NUTRICIA PRODUCT REFERENCE GUIDE Updated As of September, 2017

NUTRICIA PRODUCT REFERENCE GUIDE Updated as of September, 2017

FOR CLINICIANS Nutricia Contacts How to Contact Nutricia • Nutricia is a Global Health Company My Nutricia sales representative(s): Nutricia’s Customer Service: • Nutricia Leads the Development and Use of Advanced Medical Nutrition • Phone: (800) 365-7354 for Specialized Care Name:...... • Fax: (301) 795-2301 • Nutricia Products and Services Transform the Daily Lives of Millions of • Email: [email protected] Phone:...... Infants, Children, Adults and Aging Seniors • Live Chat: www.Neocate.com (M-F 8:30 am – 7 pm ET) Email:...... This guide is a convenient reference for clinicians to the full range of Nutricia’s Nutricia’s Nutrition Services: medical nutritional products. Nutricia strives to develop quality products that • Phone: (800) 365-7354 – Option 2 offer choice and flexibility to today’s patients to enhance diet acceptance. • Email: [email protected] Please note that all of our products require medical supervision. For additional Name:...... • Live Chat: www.Neocate.com (M-F 8:30 am – 5 pm ET) information, please call our Nutrition Services team or visit our web site at www.Nutricia-NA.com. Our staff is comprised of individuals with the highest Phone:...... level of expertise ready to offer support and reliability to our customers. Nutricia Metabolics: We look forward to hearing from you. Email:...... • Phone: (800) 605-0410 • Email: [email protected] Consumers and Patients: Nutricia products are available for convenient home delivery directly from Internet: Nutricia North America. Consumers can call our toll free number or visit one of Name:...... For information on Nutricia products, reimbursement,* our websites. See pages 202-203 for a list of our websites. and other helpful resources, visit www.Nutricia-NA.com. Consumers can also purchase Nutricia products through retail pharmacies. Phone:...... For a complete listing of our websites, see pages 200-201. Pharmacies can special order Nutricia products from their wholesaler or directly from Nutricia North America. Email:...... * For reimbursement information, please see page 195.

© 2017 Nutricia North America. All rights reserved. Nutricia and its brands are registered trademarks. See product labels for more specifics. 2 3 CONTENTS CONTENTS – Alphabetical Index Ordering Information...... 2-3 Complete Amino Acid Mix...... 174 Periflex Advance...... 44 Contents by Product Indications...... 6-8 Complex Essential MSD Drink Mix...... 78 PKU Periflex Early Years...... 40 Complex Junior MSD Drink Mix...... 76 PKU Periflex Junior Plus...... 43 Specialized Pediatrics Section...... 9-38 Complex MSD Amino Acid Blend...... 80 Periflex LQ...... 46 Mixing Instructions...... 24-25 Diff-Stat...... 160 PhenylAde40 Drink Mix...... 54 Household Measurements...... 26 Duocal...... 170 PhenylAde60 Drink Mix...... 56 Volume Prescription...... 27 Essential Amino Acid Mix...... 176 PhenylAde MTE Amino Acid Blend...... 58 Fiber-Stat...... 162 PhenylAde Essential Drink Mix...... 52 Dilution Charts...... 28-36 GA-1 Anamix Early Years...... 92 PhenylAde GMP Drink Mix...... 48 Metabolics Section...... 39-136 GlutarAde Amino Acid Blend...... 98 PhenylAde GMP Mix-In...... 50 Household Measurements: Metabolics...... 124-125 GlutarAde Essential GA-1 Drink Mix...... 96 PhenylAde PheBLOC LNAA...... 60 GlutarAde Junior GA-1 Drink Mix...... 94 Phlexy-10 Tablets...... 70 Mixing Instructions: Metabolics...... 126-136 HCU Anamix Early Years...... 100 Phlexy-10 Drink Mix...... 72 Low Protein Foods Section...... 137-138 HCU Anamix Next...... 102 Phlexy-Vits...... 178 Neurology Section...... 139-148 HCU Lophlex LQ...... 106 PKU Lophlex LQ...... 66 Mixing Instructions: KetoCal...... 146 IVA Anamix Early Years...... 86 PKU Lophlex Powder...... 68 IVA Anamix Next...... 88 Polycal...... 172 Specialized Adult Nutrition Section...... 149-164 KetoCal 3:1 Powder...... 140 Pro-Stat MAX...... 154 Other Medical Nutritionals Section...... 165-182 KetoCal 4:1 LQ - Vanilla and Unflavored...... 144 Pro-Stat Renal Care...... 156 Resources...... 183-202 KetoCal 4:1 Powder...... 142 Pro-Stat Sugar Free...... 150 Lanaflex...... 62 Pro-Stat Sugar Free AWC...... 152 Liquigen...... 168 Single Amino Acids...... 180 Low Protein Foods...... 138 SOD Anamix Early Years...... 122 MMA/PA Early Years...... 108 TYR Anamix Early Years...... 114 MMA/PA Anamix Next...... 110 TYR Anamix Next...... 116 Monogen...... 166 TYR Lophlex LQ...... 118 MSUD Anamix Early Years ...... 74 UCD Anamix Junior...... 120 Specialized Pediatrics Metabolics Low Protein Foods Neurology Specialized Adult Nutrition Other Nutritionals MSUD Lophlex LQ...... 84 UTI-Stat...... 158 MSUD Maxamum...... 82 XLeu Maxamum...... 90 page 9-38 page 39-136 page 137-138 page 139-148 page 149-164 page 165-182 Neocate Infant DHA/ARA...... 12 XMet Maxamum...... 104 Neocate Junior...... 16 XMet, XCys Maxamaid...... 123 Neocate Junior with Prebiotics...... 18 XMTVI Maxamum...... 112 Neocate Nutra...... 14 XPhe Maxamum...... 64 Neocate Splash...... 20 4 Neocate Syneo Infant...... 10 5 CONTENTS – By Indication and Diet Need*

Allergy, Cow and Soy Milk/Multiple Food Allergies Food Protein-Induced Enterocolitis Syndrome (FPIES) Inborn Errors of Metabolism Malabsorption Neocate Infant DHA/ARA...... 12 Neocate Infant DHA/ARA...... 12 Nutricia Metabolic Formulas...... 40-123 Duocal...... 170 Neocate Nutra...... 14 Neocate Junior...... 16 Low Protein Foods...... 138 Neocate Infant DHA/ARA...... 12 Neocate Junior...... 16 Neocate Junior with Prebiotics...... 18 Liquigen...... 168 Neocate Nutra...... 14 Neocate Junior with Prebiotics...... 18 Neocate Splash...... 20-23 Monogen...... 166 Neocate Junior...... 16 Neocate Splash...... 20-23 Neocate Syneo Infant...... 10 Duocal...... 170 Neocate Junior with Prebiotics...... 18 Neocate Syneo Infant...... 10 Gastrointestinal Health Polycal...... 172 Neocate Splash...... 20-23 Complete Amino Acid Mix...... 174 Fiber-Stat...... 162 Complete Amino Acid Mix...... 174 Liquigen...... 168 Amino Acid-Based Products Diff-Stat...... 160 Essential Amino Acid Mix...... 176 Complete Amino Acid Mix...... 174 Phlexy-Vits...... 178 Neocate Infant DHA/ARA...... 12 Gastroesophageal Reflux (GER) Maple Syrup Urine Disease Neocate Nutra...... 14 Single Amino Acids...... 180 Complex Junior MSD Drink Mix...... 76 Neocate Infant DHA/ARA...... 12 Isovaleric Acidemia Neocate Junior...... 16 Neocate Nutra...... 14 Complex Essential MSD Drink Mix...... 78 Neocate Junior with Prebiotics...... 18 Neocate Junior...... 16 IVA Anamix Early Years...... 86 Complex MSD Amino Acid Blend...... 80 Neocate Splash...... 20-23 Neocate Junior with Prebiotics...... 18 IVA Anamix Next...... 88 MSUD Anamix Early Years...... 74 Neocate Syneo Infant...... 10 Neocate Splash...... 20-23 XLeu Maxamum...... 90 MSUD Maxamum...... 82 Nutricia Metabolic Formulas...... 40-123 Neocate Syneo Infant...... 10 Ketogenic Diet MSUD Lophlex LQ...... 84 Complete Amino Acid Mix...... 174 Glutaric Acidemia Type I KetoCal 3:1 Powder...... 1 4 0 Modular Diets Essential Amino Acid Mix...... 176 KetoCal 4:1 LQ - Vanilla and Unflavored...... 144 Duocal...... 170 Single Amino Acids...... 180 GlutarAde Junior GA-1 Drink Mix...... 94 GlutarAde Essential GA-1 Drink Mix...... 96 KetoCal 4:1 Powder...... 142 Liquigen...... 168 Chylothorax GlutarAde Amino Acid Blend...... 98 Liquigen...... 168 Polycal...... 172 Liquigen...... 170 GA-1 Anamix Early Years...... 92 Long Chain Fatty Acid Oxidation Disorders Complete Amino Acid Mix...... 174 Monogen...... 168 Liquigen...... 168 Essential Amino Acid Mix...... 176 Homocystinuria/Hypermethioninemia Phlexy-Vits...... 178 Critical Illness Requiring Increased Protein HCU Anamix Early Years...... 100 Monogen...... 166 Pro-Stat MAX...... 154 HCU Anamix Next...... 102 Low Protein Diets Dialysis XMet Maxamum...... 104 Low Protein Foods...... 138 Pro-Stat Renal Care...... 156 HCU Lophlex LQ...... 106 Duocal...... 172 Eosinophilic Esophagitis (EoE) Low Serum Protein Levels Neocate Infant DHA/ARA...... 12 Pro-Stat MAX...... 154 Neocate Nutra...... 14 Pro-Stat Sugar Free AWC...... 152 Neocate Junior...... 16 Pro-Stat Sugar Free...... 150 Neocate Junior with Prebiotics...... 18 Pro-Stat Renal Care...... 156 Neocate Splash...... 20-23 Neocate Syneo Infant...... 10 Complete Amino Acid Mix...... 174

*Not a complete listing 6 7 Phenylketonuria Short Bowel Syndrome PKU Periflex Early Years...... 40 Liquigen...... 170 PKU Periflex Junior Plus...... 42 Neocate Infant DHA/ARA...... 12 Periflex LQ...... 46 Neocate Nutra...... 14 Periflex Advance...... 44 Neocate Junior...... 16 PhenylAde40 Drink Mix...... 54 Neocate Junior with Prebiotics...... 18 PhenylAde60 Drink Mix...... 56 Neocate Splash...... 20-23 PhenylAde MTE Amino Acid Blend...... 58 Complete Amino Acid Mix...... 176 PhenylAde Essential Drink Mix...... 52 Sulphite Oxidase Deficiency PhenylAde GMP Drink Mix...... 48 SOD Anamix Early Years...... 122 PhenylAde GMP Mix-In...... 50 XMet, XCys Maxamaid...... 123 PhenylAde PheBLOC LNAA...... 60 XPhe Maxamum Powder...... 64 Tyrosinemia PKU Lophlex LQ...... 66 TYR Anamix Early Years...... 114 PKU Lophlex Powder...... 68 TYR Anamix Next...... 116 Phlexy-10 Tablets...... 70 TYR Lophlex LQ...... 118 Phlexy-10 Drink Mix...... 72 Unintentional Muscle Loss Lanaflex...... 62 Pro-Stat MAX...... 154 Propionic/Methylmalonic Acidemia Pro-Stat Sugar Free...... 150 MMA/PA Early Years...... 108 Pro-Stat Sugar Free AWC...... 152 MMA/PA Anamix Next...... 110 Pro-Stat Renal Care...... 156 XMTVI Maxamum...... 112 Urea Cycle Disorders Protein-Energy Malnutrition (PEM) UCD Anamix Junior...... 120 Pro-Stat MAX...... 154 Essential Amino Acid Mix...... 178 Pro-Stat Sugar Free AWC...... 152 Urinary Tract Health Pro-Stat Sugar Free...... 150 UTI-Stat...... 158 Pro-Stat Renal Care...... 156 Wound/Pressure Injury Management Renal Failure Pro-Stat MAX...... 154 Low Protein Foods...... 138 Pro-Stat Sugar Free AWC...... 152 Duocal...... 172 Pro-Stat Sugar Free...... 150 Polycal...... 174 Pro-Stat Renal Care...... 156

8 SPECIALIZED PEDIATRICS

TM Find more information and resources on these and all of our products at www.NutriciaLearningCenter.com 9 10 SPECIALIZED PEDIATRICS • • • Fat • • • • • • • • Main Features: * 2014;75:343-51. 3. Michaelis, etal. Allergy. 2016;71(S102):58(114). Pediatr1. Burks,etal. AllergyImmunol.2015;26:316-22. 2.Harvey, etal.Pediatr Res. For product sampleinformation,pleaseseepage37.

Halal Hypoallergenic short- and long-chain fructooligosaccharides ** short- and long-chain fructooligosaccharides • • Displacement 0.71mL/g Potential RenalSoluteLoad**: 176 mOsm/L Energy distribution: Free water**:90.0% Osmolality**: 360mOsm/kg Prebiotic blendofscFOSandlcFOS* Probiotic Backed by 3clinicaltrials,clinicallyshownto: Carbohydrate Protein

Help balancethegutmicrobiotaof Support growthanddevelopment Effectively resolve foodallergysymptoms food-allergic infants (MCT33%/LCT 67%) Bifidobacterium breve

iron andnucleotides. prebiotics andprobioticsspecificallydesignedforfood-allergicinfants,containing exemptA nutritionallycomplete,powderedaminoacid-based infantformulawith Neocate 43.5% 45.1% 11.4% 3 M-16V Atstandard concentration, 20kcal/fl oz ® 1,2 Syneo

1 111436 Code Product Ordering/Reimbursement Information: office todetermine availability. WIC For guidanceonmonitoringmicronutrients, pleasesee page38. please seepages24-36. For detailson • • • • • • Indications:

™ Related GIandallergicconditions: Multiple foodallergies Cow milkallergy ‡

: Infant

Contact your stateWIC Gastroesophageal reflux Eosinophilic esophagitis(EoE) Food protein-inducedenterocolitis syndrome(FPIES) 49735-0114-36 Reimbursement scoop size,householdmeasures, directed by ahealthcare professional. venous catheterorpost-pyloric feedingtubeunless Not recommended foruseininfantswith a central B4161 Code Packaging HCPCS

information seepage 195. information For morereimbursement 4 x400g(14.1oz) Product andadministration, 1900 Calories Per Can

Nutrition Information: Inositol, mg Choline, mg Vitamin C,mg Biotin, mcg Pantothenic Acid,mcg Folic Acid,mcg Niacin, mcg Vitamin B Vitamin B Riboflavin, mcg Thiamin, mcg Vitamin K,mcg Vitamin E,IU(mg Vitamin D Vitamin A,IU(mcgRE) Vitamins SolubleFiber, g Carbohydrate, g ARA,mg DHA,mg LinoleicAcid,mg Fat, g Protein Equivalent,g Calories Nutrients a -Linolenic Acid,mg

12 6 3

, mcg , IU(mcg) , mcg a -TE) 352(8.8) Per 100g 1352(406) 2900 4900 3348 396 108 540 690 475 100 540 95.4 51.6 19.0 64.0 42.5 53.5 77.0 77.0 23.0 13.5 6.5 (4.4) 4.5 1.3 Per 100kcal 285(85.5) 1032 114 145 611 705 114 83.4 22.7 20.1 10.9 13.5 11.3 16.2 16.2 74.1 (1.9) 1.4 (0.93) 4.0 9.0 0.95 4.8 2.8 0.27 Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mcg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals

Per 100g 378 515 185 400 190 388 549 14.2 10.4 11.0 98.0 50.0 5.2 7.1 Per 100kcal 108 116 79.6 38.9 20.6 84.2 40.0 10.5 81.7 3.0 2.2 2.3 1.1 1.5 ** ASourceofDocosahexaenoic Acid(DHA) * ASourceofArachidonic Acid(ARA) Cyanocobalamin. Sodium Molybdate,D-Biotin, VitaminD Chloride, Phylloquinone, SodiumSelenite, Tocopherols, Folic Acid,Chromium Tocopherol, Potassium Iodide,Mixed Riboflavin, VitaminAAcetate,DL-alpha Pyridoxine Hydrochloride, CupricSulfate, Sulfate, ThiaminChlorideHydrochloride, M-16V, Ascorbyl Palmitate, Manganese Tocopheryl Acetate, 5’-Monophosphate DisodiumSalt,DL-alpha Calcium D-Pantothenate, Guanosine Salt, Adenosine5’-Monophosphate, Inosine 5’-Monophosphate Disodium Cytidine 5’-Monophosphate, Niacinamide, 5’-Monophosphate DisodiumSalt, Sulfate, ZincL-Carnitine, Uridine L-Ascorbic Acid,Taurine, Ferrous M. alpina Tricalcium Citrate, MagnesiumL-Aspartate, Chloride, CholineBitartrate, L-Methionine, L-Cystine, L-Tryptophan, Magnesium L-Histidine, L-Alanine, SodiumChloride, L-Phenylalanine, L-Tyrosine, L-Serine, Glycine, L-Isoleucine, L-Threonine, L-Proline, L-Valine, CAEM(anemulsifier), Tripotassium Citrate, L-Glutamine, Dibasic, L-Leucine, L-Lysine Acetate, L-Aspartate, CalciumPhosphate 2% ofeachthefollowing:L-Arginine (4%) AndInulin(0.5%),andlessthan Fructooligosaccharides (Oligofructose Sunflower Oil(4%),Canola(4%)), (8%), HighOleicSunflowerOil(5%), Vegetable Oil(MediumChainTriglycerides Corn SyrupSolids(51%),Refined Ingredients: Oil*, C. cohnii Bifidobacterium breve Oil**, M-Inositol, 3 ,

11 Neocate Syneo Infant Syneo Neocate 12 SPECIALIZED PEDIATRICS • • • • • • • • • • Main Features: please seepage 37. For productsample information, Hypoallergenic 168 mOsm/L Fat Carbohydrate Protein 340 mOsm/kg support Neocate DHA andARAat1:1ratio 4.8 mgper100kcals Displacement Halal &Kosher Pareve Potential RenalSoluteLoad: Energy distribution: Free water (at0.67kcal/mL): 90.3% Osmolality (at0.67kcal/mL): Over 100publications andcounting DHA at0.35%fattyacids Nucleotides, presentinhumanmilk (MCT 33%/LCT 67%)

containing ironandnucleotides. exemptA nutritionallycomplete,powderedaminoacid-based infantformula Neocate 45.7% 43.1% 11.2% 0.70 mL/g

® InfantDHA/ARA For guidanceonmonitoringmicronutrients, pleasesee page38. please seepages24-36. For detailson • • • Indications:

12595 Code Product Ordering/Reimbursement Information: Related GIandallergicconditions: Multiple foodallergies Cow milkallergy office todetermine availability. WIC • • • • • Gastroesophageal reflux Malabsorption Eosinophilic esophagitis(EoE) Food protein-inducedenterocolitis syndrome(FPIES) Short bowelsyndrome(SBS) ‡ :

Contact your stateWIC

49735-0125-95 Reimbursement scoop size,householdmeasures, B4161 Code Packaging HCPCS

information see page195. information For morereimbursement 4 x400g(14.1oz) Product andadministration, 1932 Per Calories Can

2900 4900 3565 419 108 540 690 483 100 540 95.4 51.6 19.0 64.0 42.5 52.0 81.6 81.6 24.5 13.5 1.3 6.8 (4.6) Per 100kcal 280(84.1) 1014 110 140 600 738 112 86.8 22.4 19.8 10.7 13.3 10.8 16.9 16.9 3.9 8.8 5.1 2.8 0.27 1.4 (0.94) Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mcg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals Per 100g 386 525 189 100 410 200 397 561 14.5 10.6 11.3 51.0 5.3 7.3 Per 100kcal 109 116 79.9 39.1 20.7 84.9 41.4 10.6 82.2 3 2.2 2.3 1.1 1.5 ** ASource ofDocosahexaenoic Acid(DHA) * ASourceofArachidonic Acid(ARA) D-Biotin, Vitamin D Sodium Selenite, Molybdate, Acid, ChromiumChloride, Phylloquinone, Potassium Iodide, Mixed Tocopherols, Folic Vitamin AAcetate,DL-alpha Tocopherol, Hydrochloride, CupricSulfate, Riboflavin, Chloride Hydrochloride, Pyridoxine Palmitate, ManganeseSulfate,Thiamin DL-alpha Tocopheryl Acetate,Ascorbyl 5’-Monophosphate DisodiumSalt, Calcium D-Pantothenate, Guanosine Salt, Adenosine5’-Monophosphate, Inosine 5’-Monophosphate Disodium Cytidine 5’-Monophosphate, Niacinamide, 5’-Monophosphate DisodiumSalt, Zinc Sulfate,L-Carnitine, Uridine Acid, Taurine, Ferrous Sulfate, C. Cohnii Magnesium L-Aspartate, L-Methionine, Tricalcium Citrate, L-Tryptophan, CholineBitartrate, Chloride, L-Cystine, MagnesiumChloride, L-Serine, L-Histidine, L-Alanine, Sodium L-Threonine, L-Phenylalanine, L-Tyrosine, emulsifier), L-Valine, Glycine, L-Isoleucine, L-Glutamine, L-Proline, CAEM(an Tripotassium Citrate, L-Lysine Acetate, L-Arginine L-Aspartate, L-Leucine, less than2%ofeachthefollowing: Calcium PhosphateDibasic(2%),and Sunflower Oil(5%),Canola(4%)), (8%), HighOleicSunflowerOil(6%), Vegetable Oil(Medium ChainTriglycerides Corn SyrupSolids(54%),Refined Ingredients: Oil**, M-Inositol,L-Ascorbic 3 , Cyanocobalamin. M. Alpina Oil*,

13 ARA / DHA Infant Neocate 14 SPECIALIZED PEDIATRICS • • • • • • • • Main Features: nutrition. Notforbottle ortubefeed. Note: Notsuitable as solesourceof please seepage 37. For productsample information, Fat Carbohydrate Energy distribution: and preservatives Free from artificialflavors, colors Good sourceofvitaminD, zincandiron High incalcium Milk protein-andgluten-free amino acids Made with100%non-allergenic Hypoallergenic Smooth, spoonableconsistency Protein (MCT 4%/LCT 96%)

57% 36% 7% The first and only amino acid-based semi-solid medical foodforchildrenThe firstandonlyaminoacid-basedsemi-solidmedical Neocate and infantsover 6monthsofage.

please seepages24-36. For detailson • • • Indications: 66739 Code Product Ordering/Reimbursement Information: office todetermine availability. WIC Related GIandallergicconditions: Multiple foodallergies Cow milkallergy

® • • • •

Nutra Gastroesophageal reflux Malabsorption Eosinophilic esophagitis(EoE) Short bowelsyndrome(SBS) ‡ :

Contact your stateWIC 49735-016739 Reimbursement scoop size,householdmeasures, B4161 Code Packaging HCPCS

information seepage195. information For morereimbursement 4 x400g(14.1oz) Product andadministration, 1888 Per Calories Can

Nutrition Information: Inositol, mg Choline, mg Vitamin C,mg Biotin, mcg Pantothenic Acid,mcg Folic Acid,mcg Niacin, mcg Vitamin B Vitamin B Riboflavin, mcg Thiamin, mcg Vitamin K,mcg Vitamin E,IU(mg Vitamin D Vitamin A,IU(mcgRE) Vitamins Carbohydrate, g Fat, g Protein Equivalent,g Calories Nutrients Linoleic Acid,mg 12 6 3 , mcg , IU(mcg) , mcg a T.E.) 172(4.3) Per 100g 649(195) 3222 1400 1100 250 250 318 472 175 49.0 45.0 23.0 27.5 18.5 67.4 18.8 Serving 3.4 (2.3) 0.6 9.1 8.2 Per Suggested (37 gPowder) 1192 240(72.2) 518 407 118 63.6(1.6) 92.5 18.1 16.7 10.2 92.5 24.9 1.3 (0.84) 0.22 8.5 3.4 6.8 7.0 3.0

Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mcg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals Per 100g <20 310 310 340 668 44.0 38.0 11.3 10.0 41.4 21.0 Serving 8.8 4.1 5.9 Per Suggested (37 gPowder) <10 115 115 126 247 16.3 14.1 15.3 4.2 3.7 3.3 1.5 2.2 7.8

Cyanocobalamin. Phylloquinone, D-Biotin,VitaminD Sodium Selenite,Molybdate, Chromium Chloride,Folic Acid, Vitamin AAcetate,Potassium Iodide, Pyridoxine Hydrochloride, Riboflavin, Sulfate, ThiaminChlorideHydrochloride, Niacinamide, ManganeseSulfate,Cupric Acetate, CalciumD-Pantothenate, L-Carnitine, DL-Alpha Tocopheryl Ferrous Sulfate,Taurine, ZincSulfate, Acetate, M-Inositol,L-Ascorbic Acid, Magnesium L-Aspartate, Magnesium L-Methionine, CholineBitartrate, L-Alanine, L-Cystine, L-Tryptophan, L-Tyrosine, L-Serine, L-Histidine, L-Threonine, L-Phenylalanine, L-Proline, L-Valine, Glycine, L-Isoleucine, CAEM (AnEmulsifier), L-Glutamine, L-Aspartate, L-Leucine, L-Lysine Acetate, less thaneachofthefollowing:L-Arginine Phosphate Tribasic (2%),contains2%or Sunflower (3%)),Sugar(9%),Calcium High OleicSunflower(6%),Canola(3%), (Non-Hydrogenated Coconut(6%), (19%), Refined Vegetable Oil(18%) Corn SyrupSolids(42%),RiceStarch Ingredients:

3 , 15 Nutra Neocate 16 SPECIALIZED PEDIATRICS please see page37. For productsample information, • • • • • • • • • Main Hypoallergenic Fat Carbohydrate Protein 1 kcal/mL 84.9% Dilution 1 kcal/mL 550 Dilution Displacement: 0.72 mL/g distribution: Energy Free water: Osmolality (mOsm/kg): Standard dilution=1kcal/mL Available inunflavored, tropical&chocolate Nutritionally complete 100% non-allergenicfreeaminoacids (MCT 35%/LCT 65%) Feature Unflavored Unflavored

Unflavored Tropical/Chocolate 45% Tropical Chocolate 42% 13% 84.0% 630 Tropical Chocolate

650 84.0% 42% 44% 14%

A nutritionally complete, powdered amino acid-based medicalfoodA nutritionallycomplete,powderedaminoacid-based Neocate for individualsover theageof1.

For guidanceonmonitoringmicronutrients, pleasesee page38. please seepages24-36. For detailson • • • Indications:

12690 -Chocolate 12124 -Tropical 11790 -Unflavored Code Product Ordering/Reimbursement Information: enterocolitissyndrome(FPIES) Related GIandallergicconditions: Multiple foodallergies Cow milkallergy

• • • • • office todetermine availability. WIC

Gastroesophageal reflux Malabsorption Food protein-induced Eosinophilic esophagitis(EoE) Short bowelsyndrome(SBS) ‡ :

Contact your stateWIC ® scoop size,householdmeasures, Junior 49735-0126-90 49735-0121-24 49735-0117-90 Code Reimbursement

B4161 B4161 B4161 Code HCPCS information seepage195. information For morereimbursement 4 x400g(14.1oz) 4 x400g(14.1oz) 4 x400g(14.1oz) Packaging Product 14-18 years 9-13 years 4-8 years 1-3 years & minerals: + 25key vitamins 100% DRIs Meets orexceeds andadministration, § forprotein 2550 kcal 1565 kcal 1370 kcal 930 kcal 1804 1804 1912 Per Can Calories

Nutrition Information: Vitamin E,IU(mg Vitamin D Vitamin A,IU(mcgRE) Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals Inositol, mg Choline, mg Vitamin C,mg Biotin, mcg Pantothenic Acid,mg Folic Acid,mcg Niacin, mg Vitamin B Vitamin B Riboflavin, mg Thiamin, mg Vitamin K,mcg Vitamins Carbohydrate, g LinoleicAcid,mg Fat, g Protein Equivalent,g Calories Nutrients a -Linolenic Acid,mg

12 6 3 , mg , IU(mcg) , mcg a T.E.) 380(9.5) 956(287) Unflavored Per 100g 2622 364 653 239 530 382 565 105 143 143 478 100 661 10.0 (6.7) 19.2 18.0 21.5 85.2 76.5 44.6 14.4 19.2 49.5 24.0 16.0 1.9 0.62 4.7 7.4 1.9 4.3 0.96 0.61 0.48 200(60.0) Per 100kcal 137 111 118 549 138 76.2 50.0 17.8 16.0 79.9 22.0 29.9 29.9 10.4 79.5 (2.0) 2.1 (1.4) 0.40 4.0 3.8 4.5 0.13 0.98 1.6 9.3 3.0 0.40 0.90 0.20 0.13 4.0 5.0 3.3 0.10 Tropical andChocolate 902(271) 360(9.0) 2300 Per 100g 343 653 225 530 359 540 105 143 143 580 451 18.0 18.0 21.5 85.2 76.5 44.6 13.5 19.2 49.5 21.0 16.0 9.4 (6.3) 1.8 0.62 4.7 7.4 1.9 4.3 0.90 0.61 0.48 200(60.1) Per 100kcal 510 145 118 120 129 100

76.1 49.9 79.6 23.3 31.7 31.7 18.9 17.0 11.0 79.8 (2.0) 2.1 (1.4) 0.40 4.0 4.0 4.8 9.9 3.0 4.3 4.7 3.5 0.14 1.0 1.6 0.42 0.95 0.20 0.14 0.11 Sweetener: Sucralose. less than2% ofthefollowing:Artificial Artificial Flavor (7.2%), Sugar(4.7%),and Chocolate Sweetener: AcesulfamePotassium. and lessthan2%ofthefollowing: Artificial Artificial Flavor (5.2%),CitricAcid (3.2%), Tropical Vitamin D Selenite, Phylloquinone, D-Biotin, Chloride, SodiumMolybdate, Folic Acid,Potassium Iodide,Chromium Hydrochloride, VitaminAAcetate, Chloride Hydrochloride, Pyridoxine Sulfate, CupricRiboflavin, Thiamin Calcium D-Pantothenate, Manganese Alpha Tocopheryl Acetate,Niacinamide, Sulfate, L-Carnitine, ZincSulfate,DL- Propylene Glycol Alginate,Taurine, Ferrous M-Inositol, L-Ascorbic Acid,L-Cystine, Acid EstersofMonoandDiglycerides, L-Tryptophan, L-Tyrosine, DiacetylTartaric Phosphate Tribasic, CholineBitartrate, L-Alanine, MagnesiumAcetate,Calcium Sodium Chloride,L-Histidine, L-Serine, L-Threonine, MonoandDiglycerides, L-Isoleucine, N-Acetyl-L-Methionine, L-Proline, SiliconDioxide, L-Valine, Glycine, Dibasic, L-Leucine, L-Phenylalanine, Tripotassium Citrate, CalciumPhosphate less than2%ofeachthefollowing: (2.3%), L-Lysine L-Aspartate (2%),and Oil (8%)),L-Arginine (2.4%),L-Glutamine Canola Oil(8%),HighOleicSafflower Oils (Palm Kernel and/or CoconutOil(8%), Corn Syrup Solids (52%), Refined Vegetable Ingredients: flavored version alsocontains: 3 flavored version alsocontains: , Cyanocobalamin.

17 Junior Neocate 18 SPECIALIZED PEDIATRICS please seepage 37. For productsample information, • • • • • • • • • • Main Displacement: Hypoallergenic Fat Carbohydrate Protein 1 kcal/mL Dilution 1 kcal/mL Dilution & strawberry total guthealth Energy distribution: Energy Free water: Osmolality (mOsm/kg): Standard dilution=1kcal/mL Available inunflavored, vanilla Nutritionally complete 100% non-allergenicfreeaminoacids Contains prebioticfibertohelpsupport (MCT 35%/LCT 65%) Feature

Unflavored Unflavored Unflavored Unflavored s: 0.74 mL/g 84.5% 45% 42% 13% 550

0.71 mL/g 84.5% Vanilla Vanilla Vanilla Vanilla 41% 45% 14% 650

Strawberry Strawberry Strawberry Strawberry 0.71 mL/g 84.9% 41% 45% 14% 630

For guidanceonmonitoringmicronutrients, pleasesee page38. please seepages24-36. For detailson • • • Indications: 86456 -Strawberry 60627 -Vanilla 12912 -Unflavored Code Product Ordering/Reimbursement Information:

office todetermine availability. WIC enterocolitissyndrome(FPIES) Related GIandallergicconditions: Multiple foodallergies Cow milkallergy

• • • • • food withprebioticfiberforindividuals over theageof1. medicalA nutritionallycomplete,powderedaminoacid-based Neocate

Gastroesophageal reflux Malabsorption Food protein-induced Eosinophilic esophagitis(EoE) Short bowel ‡ :

Contact your stateWIC scoop size,householdmeasures, 49735-016456 49735-010627 49735-012912 Code Reimbursement syndrome (SBS) ® JuniorwithPrebiotics

B4161 B4161 B4161 Code HCPCS information see page195. information For morereimbursement 4 x400g(14.1oz) 4 x400g(14.1oz) 4 x400g(14.1oz) Packaging Product 14-18 years 9-13 years 4-8 years 1-3 years & minerals: + 25key vitamins 100% DRIs Meets orexceeds andadministration, § forprotein 2550 kcal 1565 kcal 1370 kcal 930 kcal 1876 1836 1912 Per Can Calories

Chloride, Potassium, Sodium, Selenium, Chromium, mg mg Molybdenum, Iodine, mg mcg Copper, mcg Manganese, mcg Zinc, mcg Iron, mcg Magnesium, mg Phosphorus, mg Calcium, mg Minerals mg Inositol, Choline, mg mg Vitamin C,mg Biotin, Pantothenic Acid,mg mg Folic Acid,mcg mg Niacin, mcg Vitamin B Vitamin B Riboflavin, mg mg Thiamin, Vitamin K,mcg Vitamin E,IU(mg Vitamin D mg Vitamin A,IU(mcgR.E.) Vitamins SolubleFiber, g Carbohydrate, LinoleicAcid,mg Fat, g Protein Equivalent,g Calories Nutrients g Nutrition Information: a -Linolenic Acid,mg

12 6 3 , mg , IU(mcg) , mcg a T.E.) 380(9.5) Per 100g 2622 956(287) 364 76.2 653 137 239 50.0 530 111 382 79.9 565 118 105 22.0 143 29.9 143 478 100 661 19.2 4.0 18.0 3.8 21.5 4.5 85.2 17.8 76.5 16.0 44.6 14.4 3.0 19.2 49.5 10.4 24.0 5.0 16.0 10.0 (6.7) 1.9 0.40 0.62 0.13 4.7 0.98 7.4 1.6 1.9 4.3 0.90 0.96 0.61 0.13 1.9 0.48 0.10 Unflavored Per 100kcal 200 (60.0) 549 138 29.9 79.5 (2.0) 9.3 0.40 0.20 4.0 0.40 3.3 2.1 (1.4) 916(276) 364(9.1) Per 100g 2300 349 653 230 530 367 542 105 143 459 143 580 18.4 18.0 21.5 85.2 76.5 13.8 51.4 21.0 44.6 19.2 16.0 1.8 0.62 4.7 7.4 4.3 0.61 1.9 0.92 1.9 0.48 9.5 (6.4) Vanilla 200(60.1) Per 100kcal 142 115 118 100 501 126 79.3(2.0) 76.0 50.1 18.6 16.7 80.0 22.9 31.2 11.2 31.2 0.39 4.0 3.9 4.7 0.14 1.0 1.6 3.0 0.94 0.13 4.6 9.7 0.41 0.20 4.2 0.41 3.5 0.10 2.1 (1.4) 956(287) 372(9.3) 2346 Per 100g 653 139 530 113 565 120 469 100 364 77.6 239 51.0 382 81.5 105 22.4 143 30.5 143 592 85.2 18.2 76.5 16.3 52.9 11.3 19.2 4.1 18.0 3.8 21.5 4.6 14.4 3.1 21.5 4.6 44.6 19.2 16.0 10.0 (6.7) 1.9 0.41 0.62 0.13 4.7 1.0 7.4 1.6 4.3 0.92 0.61 0.13 1.9 0.96 1.9 0.48 0.10 Strawberry 204(61.2) Per 100kcal 500 126 30.5 79.3 (2.0) 9.5 0.41 0.20 4.1 0.40 3.4 2.1 (1.4) contains less than2%ofCitricAcid. Strawberry Flavor, ArtificialSweetener:Sucralose. less than2%ofthefollowing: Artificial versions alsocontain:Sugar (8%),and Vanilla andStrawberry Cyanocobalamin. Phylloquinone, D-Biotin,VitaminD Molybdate, SodiumSelenite, Iodide, ChromiumChloride,Sodium A Acetate,Folic Acid, Potassium Pyridoxine Hydrochloride, Vitamin Thiamin ChlorideHydrochloride, Sulfate, CupricRiboflavin, D-Pantothenate, Manganese Acetate, Niacinamide,Calcium Zinc Sulfate,DL-Alpha Tocopheryl Taurine, Ferrous Sulfate,L-Carnitine, L-Cystine, Propylene Glycol Alginate, M-Inositol, L-Ascorbic Acid, Esters ofMonoandDiglycerides, L-Tyrosine, DiacetylTartaric Acid Choline Bitartrate, L-Tryptophan, Acetate, CalciumPhosphateTribasic, L-Serine, L-Alanine, Magnesium Sodium Chloride,L-Histidine, L-Threonine, MonoandDiglycerides, L-Isoleucine, N-Acetyl-L-Methionine, Silicon Dioxide, L-Valine, Glycine, oligosaccharide, Inulin,L-Proline, L-Leucine, L-Phenylalanine, Fructo- Calcium PhosphateDibasic, following: Tripotassium Citrate, and lessthan2%ofeachthe (2.3%), L-Lysine L-Aspartate (2%), L-Arginine (2.4%),L-Glutamine High OleicSafflowerOil(7.5%)), Coconut Oil(8%),Canola(7.5%), Vegetable Oils(Palm Kernel and/or Corn SyrupSolids(51%),Refined Ingredients: flavored version also flavored

3 , 19 Prebiotics with Junior Neocate 20 SPECIALIZED PEDIATRICS • • • • • • • • • • Main Features: please see page37. For productsample information, Hypoallergenic Fat Carbohydrate drink boxes Free water: 84.6% Osmolality: 670mOsm/kg Protein Energy distribution: Energy density=1kcal/mL Available inunflavored Gluten- andcasein-free Convenient ready-to-feed8fl oz Nutritionally complete 100% non-allergenicfreeaminoacids (MCT 35%/LCT 65%) individuals overindividuals theageof1. The firstandonlyunflavored ready-to-feed aminoacid-basedmedicalfoodfor hypoallergenic Neocate

46% 42% 12% ® Splash,Unflavored

For detailsonadministration, please seepages24-36. • • • Indications: 84451 -Unflavored Code Product Ordering/Reimbursement Information:

office todetermine availability. WIC • • enterocolitissyndrome(FPIES) • • Related GIandallergicconditions: Multiple foodallergies Cow milkallergy •

Gastroesophageal reflux Malabsorption Eosinophilic esophagitis(EoE) Short bowelsyndrome(SBS) Food protein-induced ‡ :

Contact your stateWIC 49735-0144-51 Code Reimbursement

B4161 Code HCPCS information seepage195. information For morereimbursement 27 x237mL(8floz) Packaging Product 14-18 years 9-13 years 4-8 years 1-3 years & minerals: + 25key vitamins 100% DRIs Meets orexceeds

§ forprotein 2550 mL 1565 mL 1370 mL 930 mL 237 Per Box Calories

Nutrition Information: Inositol, mg Choline, mg Vitamin C,mg Biotin, mcg Pantothenic Acid,mg Folic Acid,mcg Niacin, mg Vitamin B Vitamin B Riboflavin, mg Thiamin, mg Vitamin K,mcg Vitamin E,IU(mg Vitamin D Vitamin A,IU(mcgR.E.) Vitamins Carbohydrate, g LinoleicAcid,mg Fat, g Protein Equivalent,g Calories Nutrients 12 6 3 , mg , IU(mcg) , mcg a T.E.) Per drinkbox 190(4.7) (237 mL) 474(142) 690 237 52.1 70.9 22.0 70.9 24.9 12.1 0.24 5.0 (3.3) 0.95 7.1 0.95 2.1 0.47 0.31 9.5 7.1 200(60.0) 291 100 100 mL 29.9 29.9 10.5 80.0 (2.0) Per 22.0 0.10 2.1 (1.4) 0.40 9.3 3.0 0.40 0.90 0.20 0.13 4.0 5.1 3.0

Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals Per drinkbox (237 mL) 180 325 119 237 190 280 10.7 42.2 37.9 9.5 9.0 0.31 2.3 3.6 137 100 118 100 mL 76.0 50.0 80.0 17.8 16.0 Per 4.5 4.0 3.8 0.13 0.98 1.5

D-Biotin, VitaminD Sodium Selenite,Phylloquinone, Chromium Chloride,SodiumMolybdate, Palmitate, Folic Acid,Potassium Iodide, Pyridoxine Hydrochloride, VitaminA Thiamin ChlorideHydrochloride, Sulfate, CupricRiboflavin, Calcium D-Pantothenate, Manganese alpha Tocopheryl Acetate,Niacinamide, Sulfate, L-Carnitine, ZincSulfate,DL- M-Inositol, L-Cystine, Taurine, Ferrous Chloride, L-Tyrosine, CelluloseGum, Bitartrate, L-Tryptophan, Calcium Chloride, MagnesiumAcetate,Choline L-Alanine, MalicAcid,Potassium L-Histidine, L-Serine, L-Ascorbic Acid, N-Acetyl L-Methionine, L-Threonine, Citrate, L-Valine, Glycine, L-Isoleucine, Mono- andDiglycerides, Trisodium Acid EstersOfMono-andDiglycerides, Citrate, L-Proline, DiacetylTartaric L-Leucine, L-Phenylalanine, Tripotassium L-Aspartate, MicrocrystallineCellulose, Glycerophosphate, L-Arginine, L-Lysine of eachthefollowing:Calcium Canola Oil(0.6%)),andlessthan2% Kernel and/or CoconutOil)(1.8%), Chain Triglycerides (Modified Palm Oleic SunflowerOil(2.3%),Medium (5%), Refined Vegetable Oils(High Water (85%),Maltodextrin (6%),Sugar Ingredients:

3 , Cyanocobalamin. 21 Unflavored Splash, Neocate 22 SPECIALIZED PEDIATRICS • • • • • • • • • • Main Features: please seepage 37. For productsample information, Osmolality: Hypoallergenic 740 mOsm/kg 790 mOsm/kg Fat Carbohydrate Protein Unflavored Orange-Pineapple, Grape, Tropical Fruit, drink boxes Free water:84.6% Energy distribution: Energy density=1kcal/mL Available in4great-tastingflavors: Gluten- andcasein-free Convenient ready-to-feed8fl oz Nutritionally complete 100% non-allergenicfreeaminoacids (MCT 35%/LCT 65%)

(Orange-Pineapple, Tropical Fruit) (Grape)

46% 42% 12% medical foodforindividualsover theageof1. The firstandonlyflavored, nutritionally complete,ready-to-feedaminoacid-based Neocate

® For detailsonadministration, please seepages24-36. • • • Indications: 122437- Tropical Fruit 122435- Grape 122436- Orange Pineapple Code Product Ordering/Reimbursement Information: Splash

office todetermine availability. WIC enterocolitissyndrome(FPIES) Related GIandallergicconditions: Multiple foodallergies Cow milkallergy • • • • •

Gastroesophageal reflux Malabsorption Food protein-induced Eosinophilic esophagitis(EoE) Short bowelsyndrome(SBS) ‡ :

Contact your stateWIC 49735-0124-37 49735-0124-35 49735-0124-36 Code Reimbursement

B4161 B4161 B4161 Code HCPCS information seepage195. information For morereimbursement 27 x237mL(8floz) 27 x237mL(8floz) 27 x237mL(8floz) Packaging Product 14-18 years 9-13 years 4-8 years 1-3 years & minerals: + 25key vitamins 100% DRIs Meets orexceeds Upgrade as of Upgrade asof September 2017 § forprotein 2550 mL 1565 mL 1370 mL 930 mL

237 237 237 Per Box Calories

Nutrition Information: Inositol, mg Choline, mg Vitamin C,mg Biotin, mcg Pantothenic Acid,mg Folic Acid,mcg Niacin, mg Vitamin B Vitamin B Riboflavin, mg Thiamin, mg Vitamin K,mcg Vitamin E,IU(mg Vitamin D Vitamin A,IU(mcgR.E.) Vitamins Carbohydrate, g LinoleicAcid,mg Fat, g Protein Equivalent,g Calories Nutrients 12 6 3 , mg , IU(mcg) , mcg a T.E.) Per drinkbox 190(4.7) (237 mL) 474(142) 690 237 52.1 70.9 22.0 70.9 24.9 12.1 0.24 5.0 (3.3) 0.95 7.1 0.95 2.1 0.47 0.31 9.5 7.1 200(60.0) 291 100 100 mL 29.9 29.9 10.5 80.0 (2.0) Per 22.0 0.10 2.1 (1.4) 0.40 9.3 3.0 0.40 0.90 0.20 0.13 4.0 5.1 3.0

2% of:Sucralose. Orange-Pineapple of: AcesulfamePotassium. Tropical Fruit Sucralose. Grape Cyanocobalamin. Phylloquinone, D-Biotin,VitaminD Potassium Iodide,SodiumMolybdate, Pyridoxine Hydrochloride, Folic Acid, Hydrochloride, Vitamin APalmitate, Chromium Chloride,ThiaminChloride Selenite, CupricSulfate,Riboflavin, Manganese Sulfate,Sodium Niacinamide, CalciumD-Pantothenate, Sulfate, Dl-Alpha Tocopheryl Acetate, Lactate, Taurine, L-Carnitine, Zinc Acid, M-Inositol,L-Cystine, Ferrous L-Tyrosine, CelluloseGum,L-Ascorbic L-Tryptophan, CalciumChloride, Magnesium Acetate,CholineBitartrate, L-Serine, L-Alanine, Potassium Chloride, L-Methionine, L-Threonine, L-Histidine, L-Valine, Glycine, L-Isoleucine, N-Acetyl Diglycerides, Trisodium Citrate, L-Proline, Mono- AndDiglycerides, Mono-And Diacetyl Tartaric AcidEstersOf Tripotassium Citrate, L-Phenylalanine, Microcrystalline Cellulose,L-Leucine, Acid, L-Arginine, L-Lysine L-Aspartate, Calcium Glycerophosphate, Malic Of TheFollowing: ArtificialFlavors, Canola Oil),AndLess Than2%OfEach Palm Kernel And/Or CoconutOil), Medium ChainTriglycerides (Modified Vegetable Oils(High OleicSunflowerOil, Water, Maltodextrin, Sugar, Refined Ingredients: alsocontainslessthan2% of: alsocontainslessthan2% alsocontains lessthan

3 , 23 Splash Neocate 24 SPECIALIZED PEDIATRICS than 24 hours.Do notfreeze. Liquids: a refrigerator) and usewithinoneweek. Packets: store inacool,dryplace (notarefrigerator). SyneoInfant). Usewithinonemonth (twoweeksforNeocate Cans: STORAGE: • • • • • • • • DIRECTIONS FORPREPARATION ANDUSE:

Household measuresarenotrecommended formeasuringpowderedNutriciaproducts. up to Tube feedinghangtime: or stirformulaimmediatelybeforeuse. (2-4ºC) andkept nolongerthan post-pyloric feedingtubeunlessdirectedorsupervisedby ahealthcareprofessional. • • condition ofthepatient.Intendedforuseundermedicalsupervision. All scoopsshouldbeunpacked andlevel. Useascalethatmeasuresingrams accurate forthe most results. Discard formulaleftinbottleorcup Once formulaispreparedordrinkbox is opened,formulashouldbestoredinarefrigerator at35-40ºF If taken orally, formulasforbeyond 1year ofagearebestserved chilled. Do notboilformulaoruseamicrowave toprepareorwarmformula. All formulascanbetaken orally ortubefed.Notforparenteral use. Intake andmedical tobedeterminedbyweight ahealthcareprofessionalandisdependentontheage,body NeocateSyneoInfantisnotrecommendedforuseininfantswithacentral venous or catheter NeocateNutra isasemi-solidmedicalfoodandnotforbottleortubefeeding. Store unopenedcans atroomtemperature. Avoid extreme temperatures. resealcanand Onceopened, Storeunopened productinacool, dryplace.Once opened,storeinarefrigerator andkeep nolonger 4 hours Store unopenedpackets atroomtemperature. (not dryplace in acool, Onceopened, resealandstore , atwhichtimeunusedformulashouldbe discarded. Nutriciarecommendsformulacanbesafelykept atroomtemperature for 24 hours 1 hour fromthetimeofpreparation Shake liquids). (timeofopeningfor after feedingstarts.

Shake wellbefore use. NEOCATE SPLASH Do notwarmprepared product.Notsuitableasasolesource ofnutrition. discarded ifnotused withinonehour. Neocate Nutra canbeaddedtocooked not addtovery dishes.Do hotfoods. Neocate Nutra should bepreparedimmediatelypriorto feeding.Any remaining shouldbe prepared product NEOCATE NUTRA NEOCATE JUNIOR the useofsterilizedbottles. (40°C) may lessenthebenefits oftheprobioticcultures. *For NeocateSyneo Infant:Mixingwithwaterwarmerthan104°F(40°C) formulaabove orwarming 104°F Only usethescoopprovided. To make astandarddilution(20cal/floz),add1unpacked level fluidounceofwater. scoopofpowdertoeach NEOCATE SYNEOINFANT ANDNEOCATE INFANT DHA/ARA DIRECTIONS FORPREPARATION ANDUSE: consistency, addmoreorlesswaterasrequired. 3. 2. 1. 3. 2. 1. 3. 2. 1.

Gradually add the required amount of water while stirring withacleanspoon.Mixuntilthickened. Towhile water alterthe of amount required the add Gradually 24 hours.Oncefeedingbegins,usewithin1hourordiscard. Add therecommendednumberofscoops ofNeocateNutra toacleanbowl. Wash handsthoroughlyandcleanthepreparation area. Cover andshake untilthepowderhasdissolved. Add theprescribedamountofNeocateJuniortowater. Measure therequiredamountofwarmorcoolwaterintoacontainer Cap bottle;shake well.Feed immediatelyORrefrigerate immediatelyat35-40°F(2-4°C) usewithin and Add 1unpacked level scoopofpowdertoeach1flozwater.* Wash handsthoroughlyandcleanpreparation area. cooled, boiledwaterbeusedwhenpreparing theproductforinfants. serving sizecanbepreparedby adding1flozofwater to4scoopsofpowder(18.5g).Itisrecommendedthat The suggestedservingis8scoops(37g) of powderplus2flozwatertogive aspoonableconsistency. Asmaller We waterforpreparation recommendcooled,boiled and Refer toproductlabelsforfullpreparation instructions Not for bottle or tubefeeding Not forbottle . .

25 Instructions Mixing Pediatrics Specialized 26 SPECIALIZED PEDIATRICS *US measures: 1cup =240mL;½ cup=120mL; ⅓cup=80 mL;¼cup =60mL;1 so arepreferable tohouseholdmeasures. North America recommends using agramscaleforgreatest accuracy. The scoops Nutriciaprovidesare validatedforusewithNutricia formulas, approximations onlyandhavebeenprovided forconvenience:results canvarysignificantly based ontheindividual,device, andmethod.Nutricia Household measuresarebased onstandardUS,dryhouseholdmeasures.* All measuresarelevel andunpacked. These valuesare Household Measures 1 cup 1/2 cup 1/3 cup 1/4 cup 1 Tbsp 1 tsp 1/2 tsp 1 scoop Neocate JuniorwithPrebiotics,Vanilla 1 cup 1/2 cup 1/3 cup 1/4 cup 1 Tbsp 1 tsp 1/2 tsp 1 scoop Neocate JuniorwithPrebiotics,Strawberry 1 cup 1/2 cup 1/3 cup 1/4 cup 1 Tbsp 1 tsp 1/2 tsp 1 scoop Neocate SyneoInfant Measure 120 g 111 g 130 g Measure Weight 60 g 40 g 30 g 55.5 g 37.0 g 27.8 g 65.0 g 43.3 g 32.5 g 7.5 g 2.5 g 1.3 g 8.2 g 6.9 g 2.3 g 1.2 g 8.0 g 8.1 g 2.7 g 1.4 g 4.7 g

1 cup 1/2 cup 1/3 cup 1/4 cup 1 Tbsp 1 tsp 1/2 tsp 1 scoop Neocate JuniorwithPrebiotics,Unflavored 1 cup 1/2 cup 1/3 cup 1/4 cup 1 Tbsp 1 tsp 1/2 tsp 1 scoop Neocate Junior, Unflavored, Tropical andChocolate 1 cup 1/2 cup 1/3 cup 1/4 cup 1 Tbsp 1 tsp 1/2 tsp 1 scoop Neocate InfantDHA/ARAandNutra

Tbsp = 15mL;1tsp =5mL;½tsp =2.5mL Neocate MixingTool andHouseholdMeasuresCalculator Visit NutriciaLearningCenter.com 129 g 116 g 126 g Weight 64.5 g 43 g 32.3 g 58 g 38.7 g 29 g 63 g 42 g 31.5 g 8.1 g 2.7 g 1.4 g 8.2 g 7.3 g 2.3 g 1.2 g 8.2 g 7.9 g 2.6 g 1.3 g 4.6 g

for the

Number of cases permonth (30 days) arerounded upto thenearest whole number. Volume Prescription 40 oz 36 oz 32 oz 28 oz 24 oz 20 oz Volume/ Total Vol/can DHA/ARA Neocate Infant Total Vol/can Infant Neocate Syneo Total Servings/can 4 Servings 3 Servings 2 Servings 1 Serving Servings/day 32 floz 28 floz 24 floz 20 floz 40 floz 36 floz day

Neocate Neocate Syneo Syneo Infant (# cans/month) 13 11 10 9 8 6 20 kcal/fl oz 97 floz 95 floz

(# cans/mon) Neocate JuniorUnflavored

DHA/ARA Neocate Neocate 19 17 16 14 12 10 Infant Infant 12 11 10 9 7 6 30 kcal/fl oz

(# cans/mon) Neocate Neocate Syneo Syneo Infant (# cans/month) 14 13 11 10 8 7 22 kcal/fl oz 4 scoopsNutra (88kcal) (# cs/mon) 6 5 3 2 88 floz 86 floz

Neocate SyneoInfantandDHA/ARA

5 5 4 4 3 3 DHA/ARA Neocate Neocate 21 Servings Infant Infant 14 12 11 10 8 7

Neocate Neocate Syneo Syneo Infant (# cans/month) 15 14 12 11 9 8 24 kcal/fl oz (# cs/mon) 81 floz 79 floz (# cans/mon) Neocate Nutra

Volume/day 2 2 1 1 DHA/ARA Neocate Neocate Neocate JuniorFlavored 20 18 16 14 12 10 Infant Infant 15 13 12 10 9 7 30 kcal/fl oz

Neocate Neocate Syneo Syneo Infant (# cans/month) 13 11 10 16 15 8 26 kcal/fl oz (# cs/mon) 74 floz 73 floz

DHA/ARA Neocate Neocate 5 5 4 4 3 3 Infant Infant 10 16 15 13 11 8

(# cans/mon) Neocate Neocate Syneo Syneo Infant (# cans/month) 16 14 12 11 18 9 8 scoopsNutra (175kcal) 28 kcal/fl oz 12 69 floz 68 floz 9 6 3 (# boxes/mon)

DHA/ARA Neocate Neocate 152 137 122 107 Infant Infant 10 Servings 92 76 Neocate Splash 17 16 14 12 10 9 30 kcal/fl oz

Neocate Neocate Syneo Syneo Infant (# cans/month) (# cs/mon) 19 17 15 13 11 9 30 kcal/fl oz (# cs/mon) 64 floz 63 floz

3 2 1 3

6 6 5 4 4 3 DHA/ARA Neocate Neocate Infant Infant 19 17 15 13 11 9

27 Measurements Household Pediatrics Specialized 28 SPECIALIZED PEDIATRICS Neocate Chloride, mg Potassium, mg Sodium,mg Selenium,mcg Chromium,mcg Molybdenum,mcg Iodine,mcg Copper, mcg Manganese,mcg Zinc,mg Iron,mg Magnesium,mg Phosphorus,mg Calcium,mg Minerals Inositol,mg Choline,mg VitaminC,mg Biotin,mcg Pantothenic Acid,mcg Folic Acid,mcg Niacin,mcg VitaminB VitaminB Riboflavin, mcg Thiamin,mcg VitaminK,mcg VitaminE,IU VitaminD VitaminA,IU Vitamins LinoleicAcid,mg SolubleFiber, g Carbohydrate, g Fat,g ProteinEquivalent,g Calories Dilution Nutrients per100mL α -Linolenic Acid,mg

12 6 3 , mcg , IU , mcg ® Syneo™ Infant 20 kcal/fl oz 407 688 190 470 49.4 75.8 66.7 55.6 53.1 72.3 26 13.8 56.1 26.7 54.5 77.1 15.2 13.4 75.8 96.8 0.2 2.0 1.5 1.5 0.7 1.0 7.0 7.2 2.7 9.0 6.0 0.9 0.6 7.5 3.2 1.9

Nutrient DilutionChart 22 kcal/fl oz 448 756 209 517 107 54.3 83.4 73.3 61.1 58.4 79.5 28.6 15.1 61.8 29.3 59.9 84.8 16.7 14.7 83.4 0.2 2.2 1.6 1.7 0.8 1.1 7.7 8.0 2.9 9.9 6.6 1.0 0.7 8.3 3.6 2.1 24 kcal/fl oz 488 825 116 228 564 59.3 90.9 80 66.7 10.8 63.7 86.7 31.2 16.5 67.4 32.0 65.3 92.5 18.2 16.1 90.9 0.2 2.4 1.8 1.9 0.9 1.2 8.4 8.7 3.2 7.2 1.1 0.8 9.0 3.9 2.3 26 kcal/fl oz 529 894 126 247 611 100 64.2 98.5 86.7 72.3 11.7 69.0 94.0 33.8 17.9 73.0 34.7 70.8 19.7 17.4 98.5 0.2 2.6 1.9 2.0 0.9 1.3 9.1 9.4 3.5 7.8 1.2 0.8 9.8 4.2 2.5 28 kcal/fl oz 106 570 963 136 266 658 101 108 106 69.2 93.3 77.8 12.6 10.1 10.5 74.3 36.4 19.3 78.6 37.3 76.2 21.2 18.7 1.0 0.3 2.8 2.0 2.2 1.4 9.8 3.7 8.4 1.3 0.9 4.5 2.7 30 kcal/fl oz 1032 114 100 108 116 611 114 145 285 705 74.1 83.4 10.5 10.9 13.5 11.3 79.6 38.9 20.6 84.2 40.0 81.7 22.7 20.1 0.3 1.1 3.0 2.2 2.3 1.5 4.0 9.0 1.4 0.9 4.8 2.8 Neocate Chloride, mg Potassium, mg Sodium,mg Selenium,mcg Chromium,mcg Molybdenum,mcg Iodine,mcg Copper, mcg Manganese,mcg Zinc,mg Iron,mg Magnesium,mg Phosphorus,mg Calcium,mg Minerals Inositol,mg Choline,mg VitaminC,mg Biotin,mcg Pantothenic Acid,mcg Folic Acid,mcg Niacin,mcg VitaminB VitaminB Riboflavin, mcg Thiamin,mcg VitaminK,mcg VitaminE,IU VitaminD VitaminA,IU Vitamins LinoleicAcid,mg Carbohydrate, g Fat,g ProteinEquivalent,g Calories Dilution Nutrients per100mL α -Linolenic Acid,mg

12 6 3 , mcg , IU , mcg ® InfantDHA/ARA

20 kcal/fl oz 400 676 187 492 74.5 48.6 66.7 57.9 53.3 72.5 26.1 13.8 56.6 27.6 54.8 77.4 14.9 13.2 74.5 95.2 0.18 2.0 1.5 1.6 0.73 1.0 7.0 7.1 2.6 8.8 5.9 0.94 7.2 3.4 1.9

Nutrient DilutionChart 22 kcal/fl oz 440 744 105 205 541 82.0 53.4 73.3 63.7 58.6 79.7 28.7 15.2 62.2 30.4 60.3 85.2 16.4 14.5 82.0 0.2 2.2 1.6 1.7 0.8 1.1 7.7 7.8 2.9 9.7 6.5 1.0 7.9 3.7 2.0 24 kcal/fl oz 480 812 114 224 590 89.4 58.3 80.0 69.5 63.9 87.0 31.3 16.6 67.9 33.1 65.8 92.9 17.9 15.8 10.6 89.4 0.22 2.4 1.8 1.9 0.88 1.2 8.4 8.5 3.1 7.0 1.1 8.6 4.1 2.2 26 kcal/fl oz 101 520 879 124 243 640 96.9 63.2 86.7 75.3 69.3 94.2 33.9 17.9 73.6 35.9 71.2 19.4 17.1 11.5 96.9 0.23 2.6 1.9 2.0 0.95 1.3 9.2 9.3 3.4 7.6 1.2 9.3 4.4 2.4 28 kcal/fl oz 104 101 108 560 947 104 133 261 689 68.0 93.3 81.0 74.6 36.5 19.3 79.2 38.6 76.7 20.9 18.4 10.0 12.4 10.0 0.25 2.8 2.0 2.2 1.0 1.4 9.9 3.7 8.2 1.3 4.7 2.6 30 kcal/fl oz 1014

112 100 109 116 600 112 143 280 738

72.9 86.8 79.9 39.1 20.7 84.9 41.4 10.6 82.2 22.4 19.8 10.7 13.3 10.8 0.27 3.0 2.2 2.3 1.1 1.5 3.9 8.8 1.4 5.1 2.8 29 Charts Dilution Pediatrics Specialized 30 SPECIALIZED PEDIATRICS For household measures,seepage26. ~0.71 mL water. scale provides greatestaccuracy. 1level,unpackedscoop yields4.7gramspowder andprovides22.33kcal. 1gramprovides4.75kcal anddisplaces † * This chartassumes1floz=30mL. Water volumesareexact,but final volumeofpreparedformulamayvaryslightly. 33.0 29.0 25.0 21.0 17.0 14.5 11.0 8.0 5.5 4.5 fl oz Volume of 32.0 28.0 24.0 20.0 18.0 16.0 11.0 8.0 5.0 3.0 fl oz Volume of Neocate Scoops shouldbeleveland unpacked.WhilethescoopsNutriciaprovidesarevalidated forusewithNutriciaformul Water* Water* 20 kcal/fl oz(Standarddilution) 990 870 750 630 510 435 330 240 165 135 960 840 720 600 540 480 330 240 150 mL mL 90 Neocate PowderNeocate PowderNeocate scoops scoops 22 kcal/fl oz 37 32 28 23 19 16 12 32 28 24 20 18 16 11 Amount of Amount of 9 6 5 8 5 3 ® Syneo™ Infant 173.9 150.4 131.6 108.1 150.4 131.6 112.8 grams grams 89.3 75.2 56.4 42.3 28.2 23.5 94.0 84.6 75.2 51.7 37.6 23.5 14.1 † †

37.1 32.6 28.1 23.6 19.1 16.3 12.3 35.6 31.1 26.7 22.2 20.0 17.8 12.2 fl oz fl oz Final Volume*Final Volume*Final Approximate Approximate 9.0 6.2 5.1 9.0 5.5 3.3 1115 1065 975 845 705 575 490 370 270 185 150 935 800 665 600 535 365 270 165 100 mL mL

32.0 28.0 24.0 21.0 17.0 14.0 9.0 6.0 3.0 1.5 fl oz 30.0 28.0 24.0 21.0 18.0 14.0 11.5 10.5 9.0 6.5 fl oz Volume of Volume of Water* Water* 960 840 720 630 510 420 270 180 900 840 720 630 540 420 345 315 270 195 Dilution Charts mL mL 90 45

Neocate PowderNeocate PowderNeocate scoops scoops 26 kcal/fl oz 24 kcal/fl oz 43 37 32 28 23 19 12 37 34 29 26 22 17 14 13 11 Amount of Amount of 8 8 4 2 202.1 173.9 150.4 131.6 108.1 173.9 159.8 136.3 122.2 103.4 grams grams 89.3 56.4 37.6 79.9 65.8 61.1 51.7 37.6 18.8 9.4

† †

Final Volume*Final Volume*Final Approximate Approximate 36.8 32.1 27.6 24.1 19.6 16.1 10.3 34.1 31.8 27.2 23.9 20.4 15.9 13.1 11.9 10.2 fl oz fl oz 6.9 7.4 3.4 1.7 1105 1025 965 825 725 585 485 310 205 955 815 715 615 475 390 360 305 220 105 mL mL 50

32.0 28.0 24.0 20.0 17.0 14.0 11.5 9.5 5.0 2.5 fl oz 32.0 27.0 24.0 20.0 17.0 13.0 11.0 9.0 7.5 5.5 fl oz Volume of Volume of Water* Water* 960 840 720 600 510 420 345 285 150 960 810 720 600 510 390 330 270 225 165 mL mL 75

as, weighingpowderusing agram Neocate PowderNeocate PowderNeocate scoops scoops 30 kcal/fl oz 28 kcal/fl oz 51 44 38 32 27 22 18 15 47 39 35 29 25 19 16 13 11 Amount of Amount of 8 8 4 239.7 206.8 178.6 150.4 126.9 103.4 221 183 165 136 118 grams grams 84.6 70.5 37.6 89.3 75.2 61.1 51.7 37.6 18.8

† †

Final Volume*Final Volume*Final Approximate Approximate 37.7 32.9 28.2 23.6 20.0 16.4 13.5 11.2 37.2 31.3 27.9 23.2 19.8 15.1 12.8 10.4 fl oz fl oz 5.9 8.7 6.4 2.9 1130 1115

175 260 190 985 845 705 600 495 405 335 940 835 695 595 455 385 315

mL mL 90

Specialized Pediatrics Dilution Charts Dilution Pediatrics Specialized For household measures,seepage26. ~0.70 mL water. scale provides greatestaccuracy. 1level,unpackedscoop yields4.6gramspowder andprovides22.22kcal. 1gramprovides4.83kcal anddisplaces † * This chartassumes1floz=30mL. Water volumesareexact,but final volumeofpreparedformulamayvaryslightly. 32.5 29.0 25.5 22.0 18.0 14.5 11.0 8.0 5.5 4.5 fl oz Volume of 31.0 29.0 25.0 22.0 18.0 15.0 11.0 7.0 5.0 3.0 fl oz Volume of Neocate Scoops shouldbeleveland unpacked.WhilethescoopsNutriciaprovidesarevalidated forusewithNutriciaformul Water* Water* 20 kcal/fl oz(Standarddilution) 975 870 765 660 540 435 330 240 165 135 930 870 750 660 540 450 330 210 150 mL mL 90 Neocate PowderNeocate PowderNeocate scoops scoops 22 kcal/fl oz 36 32 28 24 20 16 12 31 29 25 22 18 15 11 Amount of Amount of 3 9 6 5 7 5 ® InfantDHA/ARA 165.6 147.2 128.8 110.4 142.6 133.4 115.0 101.2 grams grams 92.0 73.6 55.2 82.8 69.0 50.6 13.8 41.4 27.6 23.0 32.2 23.0 † †

36.4 32.4 28.5 24.6 20.1 16.2 12.3 34.3 32.1 27.7 24.4 19.9 16.6 12.2 fl oz fl oz Final Volume*Final Volume*Final Approximate Approximate 3.3 9.0 6.1 5.0 7.8 5.5 1091 1030 100 973 855 737 604 487 369 269 184 151 963 831 731 598 498 365 233 166 mL mL

30.0 27.5 24.5 21.0 18.0 14.0 10.5 7.5 4.5 3.0 fl oz 32.0 28.5 24.5 21.5 18.0 14.0 10.5 6.5 5.0 2.5 fl oz Volume of Volume of Water* Water* 900 825 735 630 540 420 315 225 135 960 855 735 645 540 420 315 195 150 Dilution Charts mL mL 90 75

Neocate PowderNeocate PowderNeocate scoops scoops 26 kcal/fl oz 24 kcal/fl oz 40 37 33 28 24 19 14 10 39 35 30 26 22 17 13 Amount of Amount of 4 3 6 8 6 184.0 170.2 151.8 128.8 110.4 179.4 161 138 119.6 101.2 grams grams 18.4 13.8 87.4 64.4 46.0 27.6 78.2 59.8 36.8 27.6

† †

Final Volume*Final Volume*Final Approximate Approximate 34.3 31.5 28.0 24.0 20.6 16.0 12.0 36.2 32.3 27.7 24.3 20.4 15.8 11.9 fl oz fl oz 3.4 2.8 8.6 5.1 7.4 5.6 1029 1086 103 944 841 720 617 481 360 257 154 968 832 729 611 475 357 221 169 mL mL 85

31.0 28.0 24.0 20.5 17.0 14.0 10.0 7.0 5.0 2.5 fl oz 31.5 28.0 24.0 20.5 17.0 14.5 11.0 9.0 7.5 5.5 fl oz Volume of Volume of Water* Water* 930 840 720 615 510 420 300 210 150 945 840 720 615 510 435 330 270 225 165 mL mL 75

as, weighingpowderusing agram Neocate PowderNeocate PowderNeocate scoops scoops 30 kcal/fl oz 28 kcal/fl oz 49 44 38 32 27 22 16 11 46 41 35 30 25 21 16 13 11 Amount of Amount of 8 4 8 225.4 202.4 174.8 147.2 124.2 101.2 211.6 188.6 161.0 138.0 115.0 grams grams 73.6 50.6 36.8 18.4 96.6 73.6 59.8 50.6 36.8

† †

Final Volume*Final Volume*Final Approximate Approximate 36.3 32.7 28.1 23.9 19.9 16.4 11.7 36.4 32.4 27.8 23.7 19.7 16.8 12.7 10.4 fl oz fl oz 8.2 5.9 2.9 8.7 6.4 1088 1093

982 842 718 597 491 352 972 833 712 591 503 382 312 245 176 260 191

mL mL 88

31 Charts Dilution Pediatrics Specialized 32 SPECIALIZED PEDIATRICS Neocate Water Volume* Water Volume* Water Volume* Water Volume* For household measures, see page26. Visit www.NutriciaLearningCenter forprintable dilution charts and theNeocate Mixing Tool. 4.78 kcal anddisplaces ~0.72mL water. using a gramscaleprovides greatest accuracy. 1level,unpacked scoopyields8.2grams powderandprovides39.2 kcal.1gramprovides † *This chartassumes 1floz=30mL. Water volumesare exact,butfinalvolumeof preparedformulamayvary slightly. Scoops should belevelandunpacked.While thescoopsNutriciaprovides arevalidatedforuse withNutriciaformul 29.0 17.0 12.0 30.0 20.0 16.0 11.5 30.0 19.0 16.0 11.0 30.0 21.0 10.5 fl oz fl oz fl oz fl oz 8.0 4.0 8.5 8.0 7.0 3.5 870 510 360 240 120 900 600 480 345 255 900 570 480 330 240 900 630 315 210 105 mL mL mL mL ® Junior, Unflavored NeocatePowder NeocatePowder NeocatePowder NeocatePowder scoops scoops scoops scoops 26 kcal/fl oz 24 kcal/fl oz 22 kcal/fl oz 20 kcal/fl oz 22 13 21 14 11 19 12 10 17 12 9 6 3 8 6 7 5 6 4 2

grams grams grams grams 180 107 172 115 156 139 73.8 49.2 24.6 90.2 65.6 49.2 98.4 82.0 57.4 41.0 98.4 49.2 32.8 16.4 † † † †

FinalVolume* FinalVolume* FinalVolume* FinalVolume* 33.3 19.6 13.8 34.1 22.8 18.2 13.1 33.7 21.4 18.0 12.4 33.3 23.4 11.7 fl oz fl oz fl oz fl oz 9.2 4.6 9.7 9.0 7.8 3.9 Dilution Charts 1000 1024 1012 1000 587 413 275 138 683 545 392 290 641 539 371 270 701 350 234 117 mL mL mL mL

Water Volume* Water Volume* Water Volume* Water Volume* 27.0 21.0 14.5 11.5 28.0 21.5 18.5 15.5 12.5 28.0 20.0 10.0 30.0 24.0 18.0 12.0 fl oz fl oz fl oz fl oz 8.5 6.5 3.5 6.0

810 630 435 345 255 840 645 555 465 375 840 600 300 200 100 900 720 540 360 180 30 kcal/fl oz(Standarddilution) mL mL mL mL NeocatePowder NeocatePowder NeocatePowder NeocatePowder

scoops scoops scoops scoops 34 kcal/fl oz 32 kcal/fl oz 28 kcal/fl oz 28 22 15 12 27 21 18 15 12 25 18 25 20 15 10 9 9 6 3 5

grams grams grams grams 230 180 123 221 172 148 123 205 148 205 164 123 98.4 73.8 98.4 73.8 49.2 24.6 82.0 41.0

† † † †

as, weighing powder FinalVolume* FinalVolume* FinalVolume* FinalVolume* 32.5 25.3 17.5 13.9 10.3 33.3 25.6 22.0 18.5 14.9 32.9 24.0 11.8 34.9 27.9 21.0 14.0 fl oz fl oz fl oz fl oz 8.0 4.0 7.0

1048

240 120 210 975 760 524 416 308 999 769 661 554 446 988 715 353 838 629 419 mL mL mL mL Specialized Pediatrics Dilution Charts Dilution Pediatrics Specialized For household measures, seepage 26.Visit www.NutriciaLearningCenter for printabledilution charts and theNeocate Mixing Tool. 4.78 kcal anddisplaces ~0.74mL water. using agram scale providesgreatestaccuracy. 1level,unpacked scoopyields8.2grams powderandprovides39.2 kcal.1gramprovides † *This chartassumes 1floz=30mL. Water volumesare exact,butfinalvolumeof preparedformulamayvary slightly. Scoops should belevelandunpacked.While thescoopsNutriciaprovides arevalidatedforuse withNutriciaformul Neocate

29.0 21.0 13.0 29.0 20.0 16.0 11.5 30.0 19.0 14.0 11.0 30.0 21.0 12.5 Water Volume* Water Volume* Water Volume* Water Volume* fl oz fl oz fl oz fl oz 9.0 6.5 8.5 8.0 7.0 3.5 870 630 390 270 195 870 600 480 345 255 900 570 420 330 240 900 630 375 210 105 ® mL mL mL mL JuniorwithPrebiotics,Unflavored scoops scoops scoops scoops Neocate Powder Neocate Powder Neocate Powder Neocate Powder 26 kcal/fl oz 24 kcal/fl oz 22 kcal/fl oz 20 kcal/fl oz 22 16 10 20 14 11 19 12 17 12 7 5 8 6 9 7 5 7 4 2

180 131 164 115 156 139 grams grams grams grams 82.0 90.2 98.4 98.4 57.4 41.0 65.6 49.2 73.8 57.4 41.0 57.4 32.8 16.4 † † † †

fl oz fl oz fl oz fl oz 33.4 24.2 15.0 33.0 22.8 18.2 33.8 21.4 33.4 23.4 10.4 13.1 15.8 12.4 13.9 Final Volume* Final Volume* Final Volume* Final Volume* 7.5 9.7 9.0 7.8 3.9 Dilution Charts

1003 1015 1003 727 451 991 685 547 643 703 312 225 394 291 475 372 270 417 234 117 mL mL mL mL

26.0 20.0 15.0 10.5 28.0 25.5 21.5 17.5 14.5 28.0 20.0 11.0 28.0 23.0 17.0 Water Volume* Water Volume* Water Volume* Water Volume* fl oz fl oz fl oz fl oz 7.5 6.5 3.5 9.5 6.0 30 kcal/fl oz(Standarddilution) 780 600 450 315 840 765 645 525 435 840 600 330 840 690 510 225 200 100 285 180 mL mL mL mL

scoops scoops scoops scoops Neocate Powder Neocate Powder Neocate Powder Neocate Powder 34 kcal/fl oz 32 kcal/fl oz 28 kcal/fl oz 27 21 16 11 27 25 21 17 14 25 18 10 23 19 14 8 6 3 8 5

as, weighing powder 221 172 131 221 205 172 139 115 205 148 189 156 115 grams grams grams grams 90.2 82.0 65.6 49.2 24.6 65.6 41.0 † † † †

fl oz fl oz fl oz fl oz 31.5 24.2 18.2 12.7 33.5 30.6 25.7 20.9 17.3 33.1 24.0 13.0 32.7 26.8 19.8 11.1 Final Volume* Final Volume* Final Volume* Final Volume* 9.1 8.0 4.0 7.0

1004 944 727 547 382 917 772 628 520 992 715 391 980 805 595 334 274 240 120 210 mL mL mL mL 33 Charts Dilution Pediatrics Specialized 34 SPECIALIZED PEDIATRICS Neocate For household measures, seepage 26.Visit www.NutriciaLearningCenter for printabledilution chartsand theNeocate Mixing Tool. displaces gram scaleprovides greatestaccuracy. 1level,unpacked scoopyields8.2grams powderandprovides37.64 kcal.1gramprovides4.59 kcaland † *This chartassumes 1floz=30mL. Water volumesare exact,butfinalvolumeof preparedformulamayvary slightly. Scoops should belevelandunpacked.While thescoopsNutriciaprovides arevalidatedforuse withNutriciaformul Water Volume* Water Volume*

Water Volume* 29.0 21.0 15.0 29.0 20.0 15.0 10.0 28.0 20.0 15.0 10.0 29.0 21.0 14.0 Water Volume* fl oz fl oz fl oz fl oz 5.5 9.0 4.5 5.0 5.0 9.5 ~0.71 165 870 630 450 270 135 870 600 450 300 150 840 600 450 300 150 870 630 420 285 mL ® mL mL mL mL JuniorwithPrebiotics,Vanilla water. Neocate Powder scoops scoops scoops scoops Neocate Powder Neocate Powder Neocate Powder 26 kcal/fl oz 24 kcal/fl oz 22 kcal/fl oz 20 kcal/fl oz 19 14 10 17 12 22 16 12 21 15 10 4 6 3 9 6 3 8 4 7

156 115 139 180 131 172 123 grams grams grams grams 32.8 82.0 49.2 24.6 98.4 73.8 49.2 24.6 98.4 65.6 32.8 82.0 57.4 †

† † †

Final Volume* fl oz fl oz fl oz fl oz 32.7 23.7 16.9 10.2 32.3 22.3 16.7 11.2 32.3 23.1 17.3 11.6 33.1 23.9 15.9 10.9 Final Volume* Final Volume* Final Volume* 6.3 5.1 5.6 5.8 Dilution Charts 188 981 712 508 305 152 969 670 502 335 167 968 693 520 347 173 992 717 478 326 mL mL mL mL

Water Volume* Water Volume* Water Volume* 28.0 20.0 15.5 10.0 30.0 26.5 22.5 18.5 15.5 28.0 21.0 14.0 28.0 21.0 14.0 Water Volume* fl oz fl oz fl oz fl oz 5.5 7.5 4.0 7.0 3.5 30 kcal/fl oz(Standarddilution) 840 600 465 300 165 900 795 675 555 465 840 630 420 225 120 840 630 420 210 105 mL mL mL mL Neocate Powder scoops scoops scoops scoops Neocate Powder Neocate Powder Neocate Powder 34 kcal/fl oz 32 kcal/fl oz 28 kcal/fl oz 31 22 17 11 31 27 23 19 16 26 20 13 24 18 12 6 7 4 6 3

254 180 139 254 221 189 156 131 213 164 107 197 148 grams grams grams grams 90.2 49.2 57.4 32.8 98.4 49.2 24.6 †

as, weighing powder usinga † † †

Final Volume* fl oz fl oz fl oz fl oz 34.0 24.3 18.8 12.1 36.0 31.7 27.0 22.2 18.6 33.0 25.0 16.5 32.7 24.5 16.3 Final Volume* Final Volume* Final Volume* 6.7 9.0 5.0 8.2 4.1

1020 1080 200 270 150 245 122 728 564 364 952 809 666 558 991 750 496 980 735 490 mL mL mL mL Specialized Pediatrics Dilution Charts Dilution Pediatrics Specialized For household measures, seepage 26.Visit www.NutriciaLearningCenter for printabledilution chartsand theNeocate Mixing Tool. 4.69 kcal anddisplaces ~0.71mL water. using agram scale providesgreatestaccuracy. 1level,unpacked scoopyields8.0grams powderandprovides37.5 kcal.1gramprovides † *This chartassumes 1floz=30mL. Water volumesare exact,butfinalvolumeof preparedformulamayvary slightly. Scoops should belevelandunpacked.While thescoopsNutriciaprovides arevalidatedforuse withNutriciaformul Neocate

28.0 20.0 10.0 29.0 22.0 12.5 29.0 20.0 12.0 32.0 22.0 15.0 Water Volume* Water Volume* Water Volume* Water Volume* fl oz fl oz fl oz fl oz 7.5 2.5 9.5 5.5 7.5 3.0 8.5 5.0 840 600 300 225 870 660 375 285 165 870 600 360 225 960 660 450 255 150 ® mL mL mL mL 75 90 JuniorwithPrebiotics,Strawberry scoops scoops scoops scoops Neocate Powder Neocate Powder Neocate Powder Neocate Powder 26 kcal/fl oz 24 kcal/fl oz 22 kcal/fl oz 20 kcal/fl oz 22 16 21 16 19 13 19 13 8 6 2 9 7 4 8 5 2 9 5 3

176 128 168 128 152 104 152 104 grams grams grams grams 64.0 48.0 16.0 72.0 56.0 32.0 64.0 40.0 16.0 72.0 40.0 24.0 † † † †

fl oz fl oz fl oz fl oz 32.2 23.0 33.0 25.0 32.6 22.5 35.6 24.5 11.5 14.2 10.8 13.5 16.7 Final Volume* Final Volume* Final Volume* Final Volume* 8.6 2.9 6.3 8.4 3.4 9.4 5.6 Dilution Charts

1068 965 691 989 751 978 674 734 345 259 426 325 188 405 253 101 501 283 167 mL mL mL mL 86

26.5 20.0 15.5 10.0 34.5 29.5 24.5 19.5 15.5 28.0 21.0 11.5 28.0 22.0 10.5 Water Volume* Water Volume* Water Volume* Water Volume* fl oz fl oz fl oz fl oz 5.5 7.5 4.0 7.0 3.5 1035 30 kcal/fl oz(Standarddilution) 795 600 465 300 885 735 585 465 840 630 345 840 660 315 165 225 120 210 105 mL mL mL mL

scoops scoops scoops scoops Neocate Powder Neocate Powder Neocate Powder Neocate Powder 34 kcal/fl oz 32 kcal/fl oz 28 kcal/fl oz 29 22 17 11 35 30 25 20 16 26 20 11 24 19 9 6 7 4 6 3

as, weighing powder 232 176 136 280 240 200 160 128 208 160 192 152 grams grams grams grams 88.0 88.0 72.0 48.0 56.0 32.0 48.0 24.0 † † † †

fl oz fl oz fl oz fl oz 32.0 24.2 18.7 12.1 41.1 35.2 29.2 23.3 18.5 32.9 25.0 13.6 32.5 25.6 12.2 Final Volume* Final Volume* Final Volume* Final Volume* 6.6 9.0 5.0 8.1 4.1

1234 1055 960 725 562 362 877 699 556 988 744 407 976 768 366 199 265 143 244 122 mL mL mL mL 35 Charts Dilution Pediatrics Specialized 36 SPECIALIZED PEDIATRICS Neocate For household measures, seepage 26.Visit www.NutriciaLearningCenter for printabledilution chartsand theNeocate Mixing Tool. displaces gram scaleprovides greatestaccuracy. 1level,unpacked scoopyields8.2grams powderandprovides37.0 kcal.1gramprovides4.51 kcaland † *This chartassumes 1floz=30mL. Water volumesare exact,butfinalvolumeof preparedformulamayvary slightly. Scoops should belevelandunpacked.While thescoopsNutriciaprovides arevalidatedforuse withNutriciaformul Water Volume* Water Volume*

Water Volume* 28.0 19.0 12.0 30.0 20.0 15.0 10.0 28.0 21.0 16.0 11.0 28.0 19.0 15.0 Water Volume* fl oz fl oz fl oz fl oz 4.0 6.0 3.0 5.0 8.5 8.0 ~0.72 120 840 570 360 180 900 600 450 300 150 840 630 480 330 255 840 570 450 240 mL ® mL mL mL mL 90 Junior, ChocolateandTropical water. Neocate Powder scoops scoops scoops scoops Neocate Powder Neocate Powder Neocate Powder 26 kcal/fl oz 24 kcal/fl oz 22 kcal/fl oz 20 kcal/fl oz 19 13 18 12 23 17 13 21 14 11 3 8 4 2 9 6 3 9 7 6

156 107 148 189 139 107 172 115 grams grams grams grams 24.6 65.6 32.8 16.4 98.4 73.8 49.2 24.6 73.8 57.4 90.2 49.2 †

† † †

Final Volume* fl oz fl oz fl oz fl oz 31.7 21.6 13.6 33.5 22.4 16.8 11.2 32.5 24.3 18.6 12.8 32.1 21.8 17.2 Final Volume* Final Volume* Final Volume* 4.6 6.8 3.4 5.6 9.9 9.2 Dilution Charts 1006 138 952 647 407 204 102 671 503 335 168 976 730 557 383 296 964 653 515 275 mL mL mL mL

Water Volume* Water Volume* Water Volume* 27.0 22.0 15.0 28.0 20.0 15.5 12.5 28.0 20.0 11.5 27.0 20.0 16.0 12.5 Water Volume* fl oz fl oz fl oz fl oz 9.0 4.5 9.5 7.0 4.0 8.0 30 kcal/fl oz(Standarddilution) 810 660 450 270 135 840 600 465 375 285 840 600 345 210 120 810 600 480 375 240 mL mL mL mL Neocate Powder scoops scoops scoops scoops Neocate Powder Neocate Powder Neocate Powder 34 kcal/fl oz 32 kcal/fl oz 28 kcal/fl oz 30 25 17 10 29 21 16 13 10 27 20 11 24 18 14 11 5 7 4 7

246 205 139 238 172 131 107 221 164 197 148 115 grams grams grams grams 82.0 41.0 82.0 90.2 57.4 32.8 90.2 57.4 †

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37 Charts Dilution Pediatrics Specialized 38 SPECIALIZED PEDIATRICS allergies, andrelated dietisindicated. GIandallergicconditions forwhichanaminoacid-based management ofcowmilkallergy, fordietary ** Neocateisanaminoacid-basedformula multiplefoodprotein systemic conditions,ofteninconjunctionwithtubefeedingand/ hydrocephalus); respiratory (lungdisease,tracheostomy, aspiration); cardiac (congenitaldisease); heart andother esophageal atresia, tracheoesophageal fistula);neurological conditions(suchasseizures, intraventricular hemorrhage, multiple systems,includingcongenitalgastrointestinal anomaliesandGIsurgeries (suchasnecrotizing enterocolitis, * Aretrospective review identifiedcasestudiesof patients onprimaryorsolesource covering diagnoses nutritionwith prematurity. Neocate** formulasare intendedforuseunder medicalsupervision. multiple diagnosesandintestinaldisease,* withtubefeedingand/or especiallyincombination ahistoryof Neocate isusedasaprimaryorsolesource complex ofnutritionforpatientswith systemicdiseaseinvolving Serum levels ofmicronutrients, shouldberoutinely phosphorus, particularly monitored byclinicianswhen Update onMonitoringMicronutrients or ahistoryofprematurity. METABOLICS

Find more information and resources on these and all of our products at www.NutriciaLearningCenter.com 3939 PKU Periflex Early Years

Nutrition Information: Ingredients: Per 10 g Per 10 g Corn Syrup Solids, Refined Vegetable ® Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Oils (High Oleic Sunflower, Soy, PKU Periflex Early Years Calories 473 350 Vitamin A, IU (mcg RE) 1305.(392) 967.(290) Non-hydrogenated Coconut, Canola, Protein Equivalent,g 13.5 10.0 Vitamin D3, IU (mcg) 348.(8.7) 258.(6.4) Sunflower), Galacto-oligosaccharides A phenylalanine-free powdered infant formula with iron, for the dietary Fat, g 23.0 17.0 Vitamin E, IU (mg α-TE) 10.9 (7.3) 8.1 (5.4) (GOS) Dried Syrup (from milk), L-Arginine management of phenylketonuria (PKU). Contains DHA and ARA, and a unique Saturated, g 7.5 5.6 Vitamin K, mcg 38.0 28.1 L-Aspartate, L-Leucine, L-Lysine Acetate, blend of prebiotic fiber. Monounsaturated, g 9.4 7.0 Thiamin, mcg 640 474 L-Tyrosine, L-Glutamine, L-Proline, Polyunsaturated, g 5.0 3.7 Riboflavin, mcg 500 370 Tricalcium Phosphate, L-Valine, CAEM DHA, mg 70.0 51.9 Vitamin B6, mcg 500 370 (an emulsifier), Glycine, L-Isoleucine, ARA, mg 140 104 Vitamin B12, mcg 1.2 0.89 L-Threonine, L-Serine, L-Histidine, Main Features: Indications: Linoleic Acid,mg 3500 2593 Niacin, mcg 2200 1630 L-Alanine, Potassium Chloride, Fructo- Carbohydrate, g 53.0 39.3 Folic Acid, mcg 55.0 40.7 oligosaccharides (FOS), Tripotassium • Phenylalanine-free powdered infant • Phenylketonuria Fiber, g 5.3 3.9 Pantothenic Acid, mcg 2800 2074 Citrate, Sodium Phosphate Dibasic, GOS, g 4.7 3.5 Biotin, mcg 18.2 13.5 L-Cystine, M. Alpina Oil*, L-Tryptophan, formula with iron FOS, g 0.55 0.41 For details on administration and household measurements, please Vitamin C, mg 49.0 36.3 Choline Bitartrate, L-Methionine, • Includes DHA & ARA Amino Acids, g Choline, mg 91.0 67.4 Magnesium Acetate, Magnesium see pages 124-136. L-Alanine 0.62 0.46 • Contains a prebiotic fiber blend Inositol, mg 98.0 72.6 Aspartate, C. Cohnii Oil**, Sodium L-Arginine 1.09 0.81 Minerals Chloride, M-Inositol, L-Ascorbic Acid, • Unflavored powder L-Aspartic Acid 1.02 0.76 Calcium, mg 371 275 Ferrous Sulfate, Taurine, Zinc Sulfate, Ordering/Reimbursement Information: L-Cystine 0.41 0.30 • Contains a balanced mixture of all other Phosphorus, mg 270 200 L-Carnitine, DL-alpha Tocopheryl Acetate, Product Reimbursement HCPCS Product Calories L-Glutamine 1.28 0.95 Magnesium, mg 52.5 38.9 Calcium D-Pantothenate, Niacinamide, essential and non-essential amino acids, Code Code Code* Packaging Per Can Glycine 0.96 0.71 Iron, mg 7.3 5.4 Ascorbyl Palmitate, Manganese Sulfate, carbohydrates, fat, vitamins, minerals 90164 49735-0101-64 B4162 6 x 400 g (14.1 oz) 1892 L-Histidine 0.63 0.47 Zinc, mg 5.2 3.9 Cupric Sulfate, Thiamin Chloride and trace elements L-Isoleucine 0.96 0.71 Manganese, mcg 390 289 Hydrochloride, Pyridoxine Hydrochloride, L-Leucine 1.65 1.2 Copper, mcg 390 289 Riboflavin, Vitamin A Acetate, DL-alpha • Provides 13.5 g of protein equivalent L-Lysine 1.11 0.82 Iodine, mcg 82.5 61.1 WIC‡: Contact your state WIC For more reimbursement Tocopherol, Mixed Tocopherols, Potassium per 100 g of powder L-Methionine 0.26 0.19 Molybdenum, mcg 10.9 8.1 Iodide, Chromium Chloride, Folic Acid, office to determine availability. information see page 195. • Osmolality (at 0.7 kcal/mL): L-Phenylalanine Nil Added Nil Added Chromium, mcg 12.5 9.3 Phylloquinone, Sodium Selenite, Sodium L-Proline 1.1 0.81 Selenium, mcg 14.1 10.4 Molybdate, D-Biotin, Vitamin D3, 380 mOsm/kg L-Serine 0.72 0.53 Sodium, mg 171 127 Cyanocobalamin Based on dilution of 5 g powder L-Threonine 0.81 0.6 Potassium, mg 454 336 (1 unpacked level scoop) to 1 fl oz L-Tryptophan 0.31 0.23 Chloride, mg 321 238 CONTAINS: Soy Oil, Coconut Oil, Milk. L-Tyrosine 1.44 1.07 Metabolics (30 mL) water L-Valine 1.05 0.78 * A source of Arachidonic Acid (ARA) • Displacement: 0.75 mL/g L-Carnitine 0.01 0.01 ** A source of Docosahexaenoic Acid Taurine 0.02 0.01 (DHA) Contains GOS/FOS 0.8 g per 100 mL 40 * S9435 = For individuals who submit their bills to insurance on their own. 41 PKU Periflex Junior Plus

Nutrition Information: Ingredients: Per 10 g Per 10 g Corn Syrup Solids, Refined Vegetable Oils ® Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent (High Oleic Sunflower, Canola, Medium PKU Periflex Junior Plus Calories (flavors) 385.(377) 138.(135) Vitamin A, IU (mcg RE) 1399.(420) 500.(150) Chain Triglycerides (Palm Kernel and/or Protein Equivalent, g 28 10 Vitamin D , IU (mcg) 840.(21.0) 300.(7.5) Coconut Oil), Sunflower), L-Alanine, Glycine, A phenylalanine-free, powdered medical food for the dietary 3 Fructo-oligosaccharides, L-Glutamine, Fat, g 12.5 4.5 Vitamin E, IU (mg α-TE) 12.5 (8.4) 4.5 (3) Inulin, Corn Starch, L-Tyrosine, Calcium management of phenylketonuria (PKU) in children over 1 year of age. Saturated, g 2 0.71 Vitamin K, mcg 14 5 Phosphate Dibasic, L-Lysine Acetate, Monounsaturated, g 8.2 2.9 Thiamin, mg 0.93 0.33 L-Threonine, Microcrystalline Cellulose, L-Leucine, L-Proline, Artificial Flavor, Gum Polyunsaturated, g 1.8 0.64 Riboflavin, mg 0.73 0.26 Arabic, L-Cystine, L-Arginine, L-Valine, DHA, mg 180 64.3 Vitamin B6, mg 0.73 0.26 L-Isoleucine, Tripotassium Citrate, Trisodium Citrate, L-Serine, Calcium Chloride, Carbohydrate, g (flavors) 43.2 (41.2) 15.4 (14.7) 12 Main Features: Indications: Vitamin B , mcg 1.3 0.46 L-Methionine, L-Histidine, Maltodextrin, Fiber, g 11.2 4 Niacin, mg 2.0 0.71 Choline Bitartrate, Magnesium Hydrogen Soluble 8 2.9 Folic Acid, mcg 210 75 Phosphate, Magnesium L-Aspartate, CAEM • Phenylalanine-free • Phenylketonuria (an emulsifier), C. Cohnii Oil*, L-Tryptophan, Insoluble 3.2 1.1 • Contains a balanced mixture of all Pantothenic Acid, mg 4.2 1.5 Tricalcium Citrate, L-Ascorbic Acid, Soy Amino Acids, g Biotin, mcg 11.2 4 Fiber, M-Inositol, Taurine, Ferrous Sulfate, other essential and non-essential For details on administration and household measurements, please L-Alanine 4.76 1.7 Vitamin C, mg 42 15 Sunflower Lecithin, L-Carnitine, Zinc amino acids, carbohydrate (including see pages 124-136. Sulfate, DL-alpha Tocopheryl Acetate, L-Arginine 1.74 0.62 Choline, mg 224 80 Calcium D-Pantothenate, Manganese a multi-fiber blend), fat (including L-Aspartic Acid 0.42 0.15 Inositol, mg 56 20 Sulfate, Niacinamide, Cupric Sulfate, DHA), vitamins, minerals and trace Ordering/Reimbursement Information: L-Cystine 1.9 0.68 Minerals Thiamin Chloride Hydrochloride, Pyridoxine Product Reimbursement HCPCS Product Calories Hydrochloride, Riboflavin, Vitamin A elements L-Glutamine 3.36 1.2 Calcium, mg 980 350 Acetate, Ascorbyl Palmitate, Folic Acid, Code Code Code* Packaging Per Can • Age-appropriate DRI formulation Glycine 4.59 1.6 Phosphorus, mg 641 228.9 Potassium Iodide, Mixed Tocopherols, 89477 - Plain 49735-0194-77 B4162 6 x 400 g (14.1 oz) 1540 L-Histidine 0.7 0.25 Sodium Molybdate, Sodium Selenite, • Provides 28 g protein equivalent and Magnesium, mg 113 40.4 Chromium Chloride, DL-alpha Tocopherol, 89478 - Vanilla 49735-0194-78 B4162 6 x 400 g (14.1 oz) 1508 L-Isoleucine 1.4 0.50 Iron, mg 10 3.6 Vitamin D , Phylloquinone, D-Biotin, 12.5 g fat per 100 g of powder 3 89474 - Berry 49735-0194-74 B4162 6 x 400 g (14.1 oz) 1508 L-Leucine 2.24 0.80 Zinc, mg 4.9 1.75 Cyanocobalamin • Available in plain, vanilla, berry and Berry version also contains: Natural Flavor, 89476 - Orange 49735-0194-76 B4162 6 x 400 g (14.1 oz) 1508 L-Lysine 1.85 0.66 Manganese, mg 0.92 0.33 Malic Acid, Artificial Sweetener: Sucralose, orange L-Methionine 0.73 0.26 Copper, mcg 560 200 Artificial Color (Beet Red). L-Phenylalanine Nil Added Nil Added Iodine, mcg 139 49.6 Vanilla version also contains: Artificial • Osmolality (at 1.1 kcal/mL): WIC‡: Contact your state WIC For more reimbursement Sweetener: Sucralose. L-Proline 2.24 0.80 Molybdenum, mcg 25.5 9.1 1340 mOsm/kg office to determine availability. information see page 195. Orange version also contains: Citric Acid, Based on dilution of 36 g powder L-Serine 1.2 0.43 Chromium, mcg 10.2 3.6 Natural Flavor, Artificial Sweetener: L-Threonine 2.52 0.90 Selenium, mcg 28.2 10.1 Sucralose, Artificial Colors (Beta Carotene, (approx 4 scoops) to 3.5 fl oz Beet Red). Metabolics (100 mL) water L-Tryptophan 0.42 0.15 Sodium, mg 280 100 L-Tyrosine 2.66 1.0 Potassium, mg 445 158.9 CONTAINS: Soy, Coconut Oil • Displacement: 0.72 mL/g L-Valine 1.68 0.60 Chloride, mg 406 145 *A source of Docosahexaenoic Acid (DHA) L-Carnitine 0.02 0.01 42 * S9435 = For individuals who submit their bills to insurance on their own. 43 Taurine 0.05 0.02 Periflex Advance NEW LOOK SPRING Nutrition Information: Ingredients: 2017 ® Per 10 g Per 10 g Corn Syrup Solids, High Oleic Safflower Periflex Advance Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Oil, Canola Oil, L-Lysine, L-Aspartate, Calories (orange) 385 (369) 110 (105.4) Vitamin A, IU (mcg RE) 1951.(586) 557.4 (167.4) L-Glutamine, L -Leucine, L-Tyrosine, A phenylalanine-free, powdered medical food for the dietary management of Protein Equivalent, g 35 10 Vitamin D3, IU (mcg) 292.(7.3) 83.4 (2.1) L-Proline, L -Arginine, L-Valine, Glycine, phenylketonuria (PKU) in older children and adults, including pregnant women Fat, g 12.6 3.6 Vitamin E, IU (mg α-TE) 16.2 (10.9) 4.6 (3.1) L-Isoleucine, Magnesium Hydrogen Phosphate, L-Threonine, and 2% or and women of child-bearing age. Saturated, g 1.4 0.4 Vitamin K, mcg 71.8 20.5 less of each of the following: L-Serine, Monounsaturated, g 7.9 2.3 Thiamin, mg 0.8 0.2 Disodium Hydrogen Phosphate, Polyunsaturated, g 2.7 0.8 Riboflavin, mg 0.85 0.2 L-Histidine, L-Alanine, Potassium Main Features: Indications: Linoleic Acid, mg 2064 590 Vitamin B6, mg 1.4 0.4 Chloride, Choline Hydrogen Tartrate, • Phenylalanine-free • Phenylketonuria α-Linolenic Acid, mg 535 153 Vitamin B12, mcg 2.7 0.8 L-Cystine, L-Tryptophan, Sugar, Carbohydrate, g (orange) 33 (29) 9.4 (8.3) Niacin, mg 5 1.4 L-Methionine, Fractionated Coconut Oil, • Contains a balanced mixture of all other For details on administration and household measurements, Amino Acids, g Folic Acid, mcg 430 122.9 L-Lysine Acetate, CAEM (An Emulsifier), essential and non-essential amino acids, Tripotassium Citrate, Taurine, L-Ascorbic please see pages 124-136. L-Alanine 1.4 0.40 Pantothenic Acid, mg 4.3 1.2 carbohydrate, fat, vitamins, minerals Acid, M-Inositol, Ferrous Sulfate, L-Arginine 2.6 0.74 Biotin, mcg 21.4 6.1 L-Carnitine, Zinc Sulfate, DL-Alpha and trace elements L-Aspartic Acid 2.5 0.71 Vitamin C, mg 54.3 15.5 Tocopherol Acetate, Manganese Sulfate, • Periflex Advance provides 35 g of L-Cystine 0.96 0.27 Choline, mg 376 107.4 Niacinamide, Calcium D-Panthothenate, protein equivalent and 12.6 g of fat Glycine 2.5 0.71 Inositol, mg 70 20 Cupric Sulfate, Pyridoxine Hydrochloride, per 100 g of powder Ordering/Reimbursement Information: L-Histidine 1.5 0.43 Minerals Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, • Meets protein requirements in lower Product Reimbursement HCPCS Product Calories L-Isoleucine 2.4 0.69 Calcium, mg 1035 296 Code Code Code* Packaging Per Can Potassium Iodide, Chromium Chloride, volume when compared to L-Leucine 4.0 1.14 Phosphorus, mg 995 284 Sodium Selenite, Sodium Molybdate, 118305 - Unflavored 49735-0183-05 B4157 or 6 x 454 g (1 lb) 1748 L-Lysine 3.1 0.89 Magnesium, mg 268 76.6 Periflex Junior Plus Phylloquinone, D-Biotin, Vitamin D3, B4162 L-Methionine 0.64 0.18 Iron, mg 12.9 3.7 • Pleasant taste, smell and texture Cyanocobalamin. 118307 - Orange 49735-0183-07 B4157 or 6 x 454 g (1 lb) 1675 L-Phenylalanine Nil Added Nil Added Zinc, mg 7.9 2.3 Unflavored version also contains: B4162 • Available in unflavored and orange L-Proline 2.8 0.80 Manganese, mg 1.6 0.5 Tricalcium Citrate and 2% or less of • Osmolality (mOsm/kg): L-Serine 1.8 0.51 Copper, mcg 720 206 Tricalcium Phosphate. ‡ Orange flavored version also contains: Dilution Unflavored Orange WIC : Contact your state WIC For more reimbursement L-Threonine 1.9 0.54 Iodine, mcg 115 32.9 office to determine availability. information see page 195. Artificial Flavor, Citric Acid, Tricalcium 1 to 5 830 890 L-Tryptophan 0.78 0.22 Molybdenum, mcg 32.4 9.3 Phosphate and 2% or less of each of the 1 to 4 1060 1100 L-Tyrosine 3.5 1.00 Chromium, mcg 22.8 6.5 following: Tricalcium Citrate, Guar Gum, Metabolics • Displacement: 0.6 mL/g L-Valine 2.5 0.71 Selenium, mcg 50.8 14.5 Xanthan Gum, Artificial Sweetener: L-Carnitine 0.03 0.01 Sodium, mg 490 140 Sucralose, Artificial Colors (Beet Red, Taurine 0.12 0.03 Potassium, mg 613 175 Beta Carotene). * S9435 = For individuals who submit their bills to insurance on their own. 44 L-Glutamine 4.3 1.23 Chloride, mg 490 140 CONTAINS: Coconut Oil. 45 Periflex LQ

Nutrition Information: Ingredients: ® Per 10 g Per 10 g Periflex LQ Nutrients Per 250 mL Protein Equivalent Vitamins Per 250 mL Protein Equivalent Water, Sugar, and less than 2% of each of Calories 160 107 Vitamin A, IU (mcg RE) 833 (250) 555.(167) the following: Calcium Glycerophosphate, A phenylalanine-free, ready-to-drink medical food for the dietary Protein Equivalent, g 15 10 Vitamin D3, IU (mcg) 130 (3.3) 87 (2.2) High Oleic Sunflower Oil, L-Lysine management of phenylketonuria (PKU) in children and adults, Fat, g 5 3.3 Vitamin E, IU (mg α-TE) 7 (4.8) 4.7 (3.2) Acetate, Canola Oil, L-Leucine, L-Tyrosine, Artificial Flavor, L-Proline, L-Arginine, Saturated, g 0.75 0.5 Vitamin K, mcg 30.8 21 including pregnant women and women of child-bearing age. L-Valine, Glycine, L-Aspartic Acid, Monounsaturated, g 3 2 Thiamin, mg 0.35 0.23 L-Isoleucine, Micro-Crystalline Cellulose, Polyunsaturated, g 1 0.7 Riboflavin, mg 0.38 0.25 Citric Acid, L-Threonine, L-Serine, Carbohydrate, g 13.8 9.2 Vitamin B6, mg 0.6 0.4 Magnesium Acetate, Tripotassium Amino Acids, g Vitamin B , mcg 1.2 0.8 Citrate, L-Histidine, L-Alanine, L-Cystine, Main Features: Indications: 12 L-Alanine 0.68 0.45 Niacin, mg 2.1 1.4 Choline Hydrogen Tartrate, N-Acetyl, L-Methionine, Sodium Chloride, • Phenylalanine-free • Phenylketonuria L-Arginine 1.28 0.85 Folic Acid, mcg 184 123 L-Tryptophan, Trisodium Citrate, L-Aspartic Acid 1.2 0.80 Pantothenic Acid, mg 1.9 • Contains a balanced mixture of other 1.3 Soybean Oil, L-Ascorbic Acid, Diacetyl amino acids, carbohydrate, vitamins L-Cystine 0.48 0.32 Biotin, mcg 9.3 6.2 Tartaric Acid Esters of Monoglycerides, and minerals For details on administration, please see pages 124-136. Glycine 1.23 0.82 Vitamin C, mg 23.3 16 Mono- and Diglycerides, Guar Gum, L-Histidine 0.73 0.49 Choline, mg 161 107 Xanthan Gum, Artificial Sweetener: • Can easily be used along with or in L-Isoleucine 1.13 0.75 Inositol, mg 30 20 Acesulfame Potassium, Taurine, place of PKU Periflex Junior Plus or L-Leucine 1.95 1.30 Minerals M-Inositol, Ferrous Sulphate, Tricalcium Phosphate, Carnitine, Zinc Advance Ordering/Reimbursement Information: L-Lysine 1.5 1.00 Calcium, mg 400 267 Sulfate, DL-Alpha Tocopherol Acetate, • No measuring or mixing Product Reimbursement HCPCS Product Calories Per L-Methionine 0.33 0.22 Phosphorus, mg 288 192 Code Code Code* Packaging Container Niacinamide, Manganese Sulphate, L-Phenylalanine Nil Added Nil Added Magnesium, mg 114 76 Calcium-D-Pantothenate, Cupric Sulfate, • Great addition to any daily PKU 80177 - Orange 49735-0125-51 B4162 or 18 x 250 mL (8.5 fl oz) 160 L-Proline 1.38 0.92 Iron, mg 5.5 3.7 Pyridoxine Hydrochloride, Thiamin diet plan Créme B4157 L-Serine 0.85 0.57 Zinc, mg 3.5 2 Chloride Hydrochloride, Riboflavin, • Periflex LQ provides 15 g of protein 80176 - Berry 49735-0125-24 B4162 or 18 x 250 mL (8.5 fl oz) 160 L-Threonine 0.95 0.63 Manganese, mg 0.7 0.5 Vitamin A Acetate, Potassium Iodide, Créme B4157 Chromium Chloride, Sodium Selenite, equivalent and 5 g of fat per 250 mL L-Tryptophan 0.38 0.25 Copper, mcg 310 207 Sodium Molybdate, Phylloquinone, container L-Tyrosine 1.73 1.15 Iodine, mcg 49 33 ‡ D-Biotin, Cholecalciferol, Folic Acid, • Available in orange créme and WIC : Contact your state WIC For more reimbursement L-Valine 1.25 0.83 Molybdenum, mcg 14 9 Cyanocobalamin. office to determine availability. information see page 195. L-Carnitine 0.01 0.01 Chromium, mcg 9.8 7 berry créme flavors CONTAINS: Soybean Oil. Taurine 0.08 0.05 Selenium, mcg 21.8 15 Metabolics • Osmolality (at 0.64 kcal/mL): L-Glutamine Nil Added Nil Added Sodium, mg 210 140 Orange 1080 mOsm/kg Potassium, mg 263 175 Berry 1030 mOsm/kg Chloride, mg 210 140 46 • Free water: 84% * S9435 = For individuals who submit their bills to insurance on their own. 47 PhenylAde GMP Drink Mix PhenylAde® GMP Drink Mix Nutrition Information: Ingredients: Per 10 g Protein Equivalent Per 10 g Protein Equivalent Whey Protein Concentrate* (FROM MILK), A phenylalanine-low, powdered medical food containing a balanced mix Nutrients Per 100 g (1 scoop/pouch) Vitamins Per 100 g (1 scoop/pouch) Refined Vegetable Oils (Canola, Safflower, of glycomacropeptide (GMP), essential and non-essential amino acids, Calories 396 132 Vitamin A, IU (mcg RE) 2040.(765) 680.(255) Coconut and Soybean), Modified Corn Protein Equivalent, g 30.0 10.0 Vitamin D3, IU (mcg) 900.(22.5) 300.(7.5) Starch, Dextrin, Maltodextrin, L-Tyrosine, carbohydrates (including fiber), fat (including docosahexaenoic acid Phenylalanine, mg 46.0 15.3 Vitamin E, IU (mg α-TE) 22.8 (15.3) 7.6.(5.1) Tricalcium Phosphate. Contains 2 % or less (DHA)), vitamins, minerals and trace elements. Fat, g 12.0 4.0 Vitamin K, mcg 72 24 of the following: L-Glycine, Magnesium Saturated, g 2.8 0.93 Thiamin, mg 1.8 0.6 Phosphate, L-Leucine, L-Histidine, Monounsaturated, g 6.3 2.1 Riboflavin, mg 1.8 0.6 L-Arginine, Potassium Chloride, L-Cystine, Choline Bitartrate, Dicalcium Phosphate, Main Features: Polyunsaturated, g 2.5 0.84 Vitamin B6, mg 1.7 0.56 Indications: L-Tryptophan, C. Cohnii Oil**, Glucose DHA, mg 155 51.6 Vitamin B12, mcg 3.6 1.2 • Low in Phenylalanine Syrup Solids, Potassium Citrate, Ascorbyl • Phenylketonuria Carbohydrate, g 42.0 14.0 Niacin, mg 15.0 5.0 • Suitable for individuals with PKU Palmitate, Mixed Tocopherols, Silicon Fiber, g 4.5 1.5 Folic Acid, mcg 360 120 Dioxide, Rosemary Extract, Sodium over 1 year of age For details on administration, please see pages 124-136. Amino Acids, g Pantothenic Acid, mg 4.8 1.6 Chloride, Ascorbic Acid, Taurine, Inositol, • Complete with essential vitamins L-Alanine 1.3 0.44 Biotin, mcg 36 12 Mannitol, Vitamin E Acetate, Ferrous and minerals L-Arginine 1.4 0.47 Vitamin C, mg 72 24 Sulfate, L-Carnitine, Glycerol Mono and Ordering/Reimbursement Information: 100 • Contains a source of DHA L-Aspartic acid 1.9 0.63 Choline, mg 300 Distearate, High Oleic Sunflower Oil, L-Cystine 0.93 0.31 Inositol, mg 60 20 Sodium Polyphosphate, Sunflower Lecithin, • 1.5 grams of soluble fiber per each Product Reimbursement HCPCS Product Calories Per L-Glutamic acid 4.1 1.4 Minerals Niacinamide, Zinc Oxide, Sodium Ascorbate, Code Code Code* Packaging Can/Pouch 10 g PE serving L-Glycine 2.2 0.75 Calcium, mg 1050 350 Vitamin D3, Vitamin A Palmitate, Copper • PhenylAde GMP Drink Mix provides CANS L-Histidine 1.5 0.49 Phosphorus, mg 945 315 Gluconate, Manganese Sulfate, D-Calcium 6832 - Vanilla 49735-0168-32 B4157 or B4162 4 x 400 g (14.1 oz) 1584 L-Isoleucine 2.3 0.76 Magnesium, mg 252 84 Pantothenate, D-Biotin, Beta-Carotene, 30 g of protein equivalent and 12 g Thiamin Hydrochloride, Pyridoxine POUCHES L-Leucine 2.3 0.78 Iron, mg 13.2 4.4 of fat per 100 g of powder Hydrochloride, Riboflavin, Potassium 68324 - Vanilla 49735-0183-04 B4157 or B4162 16 x 33.3 g (1.2 oz) 132 L-Lysine 1.3 0.44 Zinc, mg 10.2 3.4 • Available in vanilla and original flavor Iodide, Vitamin K1, Sodium Selenite, Folic 114116 - Original 49735-0141-16 B4157 or B4162 16 x 33.3 g (1.2 oz) 132 L-Methionine 0.44 0.15 Manganese, mg 1.6 0.52 Acid, Vitamin B12, Chromium Chloride, • Available in cans and pouches L-Phenylalanine 0.05 0.02 Copper, mcg 1200 400 Sodium Molybdate. • Osmolality (at 0.73 kcal/mL): ‡ L-Proline 2.6 0.86 Iodine, mcg 135 45 WIC : Contact your state WIC For more reimbursement Original version also contains: Corn L-Serine 1.6 0.54 Molybdenum, mcg 54 18 460 mOsm/kg office to determine availability. information see page 195. Syrup Solids and 2% or less of Sugar, L-Threonine 3.7 1.2 12 Based on dilution of 33.3 g powder Chromium, mcg 36 Natural Flavors. 16 (1 scoop or 1 pouch) to 5 fl oz L-Tryptophan 0.72 0.24 Selenium, mcg 48 * S9435 = For individuals who submit their bills to insurance on their own. L-Tyrosine 3.7 1.2 Sodium, mg 465 155 Vanilla version also contains: Sugar, (150 mL) water Natural and Artificial Flavors. Metabolics L-Valine 1.8 0.61 Potassium, mg 1047 349 • Displacement: 0.9 mL/g L-Carnitine 0.04 0.01 Chloride, mg 569 190 CONTAINS: Milk, Soybean Oil, Coconut Oil. Taurine 0.09 0.03 *Contains 15.3 mg of phenylalanine/10 g protein equivalent 48 **A source of Docosahexaenoic Acid (DHA) 49 PhenylAde GMP Mix-In

Nutrition Information: Ingredients: Per 10 g Protein Per 10 g Protein Whey Protein Concentrate* (FROM ® Nutrients Per 100 g Equivalent (1 pouch) Minerals Per 100 g Equivalent (1 pouch) MILK), L-Tyrosine, Glycine, L-Leucine, PhenylAde GMP Mix-In Calories 334 42 Calcium, mg 32 4 L-Histidine, L-Arginine, Corn Syrup Protein Equivalent 80 10 Phosphorus, mg 320 40 Solids, L-Cystine. Contains 2 % or A powdered medical food, low in phenylalanine containing a balanced Fat, g <0.5 <0.5 Potassium, mg 1160 145 less of the following: L-Tryptophan, mix of glycomacropeptide (GMP), essential and non-essential amino Carbohydrate, g 2.7 <0.5 Sodium, mg 960 120 Refined Vegetable Oils (Canola, acids, some carbohydrates and fat. Amino Acids, g Safflower, Coconut and Soybean), L-Alanine, g 3.5 0.44 Silicon Dioxide, Taurine, Modified Corn Starch, Maltodextrin, L-Arginine, g 3.8 0.47 L-Carnitine, Ascorbyl Palmitate, L-Aspartic acid, g 5 0.63 Rosemary Extract, Mixed Tocopherols, L-Cystine, g 2.5 0.31 Tricalcium Phosphate. Main Features: Indications: L-Glutamic acid, g 11 1.4 • Low in Phenylalanine Glycine, g 5.9 0.75 *Contains 15.3 mg of • Phenylketonuria phenylalanine/10 g protein equivalent • Suitable for individuals with PKU L-Histidine, g 3.9 0.49 CONTAINS: Milk, Soybean Oil, over 1 year of age For details on administration, please see pages 124-136. L-Isoleucine, g 6 0.76 L-Leucine, g 6.2 0.78 Coconut Oil. • Provides 80 g protein equivalent per L-Lysine, g 3.5 0.44 100 g of powder L-Methionine, g 1.2 0.15 Note: Must be combined with an • Mixes easily with water, flavored Ordering/Reimbursement Information: L-Phenylalanine, g 0.12 0.02 appropriate vitamin & mineral L-Proline, g 6.8 0.86 supplement when taken as the sole drinks or other PKU formula source of PKU Medical Food. • Available in pouches only Product Reimbursement HCPCS Product Calories L-Serine, g 4.3 0.54 Code Code Code* Packaging Per Pouch L-Threonine, g 9.7 1.2 116130 49735-0111-61 B4155 20 x 12.5 g (0.44 oz) 42 L-Tryptophan, g 1.9 0.24 L-Tyrosine, g 9.8 1.2 L-Valine, g 4.8 0.61 WIC‡: Contact your state WIC For more reimbursement L-Carnitine, g 0.08 0.01 office to determine availability. information see page 195. Taurine, g 0.24 0.03 Metabolics

* S9435 = For individuals who submit their bills to insurance on their own.

50 51 PhenylAde Essential Drink Mix

® Nutrition Information: Ingredients: PhenylAde Essential Drink Mix Per 10 g Protein Per 10 g Protein Corn Syrup Solids, Modified Corn Starch, Equivalent Equivalent Canola Oil, Maltodextrin, Safflower Oil, A phenylalanine-free, powdered medical food for the dietary Nutrients Per 100 g (1 scoop/pouch) Vitamins Per 100 g (1 scoop/pouch) Dextrin, L-Asparagine Monohydrate, Calories 393 157 Vitamin A, IU (mcg RE) 1700 (637) 680 (255) L-Glutamine, L-Tyrosine, L-Lysine Acetate, management of phenylketonuria (PKU) in children and adults, including L-Alanine, L-Leucine, L-Serine. Contains Protein Equivalent, g 25 10 (25% as beta-carotene) pregnant women and women of child-bearing age. 2% or less of the following: L-Arginine, Fat, g 13 5 Vitamin D3, IU (mcg) 600 (15) 240 (6) Monocalcium Phosphate, L-Valine, Dicalcium Saturated, g 3 1.2 Vitamin E, IU (mg α-TE) 19 (12.7) 7.6 (5.1) Phosphate, Sodium Citrate, Glycine, L-Proline, Monounsaturated, g 6.8 2.7 Vitamin K, mcg 61 24 Potassium Citrate, Coconut Oil, Soybean Oil, L-Threonine, L-Isoleucine, Potassium Main Features: Indications: Polyunsaturated, g 2.8 1.1 Thiamin, mg 1.5 0.6 Chloride, L-Histidine, L-Methionine, Choline Linoleic Acid, mg 1936 774 Riboflavin, mg 1.5 0.6 Bitartrate, L-Tryptophan, Flaxseed Oil, • Phenylalanine-free • Phenylketonuria Magnesium Oxide, L-Cystine, Ascorbyl α-Linolenic Acid, mg 725 290 Vitamin B6, mg 1.4 0.56 Palmitate, Mixed Tocopherols, Rosemary • Complete with essential vitamins Vitamin B12, mcg 3.0 1.2 For details on administration and household measurements, please Carbohydrate, g 46 18 Extract, Silicon dioxide, Tricalcium Phosphate, and minerals see pages 124-136. Fiber, g 3.9 1.5 Niacin, mg 17 6.8 Sodium Chloride, Taurine, Ascorbic Acid, • 1.5 grams of soluble fiber Amino Acids, g Folic Acid, mcg 300 120 Inositol, Ferric Orthophosphate, Vitamin E L-Alanine 2.32 0.93 Pantothenic Acid, mg 4 1.6 Acetate, L-Carnitine, Niacinamide, Calcium per serving Ordering/Reimbursement Information: Phosphate, Zinc Oxide, Copper Gluconate, L-Arginine 1.97 0.79 Biotin, mcg 30 12 • PhenylAde Essential Drink Mix Vitamin K1, Vitamin D3, Vitamin A Palmitate, L-Asparagine 3.49 1.40 Vitamin C, mg 60 24 D-Calcium Pantothenate, Manganese provides 25 g of protein equivalent Product Reimbursement HCPCS Product Calories Per Code Code Code* Packaging Can/Pouch L-Cystine 0.34 0.14 Choline, mg 210 84 Sulfate, Mono- and Diglycerides, D-Biotin, and 13 g of fat per 100 g of powder Inositol, mg 50 20 Beta-carotene, Pyridoxine Hydrochloride, CANS L-Glutamine 3.89 1.56 Riboflavin, Thiamin Mononitrate, Potassium Minerals • Available in chocolate, vanilla, 9501 - Chocolate 00847-0950-12 B4157 or B4162 4 x 454 g (1 lb) 1784 Glycine 1.52 0.61 Iodide, Sodium Selenite, Folic Acid, Vitamin L-Histidine 0.63 0.25 Calcium, mg 822 329 B12, Chromium Chloride, Sodium Molybdate. orange creme, strawberry, 9502 - Vanilla 00847-0950-22 B4157 or B4162 4 x 454 g (1 lb) 1784 L-Isoleucine 1.04 0.42 Phosphorus, mg 788 315 CONTAINS: Coconut Oil, Soybean Oil. and unflavored 9503 - Orange Creme 00847-0950-32 B4157 or B4162 4 x 454 g (1 lb) 1784 L-Leucine 2.24 0.90 Magnesium, mg 210 84 Chocolate flavored version also contains: • Available in cans and pouches 9504 - Strawberry 00847-0950-42 B4157 or B4162 4 x 454 g (1 lb) 1784 L-Lysine 1.82 0.73 Iron, mg 11 4.4 Sugar, Natural and Artificial Flavor, and less • Osmolality (at 0.65 kcal/mL): 9508 - Unflavored 00847-0950-82 B4157 or B4162 4 x 454 g (1 lb) 1784 L-Methionine 0.61 0.24 Zinc, mg 10 4 than 2% of the following: FD&C Red#40, FD&C Yellow#5, FD&C Blue #2. 800 mOsm/kg POUCHES L-Phenylalanine Nil Added Nil Added Manganese, mg 1.3 0.52 95014 - Chocolate 00847-0950-14 B4157 or B4162 16 x 40 g (1.4 oz) 157 L-Proline 1.52 0.61 Copper, mcg 1000 400 Vanilla flavored version also contains: Sugar, Based on dilution of 40 g powder Natural and Artificial Flavor, and less than 2% (1 scoop or 1 pouch) to 7 fl oz 95024 - Vanilla 00847-0950-24 B4157 or B4162 16 x 40 g (1.4 oz) 157 L-Serine 2.24 0.90 Iodine, mcg 100 40 of the following: Titanium Dioxide. L-Threonine 1.15 0.46 Molybdenum, mcg 45 18 (210 mL) water 95034 - Orange Creme 00847-0950-34 B4157 or B4162 16 x 40 g (1.4 oz) 157 Orange Creme flavored version also contains: 95044 - Strawberry 00847-0950-44 B4157 or B4162 16 x 40 g (1.4 oz) 157 L-Tryptophan 0.58 0.23 Chromium, mcg 30 12 Sugar, Natural and Artificial Flavor, and less • Displacement: 0.75 mL/g L-Tyrosine 2.69 1.08 Selenium, mcg 40 16 than 2% of the following: FD&C Yellow #6. Metabolics 95084 - Unflavored 00847-0950-84 B4157 or B4162 16 x 40 g (1.4 oz) 157 L-Valine 1.7 0.67 Sodium, mg 388 155 Strawberry flavored version also contains: Potassium, mg 872 349 Sugar, Natural and Artificial Flavor, and less WIC‡: Contact your state WIC For more reimbursement L-Carnitine 0.04 0.01 Taurine 0.08 0.03 Chloride, mg 475 190 than 2% of the following: FD&C Red #40, office to determine availability. information see page 195. FD&C Blue #1. 52 53 * S9435 = For individuals who submit their bills to insurance on their own. PhenylAde40 Drink Mix

Nutrition Information: Ingredients: Per 10 g Protein Per 10 g Protein ® Corn Syrup Solids, Sugar, L-Glutamine, PhenylAde 40 Drink Mix Equivalent Equivalent Nutrients Per 100 g (1 pouch) Vitamins Per 100 g (1 pouch) L-Asparagine Monohydrate, L-Serine, Calories 330 83 Vitamin A, IU (mcg RE) 1557 (584) 389 (146) L-Alanine, L-Tyrosine, L-Lysine A phenylalanine-free, powdered medical food for the dietary Monohydrochloride, L-Leucine, Protein Equivalent, g 40 10 (25% as beta-carotene) management of phenylketonuria (PKU) in children and adults, including L-Arginine, L-Valine, Citric Acid, Fat, g 2 0.5 Vitamin D , IU (mcg) 347 (8.7) 87 (2.2) 3 Tricalcium Phosphate, Glycine, L-Proline, pregnant women and women of child-bearing age. Vitamin E, IU (mg -TE) 15.4 (10.3) 3.9 (2.6) Saturated, g 0.48 0.12 α Natural Flavor. Contains 2% or less of Monounsaturated, g 1.1 0.28 Vitamin K, mcg 60 15 the following: L-Threonine, L-Isoleucine, Main Features: Indications: Polyunsaturated, g 0.40 0.10 Thiamin, mg 1.4 0.35 Magnesium Phosphate, L-Methionine, Carbohydrate, g 38 9.5 Riboflavin, mg 1.3 0.32 Sodium Citrate, L-Histidine, Dipotassium • Phenylalanine-free • Phenylketonuria Amino Acids, g Vitamin B6, mg 1.5 0.38 Phosphate, Modified Corn Starch, • Complete with essential vitamins L-Alanine 3.85 0.96 Vitamin B12, mcg 2.8 0.7 Canola Oil, Maltodextrin, Safflower and minerals For details on administration and household measurements, please L-Arginine 3.27 0.82 Niacin, mg 16.4 4.1 Oil, Choline Bitartrate, Potassium see pages 124-136. L-Asparagine 5.04 1.26 Folic Acid, mcg 468 117 Chloride, L-Tryptophan, L-Cystine, • Only 0.5 gram of fat and 83 calories L-Cystine 0.55 0.14 Pantothenic Acid, mg 5.8 1.5 Sodium Chloride, Coconut Oil, Soybean per serving L-Glutamine 6.34 1.59 Biotin, mcg 35 8.8 Oil, Taurine, Silicon Dioxide, Inositol, • PhenylAde40 Drink Mix provides Glycine 2.47 0.62 Vitamin C, mg 75 18.9 Ascorbic Acid, L-Carnitine, Ascorbyl Palmitate, Mixed Tocopherols, Rosemary L-Histidine 1.02 0.26 Choline, mg 284 71 40 g of protein equivalent and 2 g of Ordering/Reimbursement Information: Extract, Ferric Orthophosphate, Vitamin L-Isoleucine 1.64 0.41 Inositol, mg 86 22 fat per 100 g of powder E Acetate, Zinc Sulfate, Niacinamide, Product Reimbursement HCPCS Product Calories Minerals • Available in citrus and unflavored L-Leucine 3.64 0.91 Sucralose, D-Calcium Pantothenate, Code Code Code* Packaging Per Pouch L-Lysine 2.98 0.75 Calcium, mg 894 224 single serve pouches Vitamin K1, Manganese Sulfate, 95404 - Unflavored 00847-0954-04 B4157 or B4162 20 x 25 g (0.88 oz) 83 L-Methionine 1.08 0.27 Phosphorus, mg 809 202 Vitamin A Palmitate, D-Biotin, Vitamin • Osmolality (at 0.63 kcal/mL): 95414 - Citrus 00847-0954-14 B4157 or B4162 20 x 25 g (0.88 oz) 83 L-Phenylalanine Nil Added Nil Added Magnesium, mg 209 52 D3, Beta-carotene, Copper Sulfate, 1110 mOsm/kg L-Proline 2.47 0.62 Iron, mg 12 3 Pyridoxine Hydrochloride, Potassium Based on dilution of 25 g powder L-Serine 4.08 1.02 Zinc, mg 8 2 Iodide, Thiamin Mononitrate, Riboflavin, Sodium Selenite, Folic Acid, Vitamin B12, (1 pouch) to 4 fl oz (120 mL) water WIC‡: Contact your state WIC For more reimbursement L-Threonine 1.92 0.48 Manganese, mg 1.8 0.45 Copper, mcg 869 217 Chromium Chloride, Sodium Molybdate. office to determine availability. information see page 195. L-Tryptophan 0.61 0.15 • Displacement: 0.48 mL/g L-Tyrosine 3.78 0.95 Iodine, mcg 133 33 CONTAINS: Coconut Oil, Soybean Oil. L-Valine 2.74 0.69 Molybdenum, mcg 40 10 * S9435 = For individuals who submit their bills to insurance on their own. L-Carnitine 0.06 0.01 Chromium, mcg 27 6.7 Citrus flavored version also contains: less Metabolics Taurine 0.12 0.03 Selenium, mcg 56 13.9 than 2% of the following: FD&C Yellow #5. Sodium, mg 424 106 Potassium, mg 776 194 Chloride, mg 1322 331 54 55 Vitamin A....

Vitamin K..... PhenylAde60 Drink Mix Nutrition Information: Ingredients: Per 10 g Protein Per 10 g Protein Unflavored: L-Asparagine Monohydrate, ® Equivalent Equivalent L-Glutamine, Sugar, L-Tyrosine, L-Lysine Acetate, PhenylAde 60 Drink Mix Nutrients Per 100 g (1 scoop/pouch) Vitamins Per 100 g (1 scoop/pouch) L-Alanine, L-Leucine, L-Serine, L-Arginine, L-Valine, Tricalcium Phosphate, Glycine, L-Proline, Calories 294 49 Vitamin A, IU (mcg RE) 2331 (874) 389 (146) L-Threonine, Corn Syrup Solids, L-Isoleucine, A phenylalanine-free, powdered medical food for the dietary Protein Equivalent, g 60 10 (25% as beta-carotene) Magnesium Phosphate. Contains 2% or less Fat, g 1 0.17 Vitamin D , IU (mcg) 520 (13) 87 (2.2) of the following: Sodium Citrate, L-Histidine, management of phenylketonuria (PKU) in children and adults, including 3 L-Methionine, L-Tryptophan, Dipotassium pregnant women and women of child-bearing age. Saturated, g <0.5 <0.1 Vitamin E, IU (mg α-TE) 23 (15.4) 3.8 (2.6 Phosphate, Potassium Chloride, Choline Monounsaturated, g <0.5 <0.1 Vitamin K, mcg 90 15 Bitartrate, Soy Lecithin, L-Cystine, Sodium Chloride, Silicon Dioxide, Modified Corn Starch, Polyunsaturated, g <0.5 <0.1 Thiamin, mg 2.1 0.35 Taurine, Canola Oil, Maltodextrin, Safflower Carbohydrate, g 11 2 Riboflavin, mg 1.9 0.32 Oil, Ascorbic Acid, Inositol, L-Carnitine, Ferric Orthophosphate, Vitamin E Acetate, Coconut Oil, Amino Acids, g Vitamin B6, mg 2.3 0.38 Main Features: Indications: Soybean Oil, Zinc Sulfate, Niacinamide, Sucralose, L-Alanine 5.56 0.93 Vitamin B12, mcg 4.2 0.7 D-Calcium Pantothenate, Vitamin K1, Ascorbyl L-Arginine 4.72 0.79 Niacin, mg 25 4.1 Palmitate, Mixed Tocopherols, Rosemary Extract, • Phenylalanine-free • Phenylketonuria Manganese Sulfate, Vitamin A Palmitate, D-Biotin, L-Asparagine 8.36 1.39 Folic Acid, mcg 700 117 • Complete with essential vitamins Vitamin D3, Beta-carotene, Copper Sulfate, For details on administration and household measurements, please L-Cystine 0.81 0.13 Pantothenic Acid, mg 8.7 1.5 Pyridoxine Hydrochloride, Potassium Iodide, and minerals L-Glutamine 9.31 1.55 Biotin, mcg 53 8.8 Thiamin Mononitrate, Riboflavin, Sodium Selenite, see pages 124-136. Folic Acid, Vitamin B12, Chromium Chloride, • Only 49 calories per serving Glycine 3.63 0.61 Vitamin C. mg 113 19 Sodium Molybdate. • PhenylAde60 Drink Mix provides L-Histidine 1.51 0.25 Choline, mg 425 71 CONTAINS: Soy, Coconut Oil. L-Isoleucine 2.49 0.42 Inositol, mg 129 22 60 g of protein equivalent and 1 g of Ordering/Reimbursement Information: Vanilla: L-Asparagine Monohydrate, L-Glutamine, fat per 100 g of powder L-Leucine 5.37 0.90 Minerals Sugar, L-Tyrosine, L-Lysine Acetate, L-Alanine, L-Lysine 4.36 0.73 Calcium, mg 1300 217 L-Leucine, L-Serine, L-Arginine, L-Valine, Tricalcium Phosphate, Glycine, L-Proline, L-Threonine, • Available in vanilla and unflavored Product Reimbursement HCPCS Product Calories Per L-Methionine 1.45 0.24 Phosphorus, mg 1194 199 Code Code Code* Packaging Can/Pouch Natural and Artificial Flavor, L-Isoleucine, Magnesium, mg 310 52 Magnesium Phosphate. Contains 2% or less • Available in cans or single serve CANS L-Phenylalanine Nil Added Nil Added Iron, mg 18 3 of the following: Sodium Citrate, L-Histidine, pouches 9560 - Unflavored 00847-0956-02 B4157 or B4162 4 x 454 g (1 lb) 1335 L-Proline 3.63 0.61 L-Methionine, L-Tryptophan, Dipotassium Zinc, mg 12 2 • Osmolality (at 0.49 kcal/mL): 9562 - Vanilla 00847-0956-22 B4157 or B4162 4 x 454 g (1 lb) 1335 L-Serine 5.37 0.90 Phosphate, Potassium Chloride, Choline L-Threonine 2.76 0.46 Manganese, mg 2.7 0.45 Bitartrate, Soy Lecithin, L-Cystine, Sodium 1256 mOsm/kg POUCHES Chloride, Taurine, Ascorbic Acid, Inositol, Silicon L-Tryptophan 1.38 0.23 Copper, mcg 1300 217 95604 - Unflavored 00847-0956-04 B4157 or B4162 30 x 16.7 g (0.59 oz) 49 Dioxide, L-Carnitine, Ferric Orthophosphate, Based on dilution of 16.7 g powder L-Tyrosine 6.45 1.08 Iodine, mcg 180 30 Sucralose, Vitamin E Acetate, Zinc Sulfate, 95624 - Vanilla 00847-0956-24 B4157 or B4162 30 x 16.7 g (0.59 oz) 49 Niacinamide, D-Calcium Pantothenate, Vitamin (1 scoop or 1 pouch) to 3 fl oz L-Valine 4.01 0.67 Molybdenum, mcg 60 10 K1, Manganese Sulfate, Vitamin A Palmitate, (90 mL) water L-Carnitine 0.09 0.01 Chromium, mcg 40 6.7 D-Biotin, Vitamin D3, Beta-carotene, Copper ‡ Taurine 0.18 0.03 Selenium, mcg 83 14 Sulfate, Pyridoxine Hydrochloride, Potassium • Displacement: 0.54 mL/g WIC : Contact your state WIC For more reimbursement Iodide, Thiamin Mononitrate, Riboflavin, Sodium Metabolics Sodium, mg 600 100 office to determine availability. information see page 195. Selenite, Folic Acid, Vitamin B12, Chromium Potassium, mg 1162 194 Chloride, Sodium Molybdate. * S9435 = For individuals who submit their bills to insurance on their own. Chloride, mg 900 150 CONTAINS: Soy.

56 57 PhenylAde MTE Amino Acid Blend Nutrition Information: Ingredients: Per 10 g Protein Equivalent L-Asparagine Monohydrate, L-Glutamine, ® Nutrients Per 100 g (1 scoop/pouch) L-Tyrosine, L-Lysine Acetate, L-Alanine, PhenylAde MTE Amino Acid Blend Calories 312 40 L-Leucine, L-Serine, L-Arginine, L-Valine, Protein Equivalent, g 78 10 Glycine, L-Proline, L-Threonine, A phenylalanine-free, powdered medical food for the dietary management of Fat, g 0 0 L-Isoleucine, Dicalcium Phosphate, phenylketonuria (PKU) in children and adults, including pregnant women and Carbohydrate, g 0 0 L-Histidine, L-Methionine, L-Tryptophan, L-Cystine, Magnesium Phosphate women of child-bearing age. Amino Acids, g L-Alanine 7.23 0.93 (Dibasic), Silicon Dioxide, Taurine, L-Arginine 6.13 0. 79 L-Carnitine, Calcium Citrate, Chromium L-Asparagine 10.87 1.40 Chloride, Sodium Selenite, Sodium Molybdate. Main Features: Indications: L-Cystine 1.05 0. 14 L-Glutamine 12.11 1.55 Note: Must be combined with an • Phenylalanine-free • Phenylketonuria Glycine 4.72 0. 61 L-Histidine 1.96 0. 25 appropriate vitamin & mineral • Only 40 calories per serving L-Isoleucine 3.24 0. 42 supplement when taken as the sole For details on administration and household measurements, please source of amino acid protein. see pages 124-136. L-Leucine 6.98 0. 90 • 100 g of powder provides 78 g of L-Lysine 5.67 0. 73 protein equivalent L-Methionine 1.89 0. 24 L-Phenylalanine Nil Added Nil Added • PhenylAde MTE Amino Acid Ordering/Reimbursement Information: L-Proline 4.72 0. 61 Blend contains added calcium, L-Serine 6.98 0. 90 Product Reimbursement HCPCS Product Calories Per L-Threonine 3.59 0. 46 phosphorus, magnesium, chromium, Code Code Code* Packaging Can/Pouch L-Tryptophan 1.79 0. 23 molybdenum, and selenium CANS L-Tyrosine 8.39 1.08 9596 - MTE 00847-0959-60 B4155 4 x 454 g (1 lb) 1421 L-Valine 5.22 0. 67 • Available in cans and single-serve POUCHES L-Carnitine 0. 11 0.01 pouches 95964 - MTE 00847-0959-64 B4155 30 x 12.8 g (0.45 oz) 40 Taurine 0. 24 0.03 Minerals • Displacement: 0.47 mL/g Calcium, mg 570 73 WIC‡: Contact your state WIC For more reimbursement Chloride, mg Trace Trace office to determine availability. information see page 195. Chromium, mcg 23 3 Magnesium, mg 123 15.8

Metabolics Molybdenum, mcg 23 3 * S9435 = For individuals who submit their bills to insurance on their own. Phosphorus, mg 570 73 Sodium, mg Trace Trace Selenium, mcg 26 3.3 58 59 PhenylAde PheBLOC LNAA

Nutrition Information: Ingredients: ® ™ Per Tablet Per 5 Tablets Per 10 Tablets Per Pouch Per 2 Pouches Tablet Ingredients: PhenylAde PheBLOC LNAA Nutrients (750mg) (3,750mg) (7,500mg) Nutrients (3g Powder) (6g Powder) L-Tyrosine, Calcium Calories 3 15 30 Calories 10 20 Carbonate, L-Tryptophan, A phenylalanine-free medical food containing the remaining essential Protein Equivalent, g 0.44 2.2 4.4 Protein Equivalent, g 2.2 4.4 L-Methionine, amino acids (large neutral amino acids and lysine) for the dietary Fat, g 0.02 0.1 0.2 Fat, g 0 0 Microcrystalline Cellulose, management of phenylketonuria (PKU) in individuals over 12 years of age. Carbohydrate, g 0.2 1 2 Carbohydrate, g 0.34 0.68 L-Arginine, L-Threonine, Minerals Minerals L-Valine, L-Isoleucine, L-Histidine, L-Leucine, Calcium, mg 43.5 218 435 Sodium, mg Trace Trace L-Lysine Monohydrochloride, Sodium, mg 0.82 4.1 8.2 Chloride, mg 28 56 Hydroxypropyl Amino Acids, g Main Features: Indications: Chloride, mg 5.5 28 55 Methylcellulose, Stearic L-Arginine 0.17 0.34 • Phenylketonuria Amino Acids, g Acid, Croscarmellose • Phenylalanine-free L-Arginine 0.03 0.17 0.34 L-Histidine 0.16 0.31 Sodium, Magnesium • Provides full compliment of Precautions: L-Histidine 0.03 0.16 0.31 L-Isoleucine 0.16 0.32 Stearate and Silicon Dioxide. L-Isoleucine 0.03 0.16 0.32 L-Leucine 0.15 0.31 essential amino acids (without • Not for use when planning or during pregnancy L-Leucine 0.03 0.15 0.31 L-Lysine 0.12 0.23 Powder Ingredients: phenylalanine) • Seek medical advice before using with serotonergic L-Lysine 0.02 0.12 0.23 L-Methionine 0.25 0.50 L-Tyrosine, Maltodextrin, • Simplifies diet management medications L-Methionine 0.05 0.25 0.50 L-Phenylalanine Nil Added Nil Added L-Tryptophan, L-Methionine, L-Phenylalanine Nil Added Nil Added Nil Added L-Threonine 0.16 0.33 L-Arginine, L-Threonine, • Suitable for those currently using For details on administration, please see pages 124-136. L-Threonine 0.03 0.16 0.33 L-Tryptophan 0.31 0.61 L-Valine, L-Isoleucine, sapropterin and prefer L-Tryptophan 0.06 0.31 0.61 L-Tyrosine 0.98 1.97 L-Histidine, L-Leucine and L-Lysine Monohydrochloride non-liquid PKU formula L-Tyrosine 0.20 0.98 1.97 L-Valine 0.16 0.32 • An option for late-diagnosed or Ordering/Reimbursement Information: L-Valine 0.03 0.16 0.32 those who have never been Product Reimbursement HCPCS Product on-diet Code Code Code* Packaging Calories TABLETS • Available in tablets or powder 95501 00847-0955-01 B9998 550 x 750 mg (0.03 oz) 1650/pack POUCHES 95504 00847-0955-04 B4155 110 x 3 g (0.11 oz) 1100/case Visit NutriciaLearningCenter.com for Metabolics guidelines on the usage of PhenylAde PheBloc LNAA in the dietary * S9435 = For individuals who submit their bills to insurance on their own. management of PKU. 60 61 Lanaflex

Nutrition Information: Ingredients: ® Lanaflex Per Sachet Per Sachet Sugar, Calcium Phosphate, Artificial Nutrients (15.8 g) Per 100 g Minerals (15.8 g) Per 100 g Flavors, L-Histidine, L-Tryptophan, A phenylalanine-free powdered medical food containing the remaining essential Calories 40 253 Calcium, mg 474 2998 L-Tyrosine, Tricalcium Phosphate, amino acids (large neutral amino acids and lysine) for the dietary management of Protein Equivalent, g 5.2 33 Phosphorus, mg 456 2888 Magnesium Acetate, L-Lysine Acetate, Fat, g 0.16 1 Magnesium, mg 122 775 N-Acetyl-L-Methionine, L-Leucine, phenylketonuria (PKU) in individuals over 12 years of age. Carbohydrate g 4.4 28 Iron, mg 5.9 37.6 L-Methionine, L-Threonine, L-Valine, Amino Acids, g Zinc, mg 3.7 23.2 L-Isoleucine, Choline Bitartrate, Guar L-Histidine 0.92 5.85 Manganese, mg 0.73 4.6 Gum, Soy Lecithin, Citric Acid, L-Ascorbic L-Isoleucine 0.46 2.92 Copper, mcg 332 2100 Acid, M-Inositol, Ferrous Sulfate, Artificial Sweetener (Acesulfame Potassium), L-Leucine 0.46 2.92 Iodine, mcg 52.3 331 DL-Alpha-Tocopheryl Acetate, Zinc Main Features: Indications: L-Lysine 0.46 2.92 Molybdenum, mcg 14.9 94.2 Sulfate, Nicotinamide, Manganese L-Methionine 0.92 5.85 • Phenylalanine-free • Phenylketonuria Chromium, mcg 10.6 66.9 Sulfate, Calcium-D-Pantothenate, Cupric L-Threonine 0.46 2.92 Selenium, mcg 23.1 146 • Contains lysine and other large neutral Sulfate, Pyridoxine Hydrochloride, Precautions: L-Tryptophan 0.92 5.85 Sodium, mg 4.9 31 Riboflavin, Vitamin A Acetate, Folic amino acids L-Tyrosine 0.92 5.85 Potassium, mg 3.5 22 Acid, Artificial Color (Beta Carotene), • Contains carbohydrate, vitamins, minerals • Not for use when planning or during pregnancy L-Valine 0.46 2.92 Chloride, mg 0.25 1.6 Potassium Iodide, Chromium Chloride, and trace elements Vitamins Sodium Selenite, Sodium Molybdate, • Seek medical advice before using with serotonergic Vitamin A IU, (mcg RE) 892 (268) 5644 (1695) Phylloquinone, D-Biotin, Cholecalciferol, medications Cyanocobalamin. • One sachet of Lanaflex provides Vitamin D3 IU, (mcg) 135 (3.4) 852 (21.3) 6 g of amino acids equivalent to Vitamin E IU, (mg α-TE) 7.4 (5) 46.9 (31.5) CONTAINS: Soy. 5.2 g of protein For details on administration, please see pages 124-136. Vitamin K, mcg 32.7 207 • Available in orange flavor Thiamin, mg 0.36 2.3 Riboflavin, mg 0.38 2.4 • Osmolality (mOsm/kg): Vitamin B6, mg 0.65 4.1 Dilution Ordering/Reimbursement Information: Vitamin B12, mcg 1.3 8 1 to 4 1350 Product Reimbursement HCPCS Product Calories Niacin, mg 2.2 14.2 Code Code Code* Packaging Per Sachet Folic Acid, mcg 197 1246 12643 49735-0126-43 B4157 40 x 15.8 g (0.6 oz) 40 Pantothenic Acid, mg 1.9 12.2 Visit NutriciaLearningCenter.com for Biotin, mcg 9.8 61.9 guidelines for the usage of Lanaflex in Vitamin C, mg 25.1 159 Metabolics the dietary management of PKU. Choline, mg 165 1045 Inositol, mg 32.1 203 * S9435 = For individuals who submit their bills to insurance on their own. 62 63 XPhe Maxamum

Nutrition Information: Ingredients: ® Per 10 g Per 10 g XPhe Maxamum Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Sugar, L-Arginine L-Aspartate, L-Lysine Calories 305 76 Vitamin A, IU (mcg RE) 2228 (669) 557 (167) Acetate, L-Glutamine, L-Leucine, A phenylalanine-free powdered medical food for the dietary management of Protein Equivalent, g 40 10 Vitamin D3, IU (mcg) 332 (8.3) 83 (2.1) L-Tyrosine, Calcium Glycerophosphate, phenylketonuria (PKU) in older children and adults, including pregnant women and Fat, g <1 <0.25 Vitamin E, IU (mg α-TE) 18.3 (12.3) 4.6 (3.1) L-Proline, L-Valine, Glycine, L-Isoleucine, L-Threonine, Tripotassium Citrate, women of child-bearing age. Carbohydrate, g 34 8.5 Vitamin K, mcg 82 21 Magnesium Hydrogen Phosphate, and 2% Amino Acids, g Thiamin, mg 0.91 0.23 or less of each of the following: L-Serine, L-Alanine 1.6 0.40 Riboflavin, mg 0.97 0.24 L-Histidine, L-Alanine, Calcium Phosphate L-Arginine 3 0.75 Vitamin B6, mg 1.6 0.4 Dibasic, Choline Bitartrate, L-Cystine, Main Features: Indications: L-Aspartic Acid 2.8 Tricalcium Phosphate, Sodium Chloride, 0.70 Vitamin B12, mcg 3.1 0.8 N-Acetyl L-Methionine, Trisodium Citrate, • Phenylalanine-free • Phenylketonuria L-Cystine 1.1 0.28 Niacin, mg 5.7 1.4 Glycine 2.8 0.70 Folic Acid, mcg 491 123 L-Tryptophan, Soy Lecithin, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, • Contains a balanced mixture of all other L-Histidine 1.7 0.43 Pantothenic Acid, mg 4.9 1.2 M-Inositol, Ferrous Sulfate, L-Carnitine, essential and non-essential amino acids, L-Isoleucine 2.7 0.68 Biotin, mcg 24.5 6.1 For details on administration and household measurements, please Zinc Sulfate, DL-Alpha Tocopheryl carbohydrate, vitamins, minerals and L-Leucine 4.6 1.15 Vitamin C, mg 62 16 Acetate, Niacinamide, Manganese trace elements see pages 124-136. L-Lysine 3.5 0.88 Choline, mg 430 108 Sulfate, Calcium D-Pantothenate, Cupric • Age-appropriate DRI formulation L-Methionine 0.73 0.18 Inositol, mg 80 20 Sulfate, Pyridoxine Hydrochloride, L-Phenylalanine Nil Added Nil Added Minerals Sodium Selenite, Thiamin Chloride • XPhe Maxamum provides 40 g of Ordering/Reimbursement Information: Hydrochloride, Riboflavin, Vitamin A L-Proline 3.2 0.80 Calcium, mg 1183 296 protein equivalent per 100 g of powder Product Reimbursement HCPCS Product Calories Per Acetate, Folic Acid, Potassium Iodide, L-Serine 2 Phosphorus, mg 1137 284 Code Code Code* Packaging Can/Pouch 0.50 Chromium Chloride, Sodium Molybdate, • Available in unflavored and orange flavor L-Threonine 2.2 0.55 Magnesium, mg 306 77 Phylloquinone, D-Biotin, Vitamin D , CANS 3 L-Tryptophan 0.89 0.22 Iron, mg 14.7 3.7 Cyanocobalamin. • Contains <1 g of fat per 10 g PE thereby 118324 - Orange 49735-0183-24 B4162 or B4157 6 x 454 g (1 lb) 1385 allowing greater flexibility in modifying L-Tyrosine 4 1.00 Zinc, mg 9 2 118323 - Unflavored 49735-0183-23 B4162 or B4157 6 x 454 g (1 lb) 1385 Orange flavored version also contains: energy intake L-Valine 2.9 0.73 Manganese, mg 1.8 0.5 Citric Acid, and 2% or less of each of POUCHES L-Carnitine 0.039 0.01 Copper, mcg 820 205 • Available in cans or pouches the following: Artificial Flavor, Artificial 12312 - Orange 49735-0123-02 B4162 or B4157 30 x 50 g (1.8 oz) 153 Taurine 0.14 0.04 Iodine, mcg 131 33 Sweetener: Acesulfame Potassium, • Osmolality (mOsm/kg): 12311 - Unflavored 49735-0123-01 B4162 or B4157 30 x 50 g (1.8 oz) 153 L-Glutamine 4.9 1.23 Molybdenum, mcg 37 9 Artificial Colors (Beta Carotene, Beet Red). Dilution Unflavored Orange Chromium, mcg 26 7 CONTAINS: Soy 1 to 7 770 790 WIC‡: Contact your state WIC For more reimbursement Selenium, mcg 58 15 Metabolics 1 to 5 1090 1140 office to determine availability. information see page 195. Sodium, mg 560 140 • Displacement: 0.6 mL/g Potassium, mg 700 175 * S9435 = For individuals who submit their bills to insurance on their own. Chloride, mg 560 140 64 65 Ingredients: PKU Lophlex LQ Water, and less than 2% of each of the Nutrition Information: following: L-Leucine, Citric Acid, L-Proline, ® Per Pouch Per 10 g Per Pouch Per 10 g L-Arginine, Glycine, L-Tyrosine, L-Lysine PKU Lophlex LQ Nutrients (125 mL) Protein Equivalent Vitamins (125 mL) Protein Equivalent Acetate, L-Valine, L-Aspartic Acid, L-Isoleucine, Dicalcium Phosphate, L-Alanine, Calories 120 60 Vitamin A, IU (mcg RE) 949 (285) 475 (143) L-Serine, L-Threonine, L-Histidine, L-Lysine, A phenylalanine-free*, ready-to-drink medical food containing amino acids, Protein Equivalent, g 20 10 Vitamin D , IU (mcg) 320 (8) 160 (4) L-Aspartate, Maltodextrin, Magnesium 3 Acetate, L-Cystine, Choline Bitartrate, vitamins and minerals and DHA, based on fruit juice (from concentrate) with Fat, g 0.44 0.2 Vitamin E, IU (mg α-TE) 4.8 (3.2) 2.4 (1.6) L-Tryptophan, Sugar, C. Cohnii Oil**, N-Acetyl natural flavor; for the dietary management of proven phenylketonuria (PKU) in DHA, mg 150 75 Vitamin K, mcg 24.9 12.5 L-Methionine, Microcrystalline Cellulose, L-Ascorbic Acid, Taurine, L-Methionine, Guar individuals 4 years and older, including pregnant women and women of Carbohydrate, g 9.3 4.7 Thiamin, mg 0.54 0.27 Gum, Sunflower Lecithin, Xanthan Gum, Fiber, g 0.5 0.25 Riboflavin, mg 0.5 0.25 M-Inositol, Potassium Sorbate (preservative child-bearing age. to delay spoilage), Ferrous Lactate, Cellulose Amino Acids, g Vit. B6, mg 0.58 0.29 Gum, Artificial Sweetener: Acesulfame L-Alanine 1.16 0.58 Vit. B12, mcg 1.8 0.90 Potassium, L-Carnitine, Sodium Benzoate (preservative to delay spoilage), Zinc Sulfate, Main Features: L-Arginine 2 1 Niacin, mg 7.1 3.6 Niacinamide, DL-alpha Tocopheryl Acetate, Indications: L-Aspartic Acid 1.75 0.88 Folic Acid, mcg 120 60 Calcium D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Thiamin Chloride • Phenylalanine-free • Phenylketonuria L-Cystine 0.51 0.26 Pantothenic Acid, mg 1.8 0.9 Hydrochloride, Pyridoxine Hydrochloride, Glycine 1.88 0.94 Biotin, mcg 53.4 26.7 Vitamin A Palmitate, Riboflavin, Folic Acid, • Low volume; provides 20 g PE in just Potassium Iodide, Ascorbyl Palmitate, Mixed L-Histidine 0.79 0.40 Vitamin C, mg 17.8 8.9 4.2 fl oz (125 mL) For details on administration, please see pages 124-136. Tocopherols, Sodium Molybdate, D-Biotin, L-Isoleucine 1.24 0.62 Choline, mg 153 76.5 Sodium Selenite, Chromium Chloride, Phylloquinone, Vitamin D3, Cyanocobalamin. • Convenient ready-to-drink L-Leucine 2.13 1.1 Inositol, mg 40.6 20.3 **A Source Of Docosahexaenoic Acid (DHA) L-Lysine 1.63 0.82 Minerals • Made with real fruit juice from Juicy Orange flavored version also contains: concentrate Ordering/Reimbursement Information: L-Methionine 0.34 0.17 Calcium, mg 319 160 Orange Juice from Concentrate (45.5%), Product Reimbursement HCPCS Product Calories L-Phenylalanine Trace* Trace* Phosphorus, mg 244 122 Corn Syrup Solids, and less than 2% of • Contains a balanced mixture of the following: Natural Flavor, Artificial Code Code Code* Packaging Per Pouch L-Proline 2 1 Magnesium, mg 96.3 48.2 other essential and non-essential amino Sweetener: Sucralose. 86051 49735-0161-30 B4157 and 30 x 4.2 fl oz 120 L-Serine 1.09 0.55 Iron, mg 5.1 2.6 Mixed Berry Blast flavored version also acids, carbohydrates, vitamins and Juicy Orange B4162 (125 mL) L-Threonine 1.04 0.52 Zinc, mg 3.8 1.9 contains: Apple Juice from Concentrate minerals (34.1%), Grape Juice from Concentrate (6.9%), 86021 49735-0161-29 B4157 and 30 x 4.2 fl oz 120 L-Tryptophan 0.41 0.21 Manganese, mg 0.56 0.28 Blackcurrant Juice from Concentrate (2.5%), • Provides 150 mg of DHA per pouch Mixed Berry Blast B4162 (125 mL) L-Tyrosine 1.88 0.94 Copper, mcg 563 282 and less than 2% of the following: Elderberry 86055 49735-0195-35 B4157 and 30 x 4.2 fl oz 120 Juice from Concentrate (0.6%), Natural • Available in juicy orange, mixed berry L-Valine 1.38 0.69 Iodine, mcg 56.3 28.2 Flavor, Concentrate (Apple, Blackcurrant, Juicy Tropical B4162 (125 mL) Radish), Artificial Sweetener: Sucralose. blast and juicy tropical flavors L-Carnitine 0.01 0.01 Molybdenum, mcg 25 12.5 Taurine 0.1 0.05 Chromium, mcg 10.8 5.4 Juicy Tropical flavored version also contains: • Osmolality (at 0.96 kcal/mL): WIC‡: Contact your state WIC For more reimbursement Orange Juice from Concentrate (18%), Mango Selenium, mcg 26.8 13.4 Puree from Concentrate (6.4%), Mandarin Metabolics office to determine availability. information see page 195. 2460 mOsm/kg Sodium, mg <25 <12.5 Juice from Concentrate (4.0%), Corn Syrup Solids, and less than 2% of the following: * S9435 = For individuals who submit their bills to insurance on their own. Potassium, mg 90 45 Artificial Flavor. *May contain traces of phenylalanine (PHE) from fruit juice (from concentrate). Chloride, mg <25 <12.5 Juicy Orange contains 45.5% juice. 66 Mixed Berry Blast contains 44.1% juice. 67 Juicy Tropical contains 28.4% juice. PKU Lophlex Powder NEW LOOK SPRING Nutrition Information: Ingredients: 2017 Nutrients Per 100 g Per sachet (14.3 g) Vitamins Per 100 g Per sachet (14.3 g) Berry: L-Lysine L-Aspartate, L-Leucine, Calories 286 41 Vitamin A, IU (mcg RE) 3896 (1170) 557 (167) L-Tyrosine, L-Proline, L-Arginine, Calcium ® Phosphate Tribasic, L-Valine, Glycine, PKU Lophlex Powder Protein Equivalent, g 70 10 Vitamin D3, IU (mcg) 580 (14.5) 82.9 (2.1) L-Isoleucine, L-Threonine, Magnesium Fat, g 0.2 0.03 Vitamin E, IU (mg α-TE) 32 (21.5) 4.6 (3.1) Hydrogen Phosphate, L-Glutamine, L-Serine, L-Histidine, L-Alanine, Citric Acid, L-Cystine, A low volume, phenylalanine-free, powdered medical food for the dietary Carbohydrate, g 1 0.14 Vitamin K, mcg 143 20.4 N-Acetyl L-Methionine, Choline Bitartrate, management of phenylketonuria (PKU) in older children and adults, including Amino Acids, g Thiamin, mg 1.6 0.23 L-Tryptophan, Calcium Phosphate Monobasic, L-Alanine 3.3 0.47 Guar Gum, Artificial Flavor, Soy Lecithin, pregnant women and women of child-bearing age. Riboflavin, mg 1.7 0.24 L-Ascorbic Acid, M-Inositol, Artificial L-Arginine 5.8 0.83 Vitamin B6, mg 2.8 0.4 Sweetener: Acesulfame Potassium*, Taurine, L-Aspartic Acid 5.4 0.77 Vitamin B , mcg 5.5 0.79 Ferrous Sulfate, L-Carnitine, Zinc Sulfate, 12 Dl-Alpha Tocopheryl Acetate, Niacinamide, L-Cystine 2.2 0.31 Niacin, mg 10 1.4 Manganese Sulfate, Calcium D-Pantothenate, Glycine 5.1 0.73 Folic Acid, mcg 860 123 Cupric Sulfate, Pyridoxine Hydrochloride, Main Features: Thiamin Chloride Hydrochloride, Riboflavin, Indications: L-Histidine 3.3 0.47 Pantothenic Acid, mg 8.6 1.2 Vitamin A Acetate, Folic Acid, Beet Juice (For • Phenylalanine-free L-Isoleucine 5.1 0.73 Biotin, mcg 43 6.1 Color), Potassium Iodide, Chromium Chloride, • Phenylketonuria L-Leucine 8.7 1.24 Vitamin C, mg 110 15.7 Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D , • Low volume and low calorie 3 L-Lysine 5.9 0.84 Choline, mg 720 103 Cyanocobalamin. • Contains vitamins, minerals, and For details on administration, please see pages 124-136. L-Methionine 1.4 0.2 Inositol, mg 140 20 Orange L-Lysine L-Aspartate, L-Leucine, trace elements L-Phenylalanine Nil Added Nil Added Minerals L-Tyrosine, L-Proline, L-Arginine, Calcium L-Proline 6.2 0.89 Calcium, mg 2070 296 Phosphate Tribasic, L-Valine, Glycine, • Age-appropriate DRI formulation L-Isoleucine, Magnesium Hydrogen L-Serine 3.8 0.54 Phosphorus, mg 1990 285 Phosphate, L-Threonine, L-Glutamine, • Lophlex provides 10 g of protein L-Threonine 4.3 0.61 Magnesium, mg 535 76.5 L-Serine, L-Histidine, L-Alanine, Citric Acid, Ordering/Reimbursement Information: L-Cystine, N-Acetyl L-Methionine, Choline equivalent per sachet L-Tryptophan 1.7 0.24 Iron, mg 25.7 3.7 Product Reimbursement HCPCS Product Calories Bitartrate, L-Tryptophan, Calcium Phosphate • Available in berry and orange flavors L-Tyrosine 7.8 1.12 Zinc, mg 15.8 2.3 Monobasic, Artificial Flavor, Guar Gum, Soy Code Code Code* Packaging Per Sachet Lecithin, L-Ascorbic Acid, M-Inositol, Artificial • Osmolality (mOsm/kg): 12169 - Berry 49735-0121-69 B4157 or 30 x 14.3 g (0.5 oz) 42 L-Valine 5.6 0.8 Manganese, mg 3.1 0.44 Sweetener: Acesulfame Potassium*, Taurine, B4162 L-Carnitine 0.06 0.01 Copper, mcg 1430 204 Ferrous Sulfate, L-Carnitine, Zinc Sulfate, Dilution Orange Berry Taurine 0.11 0.02 Iodine, mcg 229 32.7 Dl-Alpha Tocopheryl Acetate, Niacinamide, 12167 - Orange 49735-0121-67 B4157 or 30 x 14.3 g (0.5 oz) 42 Manganese Sulfate, Calcium D-Pantothenate, 1 to 5 1390 1340 B4162 L-Glutamine 3.95 0.56 Molybdenum, mcg 65 9.3 Cupric Sulfate, Pyridoxine Hydrochloride, Chromium, mcg 46 6.6 Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Beet Juice (For Color), WIC‡: Contact your state WIC For more reimbursement Selenium, mcg 101 14.4 Beta Carotene (For Color), Folic Acid, Sodium, mg <20 <3 Potassium Iodide, Chromium Chloride, Metabolics office to determine availability. information see page 195. Potassium, mg <40 <6 Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Chloride, mg <1 <1 Cyanocobalamin. * S9435 = For individuals who submit their bills to insurance on their own. Both Flavors 68 CONTAINS: Soy. 69 Phlexy-10 Tablets

Nutrition Information: Ingredients: Phlexy-10® Tablets Per 10 Per 12 Microcrystalline Cellulose, L-Leucine, Nutrients Tablets Tablets L-Tyrosine, L-Lysine Hydrochloride, Calories 41 49 L-Proline, L-Arginine, L-Valine, L-Aspartic A phenylalanine-free medical food in tablet form for the dietary Protein Equivalent, g 8.3 10.0 Acid, Pregelatinized Corn Starch, Glycine, management of phenylketonuria (PKU) in individuals over 8 years of Fat, g 0.38 0.46 L-Isoleucine, L-Threonine, L-Glutamine, age, including pregnant women and women of child-bearing age. Saturated, g 0.36 0.43 L-Serine, L-Alanine, L-Histidine, Magnesium Carbohydrate, g 3.7 4.3 Stearate, L-Cystine, Hydroxypropyl Methyl Fiber, g 3.0 3.5 Cellulose, L-Tryptophan, Acacia Gum, Amino Acids, g L-Methionine, Stearic Acid, Glycerol, L-Alanine 0.41 0.49 Taurine, L-Carnitine. L-Arginine 0.72 0.86 Main Features: Indications: L-Aspartic Acid 0.68 0.82 L-Cystine 0.27 0.32 • Phenylalanine-free • Phenylketonuria L-Glutamic Acid Nil Added Nil Added • Every 12 tablets provide 10 g of Glycine 0.64 0.77 For details on administration, please see pages 124-136. L-Histidine 0.41 0.49 protein equivalent L-Isoleucine 0.64 0.77 • A great alternative to PKU liquid L-Leucine 1.09 1.3 consumption L-Lysine 0.74 0.89 L-Methionine 0.17 0.20 Ordering/Reimbursement Information: L-Phenylalanine Nil Added Nil Added L-Proline 0.77 0.92 Product Reimbursement HCPCS Product Code Code Code* Packaging Calories L-Serine 0.47 0.56 L-Threonine 0.54 0.65 11951 - Tablets 49735-0019-51 A9270 75/bottle 285/bottle L-Tryptophan 0.22 0.26 L-Tyrosine 0.97 1.2 L-Valine 0.7 0.84 WIC‡: Contact your state WIC For more reimbursement L-Carnitine 0.01 0.01 office to determine availability. information see page 195. Taurine 0.01 0.02 L-Glutamine 0.50 0.60 Metabolics

70 * S9435 = For individuals who submit their bills to insurance on their own. 71 Phlexy-10 Drink Mix

® Nutrition Information: Ingredients: Phlexy-10 Drink Mix Per 20 g Phlexy-10 Drink Mix (blackcurrant/ Pouch apple): Sucrose, L-Lysine Aspartate, A phenylalanine-free powdered medical food for the dietary Nutrients L-Leucine, L-Tyrosine, Artificial Flavors, management of phenylketonuria (PKU) in children and adults, Calories 69 L-Proline, L-Arginine, L-Valine, L-Isoleucine, Protein Equivalent, g 8.33 Glycine, Malic Acid, L-Threonine, including pregnant women and women of child-bearing age. Fat, g Nil Added L-Glutamine, Corn Syrup Solids, L-Serine, Saturated, g Nil Added L-Histidine, L-Alanine, L-Cystine, N-Acetyl Monounsaturated, g Nil Added L-Methionine, L-Tryptophan, Soy Lecithin, Polyunsaturated, g Nil Added Taurine, L-Carnitine, Artificial Sweetener: Acesulfame Potassium, Artificial Color. Main Features: Indications: Carbohydrate, g 8.8 Fiber, g Nil Added Phlexy-10 Drink Mix (tropical surprise): • Phenylalanine-free • Phenylketonuria Amino Acids, g Sucrose, L-Lysine Aspartate, Artificial Flavors, L-Leucine, L-Tyrosine, L-Proline, • Available in black currant/apple or L-Alanine 0.41 L-Arginine 0.72 L-Arginine, L-Valine, Citric Acid, Glycine, For details on administration, please see pages 124-136. L-Isoleucine, L-Threonine, L-Glutamine, tropical surprise flavor L-Aspartic Acid 0.68 Corn Syrup Solids, L-Serine, L-Histidine, • Each pouch provides 8.33 g PE L-Cystine 0.27 L-Alanine, L-Cystine, N-Acetyl L-Methionine, Glycine 0.64 • Convenient, pre-measured single L-Tryptophan, Soy Lecithin, Artificial L-Histidine 0.41 serve pouches Sweetener: Acesulfame Potassium, Taurine, Ordering/Reimbursement Information: L-Isoleucine 0.64 L-Carnitine, Artificial Color. • Osmolality (mOsm/kg): L-Leucine 1.09 Product Reimbursement HCPCS Product CONTAINS: Soy. Dilution Blackcurrant- Tropical Code Code Code* Packaging Calories L-Lysine 0.74 L-Methionine 0.17 Must combine with an appropriate vitamin Apple Surprise 11467 - Drink Mix 49735-0114-67 B4157 or 30 x 20 g (0.7 oz) 69/pouch and mineral supplement when taken as the (Blackcurrant-Apple) B4162 L-Phenylalanine Nil Added sole source of amino acid protein. 1 to 5 1172 1140 L-Proline 0.77 11910 - Drink Mix 49735-0119-10 B4157 or 30 x 20 g (0.7 oz) 69/pouch L-Serine 0.47 (Tropical Surprise) B4162 L-Threonine 0.54 L-Tryptophan 0.22 WIC‡: Contact your state WIC For more reimbursement L-Tyrosine 0.97 L-Valine 0.7 office to determine availability. information see page 195. L-Carnitine 0.007

Metabolics Taurine 0.014 L-Glutamine 0.5 * S9435 = For individuals who submit their bills to insurance on their own.

72 73 MSUD Anamix Early Years

Ingredients: ® Nutrition Information: MSUD Anamix Early Years Per 10 g Per 10 g Corn Syrup Solids, Refined Vegetable Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Oils (High Oleic Sunflower, Soy, A valine-, leucine-, and isoleucine-free powdered infant formula with iron, for the Calories 473 350 Vitamin A, IU (mcg RE) 1305.(392) 967.(290) Non-Hydrogenated Coconut, Canola, dietary management of maple syrup urine disease (MSUD). Contains DHA and Protein Equivalent,g 13.5 10.0 Vitamin D3, IU (mcg) 348.(8.7) 258.(6.4) Sunflower), Galacto-oligosaccharides Fat, g 23.0 17.0 Vitamin E, IU (mg α-TE) 10.9 (7.3) 8.1 (5.4) (GOS) Dried Syrup (from milk), L-Lysine ARA, and a unique blend of prebiotic fiber. Saturated, g 7.5 5.6 Vitamin K, mcg 38.0 28.1 L-Glutamate, L-Proline, L-Arginine, Monounsaturated, g 9.4 7.0 Thiamin, mcg 640 474 Glycine, L-Aspartic Acid, Tricalcium Polyunsaturated, g 5.0 3.7 Riboflavin, mcg 500 370 Phosphate, L-Threonine, CAEM (an Main Features: Indications: DHA, mg 70.0 51.9 Vitamin B6, mcg 500 370 emulsifier), L-Tyrosine, L-Phenylalanine, • Maple syrup urine disease (MSUD) ARA, mg 140 104 Vitamin B12, mcg 1.2 0.89 L-Serine, L-Histidine, L-Alanine, Potassium • Valine-, leucine-, and isoleucine-free Linoleic Acid,mg 3500 2593 Niacin, mcg 2200 1630 Chloride, Fructo-oligosaccharides powdered infant formula with iron Carbohydrate, g 53.0 39.3 Folic Acid, mcg 55.0 40.7 (FOS), Tripotassium Citrate, L-Cystine, For details on administration and household measurements, please • Includes DHA & ARA Fiber, g 5.3 3.9 Pantothenic Acid, mcg 2800 2074 L-Tryptophan, Sodium Phosphate Dibasic, see pages 124-136. GOS, g 4.7 3.5 Biotin, mcg 18.2 13.5 Magnesium Acetate, L-Methionine, M. • Contains a prebiotic fiber blend FOS, g 0.55 0.41 Vitamin C, mg 49.0 36.3 Alpina Oil*, Choline Bitartrate, C. Cohnii • Unflavored powder Amino Acids, g Choline, mg 91.0 67.4 Oil**, L-Glutamine, Sodium Chloride, L-Alanine 0.82 0.61 Inositol, mg 98.0 72.6 M-Inositol, L-Ascorbic Acid, L-Glutamic • Contains a balanced mixture of all L-Arginine 1.4 1.0 Minerals Acid, Taurine, Ferrous Sulfate, Zinc other essential and non-essential L-Aspartic Acid 1.2 0.89 Calcium, mg 371 275 Sulfate, L-Carnitine, DL-alpha Tocopheryl amino acids, carbohydrates, fat, Ordering/Reimbursement Information: L-Cystine 0.52 0.39 Phosphorus, mg 270 200 Acetate, Calcium D-Pantothenate, L-Glutamic Acid 1.6 1.2 Magnesium, mg 52.5 38.9 Niacinamide, Ascorbyl Palmitate, vitamins, minerals and trace elements Product Reimbursement HCPCS Product Calories L-Glutamine 0.13 0.10 Iron, mg 7.3 5.4 Manganese Sulfate, Cupric Sulfate, Code Code Code* Packaging Per Can • Provides 13.5 g of protein equivalent Glycine 1.29 0.96 Zinc, mg 5.2 3.9 Thiamine Chloride Hydrochloride, per 100 g of powder 90168 49735-0101-68 B4162 6 x 400 g (14 oz) 1892 L-Histidine 0.8 0.59 Manganese, mcg 390 289 Pyridoxine Hydrochloride, Riboflavin, L-Isoleucine Nil Added Nil Added Copper, mcg 390 289 Vitamin A Acetate, DL-alpha Tocopherol, • Osmolality (at 0.7 kcal/mL): L-Leucine Nil Added Nil Added Iodine, mcg 82.5 61.1 Mixed Tocopherols, Potassium Iodide, ‡ 380 mOsm/kg WIC : Contact your state WIC For more reimbursement L-Lysine 1.45 1.1 Molybdenum, mcg 10.9 8.1 Chromium Chloride, Folic Acid, Based on dilution of 5 g powder office to determine availability. information see page 195. L-Methionine 0.34 0.25 Chromium, mcg 12.5 9.3 Phylloquinone, Sodium Selenite, Sodium L-Phenylalanine 0.94 0.70 (1 unpacked level scoop) to 1 fl oz Selenium, mcg 14.1 10.4 Molybdate, D-Biotin, Vitamin D3, L-Proline 1.56 1.2 Sodium, mg 171 127 Cyanocobalamin. (30 mL) water L-Serine 0.96 0.71 Potassium, mg 454 336 CONTAINS: Soy Oil, Coconut Oil, Milk. • Displacement: 0.75 mL/g L-Threonine 1.05 0.78 Chloride, mg 321 238 L-Tryptophan 0.42 0.31 *A source of Arachidonic Acid (ARA) Metabolics L-Tyrosine 0.94 0.70 **A source of Docosahexaenoic Acid L-Valine Nil Added Nil Added Visit NutriciaLearningCenter.com * S9435 = For individuals who submit their bills to insurance on their own. (DHA) for guidelines for the nutritional L-Carnitine 0.01 0.01 Taurine 0.02 0.01 Contains GOS/FOS 0.8 g per 100 mL 74 management of MSUD. 75 Complex Junior MSD Drink Mix

Nutrition Information: Ingredients: Nutrients Per 100 g Per 100 kcal Vitamins Per 100 g Per 100 kcal Corn Syrup Solids, Maltodextrin, Modified Calories 494 100 Vitamin A, IU (mcg RE) 1187.(356) 240.(72) Complex Junior MSD Drink Mix Corn Starch, Canola Oil, Safflower Oil, Protein Equivalent, g 13 2.6 Vitamin D3, IU (mcg) 429.(10.7) 87.(2.2) Coconut Oil, L-Glutamine, Soybean Oil. Fat, g 29 6 Vitamin E, IU (mg -TE) 13.8 (9.2) 2.8 (1.9) A valine-, leucine-, and isoleucine-free powdered medical food for the dietary management of α Contains 2% or less of the following: Saturated, g 10.2 2.1 Vitamin K, mcg 62 12.6 Tricalcium Phosphate, L-Lysine Acetate, maple syrup urine disease (MSUD) in young children. Monounsaturated, g 13.4 2.7 Thiamin, mg 1.1 0.22 L-Alanine, L-Phenylalanine, L-Tyrosine, Polyunsaturated, g 5.0 1.0 Riboflavin, mg 0.81 0.16 Sodium Citrate, Dipotassium Phosphate, DHA, mg 88 17.9 Vitamin B6, mg 0.78 0.16 L-Threonine, L-Histidine, L-Asparagine ARA, mg 88 17.9 Vitamin B12, mcg 2 0.4 Linoleic Acid, mg 3730 755 Niacin, mg 5.8 1.2 Monohydrate, L-Proline, L-Tryptophan, Main Features: Indications: Carbohydrate, g 46 9 Folic Acid, mcg 140 28 Choline Bitartrate, L-Arginine, Ascorbyl Amino Acids, g Pantothenic Acid, mg 3.4 0.69 Palmitate, Mixed Tocopherols, • Valine-, leucine-, and isoleucine-free • Maple syrup urine disease (MSUD) L-Alanine 1.40 0.28 Biotin, mcg 36 7.2 Magnesium Chloride, Rosemary Extract, L-Arginine 0.66 0.13 Vitamin C, mg 78 15.8 L-Serine, Potassium Citrate, Potassium • Amino acid profile specifically L-Asparagine 0.75 0.15 Choline, mg 244 49 Chloride, L-Glutamic Acid, L-Methionine, designed for MSUD; clinically L-Cystine 0.29 0.06 Inositol, mg 148 30 Glycine, Silicon Dioxide, L-Cystine, C. Cohnii Oil, Glucose Syrup Solids, Mono- † For details on administration and household measurements, please L-Glutamic Acid 0.45 0.09 Minerals researched in one study and Diglycerides, M. Alpina Oil, Inositol, see pages 124-136. L-Glutamine 3.71 0.75 Calcium, mg 596 121 • Includes DHA & ARA Glycine 0.35 0.07 Phosphorus, mg 444 90 Ascorbic Acid, Zinc Sulfate, Taurine, L-Histidine 0.92 0.19 Magnesium, mg 68 13.8 Ferrous Sulfate, High Oleic Sunflower • Essential vitamins and minerals to L-Isoleucine Nil Added Nil Added Iron, mg 14.7 3 Oil, Mannitol, L-Carnitine, Vitamin E help meet needs of young children L-Leucine Nil Added Nil Added Zinc, mg 29 5.8 Acetate, Glycerol, Mono- and Distearate, with MSUD Ordering/Reimbursement Information: L-Lysine 1.17 0.24 Manganese, mg 0.44 0.09 Natural Flavor, Sodium Polyphosphate, L-Methionine 0.38 0.08 Copper, mcg 952 193 Sunflower Lecithin, Sodium Ascorbate, • Mild neutral flavor Product Reimbursement HCPCS Product Calories L-Phenylalanine 1.14 0.23 Iodine, mcg 96 19.4 Vitamin K1, Niacinamide, Vitamin A Code Code Code* Packaging Per Can L-Proline 0.76 0.16 Molybdenum, mcg 15.8 3.2 Palmitate, Vitamin D3, D-Calcium L-Serine 0.58 0.12 Chromium, mcg 16.2 3.3 • Provides 13 g of protein equivalent 5910 00847-0591-02 B4157 or B4162 4 x 400 g (14.1 oz) 1976 Pantothenate, D-Biotin, Copper per 100 g of powder L-Threonine 0.94 0.19 Selenium, mcg 44 8.9 Sulfate, Manganese Sulfate, Thiamin L-Tryptophan 0.69 0.14 Sodium, mg 303 61 ‡ Hydrochloride, Potassium Iodide, • Displacement: 0.7 mL/g WIC : Contact your state WIC For more reimbursement L-Tyrosine 1.14 0.23 Potassium, mg 797 161 Pyridoxine Hydrochloride, Sodium information see page 195. L-Valine Nil Added Nil Added office to determine availability. Chloride, mg 384 78 Selenite, Riboflavin, Vitamin 12B , Folic L-Carnitine 0.03 0.01 Acid, Chromium Chloride, Sodium Taurine 0.07 0.01 Molybdate. Metabolics * S9435 = For individuals who submit their bills to insurance on their own. CONTAINS: Coconut Oil, Soybean Oil. † Strauss KA et al. Mol Genet Metab. 2010;99:333-45.

76 77 Complex Essential MSD Drink Mix

Nutrition Information: Ingredients: Complex Essential MSD Drink Mix Per 10 g Protein Per 10 g Protein Sugar, L- Glutamine, Modified Food Equivalent Equivalent Starch, Dextrin, Canola Oil, Maltodextrin, Nutrients Per 100 g (1 scoop) Nutrients Per 100 g (1 scoop) Safflower Oil, L-Lysine Acetate, A valine-, leucine-, and isoleucine-free powdered medical food for the dietary management Calories 380 152 Vitamin A, IU (mcg RE) 1700 (637) 680 (255) L-Alanine, Natural and Artificial Flavor, of maple syrup urine disease (MSUD) in children and adults, including pregnant women and Protein Equivalent, g 25 10 (25% as beta-carotene) Tricalcium Phosphate, Potassium women of child bearing age. Fat, g 12 5 Vitamin D3, IU (mcg) 600 (15) 240 (6) Citrate, L-Phenylalanine, L-Tyrosine. Saturated, g 2.8 1.1 Vitamin E, IU (mg α-TE) 18.4 (12.3) 7.3 (4.9) Contains 2% or less of the following: Monounsaturated, g 6.3 2.5 Vitamin K, mcg 50 20 L-Threonine, L-Histidine, L-Asparagine Polyunsaturated, g 2.7 1.1 Thiamin, mg 1.5 0.6 Monohydrate, Magnesium Phosphate, Linoleic Acid, mg 1733 693 Riboflavin, mg 1.5 0.6 Sodium Chloride, L-Proline, Dipotassium Main Features: Indications: α-Linolenic Acid, mg 662 265 Vitamin B6, mg 1.3 0.52 Phosphate, L-Tryptophan, L-Arginine, • Maple syrup urine disease (MSUD) Carbohydrate, g 47 19 Vitamin B12, mcg 2 0.8 L-Serine, Coconut Oil, Soybean Oil, • Valine-, leucine-, and isoleucine-free Fiber, g 3.9 1.5 Niacin, mg 12 4.8 L-Glutamic Acid, L-Methionine, Glycine, • Amino acid profile specifically Amino Acids, g Folic Acid, mcg 250 100 L-Cystine, Flaxseed Oil, Titanium Dioxide, designed for MSUD; clinically L-Alanine 2.70 1.08 Pantothenic Acid, mg 5.5 2.2 Choline Bitartrate, Ascorbyl Palmitate, L-Arginine 1.28 0.51 Biotin, mcg 30 12 Mixed Tocopherols, Rosemary Extract, † For details on administration and household measurements, please researched in one study L-Asparagine 1.45 0.58 Vitamin C, mg 60 24 Sodium Citrate, Taurine, Ascorbic Acid, see pages 124-136. • Complete with essential vitamins L-Cystine 0.56 0.22 Choline, mg 100 40 L-Carnitine, Ferrous Sulfate, Inositol, L-Glutamic Acid 0.86 0.35 Inositol, mg 40 16 Vitamin E Acetate, Zinc Sulfate, Calcium and minerals L-Glutamine 7.17 2.87 Minerals Phosphate, Niacinamide, Copper Glycine 0.67 0.27 Calcium, mg 886 355 Gluconate, D-Calcium Pantothenate, • Provides 25 g of protein equivalent Ordering/Reimbursement Information: L-Histidine 1.79 0.71 Phosphorus, mg 864 346 Vitamin D3, Vitamin A Palmitate, Vitamin per 100 g powder L-Isoleucine Nil Added Nil Added Magnesium, mg 200 80 Product Reimbursement HCPCS Product Calories K1, Manganese Sulfate, Mono –and Code Code Code* Packaging Per Can L-Leucine Nil Added Nil Added Iron, mg 13 5 Diglycerides, D-Biotin, Beta-carotene, • Vanilla flavor L-Lysine 2.27 0.91 Zinc, mg 12 4.8 Chromium Chloride, Sodium Selenite, 5972 00847-0597-22 B4157 or B4162 4 x 454 g (1 lb) 1725 L-Methionine 0.74 0.30 • Osmolality (at 0.63 kcal/mL): Manganese, mg 1.5 0.6 Pyridoxine Hydrochloride, Riboflavin, L-Phenylalanine 2.20 0.88 Copper, mcg 1000 400 Potassium Iodide, Thiamin Mononitrate, 813 mOsm/kg L-Proline 1.48 0.59 Iodine, mcg 120 48 Folic Acid, Sodium Molybdate, Based on dilution of 40 g powder WIC‡: Contact your state WIC For more reimbursement L-Serine 1.12 0.45 Molybdenum, mcg 75 30 Vitamin B12. (1 scoop) to 7 fl oz (210 mL) water office to determine availability. information see page 195. L-Threonine 1.81 0.72 Chromium, mcg 40 16.1 L-Tryptophan 1.33 0.53 Selenium, mcg 100 40 CONTAINS: Coconut Oil, Soybean Oil. • Displacement: 0.75 mL/g L-Tyrosine 2.20 0.88 Sodium, mg 600 240

Metabolics * S9435 = For individuals who submit their bills to insurance on their own. L-Valine Nil Added Nil Added Potassium, mg 1301 520 L-Carnitine 0.06 0.02 Chloride, mg 860 344 Taurine 0.14 0.06 † Strauss KA et al. Mol Genet Metab. 2010;99:333-45. 78 79 Complex MSD Amino Acid Blends

Nutrition Information: Ingredients: Per 10 g Protein Per 10 g L-Glutamine, L-Lysine Acetate, L-Alanine, Complex MSD Amino Acid Blend Equivalent Protein Equivalent L-Phenylalanine, L-Tyrosine, L-Threonine, Nutrients Per 100 g (1 scoop) Amino Acids, g Per 100 g (1 scoop) L-Histidine, L-Asparagine Monohydrate, A valine-, leucine-, and isoleucine-free powdered medical food for the dietary management of Calories 323 40 L-Alanine 8.72 1.08 L-Proline, L-Tryptophan, L-Arginine, maple syrup urine disease (MSUD) in children and adults. Protein Equivalent, g 81 10 L-Arginine 4.13 0.51 L-Serine, L-Glutamic Acid, L-Methionine, Fat, g 0 0 L-Asparagine 4.67 0.58 Glycine, L-Cystine, Taurine, Silicon Carbohydrate, g 0 0 L-Cystine 1.80 0.22 Dioxide, L-Carnitine. L-Glutamic Acid 2.79 0.35 L-Glutamine 23.12 2.87 Note: Must combine with an appropriate Glycine 2.16 0.27 Main Features: Indications: vitamin & mineral supplement when L-Histidine 5.76 0.71 • Maple syrup urine disease (MSUD) taken as the sole source of amino acid • Valine-, leucine-, and isoleucine-free L-Isoleucine Nil Added Nil Added protein. L-Leucine Nil Added Nil Added • Amino acid profile specifically For details on administration and household measurements, please L-Lysine 7.32 0.91 designed for MSUD; clinically see pages 124-136. L-Methionine 2.38 0.30 researched in one study† L-Phenylalanine 7.08 0.88 L-Proline 4.76 0.59 • Does not contain fat, carbohydrates, L-Serine 3.60 0.45 vitamins and minerals L-Threonine 5.83 0.72 L-Tryptophan 4.28 0.53 • 40 calories per serving Ordering/Reimbursement Information: L-Tyrosine 7.08 0.88 • Provides 81 g of protein equivalent L-Valine Nil Added Nil Added per 100 g of powder Product Reimbursement HCPCS Product Calories L-Carnitine 0.19 0.02 Code Code Code* Packaging Per Can Taurine 0.46 0.06 • Unflavored 5900 00847-0590-00 B4155 or B9998 4 x 454 g (1 lb) 1466

• Displacement: 0.48 mL/g WIC‡: Contact your state WIC For more reimbursement office to determine availability. information see page 195. Metabolics † Strauss KA et al. Mol Genet Metab. 2010;99:333-45. * S9435 = For individuals who submit their bills to insurance on their own.

80 81 MSUD Maxamum

Nutrition Information: Ingredients: ® Per 10 g Per 10 g MSUD Maxamum Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Sugar, L-Lysine L-Glutamate, Corn Syrup Calories 305 76 Vitamin A, IU (mcg RE) 2228 (669) 557 (167) Solids, Calcium Phosphate Dibasic, L-Proline, L-Arginine, Glycine, L-Aspartic Protein Equivalent, g 40 10 Vitamin D , IU (mcg) 332 (8.3) 83 (2.1) A valine-, leucine-, and isoleucine-free powdered medical food for the dietary 3 Acid, L-Threonine, L-Phenylalanine, Fat, g <1 <0.25 management of maple syrup urine disease (MSUD) in older children and adults, including Vitamin E, IU (mg α-TE) 18.3 (12.3) 4.6 (3.1) L-Tyrosine, L-Serine, Artificial Flavor, pregnant women and women of child-bearing age. Carbohydrate, g 34 8.5 Vitamin K, mcg 82 21 L-Histidine, L-Alanine, Citric Acid, Amino Acids, g Thiamin, mg 0.91 0.23 Magnesium Acetate, L-Cystine, L-Alanine 2.4 0.60 Riboflavin, mg 0.97 0.24 L-Tryptophan, Tripotassium Citrate, Choline Bitartrate, L-Methionine, L-Arginine 4.1 1.03 Vitamin B6, mg 1.6 0.4 L-Aspartic Acid 3.4 0.85 Vitamin B , mcg 3.1 0.8 Sodium Chloride, Soy Lecithin, Disodium 12 Hydrogen Phosphate, Dipotassium Main Features: Indications: L-Cystine 1.6 0.40 Niacin, mg 5.7 1.4 Hydrogen Phosphate, L-Glutamine, • Valine-, leucine-, and isoleucine-free • Maple syrup urine disease (MSUD) L-Glutamic Acid 4.6 1.15 Folic Acid, mcg 491 123 Tricalcium Phosphate, L-Glutamic Acid, Glycine 3.7 0.93 Pantothenic Acid, mg 4.9 1.2 • Contains a balanced mixture of all other Taurine, L-Ascorbic Acid, M-Inositol, L-Histidine 2.3 0.58 Biotin, mcg 24.5 6.1 Ferrous Sulfate, L-Carnitine, Zinc Sulfate, essential and non-essential amino acids, L-Isoleucine Nil Added Nil Added Vitamin C, mg 62 16 DL-Alpha Tocopheryl Acetate, carbohydrate, vitamins, minerals and For details on administration and household measurements, please L-Leucine Nil Added Nil Added Choline, mg 430 108 Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric trace elements see pages 124-136. L-Lysine 4.2 1.05 Inositol, mg 80 20 Sulfate, Pyridoxine Hydrochloride, L-Methionine 0.99 0.25 • Age-appropriate DRI formulation Minerals Sodium Selenite, Thiamin Chloride • MSUD Maxamum provides L-Phenylalanine 2.8 0.70 Calcium, mg 1183 296 Hydrochloride, Riboflavin, Vitamin A 40 g of protein equivalent per L-Proline 4.5 1.13 Phosphorus, mg 1137 284 Acetate, Folic Acid, Artificial Colors L-Serine 2.8 0.70 Magnesium, mg 306 77 (Beta-Carotene, Beet Red), Potassium 100 g of powder Ordering/Reimbursement Information: L-Threonine 3.1 0.78 Iron, mg 14.7 3.7 Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, • Available in orange flavor Product Reimbursement HCPCS Product Calories L-Tryptophan 1.3 0.33 Zinc, mg 9 2 Vitamin D , Cyanocobalamin. • Contains <1 g of fat per 10 g PE thereby Code Code Code* Packaging Per Can L-Tyrosine 2.8 0.70 Manganese, mg 1.8 0.5 3 allowing greater flexibility in modifying 117789 49735-0177-89 B4157 or 6 x 454 g (1 lb) 1385 L-Valine Nil Added Nil Added Copper, mcg 820 205 CONTAINS: Soy. energy intake B4162 L-Carnitine 0.04 0.01 Iodine, mcg 131 33 Taurine 0.14 0.04 Molybdenum, mcg 37 9 • Osmolality (mOsm/kg): WIC‡: Contact your state WIC For more reimbursement L-Glutamine 0.32 0.08 Chromium, mcg 26 7 Dilution

Metabolics office to determine availability. information see page 195. Selenium, mcg 58 15 1 to 7 750 Sodium, mg 560 140 1 to 5 1090 Potassium, mg 700 175 • Displacement: 0.6 mL/g Chloride, mg 560 140 82 * S9435 = For individuals who submit their bills to insurance on their own. 83 MSUD Lophlex LQ

Nutrition Information: ® Ingredients: MSUD Lophlex LQ Per Pouch Per 10 g Per Pouch Per 10 g Nutrients (4.2 fl oz) Protein Equivalent Vitamins (4.2 fl oz) Protein Equivalent Water, Apple Juice from Concentrate (34.1%), Grape Juice from Concentrate A valine-, leucine-, and isoleucine-free* ready-to-drink medical food containing amino Calories 120 60 Vitamin A, IU (mcg RE) 949.(285 475.(143) (6.9%), Blackcurrant Juice from Concentrate (2.5%), L-Lysine Acetate, acids, carbohydrates, vitamins, minerals and DHA, based on mixed fruit juices (from Protein Equivalent, g 20 10 Vitamin D3, IU (mcg) 320.(8.0) 160.(4.0) Fat, g 0.44 0.22 L-Proline, Citric Acid, L-Tyrosine, concentrate) with natural flavor; for the dietary management of proven maple syrup Vitamin E, IU (mg α-TE) 4.8 (3.2) 2.4 (1.6) L-Arginine, Glycine, L-Serine, L-Aspartic DHA, mg 150 75 Vitamin K, mcg 24.9 12.5 Acid, L-Alanine, L-Threonine, Corn urine disease (MSUD) in individuals 4 years and older, including pregnant women and Carbohydrate, g 9.3 4.7 Thiamin, mg 0.54 0.27 Syrup Solids, L-Cystine, L-Phenylalanine, women of child-bearing age. Dicalcium Phosphate, L-Histidine, Fiber, g 0.50 0.25 Riboflavin, mg 0.50 0.25 Elderberry Juice from Concentrate Amino Acids, Vitamin B6, mg 0.58 0.29 (0.6%), Maltodextrin, Magnesium Acetate, L-Alanine 1.40 0.70 Vitamin B , mcg 1.8 0.90 N-Acetyl L-Methionine, L-Tryptophan, 12 Choline Bitartrate, C. Cohnii Oil*, Sugar, Main Features: Indications: L-Arginine 1.90 0.95 Niacin, mg 7.1 3.6 Microcrystalline Cellulose, Natural L-Aspartic Acid 1.45 0.73 Folic Acid, mcg 120 60.0 Flavor, Fruit Concentrate (Apple, • Maple syrup urine disease (MSUD) • Valine-, leucine-, and isoleucine-free L-Cystine 1.20 0.60 Pantothenic Acid, mg 1.8 0.9 Blackcurrant, Radish), L-Ascorbic Acid, Taurine, Guar Gum, Sunflower Lecithin, Glycine 1.90 0.95 • Low volume; provides 20 g PE in just 4.2 For details on administration, please see pages 124-136. Biotin, mcg 53.4 26.7 Xanthan Gum, M-Inositol, Potassium fl oz (125 mL) L-Histidine 1.00 0.50 Vitamin C, mg 17.8 8.9 Sorbate (preservative to delay spoilage), L-Isoleucine Trace* Trace* Artificial Sweetener: Sucralose, • Convenient ready-to-drink Choline, mg 153 76.5 Ferrous Lactate, Artificial Sweetener: L-Leucine Trace* Trace* Inositol, mg 40.6 20.3 Acesulfame Potassium, Sodium Benzoate • Based on fruit juices (from concentrate) L-Lysine 1.78 0.89 Mineral (preservative to delay spoilage), Zinc Sulfate, L-Carnitine, Niacinamide, with natural flavor - no artificial flavors L-Methionine 0.43 0.22 Calcium, mg 319 160 DL-alpha Tocopheryl Acetate, Calcium • Contains a balanced mixture of L-Phenylalanine 1.18 0.59 Phosphorus, mg 244 122 D-Pantothenate, Manganese Sulfate, L-Proline 2.38 1.19 Magnesium, mg 96.3 48.2 Cupric Sulfate, Thiamin Chloride other essential and non-essential amino Ordering/Reimbursement Information: Hydrochloride, Pyridoxine Hydrochloride, acids, carbohydrates, vitamins, minerals Product Reimbursement HCPCS Product Calories L-Serine 1.65 0.83 Iron, mg 5.1 2.6 Vitamin A Palmitate, Riboflavin, Folic Code Code Code* Packaging Per Pouch L-Threonine 1.30 0.65 Zinc, mg 3.8 1.9 Acid, Potassium Iodide, Ascorbyl and DHA Palmitate, Mixed Tocopherols, Sodium 82112 49735-0167-49 B4157 or B4162 30 X 4.2 fl oz (125 mL) 120 L-Tryptophan 0.53 0.27 Manganese, mg 0.56 0.28 • Provides 150 mg DHA per pouch Molybdate, D-Biotin, Sodium Selenite, L-Tyrosine 2.00 1.00 Copper, mcg 563 282 Chromium Chloride, Phylloquinone, • Available in mixed berry blast flavor L-Valine Trace* Trace* Iodine, mcg 56.3 28.2 Vitamin D , Cyanocobalamin. WIC‡: Contact your state WIC For more reimbursement 3 L-Carnitine 0.01 0.01 Molybdenum, mcg 25.0 12.5 • Osmolality (at 0.96 kcal/mL): office to determine availability. information see page 195. Contains 44.1% juice. Taurine 0.06 0.03 Chromium, mcg 10.8 5.4 2460 mOsm/kg *A Source of Docosahexaenoic Acid

Metabolics Selenium, mcg 26.8 13.4 * S9435 = For individuals who submit their bills to insurance on their own. (DHA). Sodium, mg <25.0 <12.5 Potassium, mg 90 45 *May contain traces of leucine, isoleucine and valine from fruit juice (from concentrate) at a level of <1.5 mg per 100 mL. Chloride, mg <25.0 <12.5 84 85 IVA Early Years Anamix

Nutrition Information: Per 10 g Per 10 g Ingredients: ® IVA Anamix Early Years Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Corn Syrup Solids, Refined Vegetable Calories 473 350 Vitamin A, IU (mcg RE) 1305.(392) 967.(290) Oils (High Oleic Sunflower, Soy, Non-Hydrogenated Coconut, Canola, A leucine-free powdered infant formula with iron, for the dietary management of Protein Equivalent,g 13.5 10.0 Vitamin D3, IU (mcg) 348.(8.7) 258.(6.4) Fat, g 23.0 17.0 Vitamin E, IU (mg α-TE) 10.9 (7.3) 8.1 (5.4) Sunflower), Galacto-oligosaccharides isovaleric acidemia (IVA). Contains DHA and ARA, and a unique blend of prebiotic fiber. Saturated, g 7.5 5.6 Vitamin K, mcg 38.0 28.1 (GOS) Dried Syrup (from milk), L-Lysine Monounsaturated, g 9.4 7.0 Thiamin, mcg 640 474 L-Glutamate, L-Proline, Glycine, L-Arginine, Tricalcium Phosphate, Polyunsaturated, g 5.0 3.7 Riboflavin, mcg 500 370 L-Aspartic Acid, CAEM (an emulsifier), DHA, mg 70.0 51.9 Vitamin B6, mcg 500 370 L-Tyrosine, L-Phenylalanine, L-Alanine, ARA, mg 140 104 Main Features: Indications: Vitamin B12, mcg 1.2 0.89 L-Threonine, L-Histidine, L-Serine, Linoleic Acid,mg 3500 2593 Niacin, mcg 2200 1630 Potassium Chloride, Fructo- Carbohydrate, g 53.0 39.3 • Leucine-free powdered infant formula • Isovaleric acidemia Folic Acid, mcg 55.0 40.7 oligosaccharides (FOS), Tripotassium Fiber, g 5.3 3.9 Pantothenic Acid, mcg 2800 2074 Citrate, L-Valine, L-Cystine, L-Isoleucine, with iron • Other proven disorders of leucine metabolism GOS, g 4.7 3.5 Biotin, mcg 18.2 13.5 Sodium Phosphate Dibasic, Magnesium • Includes DHA & ARA FOS, g 0.55 0.41 Vitamin C, mg 49.0 36.3 Acetate, M. Alpina Oil*, L-Methionine, Amino Acids, g Choline, mg 91.0 67.4 L-Glutamic Acid, L-Tryptophan, Choline • Contains a prebiotic fiber blend L-Alanine 0.74 0.55 Inositol, mg 98.0 72.6 Bitartrate, C. Cohnii Oil**, L-Glutamine, Sodium Chloride, M-Inositol, L-Ascorbic • Unflavored powder For details on administration and household measurements, please L-Arginine 1.21 0.90 Minerals L-Aspartic Acid 1.02 0.76 Calcium, mg 371 275 Acid, Taurine, Ferrous Sulfate, Zinc see pages 124-136. Sulfate, L-Carnitine, DL-Alpha Tocopheryl • Contains a balanced mixture of all other L-Cystine 0.44 0.33 Phosphorus, mg 270 200 Acetate, Calcium D-Pantothenate, essential and non-essential amino acids, L-Glutamic Acid 1.35 1 Magnesium, mg 52.5 38.9 Niacinamide, Ascorbyl Palmitate, carbohydrates, fat, vitamins, minerals L-Glutamine 0.11 0.08 Iron, mg 7.3 5.4 Manganese Sulfate, Cupric Sulfate, and trace elements Ordering/Reimbursement Information: Glycine 2.18 1.6 Zinc, mg 5.2 3.9 Thiamine Chloride Hydrochloride, L-Histidine 0.7 0.52 Manganese, mcg 390 289 Pyridoxine Hydrochloride, Riboflavin, • Provides 13.5 g of protein equivalent Product Reimbursement HCPCS Product Calories L-Isoleucine 0.42 0.31 Copper, mcg 390 289 Vitamin A Acetate, DL-alpha Tocopherol, Code Code Code* Packaging Per Can per 100 g of powder L-Leucine Nil Added Nil Added Iodine, mcg 82.5 61.1 Mixed Tocopherols, Potassium Iodide, 90211 49735-0102-11 B4162 6 x 400 g (14 oz) 1892 L-Lysine 1.06 0.79 Molybdenum, mcg 10.9 8.1 Chromium Chloride, Folic Acid, • Osmolality (at 0.7 kcal/mL): L-Methionine 0.3 0.22 Chromium, mcg 12.5 9.3 Phylloquinone, Sodium Selenite, Sodium 380 mOsm/kg L-Phenylalanine 0.82 0.61 Selenium, mcg 14.1 10.4 Molybdate, D-Biotin, Vitamin D3, Based on dilution of 5 g powder WIC‡: Contact your state WIC For more reimbursement L-Proline 2.19 1.6 Sodium, mg 171 127 Cyanocobalamin. (1 unpacked level scoop) to 1 fl oz office to determine availability. information see page 195. L-Serine 0.68 0.50 Potassium, mg 454 336 CONTAINS: Soy Oil, Coconut Oil, Milk. L-Threonine 0.72 0.53 Chloride, mg 321 238 (30 mL) water L-Tryptophan 0.27 0.20 *A source of Arachidonic Acid (ARA)

Metabolics * S9435 = For individuals who submit their bills to insurance on their own. • Displacement: 0.75 mL/g L-Tyrosine 0.8 0.59 **A source of Docosahexaenoic Acid L-Valine 0.48 0.36 (DHA) L-Carnitine 0.01 0.01 Taurine 0.02 0.01 Contains GOS/FOS 0.8 g per 100 mL 86 87 IVA Next Anamix

Nutrition Information: Per 10 g Per 10 g Ingredients: ® Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent IVA Anamix Next Calories 377 134.6 Vitamin A, IU (mcg R.E.) 1748.(525) 628.(187.5) Corn Syrup Solids, Refined Vegetable Oils (High Oleic Sunflower, Canola, Medium Protein Equivalent, g 28 10 Vitamin D3, IU (mcg) 1052.(26.3) 379.(9.4) Chain Triglycerides (Palm Kernel and/ A leucine-free powdered medical food for the dietary management of isovaleric Fat, g 12.5 4.5 Vitamin E, IU (mg-α-TE) 15.6.(10.5) 5.6.(3.8) or Coconut Oil), Sunflower), Glycine, Vitamin K, mcg 17.5 6.3 acidemia in individuals over 1 year of age. Saturated, g 2.0 0.71 L-Proline, Calcium Phosphate Dibasic, Thiamin, mg 1.2 0.43 Monounsaturated, g 8.2 2.9 Fructo-oligosaccharides, L-Glutamine, Polyunsaturated, g 1.8 0.64 Riboflavin, mg 0.91 0.33 Inulin, L-Lysine Acetate, Corn Starch, Vitamin B , mg 0.91 0.33 DHA, mg 180 64 6 Microcrystalline Cellulose, L-Arginine, Vitamin B , mcg 1.6 0.57 Carbohydrate, g 41.2 14.7 12 Artificial Flavor, Magnesium L-Aspartate, Fiber, g 11.2 4.0 Niacin, mg 2.5 0.89 Gum Arabic, L-Glutamic Acid, L-Tyrosine, Main Features: Indications: Soluble, g 8.0 2.9 Folic Acid, mcg 263 93.9 L-Phenylalanine, Tripotassium Citrate, Insoluble, g 3.2 1.1 Pantothenic Acid, mg 5.3 1.9 L-Threonine, L-Serine, L-Histidine, • Leucine-free • Isovaleric acidemia Amino Acids, g Biotin, mcg 14 5 L-Alanine, L-Valine, Trisodium Citrate, L-Cystine, L-Isoleucine, Maltodextrin, L-Alanine 1.35 0.48 Vitamin C, mg 52.5 18.8 • Contains a balanced mixture of all other Choline Bitartrate, Calcium Chloride, For details on administration and household measurements, please L-Arginine 2.35 0.84 Choline, mg 280 100 essential and non-essential amino acids, L-Methionine, L-Tryptophan, CAEM (an see pages 124-136. L-Aspartic Acid 2.0 0.71 Inositol, mg 70 25 carbohydrate (including a multi-fiber Minerals emulsifier), C. Cohnii Oil*, L-Aspartic L-Cystine 0.94 0.34 Acid, Sodium Chloride, L-Ascorbic Acid, blend), fat (including DHA), vitamins, Calcium, mg 1225 437.5 L-Glutamic acid 1.88 0.67 M-Inositol, Soy Fiber, Taurine, Ferrous Phosphorus, mg 801 286.1 minerals, and trace elements L-Glutamine 3.16 1.1 Sulfate, Sunflower Lecithin, L-Carnitine, • Provides 28 g protein equivalent and Glycine 4.6 1.6 Magnesium, mg 140 50 Zinc Sulfate, DL-alpha Tocopheryl Acetate, Iron, mg 12.5 4.5 12.5 g fat per 100 g of powder L-Histidine 1.4 0.50 Calcium D-Pantothenate, Manganese Ordering/Reimbursement Information: L-Isoleucine 0.92 0.33 Zinc, mg 6.1 2.2 Sulfate, Niacinamide, Cupric Sulfate, • Available in Plain L-Leucine Nil Added Nil Added Manganese, mg 1.2 0.4 Thiamine Chloride Hydrochloride, Product Reimbursement HCPCS Product Calories L-Lysine 2.2 0.79 Copper, mcg 700 250 Pyridoxine Hydrochloride, Riboflavin, • Osmolality (at 1.1 kcal/mL): Code Code Code* Packaging Per Can 1220 mOsm/kg L-Methionine 0.64 0.23 Iodine, mcg 174 62.1 Vitamin A Acetate, Folic Acid, Ascorbyl 89471 49735-0194-71 B4157 or 6 x 400 g (14 oz) 1508 L-Phenylalanine 1.7 0.61 Molybdenum, mcg 31.9 11.4 Palmitate, Potassium iodide, Mixed Based on dilution of 36 g powder B4162 Tocopherols, Sodium Molybdate, Sodium L-Proline 4.1 1.5 Chromium, mcg 12.8 4.6 (approx. 4 scoops) to 3.5 fl oz Selenite, Chromium Chloride, DL-alpha L-Serine 1.5 0.52 Selenium, mcg 35.3 12.6 Tocopherol, Vitamin D , Phylloquinone, (100 mL) water WIC‡: Contact your state WIC For more reimbursement Sodium, mg 350 125 3 L-Threonine 1.5 0.54 D-Biotin, Cyanocobalamin. • Displacement: 0.72 mL/g office to determine availability. information see page 195. L-Tryptophan 0.58 0.21 Potassium, mg 556 198.6 Metabolics L-Tyrosine 1.7 0.61 Chloride, mg 508 181.4 CONTAINS: Coconut Oil, Soy. * S9435 = For individuals who submit their bills to insurance on their own. L-Valine 1.0 0.37 *A source of Docosahexaenoic Acid L-Carnitine 0.02 0.01 (DHA) Taurine 0.06 0.02 88 89 XLeu Maxamum

® Nutrition Information: Ingredients: XLeu Maxamum Per 10 g Per 10 g Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Sugar, L-Lysine L-Glutamate, L-Proline, A leucine-free powdered medical food for the dietary management of isovaleric acidemia Calories 305 76 Vitamin A, IU (mcg RE) 2228 (669) 557 (167) Glycine, Corn Syrup Solids, Calcium Phosphate Dibasic, L-Arginine, L-Aspartic Protein Equivalent, g 40 10 Vitamin D , IU (mcg) 332 (8.3) 83 (2.1) and other proven disorders of leucine metabolism in older children and adults, including 3 Acid, L-Phenylalanine, Artificial Flavor, Fat, g <1 pregnant women and women of child-bearing age. <0.25 Vitamin E, IU (mg α-TE) 18.3 (12.3) 4.6 (3.1) L-Tyrosine, L-Alanine, L-Threonine, Citric Carbohydrate, g 34 8.5 Vitamin K, mcg 82 21 Acid, L-Histidine, L-Serine, Magnesium Amino Acids, g Thiamin, mg 0.91 0.23 Acetate, L-Valine, L-Cystine, L-Isoleucine, L-Alanine 2.2 0.55 Riboflavin, mg 0.97 0.24 Tripotassium Citrate, Choline Bitartrate, L-Arginine 3.6 Sodium Chloride, L-Methionine, 0.90 Vitamin B6, mg 1.6 0.4 L-Aspartic Acid 3 0.75 Vitamin B , mcg 3.1 0.8 L-Glutamic Acid, L-Tryptophan, Soy Main Features: Indications: 12 Lecithin, Disodium Hydrogen Phosphate, L-Cystine 1.3 0.33 Niacin, mg 5.7 1.4 Dipotassium Hydrogen Phosphate, • Leucine-free • Isovaleric acidemia L-Glutamic Acid 3.9 0.98 Folic Acid, mcg 491 123 L-Glutamine, Tricalcium Phosphate, • Contains a balanced mixture of all other • Other proven disorders of leucine metabolism Glycine 6.3 1.58 Pantothenic Acid, mg 4.9 1.2 Taurine, L-Ascorbic Acid, M-Inositol, essential and non-essential amino acids, L-Histidine 2.1 0.53 Biotin, mcg 24.5 6.1 Ferrous Sulfate, L-Carnitine, Zinc carbohydrate, vitamins, minerals and L-Isoleucine 1.2 0.30 Vitamin C, mg 62 16 Sulfate, DL-Alpha Tocopheryl Acetate, L-Leucine Nil Added Nil Added Choline, mg 430 108 Niacinamide, Manganese Sulfate, trace elements (including iron, selenium Calcium D-Pantothenate, Cupric For details on administration and household measurements, please L-Lysine 3 0.75 Inositol, mg 80 20 and chromium) Sulfate, Pyridoxine Hydrochloride, L-Methionine 0.86 see pages 124-136. 0.22 Minerals Sodium Selenite, Thiamin Chloride • Age-appropriate DRI formulation L-Phenylalanine 2.3 0.58 Calcium, mg 1183 296 Hydrochloride, Riboflavin, Vitamin A • XLeu Maxamum provides 40 g of L-Proline 6.3 1.58 Phosphorus, mg 1137 284 Acetate, Folic Acid, Artificial Colors protein equivalent per 100 g of powder L-Serine 1.9 0.48 Magnesium, mg 306 77 (Beta-Carotene, Beet Red), Potassium Ordering/Reimbursement Information: L-Threonine 2.1 0.53 Iron, mg 14.7 3.7 Iodide, Chromium Chloride, Sodium • Available in orange flavor L-Tryptophan 0.79 0.20 Zinc, mg 9 2 Molybdate, Phylloquinone, D-Biotin, Product Reimbursement HCPCS Product Calories Vitamin D , Cyanocobalamin. • Contains <1 g of fat per 10 g PE Code Code Code* Packaging Per Can L-Tyrosine 2.3 0.58 Manganese, mg 1.8 0.5 3 thereby allowing greater flexibility in 117790 49735-0177-90 B4157 or 6 x 454 g (1 lb) 1385 L-Valine 1.4 0.35 Copper, mcg 820 205 CONTAINS: Soy. modifying energy intake B4162 L-Carnitine 0.04 0.01 Iodine, mcg 131 33 • Osmolality (mOsm/kg): Taurine 0.14 0.04 Molybdenum, mcg 37 9 Dilution WIC‡: Contact your state WIC For more reimbursement L-Glutamine 0.32 0.08 Chromium, mcg 26 7 Metabolics 1 to 7 800 office to determine availability. information see page 195. Selenium, mcg 58 15 1 to 5 1120 Sodium, mg 560 140 * S9435 = For individuals who submit their bills to insurance on their own. Potassium, mg 700 175 • Displacement: 0.6 mL/g Chloride, mg 560 140 90 91 GA-1 Anamix Early Years

Nutrition Information: Ingredients: Per 10 g ® Per 10 g GA-1 Anamix Early Years Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Corn Syrup Solids, Refined Vegetable Calories 473 350 Vitamin A, IU (mcg RE) 1305.(392) 967.(290) Oils (High Oleic Sunflower, Soy, Protein Equivalent,g 13.5 10.0 Non-hydrogenated Coconut, Canola, A lysine-free, low tryptophan powdered infant formula with iron, for the Vitamin D3, IU (mcg) 348.(8.7) 258.(6.4) Fat, g 23.0 17.0 Vitamin E, IU (mg α-TE) 10.9 (7.3) 8.1 (5.4) Sunflower), Galacto-oligosacharides dietary management of glutaric aciduria type 1 (GA-1). Contains DHA and Saturated, g 7.5 5.6 Vitamin K, mcg 38.0 28.1 (GOS) Dried Syrup (from milk), L-Leucine, ARA, and a unique blend of prebiotic fiber. Monounsaturated, g 9.4 7.0 Thiamin, mcg 640 474 L-Glutamic Acid, L-Proline, L-Arginine, Polyunsaturated, g 5.0 3.7 Riboflavin, mcg 500 370 L-Valine, L-Isoleucine, Tricalcium Phosphate, Glycine, L-Aspartic Acid, DHA, mg 70.0 51.9 Vitamin B6, mcg 500 370 ARA, mg 140 104 Vitamin B , mcg 1.2 0.89 CAEM (an emulsifier), L-Threonine, 12 L-Tyrosine, L-Phenylalanine, L-Serine, Main Features: Indications: Linoleic Acid,mg 3500 2593 Niacin, mcg 2200 1630 Carbohydrate, g 53.0 39.3 Folic Acid, mcg 55.0 40.7 L-Histidine, L-Alanine, Potassium Fiber, g 5.3 3.9 Pantothenic Acid, mcg 2800 2074 Chloride, Fructo-oligosaccharides (FOS), • Lysine-free, low tryptophan • Glutaric acidemia type I Tripotassium Citrate, L-Cystine, Sodium powdered infant formula with iron GOS, g 4.7 3.5 Biotin, mcg 18.2 13.5 FOS, g 0.55 0.41 Vitamin C, mg 49.0 36.3 Phosphate Dibasic, Magnesium Acetate, • Includes DHA & ARA Amino Acids, g Choline, mg 91.0 67.4 M. Alpina Oil*, L-Methionine, Choline Bitartrate, C. Cohnii Oil**, L-Glutamine, For details on administration and household measurements, please L-Alanine 0.68 0.50 Inositol, mg 98.0 72.6 • Contains a prebiotic fiber blend L-Arginine 1.18 0.87 Minerals Sodium Chloride, M-Inositol, L-Ascorbic • Unflavored powder see pages 124-136. L-Aspartic Acid 0.98 0.73 Calcium, mg 371 275 Acid, L-Tryptophan, Taurine, Ferrous L-Cystine 0.45 0.33 Phosphorus, mg 270 200 Sulfate, Zinc Sulfate, L-Carnitine, • Contains a balanced mixture of all L-Glutamic Acid 1.33 0.99 Magnesium, mg 52.5 38.9 DL-alpha Tocopheryl Acetate, Calcium other essential and non-essential Ordering/Reimbursement Information: L-Glutamine 0.11 0.08 Iron, mg 7.3 5.4 D-Pantothenate, Niacinamide, amino acids, carbohydrates, fat, Glycine 1.06 0.79 Zinc, mg 5.2 3.9 Ascorbyl Palmitate, Manganese Sulfate, vitamins, minerals and trace elements Product Reimbursement HCPCS Product Calories L-Histidine 0.68 0.50 Manganese, mcg 390 289 Cupric Sulfate, Thiamine Chloride Code Code Code* Packaging Per Can L-Isoleucine 1.06 0.79 Copper, mcg 390 289 Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, DL-alpha • Provides 13.5 g of protein equivalent 90217 49735-0102-17 B4162 6 x 400 g (14 oz) 1892 L-Leucine 1.81 1.3 Iodine, mcg 82.5 61.1 per 100 g of powder L-Lysine Nil Added Nil Added Molybdenum, mcg 10.9 8.1 Tocopherol, Mixed Tocopherols, Potassium Iodide, Chromium Chloride, • Osmolality (at 0.7 kcal/mL): L-Methionine 0.29 0.21 Chromium, mcg 12.5 9.3 WIC‡: Contact your state WIC For more reimbursement L-Phenylalanine 0.8 0.59 Selenium, mcg 14.1 10.4 Folic Acid, Phylloquinone, Sodium 380 mOsm/kg office to determine availability. information see page 195. L-Proline 1.29 0.96 Sodium, mg 171 127 Selenite, Sodium Molybdate, D-Biotin, Based on dilution of 5 g powder L-Serine 0.8 0.59 Potassium, mg 454 336 Vitamin D3, Cyanocobalamin (1 unpacked level scoop) to 1 fl oz L-Threonine 0.89 0.66 Chloride, mg 321 238 CONTAINS: Soy Oil, Coconut Oil, Milk. * S9435 = For individuals who submit their bills to insurance on their own. L-Tryptophan 0.09 0.07 Metabolics (30 mL) water L-Tyrosine 0.8 0.59 *A source of Arachidonic Acid (ARA) • Displacement: 0.75 mL/g L-Valine 1.16 0.86 **A source of Docosahexaenoic Acid L-Carnitine 0.01 0.01 (DHA) Taurine 0.02 0.01 92 Contains GOS/FOS 0.8 g per 100 mL 93 GlutarAde Junior GA-1 Drink Mix

Nutrition Information: Ingredients: ™ Nutrients Per 100 g Per 100 kcal Vitamins Per 100 g Per 100 kcal Corn Syrup Solids, Modified Corn Starch, GlutarAde Junior GA-1 Drink Mix Calories 410 100 Vitamin A, IU (mcg RE) 1373.(412 335.(101) Canola Oil, Maltodextrin, Safflower Oil, Protein Equivalent, g 10 2.5 Vitamin D3, IU (mcg) 525.(13.1) 128.(3.2) Natural and Artificial Flavor. Contains A lysine-free and low tryptophan powdered medical food for the dietary management of Fat, g 10 2.5 Vitamin E, IU (mg α-TE) 8.5 (5.7) 2.1 (1.4) 2% or less of the following: L-Glutamine, glutaric aciduria type 1 (GA-1) in young children. Saturated, g 2.2 0.55 Vitamin K, mcg 34 8.3 L-Leucine, Tricalcium Phosphate, Monounsaturated, g 5.2 1.3 Thiamin, mg 0.83 0.2 L-Arginine, L-Valine, Coconut Oil, Polyunsaturated, g 2.6 0.63 Riboflavin, mg 0.69 0.17 Soybean Oil, L-Isoleucine, L-Asparagine Linoleic Acid, mg 1487 363 Vitamin B6, mg 0.66 0.16 Monohydrate, Dipotassium Phosphate, α-Linolenic Acid, mg 815 199 Vitamin B12, mcg 1.4 0.35 Flaxseed Oil, L-Tyrosine, L-Phenylalanine, Carbohydrate, g 69 17 Niacin, mg 6.6 1.6 L-Threonine, L-Proline, Choline Bitartrate, Main Features: Indications: Amino Acids, g Folic Acid, mcg 150 37 Potassium Chloride, L-Ornithine-Alpha • Glutaric acidemia type I L-Alanine 0.48 0.12 Pantothenic Acid, mg 6 1.5 Ketoglutarate, L-Alanine, Magnesium • Lysine-free L-Arginine 1.08 0.26 Biotin, mcg 31 7.6 Phosphate, L-Methionine, L-Glutamic L-Asparagine 0.72 0.18 Vitamin C, mg 56 13.6 • Amino acid profile specifically For details on administration and household measurements, please Acid, L-Histidine, Glycine, L-Serine, L-Cystine 0.18 0.04 Choline, mg 213 52 Ascorbyl Palmitate, Sodium Citrate, designed for GA-1; clinically see pages 124-136. L-Glutamic Acid 0.36 0.09 Inositol, mg 125 30 researched in one study† Mixed Tocopherols, Rosemary L-Glutamine 1.80 0.44 Minerals Extract, L-Cystine, Sodium Chloride, • Contains arginine and 60 mg of Glycine 0.24 0.06 Calcium, mg 460 112 Inositol, Silicon Dioxide, Ascorbic Acid, L-Histidine 0.36 0.09 Phosphorus, mg 400 97 L-Tryptophan, Taurine, Ferrous Sulfate, tryptophan per 100 g powder L-Isoleucine 0.84 0.21 Magnesium, mg 60 14.6 Calcium Phosphate, L-Carnitine, Zinc L-Leucine 1.38 0.34 Iron, mg 8 2 • Contains a source of Omega-3 Sulfate, Vitamin E Acetate, Niacinamide, L-Lysine Nil Added Nil Added Zinc, mg 7 1.6 fatty acids Ordering/Reimbursement Information: Calcium D-Pantothenate, Mono- and L-Methionine 0.41 0.10 Manganese, mg 0.43 0.1 Diglycerides, Vitamin A Palmitate, • Complete with vitamins and minerals Product Reimbursement HCPCS Product Calories L-Ornithine 0.24 0.06 Copper, mcg 500 122 Vitamin D3, Copper Gluconate, Vitamin Code Code Code* Packaging Per Can L-Phenylalanine 0.64 0.16 Iodine, mcg 90 22 • Plain flavor K1, D-Biotin, Manganese Sulfate, 7510 00847-0751-02 B4157 or B4162 4 x 400 g (14.1 oz) 1640 L-Proline 0.60 0.15 Molybdenum, mcg 18 4.4 • Provides 10 g protein equivalent per L-Serine 0.24 0.06 Chromium, mcg 12 2.9 Sodium Selenite, Thiamin Mononitrate, L-Threonine 0.64 0.16 Selenium, mcg 40 9.7 Pyridoxine Hydrochloride, Riboflavin, 100 g powder Potassium Iodide, Chromium Chloride, ‡ L-Tryptophan 0.06 0.01 Sodium, mg 221 54 WIC : Contact your state WIC For more reimbursement Folic Acid, Vitamin B12, Sodium • Displacement: 0.6 mL/g L-Tyrosine 0.72 0.18 Potassium, mg 589 144 information see page 195. office to determine availability. L-Valine 0.96 0.23 Chloride, mg 332 81 Molybdate. L-Carnitine 0.03 0.01 CONTAINS: Coconut Oil, Soybean Oil.

Metabolics Taurine 0.06 0.01 † Strauss KA, et al. Mol Genet Metab. 2011. * S9435 = For individuals who submit their bills to insurance on their own.

94 95 GlutarAde Essential GA-1GlutarAde Drink Mix

Nutrition Information: Ingredients: ™ Per 10 g Protein Equivalent Per 10 g Protein Equivalent Sugar, Modified Corn Starch, Canola Oil, GlutarAde Essential GA-1 Drink Mix Nutrients Per 100 g (1 scoop) Vitamins Per 100 g (1 scoop) Maltodextrin, Safflower Oil, Dextrin, Calories 385 154 Vitamin A, IU (mcg RE) 1700.(637) 680.(255) L-Glutamine, L-Leucine, Natural and A lysine-free and low tryptophan powdered medical food for the dietary management of Protein Equivalent, g 25 10 (25% as beta-carotene) Artificial Flavor, L-Arginine, Dicalcium Fat, g 13 5 glutaric aciduria type 1 (GA-1) in children and adults, including pregnant women and women Vitamin D3, IU (mcg) 600.(15) 240.(6) Phosphate, L-Valine, L-Isoleucine, Saturated, g 3.1 1.2 Vitamin E, IU (mg α-TE) 19.1 (12.8) 7.6 (5.1) of child bearing age. Monounsaturated, g 6.9 2.8 L-Asparagine Monohydrate. Contains Vitamin K, mcg 70 28 2% or less of the following: L-Tyrosine, Polyunsaturated, g 2.9 1.2 Thiamin, mg 1.5 0.6 Linoleic Acid, mg 1936 774 Riboflavin, mg 1.5 0.6 Tricalcium Phosphate, L-Phenylalanine, α-Linolenic Acid, mg 730 292 Vitamin B6, mg 1.4 0.56 L-Threonine, L-Proline, Potassium Carbohydrate, g 45 18 Vitamin B12, mcg 3 1.2 Citrate, L-Ornithine-Alpha Ketoglutarate, Main Features: Indications: Fiber, g 3.9 1.5 Niacin, mg 15.5 6.2 L-Alanine, Coconut Oil, Soybean Oil, Amino Acids, g Folic Acid, mcg 300 120 L-Methionine, Sodium Citrate, Potassium • Glutaric acidemia type I L-Alanine 1.20 0.48 • Lysine-free Pantothenic Acid, mg 7.5 3 Chloride, L-Glutamic Acid, L-Histidine, L-Arginine 2.7 1.08 Biotin, mcg 30 12 • Amino acid profile specifically L-Asparagine 1.8 0.72 Choline Bitartrate, Glycine, L-Serine, Vitamin C, mg 60 24 L-Cystine, Flaxseed Oil, Magnesium designed for GA-1; clinically L-Cystine 0.45 0.18 Choline, mg 313 125 researched in one study† For details on administration and household measurements, please L-Glutamic Acid 0.9 0.36 Inositol, mg 50 20 Oxide, Ascorbyl Palmitate, Mixed L-Glutamine 4.51 1.8 Tocopherols, Rosemary Extract, Silicon see pages 124-136. Minerals: • Contains arginine and 150 mg of Glycine 0.6 0.24 Calcium, mg 1257 503 Dioxide, L-Tryptophan, Taurine, Sodium tryptophan per 100 g powder L-Histidine 0.9 0.36 Phosphorus, mg 787 315 Chloride, Ascorbic Acid, Inositol, Ferric L-Isoleucine 2.1 0.84 Magnesium, mg 201 80 Orthophosphate, Vitamin E Acetate, • Contains a source of Omega-3 L-Leucine 3.46 1.38 Iron, mg 11.3 4.5 L-Lysine Nil Added Nil Added L-Carnitine, Niacinamide, Calcium fatty acids Ordering/Reimbursement Information: Zinc, mg 10 4 Phosphate, Zinc Oxide, Sucralose, L-Methionine 1.02 0.41 Manganese, mg 1.9 0.76 L-Ornithine 0.6 0.24 D-Calcium Pantothenate, Copper • Provides 25 g protein equivalent per Product Reimbursement HCPCS Product Calories Copper, mcg 1000 400 L-Phenylalanine 1.59 0.64 Gluconate, Vitamin K1, Vitamin D3, 100 g powder Code Code Code* Packaging Per Can Iodine, mcg 115 46 L-Proline 1.5 0.6 Molybdenum, mcg 31 12.4 Manganese Sulfate, Vitamin A Palmitate, • Vanilla flavor 7542 00847-0754-22 B4157 or B4162 4 x 454 g (1 lb) 1748 L-Serine 0.6 0.24 Chromium, mcg 21 8.6 Mono- and Diglycerides, D-Biotin, Beta- L-Threonine 1.59 0.64 Selenium, mcg 63 25 carotene, Pyridoxine Hydrochloride, • Osmolality (at 0.64 kcal/mL): L-Tryptophan 0.15 0.06 Sodium, mg 384 154 Potassium Iodide, Riboflavin, Thiamin L-Tyrosine 1.8 0.72 797 mOsm/kg WIC‡: Contact your state WIC For more reimbursement Potassium, mg 874 350 Mononitrate, Sodium Selenite, Folic Acid, L-Valine 2.4 0.96 Chloride, mg 475 190 Based on dilution of 40 g powder office to determine availability. information see page 195. L-Carnitine 0.04 0.01 Vitamin B12, Chromium Chloride, Sodium (1 scoop) to 7 fl oz (210 mL) water Taurine 0.15 0.06 Molybdate. Metabolics • Displacement: 0.75 mL/g CONTAINS: Coconut Oil, Soybean Oil.

† Strauss KA, et al. Mol Genet Metab. 2011. * S9435 = For individuals who submit their bills to insurance on their own. 96 97 GlutarAde Amino Acid Blend

Nutrition Information: Ingredients: ™ Per 10 g Protein Per 10 g Protein L-Glutamine, L-Leucine, L-Arginine, GlutarAde Amino Acid Blend Equivalent Equivalent L-Valine, L-Isoleucine, L-Asparagine Nutrients Per 100 g (1 scoop) Amino Acids, g Per 100 g (1 scoop) Monohydrate, L-Tyrosine, A lysine-free and low tryptophan powdered medical food for the dietary management of Calories 324 40 L-Alanine 3.86 0.48 L-Phenylalanine, L-Threonine, L-Proline, glutaric aciduria type 1 (GA-1) in children and adults. Protein Equivalent, g 81 10 L-Arginine 8.69 1.07 L-Ornithine-Alpha Ketoglutarate, Fat, g 0 0 L-Asparagine 5.79 0.71 L-Alanine, L-Methionine, L-Glutamic Acid, Carbohydrate, g 0 0 L-Cystine 1.45 0.18 L-Histidine, Glycine, L-Serine, L-Cystine, Taurine, L-Tryptophan, Silicon Dioxide, Sodium, mg 355 44 L-Glutamic Acid 2.90 0.36 L-Carnitine. L-Glutamine 14.48 1.79 Main Features: Indications: Glycine 1.93 0.24 • Lysine-free • Glutaric acidemia type I L-Histidine 2.90 0.36 Note: Must combine with an appropriate L-Isoleucine 6.76 0.83 vitamin & mineral supplement when • Amino acid profile specifically L-Leucine 11.10 1.37 taken as the sole source of amino acid designed for GA-1; clinically For details on administration and household measurements, please protein. see pages 124-136. L-Lysine Nil Added Nil Added researched in one study† L-Methionine 3.28 0.41 • Contains arginine and 480 mg of L-Ornithine 1.93 0.24 tryptophan per 100 g powder L-Phenylalanine 5.12 0.63 L-Proline 4.83 0.60 • Does not contain fat, carbohydrates, L-Serine 1.93 0.24 vitamins and minerals Ordering/Reimbursement Information: L-Threonine 5.12 0.63 • 40 calories per serving Product Reimbursement HCPCS Product Calories L-Tryptophan 0.48 0.06 • Provides 81 g of protein equivalent Code Code Code* Packaging Per Can L-Tyrosine 5.79 0.71 per 100 g of powder 7500 00847-0750-00 B4155 or B9998 4 x 454 g (1 lb) 1471 L-Valine 7.72 0.95 L-Carnitine 0.20 0.03 • Unflavored Taurine 0.48 0.06 • Displacement: 0.48 mL/g WIC‡: Contact your state WIC For more reimbursement office to determine availability. information see page 195. Metabolics

† Strauss KA, et al. Mol Genet Metab. 2011. * S9435 = For individuals who submit their bills to insurance on their own. 98 99 HCU Anamix Early Years

Nutrition Information: Ingredients: Per 10 g Per 10 g ® Corn Syrup Solids, Refined Vegetable HCU Anamix Early Years Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Oils (High Oleic Sunflower, Soy, Calories 473 350 Vitamin A, IU (mcg RE) 1305.(392) 967.(290) Non-Hydrogenated Coconut, Canola, Protein Equivalent,g 13.5 10.0 Vitamin D3, IU (mcg) 348.(8.7) 258.(6.4) Sunflower), Galacto-oligosaccharides A methionine-free powdered infant formula with iron, for the dietary Fat, g 23.0 17.0 (GOS) Dried Syrup (from milk), L-Lysine Vitamin E, IU (mg α-TE) 10.9 (7.3) 8.1 (5.4) L-Glutamate, L-Leucine, L-Proline, management of Vitamin B6 non-responsive homocystinuria or Saturated, g 7.5 5.6 Vitamin K, mcg 38.0 28.1 Tricalcium Phosphate, L-Arginine, hypermethioninemia. Contains DHA and ARA, and a unique blend of Monounsaturated, g 9.4 7.0 Thiamin, mcg 640 474 L-Valine, Glycine, L-Isoleucine, CAEM (an prebiotic fiber. Polyunsaturated, g 5.0 3.7 Riboflavin, mcg 500 370 emulsifier), L-Aspartic Acid, L-Threonine, DHA, mg 70.0 51.9 Vitamin B6, mcg 500 370 L-Serine, L-Phenylalanine, L-Tyrosine, L-Alanine, L-Histidine, Potassium ARA, mg 140 104 Vitamin B12, mcg 1.2 0.89 Linoleic Acid,mg 3500 2593 Niacin, mcg 2200 1630 Chloride, Fructo-oligosaccharides (FOS), Tripotassium Citrate, Sodium Phosphate Carbohydrate, g 53.0 39.3 Folic Acid, mcg 55.0 40.7 Dibasic, L-Cystine, Magnesium Acetate, Main Features: Indications: Fiber, g 5.3 3.9 Pantothenic Acid, mcg 2800 2074 M. Alpina Oil*, L-Tryptophan, Choline GOS, g 4.7 3.5 Biotin, mcg 18.2 13.5 Bitartrate, C. Cohnii Oil**, L-Glutamine, • Methionine-free powdered infant • Vitamin B6 non-responsive homocystinuria FOS, g 0.55 0.41 Vitamin C, mg 49.0 36.3 Sodium Chloride, M-Inositol, L-Ascorbic formula with iron • Hypermethioninemia Amino Acids, g Choline, mg 91.0 67.4 Acid, L-Glutamic Acid, Taurine, Ferrous L-Alanine 0.64 0.47 Sulfate, Zinc Sulfate, L-Carnitine, • Includes DHA & ARA Inositol, mg 98.0 72.6 DL-Alpha Tocopheryl Acetate, Calcium L-Arginine 1.09 0.81 Minerals D-Pantothenate, Niacinamide, • Contains a prebiotic fiber blend L-Aspartic Acid 0.93 0.69 Calcium, mg 371 275 Ascorbyl Palmitate, Manganese Sulfate, • Unflavored powder For details on administration and household measurements, please L-Cystine 0.41 0.30 Phosphorus, mg 270 200 Cupric Sulfate, Thiamine Chloride L-Glutamic Acid 1.22 0.90 Magnesium, mg 52.5 38.9 Hydrochloride, Pyridoxine Hydrochloride, • Contains a balanced mixture of all see pages 124-136. L-Glutamine 0.11 0.08 Iron, mg 7.3 5.4 Riboflavin, Vitamin A Acetate, DL-alpha Tocopherol, Mixed Tocopherols, other essential and non-essential Glycine 0.99 0.73 Zinc, mg 5.2 3.9 Potassium Iodide, Chromium Chloride, amino acids, carbohydrates, fat, L-Histidine 0.62 0.46 Manganese, mcg 390 289 Folic Acid, Phylloquinone, Sodium Ordering/Reimbursement Information: L-Isoleucine 0.98 0.73 Copper, mcg 390 289 Selenite, Sodium Molybdate, D-Biotin, vitamins, minerals and trace elements L-Leucine 1.67 1.2 Iodine, mcg 82.5 61.1 Vitamin D3, Cyanocobalamin Product Reimbursement HCPCS Product Calories L-Lysine 1.14 0.84 Molybdenum, mcg 10.9 8.1 • Provides 13.5 g of protein equivalent Code Code Code* Packaging Per Can CONTAINS: Soy Oil, Coconut Oil, Milk. per 100 g of powder L-Methionine Nil Added Nil Added Chromium, mcg 12.5 9.3 90169 49735-0101-69 B4162 6 x 400 g (14 oz) 1892 L-Phenylalanine 0.74 0.55 Selenium, mcg 14.1 10.4 *A source of Arachidonic Acid (ARA) • Osmolality (at 0.7 kcal/mL): L-Proline 1.18 0.87 Sodium, mg 171 127 **A source of Docosahexaenoic Acid L-Serine 0.73 0.54 380 mOsm/kg Potassium, mg 454 336 (DHA) Based on dilution of 5 g powder WIC‡: Contact your state WIC For more reimbursement L-Threonine 0.82 0.61 Chloride, mg 321 238 L-Tryptophan 0.33 0.24 Contains GOS/FOS 0.8 g per 100 mL Metabolics office to determine availability. information see page 195. (1 unpacked level scoop) to 1 fl oz L-Tyrosine 0.74 0.55 (30 mL) water L-Valine 1.07 0.79 * S9435 = For individuals who submit their bills to insurance on their own. • Displacement: 0.75 mL/g L-Carnitine 0.01 0.01 Taurine 0.02 0.01 100 101 HCU Anamix Next

Nutrition Information: Per 10 g Ingredients: ® Per 10 g HCU Anamix Next Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Corn Syrup Solids, Refined Vegetable Calories 385 137.5 Vitamin A, IU (mcg RE) 1399.(420) 500.(150) Oils (High Oleic Sunflower, Canola, A methionine-free, powdered medical food for the dietary management of Protein Equivalent, g 28 10 Vitamin D3, IU (mcg) 840.(21) 300.(7.5) Medium Chain Triglycerides (Palm Fat, g 12.5 4.5 Vitamin E, IU (mg α-TE) 12.5 (8.4) 4.5 (3) Kernel and/or Coconut Oil), Sunflower), homocystinuria in individuals over 1 year of age. Saturated, g 2.0 0.71 Vitamin K, mcg 14 5 L-Arginine L-Aspartate, L-Leucine, Monounsaturated, g 8.2 2.9 Thiamin, mg 0.93 0.33 Fructo-oligosaccharides, L-Lysine Polyunsaturated, g 1.8 0.64 Riboflavin, mg 0.73 0.26 Acetate, Inulin, Corn Starch, L-Glutamine, DHA, mg 180 64 Calcium Phosphate Dibasic, L-Proline, Vitamin B6, mg 0.73 0.26 Carbohydrate, g 43.2 15.4 Vitamin B , mcg 1.3 0.5 Microcrystalline Cellulose, L-Valine, 12 Artificial Flavor, Glycine, L-Isoleucine, Fiber, g 11.2 4 Niacin, mg 2.0 0.71 L-Threonine, Gum Arabic, L-Tyrosine, Soluble, g 8 2.9 Folic Acid, mcg 210 75 Main Features: Indications: L-Serine, L-Cystine, L-Phenylalanine, Insoluble, g 3.2 1.1 Pantothenic Acid, mg 4.2 1.5 L-Alanine, Tripotassium Citrate, Trisodium • Methionine-free • Homocystinuria Amino Acids, g Biotin, mcg 11.2 4 Citrate, L-Histidine, Calcium Chloride, L-Alanine 1.4 0.5 Vitamin C, mg 42 15 • Contains a balanced mixture of all Magnesium Hydrogen Phosphate, L-Arginine 2.25 0.8 Choline, mg 224 80 Maltodextrin, Choline Bitartrate, CAEM other essential and non-essential For details on administration and household measurements, please see pages 124-136. L-Aspartic Acid 2 0.71 Inositol, mg 56 20 (an emulsifier), L-Tryptophan, C. Cohnii amino acids, carbohydrate (including a L-Cystine 1.5 0.54 Minerals Oil*, Magnesium L-Aspartate, Tricalcium multi-fiber blend), fat (including DHA), L-Glutamine 2.6 0.93 Calcium, mg 980 350 Citrate, L-Ascorbic Acid, Soy Fiber, vitamins, minerals, and trace elements Glycine 2.13 0.76 Phosphorus, mg 641 229 M-Inositol, Taurine, Ferrous Sulfate, L-Histidine 1.22 0.44 Magnesium, mg 113 40 Sunflower Lecithin, L-Carnitine, Zinc • Provides 28 g protein equivalent and Ordering/Reimbursement Information: L-Isoleucine 2.1 0.75 Iron, mg 10 3.6 Sulfate, DL-alpha Tocopheryl Acetate, 12.5 g fat per 100 g of powder L-Leucine 3.46 1.24 Zinc, mg 4.9 1.8 Calcium D-Pantothenate, Manganese Product Reimbursement HCPCS Product Calories Sulfate, Niacinamide, Cupric Sulfate, L-Lysine 2.44 0.87 Manganese, mg 0.92 0.33 • Available in Plain Code Code Code* Packaging Per Can Thiamine Chloride Hydrochloride, L-Methionine Nil Added Nil Added Copper, mcg 560 200 • Osmolality (at 1.1 kcal/mL): 89470 49735-0194-70 B4162 6 x 400 g 1540 Pyridoxine Hydrochloride, Riboflavin, L-Phenylalanine 1.5 0.54 Iodine, mcg 139 49.6 1340 mOsm/kg B4157 Vitamin A Acetate, Ascorbyl Palmitate, L-Proline 2.52 0.9 Molybdenum, mcg 25.5 9.1 Folic Acid, Potassium iodide, Mixed Based on dilution of 36 g powder L-Serine 1.57 0.56 Chromium, mcg 10.2 3.6 ‡ Tocopherols, Sodium Molybdate, Sodium (approx 4 scoops) to 3.5 fl oz WIC : Contact your state WIC For more reimbursement L-Threonine 2 0.71 Selenium, mcg 28.2 10.1 Selenite, Chromium Chloride, DL-alpha office to determine availability. information see page 195. L-Tryptophan 0.5 0.18 Sodium, mg 280 100 (100 mL) water Tocopherol, Vitamin D3, Phylloquinone, L-Tyrosine 1.6 0.57 Potassium, mg 445 158.9 D-Biotin, Cyanocobalamin Metabolics • Displacement: 0.72 mL/g L-Valine 2.3 0.82 Chloride, mg 406 145 * A source of Docosahexaenoic Acid L-Carnitine 0.02 0.01 (DHA) CONTAINS: Coconut Oil, Soy. Taurine 0.05 0.02 * S9435 = For individuals who submit their bills to insurance on their own. 102 103 XMet Maxamum

Nutrition Information: Ingredients: XMet Maxamum® Per 10 g Per 10 g Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Sugar, L-Lysine L-Glutamate, Corn Syrup Calories 305 76 Vitamin A, IU (mcg RE) 2228.(669) 557.(167) Solids, L-Leucine, Calcium Phosphate A methionine-free powdered medical food for the dietary management of Vitamin B 6 Protein Equivalent, g 40 10 Vitamin D3, IU (mcg) 332.(8.3) 83.(2.1) Dibasic, L-Proline, L-Arginine, L-Valine, non-responsive homocystinuria or hypermethioninemia in older children and adults, Fat, g <1 <0.25 Vitamin E, IU (mg α-TE) 18.3 (12.3) 4.6 (3.1) Glycine, L-Isoleucine, L-Aspartic Acid, L-Threonine, Artificial Flavor, including pregnant women and women of child-bearing age. Carbohydrate, g 34 8.5 Vitamin K, mcg 82 21 L-Phenylalanine, L-Tyrosine, L-Serine, Amino Acids, g Thiamin, mg 0.91 0.23 Citric Acid, Magnesium Acetate, L-Alanine 1.8 0.45 Riboflavin, mg 0.97 0.24 L-Alanine, L-Histidine, Tripotassium L-Arginine 3.2 0.80 Vitamin B6, mg 1.6 0.4 Citrate, L-Cystine, Choline Bitartrate, L-Aspartic Acid 2.7 0.68 L-Tryptophan, Sodium Chloride, Soy Vitamin B12, mcg 3.1 0.8 Main Features: Indications: L-Cystine 1.2 0.30 Niacin, mg 5.7 1.4 Lecithin, Disodium Hydrogen Phosphate, L-Glutamic Acid 3.6 0.90 Folic Acid, mcg 491 123 Dipotassium Hydrogen Phosphate, • Methionine-free • Vitamin B non-responsive homocystinuria L-Glutamine, Tricalcium Phosphate, 6 Glycine 2.8 0.70 Pantothenic Acid, mg 4.9 1.2 L-Glutamic Acid, Taurine, • Contains a balanced mixture of all other • Hypermethioninemia L-Histidine 1.8 0.45 Biotin, mcg 24.5 6.1 L-Ascorbic Acid, M-Inositol, Ferrous essential and non-essential amino acids, L-Isoleucine 2.8 0.70 Vitamin C, mg 62 16 Sulfate, L-Carnitine, Zinc Sulfate, carbohydrate, vitamins, minerals and L-Leucine 4.9 1.23 Choline, mg 430 108 DL-Alpha Tocopheryl Acetate, L-Lysine 3.3 0.83 Inositol, mg 80 20 Niacinamide, Manganese Sulfate, trace elements For details on administration and household measurements, please L-Methionine Nil Added Nil Added Minerals Calcium D-Pantothenate, Cupric • Age-appropriate DRI formulation Sulfate, Pyridoxine Hydrochloride, see pages 124-136. L-Phenylalanine 2.2 0.55 Calcium, mg 1183 296 Sodium Selenite, Thiamin Chloride • XMet Maxamum provides 40 g of L-Proline 3.4 0.85 Phosphorus, mg 1137 284 protein equivalent per 100 g of powder Hydrochloride, Riboflavin, Vitamin A L-Serine 2.1 0.53 Magnesium, mg 306 77 Acetate, Folic Acid, Artificial Colors • Available in orange flavor Ordering/Reimbursement Information: L-Threonine 2.4 0.60 Iron, mg 14.7 3.7 (Beta-Carotene, Beet Red), Potassium • Contains <1 g of fat per 10 g PE L-Tryptophan 0.95 0.24 Zinc, mg 9 2 Iodide, Chromium Chloride, Sodium Product Reimbursement HCPCS Product Calories L-Tyrosine 2.2 0.55 Manganese, mg 1.8 0.5 Molybdate, Phylloquinone, D-Biotin, thereby allowing greater flexibility in Code Code Code* Packaging Per Can Vitamin D , Cyanocobalamin. L-Valine 3.1 0.78 Copper, mcg 820 205 3 modifying energy intake 117795 49735-0177-95 B4157 or 6 x 454 g (1 lb) 1385 L-Carnitine 0.039 0.01 Iodine, mcg 131 33 CONTAINS: Soy. B4162 • Osmolality (mOsm/kg): Taurine 0.14 0.04 Molybdenum, mcg 37 9 Dilution L-Glutamine 0.32 0.08 Chromium, mcg 26 7 1 to 7 800 WIC‡: Contact your state WIC For more reimbursement Selenium, mcg 58 15 Metabolics 1 to 5 1190 office to determine availability. information see page 195. Sodium, mg 560 140 Potassium, mg 700 175 • Displacement: 0.6 mL/g * S9435 = For individuals who submit their bills to insurance on their own. Chloride, mg 560 140 104 105 HCU Lophlex LQ

Nutrition Information: Ingredients: Per Pouch Per 10 g Per Pouch Per 10 g ® Nutrients (4.2 fl oz) Protein Equivalent Vitamins (4.2 fl oz) Protein Equivalent Water, Apple Juice from Concentrate HCU Lophlex LQ (34.1%), Grape Juice from Concentrate Calories 120 60 Vitamin A, IU (mcg RE) 949.(285) 475.(143) (6.9%), Blackcurrant Juice from Concentrate (2.5%), L-Arginine A methionine-free*, ready-to-drink medical food containing amino acids, carbohydrates, Protein Equivalent, g 20 10 Vitamin D3, IU (mcg) 320.(8.0) 160.(4.0) Fat, g 0.44 0.22 L-Aspartate, L-Leucine, L-Lysine Acetate, vitamins, minerals and DHA, based on mixed fruit juices (from concentrate) with natural Vitamin E, IU (mg α-TE) 4.8 (3.2) 2.4 (1.6) Citric Acid, L-Proline, L-Tyrosine, Glycine, DHA, mg 150 75 Vitamin K, mcg 24.9 12.5 flavor; for the dietary management of proven homocystinuria in individuals 4 years and L-Valine, L-Serine, L-Isoleucine, Corn Carbohydrate, g 9.3 4.7 Thiamin, mg 0.54 0.27 Syrup Solids, Dicalcium Phosphate, older, including pregnant women and women of child-bearing age. L-Alanine, L-Threonine, L-Phenylalanine, Fiber, g 0.50 0.25 Riboflavin, mg 0.50 0.25 L-Cystine, L-Histidine, Elderberry Amino Acids, g Vitamin B6, mg 0.58 0.29 Juice from Concentrate (0.6%), L-Alanine 1.18 0.59 Vitamin B , mcg 1.8 0.90 Maltodextrin, Magnesium L-Aspartate, 12 Magnesium Acetate, L-Tryptophan, L-Arginine 1.50 0.75 Niacin, mg 7.1 3.6 Choline Bitartrate, C. Cohnii Oil*, Sugar, Main Features: Indications: L-Aspartic Acid 1.73 0.87 Folic Acid, mcg 120 60.0 Microcrystalline Cellulose, Natural L-Cystine 0.98 0.49 Pantothenic Acid, mg 1.8 0.9 Flavor, Fruit Concentrate (Apple, • Methionine-free • Homocystinuria Blackcurrant, Radish), L-Ascorbic Acid, Glycine 1.60 0.80 Biotin, mcg 53.4 26.7 Taurine, Guar Gum, Sunflower Lecithin, • Low volume; provides 20 g PE in just 4.2 For details on administration, please see pages 124-136. L-Histidine 0.85 0.43 Vitamin C, mg 17.8 8.9 Xanthan Gum, M-Inositol, Potassium fl oz (125 mL) L-Isoleucine 1.35 0.68 Sorbate (preservative to delay spoilage), Choline, mg 153 76.5 Artificial Sweetener: Sucralose, Artificial • Convenient ready-to-drink L-Leucine 2.30 1.15 Inositol, mg 40.6 20.3 Sweetener: Acesulfame Potassium, L-Lysine 1.55 0.78 Minerals Ferrous Lactate, Sodium Benzoate • Based on fruit juices (from concentrate) (preservative to delay spoilage), Zinc with natural flavor - no artificial flavors L-Methionine Trace* Trace* Calcium, mg 319 160 Sulfate, L-Carnitine, Niacinamide, Ordering/Reimbursement Information: L-Phenylalanine 1.00 0.50 Phosphorus, mg 244 122 DL-alpha Tocopheryl Acetate, Calcium • Contains a balanced mixture of other L-Proline 2.03 1.02 Magnesium, mg 96.3 48.2 D-Pantothenate, Manganese Sulfate, essential and non-essential amino acids, Product Reimbursement HCPCS Product Calories Cupric Sulfate, Thiamin Chloride Code Code Code* Packaging Per Pouch L-Serine 1.38 0.69 Iron, mg 5.1 2.6 Hydrochloride, Pyridoxine Hydrochloride, carbohydrates, vitamins, minerals and L-Threonine 1.13 0.57 Vitamin A Palmitate, Riboflavin, Folic 82111 49735-0167-48 B4157 or B4162 30 X 4.2 fl oz (125 mL) 120 Zinc, mg 3.8 1.9 DHA L-Tryptophan 0.45 0.23 Manganese, mg 0.56 0.28 Acid, Potassium Iodide, Ascorbyl Palmitate, Mixed Tocopherols, Sodium • Provides 150 mg DHA per pouch L-Tyrosine 1.65 0.83 Copper, mcg 563 282 Molybdate, D-Biotin, Sodium Selenite, WIC‡: Contact your state WIC For more reimbursement L-Valine 1.45 0.73 Iodine, mcg 56.3 28.2 Chromium Chloride, Phylloquinone, • Available in mixed berry blast flavor Vitamin D , Cyanocobalamin. office to determine availability. information see page 195. L-Carnitine 0.01 0.01 Molybdenum, mcg 25.0 12.5 3 • Osmolality (at 0.96 kcal/mL): Contains 44.1% juice. * S9435 = For individuals who submit their bills to insurance on their own. Taurine 0.06 0.03 Chromium, mcg 10.8 5.4

Metabolics 2460 mOsm/kg Selenium, mcg 26.8 13.4 *A Source of Docosahexaenoic Acid Sodium, mg <25.0 <12.5 (DHA). Potassium, mg 90 45 *May contain traces of methionine from fruit juice (from concentrate) at a level of <2 mg per 100 mL. Chloride, mg <25.0 <12.5 106 107 MMA/PA Anamix Early Years

Nutrition Information: Ingredients: ® Per 10 g Per 10 g MMA/PA Anamix Early Years Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Corn Syrup Solids, Refined Vegetable Calories 473 350 Vitamin A, IU (mcg RE) 1305.(392) 967.(290) Oils (High Oleic Sunflower, Soy, Non-hydrogenated Coconut, Canola, A methionine-, threonine- and valine-free, low in isoleucine powdered infant formula Protein Equivalent,g 13.5 10.0 Vitamin D3, IU (mcg) 348.(8.7) 258.(6.4) with iron, for the dietary management of methylmalonic or propionic acidemia (MMA/ Fat, g 23.0 17.0 Vitamin E, IU (mg α-TE) 10.9 (7.3) 8.1 (5.4) Sunflower), Galacto-oligosaccharides Saturated, g 7.5 5.6 Vitamin K, mcg 38.0 28.1 (GOS) Dried Syrup (from milk), L-Lysine PA). Contains DHA and ARA, and a unique blend of prebiotic fiber. Monounsaturated, g 9.4 7.0 Thiamin, mcg 640 474 L-Glutamate, L-Leucine, L-Alanine, Polyunsaturated, g 5.0 3.7 Riboflavin, mcg 500 370 L-Arginine, L-Aspartic Acid, Tricalcium Phosphate, CAEM (an emulsifier), DHA, mg 70.0 51.9 Vitamin B6, mcg 500 370 L-Histidine, L-Phenylalanine, L-Tyrosine, ARA, mg 140 104 Vitamin B12, mcg 1.2 0.89 Main Features: Indications: Linoleic Acid,mg 3500 2593 Niacin, mcg 2200 1630 L-Serine, Glycine, L-Proline, Potassium Carbohydrate, g 53.0 39.3 Folic Acid, mcg 55.0 40.7 Chloride, Fructo-oligosaccharides • A methionine-, threonine- and valine- • Methylmalonic acidemia Fiber, g 5.3 3.9 Pantothenic Acid, mcg 2800 2074 (FOS), Tripotassium Citrate, L-Cystine, GOS, g 4.7 3.5 Biotin, mcg 18.2 13.5 L-Tryptophan, Sodium Phosphate free, low in isoleucine powdered • Propionic acidemia FOS, g 0.55 0.41 Vitamin C, mg 49.0 36.3 Dibasic, Magnesium Acetate, M. Alpina infant formula with iron Amino Acids, g Choline, mg 91.0 67.4 Oil*, Choline Bitartrate, C. Cohnii Oil**, • Includes DHA & ARA For details on administration and household measurements, please L-Alanine 1.6 1.2 Inositol, mg 98.0 72.6 L-Glutamine, Sodium Chloride, M-Inositol, see pages 124-136. L-Arginine 1.4 1.0 Minerals L-Ascorbic Acid, L-Glutamic Acid, • Contains a prebiotic fiber blend L-Aspartic Acid 1.27 0.94 Calcium, mg 371 275 Taurine, Ferrous Sulfate, Zinc Sulfate, • Unflavored powder L-Cystine 0.51 0.38 Phosphorus, mg 270 200 L-Carnitine, DL-alpha Tocopheryl Acetate, L-Glutamic Acid 1.59 1.2 Magnesium, mg 52.5 38.9 Calcium D-Pantothenate, Niacinamide, • Contains a balanced mixture of all L-Glutamine 0.11 0.08 Iron, mg 7.3 5.4 Ascorbyl Palmitate, Manganese Sulfate, other essential and non-essential Glycine 0.64 0.47 Zinc, mg 5.2 3.9 Cupric Sulfate, Thiamine Chloride amino acids, carbohydrates, fat, Ordering/Reimbursement Information: L-Histidine 0.94 0.70 Manganese, mcg 390 289 Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, DL-alpha vitamins, minerals and trace elements L-Isoleucine <0.01 <0.01 Copper, mcg 390 289 Product Reimbursement HCPCS Product Calories L-Leucine 2.12 1.6 Iodine, mcg 82.5 61.1 Tocopherol, Mixed Tocopherols, • Provides 13.5 g of protein equivalent Code Code Code* Packaging Per Can L-Lysine 1.43 1.1 Molybdenum, mcg 10.9 8.1 Potassium Iodide, Chromium Chloride, per 100 g of powder 90215 49735-0102-15 B4162 6 x 400 g (14 oz) 1892 L-Methionine Nil Added Nil Added Chromium, mcg 12.5 9.3 Folic Acid, Phylloquinone, Sodium L-Phenylalanine 0.93 0.69 Selenium, mcg 14.1 10.4 Selenite, Sodium Molybdate, D-Biotin, • Osmolality (at 0.7 kcal/mL): L-Proline 0.64 0.47 Sodium, mg 171 127 Vitamin D3, Cyanocobalamin 380 mOsm/kg WIC‡: Contact your state WIC For more reimbursement L-Serine 0.89 0.66 Potassium, mg 454 336 CONTAINS: Soy Oil, Coconut Oil, Milk. Based on dilution of 5 g powder office to determine availability. information see page 195. L-Threonine Nil Added Nil Added Chloride, mg 321 238 L-Tryptophan 0.41 0.30 *A source of Arachidonic Acid (ARA) Metabolics (1 unpacked level scoop) to 1 fl oz L-Tyrosine 0.93 0.69 (30 mL) water * S9435 = For individuals who submit their bills to insurance on their own. **A source of Docosahexaenoic Acid L-Valine Nil Added Nil Added (DHA) • Displacement: 0.75 mL/g L-Carnitine 0.01 0.01 Taurine 0.02 0.01 Contains GOS/FOS 0.8 g per 100 mL 108 109 MMA/PA Anamix Next

Nutrition Information: Ingredients: ® Per 10 g Per 10 g MMA/PA Anamix Next Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Corn Syrup Solids, Refined Vegetable Calories 377 135 Vitamin A, IU (mcg RE) 1748.(525) 628.(189) Oils (High Oleic Sunflower, Canola, A methionine-, threonine-, valine-free, low isoleucine, powdered medical food for the Protein Equivalent, g 28 10 Vitamin D3, IU (mcg) 1052.(26.3) 379.(9.6) Medium Chain Triglycerides (Palm dietary management of methylmalonic acidemia and propionic acidemia in individuals over Fat, g 12.5 4.5 Vitamin E, IU (mg α-TE) 15.6 (10.5) 5.6 (3.8) Kernel and/or Coconut Oil), Sunflower), Saturated, g 2.0 0.71 Vitamin K, mcg 17.5 6.4 L-Leucine, L-Lysine Acetate, L-Glutamine, 1 year of age. Monounsaturated, g 8.2 2.9 Thiamin, mg 1.2 0.4 Fructo-oligosaccharides, L-Alanine, Polyunsaturated, g 1.8 0.64 Riboflavin, mg 0.91 0.32 Inulin, Calcium Phosphate Dibasic, DHA, mg 180 64 L-Arginine, Corn Starch, L-Aspartic Vitamin B6, mg 0.91 0.32 Carbohydrate, g 41.2 14.8 Vitamin B , mcg 1.6 0.56 Acid, Microcrystalline Cellulose, 12 Artificial Flavor, L-Histidine, L-Tyrosine, Fiber, g 11.2 4 Niacin, mg 2.5 0.90 L-Phenylalanine, L-Serine, Gum Arabic, Soluble, g 8 2.9 Folic Acid, mcg 263 94.8 Main Features: Indications: Tripotassium Citrate, Trisodium Citrate, Insoluble, g 3.2 1.1 Pantothenic Acid, mg 5.3 1.92 • Methionine-, threonine-, valine-free • Methylmalonic Acidemia L-Cystine, Glycine, L-Proline, Calcium Amino Acids, g Biotin, mcg 14 5.2 Chloride, Magnesium Hydrogen • Low isoleucine • Propionic Acidemia L-Alanine 3.42 1.22 Vitamin C, mg 52.5 18.8 Phosphate, Maltodextrin, Choline L-Arginine 3.0 1.07 Choline, mg 280 100 • Contains a balanced mixture of all other Bitartrate, L-Tryptophan, Tricalcium L-Aspartic Acid 2.72 0.97 Inositol, mg 70 25.2 Citrate, CAEM (an emulsifier), C. essential and non-essential amino acids, For details on administration and household measurements, please see pages 124-136. L-Cystine 1.56 0.56 Minerals Cohnii Oil*, L-Ascorbic Acid, M-Inositol, carbohydrate (including a multi-fiber L-Glutamine 3.61 1.29 Calcium, mg 1225 440 Soy Fiber, Taurine, Ferrous Sulfate, blend), fat (including DHA), vitamins, Glycine 1.37 0.49 Phosphorus, mg 801 288 Sunflower Lecithin, L-Carnitine, Zinc minerals, and trace elements L-Histidine 2.02 0.72 Magnesium, mg 140 50.4 Sulfate, DL-alpha Tocopheryl Acetate, Ordering/Reimbursement Information: L-Isoleucine <0.03 <0.03 Iron, mg 12.5 4.4 Calcium D-Pantothenate, Manganese • Provides 28 g protein equivalent and L-Leucine 4.54 1.62 Zinc, mg 6.1 2.2 Sulfate, Niacinamide, Cupric Sulfate, Thiamine Chloride Hydrochloride, 12.5 g fat per 100 g of powder Product Reimbursement HCPCS Product Calories L-Lysine 3.05 1.09 Manganese, mg 1.2 0.44 Pyridoxine Hydrochloride, Riboflavin, Code Code Code* Packaging Per Can L-Methionine Nil Added Nil Added Copper, mcg 700 252 • Available in Plain Vitamin A Acetate, Folic Acid, Ascorbyl 89472 49735-0194-72 B4162 6 x 400 g 1508 • Osmolality (at 1.1 kcal/mL): L-Phenylalanine 1.99 0.71 Iodine, mcg 174 62.8 Palmitate, Potassium iodide, Mixed B4157 L-Proline 1.37 0.49 Molybdenum, mcg 31.9 11.4 1220 mOsm/kg Tocopherols, Sodium Molybdate, Sodium L-Serine 1.98 0.71 Chromium, mcg 12.8 4.8 Selenite, Chromium Chloride, DL-alpha Based on dilution of 36 g powder ‡ L-Threonine Nil Added Nil Added Selenium, mcg 35.3 12.8 Tocopherol, Vitamin D , Phylloquinone, WIC : Contact your state WIC For more reimbursement 3 (approx 4 scoops) to 3.5 fl oz office to determine availability. information see page 195. L-Tryptophan 0.69 0.25 Sodium, mg 350 126 D-Biotin, Cyanocobalamin L-Tyrosine 1.99 0.71 Potassium, mg 556 200 Metabolics (100 mL) water CONTAINS: Coconut Oil, Soy. • Displacement: 0.72 mL/g * S9435 = For individuals who submit their bills to insurance on their own. L-Valine Nil Added Nil Added Chloride, mg 508 183 L-Carnitine 0.02 0.01 *A source of Docosahexaenoic Acid Taurine 0.06 0.02 (DHA) 110 111 XMTVI Maxamum

® Nutrition Information: Ingredients: XMTVI Maxamum Per 10 g Per 10 g Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Sugar, L-Lysine L-Glutamate, L-Leucine, A methionine-, threonine-, valine-free and isoleucine-low medical food for the dietary Calories 305 76 Vitamin A, IU (mcg RE) 2228 (669) 557 (167) Corn Syrup Solids, L-Alanine, Calcium Protein Equivalent, g 40 10 Vitamin D , IU (mcg) 332 (8.3) 83 (2.1) Phosphate Dibasic, L-Arginine, L-Aspartic management of Vitamin B12 non-responsive methylmalonic acidemia or propionic acidemia 3 Fat, g <1 <0.25 Vitamin E, IU (mg α-TE) 18.3 (12.3) 4.6 (3.1) Acid, L-Histidine, L-Phenylalanine, in older children and adults, including pregnant women and women of child-bearing age. L-Tyrosine, L-Serine, Artificial Flavor, Carbohydrate, g 34 8.5 Vitamin K, mcg 82 21 Citric Acid, Magnesium Acetate, Glycine, Amino Acids, g 0.23 Thiamin, mg 0.91 L-Proline, L-Cystine, L-Tryptophan, L-Alanine 4.6 1.15 Riboflavin, mg 0.97 0.24 Tripotassium Citrate, Choline Bitartrate, L-Arginine 4.1 1.03 Vitamin B , mg 1.6 0.4 Sodium Chloride, Soy Lecithin, Disodium Main Features: Indications: 6 L-Aspartic Acid 3.6 0.90 Hydrogen Phosphate, Dipotassium Vitamin B12, mcg 3.1 0.8 L-Cystine 1.5 0.38 Niacin, mg 5.7 1.4 Hydrogen Phosphate, L-Glutamine, • Methionine-, threonine-, valine-free • Vitamin B12 non-responsive methylmalonic acidemia and isoleucine-low L-Glutamic Acid 4.5 1.13 Folic Acid, mcg 491 123 Tricalcium Phosphate, L-Glutamic Acid, • Propionic acidemia Taurine, L-Ascorbic Acid, M-Inositol, Glycine 1.8 0.45 Pantothenic Acid, mg 4.9 1.2 • Contains a balanced mixture of all Ferrous Sulfate, L-Carnitine, Zinc L-Histidine 2.8 0.70 6.1 other essential and non-essential For details on administration and household measurements, please Biotin, mcg 24.5 Sulfate, DL-Alpha Tocopheryl Acetate, L-Isoleucine <0.14 Trace Vitamin C, mg 62 16 amino acids, carbohydrate, vitamins, see pages 124-136. Niacinamide, Manganese Sulfate, L-Leucine 6.2 1.55 Choline, mg 430 108 Calcium D-Pantothenate, Cupric minerals and L-Lysine 4.2 1.05 Inositol, mg 80 20 Sulfate, Pyridoxine Hydrochloride, trace elements L-Methionine Nil Added Nil Added Minerals Sodium Selenite, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A • Age-appropriate DRI formulation L-Phenylalanine 2.7 0.68 Calcium, mg 1183 296 Acetate, Folic Acid, Artificial Colors (Beta L-Proline 1.9 0.48 284 • XMTVI Maxamum provides Phosphorus, mg 1137 Carotene, Beet Red), Potassium Iodide, 40 g of protein equivalent per Ordering/Reimbursement Information: L-Serine 2.6 0.65 Magnesium, mg 306 77 Chromium Chloride, Sodium Molybdate, L-Threonine Nil Added Nil Added Iron, mg 14.7 3.7 Phylloquinone, D-Biotin, Vitamin D , 100 g of powder Product Reimbursement HCPCS Product Calories 3 L-Tryptophan 1.2 0.30 Zinc, mg 9 2 Cyanocobalamin. Code Code Code* Packaging Per Can • Available in orange flavor L-Tyrosine 2.7 0.68 Manganese, mg 1.8 0.5 117779 49735-0177-79 B4162 or 6 x 454 g (1 lb) 1385 CONTAINS: Soy. • Contains <1 g of fat per 10 g PE B4157 L-Valine Nil Added Nil Added Copper, mcg 820 205 thereby allowing greater flexibility in L-Carnitine 0.039 0.01 Iodine, mcg 131 33 Taurine 0.14 0.04 Molybdenum, mcg 37 9 modifying energy intake ‡ WIC : Contact your state WIC For more reimbursement L-Glutamine 0.32 0.08 7 • Osmolality (mOsm/kg): Chromium, mcg 26 office to determine availability. information see page 195. Selenium, mcg 58 15 Metabolics Dilution * S9435 = For individuals who submit their bills to insurance on their own. Sodium, mg 560 140 1 to 7 740 Potassium, mg 700 175 1 to 5 1070 Chloride, mg 560 140 112 • Displacement: 0.6 mL/g 113 TYR Anamix Early Years

Nutrition Information: Ingredients: ® Per 10 g Per 10 g TYR Anamix Early Years Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Corn Syrup Solids, Refined Vegetable Calories 473 350 Vitamin A, IU (mcg RE) 1305.(392) 967.(290) Oils (High Oleic Sunflower, Soy, Non-hydrogenated Coconut, Canola, A phenylalanine-, tyrosine-free powdered infant formula with iron, for the dietary Protein Equivalent,g 13.5 10.0 Vitamin D , IU (mcg) 348.(8.7) 258.(6.4) 3 Sunflower), Galacto-oligosaccharides Fat, g 23.0 17.0 management of tyrosinemia (TYR). Contains DHA and ARA, and a unique blend of Vitamin E, IU (mg α-TE) 10.9 (7.3) 8.1 (5.4) (GOS) Dried Syrup (from milk), L-Lysine prebiotic fiber. Saturated, g 7.5 5.6 Vitamin K, mcg 38.0 28.1 L-Glutamate, L-Leucine, L-Proline, Monounsaturated, g 9.4 7.0 Thiamin, mcg 640 474 L-Arginine, L-Valine, Tricalcium Polyunsaturated, g 5.0 3.7 Riboflavin, mcg 500 370 Phosphate, Glycine, L-Isoleucine, DHA, mg 70.0 51.9 Vitamin B6, mcg 500 370 L-Aspartic Acid, CAEM (an emulsifier), Main Features: Indications: ARA, mg 140 104 Vitamin B12, mcg 1.2 0.89 L-Threonine, L-Serine, L-Alanine, Linoleic Acid,mg 3500 2593 Niacin, mcg 2200 1630 L-Histidine, Potassium Chloride, Fructo- • A phenylalanine-, tyrosine-free • Tyrosinemia Carbohydrate, g 53.0 39.3 Folic Acid, mcg 55.0 40.7 oligosaccharides (FOS), Tripotassium powdered infant formula with iron Fiber, g 5.3 3.9 Pantothenic Acid, mcg 2800 2074 Citrate, L-Cystine, Sodium Phosphate Dibasic, L-Tryptophan, Magnesium • Includes DHA & ARA GOS, g 4.7 3.5 Biotin, mcg 18.2 13.5 FOS, g 0.55 0.41 Vitamin C, mg 49.0 36.3 Acetate, M. Alpina Oil*, L-Methionine, Choline Bitartrate, C. Cohnii Oil**, • Contains a prebiotic fiber blend For details on administration and household measurements, please Amino Acids, g Choline, mg 91.0 67.4 L-Glutamine, Sodium Chloride, M-Inositol, see pages 124-136. L-Alanine 0.68 0.50 • Unflavored powder Inositol, mg 98.0 72.6 L-Ascorbic Acid, L-Glutamic Acid, • Contains a balanced mixture of all L-Arginine 1.19 0.88 Minerals Taurine, Ferrous Sulfate, Zinc Sulfate, L-Aspartic Acid 1 0.74 Calcium, mg 371 275 L-Carnitine, DL-alpha Tocopheryl Acetate, other essential and non-essential L-Cystine 0.45 0.33 Phosphorus, mg 270 200 Calcium D-Pantothenate, Niacinamide, amino acids, carbohydrates, fat, Ordering/Reimbursement Information: L-Glutamic Acid 1.34 0.99 Magnesium, mg 52.5 38.9 Ascorbyl Palmitate, Manganese Sulfate, vitamins, minerals and trace elements L-Glutamine 0.11 0.08 Iron, mg 7.3 5.4 Cupric Sulfate, Thiamine Chloride • Provides 13.5 g of protein equivalent Product Reimbursement HCPCS Product Calories Glycine 1.07 0.79 Zinc, mg 5.2 3.9 Hydrochloride, Pyridoxine Hydrochloride, Code Code Code* Packaging Per Can L-Histidine 0.68 0.50 Manganese, mcg 390 289 Riboflavin, Vitamin A Acetate, DL-alpha per 100 g of powder Tocopherol, Mixed Tocopherols, 90218 49735-0102-18 B4162 6 x 400 g (14 oz) 1892 L-Isoleucine 1.07 0.79 Copper, mcg 390 289 • Osmolality (at 0.7 kcal/mL): L-Leucine 1.83 1.4 Iodine, mcg 82.5 61.1 Potassium Iodide, Chromium Chloride, L-Lysine 1.24 0.92 Molybdenum, mcg 10.9 8.1 Folic Acid, Phylloquinone, Sodium 380 mOsm/kg Selenite, Sodium Molybdate, D-Biotin, L-Methionine 0.29 0.21 Chromium, mcg 12.5 9.3 ‡ Vitamin D3, Cyanocobalamin Based on dilution of 5 g powder WIC : Contact your state WIC For more reimbursement L-Phenylalanine Nil Added Nil Added Selenium, mcg 14.1 10.4 (1 unpacked level scoop) to 1 fl oz office to determine availability. information see page 195. L-Proline 1.3 0.96 Sodium, mg 171 127 CONTAINS: Soy Oil, Coconut Oil, Milk. (30 mL) water L-Serine 0.8 0.59 Potassium, mg 454 336 *A source of Arachidonic Acid (ARA) L-Threonine 0.89 0.66 • Displacement: 0.75 mL/g * S9435 = For individuals who submit their bills to insurance on their own. Chloride, mg 321 238 L-Tryptophan 0.36 0.27 **A source of Docosahexaenoic Acid Metabolics L-Tyrosine Nil Added Nil Added (DHA) L-Valine 1.17 0.9 Visit NutriciaLearningCenter.com Contains GOS/FOS 0.8 g per 100 mL for guidelines for the nutritional L-Carnitine 0.01 0.0 Taurine 0.02 0.0 114 management of TYR. 115 TYR Anamix Next

Nutrition Information: Ingredients: Per 10 g Per 10 g ® Nutrients Per 100 g Protein Equivalent Vitamins Per 100 g Protein Equivalent Corn Syrup Solids, Refined Vegetable Oils TYR Anamix Next Calories 385 138 Vitamin A, IU (mcg RE) 1399.(420) 499.(150) (High Oleic Sunflower, Canola, Medium Protein Equivalent, g 28 10 Vitamin D , IU (mcg) 840.(21) 300.(7.5) Chain Triglycerides (Palm Kernel and/ A phenylalanine- and tyrosine-free, powdered medical food for the dietary management 3 Fat, g 12.5 4.5 Vitamin E, IU (mg α-TE) 12.5 (8.4) 4.5 (3) or Coconut Oil), Sunflower), L-Alanine, Glycine, Fructo-oligosaccharides, of tyrosinemia in individuals over 1 year of age. Saturated, g 2 0.71 Vitamin K, mcg 14 5 L-Glutamine, L-Lysine Acetate, ]Inulin, Monounsaturated, g 8.2 2.9 Thiamin, mg 0.93 0.33 Polyunsaturated, g 1.8 0.64 L-Threonine, Corn Starch, L-Cystine, Riboflavin, mg 0.73 0.26 DHA, mg 180 64.3 L-Proline, Calcium Phosphate Dibasic, VitaminB , mg 0.73 0.26 Carbohydrate, g 43.2 15.4 6 L-Leucine, Microcrystalline Cellulose, Artificial Flavor, L-Valine, Gum Arabic, Fiber, g 11.2 4 Vitamin B12, mcg 1.3 0.46 Main Features: Indications: L-Arginine, L-Isoleucine, L-Serine, Soluble 8 2.9 Niacin, mg 2.0 0.71 • Phenylalanine- and tyrosine-free • Tyrosinemia Folic Acid, mcg 210 75 Tripotassium Citrate, Trisodium Insoluble 3.2 1.1 Citrate, Calcium Chloride, L-Histidine, Pantothenic Acid, mg 4.2 1.5 • Contains a balanced mixture of all Amino Acids, g Maltodextrin, Choline Bitartrate, other essential and non-essential For details on administration and household measurements, please L-Alanine 4.71 1.7 Biotin, mcg 11.2 4 Magnesium Hydrogen Phosphate, amino acids, carbohydrate (including see pages 124-136. L-Arginine 1.67 0.6 Vitamin C, mg 42 15 L-Methionine, L-Tryptophan, Magnesium a multi-fiber blend), fat (including L-Aspartic Acid 0.41 0.15 Choline, mg 224 80 L-Aspartate, CAEM (an emulsifier), DHA), vitamins, minerals and trace L-Cystine 2.71 0.97 Inositol, mg 56 20 C. Cohnii Oil*, Tricalcium Citrate, L-Glutamine 3.36 1.2 Minerals L-Ascorbic Acid, Soy Fiber, M-Inositol, elements Taurine, Ferrous Sulfate, Sunflower Glycine 3.94 1.4 Calcium, mg 980 350 • Provides 28 g protein equivalent and Ordering/Reimbursement Information: L-Histidine 0.79 0.28 Lecithin, L-Carnitine, Zinc Sulfate, Phosphorus, mg 641 229 DL-alpha Tocopheryl Acetate, Calcium L-Isoleucine 1.66 0.59 12.5 g fat per 100 g of powder Product Reimbursement HCPCS Product Calories Magnesium, mg 113 40 D-Pantothenate, Manganese Sulfate, L-Leucine 2.52 0.9 • Available in a plain flavor Code Code Code* Packaging Per Can Iron, mg 10 4 Niacinamide, Cupric Sulfate, Thiamin L-Lysine 2.24 0.8 89479 49735-0194-79 B4162 6 x 400 g (14 oz) 1540 Zinc, mg 4.9 1.8 Chloride Hydrochloride, Pyridoxine • Osmolality (at 1.1 kcal/mL): L-Methionine 0.56 0.2 B4157 Manganese, mg 0.92 0.33 Hydrochloride, Riboflavin, Vitamin A 1220 mOsm/kg L-Phenylalanine Nil Added Nil Added Copper, mcg 560 200 Acetate, Ascorbyl Palmitate, Folic Acid, Based on dilution of 36 g powder L-Proline 2.71 0.97 Potassium Iodide, Mixed Tocopherols, Iodine, mcg 139 50 WIC‡: Contact your state WIC For more reimbursement L-Serine 1.59 0.57 Sodium Molybdate, Sodium Selenite, (approx 4 scoops) to 3.5 fl oz Molybdenum, mcg 25.5 9.1 (100 mL) water office to determine availability. information see page 195. L-Threonine 2.94 1.1 Chromium Chloride, DL-alpha L-Tryptophan 0.56 0.2 Chromium, mcg 10.2 3.6 Tocopherol, Vitamin D3, Phylloquinone, • Displacement: 0.72 mL/g Selenium, mcg 28.2 10.1 D-Biotin, Cyanocobalamin

Metabolics L-Tyrosine Nil Added Nil Added * S9435 = For individuals who submit their bills to insurance on their own. L-Valine 1.96 0.7 Sodium, mg 280 100 CONTAINS: Coconut Oil, Soy. L-Carnitine 0.02 0.01 Potassium, mg 445 159 *A source of Docosahexaenoic Acid Taurine 0.05 0.02 Chloride, mg 406 145 (DHA) 116 117 TYR Lophlex LQ

Nutrition Information: Ingredients: Per Pouch Per 10 g Per Pouch Per 10 g ® Nutrients (4.2 fl oz) Protein Equivalent Vitamins (4.2 fl oz) Protein Equivalent Water, Apple Juice from Concentrate TYR Lophlex LQ (34.1%), Grape Juice from Concentrate Calories 120 60 Vitamin A, IU (mcg RE) 949 (285) 475 (143) (6.9%), Blackcurrant Juice from A tyrosine- and phenylalanine-free*, ready-to-drink medical food containing amino acids, Protein Equivalent, g 20 10 Vitamin D3, IU (mcg) 320 (8.0) 160 (4.0) Concentrate (2.5%), L-Leucine, L-Lysine carbohydrates, vitamins, minerals and DHA, based on mixed fruit juices (from concentrate) Fat, g 0.44 0.22 Vitamin E, IU (mg α-TE) 4.8 (3.2) 2.4 (1.6) Acetate, Citric Acid, L-Proline, L-Arginine, DHA, mg 150 75 Vitamin K, mcg 24.9 12.5 L-Valine, L-Aspartic Acid, Glycine, with natural flavor; for the dietary management of proven tyrosinemia in individuals 4 years L-Isoleucine, L-Serine, L-Threonine, Corn Carbohydrate, g 9.3 4.7 Thiamin, mg 0.54 0.27 and older, including pregnant women and women of child-bearing age. Syrup Solids, Dicalcium Phosphate, Fiber, g 0.50 0.25 Riboflavin, mg 0.50 0.25 L-Alanine, L-Histidine, L-Cystine, Amino Acids, g Vitamin B6, mg 0.58 0.29 Elderberry Juice from Concentrate L-Alanine 1.13 0.57 Vitamin B12, mcg 1.8 0.90 (0.6%), Maltodextrin, Magnesium Acetate, Sugar, N-Acetyl L-Methionine, L-Arginine 1.68 0.84 Main Features: Indications: Niacin, mg 7.1 3.6 L-Tryptophan, Choline Bitartrate, C. L-Aspartic Acid 1.63 0.82 Folic Acid, mcg 120 60.0 Cohnii Oil*, Microcrystalline Cellulose, • Tyrosine- and phenylalanine-free • Tyrosinemia L-Cystine 0.83 0.42 Pantothenic Acid, mg 1.8 0.9 Natural Flavor, Taurine, Fruit Concentrate Glycine 1.63 0.82 Biotin, mcg 53.4 26.7 (Apple, Blackcurrant, Radish), L-Ascorbic • Low volume; provides 20 g PE in just Acid, Guar Gum, Sunflower Lecithin, L-Histidine 0.95 0.48 4.2 fl oz (125 mL) Vitamin C, mg 17.8 8.9 Xanthan Gum, M-Inositol, Potassium L-Isoleucine 1.55 0.78 Choline, mg 153 76.5 For details on administration, please see pages 124-136. Sorbate (preservative to delay spoilage), • Convenient ready-to-drink L-Leucine 2.50 1.25 Inositol, mg 40.6 20.3 Artificial Sweetener: Sucralose, • Based on fruit juices (from concentrate) L-Lysine 1.75 0.88 Minerals Ferrous Lactate, Artificial Sweetener: Acesulfame Potassium, L-Carnitine, L-Methionine 0.40 0.20 with natural flavor - no artificial flavors Calcium, mg 319 160 Sodium Benzoate (preservative to delay • Contains a balanced mixture of L-Phenylalanine Trace* Trace* Phosphorus, mg 244 122 spoilage), Zinc Sulfate, Niacinamide, essential and non-essential amino acids, Ordering/Reimbursement Information: L-Proline 2.03 1.02 Magnesium, mg 96.3 48.2 DL-alpha Tocopheryl Acetate, Calcium L-Serine 1.30 0.65 Iron, mg 5.1 2.6 D-Pantothenate, Manganese Sulfate, carbohydrates, vitamins, minerals and Product Reimbursement HCPCS Product Calories Cupric Sulfate, Thiamin Chloride L-Threonine 1.25 0.63 DHA Code Code Code* Packaging Per Pouch Zinc, mg 3.8 1.9 Hydrochloride, Pyridoxine Hydrochloride, L-Tryptophan 0.50 0.25 Manganese, mg 0.56 0.28 82113 49735-0167-50 B4157 or B4162 30 X 4.2 fl oz (125 mL) 120 Vitamin A Palmitate, Riboflavin, Folic • Contains 150 mg of DHA per pouch L-Tyrosine Trace* Trace* Copper, mcg 563 282 Acid, Potassium Iodide, Ascorbyl • Available in mixed berry blast flavor L-Valine 1.65 0.83 Iodine, mcg 56.3 28.2 Palmitate, Mixed Tocopherols, Sodium Molybdate, D-Biotin, Sodium Selenite, ‡ L-Carnitine 0.02 0.01 • Osmolality (at 0.96 kcal/mL): WIC : Contact your state WIC For more reimbursement Molybdenum, mcg 25.0 12.5 Chromium Chloride, Phylloquinone, office to determine availability. information see page 195. Taurine 0.14 0.07 Chromium, mcg 10.8 5.4 Vitamin D , Cyanocobalamin. 2460 mOsm/kg 3

Metabolics Selenium, mcg 26.8 13.4 * S9435 = For individuals who submit their bills to insurance on their own. *A Source of Docosahexaenoic Acid Sodium, mg <25.0 <12.5 (DHA). Potassium, mg 90 45 Chloride, mg <25.0 <12.5 Contains 44.1% juice. 118 *May contain traces of tyrosine and phenylalanine from fruit juice (from concentrate). 119 UCD Anamix Junior

UCD Anamix® Junior Nutrition Information: Ingredients: Per 10 g Protein Per 10 g Protein A powdered medical food containing essential amino acids (with Unflavored: Corn Syrup Solids, Refined Nutrients Per 100 g Equivalent Vitamins Per 100 g Equivalent Vegetable Oils (High Oleic Safflower, increased levels of branched chain amino acids (BCAAs) and tryptophan), Calories 385 321 Vitamin A, IU (mcg RE) 3197.(960) 2664.(800) Canola, Fractionated Coconut), Sugar, carbohydrates, fat, vitamins and minerals; for the dietary management Protein Equivalent, g 12.0 10.0 Vitamin D3, IU (mcg) 920.(23.0) 767.(19.2) L-Leucine, Sodium Phosphate Dibasic, Tripotassium Citrate, Tricalcium of urea cycle disorders (UCD); hyperammonemia, hyperornithinemia, Fat, g 17.0 14.2 Vitamin E, IU (mg α-TE) 27.5 (18.5) 22.9 (15.4) Citrate, Tricalcium Phosphate, L-Lysine Carbohydrate, g 46.0 38.3 Vitamin K, mcg 92.2 76.8 homocitrullinemia (HHH) syndrome; and gyrate atrophy in patients over Hydrochloride, L-Valine, L-Isoleucine, Amino Acids, g the age of 1. Thiamin, mg 1.9 1.6 Magnesium Hydrogen Phosphate, L-Alanine Nil Added Nil Added Riboflavin, mg 1.5 1.3 L-Threonine, Choline Bitartrate, Main Features: Indications: L-Arginine Nil Added Nil Added Vitamin B6, mg 1.5 1.3 L-Tyrosine, Potassium Chloride, Citric L-Asparagine Nil Added Nil Added Vitamin B12, mcg 3.8 3.2 Acid Ester of Mono- And Diglycerides (An • Contains essential amino acids to • Urea Cycle Disorders (UCD) L-Aspartic Acid Nil Added Nil Added Niacin, mg 9.6 8.0 Emulsifier), L-Phenylalanine, L-Histidine, L-Tryptophan, L-Cystine, L-Methionine, help maintain a positive nitrogen L-Citrulline Nil Added Nil Added Folic Acid, mcg 461 384 • Hyperammonemia, Hyperornithinemia, Homocitrullinemia L-Ascorbic Acid, M-Inositol, Ferrous L-Cystine 0.43 0.36 balance in UCD (HHH) syndrome Pantothenic Acid, mg 6.1 5.1 Sulfate, Taurine, Zinc Sulfate, DL-alpha • Amino acid profile rich in BCAAs for L-Glutamic Acid Nil Added Nil Added Biotin, mcg 34.6 28.8 Tocopheryl Acetate, Manganese Sulfate, • Gyrate atrophy L-Glutamine Nil Added Nil Added efficient and optimal protein synthesis Vitamin C, mg 120 100 Niacinamide, L-Carnitine, Calcium-D- For details on administration and household measurements, please Glycine Nil Added Nil Added Choline, mg 480 400 Pantothenate, Cupric Sulfate, Thiamin for children with UCD Chloride Hydrochloride, Pyridoxine see pages 124-136. L-Histidine 0.51 0.43 Inositol, mg 108 90 • Sufficient non-protein calories to L-Isoleucine 2.26 1.88 Minerals Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Potassium Iodide, prevent protein being broken down for L-Leucine 3.82 3.18 Calcium, mg 1555 1296 Visit NutriciaLearningCenter.com for a practical guide for Sodium Selenite, Chromium Chloride, L-Lysine 1.92 1.60 energy and toxic metabolites the use of UCD Anamix Junior. Phosphorus, mg 1555 1296 Sodium Molybdate, PhylloquiNil Added, being produced L-Methionine 0.40 0.33 Magnesium, mg 246 205 D-Biotin, Vitamin D3, Cyanocobalamin. L-Phenylalanine 0.67 0.56 Iron, mg 26.9 22.4 • Essential micronutrients such as Vanilla flavored version also contains: L-Proline Nil Added Nil Added calcium, vitamin D, iron and zinc Ordering/Reimbursement Information: Zinc, mg 21.1 17.6 Artificial flavor. L-Serine Nil Added Nil Added Manganese, mg 3.6 3.0 supplied to compensate for low intake CONTAINS: Coconut Oil. Product Reimbursement HCPCS Product Calories L-Threonine 1.59 1.33 Copper, mcg 1900 1583 from natural food Code Code Code* Packaging Per Can L-Tryptophan 0.48 0.40 Iodine, mcg 276 230 • Available in unflavored and vanilla flavor 59292 - Unflavored 49735-0192-92 B4157 or B4162 6 X 400 g (14 oz) 1540 L-Tyrosine 1.23 1.03 Molybdenum, mcg 63.4 52.8 • Osmolality (mOsm/kg): 59293 - Vanilla 49735-0192-93 B4157 or B4162 6 X 400 g (14 oz) 1540 L-Valine 2.29 1.91 Chromium, mcg 41.3 34.4 Metabolics Dilution L-Carnitine 0.009 0.008 Selenium, mcg 76.8 64.0 1 to 3.5 1040 WIC‡: Contact your state WIC For more reimbursement Taurine 0.069 0.058 Sodium, mg 1114 928 office to determine availability. information see page 195. Potassium, mg 1613 1344 • Displacement: 0.70 mL/g 120 Chloride, mg 864 720 121 * S9435 = For individuals who submit their bills to insurance on their own. SOD

SOD Anamix® Early Years XMet, XCys Maxamaid®

A methionine- and cystine-free powdered infant formula for the dietary management of A methionine- and cystine-free powdered medical food for the dietary management of conditions requiring conditions requiring restriction of methionine and cystine (e.g. sulphite oxidase deficiency). restriction of methionine and cystine (e.g. sulphite oxidase deficiency) in individuals over 1 year of age.

Main Features: Indications: Main Features: Indications: • Methionine- and cystine-free • Sulphite oxidase deficiency • Methionine-, cystine-free powdered • Sulphite oxidase deficiency • Contains a balanced mixture of all other • Other conditions requiring restriction of methionine and infant formula with iron • Other conditions requiring restriction of methionine essential and non-essential amino acids, cystine • Includes DHA & ARA and cystine carbohydrate, vitamins, minerals and • Contains a prebiotic fiber blend trace elements For details on administration and household measurements, please For details on administration and household measurements, please • XMet, XCys Maxamaid provides 25 g of see pages 124-136. • Unflavored powder see pages 124-136. • Contains a balanced mixture of all other protein equivalent per 100 g of powder essential and non-essential amino acids, • Available as unflavored powder Additional Information: Additional Information: carbohydrates, fat, vitamins, minerals • Contains <1 g of fat per 10 g PE thereby Please note that this product is available by special order only. and trace elements Please note that this product is available by special order only. allowing greater flexibility in modifying For detailed information on XMet, XCys Maxamaid, please • Provides 13.5 g of protein equivalent For detailed information on SOD Anamix Early Years, please energy intake contact our Nutrition Services Department. per 100 g of powder contact our Nutrition Services Department. • Osmolality (mOsm/kg): • Osmolality (at 0.7 kcal/mL): Dilution Ordering/Reimbursement Information: 380 mOsm/kg Ordering/Reimbursement Information: 1 to 5 690 Based on dilution of 5 g powder 1 to 7 490 Product Reimbursement HCPCS Product Calories (1 unpacked level scoop) to 1 fl oz Product Reimbursement HCPCS Product Calories Code Code Code Packaging Per Can Code Code Code* Packaging Per Can (30 mL) water 116194 (Special Order) 49735-0114-57 B4162 3 x 500 g (17.6 oz) 1545 90212 (Special Order) 49735-0102-12 B4162 3 x 400 g (14 oz) 1892

Metabolics • Displacement: 0.75 mL/g

* S9435 = For individuals who submit their bills to insurance on their own. 122 123 Metabolic Household Measurements Household Measurements Measure g Product g Protein Measure g Product g Protein Measure g Product g Protein Measure g Product g Protein Equivalent Equivalent Equivalent Equivalent PKU Periflex Early Years HCU Anamix Next PhenylAde 40 Drink Mix Complex MSD Amino Acid Blend Enclosed scoop 5.0 0.68 Enclosed scoop 9.0 2.5 1 pouch 25 10 Enclosed scoop 12.4 10 1 Tbsp 9.0 1.2 1 Tbsp 8.3 2.3 PhenylAde 60 Drink Mix 1 Tbsp 8.2 6.6 1 cup 144 19.4 1 cup 133 37.2 Enclosed scoop or 1 pouch 16.7 10 1 cup 124 100 MSUD Anamix Early Years IVA, MMA/PA Anamix Next 1 Tbsp 9.8 5.9 Maxamum Range (Flavored & Unflavored) Enclosed scoop 5.0 0.68 Enclosed scoop 9.0 2.5 1 cup 148 90 1 Tbsp 9 3.6 1 Tbsp 9.0 1.2 1 Tbsp 8.8 2.5 PhenylAde MTE Amino Acid Blend 1 cup 145 58 1 cup 140 19.4 1 cup 140 39.2 Enclosed scoop or 1 pouch 12.8 10 GA-1, TYR, MMA/PA, HCU, IVA Anamix Early Years UCD Anamix Junior Unflavored 1 Tbsp 8.5 6.6 Enclosed scoop 5.0 0.68 Enclosed scoop 5.0 0.60 1 cup 116 90 1 Tbsp 8.8 1.2 1 Tbsp 9.0 1.1 GlutarAde Junior GA-1 Drink Mix 1 cup 140 18.9 1 cup 143 17.2 Enclosed scoop 9.8 0.98 PKU Periflex Junior Plus (Plain) UCD Anamix Junior Vanilla 1 Tbsp 9.3 0.93 Enclosed scoop 9.0 2.5 Enclosed scoop 5.0 0.60 1 cup 146 14.6 1 Tbsp 8.7 2.4 1 Tbsp 8.7 1.0 GlutarAde Essential GA-1 Drink Mix 1 cup 139 38.9 1 cup 139 16.7 Enclosed scoop 40 10 PKU Periflex Junior Plus (Flavors) Periflex Advance 1 Tbsp 10 2.5 Enclosed scoop 9.0 2.5 1 Tbsp 9.4 3.3 1 cup 160 40 1 Tbsp 8.3 2.3 1 cup 150 53 GlutarAde GA-1 Amino Acid Blend 1 cup 132 37 PhenylAde Essential Drink Mix Enclosed scoop 12.3 10 TYR Anamix Next Enclosed scoop or 1 pouch 40 10 1 Tbsp 8.5 6.9 Enclosed scoop 9.0 2.5 1 Tbsp 10 2.5 1 cup 116 94 1 Tbsp 8.6 2.4 1 cup 160 40 Complex Junior MSD Drink Mix 1 cup 137 38.4 PhenylAde GMP Drink Mix Enclosed scoop 8.5 1.1 Enclosed scoop or 1 pouch 33.3 10 1 Tbsp 8.4 1.1 1 Tbsp 6.6 2 1 cup 118 15.2 1 cup 128 38.4 Complex Essential MSD Drink Mix Household measures are based on standard US, dry household measures.* PhenylAde GMP Mix-In Enclosed scoop 40 10 All measures are level and unpacked. These values are approximations only Household measures are based on standard US, dry household measures.* 1 pouch 12.5 10 1 Tbsp 9.8 2.4 and have been provided for convenience: results can vary significantly based All measures are level and unpacked. These values are approximations only 1 cup 160 40 on the individual, device, and method. Nutricia North America recommends and have been provided for convenience: results can vary significantly based using a gram scale for greatest accuracy. The scoops Nutricia provides are on the individual, device, and method. Nutricia North America recommends Metabolics validated for use with Nutricia formulas, so are preferable to household using a gram scale for greatest accuracy. The scoops Nutricia provides are measures. validated for use with Nutricia formulas, so are preferable to household measures. *US measures: 1 cup = 240 mL; ½ cup = 120 mL; ⅓ cup = 80 mL; ¼ cup = 60 mL; 1 Tbsp = 15 mL; 1 tsp = 5 mL; ½ tsp = 2.5 mL *US measures: 1 cup = 240 mL; ½ cup = 120 mL; ⅓ cup = 80 mL; 124 ¼ cup = 60 mL; 1 Tbsp = 15 mL; 1 tsp = 5 mL; ½ tsp = 2.5 mL 125 Metabolic Mixing Instructions PKU Periflex® & Anamix® Early Years PKU Periflex® Junior Plus & Anamix® Next Powdered infant formulas with iron containing DHA and ARA, and a unique blend of prebiotic fiber. Metabolic formulas for the dietary management of metabolic disorders in individuals over one year of age. Amount of Amount of Approx. Approx. Administration: Water Powder Protein Equiv. Final Volume • Must be consumed in conjunction with a whole protein 5 fl oz (150 mL) 5 scoops (25 g) 3.4 g 5.6 fl oz (168 mL) Administration: source (e.g. breast milk or standard infant formula) in Dilution Amount of Water Final 8 fl oz (240 mL) 8 scoops (40 g) 5.4 g 9 fl oz (270 mL) • PKU Periflex Junior Plus & Anamix Next must be (kcal/mL) Powder Added Volume quantities prescribed by a dietitian or physician to meet 12 fl oz (360 mL) 12 scoops (60 g) 8.1 g 13.5 fl oz (405 mL) consumed in conjunction with whole protein and 0.6 18 g (approx 2 scoops) 3.5 fl oz (100 mL) 3.9 fl oz (114 mL) the general nutrition requirements to ensure normal 0.9 27 g (approx 3 scoops) 3.5 fl oz (100 mL) 4.0 fl oz (120 mL) *Boiling is the preferred method of sterilizing water, bottles, other nutrients in quantities prescribed by a dietitian growth and development. 1.1 36 g (approx 4 scoops) 3.5 fl oz (100 mL) 4.3 fl oz (126 mL) nipples and mixing utensils. or physician to supply the fluid and general nutrition • Formula dosage and dilution will vary depending on requirements. the age, body weight, medical condition and protein Important Preparation Information: Freshly prepared • Intended for individuals over 1 year of age. Freshly prepared formula is best. Refrigerate pre- tolerance of the infant. formula is best. Formula prepared in advance must be cooled mixed formula immediately and use within 24 hours rapidly, stored in the refrigerator and used within 24 hours of • Intake of Periflex Junior Plus or Anamix Next is Mixing Instructions: preparation. Formula remaining in the bottle after one hour dependent on the age, body weight and medical of mixing. Shake immediately before use. Tube feeding of feeding should be discarded. Powdered infant formula is condition of the individual. Periflex Junior Plus or hang time not to exceed 4 hours. • To make a standard dilution (21 kcal/fl oz), add 1 not sterile. Anamix Next should be divided into equal portions unpacked level scoop (5 g) of powder to each fluid and distributed throughout the day. Precautions: ounce of water. Only use the scoop provided. For Precautions: • Must only be consumed by individuals with proven accuracy formula should be weighed on a gram scale. Mixing Instructions: inborn errors of metabolism. Not intended for infants. • Do not boil formula or use a microwave to prepare or Not intended as sole source of nutrition. Not for • PKU Periflex/Anamix Early Years may be mixed with warm formula. • Add the desired volume of water to a shaker or warm or cool sterile water. Do not boil formula or use a other container with a tight fitting lid. Then add the parenteral use. • Must be given under strict medical supervision microwave to prepare or warm formula. prescribed amount of powder and shake until fully to infants with a proven metabolic disorder. Not Storage: To make formula: blended together. Best served chilled. intended as the sole source of nutrition. Not for • Store unopened can at room temperature. Do not 1) Wash hands thoroughly and clean the preparation area. • Standard solution is 3.5 fl oz (100 mL) water plus 36 g parenteral use. store at extreme temperatures. Once opened, 2) Pour the required amount of cooled, boiled water into powder (approx. 4 scoops) made up to a final volume Storage: of approx. 4.3 fl oz (126 mL). reseal can and store in a cool, dry place (not the sterilized feeding bottle*. refrigerator) and use within 14 days of opening.

Metabolics 3) Add the prescribed number of leveled scoops of • Store unopened cans at room temperature. Avoid formula to the water in the sterilized feeding bottle. extreme temperatures. Once opened, reseal can 4) Place cap on the bottle and shake until the powder and store in a cool, dry place. Use within two weeks. 126 dissolves. Shake immediately BEFORE USE. 127 Metabolic Mixing Instructions Periflex® Advance and Periflex® LQ Maxamum® Age-specific medical foods for the dietary management of phenylketonuria (PKU) in children and adults, Age-specific medical foods for the dietary management of metabolic disorders in older children and adults, including pregnant women and women of child-bearing age. including pregnant women and women of child-bearing age. Administration: Dilution Guidelines for Maxamum Administration: Dilution Guidelines for Periflex Advance Dilution Amount of Powder Volume of Water Approx. PE • Must be consumed in conjunction with whole protein, • Use only under the direction of a physician or Volume of Water Prescribed Amount Approx. Protein Equiv. 1 to 7 35 g 245 mL (approx. 8 fl oz) 14 g fluid and other nutrients in quantities prescribed by dietitian. Periflex must be consumed in conjunction 2 to 3 fl oz (60-90 mL) 16 g 6 g 1 to 7 1 sachet (50 g) 350 mL (approx. 12 fl oz) 20 g with whole protein, fluid and other nutrients in 4 to 5 fl oz (120-150 mL) 32 g 11 g a physician or dietitian to meet protein and general 1 to 5 35 g 175 mL (approx. 6 fl oz) 14 g quantities prescribed by a physician or dietitian 8 to 10 fl oz (240-300 mL) 64 g 22 g nutrition requirements. 1 to 5 1 sachet (50 g) 250 mL (approx. 8 fl oz) 20 g to meet phenylalanine and general nutritional 16 to 20 fl oz (480-600 mL) 128 g 45 g • Recommended intake will vary depending on the age, requirements. body weight and medical condition of the individual. • It is recommended that Maxamum be prepared at a 1 Intake is adjusted to maintain normal growth and to 7 dilution initially and advanced to a 1 to 5 dilution. • Periflex Advance is intended for older children and • Once prepared, store formula in a refrigerator for no development. For accuracy, weigh on a gram scale. These dilutions are guidelines only. May be given in adults, including pregnant women and women of longer than 24 hours from the time of preparation. The daily intake should be divided into equal portions a more concentrated form (e.g. drink or paste). If so, child-bearing age. Shake or stir prepared formula immediately before use. and distributed throughout the day. water or diluted drinks should be offered at the same • Intake of Periflex is dependent on the age, Periflex LQ • Intended for older children and adults, including time. bodyweight and medical condition of the individual. Shake well before use. Best served chilled. pregnant women and women of child-bearing age. Precautions: Periflex should be divided into equal portions and • Must only be given under strict medical supervision distributed throughout the day. Precautions: Mixing Instructions: • Must only be consumed by individuals with proven • Best served with meals. to patients with proven phenylketonuria. Not Mixing Instructions: phenylketonuria. Not intended for infants. Not intended • Make a paste of the prescribed amount of powder intended for children under one year of age. Not Periflex Advance as the sole source of nutrition. Not for parenteral use. with a small volume of chilled water. Gradually add suitable as the sole source of nutrition. Not for • Add the desired volume of water to a shaker or parenteral use. Storage: sufficient water to make the desired volume. other container with a tight fitting lid. Then add the • For best taste, consume immediately. Larger volumes Storage: prescribed amount of powder and shake until fully • Store unopened can at room temperature. Do not of prepared formula should be refrigerated and • Store unopened cans/sachets at room temperature. blended together. Dilution guidelines are shown in store at extreme temperatures. Once opened, reseal used within 24 hours of preparation. Shake or stir Do not store at extreme temperatures. Once opened, the tables below. Periflex is best served chilled. can and store in a cool, dry place (not in refrigerator) prepared formula immediately before use. reseal can and store in a cool, dry place (not in • Periflex tastes great when blended with 1 fl oz and use within one month of opening. Metabolics (30 mL) of water for every 5 to 6 grams of powder. • Store Periflex LQ in a cool dry place away from sunlight. Dilutions are guidelines only. Periflex Advance may be given in a more concentrated form (e.g., a paste or concentrated drink) by using less 128 water. If consumed in a concentrated form, water or other drinks should also be consumed at the same time. 129 Metabolic Mixing Instructions PhenylAde® Phlexy-10® Formulas for the dietary management of phenylketonuria (PKU) in children and adults, including pregnant women An interchangeable system of phenylalanine-free medical foods for the dietary management of phenylketonuria and woman of child-bearing age. (PKU) in individuals over 1 year of age, including pregnant women and women of child-bearing age. • PhenylAde GMP Mix-In Administration: Administration: Mixing Instructions: • Use only under the direction of a physician or dietitian. Add contents of 1 pouch (12.5 g) to approx. 5 - 6fl oz (150 - PhenylAde must be consumed in conjunction with whole 180 mL) of cold water or a flavored (protein-free) beverage. • The Phlexy-10 products must be consumed in • Phlexy-10 Drink Mix: Mix the contents of one protein, fluid and other nutrients in quantities prescribed • PhenylAde40 Drink Mix conjunction with whole protein, fluid and other packet with a small amount of water, stirring into a by a physician or dietitian to meet the phenylalanine and nutrients in quantities prescribed by a physician thick paste. Continue stirring while adding water Add contents of 1 pouch (25 g) to approx. general nutrient requirements. or dietitian to meet phenylalanine and general to make up a final volume of approximately 100 4-6 fl oz (120-180 mL) of cold water. nutrition requirements. Fat, carbohydrate and mL (~3.5 fl oz). Once prepared, store formula in a Mixing Instructions: • PhenylAde60 Drink Mix low protein sources may be used to supply refrigerator for no longer than 24 hours from the 1. Add prescribed amount of PhenylAde Powder to cold water, Add contents of 1 scoop or pouch (16.7 g) to approx 3 fl oz needed calories and to fulfill essential fatty acid time of preparation. Shake or stir prepared formula shake or stir until completely mixed together. (90 mL) of cold water. requirements. immediately before use. 2. Dilution may be adjusted to taste. See recommended dilution • PhenylAde Amino Acid Blends • Intake of the Phlexy-10 products will vary • Phlexy-10 Tablets: Should be taken with water or below for a guideline. Simply add one serving to single portion of low protein food, depending on the age, body weight and medical a non-phenylalanine-containing beverage. 3. Once prepared, store formula in a refrigerator for no more condition of the individual. Intake is adjusted to beverage or other PKU formula. The appropriate serving Precautions: than 24 hours from the time of preparation. Shake or stir size must be established and consumed to meet prescribed maintain normal growth and development. One prepared formula immediately before use. amino acid protein requirements. Not intended to be added packet of the drink mix or 10 tablets provide 10 g • Must only be given under strict medical supervision 4. Do not heat, bake or add to food or beverages above 130°F. to plain water. of amino acids, equivalent to 8.33 g of protein. to patients with proven phenylketonuria. Not • The Phlexy-10 products do not contain vitamins, intended for use as the sole source of nutrition. Not Recommended Dilution: Precautions: minerals, or trace elements. It is essential that intended for infants under 1 year of age. Not for • PhenylAde Essential Drink Mix • Must be consumed by individuals with proven these nutrients are supplied separately. parenteral use. phenylketonuria. Not intended for infants. Not intended as Phlexy-Vits (see pages 180-181) are available Add contents of 1 scoop or pouch (40 g) to approx. the sole source of nutrition. Not for parenteral use. to be used as a supplement to the Phlexy-10 Storage: 7 fl oz (210 mL) of cold water. System. One 7 g packet supplies the majority of • Phlexy-10 Drink Mix and Tablets should be stored • PhenylAde GMP Drink Mix Storage: vitamins and minerals needed to meet the RDA of • Store unopened can at room temperature. Do not store in a cool, dry place. Once Phlexy-10 Tablets are Add contents of 1 scoop or pouch (33.3 g) to approx. 5-6 fl oz individuals 11 years and older. Metabolics at extreme temperatures. Once opened, reseal can and opened, reseal can and store in a cool, dry place (150-180 mL) of cold water. store in a cool, dry place (not in refrigerator) and use within (not in refrigerator) and use within one month. one month of opening for all PhenylAde products except 130 PhenylAde GMP Drink Mix. PhenylAde GMP Drink Mix 131 must be used within 2 weeks after being opened. Metabolic Mixing Instructions PhenylAde® PheBLOC™ LNAA and Lanaflex® Lophlex® Powder and Lophlex® LQ Phenylalanine-free powdered medical foods containing the remaining essential amino acids (large neutral amino acids A low volume, amino acid-based medical food for the dietary management of metabolic disorders in children and and lysine). For the dietary management of phenylketonuria (PKU) in individuals over 12 years of age. adults, including pregnant women and women of child-bearing age. Administration: PhenylAde PheBLOC LNAA Administration: Mixing Instructions (Lophlex): • Add contents of 1 pouch (3 g) to ~1/2 cup of any • Use only under the direction of a physician or • Use only under the direction of a physician • Mix the contents of one sachet with a small dietitian. The product must be consumed in semi-solid food (i.e., applesauce, mashed potatoes, pudding, sorbet, etc). or dietitian. Lophlex and Lophlex LQ must be amount of water to make a paste. Continue stirring conjunction with whole protein, fluid and other consumed in conjunction with whole protein, while adding water to make up a final volume of nutrients in quantities prescribed by a physician fluid and other nutrients in quantities prescribed approximately 70 mL (2.5 fl oz). This would be a or dietitian to meet phenylalanine and general Precautions: by a physician or dietitian to meet amino 1 to 5 dilution. Lophlex may be taken in a more nutrition requirements. • Must only be consumed by individuals with proven acid and general nutrition requirements. Fat, concentrated form, either as a drink or paste. If so, • Intake of the product is dependent on the age, phenylketonuria. Suitable for individuals over 12 carbohydrate and low protein sources may be water or diluted drinks should be offered at the bodyweight and medical condition of the individual. years of age. Not suitable as the sole source of used to supply needed calories and to fulfill same time. Lophlex is best prepared with chilled nutrition. Not for parenteral use. essential fatty acid requirements. water and after preparation. Larger volumes of Mixing Instructions: • Not for use when planning or • Intake of Lophlex and Lophlex LQ will vary prepared formula should be refrigerated and Lanaflex during pregnancy. depending on the age, body weight and medical used within 24 hours of preparation. Shake or stir prepared formula immediately before use. • It is recommended that the product is prepared • Seek medical advice before using with condition of the individual. Intake is adjusted to at an approximate 1 to 4 dilution. In a screw-top serotonergic medications or any kind of maintain normal growth and development. Lophlex Precautions: container, add 60 mL (2 fl oz) of chilled water. psychotropic medications. and Lophlex LQ should be divided into equal Add the contents of one sachet and shake well portions and distributed throughout the day. • Must only be given under strict medical supervision Storage: in individuals with a proven metabolic disorder. until dissolved. The product is best consumed Preparation (Lophlex LQ) immediately. • Store unopened sachets in a cool, dry place. Not intended as a sole source of nutrition. Not for parenteral use. • If taken in a more concentrated form, water • Lophlex LQ is ready-to-drink and tastes best when or diluted drinks should be consumed served chilled. Shake vigorously before use. Storage: Visit NutriciaLearningCenter.com for guidelines immediately afterwards. on the usage of PhenylAde PheBloc LNAA, and • Store in a cool, dry place, below 86oF (not in the

Metabolics • Opened sachets should be stored in an airtight guidelines for the usage of Lanaflex in the dietary refrigerator) and away from sunlight. container and used within 24 hours. management of PKU

132 133 Metabolic Mixing Instructions Complex MSD: Junior, Essential and Amino Acid Blend GlutarAde™ GA-1: Junior, Essential and Amino Acid Blend Medical foods for the dietary management of Maple Syrup Urine Disease (MSUD) in children and adults, Medical foods for the dietary management of Glutaric Aciduria Type 1 (GA-1) in children and adults, including including pregnant women and woman of child-bearing age. pregnant women and woman of child-bearing age. Dilution of approx. 30 calories per 1 fl oz (30 mL) Dilution of approx. 30 calories per 1 fl oz (30 mL) Administration: Administration: To Make Approx. Water Amount of Powder To Make Approx. Water Amount of Powder • Use only under the direction of a physician or • Use only under the direction of a physician or dietitian. 2 fl oz (60 mL) 2 fl oz (60 mL) 14.7 g 2 fl oz (60 mL) 2 fl oz (60 mL) 12.2 g dietitian. Complex must be consumed in conjunction GlutarAde must be consumed in conjunction with whole 4 fl oz (120 mL) 4 fl oz (120 mL) 29.4 g 4 fl oz (120 mL) 4 fl oz (120 mL) 24.3 g with whole protein, fluid and other nutrients in protein, fluid and other nutrients in quantities prescribed 6 fl oz (180 mL) 6 fl oz (180 mL) 44.1 g 6 fl oz (180 mL) 6 fl oz (180 mL) 36.5 g 8 fl oz (240 mL) 8 fl oz (240 mL) 58.8 g quantities prescribed by a physician or dietitian 8 fl oz (240 mL) 8 fl oz (240 mL) 48.6 g by a physician or dietitian to meet the lysine and general to meet the branched-chain and general nutrient nutrient requirements. • GlutarAde GA-1 Essential Drink Mix requirements. • Complex Essential MSD Drink Mix Mixing Instructions: Add contents of 1 scoop (40g) to approx. 7 fl oz (210 mL) Add contents of 1 scoop (40 g) to approx. 7 fl oz (210 mL) Mixing Instructions: • Add prescribed amount of GlutarAde Powder to cold water, of cold water. of cold water. • Add prescribed amount of Complex Powder to cold shake or stir until completely mixed together. • GlutarAde GA-1 Amino Acid Blend water, shake or stir until completely mixed together. • Complex MSD Amino Acid Blend • Dilution may be adjusted to taste. See recommended Simply add one serving to single portion of low protein • Dilution may be adjusted to taste. See recommended Simply add one serving to single portion of low dilution below for a guideline. food, beverage or other GA-1 formula. dilution below for a guideline. protein food, beverage or other MSUD formula. The • Once prepared, store formula in a refrigerator for no more The appropriate serving size must be established and • Once prepared, store formula in a refrigerator for no appropriate serving size must be established and than 24 hours from the time of preparation. Shake or stir consumed to meet prescribed amino acid protein more than 24 hours from the time of preparation. Shake consumed to meet prescribed amino acid protein prepared formula immediately before use. requirements. Not intended to be added requirements. Not intended to be added to plain water. or stir prepared formula immediately before use. • Do not heat, bake or add to food or beverages above 130°F. to plain water. • Do not heat, bake or add to food or beverages above Precautions: 130°F. • Must be consumed by individuals with proven maple Recommended Dilution Precautions: • Must be consumed by individuals with proven glutaric syrup urine disease. Not intended for infants. Not • GlutarAde Junior GA-1 Drink Mix Recommended Dilution: aciduria type 1. Not intended for infants. Not intended intended as the sole source of nutrition. Not for • Complex Junior MSD Drink Mix as the sole source of nutrition. Not for parenteral use. parenteral use. Dilution of approx. 20 calories per 1 fl oz (30 mL) Dilution of approx. 20 calories per 1 fl oz (30 mL) To Make Approx. Water Amount of Powder To Make Approx. Water Amount of Powder Storage: Storage: 2 fl oz (60 mL) 2 fl oz (60 mL) 9.8 g 2 fl oz (60 mL) 2 fl oz (60 mL) 8.5 g • Store unopened can at room temperature. Do not store • Store unopened can at room temperature. Do not store 4 fl oz (120 mL) 4 fl oz (120 mL) 19.5 g Metabolics 4 fl oz (120 mL) 4 fl oz (120 mL) 17 g at extreme temperatures. Once opened, reseal can and at extreme temperatures. Once opened, reseal can and 6 fl oz (180 mL) 6 fl oz (180 mL) 29 g 6 fl oz (180 mL) 6 fl oz (180 mL) 26 g store in a cool, dry place (not in refrigerator) and use store in a cool, dry place (not in refrigerator) and use 8 fl oz (240 mL) 8 fl oz (240 mL) 39 g 8 fl oz (240 mL) 8 fl oz (240 mL) 34 g within one month of opening. within one month of opening.

134 1 level, unpacked scoop provides approx. 8.5 g of powder. For better accuracy use a gram scale. 1 level, unpacked scoop provides approx. 9.8 g of powder. For better accuracy use a gram scale. 135 UCD Anamix® Junior Medical food for the dietary management of urea cycle disorders in individuals over 1 year of age. Administration: • It is recommended that UCD Anamix Junior be prepared at a 1 to 3.5 dilution. This dilution • Must be consumed in conjunction with whole is a guideline only. An alternative dilution may protein, fluid and other nutrients in quantities be recommended by a clinician or dietitian (e.g. prescribed by a physician or dietitian to meet drink or paste). If given in a more concentrated protein and general nutrition requirements. form, water or diluted drinks should be offered • Recommended intake of UCD Anamix Junior at the same time. is dependent on age, body weight and medical • Once prepared, store formula in a refrigerator condition of the individual. Intake is adjusted for no longer than 24 hours from the time of to maintain normal growth and development. preparation. Shake or stir prepared formula For accuracy, weigh on a gram scale. The daily immediately before use. intake should be divided into equal portions and distributed throughout the day. Dilution Guidelines for UCD Anamix Junior • UCD Anamix Junior is intended for patients over Dilution Amount of Powder Volume of Water Approx. PE 1 year of age, including pregnant women and 1 to 3.5 50 g (10 scoops) 175 mL (approx. 6 fl oz) 6.0 g women of child-bearing age. Precautions: Mixing Instructions: • Must only be given under strict medical • Best served chilled with meals. supervision to patients with proven urea cycle LOW PROTEIN disorders. Not intended for children under one • Pour the required volume of cold water into a year of age. Not suitable as the sole source of glass or cup. FOODS nutrition. Not for parenteral use. • Add the prescribed amount of UCD Anamix Junior powder to the water and stir. For accuracy it is Storage: recommended to use a gram scale.

Metabolics • Store unopened cans in a cool, dry place. Do not store at extreme temperatures. Once opened, Visit NutriciaLearningCenter.com for a practical guide for Find more information and resources on these and all of our the use of UCD Anamix Junior. reseal can and store in a cool, dry place (not in refrigerator) and use within one month. products at www.NutriciaLearningCenter.com 136 137137 Loprofin, Milupa and Low Protein Foods A line of low protein foods including cake mix, pasta, rice, cereals, drink mix, crackers and more

Main Features: Indications: • A wide range of products to add variety to a • Dietary management of inherited metabolic disorders protein-restricted diet • Renal or liver failure requiring a low protein diet • Other medical conditions where a low protein diet is indicated Protein Foods Low For more information, visit www.MedicalFood.com

138 NEUROLOGY

TM Find more information and resources on these and all of our products at www.NutriciaLearningCenter.com 139 140 NEUROLOGY • Fat • • • • • • • • • • • Main No 150 mOsm/kg energy requirements Displacement Energy distribution: No artificialsweeteners Osmolality (at1kcal/mL) Standard dilution=1kcal/mL Appropriate forenteral ororal feedings Nutrient denseforchildrenwithlow Unflavored 3:1 ratio DHA andARA Nutritionally complete Carbohydrate Protein trans (LCT 100%) Fea fat tures:

ketogenic dietisindicated;designedforindividualsover 1year ofage.Amedicalfood. the dietarymanagementofintractable epilepsyandothermedicalconditionswherethe A nutritionallycomplete,ketogenic formulaina3:1ratio (fat:carbohydrate +protein)for KetoCal 87.1% 1 mL/g 4.1% 8.8%

® 3:1Powder For detailsonadministration, please seepages146-147. • • • • Indications: 16672 Code Product Ordering/Reimbursement Information:

Other disorderswheretheketogenic dietisindicated Glucose transporter type-1deficiency (GLUT1) Pyruvate dehydrogenase deficiency(PDH) Intractable epilepsy office todetermine availability. WIC ‡ : Contactyour stateWIC 49735-0166-72 Reimbursement B4154 Code Packaging HCPCS information seepage 195. information For morereimbursement 6 x300g(11oz) Product 2097 Per Calories Can

Nutrition Information: Inositol, mg Choline, mg Vitamin C,mg Biotin, mcg Pantothenic Acid,mg Folic Acid,mcg Niacin, mg Vitamin B Vitamin B Riboflavin, mg Thiamin, mg Vitamin K,mcg Vitamin E,IU(mg Vitamin D, IU(mcg) Vitamin A,IU(mcgRE) Vitamins ARA,mg DHA,mg a LinoleicAcid,mg Polyunsaturated, g Monounsaturated, g Saturated, g Fat, g Carbohydrate, g Protein, g Calories Nutrients *Standard Dilution =30kcal/fl oz - Linoleic Acid,mg 12 6 , mg , mcg a - 508(12.7) TE) Per 100g 1748(525) 12700 1270 182 153 180 140 116 116 699 100 11.8 (7.9) 84.0 13.9 55.9 16.6 22.3 25.5 67.7 15.3 0.70 1.4 2.8 4.9 0.70 0.89 7.2 Per 100kcal* 250(75.1) 1817 21.9 25.8 12.0 20.0 72.7 (1.8) 16.6 16.6 0.10 0.20 1.7 (1.1) 2.0 0.40 0.70 0.10 0.13 8.0 2.4 3.2 3.6 9.7 1.0 2.2 Taurine, mg L-Carnitine, mg Chloride, mg(mEq) Potassium, mg(mEq) Sodium, mg(mEq) Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals 287(12.5)41.0(1.8) Per 100g 440 (12.6)62.9(1.8) 900 (23.1) 124 760 510 760 48.0 48.0 18.9 26.2 31.3 10.9 95.0 0.57 7.4 Per 100kcal* 129(3.3) 109 109 17.7 13.6 73.0 4.6 4.6 2.7 3.7 4.5 0.08 1.1 1.6

(DHA) **A SourceofDocosahexaenoic Acid *A SourceofArachidonic Acid(ARA) Milk,SoyContains: Cyanocobalamin. Sodium Selenite,D-Biotin,VitaminD Sodium Molybdate,Phylloquinone, Tocopherols, ChromiumChloride, Folic Acid,Ascorbyl Palmitate, Mixed Vitamin AAcetate,Potassium Iodide, Pyridoxine Hydrochloride, Riboflavin, Thiamin ChlorideHydrochloride, Cupric Sulfate,Manganese Soy Lecithin, CalciumD-Pantothenate, alpha Tocopheryl Acetate,Niacinamide, Mono andDiglycerides, ZincSulfate,DL- L-Ascorbic Acid,L-Carnitine, Taurine, Sodium Chloride,Ascorbate, Ferrous Sulfate,SodiumCaseinate(Milk), Cohnii Oil**, L-Tryptophan, M-Inositol, Bitartrate, L-Cystine, M.AlpinaOil*, C. Dibasic, MagnesiumAcetate,Choline Potassium Chloride,CalciumPhosphate Tripotassium Citrate, CornSyrupSolids, Lactose (Milk),Tricalcium Phosphate, Sunflower), MilkProtein (Casein, Whey), Refined Vegetable Oils(Palm, Soy, Ingredients: 3 ,

141 KetoCal 3:1 Powder 3:1 KetoCal 142 NEUROLOGY • • • • • • • • • • • • • Main

No Nu Fat Carbohydrate energy requirements Osmolality (at1kcal/mL): 170mOsm/kg Displacement Energy distribution: Standard dilution=1kcal/mL Appropriate forenteral ororal feedings Nutrient denseforchildrenwithlow Contains sucralose Contains amulti-fiberblend DHA andARA Vanilla flavor 4:1 ratio Fiber Protein tritionally complete trans (LCT 100%) Fea fat tures:

A medicalfood. where theketogenic dietisindicated;designedforindividualsover 1year ofage. protein) forthedietarymanagementofintractable epilepsyandotherconditions A nutritionallycomplete,ketogenic formulaina4:1ratio (fat:carbohydrate + KetoCal 88.7% 3.1% 1 mL/g 1.5% 8.2%

® 4:1Powder For detailsonadministration, please seepages146-147. • • • • Indications: 101777 Code Product Ordering/Reimbursement Information:

office todetermine availability. WIC Other disorderswheretheketogenic dietisindicated Glucose transporter type-1deficiency (GLUT1) Pyruvate dehydrogenase deficiency(PDH) Intractable epilepsy ‡ : Contactyour stateWIC 49735-0166-70 Reimbursement B4154 Code Packaging HCPCS information seepage 195. information For morereimbursement 6 x300g(11oz) Product 2103 Per Calories Can

Nutrition Information: Inositol, mg Choline, mg Vitamin C,mg Biotin, mg Pantothenic Acid,mg Folic Acid,mcg Niacin, mg Vitamin B Vitamin B Riboflavin, mg Thiamin, mg Vitamin K,mcg Vitamin E,IU(mg Vitamin D Vitamin A,IU(mcgRE) Vitamins ARA,mg DHA,mg a LinoleicAcid,mg Polyunsaturated, g Monounsaturated, g Saturated, g Fat, g Insoluble,g Soluble,g Fiber, g Carbohydrate, g Protein, g Calories Nutri -Linolenic Acid,mg ents

12 6 3 , mg , IU(mcg) , mcg a -TE) 420(10.5) 1232(370) Per 100g 16200 1700 320 116 120 110 705 100 15.9 (10.7) 19.1 40.0 31.0 19.7 22.8 26.7 69.2 14.4 0.70 1.3 0.0191 2.9 4.9 0.70 0.89 2.1 3.2 5.3 8.2 Per 100kcal 2300 175(52.5) 241 59.6 (1.5) 45.5 16.5 17.0 15.6 0.10 2.3 (1.5) 0.18 2.7 5.7 0.0027 0.41 0.70 0.10 0.13 4.4 2.8 3.2 3.8 9.8 0.30 0.45 0.75 1.2 2.0 Fiber isnotincludedincalculatingtheketogenic ratio * StandardDilution=1kcal/mL Taurine, mg L-Carnitine, mg Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals Per 100g 726 771 481 500 420 700 33.0 45.0 27.0 14.8 28.7 86.2 96.3 0.83 3.6 7.0 Per 100kcal 103 109 68.2 12.2 71.0 13.7 59.6 99.3 4.7 6.4 3.8 2.1 4.1 0.12 0.51 0.99

§ Containssucralose 14.2 mg/100mL (DHA) ** AsourceofDocosahexaenoic Acid * AsourceofArachidonic Acid(ARA) Milk,SoyContains: Cyanocobalamin. Phylloquinone, D-Biotin,Cholecalciferol, Chromium Chloride,SodiumSelenite, Potassium Iodide,Sodium Molybdate, Palmitate, Mixed Tocopherols, Folic Acid, Riboflavin, VitaminAAcetate,Ascorbyl Hydrochloride, Pyridoxine Hydrochloride, Sulfate, CupricThiamineChloride Calcium D-Pantothenate, Manganese L-Histidine, ZincSulfate,Niacinamide, Acetate, Sucralose§,M-Inositol, Diglycerides, DL-alpha Tocopheryl Taurine, Ferrous Sulfate,Mono-and Acid, L-Valine, L-Tyrosine, L-Carnitine, L-Phenylalanine, Maltodextrin, L-Ascorbic Caseinate (Milk),SodiumAscorbate, L-Tryptophan, MagnesiumOxide,Sodium Alpina Oil*, C.CohniiOil**, Soy Fiber, L-Cystine, CholineBitartrate, M. Artificial Flavor (Vanilla), L-Arginine, Tribasic, HighAmylose CornStarch, Sodium Chloride,CalciumPhosphate Tripotassium Citrate, Potassium Chloride, (FOS), SiliconDioxide, GumArabic, Syrup Solids,Fructooligosaccharide Root Inulin,CalciumCarbonate,Corn Microcrystalline Cellulose,Chicory (Milk), Soy Lecithin, Whey (Milk), High OleicSunflower),Casein Refined Vegetable Oils(Palm, Soy, Ingredients:

143 KetoCal 4:1 Powder 4:1 KetoCal 144 NEUROLOGY • • • • • • • • • • • • • • Main No Fat Fiber Carbohydrate Unflavored Vanilla low energyrequirements Density Free water Energy distribution: Osmolality (at1.5kcal/mL): Nutrient denseforchildrenwith Contains sucralose Appropriate forenteral ororal feedings DHA andARA Contains amulti-fiberblend Great vanillaflavor orunflavored Convenient ready-to-feedliquid 4:1 ratio Nutritionally complete Protein trans (LCT 100%) Fea fat tures:

280 mOsm/kg 260 mOsm/kg 1 year ofage. Amedicalfood. other conditionswheretheketogenic dietisindicated;designedfor individuals over (fat:carbohydrate +protein)forthedietarymanagementofintractable epilepsyand A nutritionallycomplete,ready-to-feedketogenic formulain a4:1ratio KetoCal 88.7% 1.5% 3.1% 1.01g/mL 77.8% 8.2%

® 4:1LQ For detailsonadministration, please seepages146-147. • • • • Indications: 80183 –Unflavored 80180 –Vanilla Code Product Ordering/Reimbursement Information:

office todetermine availability. WIC Other disorderswheretheketogenic dietisindicated Glucose transporter type-1deficiency (GLUT1) Pyruvate dehydrogenase deficiency(PDH) Intractable epilepsy ‡ : Contactyour stateWIC 49735-0130-54 49735-0187-96 Code Reimbursement B4154 B4154 Code HCPCS information seepage195. information For morereimbursement (8 floz) 27 x237mL (8 floz) 27 x237mL Packaging Product 356 356 Per Box Calories

Taurine, mg L-Carnitine, mg Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals, Trace Elements Fiber isnotincluded incalculatingtheketogenic ratio. (mEq) (mEq) (mEq) 103(4.5) 155(4.4) 165 (4.2) 120 100 mL 18.5 22.7 88.4 88.4 Per 6.3 8.3 7.1 3.2 6.2 0.18 1.2 1.5 Per DrinkBox 244(10.6) 391(10.02) (237 mL) 367 (10.4) 284 210 210 14.9 19.7 16.8 14.7 43.8 53.8 7.6 0.43 2.8 3.6

(DHA) ** ASource of Docosahexaenoic Acid * ASourceofArachidonic Acid(ARA) Choline Chloride. Sweetener: Sucralose, SodiumHydroxide, Artificial Flavor, Sugar, Artificial Vanilla Unflavored Milk,SoyContains: Vitamin D Molybdate, Phylloquinone, D-Biotin, Chloride, SodiumSelenite, Folic Acid,Potassium Iodide,Chromium Tocopherols, DL-Alpha Tocopherol, Riboflavin, VitaminAAcetate,Mixed Hydrochloride, Pyridoxine Hydrochloride, Cupric Sulfate,ThiaminChloride Manganese Sulfate,Ascorbyl Palmitate, Niacinamide, CalciumD-Pantothenate, Tocopheryl Acetate,Soy Lecithin, L-Tryptophan, ZincSulfate,DL-Alpha Lactate, L-Carnitine, Taurine, M-Inositol, Propylene Glycol Alginate,Ferrous L-Cystine, CalciumPhosphateDibasic, Sodium Hydroxide, CholineChloride, and Diglycerides, Trisodium Citrate, Calcium PhosphateMonobasic,Mono Fructooligosaccharide ,L-Ascorbic Acid, C. CohniiOil**, MicrocrystallineCellulose, Magnesium Acetate,Potassium Chloride, Arabic, CalciumChloride,M.AlpinaOil*, Emulsifier), DipotassiumPhosphate,Gum Soy Fiber, CornStarch,Inulin,CAEM(an (Milk), Whey ProteinConcentrate (Milk), Sunflower, Soy, Palm), SodiumCaseinate Water, Refined Vegetable Oil(HighOleic Ingredients: flavored version alsocontains: 3 , Cyanocobalamin. version alsocontains:Sugar.

145 KetoCal 4:1 LQ 4:1 KetoCal 146 NEUROLOGY • • • • • • Directions forUse: 4. 3. 2. 1. KetoCal 3:1and4:1Powders For oral andtubefeeding: Directions forPreparation: KetoCal

24 hours. promptly at 39°F/4°C orlessand use within formula is open,useimmediately orrefrigerate 39°F-77°F (4°C-25°C). between eachfeed. lukewarm water(approximately 98°For37°C) should bediscarded. for upto4hours,atwhichtimeunusedformula formula canbesafelykept atroomtemperature Tube feedinghangtime consumed immediately. refrigerator andkept nolongerthan24hours. the water. be atatemperature of113-122°F(45-50°C). completely dissolve thepowder, thewatermust into acontainerthatsealswithscrewtoplid.To Once powderedformula ispreparedorliquid Do notfreeze.Recommended storage between Do notboilormicrowave formula. It isrecommendedthatthetubeflushed with For oral feeding,bestserved chilledand Once prepared,theformulashouldbestoredina Cover andshake untilthepowderhasdissolved. Add theprescribedamountofKetoCal to Measure therequiredamountofwarmwater ® Family : Nutriciarecommends

place (notinarefrigerator). Usewithin one month. opened, replacecontainer lidandstoreinacool,dry KetoCal 3:1and4:1Powders: from sunlight. Store unopenedproductinacool,dryplace andaway Storage: A gram scaleisnecessaryforproperpreparation offormula. Dilution tobedeterminedby medicalprescription: KetoCal 3:1Powder A gram scaleisnecessaryforproperpreparation offormula. Dilution tobedeterminedby medicalprescription: KetoCal 4:1Powder Mixing Guide: 45 kcal/fl oz 30 kcal/fl oz 24 kcal/fl oz 20 kcal/fl oz Dilution 45 kcal/fl oz 30 kcal/fl oz 24 kcal/fl oz 20 kcal/fl oz Dilution Powder Powder 21.4 g 14.3 g 11.4 g 21.3 g 14.2 g 11.4 g 9.5 g 9.5 g Water Water 79 mL 86 mL 89 mL 90 mL 79 mL 86 mL 88 mL 91 mL Final Volume Final Volume 100 mL 100 mL 100 mL 100 mL 100 mL 100 mL 100 mL 100 mL Once canhasbeen 240 mOsm/kg 150 mOsm/kg 120 mOsm/kg 100 mOsm/kg 260 mOsm/kg 170 mOsm/kg 130 mOsm/kg 110 mOsm/kg Osmolality Osmolality

• • • Caution: *Number ofcansandcasespermonthareroundedupto thenearestwholenumber Volume andOrderingGuide

condition ofthepatient. USE ONLY UNDERSTRICTMEDICALSUPERVISION.NOT FORPARENTERAL USE. Intake andmedical tobedeterminedbyweight, amedical professionalandisdependentonthe age,body Monitor forhypoglycemia, renalstones,hyperlipidemia, and adequategrowth. Calories/day 2000 1900 1800 1700 1600 1500 1400 1300 1200 1100 1000 900 800 700 600 Calories/mo 60000 57000 54000 51000 48000 45000 42000 39000 36000 33000 30000 27000 24000 21000 18000 Cans/mo 29 5 28 5 26 5 25 5 23 4 22 4 20 4 19 4 18 3 16 3 15 3 13 3 12 2 10 2 9 2 KetoCal 4:1 Powder Cases/mo . Cans/mo 29 5 28 5 26 5 25 5 23 4 22 4 21 4 19 4 18 3 16 3 15 3 13 3 12 2 11 2 9 2 KetoCal 3:1 Powder Cases/mo

Drink Boxes/mo (Vanilla orUnflavored) 169 161 152 144 135 127 118 110 102 93 85 76 68 59 51 KetoCal 4:1LQ Cases/mo

7 6 6 6 5 5 5 5 4 4 4 3 3 3 2

147 Use for Directions KetoCal 148 NEUROLOGY SPECIALIZED ADULT NUTRITION

Find more information and resources on these and all of our products at www.NutriciaLearningCenter.com 149 Pro-Stat Sugar Free

® Nutrition Information: Administration: Precautions: Pro-Stat Sugar Free Nutrients Per 30 mL (2 Tbsp) • Use under medical supervision • Do not add Pro-Stat to an Calories 100 • Healthcare professionals should open or closed system of the A sugar free, ready-to-drink liquid protein medical food providing 15 g Protein, g 15 tube feeding formula or into a determine intake based on of enzyme-hydrolyzed complete protein and 100 calories per 1 fl oz. Fat, g 0 container of enteral feeding. Carbohydrate, g 10 condition, estimated need, and dietary intake. • Do not add medications to Minerals Pro-Stat, even after dilution. Sodium, mg 50 • Administer orally or through Main Features: Indications: Potassium, mg 20 feeding tube. • Not suitable for use as a sole Phosphorus, mg 50 source of nutrition. • Clinically supported in 3 published trials • Increased protein needs in low volume related to: Suggested Intake: • Managing wounds (1 study)1 • Not for parenteral use. • Stage 1 & 2 pressure injuries • 1-3 servings per day. • Improving anabolism (1 study)2 • Wounds (diabetic, venous, surgical, burns) One serving = 1 fl oz. • Preserving lean body mass (1 study)3 Storage: • Unintentional muscle loss Ingredients: • Nutrient dense, providing 15 g of • Protein-Energy Malnutrition Oral Feeding: • Store at room temperature. Hydrolyzed Collagen Protein, Water, protein and 100 calories per 1 fl oz • Low serum proteins • Refrigeration causes gelling. • Hydrolyzed for rapid absorption & Glycerin, Malic Acid. Contains 2% or less: • Shake well before opening. Can • Sarcopenia Potassium Sorbate (to help protect flavor), • Discard 3 months after opening. efficient utilization4 Sodium Benzoate (to help protect flavor), be taken straight or mixed with • High in conditionally indispensable Sucralose, L-Tryptophan, Phosphoric Acid. any hot or cold beverages or food. • Record date opened on bottom amino acids needed for recovery5-10 Ordering/Reimbursement Information: Wild Cherry Punch flavored version of of container. • Sugar free Product Reimbursement HCPCS Product Calories this product contains 2% or less of each of Tube Feeding: • Do not use if seal is broken. the following: Natural flavors. • Nectar-like viscosity Code Code Code Packaging Per Unit 1. Flush feeding tube with • Lactose free, gluten free, and soy free 10064 – Wild Cherry Punch (bottle) 26974-0410-07 B4155 6 x 30 fl oz 3000 Citrus Splash, Grape and Vanilla flavored 30-60 mL of water. 30064 - Citrus Splash (bottle) 26974-0300-64 B4155 6 x 30 fl oz 3000 versions of this product contains 2% or • Kosher less of each of the following: Natural and 2. Pour 30 mL of Pro-Stat in a • Available in 4 great tasting flavors 40064 - Vanilla (bottle) 26974-0410-40 B4155 6 x 30 fl oz 3000 Artificial flavors. 50064 - Grape (bottle) 26974-0410-50 B4155 6 x 30 fl oz 3000 4-6 fl oz container. • Available in bottles (6/case) or unit 10464-U - Wild Cherry Punch (unit) 26974-0410-17 B4155 96 x 1 fl oz 100 3. Add 30-60 mL water and mix well doses (96/case) 30464-U - Citrus Splash (unit) 26974-0410-64 B4155 96 x 1 fl oz 100 with disposable spoon or tongue • For oral and enteral use 40464-U - Vanilla (unit) 26974-0410-42 B4155 96 x 1 fl oz 100 blade. Specialized Adult Nutrition 50464-U - Grape (unit) 26974-0410-52 B4155 96 x 1 fl oz 100 4. Administer Pro-Stat via syringe. 1. Lee SK, et al. Adv Skin Wound Care. 2006;19:92-6. 2. Sundell MB, et al. J Ren Nutr. 2009;19:412-21. 3. Hays NP, et al. J Am Diet Assoc. 2009;109:1082-7. 5. Flush with 30-60 mL of water. 4. Koopman R, et al. Am J Clin Nutr. 2009;90:106-15. 5. Morris Jr, SM. Annu Rev Nutr. 1992;12:81-101. 6. Curis E, et al. Amino Acids. 2005;29:177-205. 7. 150 Wu G, et al. Biochem J. 1992;281:45-8. 8. Schwedhelm E, et al. Br J Clin Pharmacol. 2008;65:51-9. 9. Waugh WH, et al. Am J Hematol. 1999;61:216. 151 10. Waugh WH, et al. J Natl Med Assoc. 2001;93:363-71. Pro-Stat Sugar Free AWC

Pro-Stat® Sugar Free AWC (Advanced Wound Care) Nutrition Information: Administration: Precautions: Nutrients Per 30 mL (2 Tbsp) • Use under medical supervision • Do not add Pro-Stat to an Calories 100 A sugar free ready-to-drink liquid protein medical food providing 17 g of enzyme- • Healthcare professionals should open or closed system of the Protein, g 17 tube feeding formula or into a hydrolyzed complete protein and 100 calories per 1 fl oz, with added arginine, citrulline, determine intake based on L-Arginine, g 3.3 container of enteral feeding. cystine, vitamin C and zinc. Fat, g 0 condition, estimated need, and • Do not add medications to Carbohydrate, g 7 dietary intake. Pro-Stat, even after dilution. Vitamins • Administer orally or through Vitamin C, mg 175 feeding tube. • Not suitable for use as a sole Main Features: Indications: Minerals source of nutrition. • Clinically shown in one study to promote • Increased protein needs in low volume related to: Zinc, mg 10 Suggested Intake: • Not for parenteral use. 1 pressure injury and wound healing • Stage 3 & 4 pressure injuries Sodium, mg 50 • 1-3 servings per day. Potassium, mg 20 • Nutrient dense, providing 17 g of protein • Multiple pressure injuries One serving = 1 fl oz. Storage: (Advanced Wound Care) Phosphorus, mg 50 and 100 calories per 1 fl oz • Hard to heal wounds (diabetic, venous, surgical, burns) Oral Feeding: • Store at room temperature. • Unintentional muscle loss • Contains added arginine, citrulline, • Shake well before opening. Can be • Refrigeration causes gelling. cystine, vitamin C and zinc • Protein-Energy Malnutrition Ingredients: • Low serum proteins taken straight or mixed with any • Discard 3 months after opening. • Hydrolyzed for rapid absorption & Hydrolyzed Collagen Protein, Water, hot or cold beverages or food. efficient utilization2 • Sarcopenia Glycerin, Malic Acid, L-Arginine. Contains • Record date opened on bottom 2% or less: L-Citrulline, L-Tryptophan, of container. • High in conditionally indispensable amino L-Cysteine HCL, Phosphoric Acid, Ascorbic Tube Feeding: 3-8 • Do not use if seal is broken. acids needed for recovery Ordering/Reimbursement Information: Acid, Potassium Sorbate (to help protect flavor), Sodium Benzoate (to help protect 1. Flush feeding tube with 30-60 mL • Sugar free Product Reimbursement HCPCS Product Calories flavor), Sucralose, Zinc Sulfate. of water. Code Code Code Packaging Per Unit • Honey-like viscosity Wild Cherry Punch flavored version of this 2. Pour 30 mL of Pro-Stat in a 4-6 40130 - Wild Cherry Punch (bottle) 26974-0410-30 B4155 4 x 30 fl oz 3000 • Lactose free, gluten free, and soy free product contains 2% or less of each of the fl oz container. 40230 - Citrus Splash (bottle) 26974-0410-23 B4155 4 x 30 fl oz 3000 following: Natural flavors. 3. Add 30-60 mL water and mix • Kosher 40130-U - Wild Cherry Punch (unit) 26974-0410-31 B4155 96 x 1 fl oz 100 Citrus Splash flavored version of this • Available in 2 great tasting flavors 40230-U - Citrus Splash (unit) 26974-0410-24 B4155 96 x 1 fl oz 100 product contains 2% or less of each of the well with disposable spoon or following: Natural and Artificial Flavors. tongue blade. Specialized Adult Nutrition • Available in bottles (6/case) or unit doses 1. Lee SK, et al. Adv Skin Wound Care. 2006;19:92-6. 2. Koopman R, et al. Am J Clin 4. Administer Pro-Stat via syringe. (96/case) Nutr. 2009;90:106-15. 3. Morris Jr, SM. Annu Rev Nutr. 1992;12:81-101. 4. Curis E, et al. Amino Acids. 2005;29:177-205. 5. Wu G, et al. Biochem J. 1992;281:45-8. 5. Flush with 30-60 mL of water. • For oral and enteral use 6. Schwedhelm E, et al. Br J Clin Pharmacol. 2008;65:51-9. 7. Waugh WH, et al. Am J 152 Hematol. 1999;61:216. 8. Waugh WH, et al. J Natl Med Assoc. 2001;93:363-71. 153 Pro-Stat MAX

Nutrition Information: Administration: Precautions: ® Nutrients Per 30 mL (2 Tbsp) • Use under medical supervision. • Do not add Pro-Stat to an Pro-Stat MAX Calories 80 • Healthcare professionals should open or closed system of the Protein, g 11 determine intake based on tube feeding formula or into a A sugar free, hydrolyzed whey-based liquid protein medical food. 100% PDCAAS* protein Fat, g 0 condition, estimated need, and container of enteral feeding. and 80 calories in 1 fl oz. Carbohydrate, g 9 dietary intake. • Do not add medications to Minerals Pro-Stat, even after dilution. Sodium, mg 35 • Administer orally or through • Not suitable for use as a sole Main Features: Indications: Potassium, mg 40 feeding tube. Phosphorus, mg 60 source of nutrition. • Nutrient dense, providing 11 g of • Increased protein needs in low volume related to: Suggested Intake: Calcium, mg 60 • Not for parenteral use. 100%-PDCAAS* protein and 80 calories in • Pressure injuries • 1-3 servings per day. 1 One serving = 1 fl oz. 1 fl oz to help meet high protein demands • Wounds (diabetic, venous, surgical, burns) Storage: • Whey-based hydrolyzed complete protein • Critical illness** Oral Feeding: • Store at room temperature. • Unintentional muscle loss Ingredients: • Optimal amount of all 9 indispensable • Shake well before opening. Can • Refrigeration causes gelling. • Protein-Energy Malnutrition be taken straight or mixed with amino acids needed for efficient Water, Glycerin, Hydrolyzed Whey • Discard 3 months after opening. protein synthesis2-6 • Low serum proteins Protein, Hydrolyzed Collagen Protein, any hot or cold beverages or food. • Sarcopenia Malic Acid. Contains 2% or less: • Record date opened on bottom • Sugar free Natural & Artificial Flavor, Phosphoric Tube Feeding: • Pre- and post-surgery Acid, L-Phenylalanine, L-Histidine, of container. • Nectar-like viscosity • Cancer L-Tryptophan, L-Methionine, Sucralose, 1. Flush feeding tube with 30-60 mL • Do not use if seal is broken. • Gluten free and soy free Potassium Sorbate (to help protect of water. flavor), Sodium Benzoate (to help protect • Available in great tasting grape flavor Ordering/Reimbursement Information: flavor). 2. Shake well before opening unit dose or bottle. • Available in bottles (4/case) and unit doses Product Reimbursement HCPCS Product Calories Contains milk (whey). (96/case) Code Code Code Packaging Per Unit 3. Pour 30 mL of Pro-Stat MAX • For oral and enteral use 90001 - Grape (bottle) 26974-0900-01 B4155 4 x 30 fl oz 2400 in a 4-6 fl oz container. 90001-U - Grape (unit) 26974-1900-01 B4155 96 x 1 fl oz 80 4. Add 30-60 mL water and mix well with disposable spoon or tongue * PDCAAS = Protein Digestibility Corrected Amino Acid Score. Specialized Adult Nutrition blade. The Food and Agriculture Organization (FAO), World Health Organization (WHO), Institute of Medicine (IOM) and Food and Drug Administration (FDA) use this method for evaluating protein quality. PDCAAS rates the utilization and digestibility of protein. 5. Administer Pro-Stat MAX via ** ICU stay for >2-3 days. 1. McClave SA, et al. J Parenter Enteral Nutr. 2009;33:277-316. 2. Pennings B, et al. Am J Clin Nutr. 2011;93:997-1005. 3. Katsanos CS, et al. Nutr Res. syringe. 2008;28:651-8. 4. FAO/WHO Expert Consultation. FAO Food and Nutrition Paper. 1991;51. 5. Institute of Medicine of the National Academies. Dietary 154 Reference Intakes for Energy, Carbohydrates, Fiber, Fat, Fatty Acids, Cholesterol, Protein, and Amino Acids (Macronutrients). 2005: 737. 6. Castellanos VH, et 6. Flush with 30-60 mL of water. 155 al. Nutr in Clin Prac. 2006;21:485-504. Pro-Stat Renal Care

Nutrition Information: Administration: Precautions: ® Nutrients Per 30 mL (2 Tbsp) • Use under medical supervision. • Do not add Pro-Stat to an Pro-Stat Renal Care Calories 100 • Healthcare professionals should open or closed system of the Protein, g 15 A sugar free, ready-to-drink liquid protein medical food providing 15 g of enzyme-hydrolyzed determine intake based on tube feeding formula or into a Fat, g 0 container of enteral feeding. complete protein, 3 g of prebiotic fiber and 100 calories per 1 fl oz. Carbohydrate, g 6 condition, estimated need, and • Do not add medications to Fiber, g 3 dietary intake. Pro-Stat, even after dilution. Minerals • Administer orally or through Sodium, mg 50 feeding tube. • Not suitable for use as a sole Main Features: Indications: Potassium, mg 20 source of nutrition. Suggested Intake: • Clinically shown in one study to improve • Increased protein needs in low volume related to: Phosphorus, mg 50 • Not for parenteral use. • 1-3 servings per day. protein anabolism in hemodialysis patients1 • Pressure injuries One serving = 1 fl oz. • 15 g of complete protein and 3 g • Wounds (diabetic, venous, surgical, burns) Storage: of prebiotic soluble fiber in 1 fl oz • Dialysis Oral Feeding: • Store at room temperature. Ingredients: • Hydrolyzed for rapid absorption and • Unintentional muscle loss • Shake well before opening. Can • Refrigeration causes gelling. efficient utilization2 • Protein-Energy Malnutrition Hydrolyzed Collagen Protein, Water, Glycerin, Polydextrose, Fructo- be taken straight or mixed with • Discard 3 months after opening. • High in conditionally indispensable amino • Low serum proteins Oligosaccharides (FOS), Malic Acid. any hot or cold beverages or food. • Record date opened on bottom acids needed for recovery3-8 Contains 2% or Less: Natural & Artificial • Sarcopenia of container. • Low volume making it appropriate for Flavor, Phosphoric Acid, L-Tryptophan, Tube Feeding: • Fluid Restricted Sucralose, Potassium Sorbate (to help • Do not use if seal is broken. fluid restricted • Inadequate protein & fiber intake protect flavor), Sodium Benzoate (to help 1. Flush feeding tube with 30-60 mL • Sugar free protect flavor). of water. • Honey-like viscosity 2. Pour 30 mL of Pro-Stat in a 4-6 fl • Lactose free, gluten free, and soy free Ordering/Reimbursement Information: oz container. • Kosher Product Reimbursement HCPCS Product Calories 3. Add 30-60 mL water and mix well Code Code Code Packaging Per Unit • Available in great tasting tangerine flavor with disposable spoon or tongue 60064 - Tangerine (bottle) 26974-0410-64 B4155 6 x 30 fl oz 3000 • Available in bottles (6/case) or unit doses blade. 60064-U - Tangerine (unit) 26974-0420-65 B4155 96 x 1 fl oz 100 Specialized Adult Nutrition (96/case) 4. Administer Pro-Stat via syringe. • For oral and enteral use 5. Flush with 30-60 mL of water. 1. Sundell MB, et al. J Ren Nutr. 2009;19:412-21. 2. Koopman R, et al. Am J Clin Nutr. 2009;90:106-15. 3. Morris Jr, SM. Annu Rev Nutr. 1992;12:81-101. 156 4. Curis E, et al. Amino Acids. 2005;29:177-205. 5. Wu G, et al. Biochem J. 1992;281:45-8. 6. Schwedhelm E, et al. Br J Clin Pharmacol. 2008;65:51-9. 7. Waugh 157 WH, et al. Am J Hematol. 1999;61:216. 8. Waugh WH, et al. J Natl Med Assoc. 2001;93:363-71. UTI-Stat

Nutrition Information: Administration: Storage: UTI-Stat® Nutrients Per 30 mL (2 Tbsp) • Use under medical supervision. • Store at room temperature. Calories 70* • Refrigeration not necessary. Sugar, g 1 • Administer orally or through A ready-to-drink medical food providing cranberry concentrate with added ingredients Minerals feeding tube. • Discard 3 months after opening. (vitamin C, D-Mannose, fructo-oligosaccharides (FOS), and bromelain) in a 1 fl oz serving Sodium, mg 15 Suggested Intake: • Record date opened on bottom for urinary tract health. Potassium, mg 20 • 1-2 servings per day as needed. of container. Phosphorus, mg 0 One serving = 1 fl oz. • Do not use if seal is broken. Proprietary Blend (Cranberry Concentrate, Ascorbic Acid, D-Mannose, FOS, Bromelain) Oral Feeding: Main Features: Indications: • Clinically shown in two studies to manage • Management of urinary tract infections *Glycerin provides a source of calories • Can be taken straight or mixed 1-2 with any hot or cold beverage. urinary tract infections • Urinary tract health • Low in sugar (1 g sugar per serving) Ingredients: Tube Feeding: • Thin viscosity Water, Glycerin, Proprietary Blend 1. Flush feeding tube with 30-60 • Lactose free, gluten free, and soy free Ordering/Reimbursement Information: (Cranberry Concentrate, Ascorbic Acid, mL water. D-Mannose, Fructo-oligosaccharides 2. Measure and administer dose • Kosher Product Reimbursement HCPCS Product Calories (FOS), Bromelain). Contains 2 % or less: Code Code Code Packaging Per Unit Sucralose, Acesulfame-K, Potassium prescribed. • Available in cranberry flavor Sorbate (to preserve flavor), Sodium 60001 - Cranberry (bottle) 26974-0410-66 B4104 4 x 30 fl oz 2100 3. Administer UTI-Stat straight • Available in bottles (4/case) or unit doses Benzoate (to preserve flavor), Phosphoric into the enteral tube. (96/case) 60001-U - Cranberry (unit) 26974-0410-67 B4104 96 x 1 fl oz 70 Acid. 4. Flush the tube with additional • For oral and enteral use 30 mL water. Precautions: • Not a substitute for antibiotics. • This product is not intended for use as an analgesic.

Specialized Adult Nutrition • Not suitable for use as a sole 1. Posthauer ME. The Director. 2008;16:13-6. 2. Efros M, et al. Urology. 2010;76:841-5. source of nutrition. • Not for parenteral use. 158 159 Diff-Stat

BLISTER PACKS Suggested Use: ** For residents/patients with a Supplement Facts: CVC, open Diff-Stat capsule COMING SOON • Take two capsules or one powder Serving Size: 2 Capsules or powder pack in a separate ® Diff-Stat Amount Per Serving Per 2 Capsules pack once daily. room. Probiotics could be Calories 5 Directions for Oral aerosolized or inadvertently A dietary supplement providing a blend of probiotics and a prebiotic that helps to Carbohydrate, g <1 introduced into a CVC line when Dietary Fiber, g <1 Consumption: promote intestinal health.† the pack is opened, presenting a Proprietary blend, mg 942 FOS (Fructo-oligosaccharides) • Consume 2 capsules with fluid contamination risk. Saccharomyces boulardii, or break open capsule and Bacillus coagulans Precautions: Main Features: Helps Promote: consume.* • Dissolve powder pack in 30 mL • Probiotics and a prebiotic working to • Intestinal health† Supplement Facts: • Diff-Stat should be taken 1 hour promote intestinal health† juice and consume.* before or 2 hours after antifungal Serving Size: 1 Powder Pack (2 g) medication. • Saccharomyces boulardii Amount Per Serving Per Powder Pack Directions for Diff-Stat Through • Do not use in case of Calories 5 a Feeding Tube:** • Bacillus coagulans Ordering/Reimbursement Information: yeast allergy. • Fructo-oligosaccharides Carbohydrate, g 1 Product Reimbursement Product Calories Sugar, g 0.5 1. Flush the tube with 30-60 ml Storage: • Available in a convenient capsule or an Code Code Packaging Per Unit Proprietary blend, mg 942 water. unflavored powder pack 80001 - Capsules (plain) 26974-0410-80 6 x 60 capsules 150 FOS (Fructo-oligosaccharides) 2. Mix contents of Diff-Stat with • Do not expose to excessive heat. 80001-U - Powder pack (Unflavored) 26974-0410-81 96 x 2 g 5 Saccharomyces boulardii, • No refrigeration required Bacillus coagulans 30 mL water and administer • Do not refrigerate. immediately straight into the • For oral and enteral use • Keep bottle tightly closed. Store enteral tube.* in a cool, dry place. Processing may impact level of colony 3. Flush the tube with additional † These statements have not been evaluated by the Food and Drug Administration. forming units (CFU). 30-60 mL water. This product is not intended to diagnose, treat, cure or prevent any disease. Other Ingredients: * Diff-Stat is only viable for Capsules: Gelatin, Natural & Artificial 30 minutes in solution. Flavors. Contains 2% or less: Rice Bran Extract, Rice Concentrate, Sucralose, † These statements have not been evaluat- Silicon Dioxide, and Ethyl Maltol. Specialized Adult Nutrition Contains milk. ed by the Food and Drug Administration. This product is not intended to diagnose, Powder Packs: Microcrystalline cellulose, treat, cure or prevent any disease. Maltodextrin, Silicon Dioxide. 160 161 Fiber-Stat

Nutrition Information: Administration: Precautions: ® Nutrients Per 30 mL (2 Tbsp) • Use under medical supervision. • Do not consume more than Fiber-Stat Calories 50* • Healthcare professionals should 60 mL (4 Tbsp) per day Carbohydrate, g 25 without healthcare provider A low volume liquid prebiotic fiber medical food for the dietary management of bowel Sugar, g 2.5 determine intake based on recommendation. regularity in persons unable to meet fiber requirements through a normal diet. Dietary Fiber, g 15 condition, estimated need, and Soluble Fiber, g 15 dietary intake. • Do not use if intestinal Minerals obstruction, fecal impaction or Sodium, mg 15 • Administer orally or through Potassium, mg 52 feeding tube. known allergy to any component Phosphorus, mg 25 is present. Indications: Suggested Intake: Main Features: * Glycerin & polydextrose provide a source • Not suitable for use as a sole • 15 grams of soluble prebiotic fiber • Constipation of calories • 1-2 servings per day. source of nutrition. One serving = 1 fl oz. (60% DV) in 1 fl oz • Bowel regularity • Not for parenteral use. • Contains fructo-oligosaccharides (FOS) • Low fiber intake Oral Feeding: and polydextrose to support Storage: • Colon health Ingredients: • Can be taken straight or mixed total gut health1- 2 Water, Polydextrose, Glycerin, Prune Juice with any hot or cold beverage. • Store and serve at room • Ready to drink or mix with any food or Concentrate, Fructo-oligosaccharides temperature. beverage (FOS). Contains 2% or less: Sodium Tube Feeding: Benzoate (to help protect flavor), • Refrigeration not necessary. • Thin viscosity Ordering/Reimbursement Information: 1. Flush feeding tube with Potassium Sorbate (to help protect flavor), • Discard 3 months after opening. Phosphoric Acid. 30-60 mL water. • Lactose free, soy free and gluten free Product Reimbursement HCPCS Product Calories Record date opened on bottom • Kosher Code Code Code Packaging Per Unit 2. Measure and administer the of container. 70001 - Prune (bottle) 26974-0410-70 B4104 6 x 30 fl oz 1500 prescribed dose via syringe. • Available in bottles (6/case) or unit doses 70400-U - Prune (unit) 26974-0410-71 B4104 96 x 1 fl oz 50 • Do not use if seal is broken. (96/case) 3. Administer Fiber-Stat straight into the enteral tube. • For oral and enteral use 4. Flush the tube with additional 30-60 mL water. Specialized Adult Nutrition

1. Losada MA, et al. Nutr Res. 2002;22:71-84. 2. Jie Z, et al. Am J Clin Nutr. 2000;72:1503-9.

162 163 Specialized Adult Nutrition

164 OTHER NUTRITIONALS

TM Find more information and resources on these and all of our products at www.NutriciaLearningCenter.com 165 166 OTHER NUTRITIONALS • Dilution • • • • • • Main Features: Displacement: 0.83mL/g 1.0 kcal/mL: 0.73 kcal/mL: Osmolality (mOsm/kg): minerals includingtrace elements Contains completeprofileofvitaminsand casein 61%,whey 39% Provides protein asacasein/whey mix; Contains DHAandARA 84% offatasMCT 26% ofcaloriesfromfat

289 mOsm/kg 235 mOsm/kg A medicalfoodforindividualsover 1year ofage. A milkprotein-basedpowder, lowinfat,andhighmediumchaintriglycerides(MCT). Monogen

® • • • • Indications: 106033 Code Product Ordering/Reimbursement Information: Chylothorax high MCTdietisindicated Other lipidandlymphaticdisorderswherealowfat, Hyperlipoproteinemia type1 Long chainfattyacidoxidation disorders office todetermine availability. WIC ‡ : Contactyour stateWIC 49735-0160-33 Code Reimbursement B4150 orB4158 Code HCPCS information seepage 195. information For morereimbursement 6 x400g(14.1oz) Packaging Product IMPROVED

1776 Per Can Calories

Nutrition Information: Folic Acid,mcg Niacin, mg Vitamin B Vitamin B Riboflavin, mg Thiamin, mg Vitamin K,mcg Vitamin E,IU(mg Vitamin D Vitamin A,IU(mcgRE) Vitamins Carbohydrate, g DHA,mg ARA,mg Linoleicacid,g LCT, g MCT, g Fat, g Protein Equivalent,g C Nutrients Contains: CoconutOil,Milk, WalnutContains: Oil D-Biotin, SodiumSelenite, VitaminD Acid, Potassium Iodide,ChromiumChloride,Sodium Molybdate,Phylloquinone, Hydrochloride, ThiaminChloride Hydrochloride, VitaminAAcetate,Riboflavin, Folic Tocopherol, CalciumD-Pantothenate, CopperSulfate, ManganeseSulfate,Pyridoxine Sulfate, ZincL-Carnitine, DL-Alpha Tocopheryl Acetate,Niacinamide, DL-Alpha L-Ascorbic Acid,L-Tryptophan, SodiumL-Ascorbate, Taurine, L-Isoleucine, Ferrous Hydrogen Phosphate,CholineChloride,M.AlpinaOil, C.CohniiOil,L-Valine, Inositol, Syrup Solids,SodiumCitrate, Potassium Chloride,CalciumCarbonate,Magnesium Oil [MediumChainTriglycerides]), Whey (Milk),CaseinateWalnut Oil,Corn Maltodextrin, SkimMilk,Refined Vegetable Oil(Modified Palm KernelAnd/Or Coconut Ingredients: alories, kcal

a -Linolenic acid,g

12 6 3 , mg , IU(mcg) , mcg a -TE) 428(10.7) 61.0 Per 100g 974(293) 444 16.1 69.1 60.0 60.0 10.8 12.9 12.9 6.6 (4.4) 0.17 2.7 0.44 0.41 0.90 2.10 0.60 0.40 219(66.0) Per 100kcal 100 13.7 96.4 (2.4) 15.6 13.5 13.5 3.6 2.4 2.9 2.9 1.5 (0.99) 0.04 0.61 0.10 0.09 0.2 0.5 0.14 0.14 0.09 3 . Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mg Zinc, mg Iron, mg Magnesium, mg Phosphorous, mg Calcium, mg Minerals Inositol, mg Choline, mg Vitamin C,mg Biotin, mcg Pantothenic Acid,mg Nutrients Per 100g 284 372 192 324 193 321 10.4 18.8 72.3 39.6 79.8 90.9 54.1 12.8 9.5 0.32 4.1 6.0 2.0 Per 100kcal 64.0 83.8 43.2 73.0 43.5 72.3 16.3 16.3 18.0 20.5 12.2 2.3 4.2 8.9 2.9 2.1 2.1 0.07 0.92 1.4 0.45 firmly after use. use contentswithinone month.Replacelid Store inacool,dryplace. Onceopened, Storage: • accuracy, useascale. Unpacked, level scoopsareapproximations only. For (1.0 kcal/mL) 30 kcal/30 mL (0.73 kcal/mL) 22 kcal/30 mL Concentration desired concentrations: The followingareguidelinesforachieving 3. 2. 1. For oral ortubefeeding: • • • Important Information: Administration:

Add theprescribedamountofMonogen Measure therequiredamountof Cover andshakeCover untilthepowderhas immediately beforeuse. preparation. Shake orstirMonogen longer than24hoursfromthetimeof be storedinarefrigerator andkept no Once prepared,theformulashould dissolved. can measures5.6g(level andunpacked). to thewater. Thescoopprovided inthe warmed waterintoacontainer. feeding inindividualsover 1year ofage. Not forparenteral use.For oral andtube acids isrecommended. Regular monitoringofessentialfatty the patient. andmedicalconditionof body weight professional andisdependentontheage, Intake isdeterminedby amedical

(4 Scoops) 22.8 g (3 Scoops) 16.8 g Powder (2 1/2 fl oz) 80 mL (3 floz) 90 mL Water

100 mL 100 mL Final Volume

167 Monogen 168 OTHER NUTRITIONALS • • • • • • • • • Main Features: Can beusedinbeverages andfoods For oral orenteral use Density: 0.97g/mL Osmolality: 10mOsm/kg High energy:4.5kcal/mL Unflavored 50% MCT/ 50%water Emulsified forbettermixing Simplifies additionofMCTs tothediet A medicalfood. acid oxidation disordersorconditionsmanagedby theketogenic diet. where MCTs arepartofdietarymanagement,suchaslong-chainfatty A highenergymedium-chaintriglyceride (MCT)emulsionforconditions Liquigen • Indications: 71957-3 (Unit) 71957 (Case) Code Product Ordering/Reimbursement Information: • • • • • Conditions whereMCTs arepartofdietarymanagement,suchas: office todetermine availability. WIC Short bowelsyndrome Fat malabsorption Chylothorax Long-chain fattyacidoxidation disorders Conditions managedby theketogenic diet ® ‡ : Contactyour stateWIC 49735-0195-73 49735-0119-57 Code Reimbursement B4155 B4155 Code HCPCS 4 x250mL(8.5floz) 3 x4250mL(8.5floz) Packaging Product information seepage195. information For morereimbursement 1125 1125 Per Bottle Calories

Nutrition Information: Diglycerides (Emulsifier),CitricAcid. and Diglycerides (Emulsifier),Monoand Oil)), Water, CitricAcidEstersofMono Triglycerides (Palm Kernel and/or Coconut Refined Vegetable Oil(MediumChain Ingredients: * Listedasfattyacids Chloride, mg Potassium, mg Sodium, mg Calcium, mg Minerals *LCT, g *MCT, g Saturated, g Fat, g Carbohydrate, g Protein, g Calories Nutrients Per 100mL None None 45.4 47.1 50 450 0.10 0.10 5.0 0.30 1.39 Per 250mL None None 114 118 125 1125 12.5 0.25 0.25 0.75 3.49 • • • Precautions: • • Administration: Not forparenteral use. source ofnutrition. Not suitableforuseasasole Use undermedicalsupervision. Shake wellbeforeuse. 5 years ofage. dilution forchildrenunder Liquigen may require condition ofthepatient. bodyweight andmedical and isdependentontheage, healthcare professionalonly should bedeterminedby a The quantityofLiquigen

• • • Storage: after use. Always replacethebottlelid 14 days. refrigerator andusewithin Once opened,storeina between 39°-77°F (4°-25°C). Recommended storage

169 Liquigen 170 OTHER NUTRITIONALS • • • • • • • • • Main Features: Displacement Fat Energy distribution: PRSL oflessthan0.017mOsm/g 0.93 mOsmwhenaddedtoasolution 1 gram contributesapproximately 310 mOsm/kg (1:3dilution): Osmolality Milk protein-free or texture offoodsandbeverages Super solublewithoutalteringthetaste of fatandcarbohydrate Unique dualenergysource provides 25kcal Calorically dense–1scoop(5g) Carbohydrate (MCT 35%/LCT 65% A powderedmedicalfoodproviding fatandcarbohydrate forincreasedcaloricintake. Duocal )

0.77 mL/g 59% 41%

• • • • • • • Indications: 118262 Code Product Ordering/Reimbursement Information: Suitable fororal andtubefeedings Catabolic states(e.g. burns, trauma, post-operative stress) Modular diets Malabsorptive states Disorders ofproteinandaminoacidmetabolism Protein restricteddiets is indicated Conditions whereahighenergy, lowfluid,electrolytesdiet office todetermine availability. WIC ‡ : Contactyour stateWIC 49735-0182-62 Code Reimbursement B4155 Code HCPCS 6 x400g(14.1oz) Packaging Product information seepage195. information For morereimbursement 1968 Per Can Calories

Nutrition Information: Phosphorus, mg Calcium, mg Chloride, mg Potassium, mg Sodium, mg Minerals Carbohydrate, g Polyunsaturated, g Monounsaturated, g Saturated, g Fat, g Protein, g Calories Nutrients of Monoglycerides. Diglycerides, DiacetylTartaric AcidEsters Coconut Oil,Palm Kernel Oil),Monoand Chain Triglycerides (Fractionated Vegetable Oils(Corn, Coconut),Medium Hydrolyzed Cornstarch,BlendofRefined Ingredients: Per 100g ≤ ≤ 492 ≤ ≤ 20.0 20.0 ≤ None 72.7 13.8 22.3 5.0 5.0 5.0 4.8 2.5

Per 10gsachet ≤ ≤ ≤ ≤ ≤ None 49.2 0.50 0.50 2.0 0.50 2.0 0.48 0.25 7.3 1.4 2.2 • • Precautions: For accuracy useagram scale. measurements areapproximations only. are level andunpacked. Household measurements. Allmeasurements Based onstandardUSdry, household 1 sachet 1 cup 1/2 cup 1/4 cup 1 Tbsp 1 tsp 1 Scoop Measure (all measuresareunpacked) Household Measures: source ofnutrition. Not suitableforuseasasole Not forparenteral use. 117 g Weight 10 g 56 g 30 g 8.5 g 2.6 g 5 g

Calories 576 276 148 49 42 13 25 • Storage: 3. 2. 1. For oral ortubefeeding: • Administration: one month. refrigerator) and usewithin in acool,dryplace(not in replace containerlid andstore temperature. Once opened, Store unopenedcanatroom serving. or stirimmediatelybefore and usedwithin24hours.Shake Duocal shouldberefrigerated powder hasdissolved. and stircontinuouslyuntilthe volume ofliquid and/or softfood of Duocal. the patient. weight andmedicalconditionof dependent ontheage,body medical is professionaland Intake tobedeterminedby a Unused foodsmixed with Add powdertotherequired Measure theprescribedamount

171 Duocal 172 OTHER NUTRITIONALS • • • • • • • • • Main Features: Displacement: 0.57 mL/g PRSL <0.01mOsm/10g 1.04 mOsmwhenaddedtoasolution 1 gram contributesapproximately 104 mOsm/kg Osmolality (10%solution): environment Manufactured inadairy-free of foodsanddrinks Neutral taste–doesnotalterthe Completely solubleinfoodsanddrinks Easily digestiblemaltodextrin approximately 5g(~20kcal) Calorically dense–1scoopprovides A powdered,concentrated sourceofenergy(maltodextrin). Amedicalfood. Polycal

™

• • Indications: 89461 Code Product Ordering/Reimbursement Information: inborn errorsofmetabolism. For thedietarymanagementof energyneedsinpatientswith indicated. Conditions whereahighenergy, lowfluidormodulardietis office todetermine availability. WIC ‡ : Contactyour stateWIC 49735-0111-52 Code Reimbursement B4155 Code HCPCS information seepage195. information For morereimbursement 12 x400g(14.1oz) Packaging Product 1536 Per Can Calories

Nutrition Information: Potassium, mg Sodium, mg Minerals Fat, g Protein, g Carbohydrate, g Calories 384 Nutrients Maltodextrin. Ingredients: Per 100g 96.0 2.0 0 0 0

• • Precautions: For accuracy useagram scale. measurements areapproximations only. are level andunpacked. Household measurements. Allmeasurements Based onstandardUSdry, household 1 cup ½ cup ⅓ ¼ cup 1 Tbsp 1 tsp ½ tsp 1 Scoop Measure (all measuresareunpacked) Household Measures: cup source ofnutrition. Not suitableforuseasasole Not forparenteral use. Weight 116 g 38.7 g 58.0 g 29.0 g 7.3 g 2.4 g 1.2 g 5 g 148 kcal 445 kcal 223 kcal 111 kcal ~20 kcal Calories

27.8 kcal 9.3 kcal 4.6 kcal use contentswithin 1 month. dry place(notinrefrigerator) and container lidandstoreinacool, dry place.Onceopened,replace Store unopenedcaninacool, Storage: • • • the patient. weight andmedicalconditionof dependent ontheage,body a medicalprofessionalandis Intake tobedeterminedby Administration: refrigerator forupto24hours. foods shouldbestoredina Unfinished beverages and stirring intohotorcoldfood. to formasmoothpastebefore powder withsufficientliquid Foods: For bestresults,mix into thebeverage andstirwell. required amountofpowder Beverages: Sprinklethe

173 Polycal 174 OTHER NUTRITIONALS • • • • • Main Features: Approximate displacement:0.75mL/g Osmolality (5%w/v): of proteinequivalentper5gpowder Complete AminoAcidMixprovides 4g enteral formulas Supplements increasedproteinneedsin non-essential aminoacids Balanced mixtureofessentialand 360 mOsm/kg A medicalfood. An unflavored, powderedmixture ofessentialandnon-essentialaminoacids. Complete AminoAcidMix

• • • • • • Indications: 553341 Code Product Ordering/Reimbursement Information: Short bowelsyndromefollowingintestinal resection Chronic intestinaldiseases(e.g. Crohn’s disease) Feeding difficultiesinpost-operative conditions Intractable malabsorption protein orotherwholeprotein) eosinphilic esophagitisorindividualswith intolerance to milk whereanoligoallergenicdietisindicated(e.g. Conditions suitable oramodularapproachisrequired Conditions inwhichanutritionallycompletefeedisnot office todetermine availability. WIC ‡ : Contactyour stateWIC 49735-0133-41 Reimbursement B4155 Code Packaging HCPCS information seepage195. information For morereimbursement 6 x200g(7oz) Product 656 Per Calories Can

Nutrition Information: L-Glutamine L-Valine L-Tyrosine L-Tryptophan L-Threonine L-Serine L-Proline L-Phenylalanine L-Methionine L-Lysine L-Leucine L-Isoleucine L-Histidine Glycine L-Glutamic Acid L-Cystine L-Aspartic Acid L-Arginine L-Alanine Amino Acids,g Carbohydrate, g Fat, g Protein Equivalent,g Calories 328 Nutrients 10.22 0.7 6.5 4.3 2.0 5.0 4.29 7.0 4.5 1.65 7.55 5.95 4.38 6.0 8.17 2.4 6.39 7.66 3.5 None None Per 100g 82 L-Glutamic Acid. L-Tryptophan, L-Methionine, L-Glutamine, L-Tyrosine, L-Alanine, L-Cystine, L-Phenylalanine, L-Histidine, L-Serine, Acid, Glycine, L-Isoleucine, L-Threonine, L-Arginine, L-Proline, L-Valine, L-Aspartic L-Lysine L-Glutamate, L-Leucine, Ingredients: • • • Precautions: a gram scale. are approximations only. For accuracy use and unpacked. Householdmeasurements measurements. Allmeasurementsarelevel Based onstandardUSdry, household 1 Tbsp 1/2 Tbsp 1 tsp 1/2 tsp Measure (all measuresareunpacked) Household Measures: source ofnutrition. Not suitable foruseasasole Not forparenteral use. of thepatient. weight andmedical condition dependent ontheage, body by adoctorordietitianandis Dosage shouldbedetermined Weight 9.5 g 4.4 g 2.9 g 1.4 g Protein Equivalent

7.79 3.61 2.38 1.15 • • Storage: • • • Administration: immediately beforeserving. time ofpreparation. Stir orshake longer than24hoursfromthe refrigerator andmustnot bekept feed shouldbestoredina reconstituted,theprepared Once after use. Always replacecontainerlid opened, usewithinonemonth. Store inacool,dryplace.Once applesauce. to soft,moistfoods,suchas Acid Mixmay alsobeadded other formulas.CompleteAmino mixed withwater, fruitjuicesor Best served as achilleddrink, that readsingrams. should beweighedonascale Complete AminoAcidMix 5 gpowderto100mLofwater). concentration is5%w/v (e.g. The recommendedfeeding

175 Complete Amino Acid Mix Acid Amino Complete 176 OTHER NUTRITIONALS • • • • Main Features: Approximate displacement:0.75mL/g Osmolality (5%w/v): 360mOsm/kg 5 gofpowder 4 gofproteinequivalentper Essential AminoAcidMixprovides amino acids Balanced mixtureofessential histidine. Amedicalfood. An unflavored, powderedmixture ofessentialaminoacids,includingcystineand Essential AminoAcidMix

• • Indications: 553342 Code Product Ordering/Reimbursement Information: suitable oramodularapproachisrequired Conditions inwhichanutritionallycompletefeedisnot Dietary managementofureacycle disorders office todetermine availability. WIC ‡ : Contactyour stateWIC 49735-0133-42 Reimbursement B4155 Code Packaging HCPCS information seepage195. information For morereimbursement 6 x200g(7oz) Product 632 Per Calories Can

Nutrition Information: L-Valine 14.56 L-Tyrosine 9.46 L-Tryptophan 2.36 L-Threonine 11.35 L-Phenylalanine 5.67 L-Methionine 3.78 L-Lysine 13.25 L-Leucine 16.17 L-Isoleucine 10.4 L-Histidine 3.78 L-Cystine 3.78 Amino Acids,g Carbohydrate, g Fat, g Protein Equivalent,g Calories 316 Nutrients L-Methionine, L-Tryptophan. L-Phenylalanine, L-Histidine, L-Cystine, L-Threonine, L-Isoleucine, L-Tyrosine, L-Lysine Acetate,L-Leucine, L-Valine, Ingredients: None None Per 100g 79 • • • Precautions: a gram scale. are approximations only. For accuracy use and unpacked. Householdmeasurements measurements. Allmeasurementsarelevel Based onstandardUSdry, household 1 Tbsp 1/2 Tbsp 1 tsp 1/2 tsp Measure (all measuresareunpacked) Household Measures:

source ofnutrition. Not suitableforuseasasole Not forparenteral use. of thepatient. weight andmedicalcondition dependent ontheage,body by adoctoror dietitianandis Dosage shouldbedetermined Weight 9.0 g 4.1 g 2.7 g 1.4 g Protein Equivalent

7.11 3.24 2.13 1.11

• • Storage: • • • Administration:

before serving. Stir orshake immediately from thetimeofpreparation. be kept longerthan24hours in arefrigerator andmustnot prepared feedshouldbestored after use. Always replacecontainerlid opened, usewithinonemonth. as applesauce. added tosoft,moistfoods,such other formulas.Itmay alsobe mixed withwater, fruitjuicesor that readsingrams. should beweighedonascale of water). 5 gpowderto100mL concentration is5%w/v (e.g. Once reconstituted,the Store inacool,dryplace.Once Best served as achilleddrink, Essential AminoAcidMix The recommendedfeeding

177 Essential Amino Acid Mix Acid Amino Essential 178 OTHER NUTRITIONALS • Main Features: and older meet theDRIofindividuals11years of vitaminsandminerals needed to One 7gpacket suppliesthemajority (11 years and older)andadults. designed tohelpmeetthemicronutrientrequirementsofolderchildren A concentrated, powderedvitamin,mineral andtrace elementpreparation Phlexy-Vits • Indications: 10685 Code Product Ordering/Reimbursement Information: Restrictive therapeutic diets 49735-0106-85 Reimbursement A9270 Code Packaging HCPCS 30 x7g Product 0.2 Calories Per Packet

Nutrition Information: Chloride, mg Potassium, mg Sodium, mg Selenium, mcg Chromium, mcg Molybdenum, mcg Iodine, mcg Copper, mcg Manganese, mg Zinc, mg Iron, mg Magnesium, mg Phosphorus, mg Calcium, mg Minerals Vitamin C,mg Biotin, mcg Pantothenic Acid,mg Folic Acid,mcg Niacin, mg Vitamin B Vitamin B Riboflavin, mg Thiamin, mg Vitamin K,mcg Vitamin E,IU(mg Vitamin D, IU(mcg) Vitamin A,IU(mcgRE) Vitamins Carbohydrate, g Fat, g Protein, g Calories 0.20 Nutrients 12 6 , mg , mcg a -TE) 400(10) 1505 1000 150 300 775 150 700 2664(800) Per 7gpacket 75.0 30.0 70.0 11.1 15.1 50.0 20.0 70.0 5.0 1.5 5.0 1.4 1.2 1.6 <0.35 <1.4 0.02 8.8 None 13.5 (9) 0.04 • • Precautions: a gram scale. are approximations only. For accuracy use and unpacked. Householdmeasurements measurements. Allmeasurementsarelevel Based onstandardUSdry, household 1 Tbsp 1 tsp 1/2 tsp 1/4 tsp Measure Weight (all measuresareunpacked) Household Measures: Vitamin D Phylloquinone, Selenite, D-Biotin,ChromiumChloride, Iodide, SodiumMolybdate, A Acetate,Folic Acid,Potassium Mononitrate, Riboflavin, Vitamin Pyridoxine Hydrochloride, Thiamin D-Pantothenate, Manganese Sulfate, Acetate, CopperGluconate,Calcium Nicotinamide, DL-Alpha Tocopheryl Ferrous Sulfate,Dextrose, ZincSulfate, Acetate, GuarGum,L-Ascorbic Acid, Calcium PhosphateDibasic,Magnesium Ingredients: source ofnutrition. Not suitable foruseasasole Not forparenteral use. 3 , Cyanocobalamin.

1.4 g 0.7 g

10 g

3 g • Storage: • • Administration: and usedwithin2-3days. be storedinanairtightcontainer Once opened,asachetshould Store inacool,dryplace. to taste. water usedwillvaryaccording amount oflemonade/juiceand volume of150 mL(5floz).The (approx. 1.5floz).Dilutetoafinal amount oflemonadeorfruitjuice to asmoothpastewithsmall Mix onesachetofPhlexy-Vits volume ofapproximately 100 mL. remaining watertogive afinal mix toasmoothpaste.Addthe Add asmallamountofwaterand

179 Phlexy-Vits 180 OTHER NUTRITIONALS • • • • • Main Features: directed by physician ordietitian. DIRECTIONS FOR USE: cool dryplace. cover withresealablelidandstoreina heat, humidityandlight.Afteropening, temperature (68º-77ºF). Protectfrom STORAGE: to hotfoodorbeverages above 130°F. WARNING: parenteral use. is nutritionallyincomplete.Notfor medical supervision.Thisproduct IMPORTANT: of metabolism. dietary managementofinbornerrors Amino Acidmedicalfoodsforthe Keep atcontrolledroom Do notheat,bake oradd For useunder Useas L-THREONINE L-METHIONINE L-VALINE L-TYROSINE L-LEUCINE L-ISOLEUCINE GLYCINE L-ARGININE Product Ordering/Reimbursement Information: water soluble.L-Tyrosine isnotwatersoluble. Note: • Suggested mixingdilution: provides 10mg ofaminoacids. into 100mLofsterilizedwater. Every 1mLof solution A 10%solutioncanbemadeby mixing1gofaminoacids This method will work forallaminoacidsthatare work This methodwill 0190T 0180M 0170V 0160T 0150L 0140I 0130G 0120A Code Product Reimbursement Pure aminoacidpowder. Single AminoAcids 49735-0001-90 49735-0001-80 00847-0017-00 00847-0016-00 00847-0015-00 00847-0014-00 00847-0013-00 00847-0012-00 B4155 B4155 B4155 B4155 B4155 B4155 B4155 B4155 Code HCPCS 1 -50gbottle 1 -50gbottle 1 -50gbottle 1 -50gbottle 1 -50gbottle 1 -50gbottle 1 -50gbottle 1 -50gbottle Description Package

181 Single Amino Acids Amino Single 182 OTHER NUTRITIONALS RESOURCES

TM Find more information and resources on these and all of our products at www.NutriciaLearningCenter.com 183 184 RESOURCES • • • • • resources andclinicaltoolsincludes: specialized nutritionalrequirements. Thissetofvaluable Nutricia Learning Centerisaunique educationtoolforcliniciansmanagingpatientswith Please visitourwebsiteforfreeelectronic copiesoftheseandtheotherflowchartsweoffer. manage patients. used asdecision-makingguidestohelpcliniciansdeterminethebestway tonutritionally specialized medicalnutritionmay behelpful.They areevidence-based toolsthatmay be These five flowchartsillustrate optionsforthenutritionmanagementofconditionswhere are available freeatwww.NutriciaLearningCenter.com The followingpagesincludepocket-sized versions flowchartsthat oftreatment Case Studies Reference Library Patient EducationTools Healthcare Professional Tools Recorded Webinars (CE eligible) Cow MilkAllergy/MultipleFoodAllergies 6+ months:

Individual requirementsasdirected byhealthcareprofessional 1+ years: 0-1 year: CONSIDER NEOCATE directed byhealthcareprofessional AABF supplement todietas a asasolesourceor (Unflavored, Grape,Orange-Pineapple) Neocate (Unflavored, Chocolate,Tropical) Neocate Neocate (Unflavored, Vanilla,Strawberry) Neocate Neocate Neocate ® ® ® ® ® ® ® Splash Junior Nutra InfantDHA/ARA JuniorwithPrebiotics Syneo™Infant TM YES b REACTION TOAN ANAPHYLACTIC IS PATIENTAT HIGH RISKOF ALLERGEN?* c b a * OFFENDING

Neocate Nutraisasupplemental semi-solidelementalfoodfor 6+months DRACMA Guidelines (Fiocchiet al,JAllergyClinImmunol 2010) may beequally reasonable. In settingswherethe costofanAABFislower,theuse AABF Hypoallergenic formula includesAABF(AminoAcid-BasedFormula) andeHF(ExtensivelyHydrolyzed Formula) ELIMINATE COW’SMILKPROTEIN AND/OR OTHERAPPROPRIATE ALLERGENS FROMDIET Hypoallergenic formula sole sourceorsupplement NO healthcare professional as directedby <2 YEARS NO NO OLD? FORMULA AN a IS COSTOF IS extensively TOLERATED? as formula (eHF) ISSUE? hydrolyzed YES c * hypoallergenic formula healthcare professional Elimination dietand as directedby YES 2+YEARS OLD? Continue witheHF as directedby professional healthcare a NO REQUIREMENTS? nutritional status Elimination diet Continue with

NUTRIENT MEETING Monitor

YES 185 Resources 186 RESOURCES Cow MilkAllergy/MultipleFood Allergies 6. 5. 4. 3. 2. 1. References: infants. JPediatr. 1997;131:741-4. Vanderhoof JA, etal.Intolerance toproteinhydrolyzed infantformulas:anunderrecognizedcauseofgastrointestinalsymptoms in Sampson HA,etal.Safetyofanaminoacid-derived infant formulainchildrenallergictocowmilk.Pediatrics. 1992;90:463-5. 2010;1119-28. Fiocchi A,etal.Diagnosisandrationale foractionagainstcow’smilkallergy(DRACMA): asummaryreport.JAllergyClinImmunol. de BoissieuD, etal.Timecourseofallergytoextensively hydrolyzed cow’smilkproteinsininfants.JPediatr. 2000;136:119-20. Pediatr. 2002;141:271-3. de BoissieuD, etal.Allergytoextensively hydrolyzed cow’smilkproteinsininfants:safetyandduration ofaminoacid-based formula.J formula. JPediatr. 1997;131:744-7. de BoissieuD,et al.Allergytoextensively hydrolyzed cowmilkproteinsininfants:identificationandtreatmentwithanaminoacid-based TM Eosinophilic Esophagitis >

nutritional assessments. Routine medicaland REQUIREMENTS? Empiric* orTailored ELIMINATION DIET * 2-7foodelimination NUTRIENT MEETING YES NO TM Supplement with AABF b > COMBINATION OFELEMENTAL feasible/tolerated. individually asmedically Reintroduce food AND ELIMINATIONDIET

6+ months: N Individual requirementsasdirectedbyhealthcareprofessional 1+ years: 0-1 year: CONSIDER NEOCATE NUTRITION THERAPY Nutritional status,ageandsocialneedsofpatient are keyindeterminingappropriatetreatment. a b

(Unflavored, Grape,Orange-Pineapple) Neocate (Unflavored, Chocolate,Tropical) Neocate (Unflavored, Vanilla,Strawberry) N Neocate Neocate AABF –AminoAcid-Based Formula Neocate Nutraisasupplemental semi-solidelementalfoodfor 6+months eocate eocate ® ® ® ® ® ® Splash Junior JuniorwithPrebiotics Nutra InfantDHA/ARA Syneo™Infant ® COMBINE IFMEDICALLYAPPROPRIATE a ELEMENTAL DIET Supplement with AABF > > as long-termsituation. nutritional assessments. Consider nutritionaltherapy Routine medicaland b PHARMACOLOGIC NO REQUIREMENTS? NUTRIENT THERAPY MEETING YES 7

187 Resources 188 RESOURCES Eosinophilic Esophagitis 7. 6. 5. 4. 3. 2. 1. References: eosinophilic esophagitisinchildren.JPediatr GastroenterolNutr. 2013; 57(S1):E4. Hait EJ, etal.Neocate®Nutra isaseffective assucralose asadelivery vehicle fororal viscousbudesonidetotreat Philadelphia, PA: Elsevier, 2009:19-27. eosinophilicesophagitis. In:FurutaPutnam PE.Evaluationofthechildwhohas GT, AtkinsD, AlamR,Eds.ImmunolAllergyClin NorthAm. 2011;128:3-20. EpubApril7,2011. Liacouras CA,etal.Eosinophilicesophagitis:updatedconsensusrecommendationsforchildrenandadults.JAllergyClinImmunol. esophagitis. NutrClinPract. 2011;26:19. Haas AM.Development, mealtimedynamicsandnutrition:useofanaminoacid-basedsemi-solidsupplementinachildwitheosinophilic Feuling MBandNoelRJ. Medicalandnutritionalmanagementofeosinophilicesophagitisinchildren.NutrClinPract. 2010;25:166-74. panel. JAllergyClinImmunol.2010;S1-58. Boyce JA, etal.Guidelinesfor thediagnosisandmanagementoffoodallergyinUnitedStates:reportNIAID-sponsoredexpert Accessed July6,2011. American DieteticAssociation.EosinophilicEsophagitis.Pediatric NutritionCareManual®. http://www.peds.nutritioncaremanual.org. TM Short BowelSyndrome Breastmilk and/orhypoallergenicformula 6+ months: Individual requirementsasdirected by healthcareprofessional 0-1 year: CONSIDER NEOCATE FULL ENTERALNUTRITION as asolesourceorsupplement to thedietasdirectedbya healthcare professional Neocate Neocate ® ® Nutra InfantDHA/ARA ® INFANT TM a b ENTERAL NUTRITION TRANSITION TO AS TOLERATED PATIENT? AGE OF YES Age-appropriate hypoallergenicformula N Individual requirementsasdirectedby healthcareprofessional 1+ years: CONSIDER NEOCATE 6+ months: N b a

AND PARENTERALNUTRITION

COMBINATION OFENTERAL Neocate Nutra isasupplemental semi-solidelemental foodfor6+months and eHF Hypoallergenic formula includesAABF(AminoAcid-BasedFormula) as asolesourceorsupplement 1+ YEARS to thedietasdirectedbya FUNCTIONAL healthcare professional GI TRACT? (Extensively Hydrolyzed Formula) PARTIALLY (Unflavored, Vanilla,Strawberry) Neocate Neocate (Unflavored, Grape,Orange-Pineapple) (Unflavored, Chocolate,Tropical) eocate eocate ® ® ® ® ® Nutra JuniorwithPrebiotics Splash Junior a b NO ENTERAL NUTRITION TRANSITION TO AS TOLERATED YES P ARENTERAL NUTRITION GI FUNCTION RETURNS? NO

189 Resources 190 RESOURCES Short BowelSyndrome 4. 3. 2. 1. References: May 31,2010. De GreefE,etal.TheinfluenceofNeocateinpaediatricshortbowelsyndromeonPNweaning.JNutrMetab.2010;pii:297575. Epub formula. JPediatr GastroenterolNutr. 1998;26:123-8. Bines J, etal.Reducingparenteral requirementinchildrenwithshortbowelsyndrome: impactofanaminoacid-basedcompleteinfant Becker PJ. Cow’smilkallergyinapreterminfant:casepresentation.ICAN:Infant,Child,&AdolescentNutrition.2009;214-9. outcomes. JPediatr. 2001;139:27-33. Andorsky DJ, etal.Nutritionalandotherpostoperative managementofneonateswithshortbowelsyndromecorrelatesclinical TM Wounds RN Assessment See appendix3 > Develop&implementPlanofCare > Weighweeklyorperfacilitypolicy > Considervit/minsupplementwith100%ofRDAifintakeispoor > Liberalizerestrictivediets > Offerpreferredfood/beverageatappropriatetexture > ProvidehighvitaminCrichfoodsdaily > Providehighcaloriefoods > DocumentinMAR > ProvidePro-Statwithmedicationpass > RecommendphysicianorderPro-Stat See appendix4 Weekly orPerFacilityPolicy Monitor Nutritional&MedicalStatus Routine of Risk RISK FACTORS See appendix1 HIGH? See appendix3 orperfacilitypolic y Monitor Nutritional &MedicalStatusWeekly YES NO * Unlesscontraindicated **RDA =90mgformales; 75mgforfemales; upperlimit=2000mg ***RDA=11mg formales;8mgfemales; upperlimit=40mg EXISTING WOUND? ® *** RDA = 11mgforadultmales;8females; upperintake level =40mg * Unlesscontraindicated **RDA =90mgforadult males;75mgforadultfemales;upper intake level =2000mg YES See appendix5 Plan asNeededUntilWoundHealed Re-evaluate NutritionalIntervention &Modify Obtain CBC,CMP, Albumin levelsas per facilitypolicy Prealbumin, (Diabetic, Venous,Surgical,Burns) Multiple PressureInjuries,HardtoHealWounds Stage 3and4PressureInjury Stage 2PressureInjury Stage 1PressureInjuryorWounds High riskforWounds Stage RN /LPNadminister30mLoncedailyuntilRDdeterminesactualdosage based oncondition,estimatedneed&dietaryintake CONSIDER PRO-STAT Adjust perclinicalcondition • • • • • NUTRITION THERAPY with 100%ofRDAifintakeispoor Multivitamin withmineralsupplement suspected deficiency Vit C**&Zinc***:Supplement>RDAif Fluid: 1mlperdaykcalconsumed Protein: 1.2-1.5gms/kg/bodyweight* Calories: 30-35kcal/kg/bodyweight ®

2,3

1 Pro-Stat SugarFreeAW Pro-Stat SugarFreeAW Pro-Stat SugarFree Pro-Stat SugarFree Pro-Stat SugarFree Pro-Stat ®

(serving size=30mL) Specializ

Nutrition C C REQUIREMENTS? Routine RDN/Dietary Manager Nutritional See appendix2 NUTRIENT MEETING Assessment NO ed Adult YES

. 191 Resources 192 RESOURCES Wounds 5. 4. 3. 2. 1. References: 24. 23. 22. 21. 20. 19. 18. 17. 2:NutritionalAssessment Appendix 16. 15. 14. 13. 12. 11. 10. 9. 8. 7. 6. 5. 4. 3. 2. 1. 1:RiskFactors Appendix Nestle NutritionInstitute.http://www.mna-elderly.com/forms/MNA_english.pdf. AccessedMarch 11,2015. Braden B.http://www.bradenscale.com/images/bradenscale.pdf. AccessedMarch11,2015. Hays NP, etal.JAmDiet Assoc.2009;109:1082-7. Lee SK,etal.AdvSkinWound Care.2006;19:92-6. National PressureUlcerAdvisoryPanel, etal.Prevention andTreatment ofPressureUlcers:ClinicalPractice Guideline.CambridgeMedia;2014. Determine nutritionalneeds Determine deviation fromcurrentbodyweight Body MassIndex Amount &qualityofproteinprovided Current dietaryintake Review ofskinassessmentscreeningtools assessment Review skinconditionperfacility’swound Review diagnosis/medical condition Albumin level is≤2.8 History ofpressureinjuries Skin exposure tourinaryorfecalincontinence Cognitive impairments diabetes Co-morbid conditions:end-stagerenaldisease, Chewing/swallowing problem/dysphagia Decline inabilitytoeatindependently deficits Diagnosis ofundernutrition/malnutrition/hydration Infections (UTI) Immobility, declineinADLs Receiving enteral/parenteral nutrition Poor oral intake Body massindex (≤18.5or≥30) in 180days Unintended weightloss≥5%in30days, ≥10% MNA-SF Braden Scale<16 ® ≤11 5 4 www.NutriciaLearningCenter.com 38. 37. 36. 35. 34. 33. 32. 31. 3:ProteinSupplementation Appendix 30. 29. 28. 27. 26. 25. nutritional goals Monitor 2-4weeks&modifyasneededtomeet and kosher are lactosefree,soy free,gluten Pro-Stat SugarFree andPro-StatSugarFree AWC Pro-Stat SugarFree AWC is honey-like Viscosity: Pro-StatSugarFree isnectar-like, > > Pro-Stat additional 30-60mL water, dilutewith30-60mLwater, &flushtubewith If administeredviatube-feeding:flushwith30-60mL or foodofchoice Based onpreference,itcanbemixed withbeverage into medcup Administer POwithmedpass,pouramountordered & Caregiver appropriate to:Nursing,Dietary, Physician, Resident, Nutrition intervention willbe communicatedas renal function affected by infection,inflammation, hydration and albumin, etc.Note:serumhepaticproteinvaluesare Nutrition relatedlaboratory values:HgbA1C,BUN, Dehydration riskfactors independently Chewing/swallowing status/ability toeat (% consumed) Average food/ fluid intake, medical food supplements steroids) Medications/medical treatments(antibiotics, Interview forfoodpreferences&intolerances Sugar Free AWC Sugar Free: ® provides: 15gprotein,100kcal/30 mL : 17gprotein,100kcal/30 mL

53. 52. 51. 50. 5:Evaluate Appendix 49. 48. 47. 46. 45. 44. 43. 42. 41. Appendix 4:MonitorNutritional&MedicalStatus 40. 39. Document &re-assessperpolicy requirements Intake meetsestimatedcalorie,protein&fluid Improved and/or stable nutritionalstatus Intact skinand/or progresstoward healing progress forpressureinjuryhealing Consider validatedtoolsuchasPUSHtomonitor improves ordeclines interdisciplinary team&adjust,ifconditionchanges, Effectiveness ofintervention incollaboration with Laboratory values,ifavailable Weight status consistent withindividual’swishes Oral intake, ifinadequate, considerenteral feeding Ability tomeetnutrientneedsorally estimated requirement Calorie, protein,fluidadequacycomparedto Acceptance &tolerance ofsupplement per policy Skin conditionand/or woundstatus weeklyor 3 months Label &dateuponopening,discardingafter atroomtemp Store Pro-Stat Specializ Nutrition ed Adult

Urinary Tract Infections(UTI) NO Routine RNAssessment RISK FACTORS See appendix1 TM of Risk HIGH? YES * Useclinicaljudgmenttodetermineactualdosage basedonriskfactors¤tcondition UTI High riskforUTI Indication CONSIDER UTI-STAT Monitor acceptanceofUTI-Stat&resolutionUTIinmedical record Re-evaluate riskfactorsand adjust dosageasnecessary See appendix2 • • • • RN/RDN Document inCarePlan&medicalrecord Encourage fluidintake Provide UTI-Statwithmedicationpass Recommend physicianorderUTI-Stat 30 mL 30 mL Serving Size NO ®

1,2 EXISTING UTI? YES to twicedailyforurinarytracthealth Twice dailyfor4weeks,thenonce Once totwicedaily Suggested Dose* ®

193 Resources 194 RESOURCES Urinary Tract Infections(UTI) 2. EfrosM,etal.Urology. 2010;76:841-5. 1. Posthauer ME.TheDirector. 2008;16:13-6. References: 20. 19. 18. 17. 16. 15. 14. 13. 12. 11. 10. 9. 8. 2:UTI-Stat Appendix 7. 6. 5. 4. 3. 2. 1. 1:RiskFactors Appendix medical record(RN) Monitor &documentacceptanceofUTI-Statresponsetotheint ervention in Continue facilitypoliciesforUTImanagement(hygiene e.g.)(RN) Encourage increasedconsumptionoffluids Document intervention incareplan UTI-Stat provides 70calories&1gofsugarper30mL dosage, administerintoenteral tube,flushtubewithadditional30mL If administeredviatube-feeding:flushtubewith30mLwater, measureappropriate UTI-Stat canbeconsumedstraight ormixed withany foodorbeverage Administer UTI-StatPOwithmedpass,pouramountorderedintocup Resident, &Caregiver Communicate administration asappropriateto:Nursing,Dietary, Physician, Recommend physician orderUTI-Stat taking forUTI cranberry juice,cranberry containingsupplements,D-Mannose,orvitaminCif Recommend thephysician holdordiscontinuecurrentordersforcranberry tablets, Asses allergytocranberry products Assess currentfluidintake/type ofliquids(thinorthickened) Orders forprophylactic antibiotics Immobility Urinary retention Incontinence Two ormoreUTIsinthepast6months Catheterization Poor fluidintake lessthan1000mL/day ® Administration www.NutriciaLearningCenter.com 1,2 Specializ Nutrition ed Adult Other ReimbursementInformation: Reimbursement Codes: WIC: Reimbursement United States, pleasecontactusat(800) 365-7354orvisitourwebsites: United States, For additionalinformationonreimbursement ofNutriciaNorthAmerica’s productsinthe codes arenotNDCnumbers. to USdatawarehousesbasedonthe formatestablishedby thedatawarehouses.These Reimbursement codeslistedinthis Guidehave beensubmittedby NutriciaNorth America http://www.fns.usda.gov/wic office todeterminethe availability ofaspecificWICeligibleNutriciaproductin yourarea– ContactyourEach WICStateagencydeterminesitsownallowedformulalist. StateWIC may Stateagencysochooses. the foodlistif beincludedonaStateagency’sauthorized WIC eligible Supplemental NutritionProgram forWomen, InfantsandChildren. ‡ WIC isaregisteredservicemarkoftheU.S. DepartmentofAgricultureforUSDA’s Special means that aproduct hasbeenapproved meansthat Federal atthe level and,therefore, www.Nutricia-NA.com . www.Neocate.com

195 Resources 196 RESOURCES • • • • • • • b food, beverages, anddrinkingwater a Individual patientrecommendationsmay vary. percentage ofindividualscovered by thisintake. prevent beingabletospecifywithconfidencethe group, butlackofdataoruncertaintyinthe believed tocover needsofallindividualsinthe The AIforotherlifestageandgendergroupsis breastfed infants,theAIismeanintake. percent) individualsinagroup.For healthy set tomeettheneedsofalmostall(9798 used asgoalsforindividualintake. RDAs are by anasterisk(*).RDAs andAIsmay bothbe Adequate Intakes (AIs)inordinarytypefollowed Dietary Allowances(RDAs) in see www.nap.edu) presentRecommended * Note: National Academies(1997-2005) Food andNutritionBoard, InstituteofMedicine, Nutrients, VitaminsandElements Adequate Intakes, Total Water, Macro- Recommended DietaryAllowancesand § Resources To Basedongproteinperkgbodyweight:

Dietary ReferenceIntakes (DRIs):

1.5 g/kg/day forinfants7-12months 1.52 g/kg/day forinfants 0-6months 1.1 g/kg/day forpregnant(usingpre- 0.80 g/kg/day foradults 0.85 g/kg/day for14-18y 0.95 g/kg/day for4-13y 1.1 g/kg/day for1-3 pregnancy weight) andlactating women tal Water includesallwatercontainedin Thetables(taken fromtheDRIreports, bold type and 31-50 y 19-30 y 14-18 y Lactation 31-50 y 19-30 y 14-18 y Pregnancy >70 y 51-70 y 31-50 y 19-30 y 14-18 y 9-13 y Females > 70y 51-70 y 31-50 y 19-30 y 14-18 y 9-13 y Males 4-8 y 1-3 y Children 7-12 mo 0-6 mo Infants Group Life Stage Macronutrients Total Water (L/d) 3.8* 3.8* 3.8* 3.0* 3.0* 3.0* 2.7* 2.7* 2.7* 2.7* 2.3* 2.1* 3.7* 3.7* 3.7* 3.7* 3.3* 2.4* 1.7* 1.3* 0.8* 0.7* a

Carbohydrate 210 210 210 175 175 175 130 130 130 130 130 130 130 130 130 130 130 130 130 130 95* 60* (g/d)

29* 29* 29* 28* 28* 21* 21* 25* 26* 26* Total Fiber ND ND (g/d) 28* 25* 30* 30* 38* 38* ND 38* 31* 25* ND 19* ND ND ND ND ND ND ND ND ND ND ND ND ND ND ND ND ND ND 30* 31* (g/d) Fat 13* 13* 13* 13* 13* 13* 11* 11* 12* 12* 11* 10* Linoleic Acid 14* 14* 17* 4.6* 17* 16* 12* 10* (g/d) 7* 4.4* a -Linolenic Acid (g/d) 1.2* 0.7* 0.5* 1.3* 1.3* 1.3* 1.4* 1.4* 1.4* 1.1* 1.1* 1.1* 1.1* 1.1* 1.0* 1.6* 1.6* 1.6* 1.6* 1.6* 0.9* 0.5*

Protein

71 71 71 71 71 71 46 46 46 46 46 34 56 56 56 56 52 34 19 13 11.0+ (g/d) 9.1* Resources Vitamins 31-50 y 19-30 y 14-18 y Lactation 31-50 y 19-30 y 14-18 y Pregnancy > 70y 51-70 y 31-50 y 19-30 y 14-18 y 9-13 y Females > 70y 51-70 y 31-50 y 19-30 y 14-18 y 9-13 y Males 4-8 y 1-3 y Children 7-12 mo 0-6 mo Infants Group Life Stage Vitamin A (mcg/d) 1,300 1,300 1,200 770 770 750 700 700 700 700 700 600 900 900 900 900 900 600 400 300 500* 400*

VitaminD (mcg/d)

10* 10*

15 15 15 15 15 15 20 15 15 15 15 15 20 15 15 15 15 15 15 15

VitaminE (mg/d)

5* 4* 19 19 19 15 15 15 15 15 15 15 15 11 15 15 15 15 15 11 7 6

120* 120* 120* 120* VitaminK 90* 90* 75* 90* 90* 75* 90* 90* 90* 90* 75* 60* 60* 55* 30* 75* (mcg/d) 2.5* 2.0* ThiaminRiboflavin Niacin

0.3* 0.2* (mg/d) 1.4 1.4 1.1 1.2 1.4 1.4 1.4 1.4 1.1 1.1 1.1 1.0 0.9 1.2 1.2 1.2 1.2 0.9 0.6 0.5 1.6 1.4 1.1 1.3 1.6 1.6 1.4 1.4 1.1 1.1 1.1 1.0 0.9 1.3 1.3 1.3 1.3 0.9 0.6 0.5 0.4* 0.3* (mg/d) (mg/d 17 18 14 16 17 17 18 18 14 14 14 14 12 16 16 16 16 12 8 6 4* 2*

)

1.0 (mg/d) Vitamin B 1.5 2.0 2.0 2.0 1.9 1.9 1.9 1.5 1.3 1.3 1.2 1.7 1.7 1.3 1.3 1.3 1.0 0.6 0.5 0.3* 0.1* 6

(mcg/d) Folate 400 500 500 500 600 600 600 400 400 400 400 400 400 400 400 400 300 200 150 300 80* 65* VitaminB (mcg/d) 2.4 2.8 2.8 2.8 2.6 2.6 2.6 2.4 2.4 2.4 2.4 2.4 2.4 2.4 2.4 1.8 1.2 0.9 0.5* 0.4* 2.4 1.8

7* 7* 7* 6* 6* 6* 5* 5* 5* 5* 5* 5* 5* 5* 5* 5* 4* 3* 2* Pantothenic Acid (mg/d) 4* 1.8* 1.7* (mcg/d) Biotin 35* 35* 35* 30* 30* 30* 30* 30* 30* 30* 25* 30* 30* 30* 30* 25* 20* 12* 20* 8* 6* 5* 550* 550* 550* 375* 250* 200* 550* 550* 550* 450* 450* 450* 425* 425* 425* 425* 400* 550* 550* 375* 150* 125* Choline (mg/d)

Vitamin C 50* 40*

120 115 80 (mg/d)

120 90 45 25 45 90 85 85 75 75 75 75 65 90 90 75 15 197 Resources 198 RESOURCES 31-50 y 19-30 y 14-18 y Lactation 31-50 y 19-30 y 14-18 y Pregnancy > 70y 51-70 y 31-50 y 19-30 y 14-18 y 9-13 y Females > 70y 51-70 y 31-50 y 19-30 y 14-18 y 9-13 y Males 4-8 y 1-3 y Children 7-12 mo 0-6 mo Infants Group Life Stage Minerals

Calcium

260* 200* (mg/d)

1,000 1,000 1,000 1,300 1,000 1,000 1,300 1,200 1,200 1,000 1,300 1,300 1,200 1,000 1,000 1,000 1,300 1,300 1,000 700

Phosphorus

275* 100*

(mg/d) 1,250 1,250 1,250 1,250 1,250 1,250 700 700 700 500 460 700 700 700 700 700 700 700 700 700 Magnesium 320 310 360 360 350 400 320 320 320 310 360 240 400 420 420 420 410 240 75* 30* 130 80 (mg/d)

0.01* Fluoride 0.5* 0.7* (mg/d) 3* 4* 4* 4* 4* 3* 2* 3* 3* 3* 3* 3* 3* 3* 3* 3* 3* 2* 1* Selenium (mcg/d) 20* 15*

70 70 70 60 60 60 55 55 55 55 55 40 55 55 55 55 55 40 30 20

Chromium 0.2* 45* 45* 44* 30* 30* 29* 20* 20* 25* 25* 24* 21* 30* 30* 35* 35* 35* 25* 15* 11* 5.5

(mcg/d)

1,300 290 1,300 290 1,300 1,000 1,000 1,000 (mcg/d) Copper 900 150 900 150 900 900 890 700 120 900 150 900 150 900 150 900 150 890 700 120 440 340 220* 130* 200* (mcg/d) Iodine 150 18 150 18 150 15 150 11 110* 290 10 220 27 220 27 220 27 90 10 90 7 (mg/d) 11 Iron 8 8 8 8 8 8 8 8 0.27* 9 9 2.6* 2.6* 2.6* 2.0+* 2.0+* 2.0+* 1.8* 1.8* 1.8* 1.8* 1.6* 1.6* 2.3* 2.3* 2.3* 2.3* 2.2* 1.9* 1.5* 1.2* Manganese (mg/d) 0.003* 0.6* Molybdenum (mcg/d) 50 12 50 12 50 13 50 11 50 11 50 12 45 8 45 8 45 8 45 8 43 9 34 8 45 11 45 11 45 11 45 11 43 11 34 8 22 5 17 3 2* 3* (mg/d) Zinc 2* 3 * Approximately 10%ofthetotalcancomefromlonger-chainn-3orn-6fattyacids. Protein Carbohydrate n-3 polyunsaturated fattyacids*( n-6 polyunsaturated fattyacids*(linoleicacid) Fat Macronutrient Acceptable MacronutrientDistributionRanges a -linolenic acid)

Children, 1-3y 0.6 -1.2 45-65 30-40 5-20 5 -10

Range (percent ofenergy) (percent Range Children, 4-18y 0.6 -1.2 45-65 10-30 25-35 5-10

0.6-1.2 45-65 20-35 10-35 5-10 Adults 199 Resources 200

RESOURCES Resources • • www.MedicalFood.com andwww.DietForLife.com • • • www.Neocate.com • • • www.NutriciaLearningCenter.com • www.Nutricia-NA.com with foodallergiesand/or relatedGIconditions.ThroughFootsteps patientsand low proteindiets. Feature onlinemetabolicshopsincluding convenient low proteinfoods,integral to community forums. Interactive, onlineresources forthemetaboliccommunitywithnews,recipes, and And more! families willhave accessto: Footsteps provides supportateachstepofapatient’sjourney whendiagnosed Neocate Footsteps. Provides valuableresourcesandsupportthroughacomprehensive program, Clinician resources,patientresourcesandcasestudies. CE-eligible webinarsby esteemedexperts. managing patientswithspecialnutritionalneeds. A communityhubandtrusted,collective resourceforhealthcareproviders Provides anoverview ofNutriciaNorthAmerica. • • • through socialcommunities. Resources toadaptinsocialsettingsthroughhelpful tipsandsupport allergy-friendly recipes,andinformationalvideos. Support inadjustingtonewlifestyleathomethrough transition guides, Assistance togaininsurance coverage forNeocate.

M M Specializ y y m Nutrition KETO PLANNE KETO PLANNE KETOGENIC DIETMADEEASY y C onnect ed Adult R R TM TM • • www.SpecializedAdultNutrition.com • • www.MyDuocal.com • • www.MyKetoPlanner.com • • www.KetoConnect.com • • • www.MyKetoCal.com Features tips, recipesandinformationonhowtoorderourproducts. Nutrition products. Educates cliniciansandconsumersaboutNutricia’s SpecializedAdult Provides informationaboutFailure-to-Thrive forcliniciansandcaregivers. Frequently asked questions,recipes,and helpful tipsonDuocal. Accessible viawebsiteormobileapplication. designed fortheketogenic dietcommunity. A dietmanagementtool,recipe-sharingdatabaseandsocialnetworkspecifically Provides information,helpfultips,recipeideasandmore. A supportblogforcaregivers ofchildrenontheketogenic dietforepilepsy. Helpful recipesandtoolsforfamiliesdietitiansusingtheketogenic diet. “Find aKetogenic Center”tool. Locate aketogenic dietcenterinNorthAmericaby usingthe Provides valuableresourcesandeducationalmaterialsforcliniciansfamilies.

201 Resources 202 RESOURCES NOTES ......

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