ACADL Antibody Cat

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ACADL Antibody Cat. No.: 25-166 ACADL Antibody Specifications HOST SPECIES: Rabbit SPECIES REACTIVITY: Human, Mouse Antibody produced in rabbits immunized with a synthetic peptide corresponding a region IMMUNOGEN: of human ACADL. TESTED APPLICATIONS: ELISA, WB ACADL antibody can be used for detection of ACADL by ELISA at 1:312500. ACADL APPLICATIONS: antibody can be used for detection of ACADL by western blot at 1 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000. POSITIVE CONTROL: 1) Cat. No. 1309 - Human Placenta Lysate PREDICTED MOLECULAR 44 kDa WEIGHT: Properties PURIFICATION: Antibody is purified by peptide affinity chromatography method. CLONALITY: Polyclonal CONJUGATE: Unconjugated PHYSICAL STATE: Liquid September 26, 2021 1 https://www.prosci-inc.com/acadl-antibody-25-166.html Purified antibody supplied in 1x PBS buffer with 0.09% (w/v) sodium azide and 2% BUFFER: sucrose. CONCENTRATION: batch dependent For short periods of storage (days) store at 4˚C. For longer periods of storage, store STORAGE CONDITIONS: ACADL antibody at -20˚C. As with any antibody avoid repeat freeze-thaw cycles. Additional Info OFFICIAL SYMBOL: ACADL ALTERNATE NAMES: ACADL, ACAD4, LCAD ACCESSION NO.: NP_001599 PROTEIN GI NO.: 4501857 GENE ID: 33 USER NOTE: Optimal dilutions for each application to be determined by the researcher. Background and References ACADL belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta- oxidation of straight-chain fatty acid. Defects in this gene are the cause of long-chain acyl- CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia.The protein BACKGROUND: encoded by this gene belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in this gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia. REFERENCES: 1) Lea, W., Biochim. Biophys. Acta 1485 (2-3), 121-128 (2000). ANTIBODIES FOR RESEARCH USE ONLY. For additional information, visit ProSci's Terms & Conditions Page. September 26, 2021 2 https://www.prosci-inc.com/acadl-antibody-25-166.html.

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