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A Case of Labyrinthine Fistula by Cholesteatoma Mimicking Lateral Canal Benign Paroxysmal Positional Vertigo

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A Case of Labyrinthine Fistula by Cholesteatoma Mimicking Lateral Canal Benign Paroxysmal Positional Vertigo online © ML Comm CASE REPORT Korean J Audiol 2014;18(3):153-157 pISSN 2092-9862 / eISSN 2093-3797 http://dx.doi.org/10.7874/kja.2014.18.3.153 A Case of Labyrinthine Fistula by Cholesteatoma Mimicking Lateral Canal Benign Paroxysmal Positional Vertigo Dae Bo Shim, Kyung Min Ko, Mee Hyun Song, and Chang Eun Song Department of Otorhinolaryngology, Myongji Hospital, Goyang, Korea Received October 31, 2014 Acute peripheral vestibulopathy, of which the chief complaint is positional vertigo, comprises Revised November 27, 2014 benign paroxysmal positional vertigo (BPPV), labyrinthitis, labyrinthine fistula, and cerebello- Accepted November 28, 2014 pontine angle tumors. Since the typical presentation of labyrinthine fistulas may be sensorineu- Address for correspondence ral hearing loss, positional vertigo, or disequilibrium, it is often difficult to distinguish from BPPV Chang Eun Song, MD or Meniere’s disease. Herein we report a 61-year-old female patient with typical symptoms and Department of Otorhinolaryngology, signs attributable to geotropic type variant of the lateral semicircular canal BPPV on the left Myongji Hospital, side, who eventually was confirmed as having a labyrinthine fistula from chronic otitis media 55 Hwasu-ro 14beon-gil, with cholesteatoma on the left side. This is another case where, even in the presence of isolat- Deogyang-gu, Goyang 412-270, ed vertigo showing typical findings of acute peripheral vestibulopathy, other otologic symp- Korea toms and signs must not be overlooked. Tel +82-31-810-5451 Korean J Audiol 2014;18(3):153-157 Fax +82-31-969-0500 KEY WORDS: Labyrinthine fistula · Cholesteatoma · Benign paroxysmal positional vertigo. E-mail [email protected] Introduction media with cholesteatoma, of which the initial nystagmus mim- icked that of the lateral semicircular canal BPPV, and thus re- The most common peripheral vestibulopathies diagnosed port it a possible explanation for the mechanism underlying from positional vertigo may include benign paroxysmal po- the nystagmus pattern. sitional vertigo (BPPV), labyrinthitis, and acute vestibular neuritis, and less commonly labyrinthine fistula or cerebello- Case Report pontine angle tumors.1) Labyrinthine fistula, in particular, is reported to rise from 3.6 to 13.9% of chronic otitis media with A 61-year-old female patient was admitted to the emergen- cholesteatoma, and known to affect the lateral semicircular cy unit with the complaint of 2 days’ dizziness of whirling canal most frequently.2,3) Typical symptoms of labyrinthine fis- nature accompanied by nausea and vomiting. The patient had tula are positional vertigo, severe disequilibrium, and senso- medical history of hypertension and diabetes mellitus. Bedside rineural hearing loss, collectively making it difficult to differ- neurologic examination revealed otherwise nonspecific. Brain entiate from BPPV or Meniere’s disease.4) Confounding the diffusion weighted image (DWI) for the differential diagnosis distinction is the sensitivity of the fistula test, of which is report- of a central pathology was normal. On otoscopic examinations, ed to be between 30 to 60% at best. High resolution comput- normal right tympanic membrane was seen, but purulent ear ed tomography of the temporal bone (TBCT) may help diag- discharge was filling the left external ear canal. The patient nose fistulas with sensitivity of 90%, but this sensitivity is had been feeling a loss of hearing in her left ear for quite a long confined to the lesions of the lateral semicircular canal, and its time and had been visiting a local otorhinolaryngologic clin- accuracy has often been doubted.5) The authors have experi- ic for several months diagnosed and treated for chronic exter- enced a case of labyrinthine fistula complicating chronic otitis nal otitis in the left ear. The patient showed spontaneous, right- beating horizontal nystagmus (6.36 d/s). There was no gaze- This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons. evoked nystagmus, and head thrust test was normal. Left-beating org/licenses/by-nc/3.0/) which permits unrestricted non-commercial horizontal nystagmus (9.70 d/s) was noted after head shaking. use, distribution, and reproduction in any medium, provided the original work is properly cited. Dix-Hallpike test to either side provoked geotropic horizontal Copyright © 2014 The Korean Audiological Society 153 Labyrinthine Fistula Mimicking Benign Paroxysmal Positional Vertigo nystagmus, but the nystagmus was stronger on the left side the therapeutic maneuver. A neurootologic examination re- (21.23 d/s on the left side compared to 15.00 d/s on the right) vealed weak spontaneous, right-beating horizontal nystag- and so was the degree of symptoms. Geotropic direction-chang- mus. After head shaking, the horizontal nystagmus was seen ing horizontal nystagmus was demonstrated on both sides to beat to the left. The patient was negative for positional nys- during the supine roll test. The intensity of the nystagmus on tagmus from the Dix-Hallpike test and supine roll test, but both sides was comparable showing 17.71 d/s on the right side left-beating horizontal nystagmus on the head bending nystag- and 17.03 d/s on the left side. The latency and duration of po- mus test and right-beating horizontal nystagmus on the lying- sitional nystagmus were 2 and 29 seconds, respectively on the down nystagmus test was demonstrated, respectively. From right side, and 3 and 30 seconds, respectively on the left side. these atypical nystagmus patterns, a thorough examination of On the head bending nystagmus or lying-down nystagmus the ear was undertaken, where keratinous debris and inflam- test, left-beating horizontal nystagmus (7.00 d/s) on the head matory polyps were hidden behind the purulent material block- bending nystagmus test and right-beating horizontal nystag- ing the left external auditory canal. The keratinous debris was mus (14.93 d/s) on the lying-down nystagmus test was dem- cleared and polypoid tissues were removed for tissue pathol- onstrated, respectively (Fig. 1). The bithermal caloric test re- ogy, after which the patient was sent for the TBCT. On the sponse demonstrated unilateral canal paresis of 29.98% on the TBCT, the left middle ear cavity was mostly occupied with soft left side. These findings collectively led to the initial impres- tissue eroding all the ossicles as well as the bone overlying the sion of geotropic variant of the left lateral semicircular canal lateral semicircular canal and the tegmen tympani (Fig. 2). BPPV on the left side combined with ipsilesional external oti- Magnetic resonance imaging and brain DWI were taken but tis. The patient received the modified Lempert maneuver for reported negative for intradural intracranial invasion. treatment of the presumptive BPPV and was prescribed with Under the diagnosis of left cholesteatomatous chronic oti- empirical topical and oral antibiotics for management of the tis media with the complication of labyrinthine fistula, the pa- external otitis. She was discharged from the emergency unit tient was admitted to the hospital. The patient was instructed for an our clinic visit scheduled for the following day. an absolute bed rest in a 30 degree head elevated position. A At the next follow-up visit, the patient still complained of a brain-blood-barrier-penetrating intravenous antibiotic and os- positional vertigo aggravated on a leftward head turn, despite motic laxative were prescribed. Pure tone audiometry, taken 10° 10° A 2.5 sec B 2.5 sec 10° 10° C 2.5 sec D 2.5 sec Fig. 1. Results of video-oculographic recordings. A: Geotropic positional nystagmus appears when the head is turned to the right in the supine position. B: Geotropic positional nystagmus appears when the head is turned to the left in the supine position. C: Left horizontal nystagmus appears when the head bent 30 degrees forward in the neutral sitting position. D: Right horizontal nystagmus appears when the patient lies supine with the head flexed 30 degrees forward. 154 Korean J Audiol 2014;18(3):153-157 Shim DB, et al. Fig. 2. Axial and coronal scans of temporal bone computed tomogra- phy (TBCT). Axial (A) and coronal (B) views of TBCT reveals a soft tis- sue density in the left middle ear cav- ity. Erosion of the lateral semicircu- lar canal by assumed cholesteatoma can be seen in the left temporal bone A B (white arrows). on the day of admission, showed normal air-conduction thresh- not involving the endosteum so that the endosteum is merely old of 18 dB HL for the right ear, and a mixed hearing loss separating the perilymphatic space from the matrix.7) In more with an air-conduction threshold of 78 dB HL for the left ear rare cases, the granulation or fibrous tissue may infiltrate the (Fig. 3A). Tissue pathology taken on the first clinic exam was membranous labyrinth, thus some authors have described a reported as a cholesteatoma. After resolution of dizziness, ca- three-stage classification of labyrinthine fistulas.8) nal wall-down tympanomastoidectomy was performed for In this case, we initially suspected the patient to have a cen- complete removal of the cholesteatoma on the 7th day of ad- tral pathology because of the inverted head shaking nystagmus mission. Intraoperatively, dehiscence of the bony labyrinth of beating to the opposite direction from the spontaneous nystag- the lateral semicircular canal was observed without any leak- mus. However, no central lesions were observed on the brain age of perilymphatic fluid after the removal of the matrix. The DWI. On both the Dix-Hallpike test and supine roll test in the dehiscence was covered by bone paste and muscle fascia. In emergency unit, substantial geotropic direction-changing hor- the immediate postoperative period, the patient complained of izontal nystagmus was provoked. Head bending nystagmus dizziness, and a weak right-beating horizontal nystagmus was was beating to the left, and lying-down nystagmus was to the observed.
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