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Index

A acral arteriovenous (cirsoid aneurysm) 256–7 ABCD (A:asymmetry; B:border; C:colour; D:diameter) acral lentiginous (ALM) 189, 194–6 rule 189 acral pseudolymphomatous of children Abrikossoff granular cell tumor 354 (APACHE) 269 acantholytic 26–7 acroangiodermatitis Mali (pseudo‐Kaposi’s ) 276–7 acantholytic (‐like) squamous cell acroasphyctic digitorum angiokeratoma (Mibelli) 267, 269 316–17 acrochordon 209–10 acantholytic SCC (epithelioma spinocellulare segregans of acrokeratosis verruciformis (Hopf) 37–8 Delacretaz) 74–6 acrolentiginous melanoma 206 acantholytic solar 16 acrospiroma, “eccrine” (misnomer) 97–8 acanthomas actinic solar keratoses 15–18 non‐viral 19–31 “activated” acral (lentiginous) melanocytic 161–2 acantholytic acanthoma 26–7 activated (irritated) 7 callus, factitial acanthoma 20–1 adenoid‐cystic basal cell carcinoma 62–3 knuckle pads (chewing pads) 21–2 adenoma sebaceum associated with Pringle–Bourneville large cell acanthoma 23–4 disease 319–21 pale (clear) cell acanthoma 22 adipophilin 117 porokeratoma (porokeratosis Mibelli) 30–1 adnexal structures 85–144 solar 19–20 hair follicle differentiation 119–43 27 benign 121–40 viral 31–9 pilar sheath acanthoma 121–2 acrokeratosis verruciformis (Hopf) 37 pilomatricoma (calcifying epithelioma 35–6 Malherbe) 137–8 molluscum contagiosum 38–9 proliferating trichilemmal (pilar) tumor (PTT) verruca vulgaris/variants 31–4 (proliferating trichilemmal cyst) 138–40 acanthosis nigricans 14–15 trichadenoma (Nikolowski) 136–7 acanthotic seborrheic keratosis 4 trichilemmoma (tricholemmoma) 122–3 accessory nipple 218 trichoblastoma (trichoblastic fibroma; immature accessory tragus 217 trichoepithelioma) 127–31 acquired fibrokeratoma 216 trichoepithelioma (sclerosing epithelial acquired immunodeficiency syndrome/human hamartoma) 131–3 immunodeficiency virus (AIDS/HIV) 273, trichoepithelioma (superficial 299, 303 trichoblastoma) 125–6 acquired melanocytic nevi, common 155–71 trichofolliculoma (folliculosebaceous cystic compound nevus 157–8 hamartoma) 133–5 dermal nevus, with maturation 158–60 tumor of the follicular infundibulum “activated” acral (lentiginous) 162–3 (infundibuloma) 124–5 ancient nevus 170–1 malignant neoplasms 140–3 balloon cell nevus 161 malignant pilomatricoma (pilomatrical combined nevus 167 carcinoma) 140–1 eczematoid melanocytic (Meyerson’s) nevus 165–6 trichilemmal carcinoma 141–2 genital melanocytic nevus COPYRIGHTED162–3 trichoblastic MATERIAL carcinoma 142–3 (leukoderma centrifugum acquisitum; nevi, hyperplasia, and hamartomas 119–21 Sutton nevus) 163–4 conical infundibular acanthoma (giant dilated pore Miescher’s nevus (dermal nevus) 160 of Winer) 120–1 nevus in pregnancy 168–9 pilosebaceous mesenchyme, benign neoplasms, osteo‐nevus of Nanta 166 trichodiscoma (follicular fibroma; recurrent (persistent) melanocytic nevus fibrofolliculoma; perifollicular () 167–8 fibroma) 143 junctional nevus 156 sebaceous differentiation 110–19 melanosis neviformis (pigmented hairy benign neoplasms 114–18 epidermal nevus) 155 Muir–Torre syndrome 115–16

Atlas of Dermatopathology: Tumors, Nevi, and Cysts, First Edition. Günter Burg, Heinz Kutzner, Werner Kempf, Josef Feit, and Bruce R. Smoller. © 2019 John Wiley & Sons Ltd. Published 2019 by John Wiley & Sons Ltd.

491

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adnexal structures (cont’d) angiohistiocytoma, multinucleate 318–19 sebaceous adenoma (NOT adenoma angioimmunoblastic T‐cell lymphoma 441–3 sebaceum) 114–15 264–9 sebaceous epithelioma (sebaceoma) 116–18 verrucous hemangioma (venous malformation) 265–9 hyperplasias and hamartomas 111–14 variant ectopic (heterotopic) sebaceous glands (Fordyce acral pseudolymphomatous angiokeratoma of glands) 111–12 children (APACHE) 269 (senile) sebaceous gland hyperplasia 112–13 angiokeratoma acroasphyctic digitorum variant: pilo‐sebaceous hamartoma 114 (Mibelli) 267, 269 malignant neoplasms 118–19 angiokeratoma circumscriptum naeviformis 267, 269 sebaceous carcinoma 118–19 Fordyce angiokeratoma 267, 269 sweat gland differentiation 86–110 multiple “pinpoint” angiokeratomas (angiokeratoma malignant adnexal neoplasms 105–10 corporis diffusum; Fabry’s disease) 267, 269 apocrine differentiation 108–10 solitary angiokeratoma 267–8 apocrine (hidr‐) (mucinous) 108–10 angioleiomyoma (angiomyoma; vascular leiomyoma) 294–5 eccrine differentiation 105–8 angiolipoleiomyoma (angiomyolipoma) 322 eccrine (mucinous) carcinoma 107–8 angiolipoma 321 microcystic adnexal carcinoma (syringomatous angiolymphoid hyperplasia with eosinophilia (ALHE) carcinoma; sclerosing sweat duct (epithelioid hemangioma) 278–9 carcinoma) 105–6 of oral mucosa 205, 206 porocarcinoma (malignant poroma) 106–7 angioma serpiginosum 250–1 nevi, hyperplasias and benign adnexal neoplasms angiomyolipoma (angiolipoleiomyoma) 322 (BAN) 86–105 angiomyoma (angioleiomyoma; vascular apocrine differentiation 93–105 leiomyoma) 294–5 anogenital mammary‐like gland 101–2 angiomyxoma 322–3 apocrine nevus 93–4 angiosarcoma, radiation‐induced 312 cylindroma (turban tumor) 100–1 anogenital and clonal Bowen’s disease 52 “eccrine” (misnomer) acrospiroma (nodular clear anogenital mammary‐like gland 101–2 cell hidradenoma; solid cystic anogenital pigmented and clonal Bowen’s disease 52 hidradenoma) 97–8 Antoni type B neuroid tissue 350 hydradenoma papilliferum (apocrine papillary APACHE (acral pseudolymphomatous angiokeratoma of cystadenoma) 102–3 children) 269 mixed tumor of the skin (chondroid syringoma) 94–5 apocrine cystadenoma 480–1 spiradenoma 99–100 apocrine (hidr‐) adenocarcinoma (mucinous) 108–10 syringocystadenoma papilliferum 103–5 apocrine nevus 93–4 tubular adenomas 95–7 apocrine papillary cystadenoma (hidradenoma eccrine differentiation 86–92 papilliferum) 102–3 eccrine syringofibroadenoma (Mascaro tumor) 87–8 appendages see adnexal structures poroma 89 APUDoma, cutaneous 360–2 variants arteriovenous malformations 256–9 common solid poroma 89 Asian people, Kimura’s disease 325 dermal duct tumor 89, 92 ATLL (adult T‐cell leukemia/lymphoma) 467–8 hidroacanthoma simplex 89, 90–1 atrophic solar keratosis 16 sweat gland nevus 86–7 atypical (dysplastic) melanocytic (Clark’s) nevus (B‐K mole syringoma (eruptive hidradenoma) 88–9 syndrome) 185–6 adult T‐cell leukemia/lymphoma (ATLL) 467–8 (AFX) and pleomorphic (dermal) AE1/AE3 positive tumor cells 105, 132 sarcoma (PDS) 231–4 AFX (atypical fibroxanthoma) 231–4 atypical lipomatous tumor (ALT) 333, 335 AIDS (acquired immunodeficiency syndrome) 273 atypical vascular lesion (AVL), radiation‐induced 308–9 AIDS/HIV (acquired immune deficiency syndrome/human immunodeficiency virus) 273, 299, 303 B AJCC staging classification 205 B‐cells ALCL (anaplastic large cell lymphoma) 424–5 centroblastic 391 ALHE (angiolymphoid hyperplasia with centrocytic 391 eosinophilia) 278–9 cutaneous mature B‐cell lymphoid neoplasms Alibert–Bazin see mycosis fungoides, classic Alibert–Bazin type (CBCL) 395–6, 443–60 ALM (acral lentiginous melanoma) 189, 194–6 cutaneous marginal zone B‐cell lymphoma alopecia, syringolymphoid hyperplasia with (syringotropic (MZL; MALT type) 444–9 mycosis fungoides) 414 differential diagnosis: multiple myeloma/ ALT (atypical lipomatous tumor) 333, 335 plasmacytoma 448–9 anaplastic large cell lymphoma (ALCL) 424–5 variant: immunocytoma 447–8 “ancient changes” 296 cutaneous spindle B‐cell lymphoma (BCL) 455–7 ancient (melanocytic) nevus 170–1 diffuse large B‐cell Lymphoma (DLBCL) 451–5 angioendotheliomatosis, systemic (intravascular large B‐cell variant: cutaneous diffuse large B‐cell lymphoma lymphoma) 461–2 (leg type) 451–4 (adenoma sebaceum associated with variant: T‐cell‐rich B‐cell lymphoma Pringle–Bourneville disease) 319–21 (DLBCL, NOS) 454–5

0004177441.INDD 492 8/9/2018 9:36:10 PM INDEX 493

extracutaneous B‐cell lymphoma (BCL) with frequent Borrelia burgdorferi 394, 447, 464 skin involvement 457–61 Borst–Jadassohn clonal (intraepidermal) seborrheic Burkitt’s lymphoma (BL) 458–9 keratosis 9, 91–2 lymphomatoid granulomatosis (Liebow) botryomykoma (lobular ) 270 (LYG) 460–1 bowenoid hypertrophic solar keratosis 18 mantle cell lymphoma 457–8 bowenoid papulosis 35–6 primary cutaneous follicle center lymphoma bowenoid seborrheic keratosis with monster cells 10 (FCL) 449–51 Bowen’s disease (carcinoma in situ) 48–54 cytomorphology, lymphoid skin infiltrates 391, 392–3 variants immunoblastic 391 clear cell Bowen’s disease 50–1 intravascular large B‐cell lymphoma (IV‐LBCL) cutaneous horn (cornu cutaneum) on Bowen’s (systemic angioendotheliomatosis) 461–2 disease 51–2 lymphoplasmacytoid 391 erythroplasia of Queyrat and vulvar intraepithelial pseudolymphoma (PSL) neoplasia 53–4 nodular B‐cell pseudolymphoma 393–6 pigmented (anogenital) and clonal Bowen’s disease 52 cutaneous B‐cell lymphoma (CBCL) pigmented basal cell carcinoma 205, 206 differentiation 395–6 BRAF mutations 189 lymphadenosis cutis benigna breast, ectopic 218 (lymphocytoma cutis) 393 Breslow depth 205 small lymphocytic 391 Brocq’s disease (parapsoriasis en plaques) 411 B‐K mole syndrome (atypical/dysplastic melanocytic Burkitt’s lymphoma (BL) 458–9 (Clark’s) nevus) 185–6 Buschke–Löwenstein tumor (giant condyloma) 41, 47–8 B‐pseudolymphoma (PL) 395–6 bacillary angiomatosis 273–4 C balloon cell melanoma 199–200 café‐au‐lait spot 151, 152 balloon cell nevus 161 calcifying epithelioma Malherbe (pilomatricoma) 137–8 BAN (benign adnexal neoplasms) 86–105 callus, factitial acanthoma 20–1 Bartonella “cannon‐ball” pattern 284 B. bacilliformis 273 capillary malformations 242–8 B. henselae 273 carcinoma B. quintana 273 see also basal cell carcinoma (BCC); Bowen’s basal cell carcinoma (BCC) disease (carcinoma in situ); squamous cell variants 52–72 carcinoma (SCC) adenoid‐cystic BCC 62–3 primary neuroendocrine (Merkel cell, trabecular) carcinoma clinical variants, ulcerating BCCs 66 of the skin (cutaneous APUDoma) 360–2 ductal, matrical or sebaceous differentiation 57–9 Carteaud and Gougerot, confluent and reticulate fibroepithelioma of Pinkus 70–2 papillomatosis 12 histological variants, metatypic BCC with squamoid (Maffucci syndrome) 252, 254 differentiation 67–8 CBCL (cutaneous B‐cell lymphoma) 395–6 infundibulocystic BCC 56 CD30+ lymphoproliferative disorders (LPD) of the nodular BCC 54–5 skin 423–30 pigmented BCC 61 CDK4 gene 335 sclerodermiform (morpheaform) BCC 64–5 cellular deep penetrating (neuro‐nevus) 173–7 superficial BCC 60 cellular neurothekeoma 357–8 syndromatic BCC (basal cell nevus syndrome, cerebriform T‐cells 390 Gorlin–Goltz) 69 (senile hemangioma) 281–2 Bazex–Dupré–Christol syndrome 69 chewing pads (knuckle pads) 21–2 BCC see basal cell carcinoma (BCC) children see pediatric conditions Bednar’s tumor 230 chloroacetate esterase (Leder) stain 465 benign adnexal neoplasms (BAN) 86–105 chondroid syringoma (mixed tumor of the skin) 94–5 benign lymphangiomatous papule (BLAP) 308–9 chronic lymphocytic leukemia (CLL) 463–4 Berti cutaneous aggressive epidermotropic CD8+ T‐cell circumscriptum naeviformis angiokeratoma 267, 269 lymphoma 436–7 cirsoid aneurysm (acral arteriovenous hemangioma) 256–7 Birt–Hogg–Dubé syndrome 143, 144 Clark’s atypical (dysplastic) melanocytic nevus (B‐K mole bizarre arborising slits 309 syndrome) 185–6 bizarre lymphatic spaces 304 classic Langerhans cell histiocytoses BL (Burkitt’s lymphoma) 458–9 eosinophilic granuloma 371, 375–6 black heel 205, 206 Hand–Schüller–Christian 371, 374–5 BLAP (benign lymphangiomatous papule) 308–9 Letterer–Siwe Langerhans cell histiocytosis 371 Blaschko line distribution 250 classification blastic plasmacytoid dendritic cell 468–9 angiolymphoid hyperplasia with eosinophilia (ALHE) 279 blood cells see hematopoietic disorders Kaposi’s sarcoma 298 blood vessels see vessels lymphatic vascular growths 259–60 Bloom’s syndrome (congenital telangiectatic erythema) 247–8 clear cell Bowen’s disease 50–1 blue nevi 171–7 clear cell hidradenoma, nodular 97–8 blue rubber bleb nevus syndrome (familial venous clear cell sarcoma (melanoma of soft parts) 203–4 malformation) 248–9 clear (pale) cell acanthoma 22

0004177441.INDD 493 8/9/2018 9:36:10 PM 494 INDEX

CLL (chronic lymphocytic leukemia) 463–4 CTCL see cutaneous mature T‐cell lymphoid clonal Bowen’s disease 52 neoplasms (CTCL) clonal (intraepidermal) seborrheic keratosis cutaneous aggressive epidermotropic CD8+ T‐cell (Borst–Jadassohn) 9, 91–2 lymphoma (Berti) 436–7 clonal proliferation, melanocytic nevus with 183–4 cutaneous angiosarcoma 309–11 cobblestone nevus 208–9 cutaneous B‐cell lymphoma (CBCL) 395–6 combined (melanocytic) nevus 167 cutaneous ciliated cyst of the lower limb 485–6 common blue nevus 171–2 cutaneous cysts 471–90 common lipoma and lipomatosis 329 with epithelial lining 472–86 common nevus of Spitz 178–9 non‐stratified squamous epithelium 485–7 common solid poroma 89 cutaneous ciliated cyst of the lower limb 485–6 composite 306 median raphe cyst 486–7 compound (acquired melanocytic) nevus 157–8 stratified squamous epithelium 472–85 compound melanocytic nevus 157–8 dermoid cyst 482–3 condyloma acuminatum 34 epidermal (infundibular) cysts 472–3 condyloma, giant (Buschke–Löwenstein tumor) 41, 47–8 variant confluent and reticulate papillomatosis (Gougerot and epidermal cyst with pigment and vellus hairs 473 Carteaud) 12 epidermal proliferating cyst 473 congenital conditions follicular hybrid cyst 477–8 ichthyosiform erythroderma 25–6 hidrocystoma (cystadenoma) 478 Langerhans cell histiocytosis (Letterer–Siwe disease) 371 variants nevi apocrine cystadenoma 480–1 benign small/medium‐sized 186–8 eccrine cystadenoma 478–8 malignant melanoma in large congenital melanocytic milia 476–7 nevus (LCMN) 196–7 pilonidal sinus/cyst 484–5 self‐healing reticulohistiocytosis steatocystoma, multiplex/simplex 481–2 (Hashimoto–Pritzker) 370 trichilemmal (isthmus‐catagen) cyst 475–6 telangiectatic erythema (Bloom’s syndrome) 247–8 vellus hair cyst 474–5 conical infundibular acanthoma (giant dilated pore of without epithelial lining (pseudocysts) Winer) 120–1 digital myxoid cyst 488–9 conjunctival malignant melanoma 204 oral mucous cyst and superficial mucocele of the lip 487–8 connective tissue 206–38 synovial cyst (ganglion) 490 fibrohistiocytic neoplasms 218–34 cutaneous diffuse large B‐cell lymphoma (leg type) 451–4 atypical fibroxanthoma (AFX) and pleomorphic cutaneous horn (cornu cutaneum) 18–19 (dermal) sarcoma (PDS) 231–4 on Bowen’s disease 51–2 218–27 cutaneous liposarcoma 333–6 dermatofibrosarcoma protuberans 227–30 cutaneous marginal zone B‐cell lymphoma (MZL; MALT variants type) 444–9 giant cell fibroblastoma 231 cutaneous mastocytoma 364–5 pigmented dermatofibrosarcoma protuberans cutaneous mature B‐cell lymphoid neoplasms (CBCL) 443–60 (Bednar’s tumor) 230 cutaneous marginal zone B‐cell lymphoma fibrous neoplasms 209–15 (MZL; MALT type) 444–9 infantile digital fibromatosis 214–15 cutaneous spindle B‐cell lymphoma 455–7 keloid 213–14 extracutaneous B‐cell lymphoma (BCL) with frequent perifollicular fibroma 210–11 skin involvement 457–61 soft fibroma (/acrochordon) 209–10 primary cutaneous follicle center lymphoma variants (FCL) 449–51 fibrous papule of the nose 212 cutaneous mature T‐cell lymphoid neoplasms pleomorphic sclerosing fibroma with multinucleated (CTCL) 405–41 cells 212–13 CD30+ lymphoproliferative disorders (LPD) of the sclerotic fibroma 211–12 skin 423–30 malformations with supernumerary tissue extranodal NK/T‐cell lymphoma, nasal type elements 216–18 (subcutaneous) 439–43 accessory nipple (ectopic breast/polythelia) 218 granulomatous slack skin 415–17 accessory tragus (preauricular tag) 217 mycosis fungoides, classic Alibert–Bazin type 405–11 acquired fibrokeratoma 216 pagetoid reticulosis (PR), unilesional supernumerary digit 216 (Woringer–Kolopp) 417–18 miscellaneous tumors 234–7 primary cutaneous peripheral lymphoma (PTL), dermatomyofibroma 236–7 unspecified (NOS) 434–8 epithelioid sarcoma 234–6 Sézary syndrome 418–20 nevi, connective tissue nevi 208–9 Sézary syndrome variant: Sézary syndrome, large cell contact dermatitis, lymphomatoid 399 transformation 420–3 cornu cutaneum 18–19 simulators and variants of mycosis fungoides: on Bowen’s disease 51–2 “parapsoriasis” 411–15 Cowden’s disease 123 subcutaneous panniculitis‐like lymphoma 431–4

0004177441.INDD 494 8/9/2018 9:36:10 PM INDEX 495

cutaneous metastasis of melanoma 197–8 DMM (desmoplastic malignant melanoma) 200–2 cutaneous (primary) follicle center lymphoma (FCL) 449–51 DNA mismatch repair proteins 116 cutaneous primary peripheral lymphoma, Dowling–Degos disease 13–14 unspecified 434–8 drug reactions causing pseudomycosis fungoides 400 cutaneous spindle B‐cell lymphoma 455–7 Dubreuilh, (Hutchinson’s freckle) 188–9 cutis marmorata telangiectatica (van Lohuizen) (nevus ductal basal cell carcinoma differentiation 57–9 vascularis reticularis) 245–6 dumb‐bell histological pattern, blue nevus 174 cylindroma (turban tumor) 100–1 Dutcher bodies 447 cystadenoma see hidrocystoma (cystadenoma) cystic hygroma 259–60 E cysts see cutaneous cysts EC (epithelioma cuniculatum) 44–5 cytomorphology, lymphoid cell types 390–1 eccrine angiomatous hamartoma 241–2 eccrine cystadenoma 478–80 D “eccrine” (misnomer) acrospiroma (nodular clear cell Dabska tumor (malignant endovascular papillary hidradenoma; solid cystic hidradenoma) 97–8 angioendothelioma) 306–8 eccrine (mucinous) carcinoma 107–8 “Dabskoid tufts” of hobnail endothelial cells 308 eccrine syringofibroadenoma (Mascaro tumor) 87–8 Darier’s disease 28 ectopic breast 218 “deck‐chair” sign 419 ectopic (heterotopic) sebaceous glands (Fordyce glands) 111–12 Delacretaz, epithelioma spinocellulare segregans 74–5 eczematoid melanocytic (Meyerson’s) nevus 165–6 dendritic cells emperipolesis 416 blastic plasmacytoid dendritic cell neoplasm 468–9 endothelial differentiation CD21+ follicular 394, 395 vessels dermal duct tumor 89, 92 benign vascular neoplasms dermal melanocytic nevus, with maturation 158–60 cherry angioma (senile hemangioma) 281–2 variant glomeruloid hemangioma in POEMS “activated” acral (lentiginous) melanocytic syndrome 287–8 nevus 161–2 infantile capillary and congenital ancient nevus 170–1 hemangioma 280–1 balloon cell nevus 161 kaposiform hemangioendothelioma 285–7 combined nevus 167 microvenular (microcapillary) hemangioma 282–3 eczematoid melanocytic (Meyerson’s) nevus 165–6 tufted angioma 283–4 genital melanocytic nevus 162–3 endovascular papillary hemangioendothelioma (papillary halo nevus (leukoderma centrifugum acquisitum; intralymphatic angioendothelioma, PILA; Sutton nevus) 163–4 malignant endovascular papillary Miescher’s nevus (dermal nevus) 160 angioendothelioma; Dabska tumor) 306–8 osteo‐nevus of Nanta 166 eosinophilic granuloma 371, 375–6 recurrent (persistent) melanocytic nevus epidermis 1–83 (pseudomelanoma) 167–8 acanthomas dermal melanocytosis 177–8 non‐viral 19–31 dermal nerve sheath myxoma (myxoid acantholytic acanthoma 26–7 neurothekeoma) 356–7 callus, factitial acanthoma 20–1 dermatitis congenital ichthyosiform erythroderma 25–6 acroangiodermatitis Mali (pseudo‐Kaposi’s knuckle pads 21–2 sarcoma) 276–7 large cell acanthoma 23–4 lymphomatoid contact dermatitis 399 differential diagnosis: epidermolytic pigmented purpuric dermatitis (lichen aureus) 402, 403–4 acanthoma 24–5 pseudo‐Kaposi’s sarcoma (acroangiodermatitis Mali) 276–7 pale (clear) cell acanthoma 22 dermatofibroma 218–27 porokeratosis Mibelli (porokeratoma) 30–1 dermatofibrosarcoma protuberans 227–30 warty dyskeratoma 27–9 dermatomyofibroma 236–7 viral 31–9 dermatosis papulosa nigra 7 acrokeratosis verruciformis (Hopf) 37–8 dermoid cyst 482–3 bowenoid papulosis 35–6 desmoplastic malignant melanoma (DMM) 200–2 molluscum contagiosum 38–9 diffuse cutaneous mast cell proliferations 365–6 verruca plana 33–4 diffuse growth patterns, lymphoid skin infiltrates 389 variant: condyloma acuminatum 34 diffuse large B‐cell lymphoma (DLBCL) 451–5 verruca vulgaris 31–3 digit, rudimentary 216, 353 epidermal cyst with pigment and vellus hairs 473 digit, supernumerary 216 epidermal proliferating cyst 473 digital myxoid cyst 488–9 (infundibular) cysts 472–3 digital recurring fibromatous tumor of children 214–15 keratoses 4–18 digitate dermatosis (small plaque parapsoriasis) 411 acanthosis nigricans 14–15 disseminated Ketron and Goodman type of Sézary acanthotic seborrheic keratosis 4 syndrome 418 activated (irritated) seborrheic keratosis 7 DLBCL (diffuse large B‐cell lymphoma) 451–5 atrophic solar keratosis 16

0004177441.INDD 495 8/9/2018 9:36:10 PM 496 INDEX

epidermis (cont’d) 24–5 Borst–Jadassohn clonal (intraepidermal) seborrheic epithelial lining, cutaneous cysts 472–86 keratosis 9, 91–2 epithelioid and/or spindle cell nevus 178–83 bowenoid hypertrophic solar keratosis 18 epithelioid angiosarcoma 315 bowenoid seborrheic keratosis with monster cells 10 epithelioid hemangioendothelioma 312–14 confluent and reticulate papillomatosis (Gougerot epithelioid hemangioma (angiolymphoid hyperplasia with and Carteaud) 12 eosinophilia, ALHE) 278–9 cornu cutaneum 18–19 epithelioid sarcoma 234–6 flat seborrheic keratosis 6 epithelioma cuniculatum () hyperkeratotic seborrheic keratosis 11 (EC/EV) 44–5 lichen planus‐like solar keratosis 17 epithelioma spinocellulare segregans of Delacretaz 74–5 melanoacanthoma (pigmented seborrheic keratosis) 8 Epstein–Barr virus (EBV) 459, 460 reticulate pigmented anomaly of the flexures eruptive hidradenoma (syringoma) 88–9 (Dowling–Degos disease) 13–14 erythrodermic mycosis fungoides 412–13 solar actinic keratoses 15–18 erythroplasia of Queyrat and vulvar intraepithelial variants neoplasia 53–4 acantholytic solar keratosis 16 estrogen receptors, stained 101 atrophic solar keratosis 16 ephelides (genuine freckles) 150 hypertrophic (bowenoid) solar keratosis 18 EV (epithelioma verrucous) 44 lichen planus‐like solar keratosis 17 extracutaneous B‐cell lymphoma (BCL) with frequent skin malignant epidermal neoplasms 48–84 involvement 457–61 basal cell carcinoma variants 52–72 extramammary Paget’s disease 146–8 adenoid‐cystic basal cell carcinoma 62–3 extranodal NK/T‐cell lymphoma, nasal type (subcutaneous) ductal, matrical or sebaceous differentiation 57–9 439–43 fibroepithelioma of Pinkus 70–2 infundibulocystic basal cell carcinoma 56 F metatypic basal cell carcinoma with squamoid Fabry’s disease (angiokeratoma corporis diffusum) 267, 269 differentiation 67–8 familial hemophagocytic lymphohistiocytosis 387–8 nodular basal cell carcinoma 54–6 familial venous malformation (blue rubber bleb nevus pigmented basal cell carcinoma 61 syndrome) 248–9 sclerodermiform (morpheaform) basal cell fat carcinoma 64–5 angiolipoleiomyoma (angiomyolipoma) 322 superficial basal cell carcinoma 60 angiolipoma 321 syndromatic basal cell carcinoma (basal cell nevus benign neoplasms 329–33 syndrome, Gorlin–Goltz) 69 common lipoma and lipomatosis 329 ulcerating basal cell carcinoma 66 (brown fat) 332–3 Bowen’s disease (carcinoma in situ) variants 48–54 332 clear cell Bowen’s disease 50–1 spindle cell lipoma 330–1 cutaneous horn (cornu cutaneum) 51–2 lipoid dermatoarthritis 378–9 erythroplasia of Queyrat and vulvar intraepithelial malignant neoplasms 333–6 neoplasia 53–4 atypical lipomatous tumor (ALT) 333, 335 pigmented (anogenital) and clonal Bowen’s disease 52 cutaneous liposarcoma 333–6 /variants 72–83 nevus (hamartoma) 328–9 acantholytic SCC (epithelioma spinocellulare pleomorphic lipoma 332 segregans of Delacretaz) 74–6 FCL (primary cutaneous follicle center lymphoma) 449–51 follicular (infundibular) squamous cell febrile ulceronecrotic PLEVA (Mucha–Habermann disease) carcinoma 77–8 437–8 myxoid squamous cell carcinoma 76–7 fibroepithelioma of Pinkus 70–2 special sites 79–84 fibrofolliculoma (trichodiscoma) 143, 210–11 spindle cell (fusicellular) squamous cell fibrohistiocytic neoplasms 218–34 carcinoma 78–9 fibroma durum 218–27 well‐differentiated squamous cell carcinoma 72–4 fibrous neoplasms 209–15 nevi 2–3 fibrous papule of the nose 12, 212 inflammatory linear verrucous epidermal nevus “firing papillae” 422 (ILVEN) 3–4 flat seborrheic keratosis 6 pigmented hairy (melanosis neviformis) 155 florid papillomatosis of the oral cavity (oral verrucous “pseudocarcinomas” and neoplasms with intermediate carcinoma) 46 malignant potential 40–8 “flower cells” in peripheral blood 467, 468 Buschke–Löwenstein tumor (giant condyloma) follicle center lymphoma (FCL), cutaneous primary 449–51 41, 47–8 follicular fibroma (trichodiscoma) 143 epithelioma cuniculatum (verrucous carcinoma) follicular hybrid cyst 477–8 (EC/EV) 44–5 follicular (infundibular) squamous cell carcinoma 77–8 florid papillomatosis of the oral cavity (oral verrucous follicular infundibulum, tumor of the carcinoma) 46 (infundibuloma) 124–5 (KA) 40–4 folliculosebaceous cystic hamartoma papillomatosis cutis carcinoides 45–6 (trichofolliculoma) 133–5

0004177441.INDD 496 8/9/2018 9:36:10 PM INDEX 497

folliculotropic (pilotropic) mycosis fungoides 413–14 trichoblastoma (trichoblastic fibroma; immature Fordyce angiokeratoma 267, 269 trichoepithelioma) 127–31 Fordyce glands (ectopic (heterotopic) sebaceous trichoepithelioma (sclerosing epithelial glands) 111–12 hamartoma) 131–3 freckles trichoepithelioma (superficial trichoblastoma) 125–6 genuine 150 trichofolliculoma (folliculosebaceous cystic Hutchinson’s 188–9 hamartoma) 133–5 senile 153–4 malignant neoplasms 140–3 fumarate hydratase deficiency 339, 340 malignant pilomatricoma (pilomatrical carcinoma) 140–1 fusicellular (spindle cell) squamous cell carcinoma 78–9 trichilemmal carcinoma 141–2 trichoblastic carcinoma 142–3 G nevi, hyperplasia, and hamartomas 119–21 ganglion (synovial cyst) 490 conical infundibular acanthoma (giant dilated pore genital mucosal lentiginous spots 154–5 of Winer) 120–1 giant cell fibroblastoma 231 hairy epidermal nevus, pigmented (melanosis giant condyloma (Buschke–Löwenstein tumor) 41, 47–8 neviformis) 155 giant dilated pore of Winer (conical infundibular halo nevus (leukoderma centrifugum acquisitum; Sutton acanthoma) 120–1 nevus) 163–4 glans penis squamous cell carcinoma 83 “haloed” atypical intraepidermal lymphocytes 406 “glomangioma” (glomuvenular malformation) 257–9 hamartomas, nevi, and malformations glomangiosarcoma (malignant ) 317–18 adnexal structures 119–21 glomeruloid hemangioma in POEMS syndrome 287–8 hair follicle differentiation 119–21 glomoid/myoid differentiation in benign vascular pilo‐sebaceous 114 neoplasms 292–5 sebaceous differentiation 111–14 glomulin gene 293 fat 328–9 glomus tumor iris of eye 346 benign 292–4 trichoepithelioma 131–3 malignant (glomangiosarcoma) 317–18 trichofolliculoma 133–5 glomuvenular malformation (“glomangioma”) 257–9 vessels 240–2 GNAQ/KRAS genes mutational testing 189 eccrine angiomatous 241–2 Gorlin–Goltz basal cell nevus syndrome 69 nevus anemicus 242 Gougerot and Carteaud confluent and reticulate phacomatosis pigmentovascularis 240 papillomatosis 12 Hand–Schüller–Christian adult Langerhans cell Goya, Francisco de, seborrheic keratosis 91 histiocytosis 371, 374–5 graft versus host disease (acute) 401 Hashimoto–Pritzker congenital self‐healing granular cell tumor (Abrikossoff) 354–5 reticulohistiocytosis 370 granular cell tumor, malignant 360 Helicobacter pylori 447 granulation tissue, vessel hyperplasia, pyogenic hemangioendothelioma composite 306 granuloma‐like 272 hematopoietic disorders 389–470 granuloma pyogenicum (lobular capillary hemangioma; cutaneous mature B‐cell lymphoid neoplasms botryomykoma) 270 (CBCL) 443–60 granulomatous mycosis fungoides 415 cutaneous marginal zone B‐cell lymphoma granulomatous slack skin 415–17 (MZL; MALT type) 444–9 granulomatous storing NLHC histiocytoses variant: immunocytoma 447–8 juvenile xanthogranuloma 380–1 differential diagnosis: multiple myeloma/ verruciform xanthoma 384–5 plasmacytoma 448–9 xanthelasma 381–2 cutaneous spindle B‐cell lymphoma 455–7 xanthelasma palpebrarum 383 diffuse large B‐cell lymphoma (DLBCL) 451–5 xanthoma disseminatum 381–2 variants grenz‐zone 450, 451 cutaneous diffuse large B‐cell lymphoma (leg Grocott stain 274 type) 451–4 T‐cell‐rich B‐cell lymphoma (DLBCL, NOS) 454–5 H extracutaneous B‐cell lymphoma (BCL) with frequent H3K27me3 expression 187 skin involvement 457–61 “hair blower” pattern 264 Burkitt’s lymphoma (BL) 458–9 hair follicle differentiation 119–43 lymphatoid granulomatosis (Liebow) (LYG) 460–1 benign neoplasms 121–40 mantle cell lymphoma 457–8 infundibuloma (tumor of the follicular primary cutaneous follicle center lymphoma infundibulum) 124–5 (FCL) 449–51 pilar sheath acanthoma 121–2 cutaneous mature T‐cell lymphoid neoplasms pilomatricoma (calcifying epithelioma Malherbe) (CTCL) 405–41 137–8 CD30+ lymphoproliferative disorders of the skin 423–30 proliferating trichilemmal (pilar) tumor (PTT) anaplastic large cell lymphoma (ALCL) 424–5 (proliferating trichilemmal cyst) 138–40 differential diagnosis: Hodgkin’s lymphoma; trichilemmoma (tricholemmoma) 122–3 lymphocyte predominance 429–30 trichoadenoma (Nikolowski) 136–7 lymphomatoid papulosis 427–9

0004177441.INDD 497 8/9/2018 9:36:10 PM 498 INDEX

hematopoietic disorders (cont’d) early vitiligo 400 neutrophil‐rich (pyogenic) anaplastic large cell graft versus host reaction (acute) 401 lymphoma 426–7 lichen planus 399 extranodal NK/T‐cell lymphoma, nasal type lichen sclerosus et atrophicus 400–1 (subcutaneous) 439–43 lymphocytic infiltration Jessner–Kanof 404–5 angioimmunoblastic T‐cell lymphoma 441–3 lymphomatoid contact dermatitis 399 hydroa vacciniforme‐like lymphoma 440–1 pigmented purpuric dermatitis (lichen aureus) 403–4 granulomatous slack skin 415–17 pityriasis lichenoides chronica 401 mycosis fungoides, classic Alibert–Bazin type 405–11 pityriasis lichenoides et varioliformis acuta large cell transformation 410 (PLEVA) 402 patch stage 405 secondary skin involvement in leukemias/ plaque stage 407–8 lymphomas 463–8 tumor stage 409–10 adult T‐cell leukemia/lymphoma (ATLL) 467–8 variant: CD8+ mycosis fungoides 409 chronic lymphocytic leukemia (CLL) 463–4 pagetoid reticulosis (PR), unilesional (Woringer– myeloid and monocytic leukemias 464–5 Kolopp) 417–18 T‐zone lymphoma 466–7 primary cutaneous peripheral lymphoma (PTL), hemophagocytic NLHC histiocytoses unspecified (NOS) 434–8 familial hemophagocytic lymphohistiocytosis 387–8 cutaneous aggressive epidermotropic CD8+ T‐cell histiocytic cytophagic panniculitis 388 lymphoma (Berti) 436–7 hereditary hemorrhagic telangiectasia differential diagnosis: febrile ulceronecrotic PLEVA (Osler–Weber–Rendu) 249–50 (Mucha–Habermann disease) 437–8 hereditary progressive mucinous histiocytosis 386–7 primary cutaneous CD4+ (acral) small/medium‐sized heterotopic (ectopic) sebaceous glands (Fordyce T‐cell lymphoproliferative disorder 435–6 glands) 111–12 Sézary syndrome 418–20 hibernoma (brown fat) 332–3 variant: Sézary syndrome large cell hidradenocarcinoma (apocrine, mucinous) 108–10 transformation 420–3 hidradenoma papilliferum (apocrine papillary simulators and variants of mycosis fungoides 411–15 cystadenoma) 102–3 erythrodermic mycosis fungoides 412–13 hidradenoma, solid cystic 97–8 folliculotropic (pilotropic) mycosis fungoides 413–14 hidroacanthoma simplex 89, 90–1 granulomatous mycosis fungoides 415 hidrocystoma (cystadenoma) 478 large plaque parapsoriasis (LPP) 412 variants “parapsoriasis” 411 apocrine cystadenoma 480–1 pigmented purpuric mycosis fungoides 412 eccrine cystadenoma 478–80 small plaque parapsoriasis (SPP) (digitate histiocytes dermatosis) 411 intralymphatic histiocytosis 324 syringotropic mycosis fungoiodes (syringolymphoid Langerhans cell (LHC) histiocytoses hyperplasia with alopecia) 414 classic LHC histiocytoses 371–6 subcutaneous panniculitis‐like lymphoma 431–4 precursors of LHC 370–1 differential diagnosis: lupus panniculitis (lupus non‐Langerhans cell (NLHC) histiocytoses profundus) 433–4 granulomatous storing 380–7 differential diagnosis: subcutaneous (panniculitis‐ hemophagocytic 387–8 like) gamma/delta lymphoma 432–3 proliferative 376–80 subcutaneous (panniculitis‐like; alpha/beta) T‐cell histiocytic cytophagic panniculitis 388 lymphoma 431–2 histological metatypical BCC variants with squamoid immature hematopoietic 468–9 differentiation 67–8 blastic plasmacytoid dendritic cell neoplasm 468–9 HIV/AIDS (human immunodeficiency virus/acquired immune intravascular lymphomas 461–3 deficiency syndrome) 273, 299, 303 intravscular large B‐cell lymphoma (IV‐LBCL) HMB45 positive cells 198, 202 (systemic angioendotheliomatosis) 461–2 hobnail targetoid hemosiderotic hemangioma 261–2 intravascular T‐cell lymphoma 462–3 Hodgkin’s lymphoma 429–30 lymphoid skin infiltrates 389–93 Hopf acrokeratosis verruciformis 37–8 cytomorphology 390–1 “horn pearls” histological appearance 68 pattern of small lymphocytic infiltrates 392–3 HTLV‐1 (human T‐cell leukemia virus‐1) 468 precursor lymphoblastic leukemia/lymphoma 470 human immunodeficiency virus/acquired immune deficiency pseudolymphoma (PL) 393–405 syndrome (HIV/AIDS) 273, 299, 303 nodular B‐cell PSL 393–6 human T‐cell leukemia virus‐1 (HTLV‐1) 468 differentiation between B‐pseudolymphoma (PL) and Hutchinson’s freckle 188–9 cutaneous B‐cell lymphoma (CBCL) 395–6 “hyaline globi” 302 lymphadenosis cutis benigna (lymphocytoma hydroa vacciniforme‐like lymphoma 440–1 cutis) 393 hyperkeratotic seborrheic keratosis 11 nodular T‐cell PL 396–9 hyperpigmentations see melanocytes papular (secondary) syphilis 398–9 hyperplasias, vessels tick bite CD30+ pseudolymphoma 396–8 acroangiodermatitis Mali (pseudo‐Kaposi’s sarcoma) 276–7 pseudo‐mycosis fungoides (mycosis fungoides bacillary angiomatosis 273–4 simulators) 399–405 granuloma pyogenicum (lobular capillary drug reactions 400 hemangioma; botryomykoma) 270

0004177441.INDD 498 8/9/2018 9:36:10 PM INDEX 499

intravascular papillary endothelial hyperplasia Kaposi’s sarcoma (KS) (Masson) 275–6 pseudo‐Kaposi’s sarcoma (acroangiodermatitis Mali) 276–7 verruga peruana 274–5 vascular 298–305 hypertrophic (bowenoid) solar keratosis 18 Kasabach–Merritt syndrome 285 keloid fibrous neoplasm 213–14 I keratoacanthoma (KA) 40–4 ILVEN (inflammatory linear verrucous epidermal keratoses nevus) 3–4 acanthosis nigricans 14–15 immature hematopoietic malignancies 468–9 confluent and reticulate papillomatosis (Gougerot and immunocytoma variant of cutaneous marginal zone B‐cell Carteaud) 12 lymphoma (MZL; MALT type) 447–8 reticulate pigmented anomaly of the flexures inclusion body fibromatosis 214–15 (Dowling–Degos disease) 13–14 indeterminate cell histiocytosis 371 seborrheic keratoses 4–18 “Indian file” growth pattern 394, 456, 465 solar (actinic) keratosis infantile capillary and congenital hemangioma 280–1 variants infantile digital fibromatosis 214–15 acantholytic solar keratosis 16 infantile myofibromatosis (perivascular myoma, incl. atrophic solar keratosis 16 myofibroma) 290–2 hypertrophic (bowenoid) solar keratosis 18 inflammatory linear verrucous epidermal nevus (ILVEN) 3–4 lichen planus‐like solar keratosis 17 infundibular (epidermal) cyst 472–3 Ketron and Goodman disseminated type 418 infundibular (follicular) squamous cell carcinoma 77–8 Ki67/MIB‐1 positive tumor cells 431 infundibulocystic basal cell carcinoma 56 Kimura’s disease 325–6 infundibuloma (benign tumor of the follicular Klippel–Trenaunay syndrome 254 infundibulum) 124–5 knuckle pads (chewing pads) 21–2 “ink” spot lentigo (reticulated melanocytic macule) 151, 152 KRAS/GNAQ genes mutational testing 189 intermediate malignant potential “pseudocarcinomas” 40–8 L vascular neoplasms 298–309 labia, mucosal lentiginous spots 154–5 Kaposi’s sarcoma (KS) 298–305 Langerhans cell (LHC) histiocytoses papillary intralymphatic angioendothelioma (PILA) classic LHC histiocytoses 371–6 (malignant endovascular eosinophilic granuloma 371, 375–6 papillaryangioendothelioma, Dabska tumor; Hand–Schüller–Christian 371, 374–5 endovascular papillary Letterer–Siwe LHC histiocytosis 371 hemangioendothelioma) 306–8 precursors of LHC histiocytoses 370–1 radiation‐induced atypical vascular lesion (AVL) congenital self‐healing reticulohistiocytosis 370 (benign lymphangiomatous papule indeterminate cell histiocytosis 371 (BLAP)) 308–9 large cell acanthoma 23–4 retiform hemangioendothelioma 305–6 large plaque parapsoriasis (LPP) 412 interstitial growth, lymphoid skin infiltrates 389 “lasagne pattern” 255 intraepidermal clonal seborrheic keratosis Launois–Bensaude syndrome 330 (Borst–Jadassohn) 9, 91–2 LCMN (melanoma in large congenital melanocytic intralymphatic histiocytosis 324 nevus) 196–7 intravascular large B‐cell lymphoma (IV‐LBCL) (systemic Leder (chloroacetate esterase) stain 465 angioendotheliomatosis) 461–2 leiomyosarcoma, superficial 342–3 intravascular papillary endothelial hyperplasia lentigo maligna Dubreuilh (Hutchinson’s freckle) 188–9 (Masson) 275–6 (LMM) 189, 192 intravascular T‐cell lymphoma 462–3 Letterer–Siwe Langerhans cell histiocytosis 371 iris hamartomas 346 leukemias irritated (activated) seborrheic keratosis 7 adult T‐cell leukemia/lymphoma (ATLL) 467–8 isthmus‐catagen (trichilemmal) cyst 475–6 chronic lymphocytic leukemia (CLL) 463–4 Ito (Ota) nevus fuscoceruleus (Mongolian spot) 177–8 myeloid and monocytic leukemias 464–5 IV‐LBCL (intravascular large B‐cell lymphoma) precursor lymphoblastic leukemia/lymphoma 470 (systemic angioendotheliomatosis) 461–2 secondary skin involvement 463–8 Ixodes ricinus 394 leukoderma centrifugum acquisitum (Sutton nevus) 163–4 LHC see Langerhans cell (LHC) histiocytoses J lichen aureus (pigmented purpuric dermatitis) 403–4 Jacob’s ulcus rodens 66 lichen planus 399 Jessner–Kanof lymphocytic infiltration 404–5 lichen planus‐like solar keratosis 17 junctional melanocytic nevus 156 lichen sclerosus et atrophicus 400–1 juvenile giant cell granuloma 380–1 Liebow lymphatoid granulomatosis (LYG) 460–1 juvenile maculopapular mastocytosis 365–6 lipoid dermatoarthritis 378–9 juvenile xanthogranuloma 380–1 Lisch nodules 346 LMM (lentigo maligna melanoma) 189, 192 K lobular capillary hemangioma (botryomykoma) 270 Kamino bodies 180 lower limb kaposiform hemangioendothelioma 285–7 see also leg kaposiform zones 255 cutaneous ciliated cyst 485–6

0004177441.INDD 499 8/9/2018 9:36:10 PM 500 INDEX

LPP (large plaque parapsoriasis) 412 malignant endovascular papillary angioendothelioma, lupus panniculitis (lupus profundus) 433–4 Dabska tumor (papillary intralymphatic LYG (lymphatoid granulomatosis) (Liebow) 460–1 angioendothelioma, PILA) 306–8 lymphadenosis cutis benigna (lymphocytoma cutis) 393 malignant epidermal neoplasms 48–84 lymphangiomatosis 263–4 basal cell carcinoma/variants 52–72 lymphatic malformations 259–64 Bowen’s disease 48–54 lymphangiomatosis 263–4 squamous cell carcinoma/variants 72–84 progressive (benign malignant fat neoplasms 333–6 lymphangioendothelioma) 262–3 malignant glomus tumor (glomangiosarcoma) 317–18 superficial (superficial lymphangioma) and deep malignant granular cell tumor 360 (cystic hygroma) lymphatic malignant immature hematopoietic conditions 468–9 malformations 259–60 malignant melanocytic neoplasms 188–206 targetoid hemosiderotic (hobnail) hemangioma 261–2 see also malignant melanoma lymphatoid granulomatosis (Liebow) (LYG) 460–1 lentigo maligna Dubreuilh (Hutchinson’s freckle) 188–9 lymphocytic infiltration Jessner–Kanof 404–5 malignant melanoma 189–206 lymphocytoma cutis (lymphadenosis cutis benigna) 393 differential diagnoses 205–6 lymphoid skin infiltrates 389–93 special histological features 198 lymphoma special localizations 204 adult T‐cell leukemia/lymphoma (ATLL) 467–8 tumor thickness/levels 205 anaplastic large cell lymphoma 424–5 variants angioimmunoblastic T‐cell lymphoma 441–3 acral lentiginous melanoma (ALM) 189, 194–6 Burkitt’s lymphoma (BL) 458–9 balloon cell melanoma 199–200 cutaneous cutaneous metastasis of melanoma 197–8 aggressive epidermotropic CD8+ T‐cell lymphoma desmoplastic malignant melanoma (DMM) 200–2 (Berti) 436–7 lentigo maligna melanoma (LMM) 189, 192 B‐cell lymphoma (CBCL) 395–6 melanoma in large congenital nevus (LCMN) 196–7 diffuse large B‐cell lymphoma (leg type) 451–4 (NM) 189, 193 marginal zone B‐cell lymphoma (MZL; MALT superficial spreading melanoma (SSM) 189–91 type) 444–9 malignant peripheral nerve sheath tumor (malignant primary cutaneous follicle center lymphoma schwannoma) 358–9 (FCL) 449–51 malignant pilomatricoma (pilomatrical carcinoma) 140–1 primary cutaneous peripheral lymphoma malignant potential (PTL), unspecified (NOS) 434–8 high, vessel neoplasms 309–18 spindle B‐cell lymphoma 455–7 intermediate, “pseudocarcinomas” 40–6 diffuse large B‐cell lymphoma (DLBCL) 451–5 MALT type cutaneous marginal zone B‐cell lymphoma extracutaneous B‐cell lymphoma with frequent skin (MZL) 444–9 involvement 457–61 mammary Paget’s disease 146–8 hydroa vacciniforme‐like lymphoma 440–1 mammary‐like gland, anogenital 101–2 intravascular large B‐cell lymphoma (IV‐LBCL) (systemic mantle cell lymphoma 457–8 angioendotheliomatosis) 461–2 Mascaro tumor (eccrine syringofibroadenoma) 87–8 intravascular T‐cell lymphoma 462–3 Masson intravascular papillary endothelial hyperplasia 275–6 mantle cell lymphoma 457–8 mast cells 363–8 neutrophil‐rich (pyogenic) anaplastic large cell diffuse cutaneous mast cell proliferations 365–6 lymphoma 426–7 solitary cutaneous mast cell proliferation 364–5 precursor lymphoblastic leukemia/lymphoma 470 systemic mast cell proliferation 367–8 secondary skin involvement 463–8 telangiectasia macularis eruptiva perstans (adults) 366–7 subcutaneous urticaria pigmentosa (juvenile maculopapular (panniculitis‐like; alpha/beta) T‐cell mastocytosis) 365–6 lymphoma 431–2 matrical basal cell carcinoma differentiation 57–9 (panniculitis‐like; gamma/delta) lymphoma 432–3 MDM2 gene 335 panniculitis‐like lymphoma 431–4 median raphe cyst 486–7 T‐cell‐rich B‐cell lymphoma (DLBCL, NOS) 454–5 melanoacanthoma (pigmented seborrheic keratosis) 8 T‐zone lymphoma 466–7 melanocytes 149–206 lymphomatoid contact dermatitis 399 malignant melanocytic neoplasms 188–206 lymphomatoid papulosis 427–9 lentigo maligna Dubreuilh (Hutchison’s freckle) 188–9 lymphoproliferative CD30+ disorders (LPD) 423–30 malignant melanoma 189–206 anaplastic large cell lymphoma (ALCL) 424–5 variants lymphomatoid papulosis 427–9 acral lentiginous melanoma (ALM) 189, 194–6 differential diagnosis: Hodgkin’s lymphoma, balloon cell melanoma 199–200 lymphocyte predominance 429–30 cutaneous metastasis of melanoma 197–8 neutrophil‐rich (pyogenic) anaplastic large cell desmoplastic malignant melanoma (DMM) 200–2 lymphoma 426–7 lentigo maligna melanoma (LMM) 189, 192 melanoma in large congenital melanocytic nevus M (LCMN) 196–7 Maffucci syndrome (cavernous hemangioma) 252, 254 nodular melanoma (NM) 189, 193 Malherbe, calcifying epithelioma (pilomatricoma) 137–8 superficial spreading melanoma (SSM) 189–91

0004177441.INDD 500 8/9/2018 9:36:10 PM INDEX 501

nevi 155–88 mixed tumor of the skin (chondroid syringoma) 94–5 benign melanocytic lesions with peculiar structural molluscum contagiosum 38–9 features 183–8 Mongolian spot (Ota; Ito; nevus fuscoceruleus) 177–8, 240 atypical (dysplastic) melanocytic (Clark’s) nevus monocytic cells, myeloid and monocytic leukemias 464–5 (B‐K mole syndrome) 185–6 monster cells, seborrheic keratosis (bowenoid) 10 congenital nevi, small/medium‐sized 186–8 morpheaform (sclerodermiform) basal cell carcinoma 64–5 melanocytic nevus with clonal proliferation 183–4 Mucha–Habermann disease (febrile ulceronecrotic blue nevi 171–7 PLEVA) 437–8 common blue nevus 171–2 mucocele, lip 487–8 variant, cellular deep penetrating blue nevus mucosal lentiginous spots (lip, buccal, genital mucosa) 154–5 (neuro‐nevus) 173–7 mucous cyst, oral 487–8 common acquired melanocytic nevi 155–71 Muir–Torre syndrome 114, 115–16 compound nevus 157–8 multicentric reticulohistiocytosis 378–9 dermal nevus with maturation 158–60 multinucleate angiohistiocytoma 318–19 variants multiple myeloma plasmacytoma 448–9 “activated” acral (lentiginous) melanocytic multiple “pinpoint” angiokeratomas (angiokeratoma corporis nevus 161–2 diffusum; Fabry’s disease) 267, 269 ancient nevus 170–1 Munro abscess 422 balloon cell nevus 161 muscle combined nevus 167 benign neoplasms eczematoid melanocytic (Meyerson’s) nevus 165–6 angioleiomyoma genital melanocytic nevus 162–3 piloleiomyoma 338–40 halo nevus (leukoderma centrifugum rhabdomyoma, adult type 340–1 acquisitum; Sutton nevus) 163–4 malignant neoplasms Miescher’s nevus (dermal nevus) 160 rhabdomyosarcoma 341 nevus in pregnancy 168–9 superficial leiomyosarcoma 342–3 osteo‐nevus of Nanta 166 mycosis fungoides recurrent (persistent) melanocytic nevus classic Alibert–Bazin type 405–11 (pseudomelanoma) 167–8 large cell transformation 410 junctional nevus 156 patch stage 405 melanosis neviformis (pigmented hairy epidermal plaque stage 407–8 nevus) 155 tumor stage 409–10 dermal melanocytosis, nevus fuscoceruleus (Ota; Ito; variant: CD8+ mycosis fungoides 409 Mongolian spot) 177–8 simulators and variants 399–405, 411–15 spindle and/or epithelial cell nevus 178–83 drug reactions 400 common nevus of Spitz 178–9 early vitiligo 400 variants 179–83 graft versus host reaction (acute) 401 pigmented spindle cell nevus (Reed) 182–3 lichen planus 399 non‐neoplastic hyperpigmentations 150–5 lichen sclerosus et atrophicus 400–1 euphelides (genuine freckles) 150 lymphocytic infiltration Jessner–Kanof 404–5 “ink” spot lentigo (reticulated melanocytic lymphomatoid contact dermatitis 399 macule) 151, 152 “parapsoriasis” 411–15 mucosal lentiginous spots (lip, buccal, genital erythrodermic mycosis fungoides 412–13 mucosa) 154–5 folliculotropic (pilotropic) mycosis fungoides 413–14 “nevus” spilus (speckled lentiginous nevus; café‐au‐lait granulomatous mycosis fungoides 415 spot) 151, 152 large plaque parasporiasis (LPP) 412 psoralen UVA (PUVA) lentigo 150–1 pigmented purpuric mycosis fungoides 412 senile freckles (solar (actinic) lentigo) 153–4 small plaque parapsoriasis (SPP) (digitate melanocytic nevus with clonal proliferation 183–4 dermatosis) 411 melanoma in large congenital melanocytic nevus syringotropic mycosis fungoides (syringolymphoid (LCMN) 196–7 hyperplasia with alopecia) 414 melanosis neviformis (pigmented hairy epidermal nevus) 155 pigmented purpuric dermatitis (lichen aureus) 403–4 Merkel cell primary neuroendocrine cutaneous pigmented purpuric mycosis fungoides 412 APUDoma 360–2 pityriasis lichenoides chronica 401 metals causing contact dermatitis 399 myeloid and monocytic leukemias 464–5 metastases, cutaneous of melanoma 197–8 myofibromatosis, infantile (perivascular myoma; metatypic basal cell carcinoma with squamoid myofibroma) 290–2 differentiation 67–8 myoid and glomoid differentiation, benign vascular Meyerson’s eczematoid melanocytic nevus 165–6 neoplasms 292–5 Mibelli angiokeratoma acroasphyctic digitorum 267, 269 myopericytoma (infantile myofibromatosis; perivascular Mibelli, porokeratosis of 30–1 myoma (incl. myofibroma)) 290–2 microcapillary (microvenular) hemangioma 282–3 myxoid cyst, digital 488–9 microcystic adnexal carcinoma 105–6 myxoid neurothekeoma 356–7 microvenular (microcapillary) hemangioma 282–3 myxoid squamous cell carcinoma 76–7 Miescher’s nevus (dermal nevus) 160 MZL (cutaneous marginal zone B‐cell lymphoma; milia 476–7 MALT type) 444–9

0004177441.INDD 501 8/9/2018 9:36:11 PM 502 INDEX

N granulomatous storing nailbed melanoma 194, 195 hereditary progressive mucinous histiocytosis 386–7 Nanta, osteo‐nevus of 166 juvenile xanthogranuloma 380–1 “nappes claires” (deck chair sign) 419 necrobiotic xanthogranuloma 385–6 natural killer (NK) cells, extranodal NK/T‐cell lymphoma, verruciform xanthoma 384–5 nasal type (subcutaneous) 439–43 xanthelasma 381–2 necrobiotic xanthogranuloma 385–6 xanthoma disseminatum 381–2 nerves hemophagocytic benign neoplasms familial hemophagocytic lymphohistiocytosis 387–8 dermal nerve sheath myxoma (myxoid histiocytic cytophagic panniculitis 388 neurothekeoma) 356–7 proliferative variant, cellular neurothekeoma 357–8 benign cephalic histiocytosis 377 granular cell tumor (Abrikossoff) 354–5 multicentric reticulohistiocytosis 378–9 neurofibroma 346–9 progressive nodular histiocytosis 376–7 Pacinian neurofibroma (pacinoma) 358 sinus histiocytosis with massive schwannoma (neurilemmoma) 349–51 lymphadenopathy 379–80 solitary neuroma (“palisaded encapsulated non‐neoplastic hyperpigmentations 150–5 neuroma”) 352–3 non‐stratified squamous epithelium, cutaneous cyst variant, traumatic neuroma 353 lining 485–7 malignant neoplasms non‐viral acanthomas 19–30 malignant granular cell tumor 360 nuclear H3K27me3 expression 187 malignant peripheral nerve sheath tumor (malignant schwannoma) 358–9 O neuroendocrine neoplasms, primary neuroendocrine oral mucosal angioma 205, 206 (Merkel cell, trabecular) carcinoma of the oral mucosal lentiginous spots 154–5 skin (cutaneous APUDoma) 360–2 oral mucous cyst and superficial mucocele of the lip 487–8 neurilemmoma (schwannoma) 349–51 oral palate, malignant melanoma 204 neuro‐nevus (cellular deep penetrating blue nevus) 173–7 oral verrucous carcinoma 46 neuroendocrine neoplasms 360–2 orificium urethrae malignant melanoma 204 neurofibroma 346–9 Osler–Weber–Rendu hereditary hemorrhagic neutrophil‐rich (pyogenic) anaplastic large cell telangiectasia 249–50 lymphoma 426–7 osteo‐nevus of Nanta 166 nevi Ota (Ito) nevus fuscoceruleus (Mongolian spot) 177–8 see also dermal melanocytic nevus, with maturation connective tissue 208–9 P epidermal 2–3 Pacinian neurofibroma (pacinoma) 358 fat nevus (hamartoma) 328–9 pagetoid reticulosis (PR), unilesional (Woringer–Kolopp) hair follicles 119–21 417–18 melanocytic 155–88 Paget’s disease 145–8 benign melanocytic lesions with peculiar structural mammary 146–8 features 183–8 extramammary 146–8 blue nevi 171–7 pale (clear) cell acanthoma 22 common acquired 155–71 palisaded encapsulated neuroma 352–3 dermal melanocytosis 177–8 panniculitis spindle and/or epithelioid cell nevus 178–83 histiocytic cytophagic 388 melanoma in large congenital nevus (LCMN) 196–7 lupus panniculitis (lupus profundus) 433–4 nevus collagenicus 208–9 subcutaneous panniculitis‐like lymphoma 431–4 nevus flammeus (portwine stain) 242–3 papillary “eccrine” (misnomer) and tubular apocrine nevus fuscoceruleus (Ota; Ito; Mongolian spot) 177–8 adenoma 95–7 “nevus” spilus (speckled lentiginous nevus; café‐au‐lait papillary hemangioma 297 spot) 151, 152 papillary intralymphatic angioendothelioma (PILA) 306–8 nevus syndrome, Gorlin–Goltz 69 papillomatosis, confluent and reticulate (Gougerot and nevus vascularis reticularis (cutis marmorata Carteaud) 12 telangiectatica) (van Lohuizen) 245–6 papillomatosis cutis carcinoides 45–6 sweat gland differentiation 86–7, 93–4 papillomatous seborrheic keratosis 7 vessels, nevus anemicus 242 papular (secondary) syphilis 398–9 nevoxanthoendothelioma 380–1 “parapsoriasis” 411–15 Nikolowski, trichoadenoma 136–7 parapsoriasis en plaques (Brocq’s disease) 411 nipple, accessory 218 parapsoriasis lichenoides 411 NLHC see non‐Langerhans cell (NLHC) histiocytoses PCFCL (peripheral cutaneous follicle center lymphoma) 456 NM (nodular melanoma) 189, 193 PDS (pleomorphic dermal sarcoma) 231–4 nodular B‐cell pseudolymphoma 393–6 pediatric conditions nodular basal cell carcinoma 54–6 Bloom’s syndrome (congenital telangiectatic nodular clear cell hidradenoma 97–8 erythema) 247–8 nodular melanoma (NM) 189, 193 Burkitt’s lymphoma 459 nodular T‐cell pseudolymphoma 396–9 congenital self‐healing reticulohistiocytosis non‐Langerhans cell (NLHC) histiocytoses (Hashimoto–Pritzker) 370

0004177441.INDD 502 8/9/2018 9:36:11 PM INDEX 503

digital recurring fibromatous tumor 214–15 Mucha–Habermann disease (febrile ulceronecrotic Hand–Schüller–Christian adult Langerhans cell PLEVA) 437–8 histiocytosis 371, 374–5 plywood fibroma 211–12 indeterminate cell histiocytosis 371 POEMS syndrome, glomeruloid hemangioma in 287–8 infantile capillary and congenital hemangioma 280–1 poikiloderma atrophicans vasculare 412 infantile digital fibromatosis 214–15 polydactyly, rudimentary 216 infantile myofibromatosis (perivascular myoma, incl. polythelia 218 myofibroma) 290–2 porocarcinoma (malignant poroma) 106–7 juvenile giant cell granuloma 380–1 porokeratosis Mibelli (porokeratoma) 30–1 juvenile maculopapular mastocytosis 365–6 poroma 89 juvenile xanthogranuloma 380–1 poroma, malignant 106–7 Letterer–Siwe Langerhans cell histiocytosis 371 porphyria cutanea tarda 476 phacomatosis pigmentovascularis 240 portwine stain (nevus flammeus) 242–3 Reye’s tumor 214–15 preauricular tag 217–18 scabies 396 precursors of Langerhans cell histiocytoses 370–1 penis, glans, squamous cell carcinoma 83 precursor of lymphoblastic leukemia/lymphoma 470 pericytic differentiation, benign vascular pregnancy, melanocytic nevus 168–9 neoplasms 288–92 primary cutaneous CD4+ (acral) small/medium‐sized T‐cell perifollicular fibroma of connective tissue 143, 210–11 lymphoproliferative disorder 435–6 peripheral cutaneous follicle center lymphoma (PCFCL) 456 primary cutaneous follicle center lymphoma (FCL) 449–51 peripheral nerve sheath tumor, malignant 358–9 primary cutaneous peripheral T‐cell lymphoma (PTL), perivascular myoma (incl. myofibroma) unspecified (NOS) 434–8 (myopericytoma) 290–2 primary neuroendocrine (Merkel cell, trabecular) phacomatosis pigmentovascularis 240 carcinoma of the skin (cutaneous pigmented conditions APUDoma) 360–2 see also melanocytes Pringle–Bourneville disease, adenoma sebaceum associated anogenital and clonal Bowen’s disease 52 with 319–21 anomaly of the flexures (Dowling‐Degos disease) 13 progressive lymphangioma (benign basal cell carcinoma 61, 205, 206 lymphangioendothelioma) 262–3 dermatofibrosarcoma protuberans (Bednar’s tumor) 230 progressive nodular histiocytosis 376–7 epidermal cyst with vellus hairs 473 proliferating trichilemmal cyst 138–40 hairy epidermal melanocytic nevus 155 proliferating trichilemmal (pilar) tumor (PTT) 138–40 mycosis fungoides, pigmented purpuric 412 proliferative histiocytoma 376–7 non‐neoplastic hyperpigmentations 150–5 proliferative NLHC histiocytoses phacomatosis pigmentovascularis 240 benign cephalic histiocytosis 377 purpuric dermatitis (lichen aureus) 403–4 multicentric reticulohistiocytosis 378–9 purpuric mycosis fungoides 412 progressive nodular histiocytosis 376–7 Reed pigmented spindle cell nevus 182–3 sinus histiocytosis with massive reticulate pigmented anomaly of the flexures lymphadenopathy 379–80 (Dowling–Degos disease) 13–14 “promontory sign” 300, 304 seborrheic keratosis 6, 8 “pseudo‐fat cells” 255 spindle cell nevus (Reed) 182–3 pseudo‐Kaposi’s sarcoma (acroangiodermatitis Mali) 276–7 urticaria pigmentosa (juvenile maculopapular pseudo‐mycosis fungoides (mycosis fungoides mastocytosis) 365–6 simulators) 399–405 PILA (papillary intralymphatic angioendothelioma) 306–8 drug reactions 400 pilar leiomyoma 338–40 early vitiligo 400 pilar sheath acanthoma 121–2 graft versus host reaction (acute) 401 pilo‐sebaceous hamartoma 114 lichen planus 399 piloleiomyoma 338–40 lichen sclerosus et atrophicus 400–1 pilomatrical carcinoma (malignant pilomatricoma) 140–1 lymphocytic infiltration Jessner–Kanof 404–5 pilomatricoma (calcifying epithelioma Malherbe) 137–8 lymphomatoid contact dermatitis 399 pilonidal sinus/cyst 484–5 pigmented purpuric dermatitis (lichen aureus) 403–4 pilosebaceous mesenchyme 143 pityriasis lichenoides chronica 401 pilotropic (folliculotropic) mycosis fungoides 413–14 pityriasis lichenoides et varioliformis acuta (PLEVA) 402 Pinkus, fibroepithelioma of 70–2 “pseudocarcinomas”/neoplasms with intermediate “pinpoint” angiokeratomas, multiple (Fabry’s disease) malignant potential 40–8 267, 269 Buschke–Löwenstein tumor (giant condyloma) 41, 47–8 pityriasis lichenoides chronica 401 epithelioma cuniculatum (verrucous carcinoma) pityriasis lichenoides et varioliformis acuta (PLEVA) 402 (EC/EV) 44–5 Mucha–Habermann disease (febrile ulceronecrotic florid papillomatosis of the oral cavity (oral verrucous PLEVA) 437–8 carcinoma) 46 “pizza sign” 129 keratoacanthoma 40–4 pleomorphic (dermal) sarcoma (PDS) 231–4 papillomatosis cutis carcinoides 45–6 pleomorphic lipoma 332 pseudocysts 487–90 pleomorphic sclerosing fibroma with multinucleated pseudolymphoma (PL) 393–405 cells 212–13 nodular B‐cell PL 393–6 PLEVA (pityriasis lichenoides et varioliformis acuta) 402 nodular T‐cell PL 396–9

0004177441.INDD 503 8/9/2018 9:36:11 PM 504 INDEX

pseudolymphoma (PL) (cont’d) ectopic (heterotopic) sebaceous glands (Fordyce pseudo‐mycosis fungoides (mycosis fungoides glands) 111–12 simulators) 399–405 (senile) sebaceous gland hyperplasia 112–13 pseudomelanoma 167–8 variant: pilo‐sebaceous hamartoma 114 PL see pseudolymphoma malignant neoplasms 118–19 psoralen UVA (PUVA) lentigo 150–1 sebaceous carcinoma 118–19 PTCH gene 69 sebaceous epithelioma (sebaceoma) 116–18 PTL (primary cutaneous peripheral lymphoma), unspecified seborrheic keratoses (SK) 4–11, 205, 206 (NOS) 434–8 Goya, Francisco de 91 PTT (proliferating trichilemmal (pilar) tumor) 138–40 variants purpuric dermatitis, pigmented (lichen aureus) 403–4 acanthotic seborrheic keratosis 6 PUVA (psoralen UVA lentigo) 150–1 activated seborrheic keratosis 7 ‐like granulation tissue 272 clonal (intraepidermal) seborrheic keratosis pyogenic (neutrophil‐rich) anaplastic large cell (Borst–Jadassohn) 9, 91–2 lymphoma 426–7 dermatosis papulosa nigra 7 flat seborrheic keratosis 6 Q hyperkeratotic Queyrat erythroplasia 53–4 seborrheic keratosis (stucco‐keratosis) 11 irritated seborrheic keratosis 7 R melanoacanthoma 8 radiation‐induced atypical vascular lesion (AVL) 308–9 papillomatous seborrheic keratosis 7 radiation‐induced (postradiation) angiosarcoma 312 pigmented seborrheic keratosis 8 raphe cyst, median 486–7 reticulated, pigmented seborrheic keratosis 6 Recklinghausen’s disease 346 seborrheic keratosis with monster cells (Bowenoid) 10 recurrent (persistent) melanocytic nevus secondary skin involvement in leukemias/ (pseudomelanoma) 167–8 lymphomas 463–8 recurring digital fibrous tumor of children 214–15 secondary syphilis, papular 398–9 Reed pigmented spindle cell nevus 182–3 segmental angiokeratoma circumscriptum naeviforme 267 reticulate pigmented anomaly of the flexures self‐healing reticulohistiocytosis, congenital (Dowling–Degos disease) 13–14 (Hashimoto–Pritzker) 370 reticulated melanocytic macule 151, 152 senile freckles (solar (actinic) lentigo) 153–4 reticulated pigmented seborrheic keratosis 6 senile hemangioma (cherry angioma) 281–2 reticulohistiocytoma, solitary 378–9 senile sebaceous gland hyperplasia 112–13 reticulohistiocytosis, multicentric 378–9 Sézary syndrome 418–20 retiform hemangioendothelioma 305–6 variant: Sézary syndrome, large cell Reye’s tumor 214–15 transformation 420–3 rhabdomyoma, adult type 340–1 SFT (solitary fibrous tumor of the skin) 289–90 rhabdomyosarcoma 341 shagreen patch 208–9 rodent ulcer 66 sinus histiocytosis with massive lymphadenopathy 379–80 “Roman bridges” 255 sinusoidal hemangioma 253–4 Rombo syndrome 69 skin tag 209–10 rudimentary digit 216 slack skin, granulomatous 415–17 supernumerary 353 small plaque parapsoriasis (SPP) (digitate dermatosis) 411 rudimentary polydactyly 216 soft fibroma (skin tag/acrochordon) 209–10 Russell bodies 447 soft parts, melanoma of (clear cell sarcoma) 203–4 solar (actinic) keratoses 15–18 S solar (actinic) lentigo, senile freckles 153–4 scabies, children 396 solar lentigo 19–20 SCC see squamous cell carcinoma (SCC) solid cystic hidradenoma 97–8 schwannoma, malignant 358–9 solitary angiokeratoma 267–8 schwannoma (neurilemmoma) 349–51 solitary cutaneous mast cell proliferation 364–5 sclerodermiform (morpheaform) basal cell carcinoma 64–5 solitary fibrous tumor of the skin (SFT) 289–90 sclerosing epithelial hamartoma (trichoepithelioma) 131–3 solitary Langerhans cell tumor (eosinophilic sclerosing hemangioma 218–27 granuloma) 371, 375–6 sclerosing sweat duct carcinoma 105–6 solitary neuroma (“palisaded encapsulated neuroma”) 352–3 sclerotic fibroma of connective tissue 211–12 solitary reticulohistiocytoma 378–9 sebaceoma (sebaceous epithelioma) 116–18 speckled lentiginous nevus 151, 152 sebaceous adenoma (NOT adenoma sebaceum) 114–15 spider angioma (nevus araneus) 244–5 sebaceous basal cell carcinoma differentiation 57–9 Spiegler–Brooke syndrome 126 sebaceous carcinoma 118–19 spindle and/or epithelioid cell nevus 178–83 sebaceous differentiation 110–19 variant, pigmented spindle cell nevus (Reed) 182–3 benign neoplasms 114–18 spindle B‐cell lymphoma (BCL), cutaneous 455–7 Muir–Torre syndrome 115–16 spindle cell (fusicellular) squamous cell carcinoma 78–9 sebaceous adenoma (NOT adenoma sebaceum) 114–15 spindle cell hemangioma (formerly spindle cell sebaceous epithelioma (sebaceoma) 116–18 hemangioendothelioma) 254–6 hyperplasias and hamartomas 111–14 spindle cell lipoma 330–1

0004177441.INDD 504 8/9/2018 9:36:11 PM INDEX 505

spinocellulare segregans, epithelioma of Delacretaz 74–5 syringocystadenoma papilliferum 103–5 spiradenoma 99–100 tubular adenomas 95–7 Spitz, common nevus of 178–9 eccrine differentiation 86–92 SPP (small plaque parapsoriasis) (digitate dermatosis) 411 eccrine syringofibroadenoma (Mascaro tumor) 87–8 squamoid differentiation, basal cell carcinoma histological poroma metatypical variants 67–8 variants squamous cell carcinoma (SCC) 72–83 common solid poroma 89 variants dermal duct tumor 89, 92 acantholytic SCC (epithelioma spinocellulare segregans hidroacanthoma simplex 89, 90–1 of Delacretaz) 74–6 sweat gland nevus 86–7 follicular (infundibular) SCC 77–8 syringoma (eruptive hidradenoma) 88–9 myxoid SCC 76–7 sweat gland nevus 86–7 special sites 79–84 symplastic hemangioma 296–7 spindle cell (fusicellular) SCC 78–9 syndromatic basal cell carcinoma (basal cell nevus well‐differentiated SCC 72–4 syndrome, Gorlin–Goltz) 69 vascular acantholytic (angiosarcoma‐like) squamous cell synovial cyst (ganglion) 490 carcinoma 316–17 syphilis, secondary, papular 398–9 squamous epithelium, cutaneous cyst lining 472–86 syringocystadenoma papilliferum 103–5 SSM (superficial spreading melanoma) 189–91 syringolymphoid hyperplasia with alopecia staghorn‐like vessels 289 (syringotropic mycosis fungoides) 414 starry sky macrophage 394 syringoma (eruptive hidradenoma) 88–9 starry sky pattern 459 syringomatous carcinoma 105–6 steatocystoma, multiplex/simplex 481–2 syringotropic mycosis fungoides (syringolymphoid storiform collagenoma 211–12 hyperplasia with alopecia) 414 stratified squamous epithelium, cutaneous cyst lining 472–85 systemic angioendotheliomatosis (intravascular large B‐cell stucco‐keratosis 11 lymphoma) 461–2 subcutaneous (panniculitis‐like; alpha/beta) T‐cell systemic mast cell proliferation 367–8 lymphoma 431–2 subcutaneous (panniculitis‐like; gamma/delta) T‐cell T lymphoma 432–3 T‐cells subcutaneous panniculitis‐like lymphoma 431–4 adult T‐cell leukemia/lymphoma (ATLL) 467–8 subungual hematoma 205, 206 angioimmunoblastic T‐cell lymphoma 441–3 superficial basal cell carcinoma 60 cutaneous aggressive epidermotropic CD8+ T‐cell superficial leiomyosarcoma 342–3 lymphoma (Berti) 436–7 superficial spreading melanoma (SSM) 189–91 cutaneous mature T‐cell lymphoid neoplasms 405–41 superficial (superficial lymphangioma) and deep (cystic CD30+ lymphoproliferative disorders (LPD) of the hygroma) lymphatic skin 423–30 malformations 259–60 extranodal NK/T‐cell lymphoma, nasal type superficial trichoblastoma (trichoepithelioma) 125–6 (subcutaneous) 439–43 supernumary tissue elements 216–18 granulomatous slack skin 415–17 supernumerary digit 216 mycosis fungoides, classic Alibert–Bazin type 405–11 rudimentary 353 pagetoid reticulosis (PR), unilesional Sutton nevus (leukoderma centrifugum acquisitum) 163–4 (Woringer–Kolopp) 417–18 sweat gland differentiation primary cutaneous peripheral lymphoma (PTL), malignant adnexal neoplasms unspecified (NOS) 434–8 apocrine differentiation 108–10 Sézary syndrome 418–20 apocrine (hidr‐)adenocarcinoma variant: Sézary syndrome, large cell (mucinous) 108–10 transformation 420–3 eccrine differentiation 105–8 simulators and variants of mycosis fungoides: eccrine (mucinous) carcinoma 107–8 “parapsoriasis” 411–15 microcystic adnexal carcinoma (syringomatous subcutaneous panniculitis‐like lymphoma 431–4 carcinoma; sclerosing sweat duct cytomorphology 390, 392, 397 carcinoma) 105–6 intravascular T‐cell lymphoma 462–3 porocarcinoma (malignant poroma) 106–7 primary cutaneous CD4+ (acral) small/medium‐sized nevi, hyperplasia and benign adnexal neoplasms 86–105 T‐cell lymphoproliferative disorder 435–6 apocrine differentiation 93–105 pseudolymphoma (PL) anogenital mammary‐like gland 101–2 nodular T‐cell pseudolymphoma 396–9 apocrine nevus 93–4 nodular T‐cell PL cylindroma (turban tumor) 100–1 papular (secondary) syphilis 398–9 “eccrine” (misnomer) acrospiroma (nodular clear tick bite CD30+ pseudolymphoma 396–8 cell hidradenoma; solid cystic T‐cell‐rich B‐cell lymphoma (DLBCL, NOS) 454–5 hidradenoma) 97–8 T‐zone lymphoma 466–7 hidradenoma papilliferum (apocrine papillary tadpoles (cysts and short ducts) 88 cystadenoma) 102–3 tags mixed tumor of the skin (chondroid syringoma) 94–5 preauricular 217–18 spiradenoma 99–100 skin tag 209–10

0004177441.INDD 505 8/9/2018 9:36:11 PM 506 INDEX

targetoid hemosiderotic (hobnail) hemangioma 261–2 verrucous carcinoma 44, 46 telangiectasia macularis eruptiva perstans (TMEP) verrucous hemangioma (venous malformation) 265–9 (adults) 366–7 verruga peruana 274–5 TEN (toxic epidermolytic necrolysis) 401 vessels 239–326 tick bite CD30+ pseudolymphoma 396–8 angiokeratomas, verrucous hemangioma (venous TMEP (telangiectasia macularis eruptiva perstans malformation) 265–9 (adults)) 366–7 arteriovenous malformations 256–9 toxic epidermolytic necrolysis (TEN) 401 acral arteriovenous hemangioma (cirsoid aneurysm) trabecular primary neuroendocrine carcinoma of the skin 256–7 (cutaneous APUDoma) 360–2 glomuvenular malformation (“glomangioma”) 257–9 tragus, accessory 217 benign vascular neoplasms 278–97 traumatic neuroma 353 endothelial differentiation 280–8 Treponema pallidum (syphilis) 398–9 cherry angioma (senile hemangioma) 281–2 trichilemmal carcinoma 141–2 glomeruloid hemangioma in POEMS trichilemmal (isthmus‐catagen) cyst 475–6 syndrome 287–8 trichilemmoma (tricholemmoma) 122–3 infantile capillary and congenital trichoadenoma (Nikolowski) 136–7 hemangioma 280–1 trichoblastic carcinoma 142–3 kaposiform hemangioendothelioma 285–7 trichoblastic fibroma 127–31 microvenular (microcapillary) hemangioma 282–3 trichoblastoma, superficial (trichoepithelioma) 125–6 tufted angioma 283–4 trichoblastoma (trichoblastic fibroma; immature epithelioid hemangioma (angiolymphoid hyperplasia trichoepithelioma) 127–31 with eosinophilia, ALHE) 278–9 trichodiscoma (follicular fibroma; fibrofolliculoma; glomoid and myoid differentiation 292–5 perifollicular fibroma) 143, 210–11 angioleiomyoma (angiomyoma; vascular trichoepithelioma leiomyoma) 294–5 immature 127–31 glomus tumor 292–4 sclerosing epithelial hamartoma 131–3 pericytic differentiation 288–92 superficial trichoblastoma 125–6 myopericytoma (infantile myofibromatosis; trichofolliculoma (folliculosebaceous cystic perivascular myoma (incl. hamartoma) 133–5 myofibroma)) 290–2 tricholemmoma (trichilemmoma) 122–3 solitary fibrous tumor of the skin (SFT) 289–90 tubular adenoma 95–7 recently described 296–7 tufted angioma 283–4 papillary hemangioma 297 turban tumor (cylindroma) 100–1 symplastic hemangioma 296–7 capillary malformations 242–8 U congenital telangiectatic erythema (Bloom’s ulcerating basal cell carcinoma 66 syndrome) 247–8 ulcus rodens 66 cutis marmorata telangiectatica (van Lohuizen) (nevus ulcus terebrans 66 vascularis reticularis) 245–6 urticaria pigmentosa (juvenile maculopapular nevus araneus (spider angioma) 244–5 mastocytosis) 365–6 nevus flammeus (portwine stain) 242–3 hamartomas, nevi, and malformations 240–2 V eccrine angiomatous hamartoma 241–2 van Lohuizen cutis marmorata telangiectatica (nevus nevus anemicus 242 vascularis reticularis) 245–6 phacomatosis pigmentovascularis 240 vascular see vessels hyperplasias 270–7 Vater–Pacini capsules, Pacinian neurofibroma (pacinoma) 358 acroangiodermatitis Mali (pseudo‐Kaposi’s vellus hair cyst 474–5 sarcoma) 276–7 vellus hairs, epidermal cyst with pigment and 473 bacillary angiomatosis 273–4 (venular aneurysm) 251 granuloma pyogenicum (lobular capillary venous malformations hemangioma; botryomykoma) 270 angioma serpiginosum 250–1 differential diagnosis: pyogenic granuloma‐like blue rubber bleb nevus syndrome (familial venous granulation tissue 272 malformation) 248–9 intravascular papillary endothelial hyperplasia cavernous hemangioma (Maffucci syndrome) 252, 254 (Masson) 275–6 hereditary hemorrhagic telangiectasia (Osler–Weber– verruga peruana 274–5 Rendu) 249–50 Kimura’s disease 325–6 sinusoidal hemangioma 253–4 lymphatic malformations 259–64 spindle cell hemangioma (formerly spindle cell lymphangiomatosis 263–4 hemangioendothelioma) 254–6 progressive lymphangioma (benign venular aneurysm (venous lake) 251 lymphangioendothelioma) 262–3 venular aneurysm (venous lake) 251 superficial (superficial lymphangioma) and deep Verocay bodies 349 (cystic hygroma) lymphatic verruca plana 33–4 malformations 259–60 verruca vulgaris/variants 31–4 targetoid hemosiderotic (hobnail) hemangioma 261–2 verruciform xanthoma 384–5 significant vascular component neoplasms

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angiofibroma (adenoma sebaceum associated with blue rubber bleb nevus syndrome (familial venous Pringle–Bourneville disease) 319–21 malformation) 248–9 angiolipoleiomyoma (angiomyolipoma) 322 cavernous hemangioma (Maffucci syndrome) angiolipoma 321 252, 254 angiomyxoma 322–3 hereditary hemorrhagic telangiectasia intralymphatic histiocytosis 324 (Osler–Weber–Rendu) 249–50 multinucleate angiohistiocytoma 318–19 sinusoidal hemangioma 253–4 vascular leiomyoma (angioleiomyoma; spindle cell hemangioma (formerly spindle cell angiomyoma) 294–5 hemangioendothelioma) 254–6 vascular neoplasms with high malignant venular aneurysm (venous lake) 251 potential 309–18 viral acanthomas 31–8 cutaneous angiosarcoma 309–11 variants epithelioid angiosarcoma 315 condyloma acuminatum 34 differential diagnosis: acantholytic (angiosarcoma‐like) verruca plana 33–4 squamous cell carcinoma 316–17 vitiligo, early 400 epithelioid hemangioendothelioma 312–14 vulvar intraepithelial neoplasia 53–4 glomangiosarcoma (malignant glomus tumor) 317–18 radiation‐induced (postradiation) angiosarcoma 312 W vascular neoplasms of intermediate malignant Warthin–Starry stain 398 potential 298–309 warty dyskeratoma 27–9 Kaposi’s sarcoma (KS) 298–305 well‐differentiated squamous cell carcinoma 72–4 papillary intralymphatic angioendothelioma (PILA) WHO‐EORTC Consensus Classification 451 (malignant endovascular papillary angioendothelioma, Winer, giant dilated pore of (conical infundibular Dabska tumor; endovascular papillary acanthoma) 120–1 hemangioendothelioma) 306–8 Woringer–Kolopp unilesional pagetoid radiation‐induced atypical vascular lesion (AVL) reticulosis 417–18 (benign lymphangiomatous papule (BLAP)) 308–9 X retiform hemangioendothelioma 305–6 xanthelasma 381–2 venous malformations 248–56, 265–9 xanthelasma palpebrarum 383 angiokeratomas, verrucous hemangioma (venous xanthogranuloma, juvenile 380–1 malformation) 265–9 xanthoma disseminatum 381–2 angioma serpiginosum 250–1 xanthoma multiplex 380–1

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