CODING REFERENCE CARD COAGULATION DEFECTS D65 Disseminated intravascular D68.312 Antiphospholipid antibody with D68.51 Activated protein C resistance coagulation hemorrhagic disorder Includes: D68.0 Von Willebrand’s Disease Includes: Factor V Leiden mutation Includes: Lupus anticoagulant w/hemorrhagic D68.52 Prothrombin gene mutation Angiohemophilia disorder D68.59 Other primary thrombophilia Factor VIII deficiency with vascular Systemic lupus erythematosus (SLE) Inhibitor with hemorrhagic disorder Includes: defect Antithrombin III deficiency Vascular hemophilia D68.318 Other hemorrhagic disorder due to intrinsic Hypercoagulable state NOS D68.1 Hereditary Factor XI Deficiency circulation anticoagulants, antibodies, or Primary hypercoagulable state NEC Includes: inhibitors Primary thrombophilia NEC Protein C deficiency Hemophilia C Includes: Protein S deficiency PTA deficiency Antithromboplastinemia Thrombophilia NOS Rosenthal’s disease Antithromboplastinogenemia D68.2 Hereditary Deficiency of other clotting Hemorrhagic disorder due to intrinsic increase in D68.61 Antiphospholipid syndrome Includes: factors antithrombin Hemorrhagic disorder due to intrinsic increase in Anticardiolipin syndrome Includes: anti-VIIIa Antiphospholipid antibody syndrome AC globulin deficiency Hemorrhagic disorder due to intrinsic increase in D68.62 Lupus anticoagulant syndrome Congenital afibrinogenemia anti- iXa Includes: Deficiency of factor I Hemorrhagic disorder due to intrinsic increase in Lupus anticoagulant Deficiency of factor II anti-XIa Presence of SLE inhibitor Deficiency of factor V Deficiency of factor VII D68.32 Hemorrhagic disorder due to extrinsic D68.69 Other thrombophilia Deficiency of factor X circulating anticoagulants Includes: Hypercoagulable states NEC Deficiency of factor XII Includes: Secondary hypercoagulable state NOS Deficiency of factor XIII Drug-induced hemorrhagic disorder Dysfibrinogenemia Hemorrhagic disorder due to increase in anti-IIa D68.8 Other specified coagulation defects Hypoproconvertinemia Hemorrhagic disorder due to increase in anti -Xa D68.9 Coagulation defect, unspecified Owren’s Disease Hyperheparinemia Proaccelerin Deficiency D68.311 Acquired hemophilia D68.4 Acquired coagulation factor deficiency *Appropriate diagnosis code for patients on Includes: Includes: therapeutic anticoagulants is Deficiency due to liver disease Autoimmune hemophilia Z79.01 Long term (current) use of anticoagulants Autoimmune inhibitors to clotting factors Deficiency due to vit. K deficiency Secondary hemophilia Rev. 10.2020 NOTE: This tool is intended to assist with documentation only and is not intended to take the place of clinical analysis. Information regarding any law or regulation does not constitute legal or tax advice and is subject to change based upon the issuance of new guidance and/or change in laws or regulations. Reference Official ICD-10-CM coding Highmark Blue Shield is an independent licensee of the Blue Cross and Blue Shield Association. guidelines and manuals or electronic medical coding software for accurate ICD-10-CM codes and specificity. .