CODING REFERENCE CARD COAGULATION DEFECTS

D65 Disseminated intravascular D68.312 Antiphospholipid antibody with D68.51 Activated protein C resistance coagulation hemorrhagic disorder Includes: D68.0 Von Willebrand’s Disease Includes: Factor V Leiden mutation Includes: Lupus anticoagulant w/hemorrhagic D68.52 Prothrombin gene mutation disorder Angiohemophilia D68.59 Other primary thrombophilia Factor VIII deficiency with vascular Systemic lupus erythematosus (SLE) Inhibitor with hemorrhagic disorder Includes: defect Antithrombin III deficiency Vascular hemophilia D68.318 Other hemorrhagic disorder due to intrinsic Hypercoagulable state NOS D68.1 Hereditary Factor XI Deficiency circulation anticoagulants, antibodies, or Primary hypercoagulable state NEC Includes: inhibitors Primary thrombophilia NEC Protein C deficiency Hemophilia C Includes: Protein S deficiency PTA deficiency Antithromboplastinemia Thrombophilia NOS Rosenthal’s disease Antithromboplastinogenemia D68.2 Hereditary Deficiency of other clotting Hemorrhagic disorder due to intrinsic increase in D68.61 Antiphospholipid syndrome Includes: factors antithrombin Hemorrhagic disorder due to intrinsic increase in Anticardiolipin syndrome Includes: anti-VIIIa Antiphospholipid antibody syndrome AC globulin deficiency Hemorrhagic disorder due to intrinsic increase in D68.62 Lupus anticoagulant syndrome Congenital afibrinogenemia anti- iXa Includes: Deficiency of factor I Hemorrhagic disorder due to intrinsic increase in Lupus anticoagulant Deficiency of factor II anti-XIa Presence of SLE inhibitor Deficiency of factor V Deficiency of factor VII D68.32 Hemorrhagic disorder due to extrinsic D68.69 Other thrombophilia Deficiency of factor X circulating anticoagulants Includes: Hypercoagulable states NEC Deficiency of factor XII Includes: Secondary hypercoagulable state NOS Deficiency of factor XIII Drug-induced hemorrhagic disorder Dysfibrinogenemia Hemorrhagic disorder due to increase in anti-IIa D68.8 Other specified coagulation defects Hypoproconvertinemia Hemorrhagic disorder due to increase in anti -Xa D68.9 Coagulation defect, unspecified Owren’s Disease Hyperheparinemia Proaccelerin Deficiency D68.311 Acquired hemophilia D68.4 Acquired coagulation factor deficiency *Appropriate diagnosis code for patients on Includes: Includes: therapeutic anticoagulants is Deficiency due to liver disease Autoimmune hemophilia Z79.01 Long term (current) use of anticoagulants Autoimmune inhibitors to clotting factors Deficiency due to vit. K deficiency Secondary hemophilia

Rev. 10.2020

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