Vascular Lesions of the Orbit Two Basic Lesion Types
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1 Q Vascular Lesions of the Orbit Two basic lesion types ?? 2 A Vascular Lesions of the Orbit Two basic lesion types Hemangiomas Malformations 3 Q Vascular Lesions of the Orbit Hemangiomas Malformations ?? 4 A Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary hemangioma hemangioma 5 Q Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary ? hemangioma hemangioma ? ? ? 6 A Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma AVM Port wine stain 7 Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma AVM Note: The 2018-19 edition of the BCSC Peds book indicates that the terms strawberry hemangioma and capillary hemangioma are outdated, and such Port wine lesions should be referred to simply as ‘hemangiomas.’ However, it also stain acknowledges that these terms persist in the ophthalmic literature. Because our community continues to use them, they will be included in this slide-set. 8 Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma AVM Note: The 2018-19 edition of the BCSC Peds book indicates that the terms strawberry hemangioma and capillary hemangioma are outdated, and such Port wine lesions should be referred to simply as ‘hemangiomas.’ However, it also stain acknowledges that these terms persist in the ophthalmic literature. Because our community continues to use them, they will be included in this slide-set. Note also that the so-called cavernous hemangioma is considered (and therefore included with) the ‘malformations.’ 9 Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma OrbitalLymphangioma lymphatic malformation AVM Finally: Note that, per both the Peds and Orbit books, the term Port wine lymphangioma has been replaced with orbital lymphatic malformation. stain 10 Q Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in termsAVM of prevalence? It is the most common Port wine stain Is there a gender predilection? Yes, it is more common in girls At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months What is the origin of these lesions? It’s not known for certain, but some experts believe they originate as nests of placental cells that ‘metastasized’ to the fetus What is the ‘life cycle’ of capillary hemangiomas? --Initially they grow, reaching maximum size by around age 12 months --Then they involute beginning at about age 2 years --75% will resolve by age 4-5 years 11 Q/A Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in termsAVM of prevalence? It is the mostmost v common least Port wine stain Is there a gender predilection? Yes, it is more common in girls At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months What is the origin of these lesions? It’s not known for certain, but some experts believe they originate as nests of placental cells that ‘metastasized’ to the fetus What is the ‘life cycle’ of capillary hemangiomas? --Initially they grow, reaching maximum size by around age 12 months --Then they involute beginning at about age 2 years --75% will resolve by age 4-5 years 12 A Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in termsAVM of prevalence? It is the most common Port wine stain Is there a gender predilection? Yes, it is more common in girls At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months What is the origin of these lesions? It’s not known for certain, but some experts believe they originate as nests of placental cells that ‘metastasized’ to the fetus What is the ‘life cycle’ of capillary hemangiomas? --Initially they grow, reaching maximum size by around age 12 months --Then they involute beginning at about age 2 years --75% will resolve by age 4-5 years 13 Q Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in termsAVM of prevalence? It is the most common Port wine stain Is there a genderWhat predilection? proportion of newborns have an orbital hemangioma? Yes, it is more1-3% common in girls At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months What is the origin of these lesions? It’s not known for certain, but some experts believe they originate as nests of placental cells that ‘metastasized’ to the fetus What is the ‘life cycle’ of capillary hemangiomas? --Initially they grow, reaching maximum size by around age 12 months --Then they involute beginning at about age 2 years --75% will resolve by age 4-5 years 14 A Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in termsAVM of prevalence? It is the most common Port wine stain Is there a genderWhat predilection? proportion of newborns have an orbital hemangioma? Yes, it is more1-3% common in girls At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months What is the origin of these lesions? It’s not known for certain, but some experts believe they originate as nests of placental cells that ‘metastasized’ to the fetus What is the ‘life cycle’ of capillary hemangiomas? --Initially they grow, reaching maximum size by around age 12 months --Then they involute beginning at about age 2 years --75% will resolve by age 4-5 years 15 Q Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in terms of prevalence? second- AVM It is the most common ^ ? Port wine stain Is there a gender predilection? What vascular tumor is the next most common? Yes, it is more common in girls Orbital lymphangioma At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months What is the origin of these lesions? It’s not known for certain, but some experts believe they originate as nests of placental cells that ‘metastasized’ to the fetus What is the ‘life cycle’ of capillary hemangiomas? --Initially they grow, reaching maximum size by around age 12 months --Then they involute beginning at about age 2 years --75% will resolve by age 4-5 years 16 A Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in terms of prevalence? second- AVM It is the most common ^ ? Port wine stain Is there a gender predilection? What vascular tumor is the next most common? Yes, it is more common in girls Orbital lymphangioma At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months What is the origin of these lesions? It’s not known for certain, but some experts believe they originate as nests of placental cells that ‘metastasized’ to the fetus What is the ‘life cycle’ of capillary hemangiomas? --Initially they grow, reaching maximum size by around age 12 months --Then they involute beginning at about age 2 years --75% will resolve by age 4-5 years 17 Q Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in termsAVM of prevalence? It is the most common Port wine stain Is there a gender predilection? Yes, it is more common in girls At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months What is the origin of these lesions? It’s not known for certain, but some experts believe they originate as nests of placental cells that ‘metastasized’ to the fetus What is the ‘life cycle’ of capillary hemangiomas? --Initially they grow, reaching maximum size by around age 12 months --Then they involute beginning at about age 2 years --75% will resolve by age 4-5 years 18 Q/A Vascular Lesions of the Orbit Hemangiomas Malformations Strawberry Capillary Cavernous hemangioma hemangioma hemangioma Lymphangioma Among the orbital vascular lesions, where does the capillary hemangioma rank in termsAVM of prevalence? It is the most common Port wine stain Is there a gender predilection? Yes, it is more common in girlsM v F At what age do orbital capillary hemangiomas present? About 1/3 are present at birth; almost all have ‘declared’ by age 6 months