Sclerocornea

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IMAGES IN CLINICAL PRACTICES Sclerocornea A term newborn delivered to a second gravida mother vaginally was noted to have an opacity in the right eye soon after birth. Eye examination revealed normal left eye and sclerisation of entire cornea on right side (Fig. 1). The thickness of opacity was more at periphery than at the center. Corneal diameter was 10 mm. The lid and adnexa were normal. Details of anterior chamber, iris and lens could not be made out. Margin of the pupil was Fig. 1. Complete opacification of right cornea. hazy. The intraocular pressure was normal. There was no facial asymmetry. Systemic opacity is more at center. The opacification examination was normal. There was no family affects the full thickness stroma that limits the history of a similar problem. A diagnosis of visualisation of posterior corneal surface and total sclerocornea was made. intraoccular structures. Histology includes disorganised collagenous tissue containing Sclerocornea, an uncommon develop- fibrils that is larger than normal. Potentially mental abnormality of anterior segment due co-existing abnormalities include shallow to mesenchymal dysgenesis presents as a anterior chamber, iris abnormalities and stationary congenital anomaly. It is usually microphthalmos. Systemic abnormalities like seen as an isolated ocular abnormality limb deformities, craniofacial and genito- involving both eyes. Occurs sporadically but urinary defects can also accompany. In may be familial or autosomal dominant in generalised sclerocornea early keratoplasty inheritance. Clinically, most often there is should be considered in an effort to provide peripheral, white, vascularised 1-2 mm vision. cornea1 rim that blends with sclera obliterating the limbus. The central cornea is Y. Ramesh Bhat, generally normal. In total sclerocornea, the K.M. Sanoj, entire cornea is involved but the center of the Department of Pediatrics, cornea is clearer than periphery, which Kasturba Medical College, distinguish it from. Peters’ anomaly where Manipal 576104, Karnataka, India. INDIAN PEDIATRICS 277 VOLUME 42__MARCH 17, 2005.

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