OriGene Technologies, Inc. 9620 Medical Center Drive, Ste 200 Rockville, MD 20850, US Phone: +1-888-267-4436 [email protected] EU: [email protected] CN: [email protected] Product datasheet for SC120022 beta (SGCB) (NM_000232) Human Untagged Clone Product data:

Product Type: Expression Plasmids Product Name: beta Sarcoglycan (SGCB) (NM_000232) Human Untagged Clone Tag: Tag Free Symbol: SGCB Synonyms: A3b; LGMD2E; LGMDR4; SGC Vector: pCMV6-XL5 E. coli Selection: Ampicillin (100 ug/mL) Cell Selection: None Fully Sequenced ORF: >NCBI ORF sequence for NM_000232, the custom clone sequence may differ by one or more nucleotides

ATGGCGGCAGCGGCGGCGGCGGCTGCAGAACAGCAAAGTTCCAATGGTCCTGTAAAGAAGTCCATGCGTG AGAAGGCTGTTGAGAGAAGGAGTGTCAATAAAGAGCACAACAGTAACTTTAAAGCTGGATACATTCCGAT TGATGAAGATCGTCTCCACAAAACAGGGTTGAGAGGAAGAAAGGGCAATTTAGCCATCTGTGTGATTATC CTCTTGTTTATCCTGGCTGTCATCAATTTAATAATAACACTTGTTATTTGGGCCGTGATTCGCATTGGAC CAAATGGCTGTGATAGTATGGAGTTTCATGAAAGTGGCCTGCTTCGATTTAAGCAAGTATCTGACATGGG AGTGATCCACCCTCTTTATAAAAGCACAGTAGGAGGAAGGCGAAATGAAAATTTGGTCATCACTGGCAAC AACCAGCCTATTGTTTTTCAGCAAGGGACAACAAAGCTCAGTGTAGAAAACAACAAAACTTCTATTACAA GTGACATCGGCATGCAGTTTTTTGACCCGAGGACTCAAAATATCTTATTCAGCACAGACTATGAAACTCA TGAGTTTCATTTGCCAAGTGGAGTGAAAAGTTTGAATGTTCAAAAGGCATCTACTGAAAGGATTACCAGC AATGCTACCAGTGATTTAAATATAAAAGTTGATGGGCGTGCTATTGTGCGTGGAAATGAAGGTGTATTCA TTATGGGCAAAACCATTGAATTTCACATGGGTGGTAATATGGAGTTAAAGGCGGAAAACAGTATCATCCT AAATGGATCTGTGATGGTCAGCACCACCCGCCTACCCAGTTCCTCCAGTGGAGACCAGTTGGGTAGTGGT GACTGGGTACGCTACAAGCTCTGCATGTGTGCTGATGGGACGCTCTTCAAGGTGCAAGTAACCAGCCAGA ACATGGGCTGCCAAATCTCAGACAACCCCTGTGGAAACACTCATTAA

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5' Read Nucleotide >OriGene 5' read for NM_000232 unedited Sequence: TTTGTAATACGACTCACTATAGGGGCGGCCGCGAATTCGCACGAGGGGAAGATGGCGGCA GCGGCGGCGGCGGCTGCAGAACAGCAAAGTTCCAATGGTCCTGTAAAGAAGTCCATGCGT GAGAAGGCTGTTGAGAGAAGGAGTGTCAATAAAGAGCACAACAGTAACTTTAAAGCTGGA TACATTCCGATTGATGAAGATCGTCTCCACAAAACAGGGTTGAGAGGAAGAAAGGGCAAT TTAGCCATCTGTGTGATTATCCTCTTGTTTATCCTGGCTGTCATCAATTTAATAATAACA CTTGTTATTTGGGCCGTGATTCGCATTGGACCAAATGGCTGTGATAGTATGGAGTTTCAT GAAAGTGGCCTGCTTCGATTTAAGCAAGTATCTGACATGGGAGTGATCCACCCTCTTTAT AAAAGCACAGTAGGAGGAAGGCGAAATGAAAATTTGGTCATCACTGGCAACAACCAGCCT ATTGTTTTTCAGCAAGGGACAACAAAGCTCAGTGTAGAAAACAACAAAACTTCTATTACA AGTGACATCGGCATGCAGTTTTTTGACCCGAGGACTCAAAATATCTTATTCAGCACAGAC TATGAAACTCATGAGTTTCATTTGCCAAGTGGAGTGAAAAGTTTGAATGTTCAAAAGGCA TCTACTGAAAGGGATTACCAGCATGCTACCAGTGATTTAATATAAAAGTGATNGGGCGTG CTATNGGTGCGTGGAAATGAANGGTGTATTCATTATGGGCAAAACCATTGAATTTACATG GNGTGGTATNNATGGAGTTAAAGGCGGNAAACAGTATCATCTAAATGGATCTGTGATGGT CAGCACCACCCGCTACCCANTNNNCTCATGAGACANNTGGGGNANTGGGGACTTGGGACC TACAGCTCTGGATGGTGCTGATGGGACCT

3' Read Nucleotide >OriGene 3' read for NM_000232 unedited Sequence: CCGCGGCACGCAATCTAGAGTCGAGTTTTTTTTTTTTTTTTTTCAATTTACAGAATTTTT ATTGTAAACAGAAGCTCATTACTAGTTATTACAAACTGAATCAACTGAAACTCAAGTTAG CAATGTGAAACACATTTATAGGCTTATTTTTGTATACCATAATTGGTAATTTTTGCCCCC TCAATACTTTTAAAAAGACTGTTAAAATTTTCAGCATTTCAATGATCTCTTATTTGTCAG GTTTAGCACCATGACATTCTCATTCCCTTAAAAAAACACTCATTCAAATCTAGGTAGAAC TTCCACCTTTCATCATCAAAATTATCACACAAAATTTATTTTGTTTTTTTCACAATGCAA AAAGAAGACAAATAAGTATATTTTAAAATATTATCAGCAGTCCGTTTTGTGTGGTTTTAC ATTTTTCTGTCTGCCCATTATTAAAAAATCTTGCATTGATTTCATTTGCCCCCCTTGTCA TTGCAACCCGTCTCTAGAATACTGTGGTAATTGAAACTAGCATGTACCTGCGCCCCCTCC CGGGGTCCTATCTTTGTCACCCACCTCCCCCATGGCTACTGCTTGTCATATCTGTGCTCA GTGCAGGGATGAGCATACAGCAGGAAGAGGCGAAGTCAGCATTTCATTTACAGAAAAATA CTATCTGGTGGAGACAATGAGTTGCTGAAGATTTACTGTGGATAAAAATAAGCCGGCCAG GCGTGGTGGCTCACACCTGTAATCCCAGCACTTTGGGAGGCCAAGGCAGGCAGATCACGA TGTCAAGAGATTGAGACCATCCTGGCCAACATGGTGAAACCCCGTCTCTACTAAAAATAC AAAAATTANCCCGGGACTGTGGCACATGCCTGTAGTCCCAGTACTCGGGAAGGCTGAGCA GAGAATCGCTTGACCCCTGGAGCANAGNTGCATGATCCANAGCGATTT Restriction Sites: NotI-NotI ACCN: NM_000232 Insert Size: 4000 bp OTI Disclaimer: Our molecular clone sequence data has been matched to the reference identifier above as a point of reference. Note that the complete sequence of our molecular clones may differ from the sequence published for this corresponding reference, e.g., by representing an alternative RNA splicing form or single nucleotide polymorphism (SNP). RefSeq: NM_000232.3, NP_000223.1 RefSeq Size: 4229 bp RefSeq ORF: 957 bp Locus ID: 6443

This product is to be used for laboratory only. Not for diagnostic or therapeutic use. ©2021 OriGene Technologies, Inc., 9620 Medical Center Drive, Ste 200, Rockville, MD 20850, US 2 / 3 beta Sarcoglycan (SGCB) (NM_000232) Human Untagged Clone – SC120022

UniProt ID: Q16585, Q5U0N0 Domains: sarcoglycan Families: Druggable Genome, Transmembrane Protein Pathways: Arrhythmogenic right ventricular cardiomyopathy (ARVC), Dilated cardiomyopathy, Hypertrophic cardiomyopathy (HCM), Viral myocarditis Summary: This gene encodes a member of the sarcoglycan family. are transmembrane components in the -glycoprotein complex which help stabilize the muscle fiber membranes and link the muscle cytoskeleton to the extracellular matrix. Mutations in this gene have been associated with limb-girdle muscular dystrophy.[provided by RefSeq, Oct 2008]

This product is to be used for laboratory only. Not for diagnostic or therapeutic use. ©2021 OriGene Technologies, Inc., 9620 Medical Center Drive, Ste 200, Rockville, MD 20850, US 3 / 3