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Benign Brain/CNS Tumors

Benign Brain/CNS Tumors

June 30, 2004

Dear Pathologist/MIS Departments: RE: New Reportable Requirements FL Clinical Laboratory Identification Program (CLIP)

NEW REQUIREMENTS As of January 1, 2004 any benign, borderline intracranial and CNS Tumor are reportable to FCDS. All Pathology laboratories that read specimens from FL patients will be responsible for reporting benign primary intra-cranial and (CNS) tumors that have been diagnosed on or after January 1, 2004.

The following is a list of ICD-9-CM Diagnostic codes to be used as a source for identifying reportable benign and CNS tumors. Remember to add this new list of codes: Casefinding List ICD-9-CM Casefinding Codes for Benign and Borderline Intracranial and CNS Tumors ICD-9 Code Description 225.0 Benign neoplasm of brain 225.1 Benign neoplasm of cranial nerves 225.2 Benign neoplasm of cerebral ; cerebral 225.3 Benign neoplasm of , cauda equina 225.4 Benign neoplasm of spinal meninges; spinal meningioma 225.8 Benign neoplasm of other specified sites of nervous system 225.9 Benign neoplasm of nervous system, part unspecified 227.3 Benign neoplasm of pituitary, craniopharyngeal duct, craniobuccal pouch, hypophysis, Rathke’s pouch, sella turcica 227.4 Benign neoplasm of , pineal body 237.0 Neoplasm of uncertain behavior of pituitary gland and craniopharyngeal duct Neoplasm of uncertain behavior of pineal gland 237.1 Neoplasm of uncertain behavior of pineal gland 237.5 Neoplasm of uncertain behavior of brain and spinal cord 237.6 Neoplasm of uncertain behavior of meninges: NOS, cerebral, spinal 237.70 , Unspecified von Recklinghausen’s Disease 237.71* Neurofibromatosis, Type One von Recklinghausen’s Disease 237.72 Neurofibromatosis, Type Two von Recklinghausen’s Disease 237.9 Neoplasm of uncertain behavior of other and unspecified parts of nervous system; cranial nerves *Code 237.71 may not be reportable, however, these diagnosis may indicate a reportable condition and should be reviewed. To get the complete listing of reportable histology codes or if you would like more information about the CLIP program please visit the FCDS website FCDS.med.miami.edu . Click the PATH LAB icon for more information. Should you have any questions please contact Mayra Alvarez, FCDS Manager of Non Hospital Sources at (305) 243-4603 or via e-mail; [email protected]. On behalf of the Department of Health and the Florida Cancer Data System, I would like to thank you and your staff for your support. Sincerely,

Jill A. MacKinnon FCDS Administrative Director

New search terms and Morphology codes 9383/1 9560/0 ACOUSTIC NEURILEMMOMA GRANULAR CELL TUMOR, NOS 9580/0 9560/0 ACOUSTIC NEURINOMA GRANULAR CELL TUMOR, SELLAR REGION 9582/0 9560/0 ACOUSTIC HEMANGIOBLASTIC MENINGIOMA 9535/0 9560/0 ACOUSTIC 9161/1 9351/1 ADAMANTINOMATOUS HEMANGIOENDOTHELIOMA, BENIGN 9130/0 8140/0 ADENOMA HEMANGIOENDOTHELIOMA, NOS 9130/1 8861/0 ANGIOLIPOMA HEMANGIOMA 9120/0 9534/0 ANGIOMATOUS MENINGIOMA , BENIGN 9150/0 9421/3 PILOCYTIC, ASTROCYTOMA PILOID HEMANGIOPERICYTOMA, NOS 9150/1 8140/1 ATYPICAL ADENOMA INTRANEURAL PERINEURIOMA 9571/0 9390/1 ATYPICAL PAPILLOMA JUVENILE ASTROCYTOMA 9421/1 9539/0 ATYPICAL MENINGIOMA LDD 9493/0 8300/0 BASOPHIL ADENOMA LEIOMYOMA, NOS 8890/0 8000/0 BENIGN BRAIN LEIOMYOMATOSIS 8890/1 9131/0 CAPILLARY HEMANGIOMA LHERMITTE-DUCLOS DISEASE 9493/0 9350/1 CARNIOPHARYNGIOMA LIPOMA, NOS 8850/0 9121/0 CAVERNOUS HEMANGIOMA LYMPHOPLASMCYTE-RICH MENGIOMA, NOS 9530/0 9560/0 CELLULAR NEURILEMMOMA MACROFIOLLICULAR ADENOMA 8334/0 9506/1 CENTRAL MELANOTIC NEURILEMMOMA 9560/0 9493/0 CEREBELLAR GRANULE CELL HYPERTROPHY MELANOTIC 9541/0 9506/1 CEREBELLAR LIPONEUROCYTOMA MENINGEAL MELANOCYTOMA 9531/0 9444/1 CHORDOID MENINGIOMA 9530/0 9538/1 CHORDOID MENINGIOMA MENINGIOMA, NOS 9530/0 9390/0 MENINGIOMATOSIS, NOS+A44 9530/1 8270/0 CHRMOPHOBE ADENOMA MENINGOTHELIAL MENINGIOMA 9531/0 8310/0 CLEAR CELL ADENOMA MENINGOTHELIOMATOUS MENINGIOMA 9531/0 9538/1 CLEAR CELL MENINGIOMA METAPLASTIC MENINGIOMA 9530/0 8005/0 CLEAR CELL TUMOR, NOS MICROCYTIC MENINGIOMA, NOS 9530/0 8334/0 COLLOID ADENOMA MICROFOLLICULAR ADENOMA 8333/0 9350/1 CRANIOPHARYNGIOMA MIXED ACIDOPHIL-BASOPHIL ADENOMA 8281/0 9084/0 DERMOID CYST, NOS MIXED CELL ADENOMA 8323/0 9412/1 DESMOPLASTIC INFANTILE ASTROCYTOMA MIXED - 9383/1 9493/0 DIFFUSE HYPERTROPHY OF THE CEREBELLAR CORTEX MONOMORPHIC ADENOMA 8146/0 8728/0 DIFFUSE MELANOCYTOSIS MUCOID CELL ADENOMA 8300/0 9413/0 DNET MYXOPAPILLARY EPENDYMOMA 9394/1 9413/0 DNT NEOPLASM, BENIGN 8000/0 DYSEMBRYOPLASTIC NEUROEPITHELIAL TUMOR 9413/0 NEOPLASM, BENIGN UNCERTAIN WHETHER BENIGN OR 8000/1 MALIGNANT DYSPLASTIC GANGLIOCYTOMA OF CEREBELLUM 9493/0 NEURILEMOMA 9560/0 ENDOTHELIOMATOUS MENINGIOMA 9531/0 NEURINOMATOSIS 9560/1 EOSINOPHILL ADENOMA 8280/0 NEUROASTROCYTOMA 9492/0 EPITHELIAL TUMOR BENIGN 8010/0 NEUROFIBROMA 9540/0 EPITHELIOID HEMANGIOENDOTHELIOMA 9133/1 NEUROFIBROMATOSIS, NOS 9540/1 FETAL ADENOMA 8333/0 NEUROGENIC TUMOR 9520/3 FIBROBLASTIC MENINGIOMA 9532/0 NEUROMA 9570/0 FIBROLIPOMA 8851/0 NEUROTHEKEOMA 9562/0 FIBROMA, NOS 8810/0 ONCOCYTIC ADENOMA 8290/0 FIBROUS MENINGIOMA 9532/0 ONCOCYTOMA 8290/0 GANGLIOCYTOMA 9492/0 OXYPHILIC ADENOMA 8290/0 9505/1 PAPILLARY ADENOMA 8260/0 GANGLIOMATOSIS OF THE CEREBELLUM 9493/0 PAPILLARY CRANIOPHARYNGIOMA 9352/1 9490/0 , NOS 8680/1 GANGLIONEUROMATOSIS 9491/0 PERINEURIOMA 9571/0 GIANT CELL GLIOMA 9384/1 9421/1 GLANDULAR PAPILLOMA 8260/0 PILOID ASTROCYTOMA 9421/1 GLIOFIBROMA 9442/1 PINEAL PARENCHYMAL TUMOR (PPT) 9361/1 , NOS 9361/1 PINEAOCYTOMA 9361/1 8272/0 PLEXIFORM NEURILEMMOMA 9560/0 PLEXIFORM NEUROFIBROMA 9550/0 8271/0 PSAMMOMATOSIS MENINGIOMA 9533/0 RATHE POUCH TUMOR 9350/1 RHABDOMYOMA, NOS 8900/0 SECRETORY MENINGIOMA 9530/0 SEGA 9384/1 SMOOTH MUSCLE TUMOR NOS 8897/1 SOFT TISSUE PERINEURIOMA, NOS 9571/0 SOFT TISSUE TUMOR BENIGN 8800/0 SOLITARY FIBROUS TUMOR 8815/0 SUBEPENDYMAL GIANT CELL ASTROCYTOMA 9384/1 SUBEPENDYMOMA 9383/1 SUBEPENDYMOMA ASTROCYTOMA 9383/1 SUBEPENDYMOMA GLIOMA 9383/1 SYNCHYTIAL MENINGIOMA 9531/0 BENIGN 9080/0 TERATOMA NOS 9080/1 TRANSITIONAL MENINGIOMA 9537/0 TUMOR CELLS BENIGN 8000/0 TUMOR CELLS, BENIGN UNCERTAIN WHETHER BENIGN 8000/1 OR MALIGNANT VENOUS HEMANGIOMA 9122/0