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Rare Lung Disease Guide

Rare Lung Disease Guide

AMERICAN THORACIC SOCIETY INTERNATIONAL CONFERENCE Rare Disease Guide

Where today’s science meets tomorrow’s careTM

Dallas, TX May 17 - May 22, 2019    conference.thoracic.org May 2019 Dear Colleagues: The scope of the American Thoracic Society is amazingly broad ­— covering pulmonary, critical care, and sleep medicine. The challenge that we face each year as we put the International Conference program together is that some clinical topics that may be of central importance to our members, conference attendees and patients may not be prominently featured in the program. This is especially the case with some rare lung diseases. With each challenge though, comes opportunity. Because of the wealth of scientific and clinical information presented at ATS 2019, these diseases, though uncommon, will be the focus of many presentations over the next several days. The purpose of this Rare Lung Disease Guide is to help you more easily find these presentations. Jess Mandel, MD In his chapter on rare lung diseases in “Breathing in America: Diseases, Progress, and Hope” (2010) Francis X. McCormack, MD noted that research on Chair, ATS International uncommon respiratory diseases has produced some of the most exciting discoveries in pulmonary medicine, stating that “Insights gained from uncommon Conference Committee lung diseases often shed light on the more common ones.” The definition of a rare disease by its prevalence varies by country. In the European Union, for instance, it is defined as a disease that affects fewer than 1 in 2,000 while in the United States it is a disease that affects fewer than 1 in 200,000. This guide was compiled by a small group of ATS Members who studied the ATS 2019 abstracts — authors requested to be considered for inclusion. Many thanks to Dr. Nishant Gupta, Dr. Jonathan Kropski, Dr. Lisa Young, Dr. Cormac McCarthy, and Dr. Justin Hewlett for their assistance with this resource. There are a number of patient advocacy groups that are exhibiting at ATS 2019. In addition to attending the presentations noted within, I encourage you to visit with them to learn more about these rare conditions. Groups listed in BOLD are members of the ATS Public Advisory Roundtable and can all be found in or near PAR PATH, near the ATS Center in the Exhibit Hall. Learn more about this group and its many contributions to the Society and its work at: www. thoracic.org/patients/par/.

Sincerely, Jess Mandel, MD Chair, ATS International Conference Committee

Alpha-1 Foundation: Booth 3021 Lung Transplant Foundation: Booth 2817 Allergy and Network: Booth 2916 LUNGevity Foundation: Booth 2923 ARDS Foundation: Booth 2823 NTM Info & Research, Inc.: Booth 2815 Children’s Interstitial Lung Disease Foundation, Inc. (CHILD): Booth 2816 Primary Ciliary Dyskinesia Foundation (PCD): Booth 2920 Foundation for Research: Booth 2921 Foundation: Booth 3126 Hermansky-Pudlak Syndrome Network, Inc.: Booth 2915 Scleroderma Foundation: Booth 2917 The LAM Foundation/: Booth 2820 Alliance: Booth 2821

List Current as of 4/2/19 DISCLAIMER The purpose of this guide is to help the American Thoracic Society International Conference attendees navigate the viewing of posters for disorders that typically get less attention at the conference because of their rarity. During abstract submission, authors were instructed to check the box for consideration in the Rare Lung Disease Guide; the abstracts on that list were then further narrowed down. Conditions represented by less than 50 abstracts were considered for inclusion. We regret that not all rare diseases could be represented, and welcome suggestions for additional categories for listing in future editions. Please email us with any suggestions: [email protected]. Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

AMYLOIDOSIS

Sunday, P557 9:15 am-4:15 pm Sarcoloidosis: A Rare Case Of Co-Existent Systemic Sarcoidosis And A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD May 19, 2019 Amyloidosis

P1005 9:15 am-4:15 pm A48: CRITICAL CARE CASE REPORTS: CAUSES AND A Case Of Fatal Caused By Diaphragmatic Amyloidosis COMPLICATIONS OF ACUTE RESPIRATORY FAILURE Area G (Hall F, Level 2), KBHCCD

Monday, P295 9:15 am-4:15 pm Rare Cause Of Chronic Cough From Pulmonary Amyloidosis B41: INTERVENTIONAL CASE REPORTS I Area C (Hall F, Level 2), KBHCCD May 20, 2019 P383 9:15 am-4:15 pm Primary Pleural Amyloidosis With Isolated Endobronchial Lesion B43: CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Tuesday, P507 9:15 am-4:15 pm Amyloidosis Diagnosed By Endobronchial Ultrasound-Guided Transbronchial C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II May 21, 2019 Needle Aspirate Area D (Hall F, Level 2), KBHCCD

Wednesday, May P430 9:15 am-3:30 pm -Lung- Transplantation For Transthyretin (TTR)-Related Hereditary D38: AND DRUG RELATED CASE Area D (Hall F, Level 2), KBHCCD 22, 2019 Amyloidosis REPORTS

P502 9:15 am-3:30 pm Hiding In Plain Sight D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P494 9:15 am-3:30 pm A Unique Case Of Diffuse Alveolar-Septal Pulmonary Amyloidosis D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P493 9:15 am-3:30 pm Amyloid Lung: A Rare Entity Of Pulmonary Nodule D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P567 9:15 am-3:30 pm A Case Report Of Tracheo-Bronchial Amyloidosis D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P619 9:15 am-3:30 pm Persistent Pulmonary Pleural Effusions In A Patient With Systemic Amyloidosis D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

AV MALFORMATION Sunday, P842 11:15 am-1:00 pm Platypnea Orthodeoxia Syndrome Following A Submassive Pulmonary A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD May 19, 2019 Embolism Monday, P296 11:15 am-1:00 pm Due To A Bleeding Bronchial Dieulafoy Lesion Treated Successfully B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I May 20, 2019 With Arterial Embolization And Argon Plasma Coagulation Area C (Hall F, Level 2), KBHCCD

P951 11:15 am-1:00 pm Anomalous Descending Aorta To Pulmonary Vein Fistula: A Rare Clinical Entity B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

3 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P964 11:15 am-1:00 pm Secondary To Pulmonary AVM: A Near-Fatal Presentation With B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD May 20, 2019 Difficult Management

P971 11:15 am-1:00 pm Not So Asymptomatic: A Large Pulmonary Arteriovenous Malformation B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

P331 11:15 am-1:00 pm Recurrent Hemoptysis Due To Diffuse Endobronchial Telangiectasia B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Wednesday, May 22, 2019 P562 11:15 am-1:00 pm Solitary Pulmonary Nodule (SPN): Step Back Before A Needle D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

BENIGN METASTASIZING LEIOMYOMA Wednesday, May P472 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm A Case Of Not So "Benign" Metastasizing Leiomyomatosis

P261 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Poster Viewing 11:15 am-1:00 pm Cancer Not Cancer: A Rare Case Of Metastatic Pulmonary Nodules Area C (Hall F, Level 2), KBHCCD

P255 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Poster Viewing 11:15 am-1:00 pm Pulmonary Benign Metastasizing Leiomyoma: A Case Report Area C (Hall F, Level 2), KBHCCD

P308 9:15 am-3:30 pm A Woman With Bilateral Pulmonary Nodules: A Rare Case Of Benign D62: THORACIC ONCOLOGY CASE REPORTS II Poster Viewing 11:15 am-1:00 pm Metastasizing Leiomyoma Area C (Hall F, Level 2), KBHCCD

BIRT-HOGG-DUBE SYNDROME Tuesday, 9:15 am-11:15 am Canonical WNT Signaling Activity Is Decreased In Multiple Models Of Birt- C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD May 21, 2019 Oral Presentation 10:45 am-11:00 am Hogg-Dube An Unsuspected Cause Of Spontaneous : Birt-Hogg-Dube C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD P991 9:15 am-4:15 pm Syndrome

Wednesday, May P489 9:15 am-3:30 pm A Rare Form Of Cystic Lung Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 A Pulmonologist's Conundrum: A Patient With Triple Threat Of Pulmonary D39: RARE DPLD CASE REPORTS P488 9:15 am-3:30 pm Embolism, Cystic Lung Disease, And Pneumothorax Area D (Hall F, Level 2), KBHCCD

Severe Cystic Lung Disease And A Renal Mass In A 35-Year-Old Man: Diagnostic D39: RARE DPLD CASE REPORTS P486 9:15 am-3:30 pm And Management Challenges Area D (Hall F, Level 2), KBHCCD 4 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, May 22, 2019 P501 9:15 am-3:30 pm Birt-Hogg-Dubé Syndrome Diagnosed In A Patient Presenting With Dyspnea D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

BRONCHIOLITIS

Sunday, A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH P1052 9:15 am-4:15 pm Forced Oscillation Technique In The Evaluation Of -Confirmed Area H (Hall F, Level 2), KBHCCD May 19, 2019 Constrictive In A Southwest Asia Deployed Veteran INHALATIONAL EXPOSURES Monday, Murine Modeling Of Deployment-Related Chronic Bronchiolitis By B28: HOW AIRWAYS MALFUNCTION: NEW CONCEPTS May 20, 2019 317 9:15 am-11:15 am Conditional Depletion Of Airway Club Cells Ballroom A Four (Level 2), KBHCCD

P956 9:15 am-4:15 pm Who Group What, Where, When, Why And How B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

B107: EFFECTS OF E-CIGARETTES AND THEIR COMPONENTS ON 709 2:15 pm-4:15 pm Airway Epithelial Progenitor Cell Dysfunction After Flavoring-Induced Vapor Ballroom D Four (Level 3), KBHCCD Exposure RESPIRATORY DYSFUNCTION, INFLAMMATION, AND REPAIR

Tuesday, Parametric Response Mapping Identifies Increased Functional Small Airways C15: OCCUPATIONAL EXPOSURES OF THE 21ST CENTURY Room D167/D174 (Level 1), KBHCCD May 21, 2019 9:15 am-11:15 am Disease In Soldiers With Biopsy Evidence Of Chronic Bronchiolitis

Follicular Bronchiolitis — A Diffuse Cystic Lung Disease Masquerading As C72: CASE REPORTS OF RARE DISEASES P1000 9:15 am-4:15 pm Severe Area G (Hall F, Level 2), KBHCCD

Wednesday, May D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND 113 9:15 am-11:15 am L-CSA, A Liposomal Formulation Of Cyclosporine A, Demonstrates Therapeutic Room C140/C142 (Level 1), KBHCCD 22, 2019 Potential For Bronchiolitis Obliterans Syndrome (BOS) TRANSPLANT

Idiopathic Obliterative Bronchiolitis Masquerading As Interstitial Lung D40: NON-INFLAMMATORY DPLDs CASE REPORTS P513 9:15 am-3:30 pm Disease Area D (Hall F, Level 2), KBHCCD

A Case Of Bronchiolitis Obliterates Diagnosed By An Ultrathin Bronchoscopy D40: NON-INFLAMMATORY DPLDs CASE REPORTS P516 9:15 am-3:30 pm After Bone Marrow Transplantation Area D (Hall F, Level 2), KBHCCD

P544 9:15 am-3:30 pm A Rarity In The Airways D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

CASTLEMAN’S DISEASE Sunday, P1118 9:15 am-4:15 pm A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS Sarcomatoid Carcinoma Of The Lung: A Rare And Unfortunate Disease Area J (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm NOT ALWAYS WHAT YOU GET 5 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location CTD-ILD Sunday, 505 2:15 pm-4:15 pm May 19, 2019 Poster Viewing 2:15 pm-2:45 pm Plasma Biomarkers Of Survival In Patients With Interstitial Lung Disease A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm

P177 9:15 am-4:15 pm Nailfold Capillaroscopy Findings In Ild Patients: Results From A Single Centre A37: DISEASE-INTERSTITIAL LUNG DISEASE Poster Viewing 11:15 am-1:00 pm Investigation Area B (Hall F, Level 2), KBHCCD

504 2:15 pm-4:15 pm Nailfold Capillaroscopy In A Prospective Interstitial Lung Disease (ILD) Cohort: Poster Viewing 2:15 pm -2:45 pm A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm IPF, CTD-ILD And IPAF Monday, 9:15 am-11:15 am Epidemiology And Effect Of Therapy In Patients With Interstitial B17: ADVANCES IN ILD THERAPY Room C155-C156 (Level 1), KBHCCD May 20, 2019 Oral Presentation 10:30 am-10:45 am With Autoimmune Features (IPAF)

P203 9:15 am-4:15 pm Prognostic Analysis Of Idiopathic Interstitial With Rheumatologic B46: IDIOPATHIC INTERSTITIAL PNEUMONIA: NATURAL HISTORY Poster Viewing 2:15 pm-2:45 pm Features: A Prospective Multicenter Cohort Study (Pair Cohort Study) Area B (Hall F, Level 2), KBHCCD Tuesday, P559 9:15 am-4:15 pm Relapsing Polychondritis Patients With Have A Lower FEV1/ C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT May 21, 2019 Poster Viewing 11:15 am-1:00 pm FVC And FEF 25-75% As Well As A Previous Diagnosis Of Asthma Area D (Hall F, Level 2), KBHCCD

P582 9:15 am-4:15 pm Long-Term Evaluation Of Pulmonary Function Tests In Subgroups Of Patients C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Poster Viewing 11:15 am-1:00 pm With Interstitial Pneumonia With Autoimmune Features Area D (Hall F, Level 2), KBHCCD

P1049 9:15 am-4:15 pm Autoimmune Serologies Predict Response To Treatment In Patients With C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Poster Viewing 11:15 am-1:00 pm Connective Tissue Related Interstitial Lung Disease (CTD-ILD) Area H (Hall F, Level 2), KBHCCD P1050 9:15 am-4:15 pm Effect Of Cotreatment With Corticosteroids In Connective Tissue Related Lung C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Disease (CTD-ILD) Patients On Mycophenolate Mofetil (MMF)

P1057 9:15 am-4:15 pm Prognosis And Pulmonary Manifestations Of A Cohort Of Patients Positive To C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Poster Viewing 11:15 am-1:00 pm TH/TO Autoantibodies. Area H (Hall F, Level 2), KBHCCD Wednesday, May 9:15 am-11:15 am Hospital Length Of Stay Following Lung Transplantation For Connective 22, 2019 Poster Viewing 11:15 am-1:00 pm Tissue Disease-Associated Interstitial Lung Disease And Idiopathic Pulmonary D13: TRANSPLANTATION Room C146 (Level 1), KBHCCD Oral Presentation 10:45 am-11:00 am Fibrosis

6 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, May 103 9:15 am-11:15 am Comparative Evaluation Of Radiographic And Autoimmune Serologic Features D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND 22, 2019 Poster Viewing 11:15 am-1:00 pm TRANSPLANT Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Between ANCA-Associated ILD And IPAF

CYSTIC LUNG DISEASE ­— OTHER

Sunday, A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE P1105 9:15 am-4:15 pm Unusual Case Of Diffuse Cystic Lung Disease Due To Metastatic Area J (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Choriocarcinoma IS NOT ALWAYS WHAT YOU GET

A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE P1131 9:15 am-4:15 pm A Brewing Case Of Malt Lymphoma: Primary Pulmonary Lymphoma Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Presenting As Cystic Lung Disease IS NOT ALWAYS WHAT YOU GET Monday, P607 9:15 am-4:15 pm B64: COPD: MECHANISM AND TREATMENT May 20, 2019 Poster Viewing 11:15 am-1:00 pm A Case Of Vanishing Lung Syndrome: A Rare Form Of Bullous Emphysema Area D (Hall F, Level 2), KBHCCD Tuesday, P1000 9:15 am-4:15 pm Follicular Bronchiolitis — A Diffuse Cystic Lung Disease Masquerading As C72: CASE REPORTS OF RARE DISEASES May 21, 2019 Poster Viewing 11:15 am-1:00 pm Severe Obstructive Lung Disease Area G (Hall F, Level 2), KBHCCD Wednesday, May P464 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS 22, 2019 Poster Viewing 11:15 am-1:00 pm A Rare Etiology Of Diffuse Cystic Lung Disease Area D (Hall F, Level 2), KBHCCD

P474 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Poster Viewing 11:15 am-1:00 pm Cystic Lung: Manifestation Of Light Chain Deposition Disease Area D (Hall F, Level 2), KBHCCD

P485 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Poster Viewing 11:15 am-1:00 pm An Uncommon Cause Of Cystic Lung Disease Area D (Hall F, Level 2), KBHCCD P495 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Holy ! A Rare Pulmonary Manifestation Of Von Recklinghausen's Disease

P522 9:15 am-3:30 pm D40: NON-INFLAMMATORY DPLDs CASE REPORTS Poster Viewing 11:15 am-1:00 pm Smoking-Related Diffuse Cystic Lung Disease Area D (Hall F, Level 2), KBHCCD

DERMATOMYOSITIS/ANTISYNTHETASE SYNDROME

Sunday, P178 9:15 am-4:15 pm Diverse Clinical Features Of Interstitial Lung Disease In Patients With The Anti- A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE May 19, 2019 Poster Viewing 11:15 am-1:00 pm SSA-52 KD Myositis-Associated Autoantibody Area B (Hall F, Level 2), KBHCCD

7 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P184 9:15 am-4:15 pm Prognostic Factors Of Clinical Evolution In Patients With Antisynthetase A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Syndrome Treated With Methotrexate, Leflunomide & Prednisone

P185 9:15 am-4:15 pm Prevalence And Diagnostic Implications Of Myositis-Specific Antibodies In A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Poster Viewing 11:15 am-1:00 pm Interstitial Lung Disease Area B (Hall F, Level 2), KBHCCD

P190 9:15 am-4:15 pm Significance And Predictive Factors Of Recurrence In Anti-Aminoacyl-TRNA A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Poster Viewing 11:15 am-1:00 pm Synthetase Antibodies-Interstitial Lung Disease Area B (Hall F, Level 2), KBHCCD Tuesday, P576 9:15 am-4:15 pm Clinical Characteristics Dermatomyositis/Polymyositis Associated Interstitial C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT May 21, 2019 Poster Viewing 11:15 am-1:00 pm Lung Disease According To The Autoantibody Area D (Hall F, Level 2), KBHCCD

P577 9:15 am-4:15 pm Methotrexate Leflunomide In The Treatment Of Patients With Interstitial Lung C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Poster Viewing 11:15 am-1:00 pm Disease Positive To Antisynthetase Autoantibodies (Antisynthetase Syndrome) Area D (Hall F, Level 2), KBHCCD

P580 9:15 am-4:15 pm The Change Of Ct Findings Of Treatment In Anti-MDA5 Autoantibodies C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Poster Viewing 11:15 am-1:00 pm Positive Dermatomyositis And RP-ILD Area D (Hall F, Level 2), KBHCCD Secondary Pulmonary Alveolar Proteinosis Presenting As Steroid Non- P956 9:15 am-4:15 pm C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND Responsive Interstitial Lung Disease In Anti-MDA5 Associated Amyopathic CLINICAL STUDIES Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Dermatomyositis 125 2:15 pm-4:15 pm Prognostic Significance Of Macrophage-Mannose Receptor, CD206, In Anti- C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL Poster Viewing 2:15 pm-2:45 pm HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm MDA5 Antibody-Positive Dermatomyositis-Associated Interstitial Lung Disease

Wednesday, May 104 9:15 am-11:15 am 22, 2019 Anti-TRNA Synthetase And Anti-PM/SCL Antibody Status Is Associated With D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND Poster Viewing 9:15 am-10:00 am TRANSPLANT Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Distinct Immunophenotypes Irrespective Of Clinical Classification

DIPNECH

Wednesday, May P491 9:15 am-3:30 pm A Rare Case Report: Diffuse Idiopathic Pulmonary Neuroendocrine Cell D39: RARE DPLD CASE REPORTS 22, 2019 Poster Viewing 11:15 am-1:00 pm Area D (Hall F, Level 2), KBHCCD P552 9:15 am-3:30 pm 30-Year-Old Female With Chronic Cough: A Presentation Of Diffuse Idiopathic D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Neuroendocrine Cell Hyperplasia (DIPNECH)

8 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location DRUG INDUCED LUNG DISEASE

Sunday, P471 9:15 am-4:15 pm IMATINIB-Induced Associated With “Radiation-Recall” Pattern May 19, 2019 In A Patient With Chronic Myelogenous Leukemia And Prior , A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm , And Immunotherapy For Non-Small Cell Lung Cancer D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P472 9:15 am-4:15 pm Acute Drug-Induced Pneumonitis From Brentuximab Therapy Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm REPORTS P475 9:15 am-4:15 pm A Case Of Secondary To Ustekinumab In The A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Treatment Of Crohn's Disease P478 9:15 am-4:15 pm Ruxolitinib Discontinuation Syndrome In A Patient With Myelofibrosis To A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Acute Myeloid Leukemia Transformation P480 9:15 am-4:15 pm Unexplained Diffuse Alveolar Hemorrhage Associated With Recent Gingko A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Use P481 9:15 am-4:15 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Long Term Consequences Of A Rare Entity: Severe Contrast Aspiration P487 9:15 am-4:15 pm Onset Of ILD And Exacerbation Of Long Standing Myositis By Statin In Patient A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm With Anti-Hmgcr Antibody P493 9:15 am-4:15 pm Enasidenib Causing Differentiation Syndrome And Pulmonary Complications A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm In A Patient With Acute Myeloid Leukemia P497 9:15 am-4:15 pm Mammalian Target Of Rapamycin (MTOR) Inhibitor Induced Pulmonary A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Alveolar Proteinosis D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P498 9:15 am-4:15 pm Dyspnea And Dry Eyes After Pembrolizumab Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm REPORTS D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P501 9:15 am-4:15 pm Dress Syndrome Without Eosinophilia And Tuberculosis Treatment Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm REPORTS P505 9:15 am-4:15 pm A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Two Cases Of Daptomycin-Induced Acute Eosinophilic Pneumonia

9 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Sunday, P507 9:15 am-4:15 pm Emerging Risk Profile Of Lung Cancer Immunotherapy: Unilateral Diffuse A39: DRUG RELATED CASE REPORTS May 19, 2019 Poster Viewing 11:15 am-1:00 pm Alveolar Hemorrhage From Osimertinib Area D (Hall F, Level 2), KBHCCD D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P511 9:15 am-4:15 pm Paclitaxel Induced Diffuse Interstitial Pneumonitis: A Case Report Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm REPORTS P515 9:15 am-4:15 pm A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm ARDS: A Complication Of TALC D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE Wednesday, May P439 9:15 am-3:30 pm Methotrexate-Induced Hypersensitivity Pneumonitis Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm REPORTS D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P440 9:15 am-3:30 pm Amiodarone Induced Diffuse Alveolar Hemorrhage, A Rare Manifestation Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm REPORTS P441 9:15 am-3:30 pm A Rare Cause Of Respiratory Failure: Daptomycin Induced Acute Eosinophilic A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pneumonia D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P442 9:15 am-3:30 pm Valproic Acid Associated Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm REPORTS D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P444 9:15 am-3:30 pm Moxifloxacin Induced Hypersensitivity Pneumonitis Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm REPORTS P445 9:15 am-3:30 pm A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Flavocoxid-Induced Pulmonary Toxicity P446 9:15 am-3:30 pm Rapidly Progressingorganising Pneumoniain Association With Tocilizumab A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Treatment And Underlying Rheumatoid Arthritis P449 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Alectinib (ALK Inhibitor) Induced Interstitial Lung Disease D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P451 9:15 am-3:30 pm Organizing Pneumonia Secondary To High Dose Therapy For Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Endometrial Carcinoma REPORTS P457 9:15 am-3:30 pm A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Linezolid Induced Interstitial Lung Disease

10 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May P594 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II 22, 2019 Poster Viewing 11:15 am-1:00 pm Bilateral Recurrent Following Treatment With Dasatinib Area D (Hall F, Level 2), KBHCCD P607 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Eosinophilic Pleural Effusion Due To Topical Minoxidil Use EOSINOPHILC DISORDERS Sunday, A Case Of Eosinophilic Pneumonia Secondary To Ustekinumab In The A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD May 19, 2019 P475 9:15 am-4:15 pm Treatment Of Crohn's Disease Hypereosinophilic Syndrome With Acute Respiratory Failure Due To Severe A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD P476 9:15 am-4:15 pm Obstructive Airway Disease In A Patient Receiving Pembrolizumab P505 9:15 am-4:15 pm Two Cases Of Daptomycin-Induced Acute Eosinophilic Pneumonia A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Idiopathic Chronic Eosinophilic Pneumonia With Bilateral Eosinophilic A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD P520 9:15 am-4:15 pm Effusions: A Unique Presentation Of A Rare Disease Acute Idiopathic Eosinophilic Pneumonia. Not All Cases Are Alike, A Diagnostic A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD P565 9:15 am-4:15 pm Challenge P522 9:15 am-4:15 pm Management Of Chronic Eosinophilic Pneumonia With Mepolizumab A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Concurrent Acute Eosinophilic Pneumonia And Mycobacterium Avium A57: NTM: CASE REPORTS Area D (Hall F, Level 2), KBHCCD P633 9:15 am-4:15 pm Complex In An Emphysematous Patient A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH P1035 9:15 am-4:15 pm Chronic Eosinophilic Pneumonia And Asthma Following Military Deployment INHALATIONAL EXPOSURES Area H (Hall F, Level 2), KBHCCD A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH P1036 9:15 am-4:15 pm When Mary Jane And Joe Camel Meet... Eosinophilic Sparks Are Born INHALATIONAL EXPOSURES Area H (Hall F, Level 2), KBHCCD

Monday, Allergic Bronchopulmonary Aspergillosis (ABPA) Related Admissions In The B34: ALLERGIC DISEASE: CLINICAL STUDIES AND MECHANISMS May 20, 2019 P9 9:15 am-4:15 pm United States & It's Outcomes In Asthmatics Area A (Hall F, Level 2), KBHCCD 508 9:15 am-11:15 am Exhaled Breath Analysis For Prediction Of Responders To Mepolizumab In B21: SEVERE ASTHMA: CLINICAL AND MECHANISTIC STUDIES Room D222-D224 (Level 2), KBHCCD Poster Discussion 10:00 am-11:15 am Patients With Severe Asthma

11 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May Casting Chronic Cough: A Case Of Plastic Due To Chronic D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS 22, 2019 P551 9:15 am-3:30 pm Eosinophilic Pneumonia In An Adult Area D (Hall F, Level 2), KBHCCD Atypical Presentation Of Allergic Bronchopulmonary Aspergillosis Mimicking D31: ALLERGY AND ASTHMA CASE REPORTS Area H (Hall F, Level 2), KBHCCD P1031 9:15 am-3:30 pm Lung Cancer FAMILIAL/GENETIC ILD

Sunday, 718 2:15 pm-4:15 pm Mucus Matters: Ferrets Demonstrate Restrictive Lung Physiology, Sustained A108: PATHOPHYSIOLOGY IN DIFFUSE PARENCHYMAL LUNG May 19, 2019 Poster Viewing 2:15 pm -2:45 pm Fibrosis, Mucociliary Decrement In Airways, And Aberrant Repair Following DISEASES Ballroom D Four (Level 3), KBHCCD Poster Discussion 2:45 pm-4:15 pm Bleomycin-Induced Pulmonary Fibrosis P307 9:15 am-4:15 pm Negligible Telomere-Independent Effect Of Telomerase On Alveolar Epithelial A61: EPITHELIAL BIOLOGY Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Cells

Tuesday, 9:15 am-11:15 am Expression Of Distinct Surfactant -C (SFTPC) Classes Reveal May 21, 2019 Common Downstream Pathways From Alveolar Type 2 Cell Quality Control C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD Oral Presentation 9:45 am-10:00 am Dysfunction To Pulmonary Fibrosis

P303 9:15 am-4:15 pm Cellular Consequences Of Uncharacterized Surfactant Protein-A2 (SFTPA2)- Gene Associated With Familial Idiopathic Pulmonary Fibrosis (IPF) C58: MECHANISMS OF PULMONARY FIBROSIS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm And Lung Cancer C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY P434 9:15 am-4:15 pm Copa Syndrome: A Rare Occurrence Of Familial Ild With Rheumatoid Arthritis LUNG DISEASES Area D (Hall F, Level 2), KBHCCD P953 9:15 am-4:15 pm Isolated Pulmonary Fibrosis: An Atypical Presentation Of Dyskeratosis C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Congenita CLINICAL STUDIES C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND P957 9:15 am-4:15 pm Pulmonary Fibrosis Due To A Novel Surfactant Protein Mutation Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm CLINICAL STUDIES P1051 9:15 am-4:15 pm C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Genetic Studies On Brazilian Patients With Familial Interstitial Pneumonias P1052 9:15 am-4:15 pm The 5-Year Experience At A Pulmonary Genetics Center: Diverse Presentations, C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Rapid Growth, And Frequent Molecular Diagnosis

12 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, May 110 1:30 pm-3:30 pm D103: IDIOPATHIC INTERSTITIAL PNEUMONIAS: 22, 2019 Poster Viewing 1:30 pm-2:15 pm The Prevalence And Progression Of Early Interstitial Lung Disease In First- Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:15 pm-3:30 pm Degree Relatives Of Patients With Familial Interstitial Pneumonia NATURAL HISTORY AND PROGNOSIS

121 1:30 pm-3:30 pm The Effects Of Tobacco Smoking Intensity And Cessation On Idiopathic D103: IDIOPATHIC INTERSTITIAL PNEUMONIAS: Poster Viewing 1:30 pm-2:15 pm NATURAL HISTORY AND PROGNOSIS Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:15 pm-3:30 pm Pulmonary Fibrosis Incidence And Progression D38: LUNG TRANSPLANTATION AND DRUG RELATED P432 9:15 am-3:30 pm Lung Transplantation In A Patient With Gaucher Disease Type 1: A Case Report Area D (Hall F, Level 2), KBHCCD And Review Of The Literature. CASE REPORTS Recurrent Pneumonia In Pregnancy Unveils Common Variable P469 9:15 am-3:30 pm Immunodeficiency And Associated Granulomatous Lymphocytic Interstitial D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Lung Disease HEPATOPULMONARY SYNDROME A59: PULMONARY REHABILITATION: MUSCLE FUNCTION Sunday, P250 9:15 am-4:15 pm Effects Of Aerobic Training On Respiratory Mechanics And Lung Inflammation Area C (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm In Rats With Hepatopulmonary Syndrome AND STRENGTH A59: PULMONARY REHABILITATION: MUSCLE FUNCTION P251 9:15 am-4:15 pm Effects Of Combined Exercise Training In Mechanical Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Properties And Inflammation In Rats With Hepatopulmonary Syndrome AND STRENGTH P319 9:15 am-4:15 pm The Role Of Placental Growth Factor As A Mediator Of Pulmonary Disease Via A61: EPITHELIAL BIOLOGY Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Human Alveolar Type 2 Pneumocyte Apoptosis Monday, P334 9:15 am-4:15 pm B42: DYSPNEA CASE REPORTS Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm An Uncommon Etiology Of Platypnea-Orthodeoxia Syndrome P343 9:15 am-4:15 pm B42: DYSPNEA CASE REPORTS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Case Of Hepatopulmonary Syndrome P954 9:15 am-4:15 pm Successful Treatment Of Severe Hepatopulmonary Syndrome With Primary B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Embolotherapy Prior To Potential Liver Transplant

13 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location HERMANSKY PUDLAK SYNDROME Sunday, 703 9:15 am-11:15 am Effective Anti-Fibrotic Therapy For Hermansky-Pudlak Syndrome Pulmonary May 19, 2019 Poster Viewing 9:15 am-10:00 am Fibrosis In Pale Ear Mice Using A Hybrid Inhibitor Of Cannabinoid Receptor 1 A29: EMERGING CONCEPTS IN LUNG FIBROSIS Ballroom D Four (Level 3), KBHCCD Poster Discussion 10:00 am-11:15 am (Cb1R) And Inducible Nitric Oxide Synthase (iNOS), MRI-1867 C59: GENETIC AND EPIGENETIC MECHANISMS IN PULMONARY Tuesday, P311 9:15 am-4:15 pm The Differential Effects Of Hermansky-Pudlak Syndrome 1 And 2 On Lung Area C (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Fibroblast Behavior FIBROSIS C59: GENETIC AND EPIGENETIC MECHANISMS IN PULMONARY P312 9:15 am-4:15 pm Shortened Telomeres In Type II Alveolar Epithelial Cells In Hermansky-Pudlak Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Syndrome Pulmonary Fibrosis FIBROSIS C64: PULMONARY FIBROSIS MODELS AND MECHANISTIC P425 9:15 am-4:15 pm Pathomechanistic Role Of Autophagy In The Development Of Lung Fibrosis Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm INSIGHTS Wednesday, May P518 9:15 am-3:30 pm Hermansky-Pudlak Syndrome Subtype 4 (HPS-4): A Novel Mutation In A 44 D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Years Old Italian Woman With Severe Pulmonary Fibrosis 622 1:30 pm-3:30 pm Ap-3-Dependent Mechanisms Regulate The Trafficking Of TP8AA 1 To Lamellar D107: MITOCHONDRIA AND ER STRESS IN HOMEOSTASIS Poster Viewing 1:30 pm-2:15 pm AND REPAIR Ballroom D Three (Level 3), KBHCCD Poster Discussion 2:15 pm-3:30 pm Bodies In Alveolar Type 2 Cells HHT Monday, P327 9:15 am-4:15 pm Multiple Pulmonary Abscesses As A Late Complication Of Pulmonary B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Arteriovenous Malformation Embolization B51: CRITICAL CARE CASE REPORTS: CARDIOVASCULAR P858 9:15 am-4:15 pm Hereditary Hemorrhagic Telangiectasia Associated High-Output Heart Failure Area F (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm DISEASES IN THE ICU II

P993 9:15 am-4:15 pm Screening For Pulmonary Arteriovenous Malformation (PAVM) In Hereditary Hemorrhagic Telagiectasia: Clinical Significance Of Pulmonary Micronodules B55: USE YOUR ILLUSION I: CLINICAL RESEARCH IN PAH Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm And/Or Positive TTCE Without PAVM HISTIOCYTIC DISORDERS Sunday, P461 9:15 am-4:15 pm Association Between Clinicopathologic Characteristics And BRAFV600E A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Expression In Chinese Patients With Langerhans Cell Histiocytosis

14 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Sunday, P462 9:15 am-4:15 pm A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE May 19, 2019 Poster Viewing 11:15 am-1:00 pm Pulmonary Langerhans Cell Histiocytosis In Adults Area D (Hall F, Level 2), KBHCCD A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS P1108 9:15 am-4:15 pm Rosai-Dorfman Disease: An Unusual Cause Of A Solitary Pulmonary Mass Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm NOT ALWAYS WHAT YOU GET Monday, P268 9:15 am-4:15 pm Secondary Hemophagocytic Lymphohistiocytosis Due To Kikuchi Fujimoto B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Disease/Systemic Lupus Erythematosus Overlap Tuesday, P560 9:15 am-4:15 pm Clinical Outcomes And Survival Following Lung Transplantation In Patients C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm With Pulmonary Langerhans Cell Histiocytosis 103 2:15 pm-4:15 pm Epidemiology And Healthcare Utilization Of Spontaneous Pneumothorax And C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL Poster Viewing 2:15 pm-2:45 pm HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Diffuse Cystic Lung Diseases In The United States Wednesday, May P480 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Pulmonary Langerhans Cell Histiocytosis And Iga Nephropathy P484 9:15 am-3:30 pm Non-Langerhans Histiocytosis: A Unique Presentation Of Erdheim-Chester D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm And IGG4 Disease P496 9:15 am-3:30 pm The Many Faces Of Interstitial Lung Disease: Transformation Of Non Specific D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Interstitial Pneumonia Into Pulmonary Langerhans Cell Histiocytosis P498 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm All That Wheezes Is Not Asthma P503 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Erdheim-Chester Disease Presenting With Spontaneous Pneumothorax HYPERSENSITIVITY PNEUMONITIS

Sunday, 707 9:15 am-11:15 am Myeloid-Derived Suppressor Cells Orchestrate Immunosuppressive Networks May 19, 2019 Poster Viewing 9:15 am-10:00 am A29: EMERGING CONCEPTS IN LUNG FIBROSIS Ballroom D Four (Level 3), KBHCCD Poster Discussion 10:00 am-11:15 am In Idiopathic Pulmonary Fibrosis A38: IDIOPATHIC INTERSTITIAL PNEUMONIA: DIAGNOSIS AND P201 9:15 am-4:15 pm Squawks In Interstitial Lung Diseases Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm NATURAL HISTORY

15 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Sunday, P519 9:15 am-4:15 pm Rituximab For Stabilization Of Fibrotic Hypersensitivity Pneumonitis In A A40: INFLAMMATORY DPLDs CASE REPORTS May 19, 2019 Poster Viewing 11:15 am-1:00 pm Patient With Continued Antigen Exposure Area D (Hall F, Level 2), KBHCCD

524 2:15 pm-4:15 pm Chronic Hypersensitivity Pneumonitis (CHP), An ILD With Distinct Molecular Poster Viewing 2:15 pm -2:45 pm A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm Signatures A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH P1033 9:15 am-4:15 pm Hypersensitivity Pneumonitis: A Clinical Case Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm INHALATIONAL EXPOSURES Monday, P148 9:15 am-4:15 pm Development Of A Patient Centered Thematic Framework For Experiences B39: GRANULOMATOUS ILDs Area B (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Living With Chronic Hypersensitivity Pneumonitis; A Qualitative Study P149 9:15 am-4:15 pm B39: GRANULOMATOUS ILDs Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Transbronchial Biopsy In Chronic Hypersensitivity Pneumonitis P155 9:15 am-4:15 pm Anti-Fibrotic Therapy For Chronic Hypersensitivity Pneumonitis: Don’t Forget B39: GRANULOMATOUS ILDs Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm The Antigen P156 9:15 am-4:15 pm Causes Of Hypersensitivity Pneumonitis: Literature Review And Development B39: GRANULOMATOUS ILDs Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Of A Knowledge Translation Tool P249 9:15 am-4:15 pm Diagnostic Challenges And Management Considerations Of Immune-Related B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Hypersensitivity Pneumonitis Associated With Immune Checkpoint Inhibitors

Tuesday, 104 2:15 pm-4:15 pm The Value Of High Resolution Computed Tomography And Surgical Lung C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL May 21, 2019 Poster Viewing 2:15 pm -2:45 pm Biopsy In Predicting Outcome For Patients With Fibrotic Hypersensitivity HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Pneumonia

110 9:15 am-11:15 am Bronchoscopic Lung Biopsy For Diffuse Parenchymal Lung Disease: Poster Viewing 9:15 am-10:00 am C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Comparison Of Forceps With Cryobiopsy

119 9:15 am-11:15 am Usefulness Of New Criteria For Chronic Hypersensitivity Pneumonitis Poster Viewing 9:15 am-10:00 am C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Established By Delphi Method

16 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Tuesday, 115 9:15 am-11:15 am Identification Of Indoor Fungal Antigens In Assessment Of Hypersensitivity May 21, 2019 Poster Viewing 9:15 am-10:00 am C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Pneumonitis — An Alternate Approach

116 9:15 am-11:15 am Standard Panels, Environmental Samples, And Hypersensitivity Pneumonitis - Poster Viewing 9:15 am-10:00 am C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Identification Of The Elusive ‘Causal Antigen’ P1035 9:15 am-4:15 pm Antinuclear Antibodies In Patients With Hypersensitivity Pneumonitis: C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Insights On Clinical Relevance From A German Double-Cohort Investigation. P599 9:15 am-4:15 pm Custom Made Serological Method To Assess Relevant Source Of Exposure In C44: ASTHMA EPIDEMIOLOGY Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Patients With Extrinsic Allergic Alveolitis Wednesday, May 9:15 am-11:15 am Rare Protein-Altering Telomere-Related Gene Variants In Patients With Chronic D12: ILD: DIAGNOSIS AND PROGNOSIS Room C155-C156 (Level 1), KBHCCD 22, 2019 Oral Presentation 10:30 am-10:45 am Hypersensitivity Pneumonitis: An Observational Cohort Study P23 9:15 am-3:30 pm D47: CRITICAL CARE CASE REPORTS: INFECTION AND SEPSIS I Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Red Tide Pneumonitis P535 9:15 am-3:30 pm Spontaneous In A Patient With Chronic Fibrotic D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Hypersensitivity Pneumonitis P546 9:15 am-3:30 pm D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Ca 15.3 As A Marker Of Chronic Hypersensitivity Pneumonitis P1034 9:15 am-3:30 pm D31: ALLERGY AND ASTHMA CASE REPORTS Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Bulky Nodules: An Atypical Presentation Of Hypersensitivity Pneumonitis IDIOPATHIC PULMONARY HEMOSIDEROSIS Wednesday, May P473 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Gluten Intolerance Of The Lung P500 9:15 am-3:30 pm A Curious Cause Of Iron Deficiency Anemia: Idiopathic Pulmonary D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Hemosiderosis

17 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location IGG4 RELATED DISEASE Sunday, P454 9:15 am-4:15 pm Thoracic Paravertebral Lesions In Patients With IGG4-Related Respiratory A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Disease

Monday, P244 9:15 am-4:15 pm Acute Respiratory Distress Syndrome (ARDS) Complicating Pulmonary May 20, 2019 Nodular Lymphocytic Hyperplasia (PNLH) Associated With Immunoglobulin B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm G4 Related Disorder (IGG4-Rd) C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY Tuesday, P438 9:15 am-4:15 pm Pulmonary IGG4 Disease — The New Masquerader? Area D (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm LUNG DISEASES C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY P451 9:15 am-4:15 pm Airway And Bone Marrow Involvement In A Patient With IGG4-Related Disease Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm LUNG DISEASES P470 9:15 am-4:15 pm C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Delayed Presentation Of IGG4 Related Lung Disease C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND P958 9:15 am-4:15 pm IGG4 Related Disease: A Possible Cause Of Lymphoid Interstitial Pneumonia Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm CLINICAL STUDIES Wednesday, May P468 9:15 am-3:30 pm Bilateral Pulmonary Nodules Secondary To IGG4-Related : D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm An Unusual Mimicker Of Malignancy P484 9:15 am-3:30 pm Non-Langerhans Histiocytosis: A Unique Presentation Of Erdheim-Chester D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm And IGG4 Disease P499 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Recurrent Pleuritis: A Pulmonary Manifestation Of IGG4 Related Disease ILD — OTHERS Sunday, P545 9:15 am-4:15 pm A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Granulomatous And Lymphocytic Ild (Glild): Revelation In Ild World A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS P1121 9:15 am-4:15 pm Diffuse Large B-Cell Lymphoma Presenting As Progressive Interstitial Lung Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Disease NOT ALWAYS WHAT YOU GET

18 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Sunday, 504 2:15 pm-4:15 pm Nailfold Capillaroscopy In A Prospective Interstitial Lung Disease (ILD) Cohort: May 19, 2019 Poster Viewing 2:15 pm -2:45 pm A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm IPF, CTD-ILD And IPAF Monday, P204 9:15 am-4:15 pm Clinical Features Of Pathologically Proven Acute Fibrinous And Organizing B46: IDIOPATHIC INTERSTITIAL PNEUMONIA: NATURAL HISTORY Area B (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Pneumonia P209 9:15 am-4:15 pm Physical Frailty In Fibrotic Lung Disease And Response To Pulmonary B60: PULMONARY REHABILITATION: GENERAL Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Rehabilitation

103 2:15 pm-4:15 pm A Pilot Randomised Controlled Trial Of Ambulatory Oxygen Versus Air Via Poster Viewing 2:15 pm -2:45 pm B103: ILD: THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Portable Concentrator In Fibrotic Interstitial Lung Disease Tuesday, 121 9:15 am-11:15 am May 21, 2019 Poster Viewing 9:15 am-10:00 am Diagnostic Delays In Interstitial Lung Diseases (ILDS) C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am 615 9:15 am-11:15 am Single-Cell Transcriptomic Analysis Of Type 2 Alveolar Epithelial Cell Poster Viewing 9:15 am-10:00 am Differentiation From Induced Pluripotent Stem Cells: An Emerging Tool To C28: PATHWAYS OF LUNG MORPHOGENESIS Ballroom D Three (Level 3), KBHCCD Poster Discussion 10:00 am-11:15 am Model Interstitial Lung Diseases P254 9:15 am-4:15 pm Melanocyte Stimulating Hormone Has Anti-Inflammatory Properties In C31: TRANSLATIONAL STUDIES IN SARCOIDOSIS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Granuloma Via Marco And P-CREB C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY P431 9:15 am-4:15 pm Pulmonary Lymphangiectasia: A Novel Histopathologic Finding In Coatomer Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Subunit Alpha (COPA) Syndrome LUNG DISEASES C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY P434 9:15 am-4:15 pm Copa Syndrome: A Rare Occurrence Of Familial ILD With Rheumatoid Arthritis Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm LUNG DISEASES C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY P456 9:15 am-4:15 pm Rapidly Evolving Pulmonary Granulomas: A NOD2 Home Genetic Testing Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm LUNG DISEASES P1092 9:15 am-4:15 pm Possible Value Of Antifibrotic Drugs In Patients With Progressive Fibrosing C39: IDIOPATHIC INTERSTITIAL PNEUMONIA: THERAPY Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Non-IPF Interstitial Lung Diseases C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL 114 2:15 pm-4:15 pm Recurrent Acute Exacerbations Of Fibrotic Interstitial Lung Diseases Room C140/C142 (Level 1), KBHCCD Poster Viewing 11:15 am-1:00 pm HISTORY AND PROGNOSIS AND ILD THERAPY

19 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May 109 9:15 am-11:15 am D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND 22, 2019 Poster Viewing 9:15 am-10:00 am Lung Allocation Score Should Be Implemented In China TRANSPLANT Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am 502 9:15 am-11:15 am Poster Viewing 9:15 am-10:00 am Single Cell Analysis Of Pulmonary Fibrosis Phenotypes D29: LUNG MULTI-OMICS TO MECHANISM Room D222-D224 (Level 2), KBHCCD Poster Discussion 10:00 am-11:15 am D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE P459 9:15 am-3:30 pm A Case Of Interstitial Fibrosis Five Years After Bleomycin Exposure Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm REPORTS P471 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Natural Course Of Pulmonary Hyalinizing Granuloma In A Decade P511 9:15 am-3:30 pm D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm To Treat Or Not To Treat: The Dip Question P512 9:15 am-3:30 pm D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Fibrosis And Embolism Secondary To Silicon Implant Leak P482 9:15 am-3:30 pm An Alternative Approach Of Diagnosing Diffuse Pulmonary D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Meningotheliomatosis (DPMS) With Transbronchial Cryobiopsy LAM Sunday, P451 9:15 am-4:15 pm -Related Symptom Variability In Patients With A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Lymphangioleiomyomatosis P452 9:15 am-4:15 pm Single Center Experience Of Lung Transplantation For A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lymphangioleiomyomatosis P457 9:15 am-4:15 pm Lymphangioleiomyomatosis (LAM) Nodules Attract And Activate Alveolar Type A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm II Cells

P459 9:15 am-4:15 pm Exosomes Released From Lymphangioleiomyomatosis-Derived Smooth Muscle-Like Cells Mediate Endothelial Cell Apoptosis And Vascular Network A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Disruption P460 9:15 am-4:15 pm Mast Cell Recruitment In And Lung Cystic Destruction; A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Opportunities For Drug Repurposing 20 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Sunday, P370 9:15 am-4:15 pm Identification Of Clinically Relevant Immunohistochemical Sub-Groups In The A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) May 19, 2019 Poster Viewing 11:15 am-1:00 pm UK National Cohort Of Lymphangioleiomyomatosis (LAM). Area C (Hall F, Level 2), KBHCCD P371 9:15 am-4:15 pm A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Role Of Kiss1 Signaling In Pulmonary Lymphangioleiomyomatosis P372 9:15 am-4:15 pm Correlative Imaging Study Of Lymphangioleiomyomatosis Tissue Sample By A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm X-Ray Micro Tomography And Histology P373 9:15 am-4:15 pm Detailed Imaging Of Lung Cysts In Lam And Bhd Patients By A High- A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Resolution Targeted CT RE-SCAN P374 9:15 am-4:15 pm A Phase Ii Clinical Trial Of The Safety Of Simvastatin In Patients With A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Lymphangioleiomyomatosis And With Tuberous Sclerosis Complex P463 9:15 am-4:15 pm Relationship Between And Development Of Spontaneous A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pneumothorax In Females With Lymphangioleiomyomatosis P464 9:15 am-4:15 pm Proteomic Profiling Of Serum Exosomes To Identify Novel Biomarkers For A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lymphangioleiomyomatosis P465 9:15 am-4:15 pm Delineating Novel Mtor-Independent Signaling Pathways For A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lymphangioleiomyomatosis And Tuberous Sclerosis Therapy P466 9:15 am-4:15 pm A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Targeting Akt As A Therapeutic Intervention In Treatment Of Lam P467 9:15 am-4:15 pm Dysregulation Of Sphingolipid Metabolism In Pulmonary A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lymphangioleiomyomatosis (LAM) Monday, P226 9:15 am-4:15 pm Effects Of Yoga On Functional Capacity And Quality Of Life In The Participants B60: PULMONARY REHABILITATION: GENERAL Area B (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm With Lymphangioleiomyomatosis: A Pilot Study Tuesday, 103 2:15 pm-4:15 pm Epidemiology And Healthcare Utilization Of Spontaneous Pneumothorax And C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL May 21, 2019 Poster Viewing 2:15 pm-2:45 pm HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Diffuse Cystic Lung Diseases In The United States 105 2:15 pm-4:15 pm Targeted High-Resolution CT RE-SCAN In Patients With C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL Poster Viewing 2:15 pm-2:45 pm HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Lymphangioleiomyomatosis Lead To Higher Score Accuracy 21 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, 109 2:15 pm-4:15 pm Lung Transplantation For Lymphangioleiomyomatosis: A Review Of The C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL May 21, 2019 Poster Viewing 2:15 pm-2:45 pm HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm United Network For Organ Sharing Database 9:15 am-11:15 am C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD Oral Presentation 10:15 am-10:30 am NK Cell Activation Is Increased In Lymphangioleiomyomatosis

9:15 am-11:15 am Disruptive Effect Of LAM-Derived Smooth Muscle Cells On Human Lung Progenitors Is Dependent On Expression Of Translationally Controlled Tumour C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD Oral Presentation 10:30 am-10:45 am Protein

101 9:15 am-11:15 am Identification Of Clinical Endotypes In Lymphangioleiomyomatosis To Poster Viewing 9:15 am-10:00 am C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Improve Personalised Care P1074 9:15 am-4:15 pm Prevalence And Clinical Characteristics Of Lymphangioleiomyomatosis In 97 C35: HEALTH SERVICES RESEARCH IN COUGH, CF, AND ILD Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Patients Wednesday, May P463 9:15 am-3:30 pm A Case Of Lymphangioleiomyomatosis With Normal Vascular Endothelial D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Growth Factors P466 9:15 am-3:30 pm Co-Existant Sarcoidosis And Lymphangioleiomyomatosis In A Patient With D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Cystic Lung Disease P470 9:15 am-3:30 pm ‘Finding Pneumo’; A Series Of Unfortunate Events Leading To A Very Rare D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Diagnosis Of Lymphangioleiomyomatosis In A Male P475 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lymphangioleiomyomatosis­—A Stitch In Time, Saves Nine P476 9:15 am-3:30 pm Sirolimusimproves Lymphangioleiomyomatosis And Pneumothoraxin A D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Patient With Tuberous Sclerosis Carrying A Novel TSC2 Mutation P497 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Case Of Tuberous Sclerosis Associated Lymphangioleimyomatosis P504 9:15 am-3:30 pm Tuberous Sclerosis With Lymphangioleiomyomatosis (LAM) Treated With D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm : A Case Report P505 9:15 am-3:30 pm Lymphangioleiomyomatosis In Patient With Segmental And Focal D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Glomerulosclerosis (SFGS) Colapsant — Case Report 22 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location MOUNIER-KUHN SYNDROME A48: CRITICAL CARE CASE REPORTS: CAUSES AND Sunday, P1000 9:15 am-4:15 pm Mounier- Kuhn Syndrome: A Rare Cause Of Recurrent Area G (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Infection COMPLICATIONS OF ACUTE RESPIRATORY FAILURE C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND Tuesday, P954 9:15 am-4:15 pm A Case Of Mounier-Kuhn Syndrome Area G (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm CLINICAL STUDIES Wednesday, May P633 9:15 am-3:30 pm D43: COPD, CF, AND CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm More Than Just Chronic Obstructive Pulmonary Disease P636 9:15 am-3:30 pm Case Of Mounier-Kuhn Syndrome: A Rare Disease Presenting With Recurrent D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pneumonia And Bronchiectasis P644 9:15 am-3:30 pm D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Case Of Mounier Kuhn’s Syndrome MUCSCULAR DYSTROPHY B65: SRN: DIAGNOSIS AND MONITORING OF SLEEP AND SLEEP Monday, P1220 9:15 am-4:15 pm Identifying Potential Predictive Factors Of Sleep Quality In Duchenne Area K (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Muscular Dystrophy DISORDERS Tuesday, 715 2:15 pm-4:15 pm Bone Marrow-Derived Macrophages Of Duchenne Muscular Dystrophy (MDX) C109: RESPIRATORY MUSCLE DYSFUNCTION: MECHANISM AND May 21, 2019 Poster Viewing 2:15 pm-2:45 pm ASSESSMENT Ballroom D Four (Level 3), KBHCCD Poster Discussion 2:45 pm-4:15 pm Mice Are Differentially “Educated” Based On Muscle Disease Stage Wednesday, May D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 P467 D5 9:15 am-3:30 pm Intrathoracic In A Patient With Pulmonary Arterial : A Rare, Yet Life-Threatening Complication Of D55: CASE REPORTS IN PULMONARY VASCULAR MEDICINE III Area G (Hall F, Level 2), KBHCCD P959 9:15 am-3:30 pm Neurofibromatosis Type 1 NON-CF BRONCHIECTASIS

Tuesday, 303 2:15 pm-4:15 pm C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO May 21, 2019 Poster Viewing 2:15 pm-2:45 pm Clinical Phenotypes Among Patients With Bronchiectasis TREATMENT Ballroom A Four (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm

23 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, 304 2:15 pm-4:15 pm Airway Clearance In Non- Bronchiectasis: Analysis From The C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO May 21, 2019 Poster Viewing 2:15 pm-2:45 pm TREATMENT Ballroom A Four (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm United States Bronchiectasis Research Registry

310 2:15 pm-4:15 pm Pseudomonas Aeruginosa Is Associated With Greater Frequency Of C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO Poster Viewing 2:15 pm-2:45 pm Exacerbations Among Patients With Non-Cystic Fibrosis Bronchiectasis In The TREATMENT Ballroom A Four (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm United States 311 2:15 pm-4:15 pm Effects Of Complex Heterozygosity Of Cftr And Ciliary Genes In Non-Cf C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO Poster Viewing 2:15 pm-2:45 pm TREATMENT Ballroom A Four (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm Bronchiectasis

317 2:15 pm-4:15 pm Inhaled Ciprofloxacin (ARD-3150) In Patients With Non-Cystic Fibrosis C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO Poster Viewing 2:15 pm-2:45 pm Bronchiectasis And Frequent Pulmonary Exacerbations: A Pooled Analysis TREATMENT Ballroom A Four (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm From Orbit-3 And Orbit-4

320 2:15 pm-4:15 pm Pseudomonas Aeruginosa Associated With Severity Of Non-Cystic Fibrosis C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO Poster Viewing 2:15 pm-2:45 pm Bronchiectasis Measured By The Modified Bronchiectasis Severity Score (BSI) TREATMENT Ballroom A Four (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm And The Faced: The US Bronchiectasis And NTM Research Registry (BRR) Study Wednesday, May P571 9:15 am-3:30 pm D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Selective Iga Deficiency And Bronchiectasis

P634 9:15 am-3:30 pm A Triple Threat: Acute Pulmonary Emboli, Pneumococcal Pneumonia And Congenital Bronchiectasis With Auto-Pneumonectomy And Compensatory D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Hyper-Lobar Expansion P646 9:15 am-3:30 pm D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Kartagener Syndrome In Identical Male Twins P645 9:15 am-3:30 pm D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Parasitic Infection Leading To Bronchiectasis OCCUPATIONAL/EXPOSURE RELATED LUNG DISORDERS A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH Sunday, P1051 9:15 am-4:15 pm Titanium Lung In A Solider With Iraq/Afghanistan War-Lung Injury (IAW-LI) Area H (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm INHALATIONAL EXPOSURES

24 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, 1007 2:15 pm-4:15 pm A104: WILDFIRE, BIOMASS, AND WORLD TRADE CENTER Trinity Ballroom 5-7 (Level 3), Omni May 19, 2019 Poster Viewing 2:15 pm-2:45 pm Airway Disease In Biomass Smoke-Associated Ild: Not Just Copd EXPOSURES Poster Discussion 2:45 pm-4:15 pm Dallas Downtown 1016 2:15 pm-4:15 pm A104: WILDFIRE, BIOMASS, AND WORLD TRADE CENTER Trinity Ballroom 5-7 (Level 3), Omni Poster Viewing 2:15 pm-2:45 pm Sarcoid-Like Granulomatous Disease: Pathologic Case Series In World Trade EXPOSURES Dallas Downtown Poster Discussion 2:45 pm-4:15 pm Center (WTC) Dust Exposed Rescue And Recovery Workers A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH P1052 9:15 am-4:15 pm Forced Oscillation Technique In The Evaluation Of Biopsy-Confirmed Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Constrictive Bronchiolitis In A Southwest Asia Deployed Veteran INHALATIONAL EXPOSURES A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH P1045 9:15 am-4:15 pm Occupational Polycaprolactone Inhalation Induced Acute Lung Injury Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm INHALATIONAL EXPOSURES Titanium Is Abundant In Fibrotic Of Two Soldiers Post-Deployment To P228 9:15 am-4:15 pm A52: SARCOIDOSIS AND EXPOSURE RELATED INTERSTITIAL LUNG Iraq And Afghanistan But Is Not Seen In Lungs Of Five Patients With Idiopathic DISEASE Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Fibrosis A52: SARCOIDOSIS AND EXPOSURE RELATED INTERSTITIAL LUNG P229 9:15 am-4:15 pm Healthcare Utilization Among Medicare Beneficiaries With Coal Worker’s Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm In The Us DISEASE P477 9:15 am-4:15 pm A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Talc Granulomatosis Masquerading As A Tree In Bud Phenomenon P490 9:15 am-4:15 pm Cavitary Lung Mass From Granulomatous Talc Disease Precipitated By A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Radiation Therapy P967 9:15 am-4:15 pm B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Fatal Case Of Foreign-Body Granulomatous Pulmonary Emboli Monday, 1006 9:15 am-11:15 am Epigenetic Signatures Of Sensitization And Disease In Beryllium-Exposed B25: OCCUPATIONAL EXPOSURES INCLUDING DEPLOYMENT Trinity Ballroom 5-7 (Level 3), Omni May 20, 2019 Poster Viewing 11:15 am-1:00 pm Individuals RELATED, MINING, AND AGRICULTURE Dallas Downtown 1004 9:15 am-11:15 am B25: OCCUPATIONAL EXPOSURES INCLUDING DEPLOYMENT Trinity Ballroom 5-7 (Level 3), Omni Poster Viewing 9:15 am-10:00 am Pneumoconiosis Mortality: Progress Towards Healthy People 2020 Goal RELATED, MINING, AND AGRICULTURE Dallas Downtown Poster Discussion 10:00 am-11:15 am Wednesday, May P525 9:15 am-3:30 pm D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Long Term Minimally Progressive Interstitial Fibrosis In A Dental Technician

25 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, May 418 9:15 am-11:15 am Recombinant Neuroglobin Reverses The Molecular Mitochondrial Effects Of D26: HEALTH EFFECTS ASSOCIATED WITH INDOOR AND 22, 2019 Poster Viewing 9:15 am-10:00 am OUTDOOR AIR POLLUTION Arena (Level 2), KBHCCD Poster Discussion 10:00 am-11:15 am Carbon Monoxide Poisoning Through Carbon Monoxide Scavenging P529 9:15 am-3:30 pm "But I Never Smoked!!!" - A Case Of Respiratory Bronchiolitis Interstitial Lung D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Disease In A Non-Smoker PCH AND PVOD Sunday, P831 9:15 am-4:15 pm Rapid Diagnosis Of Pulmonary Veno-Occlusive Disease With Bedside A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Ultrasonography Monday, P938 9:15 am-4:15 pm Pulmonary Veno-Occlusive Disease In Apatient With C282y Homozygous B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Mutation P950 9:15 am-4:15 pm A Case Of Pulmonary Veno-Occulssive Disease With Variant In Eif2ak4 B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm C.892Dela

P1006 9:15 am-4:15 pm Pulmonary Veno-Occlusive Disease In Elderly Patients With Hypoxemia Out Of Proportion To Underlying Pulmonary Or Cardiovascular Disease: An Under- B55: USE YOUR ILLUSION I: CLINICAL RESEARCH IN PAH Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Recognized Entity?

Tuesday, P1137 9:15 am-4:15 pm Mitomycin C Induces Pulmonary Vessel Endothelial-To-Mesenchymal May 21, 2019 Transition And Pulmonary Veno-Occlusive Disease Via Smad3-Dependent C50: THE PERFECT DRUG: EXPERIMENTAL TREATMENTS OF PAH Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pathway In Rats Wednesday, May P971 9:15 am-3:30 pm D55: CASE REPORTS IN PULMONARY VASCULAR MEDICINE III Area G (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm The Never Ending Battle Between The Heart And The Lung P967 9:15 am-3:30 pm D55: CASE REPORTS IN PULMONARY VASCULAR MEDICINE III Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Looks And Smells Like PAH...The Great Mimicker “PVOD” PLASTIC BRONCHITIS A48: CRITICAL CARE CASE REPORTS: CAUSES AND Sunday, P1020 9:15 am-4:15 pm Plastics In The ICU Area G (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm COMPLICATIONS OF ACUTE RESPIRATORY FAILURE Tuesday, P986 9:15 am-4:15 pm Lymphatic Plastic Bronchitis With Chyloptysis Secondary To Thoracic Duct C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Stenosis

26 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May P551 9:15 am-3:30 pm Casting Chronic Cough: A Case Of Plastic Bronchitis Due To Chronic D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS 22, 2019 Poster Viewing 11:15 am-1:00 pm Eosinophilic Pneumonia In An Adult Area D (Hall F, Level 2), KBHCCD PPFE Monday, P195 9:15 am-4:15 pm Clinical Courses Of Asymptomatic Patients With Mild Idiopathic B46: IDIOPATHIC INTERSTITIAL PNEUMONIA: NATURAL HISTORY Area B (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Pleuroparenchymal Fibroelastosis

119 2:15 pm-4:15 pm Treatment With Antifibrotic Agents In Pleuroparenchymal Fibroelastosis With Poster Viewing 2:15 pm-2:45 pm B103: ILD: THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Usual Interstitial Pneumonia Wednesday, May P523 9:15 am-3:30 pm A Case Of The Usual/Unusual: Pleuroparenchymal Fibroelastosis D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Misdiagnosed As Sarcoidosis P533 9:15 am-3:30 pm D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Case Study On Pleuroparenchymal Fibroelastosis — Is It Really An Enigma? P514 9:15 am-3:30 pm Pleuroparenchymal Fibroelastosis Progressing To Unilateral Vocal Cord D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Paralysis P526 9:15 am-3:30 pm Secondary Spontaneous Pneumothorax As A Complication Of D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pleuroparenchymal Fibroelastosis: A Case Report P527 9:15 am-3:30 pm Coexisting Together: Pleuroparenchymal Fibroelastosis With Usual Interstitial D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pneumonia PRIMARY CILIARY DYSKINESIA Sunday, P350 9:15 am-4:15 pm AC6 Regulates Microtubule-Depolymerizing Kinesin KIF19a For Ciliary Length A62: MUCUS, MUCINS, MUCOCILIARY UNIT IN LUNG DISEASE Area C (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Control In Mammals Tuesday, 312 2:15 pm-4:15 pm Airways Mucus Pathogenesis In Patients With Non-Cystic Fibrosis C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO May 21, 2019 Poster Viewing 2:15 pm-2:45 pm TREATMENT Ballroom A Four (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm Bronchiectasis And Primary Ciliary Dyskinesia 9:15 am-11:15 am C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD Oral Presentation 10:00 am-10:15 am NEK10 Loss Of Function Causes A Novel Human Motile Ciliopathy

27 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May 9:15 am-11:15 am Quantitative High Speed Video Profiling Discriminates Between Variants Of D18: BEST OF NOVEL TECHNOLOGIES AND METHODOLOGIES 22, 2019 Oral Presentation 9:15 am-9:30 am Primary Ciliary Dyskinesia Room D167/D174 (Level 1), KBHCCD P635 9:15 am-3:30 pm Beyond Young’s Syndrome: Diagnosis, Management, And Prognosis Of D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Primary Ciliary Dyskinesia. P643 9:15 am-3:30 pm D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Journey Of A Patient With Kartagener’s Syndrome PULMONARY ALVEOLAR PROTEINOSIS Sunday, P453 9:15 am-4:15 pm Prognostic Impacts Of Comorbidities In Pulmonary Alveolar Proteinosis: A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm A Nationwide Surveillance In Japan P456 9:15 am-4:15 pm A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm An Approach To Precision Medicine For Pulmonary Alveolar Proteinosis P497 9:15 am-4:15 pm Mammalian Target Of Rapamycin (MTOR) Inhibitor Induced Pulmonary A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Alveolar Proteinosis A Case Of Severe Acute Respiratory Distress Syndrome With Underlying P973 9:15 am-4:15 pm A47: CRITICAL CARE CASE REPORTS: MECHANICAL VENTILATION Pulmonary Alveolar Proteinosis That Could Not Be Saved With Extracorporeal FROM NIV TO ECMO Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Membrane Oxygenation A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH P1034 9:15 am-4:15 pm Pulmonary Alveolar Proteinosis And P-ANCA Glomerulonephritis Post Silica Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Exposure INHALATIONAL EXPOSURES

Monday, 106 2:15 pm-4:15 pm Us National Pulmonary Alveolar Proteinosis Registry: Update On Differential May 20, 2019 Poster Viewing 2:15 pm-2:45 pm B103: ILD: THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Diagnosis, Clinical Manifestations, And Current Therapy P241 9:15 am-4:15 pm A Case Of Autoimmune Pulmonary Alveolar Proteinosis With Sjögren’s B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Syndrome P257 9:15 am-4:15 pm Pulmonary Alveolar Proteinosis: A Rare Case Of Autoimmune Disruption Of B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Gm-Csf Superimposed With Secondary Inhalation Exposure

28 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Monday, P242 9:15 am-4:15 pm B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS May 20, 2019 Poster Viewing 11:15 am-1:00 pm The Surfactant Of The Matter: A Case Of Severe Pulmonary Alveolar Proteinosis Area C (Hall F, Level 2), KBHCCD P269 9:15 am-4:15 pm Effect Of Pioglitazone Therapy On Alveolar Macrophage Size In A Patient With B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Refractory Autoimmune Pulmonary Alveolar Proteinosis P324 9:15 am-4:15 pm Primary Pulmonary Alveolar Proteinosis In A Patient With Chronic B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lymphoblastic Leukemia P338 9:15 am-4:15 pm B42: DYSPNEA CASE REPORTS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Alveolar Proteinosis (PAP) C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY Tuesday, P436 9:15 am-4:15 pm Severe Pulmonary Alveolar Proteinosis In A Patient With GATA2 Deficiency Area D (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm LUNG DISEASES P558 9:15 am-4:15 pm Effect Of Whole Lung Lavage (Wll) On Exhaled Nitric Oxide Fraction (FENO) In C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Patients With Autoimmune Pulmonary Alveolar Proteinosis (APAP) P561 9:15 am-4:15 pm Clinical Observation: 5 Cases Of Wen San Ding Transdermal External C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Treatment For Idiopathic Pulmonary Alveolar Proteinosis C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND P946 9:15 am-4:15 pm Lipid Accumulation Leads To Inhibition Of M1 Response In Alveolar Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Macrophages CLINICAL STUDIES Secondary Pulmonary Alveolar Proteinosis Presenting As Steroid Non- P956 9:15 am-4:15 pm C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND Responsive Interstitial Lung Disease In Anti-Mda5 Associated Amyopathic CLINICAL STUDIES Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Dermatomyositis P983 9:15 am-4:15 pm C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Too Much Protein!

Wednesday, May P465 9:15 am-3:30 pm Long-Term Follow-Up Of A Patient With GM-CSF Antibody-Negative Pulmonary 22, 2019 Alveolar Proteinosis Following Exposure To Dust After The Great East Japan D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Earthquake P483 9:15 am-3:30 pm Dramatic Response Of Rituximab In Severe Autoimmune Pulmonary Alveolar D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Proteinosis: A Case Report

29 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May P478 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS 22, 2019 Poster Viewing 11:15 am-1:00 pm Pulmonary Alveolar Proteinosis—A Washed Up Disease Area D (Hall F, Level 2), KBHCCD PULMONARY ARTERY ANEURYSMS Sunday, P838 9:15 am-4:15 pm Death By Behcet: A Case Ofpulmonary Artery Aneurysm Secondary To Active A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Behcet's Vasculitis Monday, P957 9:15 am-4:15 pm Thrombosed Pulmonary Artery Aneurysm In A Patient With Underlying B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Eosinophilic Granulomatosis With Polyangiitis P966 9:15 am-4:15 pm An Unusual Case Of Pulmonary Artery Aneurysms With Mural Thrombus B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Formation P992 9:15 am-4:15 pm Outcomes Of Pulmonary Artery Aneurysms In Patients With Pulmonary B55: USE YOUR ILLUSION I: CLINICAL RESEARCH IN PAH Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Hypertension. A Single Center Experience Tuesday, P21 9:15 am-4:15 pm C53: TUBERCULOSIS CASE REPORTS Area A (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Rasmussen's Aneurysm: A Rare And Potentially Fatal Cause Of Hemoptysis Wednesday, May P264 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Squamous Cell Carcinoma Causing Rasmussen Aneurysm PULMONARY OSSIFICATION, CALCIFICATIONS, AND MICROLITHIASIS A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH Sunday, P1043 9:15 am-4:15 pm Fumes On A Plane! A Case Of DPO Area H (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm INHALATIONAL EXPOSURES Monday, P365 9:15 am-4:15 pm When Lungs Become Bone: A Rare Case Of Idiopathic Dendriform Pulmonary B42: DYSPNEA CASE REPORTS Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Ossification Tuesday, 9:15 am-11:15 am C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD May 21, 2019 Oral Presentation 11:00 am-11:15 am Osteogenesis And Osteolysis In Pulmonary Alveolar Microlithiasis Wednesday, May P462 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm A Calcified Curse: A Case Of Pulmonary Alveolar Microlithiasis P479 9:15 am-3:30 pm Concrete Heavy Lungs Due To Calcium Stones: Pulmonary Alveolar D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Microlithiasis: A Rare Lung Disease

30 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May P487 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS 22, 2019 Poster Viewing 11:15 am-1:00 pm Dishing Out Pulmonary Calcifications Area D (Hall F, Level 2), KBHCCD P492 9:15 am-3:30 pm D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Should I Get An Ortho Consult?: A Case Of Pulmonary Ossification P508 9:15 am-3:30 pm An Uncommon Presentation Of An Uncommon Disorder: Dendriform D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Ossification P509 9:15 am-3:30 pm Dendriform Pulmonary Ossification Complicated By Recurrent Spontaneous D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pneumothorax RARE AIRWAY DISORDERS A68: NEW TECHNIQUES, METHODOLOGIES, AND Sunday, P392 9:15 am-4:15 pm The Establishment Of Two Animal Models Of Benign Airway Stenosis And The Area C (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Therapeutic Effect Of Mitomycin C On Airway Stenosis MATHEMATICAL MODELING A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS P1114 9:15 am-4:15 pm Mimicking Lung Cancer: Pulmonary Sclerosing Pneumocytoma Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm NOT ALWAYS WHAT YOU GET P1147 9:15 am-4:15 pm A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Occurrence Of Endobronchial Granular Cell Tumor P1138 9:15 am-4:15 pm Endobronchial Choriocarcinoma Presenting With Hemoptysis Six Weeks After A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Normal Vaginal Delivery: A Bronchoscopic Diagnostic Challenge P1139 9:15 am-4:15 pm A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Endobronchial Chondroma As A Rare Cause Of Hemoptysis P1140 9:15 am-4:15 pm A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Kaposi : Bronchoscopy And Imaging Findings P1151 9:15 am-4:15 pm Tracheal Adenoid Cystic Carcinoma Presenting With Recurrent Wheeze And A A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm "Normal" Chest X-Ray Monday, P297 9:15 am-4:15 pm Excessive Dynamic Airway Collapse In A Young Woman With Hypermobility- B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Type Ehlers-Danlos Syndrome

31 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Monday, P314 9:15 am-4:15 pm Incidentally Discovered "Rock Garden"- Tracheobronchoplastica May 20, 2019 Osteochondropathica With Associated Left Sided Breast Adenocarcinoma And B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Severe Esophageal Strictures: A Rare Case Report P329 9:15 am-4:15 pm Management Of A Case Of Tracheobronchopathia Osteochondroplastica B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Causing B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT P57 9:15 am-4:15 pm Diagnostic Challenges Of Pulmonary Kaposi Sarcoma In AIDS Patients Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm DILEMMAS B69: THORACIC ONCOLOGY: OPTIMIZING DIAGNOSIS AND P107 9:15 am-4:15 pm A Population-Based Description Of Incidence And Familial Clustering Of Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Carcinoid Tumors MANAGEMENT Tuesday, P465 9:15 am-4:15 pm C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm My Oh! A Case Of Endobronchial Leiomyoma P481 9:15 am-4:15 pm You Have Mucous Membrane Pemphigoid, Causing , And C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm You Lived To Tell About It? P482 9:15 am-4:15 pm C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Case Of Endobronchial P500 9:15 am-4:15 pm C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Benign Bump: A Rare Case Of Endobronchial Chondroma P502 9:15 am-4:15 pm C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Endobronchial Leiomyoma: A Rare Form Of Bronchial Tumor Wednesday, May P245 9:15 am-3:30 pm Not Your Usual Chronic Cough — A Case Of Lymphomatoid Granulomatosis D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm With Tracheal Obstruction RARE CONGENTIAL ANOMALIES A48: CRITICAL CARE CASE REPORTS: CAUSES AND Sunday, P1006 9:15 am-4:15 pm The Unexpected Tracheal Area G (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm COMPLICATIONS OF ACUTE RESPIRATORY FAILURE P827 9:15 am-4:15 pm A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Scimitar Syndrome: A Rare Cause Of Cardiomyopathy In Adults.

32 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Sunday, P840 9:15 am-4:15 pm A Case Of And Undiagnosed Atrioventricular Canal A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I May 19, 2019 Poster Viewing 11:15 am-1:00 pm In An Adult Patient Area F (Hall F, Level 2), KBHCCD P847 9:15 am-4:15 pm A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Right Ventricular Diverticulum In Scimitar Syndrome Monday, P297 9:15 am-4:15 pm Excessive Dynamic Airway Collapse In A Young Woman With Hypermobility- B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Type Ehlers-Danlos Syndrome B51: CRITICAL CARE CASE REPORTS: CARDIOVASCULAR P852 9:15 am-4:15 pm Persistent Left Superior Vena Cava With Partial Anomalous Pulmonary Venous Area F (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Return In A Patient With Atrial Fibrillation: A Case Report DISEASES IN THE ICU II P960 9:15 am-4:15 pm B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Pathology In Abernethy Malformation

P963 9:15 am-4:15 pm Mistaken Identity: A Case Of High-Output Pulmonary Hypertension Due To Partial Anomalous Pulmonary Venous Drainage Disguised By An Arterio- B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Venous Fistula P968 9:15 am-4:15 pm B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Different Kind Of Vascular Shunt In A Hemodialysis Patient With Chest Pain P970 9:15 am-4:15 pm B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm An Undiagnosed Left Persistent Superior Vena Cava: The Role Of Pocus P1084 9:15 am-4:15 pm Always Consider The Birthmark: A Rare Case Of A Right Middle Intralobar B59: BACTERIAL INFECTION CASE REPORTS Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Bronchopulmonary Sequestration In An Adult Tuesday, P494 9:15 am-4:15 pm An Incidental Finding Of A Tracheal Bronchus In A Rheumatoid Arthritis C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Patient: Case Report P989 9:15 am-4:15 pm C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Case Of Asymptomatic Swyer-James-Macleod Syndrome P990 9:15 am-4:15 pm C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Stay Calm And Just Breathe: A Case Of Swyer-James-Mcleod Syndrome Wednesday, May P951 9:15 am-3:30 pm D55: CASE REPORTS IN PULMONARY VASCULAR MEDICINE III Area G (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm A Rare Congenital Pulmonary Malformation In An Adult Patient: Case Report

33 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May P243 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I 22, 2019 Poster Viewing 11:15 am-1:00 pm A Case Of Bronchopulmonary Sequestration Causing Recurrent Pneumonia Area C (Hall F, Level 2), KBHCCD RARE NON-MALIGNANT PLEURAL DISORDERS Monday, P417 9:15 am-4:15 pm B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Gastronomic : A Case Of Pancreatic Pleural Fistula Wednesday, May P573 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Primary Malignant Myelomatous Pleural Effusion: A Rare Entity P580 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Case Of Pancreatitis-Induced Chylothorax P590 9:15 am-3:30 pm Bilateral Primary Spontaneous Pneumothorax: A Case Report And D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Review Of Literature P596 9:15 am-3:30 pm Recurrent Non-Catamenial Secondary To Diaphragmatic D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm And Pleural P614 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Spilled Milk: A Case Of Diffuse Chylous Effusions P620 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Bilateral RARE PLEURAL TUMORS A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS Sunday, P1107 9:15 am-4:15 pm More Than Just A Cough — Gastric Adenocarcinoma Presenting With Septal Area J (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Thickening And Bilateral Pleural Effusions NOT ALWAYS WHAT YOU GET Monday, P375 9:15 am-4:15 pm B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Synovial Sarcoma: Masquerading As Massive Pleural Effusion P382 9:15 am-4:15 pm Maleficent Multiple Myeloma: A Case Of Myelomatous Pleural Metastases B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm With Effusion P385 9:15 am-4:15 pm B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Primary Pleural Lymphoma — Case Report

34 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, Occupational Asbestos Exposure And Malignant Pleural Mesothelioma, P47 9:15 am-4:15 pm B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT May 20, 2019 Biphasic Type: A Challenging Histopathological And Immunohistochemical DILEMMAS Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Diagnosis B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT P50 9:15 am-4:15 pm Endobronchial Ultrasound In Diagnosis And Staging Of Malignant Pleural Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Mesothelioma DILEMMAS B68: ONCOGENIC MUTATIONS, , AND NOVEL P72 9:15 am-4:15 pm Thoracic Metastases: A Single-Center Review Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm THERAPEUTICS

Tuesday, 416 2:15 pm-4:15 pm C110: THE FUTURE OF LUNG CANCER BIOMARKERS: WHERE May 21, 2019 Poster Viewing 2:15 pm-2:45 pm Top2a And Her2neu Evaluation In Malignant Pleural Mesothelioma SHOULD WE LOOK? Arena (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm Wednesday, May P247 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm A Rare Case Of Primary Pleural Epithelioid P252 9:15 am-3:30 pm Myeloid Sarcoma Of The Lung In The Absence Hyperleukocytosis: D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Phenomenon P263 9:15 am-3:30 pm The Monster That Burst — When A Mature Presents As D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pleuritic Chest Pain P273 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Cause Of P285 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Sarcomatoid Mesothelioma In A Patient With Myelodysplastic Syndrome P286 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Ewing Sarcoma Of The P302 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Human Herpes Virus-8 Negative Primary Effusion Lymphoma P345 9:15 am-3:30 pm D63: THORACIC ONCOLOGY CASE REPORTS III Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Malignant Of The Pleura: About A Case P597 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm What Is This Large Lung Mass? Hint: It’s Not Lung 35 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May P574 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II 22, 2019 Poster Viewing 11:15 am-1:00 pm Grapes Of Wrath: When Uveal Melanoma Targets The Pleura Area D (Hall F, Level 2), KBHCCD P576 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Entity Of Pleural-Based Pulmonary Nodules After Abdominal Trauma P276 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Hips Don’t Lie: Myxoid Liposarcoma Mimicking Massive P282 9:15 am-3:30 pm Proof Is In The Yolk A Unique Case Of Anterior Mediastinal Wideningfrom Yolk D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Sac Tumor RARE PULMONARY PARENCHYMAL TUMORS A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS Sunday, P1118 9:15 am-4:15 pm Sarcomatoid Carcinoma Of The Lung: A Rare And Unfortunate Disease Area J (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm NOT ALWAYS WHAT YOU GET A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS P1121 9:15 am-4:15 pm Diffuse Large B-Cell Lymphoma Presenting As Progressive Interstitial Lung Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Disease NOT ALWAYS WHAT YOU GET A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS P1128 9:15 am-4:15 pm A Rock-Solid Lung Mass: A Case Of Rare Inflammatory Myofibroblastic Lung Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Tumor With Challenging Diagnosis NOT ALWAYS WHAT YOU GET A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS P1130 9:15 am-4:15 pm Metastatic Chondrosarcoma Mimicking Pulmonary Embolism Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm NOT ALWAYS WHAT YOU GET A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS P1131 9:15 am-4:15 pm A Brewing Case Of Malt Lymphoma: Primary Pulmonary Lymphoma Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Presenting As Cystic Lung Disease NOT ALWAYS WHAT YOU GET A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS P1135 9:15 am-4:15 pm A Rare Tumor: Inflammatory Myofibroblastic Tumor Of The Lungs Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm NOT ALWAYS WHAT YOU GET P1153 9:15 am-4:15 pm Post Obstructive Pneumonia As A Presentation Of A Primary Bronchial A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Carcinoid Tumor: A Rare Diagnosis In A Young Adult P1156 9:15 am-4:15 pm Bronchus-Associated Lymphoid Tissue (BALT) Lymphoma Presenting As A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pneumonia Monday, P958 9:15 am-4:15 pm B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Not All That Tree-And-Buds Is Infection 36 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT Monday, P52 9:15 am-4:15 pm A Case Of Pulmonary Post-Transplant Lymphoproliferative Disorder Diagnosed Area A (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm By Bronchoalveolar Lavage Flow Cytometry DILEMMAS B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT P53 9:15 am-4:15 pm Inflammatory Pseudotumor: How Long Should We Monitor For Recurrence Of Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Disease? DILEMMAS B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT P58 9:15 am-4:15 pm Atypical Pulmonary Carcinoid And Hyponatremia Should Prompt An Extensive Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Metastatic Workup DILEMMAS B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT P59 9:15 am-4:15 pm Incidental Primary Pulmonary Mucosa-Associated Lymphoid Tissue Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lymphoma DILEMMAS B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT P61 9:15 am-4:15 pm Multi-Modal Treatment Leading To Prolonged Survival In A Patient With Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Artery Intimal Sarcoma DILEMMAS B69: THORACIC ONCOLOGY: OPTIMIZING DIAGNOSIS AND P106 9:15 am-4:15 pm Diagnostic Pitfall Of Small Sclerosing Pneumocytoma Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MANAGEMENT Tuesday, P488 9:15 am-4:15 pm The Case Of The Mistaken Identity: A Pulmonary Hamartoma That Was Actually C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm An Amyloidoma P509 9:15 am-4:15 pm C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Inflammatory Myofibroblastic Tumor: A 1 Percenter P97 9:15 am-4:15 pm Respiratory Symptoms In A High-Risk Patient; Do Not Miss Pulmonary C56: HIV: CLINICAL STUDIES AND BASIC SCIENCE MODELS Area A (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Kaposi’s Sarcoma Wednesday, May P237 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Pulmonary Involvement By Intravascular B Cell Lymphoma P239 9:15 am-3:30 pm Pulmonary Nodule In A Low Risk Patient Presenting As An Unexpected D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Diagnosis P244 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Yolk Sac Carcinoma In An Young Adult — Case Report P248 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Peripheral Primary Pulmonary Leiomyoma

37 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May P557 9:15 am-3:30 pm D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS 22, 2019 Poster Viewing 11:15 am-1:00 pm An Atypical Presentation Of Pulmonary Kaposi Sarcoma Area D (Hall F, Level 2), KBHCCD P563 9:15 am-3:30 pm D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Mastocytosis Manifesting As Chronic Cough P262 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Extra-Abdominal Desmoid Fibromatosis P265 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm An Unusual Case Of A Mediastinal Mass In A Pregnant Woman P267 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Decade-Long Ground Glass Opacity Of Mystery P270 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Desmoid Fibromatosis Of The Chest: A Case Report P278 9:15 am-3:30 pm Primary Pulmonary Angiosarcoma With Extension Into Left Atrium—Effective D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Tissue Diagnosis Method P281 9:15 am-3:30 pm A Case Of Pulmonary Sclerosing Pneumocytoma With Multiple Lung And D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Bone Metastasis P299 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Interstitial Lung Disease: Not Always Only Fibrosis P260 9:15 am-3:30 pm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm The Spark That Ignited Confusion P274 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Case Of Inflammatory Myofibroblastic Tumor P275 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Recurrent Pneumonia Or A Sticky Situation? A Rare Form Of Lung Cancer P279 9:15 am-3:30 pm Small Is Not Always Small. Deception By Nodular Size In The Diagnosis Of D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lung Cancer

38 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Wednesday, May P283 9:15 am-3:30 pm Unique Presentation Of A Rare : Mucoepidermoid Tumor Of The D62: THORACIC ONCOLOGY CASE REPORTS II 22, 2019 Poster Viewing 11:15 am-1:00 pm Lung Area C (Hall F, Level 2), KBHCCD P288 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Rare Malignant Nonsmoker Tumor: Lung Sarcoma P291 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Carcinosarcoma With Metastasis To Soft Tissue—A Rare Case Report P292 9:15 am-3:30 pm Rare Case Of Uterine Adenosarcoma Metastasis To The Lung 24 Years After D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Curative Resection P312 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm An Unusual Cause Of A Solitary : A Case Report Primary Pulmonary Malignant Melanoma-Rare Entity D62: THORACIC ONCOLOGY CASE REPORTS II

P293 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Poster Viewing 11:15 am-1:00 pm Sarcomatoid Carcinoma Of The Lung Presenting As Subcutaneous Nodules Area C (Hall F, Level 2), KBHCCD P295 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Metastatic Of The Lung P310 9:15 am-3:30 pm A Rare Case Of Primary Hepatoid Adenocarcinoma Of The Lung In A Female D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Patient P311 9:15 am-3:30 pm Metastatic Endometrial Cancer Presenting As A Pulmonary Nodule After D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Remote Hysterectomy P315 9:15 am-3:30 pm D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Extra-Nodal Marginal Zone B-Cell Lymphoma: A Case Report P338 9:15 am-3:30 pm When Antibiotics Fail: Unsuspecting Young Female With Asthma-Like D63: THORACIC ONCOLOGY CASE REPORTS III Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Exacerbations And Recurrent Pneumonias P349 9:15 am-3:30 pm D63: THORACIC ONCOLOGY CASE REPORTS III Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Fortunate Encounter With A Clinical Mimic P352 9:15 am-3:30 pm Carcinoid Tumors Of Lung And BRCA Mutations: Is There A Connection D63: THORACIC ONCOLOGY CASE REPORTS III Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Between Them? 39 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location RHEUMATOID ARTHRITIS LUNG DISEASE Sunday, P183 9:15 am-4:15 pm Prognostic Role Of Kl-6 In Rheumatoid Arthritis-Associated Interstitial A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Lung Disease P187 9:15 am-4:15 pm A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Characterization Of Airway Disease In Rheumatoid Arthritis P193 9:15 am-4:15 pm Rheumatoid Arthritis’ Clinical Characteristics Stratified By Interstitial Lung A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Disease Patterns

P194 9:15 am-4:15 pm The Design And Rationale Of The Trail Trial: A Randomized Double-Blind Phase Ii Clinical Trial Of Pirfenidone In Rheumatoid Arthritis-Associated Interstitial A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lung Disease Tuesday, P494 9:15 am-4:15 pm An Incidental Finding Of A Tracheal Bronchus In A Rheumatoid Arthritis C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Patient: Case Report 106 2:15 pm-4:15 pm Survival Of Patients With Acute Exacerbations Of Rheumatoid Arthritis C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL Poster Viewing 2:15 pm-2:45 pm HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Associated Interstitial Lung Disease SCLERODERMA Sunday, 1018 9:15 am-11:15 am Relevance Of Accelerated In Sandblasters To Rapidly Progressive A26: ENVIRONMENTAL MODIFIERS OF LUNG DISEASE Trinity Ballroom 5-7 (Level 3), Omni May 19, 2019 Poster Viewing 9:15 am-10:00 am Dallas Downtown Poster Discussion 10:00 am-11:15 am Pneumoconiosis 1017 9:15 am-11:15 am Progressive Massive Fibrosis Contributes To Pulmonary Hypertension In A26: ENVIRONMENTAL MODIFIERS OF LUNG DISEASE Trinity Ballroom 5-7 (Level 3), Omni Poster Viewing 9:15 am-10:00 am Dallas Downtown Poster Discussion 10:00 am-11:15 am Silicosis A47: CRITICAL CARE CASE REPORTS: MECHANICAL VENTILATION P982 9:15 am-4:15 pm Electrical Impedance Tomography And Ventilation Heterogeneity On A Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Silicosis Patient FROM NIV TO ECMO

509 2:15 pm-4:15 pm ATYR1923 Modulates The Inflammatory Response In Experimental Models Of Poster Viewing 2:15 pm-2:45 pm A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD Poster Discussion 2:45 pm-4:15 pm Interstitial Lung Disease

40 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, 701 2:15 pm-4:15 pm Quantitative Computed Tomography In Systemic Sclerosis-Associated A108: PATHOPHYSIOLOGY IN DIFFUSE PARENCHYMAL LUNG May 19, 2019 Poster Viewing 2:15 pm-2:45 pm DISEASES Ballroom D Four (Level 3), KBHCCD Poster Discussion 2:45 pm-4:15 pm Interstitial Lung Disease: A Densitometric Assessment Of Disease Severity P179 9:15 am-4:15 pm A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Biomarkers In Systemic Sclerosis Associated Interstitial Lung Disease P182 9:15 am-4:15 pm Predictors For The Development Of Systemic Sclerosis Associated Interstitial A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Lung Disease (SSC-ILD) — Data From The German SSC-Network P186 9:15 am-4:15 pm The Place Of Respiratory Manifestations During Scleroderma In Dakar: A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Multicentric Study P523 9:15 am-4:15 pm A New Era In Scleroderma Interstitial Lung Disease And Renal Crisis: Rationale A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm For Early Use Of Endothelin Receptor Antagonists Monday, 102 2:15 pm-4:15 pm Circulating Krebs Von Den Lungen And CC Chemokine Lligand 2 Predict May 20, 2019 Poster Viewing 2:15 pm-2:45 pm Progression Of Interstitial Lung Disease In Systemic Sclerosis Patients B103: ILD: THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Undergoing Immunosuppressive Therapy P318 9:15 am-4:15 pm B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Anthracosilicosis: A Rare Cause Of Endobronchial Tumor P986 9:15 am-4:15 pm Interstitial Lung Disease And Pulmonary Hypertension In Systemic Sclerosis: B55: USE YOUR ILLUSION I: CLINICAL RESEARCH IN PAH Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Real-World Experience 9:15 am-11:15 am Nintedanib Reduces Lung Function Decline In Patients With Systemic B17: ADVANCES IN ILD THERAPY Room C155-C156 (Level 1), KBHCCD Oral Presentation 11:00 am-11:15 am Sclerosis-Associated Interstitial Lung Disease: Results Of The Senscis Trial Tuesday, 107 2:15 pm-4:15 pm Feasibility And Efficacy Of Cohort Enrichment For Progressive Lung Fibrosis In C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL May 21, 2019 Poster Viewing 2:15 pm-2:45 pm HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Systemic Sclerosis — An EUSTAR Database Analysis

108 2:15 pm-4:15 pm Prediction And Frequency Of Progressive Lung Fibrosis In Patients With C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL Poster Viewing 2:15 pm-2:45 pm Systemic Sclerosis-Associated Interstitial Lung Disease In The World’s Largest HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD Poster Discussion 2:45 pm-4:15 pm Database Of Patients With Systemic Sclerosis (EUSTAR)

41 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, Expert Consensus On The Screening, Treatment, And Management Of Patients 124 2:15 pm-4:15 pm C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL May 21, 2019 Poster Viewing 2:15 pm-2:45 pm With Systemic Sclerosis-Associated Interstitial Lung Disease (SSC-ILD), And The Room C140/C142 (Level 1), KBHCCD Potential Future Role Of Anti-Fibrotics In A Treatment Paradigm For SSC-ILD: A HISTORY AND PROGNOSIS AND ILD THERAPY Poster Discussion 2:45 pm-4:15 pm Delphi Consensus Study P1048 9:15 am-4:15 pm Gene Expression Of Peripheral Blood Monocytes In Systemic Sclerosis C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Associated Interstitial Lung Disease P583 9:15 am-4:15 pm C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Heart Rate Recovery In Patients With Scleroderma P385 9:15 am-4:15 pm Antifibrotic Efficacy Of Nintedanib In A Cellular Model Of Scleroderma C62: FIBROBLAST BIOLOGY Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Associated Interstitial Lung Disease C64: PULMONARY FIBROSIS MODELS AND MECHANISTIC P422 9:15 am-4:15 pm Osteoclast-Like Differentiation In Mouse Model Of Silicosis Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm INSIGHTS Wednesday, May 101 9:15 am-11:15 am Nintedanib In Patients With Systemic Sclerosis-Associated Interstitial Lung D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND 22, 2019 Poster Viewing 9:15 am-10:00 am TRANSPLANT Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Disease (SSC-ILD): The Senscis Trial

102 9:15 am-11:15 am D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND Poster Viewing 9:15 am-10:00 am Scleroderma-Related Mortality In The United States From 2003 To 2016 TRANSPLANT Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am

513 9:15 am-11:15 am Single-Cell Analysis Reveals Fibroblast Heterogeneity And Myofibroblasts In Poster Viewing 9:15 am-10:00 am D29: LUNG MULTI-OMICS TO MECHANISM Room D222-D224 (Level 2), KBHCCD Poster Discussion 10:00 am-11:15 am Systemic Sclerosis-Associated Interstitial Lung Disease 605 1:30 pm-3:30 pm Circulating Mitochondrial DNA Is Associated With Fibroblast Activation And D107: MITOCHONDRIA AND ER STRESS IN HOMEOSTASIS AND Poster Viewing 1:30 pm-2:15 pm REPAIR Ballroom D Three (Level 3), KBHCCD Poster Discussion 2:15 pm-3:30 pm Disease Progression In Scleroderma Associated Interstitial Lung Disease VASCULITIS Monday, P240 9:15 am-4:15 pm Off-Label Use Of Benralizumab For Severe Eosinophilic Granulomatosis With B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD May 20, 2019 Poster Viewing 11:15 am-1:00 pm Polyangiitis

42 ADULT Rare Disease Term ADULT Date/Day Board Number/Time Abstract Title Session ID and Title Location

Monday, P266 9:15 am-4:15 pm B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS May 20, 2019 Poster Viewing 11:15 am-1:00 pm Anca Negative Eosinophilic Granulomatosis With Polyangiitis Area C (Hall F, Level 2), KBHCCD P237 9:15 am-4:15 pm B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Anti GBM Disease: A Case Report P939 9:15 am-4:15 pm B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Dilemma Of Massive Hemoptysis And Thrombosis: Hughes-Stovin Syndrome Tuesday, P439 9:15 am-4:15 pm C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Trimethoprim/Sulfamethoxazole In Induced Alveolar Hemorrhage C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY P439 9:15 am-4:15 pm Cryoglobulinemic Vasculitis: A Rare Cause Of Diffuse Alveolar Hemorrhage Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm LUNG DISEASES

Wednesday, May 122 9:15 am-11:15 am Burden Of Illness Associated With Eosinophilic Granulomatosis With D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND 22, 2019 Poster Viewing 9:15 am-10:00 am Polyangiitis (EGPA, Formerly Churg-Strauss Syndrome) In The United States: TRANSPLANT Room C140/C142 (Level 1), KBHCCD Poster Discussion 10:00 am-11:15 am Evidence From Two Administrative Claims Databases YELLOW NAIL SYNDROME Wednesday, May P604 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD 22, 2019 Poster Viewing 11:15 am-1:00 pm Yellow Nail Syndrome (YNS) P617 9:15 am-3:30 pm D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Yellow (Toe)Nail Syndrome

43 ADULT Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location ABCA3 ASSOCIATED ILD Tuesday, P759 9:15 am-4:15 pm ABCA-3 Related Surfactant Dysfunction Presenting As Neonatal Respiratory C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Failure And Clinical Improvement With Supportive Care MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P760 9:15 am-4:15 pm More Than BPD? Diagnosis, Prognosis And Treatment Of ABCA3 Deficiency In Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm An Extremely Premature Infant. MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P761 9:15 am-4:15 pm Not All ABCA3 Mutations Are Created Equal Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE

9:15 am-11:15 am Cre Recombinase-Mediated, Site-Specific Integration For Functional Poster Viewing 9:15 am-9:45 am C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD Poster Discussion 9:45 am-11:15 am Characterization Of ABCA3 Variants ACD-MPV (ALVEOLAR DYSPLASIA WITH MISALIGNMENT OF THE PULMONARY VEINS) Tuesday, P764 9:15 am-4:15 pm Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm (ACDMPV): A Case Series MALFORMATIONS, AND MORE

P1116 9:15 am-4:15 pm Synchrotron Phase Contrast Micro-Ct As A Novel Tool For Understanding Pulmonary Vascular Pathobiology And The 3D Micro-Anatomy Of Alveolar C49: TICKET TO RIDE: EXPERIMENTAL MODELS OF PAH Area J (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Capillary Dysplasia With Misaligned Pulmonary Veins AV MALFORMATION

Tuesday, P655 9:15 am-4:15 pm Vascular Malformations With Hemoptysis: Don’t Know Which Treatment To C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE May 21, 2019 Poster Viewing 11:15 am-1:00 pm PIK? Use Sirolimus! Area E (Hall F, Level 2), KBHCCD BRONCHIOLITIS OBLITERANS Sunday, P581 9:15 am-4:15 pm Clinical Study By Tonifying Lung And Spleen,Phlegm And Dispelling Stasis A53: CLINICAL STUDIES IN NEONATAL AND PEDIATRIC LUNG Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Method In Treatingchildren With Bronchiolitis Obliterans DISEASE AND CYSTIC FIBROSIS Tuesday, 903 9:15 am-11:15 am Pediatric Hematopoietic Stem Cell Transplant Patients’ Six-Minute Walk C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni May 21, 2019 Poster Viewing 9:15 am-9:45 am Test Distance Declines At Day 100 But Returns To Baseline By 1-Year Post DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Transplant

44 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location

Tuesday, 915 9:15 am-11:15 am 129 XE MRI And Six Minute Walk Test Correlations In Pediatric Patients After C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), May 21, 2019 Poster Viewing 9:15 am-9:45 am DISEASE Poster Discussion 9:45 am-11:15 am Hematopoietic Stem-Cell Transplantation Omni Dallas Downtown P660 9:15 am-4:15 pm Bronchiolitis Obliterans Secondary To Steven Johnson Syndrome, Diagnostic C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm And Therapeutic Challenges P669 9:15 am-4:15 pm Cryptogenic Organizing Pneumonia, A Rare Cause Of Pulmonary Nodules In C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Children: A Case Report CATAMENIAL HEMOPTYSIS Tuesday, P676 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Catamenial Hemoptysis In A 16- Yo African American Female CHILDHOOD INTERSTITIAL LUNG DISEASES — CONNECTIVE TISSUE DISEASE

Tuesday, P657 9:15 am-4:15 pm Progression Of Lung Disease In A Child With STING-Associated Vasculopathy C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE May 21, 2019 Poster Viewing 11:15 am-1:00 pm With Onset In Infancy Area E (Hall F, Level 2), KBHCCD P664 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm STAT5b Deficiency: A Rare Cause Of Pulmonary Alveolar Proteinosis

P665 9:15 am-4:15 pm The Use Of Tofactinib, Chronic Ventilation, And Long Term VV-ECMO In A Pediatric Patient With Rapidly Progressive Interstitial Lung Disease From C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MDA5+ Juvenile Dermatomyositis P668 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Manifestations Of Inflammatory Bowel Disease: A Case Report

P672 9:15 am-4:15 pm Pediatric Interstitial Lung Disease And Pneumomediastinum In Clinically Amyopathic Juvenile Dermatomyositis: Treatment With Pirfenidone As An C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Adjuvant CHILDHOOD INTERSTITIAL LUNG DISEASES — OTHER Sunday, P619 9:15 am-4:15 pm In Vitro Analysis Of Alloreactivity And Tolerance In Bilateral Orthotopic Lung A53: CLINICAL STUDIES IN NEONATAL AND PEDIATRIC LUNG Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Transplant (BOLT) In Tandem With Bone Marrow Transplant (BMT) Recipients DISEASE AND CYSTIC FIBROSIS

45 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location

Tuesday, P661 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE May 21, 2019 Poster Viewing 11:15 am-1:00 pm A Not So Simple Explanation Of Dyspnea In A 12-Year Old Area E (Hall F, Level 2), KBHCCD C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P762 9:15 am-4:15 pm Infant Lung Transplantation In Suspected Case Of Surfactant Protein Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Deficiency MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P763 9:15 am-4:15 pm Importance Of The Study Of The Lamelar Bodies In Respiratory Failure Of The Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Newborn MALFORMATIONS, AND MORE P667 9:15 am-4:15 pm The Diagnostic Challenge Of Nonspecific Interstitial Pneumonia In A Pediatric C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Patient P670 9:15 am-4:15 pm Progression Of Alveolar Simplification To End-Stage Fibrotic Lung Disease In C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Childhood 904 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 9:15 am-9:45 am A Novel Interstitial Lung Disease Associated With Systemic Juvenile Idiopathic DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Arthritis: Characteristics And Risk Factors 906 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 9:15 am-9:45 am Treatment Of Interstitial Lung Disease In STAT3 Gain-Of-Function Using JAK DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Inhibitors 910 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 9:15 am-9:45 am Evaluation Of Inter-Observer Variation For CT Identification Of Childhood DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Interstitial Lung Disease P263 9:15 am-4:15 pm Genomic Susceptibility To The Development Of Pediatric Interstitial Lung C31: TRANSLATIONAL STUDIES IN SARCOIDOSIS Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Disease C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P747 9:15 am-4:15 pm Bilateral Lung Transplantation In A 9-Year-Old Girl With Pulmonary Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Hypertension Associated With Severe Bronchopulmonary Dysplasia MALFORMATIONS, AND MORE CONGENTIAL ACINAR DYSPLASIA Tuesday, P754 9:15 am-4:15 pm Congenital Acinar Dysplasia: Familial Cause Of Severe Primary Lung C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Hypoplasia MALFORMATIONS, AND MORE

46 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location CONGENITAL CENTRAL HYPOVENTILATION SYNDROME Tuesday, Positional Impairment Of Gas Exchange During Diaphragm Pacing P712 9:15 am-4:15 pm C47: CASE REPORTS: PEDIATRIC CYSTIC FIBROSIS, LUNG May 21, 2019 Alleviated By Increasing Amplitude Settings In A Girl With Congenital Central INFECTION, AND SLEEP DISORDERED BREATHING Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Hypoventilation Syndrome C47: CASE REPORTS: PEDIATRIC CYSTIC FIBROSIS, LUNG P708 9:15 am-4:15 pm Early Diagnosis Non-Invasive Management In A Newborn With Classic Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Congenital Central Hypoventilation Syndrome INFECTION, AND SLEEP DISORDERED BREATHING C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P738 9:15 am-4:15 pm Congenital Central Hypoventilation Syndrome In An Infant With Multiorgan Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm System Failure MALFORMATIONS, AND MORE CONGENITAL Sunday, P578 9:15 am-4:15 pm The Health Related Quality Of Life Of Caregivers Of Children With Congenital A53: CLINICAL STUDIES IN NEONATAL AND PEDIATRIC LUNG Area D (Hall F, Level 2), KBHCCD May 19, 2 019 Poster Viewing 11:15 am-1:00 pm Diaphragmatic Hernia DISEASE AND CYSTIC FIBROSIS Monday, 918 9:15 am-11:15 am B26: CLINICAL STUDIES IN PEDIATRIC SLEEP, HOME VENTILATION Trinity Ballroom 1-3 (Level 3), Omni May 20, 2019 Poster Viewing 9:15 am-9:45 am Clinical Features And Outcomes Associated With Tracheostomy In Congenital AND NEUROMUSCULAR DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Diaphragmatic Hernia Tuesday, 608 9:15 am-11:15 am Proteomic Profiling Of Tracheal Fluid In Ovine Model Of Congenital May 21, 2019 Poster Viewing 9:15 am-9:45 am Diaphragmatic Hernia With Fetal Tracheal Occlusion Identifies Dysregulation C28: PATHWAYS OF LUNG MORPHOGENESIS Ballroom D Three (Level 3), KBHCCD Poster Discussion 9:45 am-11:15 am Of Epithelial PI3K/AKT, WNT, And NOTCH Signaling CYSTIC AND BULLOUS LUNG DISEASES — OTHER Tuesday, P673 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Large Bullous Lung Disease In A Child With Proteus Syndrome C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P745 9:15 am-4:15 pm Subxyphoid Uniport Video-Assisted Thoracic For A 13-Month-Old Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Infant: The Minimum Age Record Of Pumonary Cysts Operation MALFORMATIONS, AND MORE DIFFUSE ALVEOLAR HEMORRHAGE

Tuesday, P662 9:15 am-4:15 pm Successful Induction Treatment With Rituximab Of Isolated Pauci-Immune May 21, 2019 Pulmonary Capillaritis Presenting As Diffuse Alveolar Hemorrhage In A C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pediatric Patient

47 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location

Tuesday, P682 9:15 am-4:15 pm Hypocomplementemic Urticarial Vasculitis Syndrome With Diffuse Alveolar May 21, 2019 Hemorrhage, Bronchiectasis, And Progressive Obstructive Pulmonary Disease C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm In An 8 Year-Old Boy DUCHENNE MUSCULAR DYSTROPHY Monday, 915 9:15 am-11:15 am Comparable Rates Of Progressive Decline In Left Ventricular Function And B26: CLINICAL STUDIES IN PEDIATRIC SLEEP, HOME VENTILATION Trinity Ballroom 1-3 (Level 3), Omni May 20, 2019 Poster Viewing 9:15 am-9:45 am AND NEUROMUSCULAR DISEASE Poster Discussion 9:45 am-11:15 am Pulmonary Function In Children With Duchenne Muscular Dystrophy Dallas Downtown

Tuesday, 716 2:15 pm-4:15 pm Mri Assessment Of Diaphragm Impairment In Duschenne Muscolar Distrophy C109: RESPIRATORY MUSCLE DYSFUNCTION: MECHANISM AND May 21, 2019 Poster Viewing 2:15 pm-3:00 pm (DMD): Comparison To Optoelectronic Plethysmography And Pulmonary ASSESSMENT Ballroom D Four (Level 3), KBHCCD Poster Discussion 3:00 pm-4:15 pm Function Tests (PFTS)

P971 9:15 am-4:15 pm Application Of Machine Learning Tools Using Lung Function Tests To Predict The Age Of Permanent Wheelchair Dependence In Children With Duchenne C67: LUNG FUNCTION TEST Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Muscular Dystrophy EOSINOPHILIC DISORDERS ­— PULMONARY

Tuesday, P678 9:15 am-4:15 pm Induction Of Remission Following Treatment With Benralizumab In A 16-Year- C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE May 21, 2019 Poster Viewing 11:15 am-1:00 pm Old Male With Eosinophilic Granulomatosis With Polyangiitis Area E (Hall F, Level 2), KBHCCD P690 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Eosinophilic Pneumonia In A Pediatric Lung Transplant Patient FILAMIN A GENE MUTATION RELATED INTERSTITIAL LUNG DISEASE

Tuesday, P659 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE May 21, 2019 Poster Viewing 11:15 am-1:00 pm Novel Filamin A Mutation Related Interstitial Lung Disease In An Infant Area E (Hall F, Level 2), KBHCCD GLYCOGEN STORAGE AND METABOLIC DISORDERS Tuesday, P718 9:15 am-4:15 pm Saber-Sheath Airway With Multiple Areas Of Tracheal Stenosis Caused By C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Mucolipidosis Type II MALFORMATIONS, AND MORE HAMMAN’S SYNDROME Tuesday, P741 9:15 am-4:15 pm C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Swollen Child With A Cough Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE 48 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location HERMANSKY-PUDLAK SYNDROME Tuesday, 905 9:15 am-11:15 am Characterization Of Pulmonary Function In Children With Hermansky-Pudlak C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni May 21, 2019 Poster Viewing 9:15 am-9:45 am DISEASE Poster Discussion 9:45 am-11:15 am Syndrome Dallas Downtown C59: GENETIC AND EPIGENETIC MECHANISMS IN PULMONARY P313 9:15 am-4:15 pm Alveolar Epithelial Type 2 Cell Dysfunction In Hermansky-Pudlak Syndrome Area C (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Type 2 Patient-Derived Induced Pluripotent Stem Cells FIBROSIS HYPERSENSITIVITY PNEUMONITIS Sunday, P580 9:15 am-4:15 pm Lentil Aspiration Causing Hypersensitivity Pneumonitis: Describing A Novel A53: CLINICAL STUDIES IN NEONATAL AND PEDIATRIC LUNG Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Antigen, Novel Entity DISEASE AND CYSTIC FIBROSIS LANGERHANS CELL HISTIOCYTOSIS

Tuesday, P1010 9:15 am-4:15 pm Pulmonary Involvement Of Langerhans Cell Histiocytosis As Initial C69: LUNG CANCER May 21, 2019 Poster Viewing 11:15 am-1:00 pm Manifestation Of The Disease In A Pediatric Patient: A Case Report Area G (Hall F, Level 2), KBHCCD LYMPHATIC ANOMALIES: GENERALIZED LYMPHATIC ANOMALY (GLA), GORHAM-STOUT DISEASE (GSD) Tuesday, 921 9:15 am-11:15 am Abnormal Pulmonary Lymphatic Flow In Patients With Lymphatic Anomalies C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni May 21, 2019 Poster Viewing 9:15 am-9:45 am DISEASE Poster Discussion 9:45 am-11:15 am And Respiratory Compromise On MR Lymphangiogram Dallas Downtown C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P752 9:15 am-4:15 pm Central Conducting Lymphatic Anomaly Leading To Respiratory Failure Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE LYMPHATIC ANOMALIES: GORHAM-STOUT DISEASE Tuesday, P727 9:15 am-4:15 pm C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL A 15-Year-Old With Dyspnea And Vanishing Bones Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE NEUROENDOCRINE CELL HYPERPLASIA OF INFANCY

Tuesday, P658 9:15 am-4:15 pm Intersection Of Aerodigestive And Childhood Interstitial Lung Disease May 21, 2019 Evaluations: Infant Neuroendocrine Cell Hyperplasia Disguised By Aspiration C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm And Type 1 Laryngeal Cleft

49 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location C47: CASE REPORTS: PEDIATRIC CYSTIC FIBROSIS, LUNG Tuesday, P716 9:15 am-4:15 pm Home High Flow Nasal Cannula As A Novel Therapy For Improvement Of Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Severe OSA In A Child With NEHI INFECTION, AND SLEEP DISORDERED BREATHING NON-CF BRONCHITECTASIS

Tuesday, P688 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE May 21, 2019 Poster Viewing 11:15 am-1:00 pm A 7 Year-Old-Female With Bronchiectasis Found To Have RAG1 Mutations Area E (Hall F, Level 2), KBHCCD NON-TUBERCULOUS MYCOBACTERIAL INFECTION — PULMONARY Wednesday, P838 9:15 am-3:30 pm Evolutionary Phylogenomics Identified Hypermutable Isolates Of D34: CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND Area F (Hall F, Level 2), KBHCCD May 22, 2019 Poster Viewing 11:15 am-1:00 pm Nontuberculous Mycobacteria In A Cystic Fibrosis Chronic Infection MECHANISTIC STUDIES ORGANIZING PNEUMONIA Tuesday, P106 9:15 am-4:15 pm The Many Faces Of Cytomegalovirus Infection In The Bone Marrow C57: VIRAL LUNG INFECTION CLINICAL STUDIES AND CASE Area A (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Transplanted Lungs REPORTS PLASTIC BRONCHITIS C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Tuesday, P719 9:15 am-4:15 pm A Hypoplastic Heart And Plastic Lungs Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE PRIMARY CILIARY DYSKINESIA

Sunday, P339 9:15 am-4:15 pm Preserved Ciliary Defects In Airway Epithelia Derived From Primary Ciliary A61: EPITHELIAL BIOLOGY: May 19, 2019 Poster Viewing 11:15 am-1:00 pm Dyskinesia Basal Cells Expanded In 3T3-J2 Co-Culture Area C (Hall F, Level 2), KBHCCD Tuesday, 910 2:15 pm-4:15 pm Sensitivity Of Multiple Breath Washout And For Detection Of Early C104: THE MODERN PEDIATRIC PULMONARY FUNCTION LAB: Trinity Ballroom 1-3 (Level 3), Omni May 21, 2019 Poster Viewing 2:15 pm-2:45 pm Lung Disease In Children With Primary Ciliary Dyskinesia And Cystic Fibrosis: NEW STANDARDS AND NEW TESTS Dallas Downtown Poster Discussion 2:45 pm-4:15 pm A Multicenter Study 911 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 9:15 am-9:45 am Primary Ciliary Dyskinesia (PCD) Diagnostic Testing Before And After DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Establishment As A PCD Clinical Center 912 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 9:15 am-9:45 am Ciliary Biopsy Quality Improvement: Before And After Establishment Of A DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Primary Ciliary Dyskinesia (PCD) Clinical Center

50 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, 913 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni May 21, 2019 Poster Viewing 9:15 am-9:45 am Primary Ciliary Dyskinesia (PCD) Registry In Alberta DISEASE Poster Discussion 9:45 am-11:15 am Dallas Downtown 920 9:15 am-11:15 am Recessive DNAH9 Loss-Of-Function Mutations Cause Absence Of ODAS Type 2 C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 11:15 am-1:00 pm And Only Subtle Respiratory Ciliary Beating Defects DISEASE Dallas Downtown Wednesday, Increased NADPH In Human PCD Airway Epithelial Cells: Does The Reducing P839 9:15 am-3:30 pm D34: CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND May 22, 2019 Environment In Cells With Ciliary Dysfunction Lead To Decreased No MECHANISTIC STUDIES Area F (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Evolution? PROTEUS SYNDROME Tuesday, P724 9:15 am-4:15 pm C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Pulmonary Manifestations, Management Of Proteus Syndrome Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE PULMONARY ALVEOLAR PROTEINOSIS Sunday, P122 9:15 am-4:15 pm A45: CRITICAL CARE: OF MICE AND MEN — INSIGHTS FROM Characterization Of Murine Delivery Of Aerosolized Therapeutics Area A (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm EXPERIMENTAL AND ANIMAL MODELS IN ARDS AND SEPSIS

Monday, 2:15 pm-4:15 pm CRISPR/CAS9 Genome Editing Therapy For Hereditary Pulmonary Alveolar B94: BEST OF PEDIATRICS Dallas Ballroom G (Level 3), Omni May 20, 2019 Oral Presentation 2:45 pm-3:00 pm Proteinosis Dallas Downtown Tuesday, P671 9:15 am-4:15 pm Lobar Or Segmental Bronchoscopic Lavage As A Novel Treatment For C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Pulmonary Alveolar Proteinosis In The Pediatric Population P683 9:15 am-4:15 pm A Case Of Pediatric Autoimmune Pulmonary Alveolar Proteinosis That Has C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Been Refractory To 'Standard' Treatment

P675 9:15 am-4:15 pm Combined Use Of Whole Lung Lavage And Inhaled Sargramostim For Lysinuric Protein Intolerance–Associated Pulmonary Alveolar Proteinosis Ina C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm 13 Year-Old Male RARE PULMONARY VASCULAR DISEASE Sunday, P617 9:15 am-4:15 pm Prominentintrapulmonary Bronchopulmonary Anastomoses In Children With A53: CLINICAL STUDIES IN NEONATAL AND PEDIATRIC LUNG Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Single Ventricle Heart Disease DISEASE AND CYSTIC FIBROSIS

51 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location RARE CONGENITAL ANOMALIES Sunday, P579 9:15 am-4:15 pm Therapy At 30 Days Of Life Predicts Lung Function At 6–12 Months In Infants A53: CLINICAL STUDIES IN NEONATAL AND PEDIATRIC LUNG Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm With Congenital Diaphragmatic Hernia DISEASE AND CYSTIC FIBROSIS C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Tuesday, P731 9:15 am-4:15 pm Pulmonary Metastases In Attenuated Familial Adenomatous Polyposis Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P742 9:15 am-4:15 pm A Case Of Bilateral Pulmonary Varices Associated With Hybrid Left Pulmonary Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Cpam And Sequestration In A 2 Year-Old Girl MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P744 9:15 am-4:15 pm Dehydrated Hereditary Stomatocytosis Causing Severe Leading To Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm And Respiratory Insufficiency In A Neonate MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P748 9:15 am-4:15 pm Unilateral Lung Agenesis And Exercise Test Findings In A Previously Well Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Adolescent Female MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P749 9:15 am-4:15 pm Unilateral With Asthma Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P753 9:15 am-4:15 pm Sub-Carinal Bronchogenic Cyst Presenting With Recurrent Pleural Effusion In Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm A Ten Year Old Boy MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P756 9:15 am-4:15 pm De Novo Variant Of The SAMD9 Gene: Mirage Syndrome Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P757 9:15 am-4:15 pm A Rare Case Of Esophageal Lung With Systemic Arterial Supply Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE P978 9:15 am-4:15 pm Congenital Non-Isolated Arhinia: A Unique Case With Multi-Organ C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Involvement RARE PULMONARY VASCULAR DISEASE Tuesday, P725 9:15 am-4:15 pm C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Looking For Causes Of Chronic Hypoxemia Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE

52 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location RARE TUMORS — AIRWAY Tuesday, P726 9:15 am-4:15 pm Because Not Everything Is Asthma, Bronchial Mucoepidermoid Carcinoma In C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Pediatrics MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P732 9:15 am-4:15 pm A Tricky Diagnosis Of Mucoepidermoid Carcinoma In An Adolescent From A Tb Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Endemic Country MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P733 9:15 am-4:15 pm Primary Mucoepidermoid Carcinoma Of The Lung In A Child Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL P734 9:15 am-4:15 pm Rare Asthma Mimic In A 15-Year Old Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm MALFORMATIONS, AND MORE RARE TUMORS ­— PARENCHYMAL Tuesday, P743 9:15 am-4:15 pm Not All Mixed Cystic And Solid Lung Lesions Are Congenital Pulmonary C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Malformations: A Case Of An Isolated Pulmonary Infantile MALFORMATIONS, AND MORE SICKLE CELL DISEASE Sunday, P608 9:15 am-4:15 pm Immune Response To Pneumococcal Polysaccharide Vaccine In Children With A53: CLINICAL STUDIES IN NEONATAL AND PEDIATRIC LUNG Area D (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm Sickle Cell Disease DISEASE AND CYSTIC FIBROSIS 918 2:15 pm-4:15 pm C104: THE MODERN PEDIATRIC PULMONARY FUNCTION LAB: Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 2:15 pm-2:45 pm Estimation Of Pulmonary Capillary Blood Volume And Its Relation To Lung NEW STANDARDS AND NEW TESTS Dallas Downtown Poster Discussion 2:45 pm-4:15 pm Volumes In Children With Sickle Cell Disease P1250 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 9:15 am-9:45 am Retrospective Cohort Study Of Asthma Management In Pediatric Patients With DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Sickle Cell Disease 918 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni Poster Viewing 9:15 am-9:45 am Nocturnal Hypoxemia Measured By Polysomnogram Is Associated With Acute DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Chest Syndrome In A Pediatric Sickle Cell Disease Population

53 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location SPINAL MUSCULAR ATROPHY Sunday, P1234 9:15 am-4:15 pm Respiratory Assessments And Sleep Related Breathing Disorders In Children A69: SRN: WHAT CAN WE LEARN FROM CLINICAL AND Area K (Hall F, Level 2), KBHCCD May 19, 2019 Poster Viewing 11:15 am-1:00 pm With Spinal Muscular Atrophy EPIDEMIOLOGICAL STUDIES IN SLEEP? Monday, 914 9:15 am-11:15 am B26: CLINICAL STUDIES IN PEDIATRIC SLEEP, HOME VENTILATION Trinity Ballroom 1-3 (Level 3), Omni May 20, 2019 Poster Viewing 9:15 am-9:45 am Treatment Of Spinal Muscular Atrophy With Nusinersen Produces AND NEUROMUSCULAR DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Improvement In Pulmonary Function In Children With SMA II And SMA III B53: SLEEP DISORDERED BREATHING AND LONG-TERM P1200 9:15 am-4:15 pm Characteristics Of Sleep Disordered Breathing In Pediatric Spinal Muscular Area K (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Atrophy VENTILATION IN PEDIATRICS SURFACTANT PROTEIN C ASSOCIATED ILD

Sunday, 722 9:15 am-11:15 am Expression Of A Prototypical Surfactant Protein C Brichos Mutation Causes May 19, 2019 Poster Viewing 9:15 am-9:45 am A29: EMERGING CONCEPTS IN LUNG FIBROSIS Ballroom D Four (Level 3), KBHCCD Poster Discussion 9:45 am-11:15 am Epithelial Er Stress, Spontaneous Lung Injury And Fibrotic Remodeling Tuesday, 909 9:15 am-11:15 am C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), Omni May 21, 2019 Poster Viewing 9:15 am-9:45 am Chest CT Analysis For Features Of Fibrosis In Children With SpC Genetic DISEASE Dallas Downtown Poster Discussion 9:45 am-11:15 am Mutations SWYER-JAMES-MACLEOD SYNDROME Tuesday, P674 9:15 am-4:15 pm Acute Onset Of Swyer-James-Macleod Syndrome Following Adeno Virus In C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Infancy TBX4 ASSOCIATED DISEASE Wednesday, 322 1:30 pm-3:30 pm May 22, 2019 Poster Viewing 1:30 pm-2:15 pm The Transcription Factor TBX4 Regulates The Expression Of CYP1B1 D106: PICK YOUR POISON: GENES, DRUGS, AND PAH Ballroom A Four (Level 2), KBHCCD Poster Discussion 2:15 pm-3:30 pm /CATAMENIAL PNEUMOTHORAX

Tuesday, P656 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE May 21, 2019 Poster Viewing 11:15 am-1:00 pm Chief Complaint: Coughing Up Blood Monthly! Area E (Hall F, Level 2), KBHCCD

54 PEDIATRIC Rare Disease Term PEDIATRIC Date/Day Board Number/Time Abstract Title Session ID and Title Location VASCULITIS — ANCA ASSOCIATED Tuesday, 908 9:15 am-11:15 am Pulmonary Manifestations And Outcomes In Anca Associated Vasculitides: C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG Trinity Ballroom 1-3 (Level 3), May 21, 2019 Poster Viewing 9:15 am-9:45 am DISEASE Poster Discussion 9:45 am-11:15 am A Single Center Experience Omni Dallas Downtown VASCULITIS — GRANULOMATOSIS WITH POLYANGIITIS (GPA) Tuesday, P685 9:15 am-4:15 pm Granulomatosis With Polyangiitis In A Pediatric Patient Presented With Bell’s C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD May 21, 2019 Poster Viewing 11:15 am-1:00 pm Palsy And Pulmonary Involvement VASCULITIS — OTHER

Tuesday, P436 9:15 am-4:15 pm C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE May 21, 2019 Poster Viewing 11:15 am-1:00 pm Pulmonary Manifestations Of Behcet's Disease Area E (Hall F, Level 2), KBHCCD P687 9:15 am-4:15 pm It’s Not The Heart: An Unusual Case Of Medium Vessel Vasculitis And C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD Poster Viewing 11:15 am-1:00 pm Pulmonary Hypertension

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