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Rare Lung Disease Guide

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Rare Lung Disease Guide AMERICAN THORACIC SOCIETY INTERNATIONAL CONFERENCE Rare Lung Disease Guide Where today’s science meets tomorrow’s careTM Dallas, TX May 17 - May 22, 2019 conference.thoracic.org May 2019 Dear Colleagues: The scope of the American Thoracic Society is amazingly broad — covering pulmonary, critical care, and sleep medicine. The challenge that we face each year as we put the International Conference program together is that some clinical topics that may be of central importance to our members, conference attendees and patients may not be prominently featured in the program. This is especially the case with some rare lung diseases. With each challenge though, comes opportunity. Because of the wealth of scientific and clinical information presented at ATS 2019, these diseases, though uncommon, will be the focus of many presentations over the next several days. The purpose of this Rare Lung Disease Guide is to help you more easily find these presentations. Jess Mandel, MD In his chapter on rare lung diseases in “Breathing in America: Diseases, Progress, and Hope” (2010) Francis X. McCormack, MD noted that research on Chair, ATS International uncommon respiratory diseases has produced some of the most exciting discoveries in pulmonary medicine, stating that “Insights gained from uncommon Conference Committee lung diseases often shed light on the more common ones.” The definition of a rare disease by its prevalence varies by country. In the European Union, for instance, it is defined as a disease that affects fewer than 1 in 2,000 while in the United States it is a disease that affects fewer than 1 in 200,000. This guide was compiled by a small group of ATS Members who studied the ATS 2019 abstracts — authors requested to be considered for inclusion. Many thanks to Dr. Nishant Gupta, Dr. Jonathan Kropski, Dr. Lisa Young, Dr. Cormac McCarthy, and Dr. Justin Hewlett for their assistance with this resource. There are a number of patient advocacy groups that are exhibiting at ATS 2019. In addition to attending the presentations noted within, I encourage you to visit with them to learn more about these rare conditions. Groups listed in BOLD are members of the ATS Public Advisory Roundtable and can all be found in or near PAR PATH, near the ATS Center in the Exhibit Hall. Learn more about this group and its many contributions to the Society and its work at: www. thoracic.org/patients/par/. Sincerely, Jess Mandel, MD Chair, ATS International Conference Committee Alpha-1 Foundation: Booth 3021 Lung Transplant Foundation: Booth 2817 Allergy and Asthma Network: Booth 2916 LUNGevity Foundation: Booth 2923 ARDS Foundation: Booth 2823 NTM Info & Research, Inc.: Booth 2815 Children’s Interstitial Lung Disease Foundation, Inc. (CHILD): Booth 2816 Primary Ciliary Dyskinesia Foundation (PCD): Booth 2920 Foundation for Sarcoidosis Research: Booth 2921 Pulmonary Fibrosis Foundation: Booth 3126 Hermansky-Pudlak Syndrome Network, Inc.: Booth 2915 Scleroderma Foundation: Booth 2917 The LAM Foundation/Lymphangioleiomyomatosis: Booth 2820 Tuberous Sclerosis Alliance: Booth 2821 List Current as of 4/2/19 DISCLAIMER The purpose of this guide is to help the American Thoracic Society International Conference attendees navigate the viewing of posters for disorders that typically get less attention at the conference because of their rarity. During abstract submission, authors were instructed to check the box for consideration in the Rare Lung Disease Guide; the abstracts on that list were then further narrowed down. Conditions represented by less than 50 abstracts were considered for inclusion. We regret that not all rare diseases could be represented, and welcome suggestions for additional categories for listing in future editions. Please email us with any suggestions: [email protected]. Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location AMYLOIDOSIS Sunday, P557 9:15 am-4:15 pm Sarcoloidosis: A Rare Case Of Co-Existent Systemic Sarcoidosis And A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD May 19, 2019 Amyloidosis P1005 9:15 am-4:15 pm A48: CRITICAL CARE CASE REPORTS: CAUSES AND A Case Of Fatal Respiratory Failure Caused By Diaphragmatic Amyloidosis COMPLICATIONS OF ACUTE RESPIRATORY FAILURE Area G (Hall F, Level 2), KBHCCD Monday, P295 9:15 am-4:15 pm Rare Cause Of Chronic Cough From Pulmonary Amyloidosis B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD May 20, 2019 P383 9:15 am-4:15 pm Primary Pleural Amyloidosis With Isolated Endobronchial Lesion B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Tuesday, P507 9:15 am-4:15 pm Amyloidosis Diagnosed By Endobronchial Ultrasound-Guided Transbronchial C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II May 21, 2019 Needle Aspirate Area D (Hall F, Level 2), KBHCCD Wednesday, May P430 9:15 am-3:30 pm Heart-Lung-Kidney Transplantation For Transthyretin (TTR)-Related Hereditary D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE Area D (Hall F, Level 2), KBHCCD 22, 2019 Amyloidosis REPORTS P502 9:15 am-3:30 pm Hiding In Plain Sight D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD P494 9:15 am-3:30 pm A Unique Case Of Diffuse Alveolar-Septal Pulmonary Amyloidosis D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD P493 9:15 am-3:30 pm Amyloid Lung: A Rare Entity Of Pulmonary Nodule D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD P567 9:15 am-3:30 pm A Case Report Of Tracheo-Bronchial Amyloidosis D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD P619 9:15 am-3:30 pm Persistent Pulmonary Pleural Effusions In A Patient With Systemic Amyloidosis D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD AV MALFORMATION Sunday, P842 11:15 am-1:00 pm Platypnea Orthodeoxia Syndrome Following A Submassive Pulmonary A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD May 19, 2019 Embolism Monday, P296 11:15 am-1:00 pm Hemoptysis Due To A Bleeding Bronchial Dieulafoy Lesion Treated Successfully B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I May 20, 2019 With Arterial Embolization And Argon Plasma Coagulation Area C (Hall F, Level 2), KBHCCD P951 11:15 am-1:00 pm Anomalous Descending Aorta To Pulmonary Vein Fistula: A Rare Clinical Entity B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD 3 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P964 11:15 am-1:00 pm Hemothorax Secondary To Pulmonary AVM: A Near-Fatal Presentation With B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD May 20, 2019 Difficult Management P971 11:15 am-1:00 pm Not So Asymptomatic: A Large Pulmonary Arteriovenous Malformation B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD P331 11:15 am-1:00 pm Recurrent Hemoptysis Due To Diffuse Endobronchial Telangiectasia B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Wednesday, May 22, 2019 P562 11:15 am-1:00 pm Solitary Pulmonary Nodule (SPN): Step Back Before A Needle D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD BENIGN METASTASIZING LEIOMYOMA Wednesday, May P472 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm A Case Of Not So "Benign" Metastasizing Leiomyomatosis P261 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Poster Viewing 11:15 am-1:00 pm Cancer Not Cancer: A Rare Case Of Metastatic Pulmonary Nodules Area C (Hall F, Level 2), KBHCCD P255 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Poster Viewing 11:15 am-1:00 pm Pulmonary Benign Metastasizing Leiomyoma: A Case Report Area C (Hall F, Level 2), KBHCCD P308 9:15 am-3:30 pm A Woman With Bilateral Pulmonary Nodules: A Rare Case Of Benign D62: THORACIC ONCOLOGY CASE REPORTS II Poster Viewing 11:15 am-1:00 pm Metastasizing Leiomyoma Area C (Hall F, Level 2), KBHCCD BIRT-HOGG-DUBE SYNDROME Tuesday, 9:15 am-11:15 am Canonical WNT Signaling Activity Is Decreased In Multiple Models Of Birt- C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD May 21, 2019 Oral Presentation 10:45 am-11:00 am Hogg-Dube An Unsuspected Cause Of Spontaneous Pneumothorax: Birt-Hogg-Dube C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD P991 9:15 am-4:15 pm Syndrome Wednesday, May P489 9:15 am-3:30 pm A Rare Form Of Cystic Lung Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 A Pulmonologist's Conundrum: A Patient With Triple Threat Of Pulmonary D39: RARE DPLD CASE REPORTS P488 9:15 am-3:30 pm Embolism, Cystic Lung Disease, And Pneumothorax Area D (Hall F, Level 2), KBHCCD Severe Cystic Lung Disease And A Renal Mass In A 35-Year-Old Man: Diagnostic D39: RARE DPLD CASE REPORTS P486 9:15 am-3:30 pm And Management Challenges Area D (Hall F, Level 2), KBHCCD 4 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, May 22, 2019 P501 9:15 am-3:30 pm Birt-Hogg-Dubé Syndrome Diagnosed In A Patient Presenting With Dyspnea D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD BRONCHIOLITIS Sunday, A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH P1052 9:15 am-4:15 pm Forced Oscillation Technique In The Evaluation Of Biopsy-Confirmed Area H (Hall F, Level 2), KBHCCD May 19, 2019 Constrictive Bronchiolitis In A Southwest Asia Deployed Veteran INHALATIONAL EXPOSURES
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