy 306 Diabetic polyradiculopathy (amyotrophy) 258 HNPP 99, 329 Diabetic truncal neuropathy 128 Horner’s 82 Digital nerves of the hand 173 immunodeficiency virus-1 neuropathy 278 Disc protrusions 131 Hyperkalemic periodic paralysis 433 Distal desmin body myofibrillar myopathy 401 Hyperparathyroidism 426 Distal myopathy 400 Hyperthyroidism 426 Distal posterior interosseus nerve syndrome 171 Hypoglossal nerve 77 Disulfiram neuropathy 314 Hypokalemic periodic paralysis 436 Dorsal scapular nerve 180 Hypoparathyroidism 426 D-penicillamine 421 Hypothyroidism 425 Drug-induced myasthenic syndromes 346 Drugs related neuropathies 308 Iliohypogastric nerve 197 Duchenne muscular dystrophy (DMD) 380 Ilioinguinal nerve 199 Dysferlin 389 Inclusion body myositis (IBM) 368 Industrial agents neuropathies 304 (EMG) 20 Infections of muscle 375 Electrophysiology and muscle disease 359 Inferior gluteal nerve 202 Endocrine myopathy 425 Inflammatory neuropathy 288 Eosinophilic myositis 421 Insertional activity 20 Episodic weakness of lumbosacral plexus 114 Intercostal nerves 194 Intercostal neuralgia 128 F wave 19 Intercostobrachial nerve 196 Facial myokymia 60 Interdigital neuroma and neuritis 239 Facial nerve 56 Ischemic plexopathy 111 Familial ALS (FALS) 442 Fasciculations 11, 20 Kearns-Sayre syndrome 410 Fascioscapulohumeral muscular dystrophy 396 Kennedy’s syndrome 451 Femoral nerve 213 Fibrolipoma 243 Lamin A/C 389 Fingerprint body myopathy 404 Late responses 18 FKRP 389 Lateral cord 94 Focal myositis 370 LEMS (Lambert Eaton myasthenic syndrome) 349 Fungal myositis 377 Lesser occipital nerve 89, 90 Gamma-sarcoglycan 389 Limb girdle muscular dystrophy 388 General disease finder 453 Localized hypertrophic mononeuropathy 244 Generalized myasthenia gravis 344 Localized tetanus 354 Generalized tetanus 354 186 Genetic testing 26 Lumbar radiculopathy 129 Genitofemoral nerve 201 Lumbar stenosis 134 Glossodynia 79 Lumbosacral plexus 106 Glossopharyngeal nerve 67 Lyme disease 284 Glossopharyngeal neuralgia 69 Glycogen storage diseases 413 Magnetic stimulation techniques 19 Gowers-Laing distal myopathy 401 Malignant psoas syndrome 112 Greater auricular nerve 89 Markesbery (type 2) distal myopathy 401 Greater occipital nerve 89 Martin Gruber anastomosis 158 Guillain-Barre syndrome 290 Maternal paralysis 114 McArdle’s disease (GSD V) 414 H reflex 19 Medial cord 94 Hemifacial spasm 60 Medial plantar proper digital nerve (Joplin’s neuroma) 242 Hepatitis B neuropathy 282 Median nerve 154 Hereditary motor and sensory neuropathy type 1 324 Mercury neuropathy 322 Hereditary motor and sensory neuropathy type 2 327 425 Hereditary neuropathies 324 MFS 296 Hereditary neuropathies rare types 333 MGUS 267 Hereditary neuropathy with liability to pressure palsies Miller-Fisher syndrome 296 (HNPP) 99, 329 Minicore disease 404 473

Mitochondrial myopathies 409 Neuromuscular transmission disorders 335 Mitochondrial myopathy and cardiomyopathy 410 Neuromyotonia 11 Mitochondrial trifunctional protein deficiency 417 Neuropathic pain 16 Monoclonal gammopathy of undetermined significance Neuropathic tremor 12 (MGUS) 267 Neuropathy and porphyria 331 Mononeuropathies 141 Nonaka distal myopathy 401 Mononeuropathies: trunk 175 Notalgia paresthetica 128 Mononeuropathies: upper extremities 145 Nutritional neuropathies 297 Morton’s 242 Motor function 10 Obturator nerve 211 Motor NCV studies 17 Occipital neuralgia 90 Motor disease 439 Ocular MG 344 disease syndrome 276 Oculomotor nerve 39 Motor neuropathy 276 Oculopharyngeal muscular dystrophy (OPMD) 393 Motor scales 30 Olfactory nerve 33 Moving toes 12 Optic nerve 35 Multiple cranial nerve palsies 84 Organophosphate neuropathy 307 and neuropathy 266 Osteosclerotic myeloma 268 Muscle and myotonic diseases 357 Oxaliplatin 317 Muscle biopsy 29 Muscle cramps 12 Muscle histology 360 P/Q Ca++ channels 349 Muscle/nerve/skin biopsy 28 Paramyotonia congenita 431 Musculocutaneous nerve 151 Paraneoplastic neuropathy 273 Myalgia 16 Paraproteinemic neuropathies 266 Myasthenia gravis 337 Parasitic myositis 377 Myasthenic crisis 344 Parosmia 34 Myasthenic syndromes 340 Pectoral nerve 191 Mycobacterium leprae (Leprosy) 285 Percussion myotonia 11 Mycobacterium tuberculosis 287 Peripheral nerve involvement in cancer patients 244 Mycophenolate mofetil 344 Peripheral nerve tumors 243 Myoclonic epilepsy and ragged-red fibers (MERRF) 410 Peroneal nerve 226 Myoedema 11 Phrenic nerve 177 Myokymia 11, 21 Plantar Nerves (medial and lateral) 241 Myoneurogastrointestinal encephalopathy (MNGIE) 410 Plasma exchange 343 Myotilin 389 Platinum-compound neuropathy 317 Myotonia 11 Plexopathies 87 Myotonia congenita 428 POEMS syndrome 268 Myotonia congenita (Becker) 429 Poliomyelitis 447 Myotonia congenita (Thomsen) 429 Polymyositis (PM) 362 Myotonic discharges 20 Polyneuropathies 247 Myotonic dystrophy 385 Polyneuropathy and chemotherapy 315 Porphyria 331 Necrotic myopathies 420 Post-gastroplasty neuropathy 299 Necrotizing alcoholic myopathy 421 Post-polio syndrome 449 Nemalin myopathy 404 Posterior cord 94 Neonatal brachial plexopathy 101 Posterior cutaneous nerve of arm and forearm 171 Neonatal tetanus 355 Posterior interosseus nerve 170 Neoplastic involvement of the brachial plexus 99 Postoperative lumbosacral plexopathy 112 Neoplastic Neuropathy 271 Primary Lateral Sclerosis 442 Nerve biopsy 28 PROMM 386 Nerves of the foot 241 158 Nervus auricularis magnus 90 Proximal Lower Motor Neuron Syndrome 102 Neuralgia of the laryngeal nerve 72 Pseudoathetosis 12 Neuralgic amyotrophy 97 Pseudopupillary sparing 40 Neuralgic Amyotrophy (HNA1) 99 Pseudoradicular 134 Neuroepithelioma 243 Pudendal nerve 204 Neurofibroma 243 Pupil 82 Neurofibrosarcoma 243 Pyomyositis 377 Neuroimaging techniques 27 Pyridostigmine 342 Neuromuscular Transmission and Drugs 346 Pyridoxine neuropathy 300 474

Radial nerve 168 Thallium neuropathy 323 171 Thiamine neuropathy 302 Radiation brachial plexopathy 99 Thoracic outlet syndromes (TOS) 104 Radiculitis 24 Thoracic radiculopathy 126 Radiculomyeloneuropathy 123 Thoracic spinal nerves 192 Radiculopathies 117 Thoracodorsal nerve 189 Recurrent laryngeal neuropathies 72 230 Reflex testing 12 Tick paralysis 286 Renal disease neuropathy 260 Tinnitus 63 Repetitive nerve 19 Tissue diagnosis 28 Repetitive nerve stimulation (RNS) 341 Tocopherol neuropathy 303 Riley-Day syndrome (familial dysautonomia) 333 TOS 104 Rippling muscle 11 Toxic myopathies 420 Root avulsion 96 Toxins affecting the neuromuscular transmission 348 Transversus colli nerve 89 Sacral radiculopathy 129 Treponema pallidum (syphilis) 286 Saphenous nerve 217 Tri-ortho-cresyl phosphate 307 Saturday night palsy 170 Trigeminal nerve 46 Schwannoma 243 51 Sciatic nerve 222 TRIM32 389 Sensory disturbances 14 Trochlear nerve 43 Sensory NCV studies 18 Trypanosoma cruzi (Chagas’ disease) 286 Single Fiber EMG 341 Skin biopsy 29 Ulnar nerve 162 SMA1 (Werdnig-Hoffmann disease) 445 Uremia and myopathy 426 SMA2 (late infantile SMA) 445 SMA3 (Kugelberg-Welander disease) 445 V1, the ophthalmic nerve 49 SMAs 445 V2, the maxillary nerve 49 Smell disorders 33 V3, the mandibular nerve 49 Spinal muscular atrophies 444 V3, the mandibular nerve 49 Spondylolisthesis 134 Vacuolar myopathy 421 Spontaneous activity 20 Vagus nerve 70 Spurling 120 Vasculitic neuropathy 262, 265 Steroid myopathy 420 Very-long chain acyl-CoA dehydrogenase deficiency 417 Strachan’s Syndrome 301 Vestibular nerve 64 Subscapular nerve 184 Vinca alkaloids neuropathy 316 Superficial peroneal nerve lesions 228 Viral myositis 376 Superficial 171 Vitamin B12 deficiency 297 Superior gluteal nerve 202 Vitamin E 303 Supinator syndrome 171 Voltage-gated calcium channels 349 Supraclavicular nerve 89 Voluntary activity 20 Suprascapular nerve 182 Von Gierke disease (GSD I) 414 Sural nerve 237 Warm and dry foot syndrome 112 Tarsal tunnel syndrome 233 Welander (type 1) distal myopathy 400 Tarui’s disease (GSD VII) 414 Wolfram syndrome (DIDMOAD) 410 Taxol neuropathy 318 Telethonin 389 X-linked CMT 333 171 Tetanus 354 Zidovudine (AZT) 421