Crohn’s disease H Hashimoto’s thyroiditis (also known Landry’s paralysis (also known as Crow-Fukase syndrome (also as chronic lymphocytic thyroiditis) Miller Fisher syndrome and Guillain- known as Takatsuki disease, PEP Hashimoto’s encephalitis or Barré syndrome) syndrome, and POEMS syndrome) encephalopathy Leukocytoclastic Henoch-Schönlein purpura (also (CFA; also known as idiopathic known as anaphylactoid purpura and purpura rheumatica) Ligneous conjunctivitis alveolitis) Herpes gestationis (also known as Limited systemic sclerosis (also Demyelinating neuropathies (also gestational pemphigoid) D known as limited systemic Horton disease (also known as giant and CREST syndrome) demyelinating diseases) cell , temporal arteritis, and Linear IgA disease (LAD; also Dermatomyositis (DM) cranial arteritis) known as adult linear IgA disease) Devic’s disease (also known as Hughes syndrome (also known as (also known as systemic neuromyelitis optica) antiphospholipid syndrome) lupus erythematosus) mellitus type 1 (also known Hypocortisolism (also known as Lyme disease, chronic as insulin-dependent diabetes and hypoadrenalism, Addison’s disease, ) Lymph node syndrome (also known as mucocutaneous lymph node Discoid lupus erythematosus (DLE) Hypogammaglobulinemia syndrome and ) Dressler’s syndrome (also known as Lymphoid hamartoma (also known postmyocardial syndrome) I disease (includes both Crohn’s as angiofollicular lymph node disease and ulcerative colitis) Duhring’s disease (also known as hyperplasia, Castleman’s disease, ) and giant lymph node hyperplasia) demyelinating diseases (also known Endocarditis lenta (also known as Marchiafava-Micheli syndrome (also as demyelinating neuropathies) E subacute bacterial endocarditis) M known as paroxysmal nocturnal Endometriosis hemoglobinuria) or Marie-Strümpell disease (also gastroenteritis known as ankylosing spondylitis Idiopathic thrombocytopenic Eosinophilic fasciitis and Bekhterev’s disease) purpura (ITP; also known as Ménière’s disease nodosum and Erythroblastopenia (also known as autoimmune thrombocytopenic (also pure red cell aplasia) purpura) known as microscopic polyarteritis) Essential mixed IgA nephropathy (also known as Miller Fisher syndrome (also known as Guillain-Barré syndrome and Evans syndrome synpharyngitic glomerulonephritis and Berger’s disease) Landry’s paralysis) Experimental allergic Mixed connective tissue disease encephalomyelitis (EAE) IgG4-related sclerosing disease (MCTD; also known as Sharp’s Inclusion body myositis Fibrosingalveolitis (also known as syndrome) F Insulin-dependent diabetes (also Moersch-Woltman condition (also known as type 1 diabetes and known as stiff person syndrome) Gestational pemphigoid (also known diabetes mellitus type 1) Mooren’s G as herpes gestationis) Interstitial cystitis (also known as Mucha-Habermann disease arteritis (also known as bladder pain syndrome) (also known as acute guttate temporal arteritis, cranial arteritis, Juvenile diabetes (also known as parapsoriasis, acute parapsoriasis, and Horton disease) J diabetes mellitus type 1, insulin- acute lichenoides, dependent diabetes, and type 1 Giant lymph node hyperplasia (also and parapsoriasis or pityriasis diabetes) known as lymphoid hamartoma, lichenoides et varioliformis acuta) angiofollicular lymph node Juvenile (also Mucocutaneous lymph node hyperplasia, and Castleman’s known as juvenile idiopathic arthritis syndrome (also known as lymph disease) and Still’s disease) node syndrome and Kawasaki Glomerulonephritis Kawasaki syndrome (also known disease) K as Kawasaki disease, lymph node Goodpasture’s syndrome syndrome, and mucocutaneous Granulomatosis with polyangiitis lymph node syndrome) (GPA; also known as Wegener’s Myositis granulomatosis) Kussmaul-Maier disease (also known as ) Narcolepsy Graves’ disease N Lambert-Eaton syndrome Neuromyelitis optica (also known as Guillain-Barré syndrome (also L (also known as Lambert-Eaton Devic’s disease) known as Landry’s paralysis and myasthenic syndrome) Miller Fisher syndrome) Neutropenia

2 Ocular cicatricial pemphigoid Progressive hemifacial atrophy Stiff person syndrome (also known O (also known as benign mucous (also known as Parry Romberg as Moersch-Woltman condition) membrane pemphigoid and scarring syndrome) Still’s disease (also known as pemphigoid) juvenile rheumatoid arthritis and Optic neuritis (also known as juvenile idiopathic arthritis) Ord’s thyroiditis arthritis psoriatica and arthropathic Subacute bacterial endocarditis Ormond’s disease (also known as psoriasis) (SBE; also known as endocarditis Pure red cell aplasia (also known as lenta) Palindromic rheumatism erythroblastopenia) Susac’s syndrome (also known as P retinocochleocerebral vasculopathy) Paraneoplastic cerebellar Purpura rheumatic (also known as degeneration Henoch-Schönlein purpura and Sydenham’s chorea (also known as anaphylactoid purpura) chorea minor) Parapsoriasis varioliformis (also known as Mucha-Habermann Pyoderma gangrenosum Sympathetic ophthalmia (SO) disease acute guttate parapsoriasis, Rasmussen’s encephalitis (also Synpharyngitic glomerulonephritis acute parapsoriasis, acute pityriasis R known as chronic focal encephalitis) (also known as Berger’s disease lichenoides, parapsoriasis or Raynaud’s phenomenon, disease, and IgA nephropathy) et varioliformis or syndrome Systemic chondromalacia (also acuta) (also known as known as Paroxysmal nocturnal Reiter’s syndrome) and atrophic polychondritis) hemoglobinuria (PNH; also known Systemic lupus erythematosus as Marchiafava-Micheli syndrome) (SLE; also known as lupus) Reiter’s syndrome (also known as Parry-Romberg syndrome (also reactive arthritis) Takatsuki disease (also known as known as progressive hemifacial T PEP syndrome, POEMS syndrome, Relapsing polychondritis (also atrophy) and Crow-Fukase syndrome) known as atrophic polychondritis Pars planitis (also known as and systemic chondromalacia) Takayasu’s arteritis or disease peripheral uveitis) Restless legs syndrome (also known Temporal arteritis (also known as Parsonage-Turner syndrome as Willis-Ekbom disease) , cranial arteritis, (also known as acute brachial and Horton disease) neuropathy, acute brachial Retinocochleocerebral vasculopathy Thrombocytopenic purpura radiculitis, neuralgic amyotrophy, (also known as Susac’s syndrome) (TTP; also known as idiopathic brachial neuritis, brachial plexus thrombocytopenic purpura and neuropathy, and brachial plexitis) as Ormond’s disease) autoimmune thrombocytopenic Pediatric autoimmune Rheumatic purpura) neuropsychiatric disorders Rheumatoid arthritis Tolosa-Hunt syndrome associated with streptococcus (PANDAS) Sarcoidosis (also known as Besnier- Transverse myelitis S Boeck disease) vulgaris Type I diabetes (also known as Scarring pemphigoid (also known diabetes mellitus type 1 and insulin- PEP syndrome (also known as as ocular cicatricial pemphigoid dependent diabetes) POEMS syndrome, Crow-Fukase and benign mucous membrane Types 1, 2, and 3 autoimmune syndrome, and Takatsuki disease) pemphigoid) polyglandular syndrome Peripheral neuropathy (also Schmidt’s syndrome (also known Ulcerative colitis known as autoimmune peripheral as autoimmune polyendocrine U neuropathy) syndrome type 2) Undifferentiated connective tissue disease (UCTD) Perivenous encephalomyelitis Schnitzler syndrome Urticarial vasculitis (also known as Pernicious anemia Scleritis chronic urticaria as a manifestation POEMS syndrome (also known as Scleroderma of venulitis) Crow-Fukase syndrome, Takatsuki disease, and PEP syndrome) Sharp’s syndrome (also known as Uveitis (also known as autoimmune mixed connective tissue disease) uveitis) Polyarteritis nodosa (also known as Kussmaul-Maier disease) Sicca syndrome (also known as Vasculitis Sjögren’s syndrome) V Vesiculobullous dermatosis Silk Road disease (also known as Polymyositis (PM) Behçet’s disease) Wegener’s granulomatosis (also Postmyocardial infarction syndrome Sjögren’s syndrome (also known as W known as granulomatosis with (also known as Dressler’s syndrome) Sicca syndrome) polyangiitis) Postpericardiotomy syndrome Sperm and testicular Willis-Ekbom disease (also known Primary biliary cirrhosis (PBC) Spot baldness (also known as as restless leg syndrome) Primary sclerosing cholangitis (PSC) )

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