Publications for Matthew Kiernan

2021 Weiss, M., Macklin, E., McIlduff, C., Vucic, S., Wainger, B., Higashihara, M., Pavey, N., van den Bos, M., Menon, P., Kiernan, M., Goutman, S., Goyal, N., Rutkove, S., Ladha, S., et Kiernan, M., Vucic, S. (2021). Association of Cortical al (2021). Effects of mexiletine on hyperexcitability in sporadic Hyperexcitability and Cognitive Impairment in Patients With amyotrophic lateral sclerosis: Preliminary findings from a small Amyotrophic Lateral Sclerosis. Neurology, 96(16), e2090- phase II randomized controlled trial. Muscle and Nerve, 63(3), e2097. [M href="http://dx.doi.org/10.1002/mus.27146">[More ore Information] Information] Ahmed, R., Kiernan, M. (2021). Author Response: Phenotypic McCann, E., Henden, L., Fifita, J., Zhang, K., Grima, N., Variability in ALS-FTD and Effect on Survival. Neurology, Bauer, D., Chan Moi Fat, S., Twine, N., Pamphlett, R., Kiernan, 96(23), 1103-1104. [M Australian sporadic amyotrophic lateral sclerosis. Journal of ore Information] Medical Genetics, 58(2), 87-95. [More Information] (2021). Behavioural changes predict poorer survival in amyotrophic lateral sclerosis. Brain and Cognition, 150, Chan Moi Fat, S., McCann, E., Williams, K., Henden, L., 105710. [More Nicholson, G., et al (2021). Genetic analysis of GLT8D1 and Information] ARPP21 in Australian familial and sporadic amyotrophic lateral sclerosis. Neurobiology of Aging, 101, 2.97E+11-2.97E+13. Brainstem Correlates of Pathological Laughter and Crying [More Information] Frequency in ALS. Frontiers in Neurology, 12, 704059. [More Fifita, J., Chan Moi Fat, S., McCann, E., Williams, K., Twine, Information] N., Bauer, D., Rowe, D., Pamphlett, R., Kiernan, M., Tan, V., et al (2021). Genetic Analysis of Tryptophan Metabolism Genes Forrest, S., Kim, J., De Sousa, C., Cheong, R., Crockford, D., in Sporadic Amyotrophic Lateral Sclerosis. Frontiers in Sheedy, D., Stevens, J., McCrossin, T., Tan, R., McCann, H., Immunology, 12. [More Lewy body disease and clinical parkinsonism in amyotrophic Information] lateral sclerosis. European Journal of Neurology, 28(7), 2192- 2199. [More Kiernan, M., Vucic, S., Talbot, K., McDermott, C., Hardiman, Information] O., Shefner, J., Al-Chalabi, A., Huynh, W., Cudkowicz, M., Talman, P., et al (2021). Improving clinical trial outcomes in McManus, L., Lowery, M., Merletti, R., S�gaard, K., amyotrophic lateral sclerosis. Nature Reviews Neurology, 17(2), Besomi, M., Clancy, E., Van Die�n, J., Hug, F., Wrigley, T., 104-118. [More Information] experimental design in electromyography (CEDE) project: Terminology matrix. Journal of Electromyography and Huynh, W., Tu, S., Mahoney, C., Schwartz, R., Kiernan, M. Kinesiology, 59, 102565. [More Neurology, 96(14), 677-678. href="http://dx.doi.org/10.1212/WNL.0000000000011710">[M ore Information] Dharmadasa, T., Howells, J., Matamala, J., Simon, N., Burke, D., Vucic, S., Kiernan, M. (2021). Cortical inexcitability Agarwal, S., Highton-Williamson, E., Caga, J., Howells, J., defines an adverse clinical profile in amyotrophic lateral Dharmadasa, T., Matamala, J., Ma, Y., Shibuya, K., Hodges, J., sclerosis. European Journal of Neurology, 28(1), 90-97. [More excitability predicts cognitive phenotypes in amyotrophic Information] lateral sclerosis. Scientific Reports, 11(1), 2172. [More Hannaford, A., Pavey, N., van den Bos, M., Geevasinga, N., Information] Menon, P., Shefner, J., Kiernan, M., Vucic, S. (2021). Diagnostic Utility of Gold Coast Criteria in Amyotrophic Nathani, D., Spies, J., Barnett, M., Pollard, J., Wang, M., Lateral Sclerosis. Annals of Neurology, 89(5), 979-986. [More indications and decision tools. Muscle and Nerve, 64(2), 125- Information] 139. [More Information] Wainger, B., Macklin, E., Vucic, S., McIlduff, C., Paganoni, S., Maragakis, N., Bedlack, R., Goyal, N., Rutkove, S., Lange, D., Trinh, T., Park, S., Murray, J., Pickering, H., Lin, C., Martin, Kiernan, M., et al (2021). Effect of Ezogabine on Cortical and A., Friedlander, M., Kiernan, M., Goldstein, D., Krishnan, A. Spinal Motor Neuron Excitability in Amyotrophic Lateral (2021). Neu-horizons: neuroprotection and therapeutic use of Sclerosis: A Randomized Clinical Trial. JAMA Neurology, riluzole for the prevention of oxaliplatin-induced 78(2), 186-196. [More Cancer, 29(2), 1103-1110. href="http://dx.doi.org/10.1007/s00520-020-05591-x">[More Information] href="http://dx.doi.org/10.1007/s11764-021-01012-y">[More Information] Ahmed, R., Tse, N., Chen, Y., Henning, E., Hodges, J., Kiernan, M., Irish, M., Farooqi, I., Piguet, O. (2021). Neural Timmins, H., Li, T., Trinh, T., Kiernan, M., Harrison, M., correlates of fat preference in frontotemporal dementia: Boyle, F., Friedlander, M., Goldstein, D., Park, S. (2021). translating insights from the obesity literature. Annals of Weekly Paclitaxel-Induced Neurotoxicity in Breast Cancer: Clinical and Translational Neurology, 8(6), 1318-1329. [More [More Information] Information] Devenney, E., Tu, S., Caga, J., Ahmed, R., Ramsey, E., Zoing, 2020 M., Kwok, J., Halliday, G., Piguet, O., Hodges, J., Kiernan, M. (2021). Neural mechanisms of psychosis vulnerability and Mahoney, C., Dharmadasa, T., Huynh, W., Halpern, J., Vucic, perceptual abnormalities in the ALS-FTD spectrum. Annals of S., Mowat, D., Kiernan, M. (2020). A novel phenotype of Clinical and Translational Neurology, 8(8), 576-1591. [More heterozygous mutation in paraplegin. Muscle and Nerve, 62(1), Information] E44-E45. [More Kiernan, M. (2021). Neurology and clinical neurophysiology: Information] An artificial divide. Practical Neurology, 21(4), 274-275. [More Information] Eisen, A., Großkreutz, J., Hardiman, O., Henderson, R., Matamala, J., Simon, N., Vucic, S., Burke, D., Kiernan, M., et Mahoney, C., Ahmed, R., Huynh, W., Tu, S., Rohrer, J., al (2020). A proposal for new diagnostic criteria for ALS. Bedlack, R., Hardiman, O., Kiernan, M. (2021). Clinical Neurophysiology, 131(8), 1975-1978. [More Amyotrophic Lateral Sclerosis. CNS Drugs, 35(5), 483-505. href="http://dx.doi.org/10.1007/s40263-021-00820-1">[More Information] Vucic, S., Higashihara, M., Sobue, G., Atsuta, N., Doi, Y., Kuwabara, S., Kim, I., Kim, E., Talman, P., Menon, P., El-Wahsh, S., Finger, E., Piguet, O., Mok, V., Rohrer, J., Kiernan, M. (2020). ALS is a multistep process in South Kiernan, M., Ahmed, R. (2021). Predictors of survival in Korean, Japanese, and Australian patients. Neurology, 94(15), frontotemporal lobar degeneration syndromes. Journal of E1657-E1663. [M href="http://dx.doi.org/10.1136/jnnp-2020-324349">[More ore Information] Information] Katzeff, J., Bright, F., Lo, K., Kril, J., Connolly, A., Crossett, Caga, J., Zoing, M., Foxe, D., Ramsey, E., D'Mello, M., B., Ittner, L., Kassiou, M., Loy, C., Hodges, J., Piguet, O., Mioshi, E., Ahmed, R., Kiernan, M., Piguet, O. (2021). Kiernan, M., Halliday, G., Kim, W. (2020). Altered serum Problem-focused coping underlying lower caregiver burden in protein levels in frontotemporal dementia and amyotrophic ALS-FTD: implications for caregiver intervention. Amyotrophic lateral sclerosis indicate calcium and immunity dysregulation. Lateral Sclerosis and Frontotemporal Degeneration, 22(5-6), Scientific Reports, 10(1), 13741. [More href="http://dx.doi.org/10.1080/21678421.2020.1867180">[Mor Information] e Information] Kiernan, M., Shefner, J., Kaji, R., Burke, D. (2020). Hannaford, A., Vucic, S., Kiernan, M., Simon, N. (2021). Amyotrophic lateral sclerosis: A new diagnostic paradigm. Review article �spotlight on ultrasonography in the diagnosis Journal of Neurology, Neurosurgery and Psychiatry, 91(9), 903- of peripheral nerve disease: The evidence to date�. 904. [More Information] href="http://dx.doi.org/10.2147/IJGM.S295851">[More Information] Kandula, T., Farrar, M., Cohn, R., Carey, K., Johnston, K., Kiernan, M., Krishnan, A., Park, S. (2020). Changes in long Vucic, S., Kiernan, M., Menon, P., Huynh, W., Rynders, A., term peripheral nerve biophysical properties in childhood Ho, K., Glanzman, R., Hotchkin, M. (2021). Study protocol of cancer survivors following neurotoxic chemotherapy. Clinical RESCUE-ALS: A Phase 2, randomised, double-blind, placebo- Neurophysiology, 131(4), 783-790. [More sclerosis patients to assess bioenergetic catalysis with CNM- Information] Au8 as a mechanism to slow disease progression. BMJ Open, 11(1), e041479. [More Information] S. (2020). Characteristics and risk factors of bortezomib induced peripheral neuropathy: A systematic review of phase De Boer, E., Orie, V., Williams, T., Baker, M., De Oliveira, H., III trials. Hematological Oncology, 38(3), 229-243. [More Halliday, G., Kiernan, M., Vucic, S., et al (2021). TDP-43 Information] proteinopathies: A new wave of neurodegenerative diseases. Journal of Neurology, Neurosurgery and Psychiatry, 92(1), 86- Besomi, M., Hodges, P., Clancy, E., Van Die�n, J., Hug, F., 95. [More Information] T., Kiernan, M., et al (2020). Consensus for experimental design in electromyography (CEDE) project: Amplitude Timmins, H., Li, T., Goldstein, D., Trinh, T., Mizrahi, D., normalization matrix. Journal of Electromyography and Harrison, M., Horvath, L., Friedlander, M., Kiernan, M., Park, Kinesiology, 53, 102438. [More paclitaxel- and oxaliplatin-treated cancer survivors. Journal of Information] Cancer Survivorship. [More Kiernan, M., Vucic, S. (2020). Cortical hyperexcitability Information] evolves with disease progression in ALS. Annals of Clinical Park, S., Thurbon, R., Kiernan, M. (2020). Isaacs syndrome: and Translational Neurology, 7(5), 733-741. [More Journal of Neurology, Neurosurgery and Psychiatry, 91(12), Information] 1243-1244. [More Information] M. (2020). Early focality and spread of cortical dysfunction in Kiernan, M. (2020). Jewels in the crown: A century of amyotrophic lateral sclerosis: A regional study across the motor achievement for the Journal of Neurology, Neurosurgery & cortices. Clinical Neurophysiology, 131(4), 958-966. [More Psychiatry, 91(1). [More Information] Timmins, H., Li, T., Huynh, W., Kiernan, M., Baron-Hay, S., Kiernan, M., Bostock, H., Park, S., Kaji, R., Krarup, C., Boyle, F., Goldstein, D., Park, S. (2020). Electrophysiological Krishnan, A., Kuwabara, S., Lin, C., Misawa, S., Moldovan, and phenotypic profiles of taxane-induced neuropathy. Clinical M., Vucic, S., Burke, D., et al (2020). Measurement of axonal Neurophysiology, 131(8), 1979-1985. [More 131(1), 308-323. href="http://dx.doi.org/10.1016/j.clinph.2019.07.023">[More Mahoney, C., Kiernan, M. (2020). Expanding the availability of Information] medications for amyotrophic lateral sclerosis in Australia. Kiernan, M. (2020). Metabolomic insights into neurodegene� Medical Journal of Australia, 212(4), 189-1.89E+03. [More Psychiatry, 91(12), 1250. href="http://dx.doi.org/10.1136/jnnp-2020-324856">[More Kiernan, M. (2020). Fasciculation anxiety syndrome in Information] clinicians: FASICS. Practical Neurology, 20(6), 433-434. [More Information] priorities. Journal of Neurology, Neurosurgery and Psychiatry, Edwards, L., Halmagyi, G., Mallawaarachchi, A., Thompson, 91(2), 140-148. [More Information] syndrome. Practical Neurology, 20(4), 338-339. [More Information] Nerve Pathology Distinguishes Focal Motor Chronic McCann, E., Fifita, J., Grima, N., Galper, J., Mehta, P., Inflammatory Demyelinating Polyradiculoneuropathy From Freckleton, S., Zhang, K., Henden, L., Hogan, A., Chan Moi Multifocal Motor Neuropathy. Journal of Clinical Fat, S., Piguet, O., Hodges, J., Kwok, J., Halliday, G., Kiernan, Neuromuscular Disease, 22(1), 1-10. [Mo immunopathological analysis of CHCHD10 in Australian re Information] amyotrophic lateral sclerosis and frontotemporal dementia and de Carvalho, M., Kiernan, M., Pullman, S., Rezania, K., Turner, transgenic TDP-43 mice. Journal of Neurology, Neurosurgery M., Simmons, Z. (2020). Neurophysiological features of and Psychiatry, 91(2), 162-171. [More Frontotemporal Degeneration, 21(S1), 11-17. href="http://dx.doi.org/10.1080/21678421.2020.1837174">[Mor Wan, H., Carey, K., D'Silva, A., Vucic, S., Kiernan, M., e Information] Kasparian, N., Farrar, M. (2020). Health, wellbeing and lived Swash, M., Burke, D., Turner, M., Grosskreutz, J., Leigh, P., experiences of adults with SMA: A scoping systematic review. Decarvalho, M., Kiernan, M. (2020). Occasional essay: Upper Orphanet Journal of Rare Diseases, 15(1), 70. [More Journal of Neurology, Neurosurgery and Psychiatry, 91(3), 227- Information] 234. [More Information] Rowe, D., Kiernan, M., Bauer, D., Blair, I., Williams, K. Vucic, S., Ryder, J., Mekhael, L., Henderson, R., Mathers, S., (2020). Identity by descent analysis identifies founder events Needham, M., Schultz, D., Kiernan, M. (2020). Phase 2 and links SOD1 familial and sporadic ALS cases. npj Genomic randomized placebo controlled double blind study to assess the Medicine, 5(1), 32. [More Information] lateral sclerosis (TEALS Study): Study protocol clinical trial Higashihara, M., van den Bos, M., Menon, P., Kiernan, M., (SPIRIT Compliant). Medicine, 99(6), e18904. [Mor inhibition and facilitation. Clinical Neurophysiology, 131(5), e Information] 1000-1010. [More Piguet, O., Kiernan, M. (2020). Phenotypic variability in ALS- Information] FTD and effect on survival. Neurology, 94(19), e2005-e2013. Howells, J., Sangari, S., Matamala, J., Kiernan, M., Marchand- [M function using threshold tracking of the H reflex in healthy ore Information] subjects and patients with motor neurone disease. Clinical Turner, M., Barohn, R., Corcia, P., Fink, J., Harms, M., Neurophysiology, 131(8), 1986-1996. [More Information] href="http://dx.doi.org/10.1002/dmrr.3099">[More Information] Timmins, H., Li, T., Kiernan, M., Horvath, L., Goldstein, D., Park, S. (2020). Quantification of Small Fiber Neuropathy in Vucic, S., Westeneng, H., Al-Chalabi, A., van den Berg, L., Chemotherapy-Treated Patients. The Journal of Pain, 21(1- Talman, P., Kiernan, M. (2019). Amyotrophic lateral sclerosis Feb), 44-58. [More Amyotrophic Lateral Sclerosis and Frontotemporal Information] Degeneration, 20(7-8), 532-537. [Mor Tu, S., Wang, C., Menke, R., Talbot, K., Barnett, M., Kiernan, e Information] M., Turner, M. (2020). Regional callosal integrity and bilaterality of limb weakness in amyotrophic lateral sclerosis. Geevasinga, N., Howells, J., Menon, P., van den Bos, M., Amyotrophic Lateral Sclerosis and Frontotemporal Shibuya, K., Matamala, J., Park, S., Byth, K., Kiernan, M., Degeneration, 21(5-6), 396-402. [Mor index: Toward a personalized diagnosis of ALS. Neurology, e Information] 92(6), e536-e547. [M Huynh, W., Sharplin, L., Caga, J., Highton-Williamson, E., ore Information] Kiernan, M. (2020). Respiratory function and cognitive profile in amyotrophic lateral sclerosis. European Journal of Kiernan, M., Ziemann, U., Eisen, A. (2019). Amyotrophic Neurology, 27(4), 685-691. [More neural excitation and inhibition in the neonatal period. Muscle Information] and Nerve, 60(3), 232-235. [More Borire, A., Issar, T., Kwai, N., Visser, C., Simon, N., Poynten, Information] A., Kiernan, M., Krishnan, A. (2020). Sonographic assessment of nerve blood flow in diabetic neuropathy. Diabetic Medicine, Tu, S., Menke, R., Talbot, K., Kiernan, M., Turner, M. (2019). 37(2), 343-349. [More Lateral Sclerosis and Frontotemporal Degeneration, 20, 281- Information] 284. [Mor Farrar, M., Kiernan, M. (2020). Spinal muscular atrophy � e Information] the dawning of a new era. Nature Reviews Neurology, 16(11), 593-594. [More Information] J. (2019). Clinical and neuroimaging investigations of language disturbance in frontotemporal dementia-motor neuron disease Kiernan, M., Cornblath, D. (2020). Subacute sensory patients. Journal of Neurology, 266(4), 921-933. [More syndromes. Journal of Neurology, Neurosurgery and Information] Psychiatry, 91(8), 793-794. [More Ke, Y., Chan, G., Stefanoska, K., Au, C., Bi, M., Muller, J., Information] Przybyla, M., Feiten, A., Prikas, E., Halliday, G., Piguet, O., Kiernan, M., Kassiou, M., Hodges, J., Loy, C., Kril, J., Timmins, H., Li, T., Kiernan, M., Baron-Hay, S., Marx, G., Sutherland, G., et al (2019). CNS cell type-specific gene Boyle, F., Goldstein, D., Park, S. (2020). Taxane-induced profiling of P301S tau transgenic mice identifies genes peripheral neuropathy: differences in patient report and dysregulated by progressive tau accumulation. Journal of objective assessment. Supportive Care in Cancer, 28(9), 4459- Biological Chemistry, 294(38), 14149-14162. [More y">[More Information] Information] Huynh, W., Ahmed, R., Mahoney, C., Nguyen, C., Tu, S., Ahmed, R., Devenney, E., Strikwerda Brown, C., Hodges, J., Caga, J., Loh, P., Lin, C., Kiernan, M. (2020). The impact of Piguet, O., Kiernan, M. (2019). COG-01 Phenotypic variation cognitive and behavioral impairment in amyotrophic lateral in ?ALS-FTD and effect on survival. Amyotrophic Lateral sclerosis. Expert Review of Neurotherapeutics, 20(3), 281-293. Sclerosis and Frontotemporal Degeneration, 20, 301-308. [Mor href="http://dx.doi.org/10.1080/14737175.2020.1727740">[Mor e Information] e Information] Garg, N., Park, S., Howells, J., Vucic, S., Yiannikas, K., Kiernan, M. (2020). The Journal of Neurology, Neurosurgery Mathey, E., Nguyen, T., Noto, Y., Barnett, M., Pollard, J., and Psychiatry centenary milestone award 2020. Journal of Kiernan, M. (2019). Conduction block in immune-mediated Neurology, Neurosurgery and Psychiatry, 91(7), 677. [More Journal of Neurology, 26(8), 1121-1129. href="http://dx.doi.org/10.1111/ene.13953">[More Farrar, M., Kiernan, M. (2020). Treating adults with spinal Information] muscular atrophy with nusinersen. Journal of Neurology, Besomi, M., Hodges, P., van Dieen, J., Carson, R., Clancy, E., Neurosurgery and Psychiatry, 91(11), 1139. [More Lowery, M., et al (2019). Consensus for experimental design in Information] electromyography (CEDE) project: Electrode selection matrix. Journal of Electromyography and Kinesiology, 48, 128-144. [More Gu, Y., Dennis, S., Kiernan, M., Harmer, A. (2019). Aerobic Information] Information] Ahmed, R., Phan, K., Highton-Williamson, E., Strikwerda Bright, F., Werry, E., Dobson-Stone, C., Piguet, O., Ittner, L., Brown, C., Caga, J., Ramsey, E., Zoing, M., Devenney, E., Halliday, G., Hodges, J., Kiernan, M., Loy, C., Kassiou, M., Kim, W., Hodges, J., Piguet, O., Halliday, G., Kiernan, M. Kril, J. (2019). Neuroinflammation in frontotemporal dementia. (2019). Eating peptides: biomarkers of neurodegeneration in Nature Reviews Neurology, 15(9), 540-555. [More Annals of Clinical and Translational Neurology, 6(3), 486-495. Information] [More Information] Arnold, R., Pianta, T., Pussell, B., Endre, Z., Kiernan, M., Krishnan, A. (2019). Potassium control in chronic kidney Huynh, W., Dharmadasa, T., Vucic, S., Kiernan, M. (2019). disease: implications for neuromuscular function. Internal Functional biomarkers for amyotrophic lateral sclerosis. Medicine Journal, 49(7), 817-825. [More href="http://dx.doi.org/10.3389/fneur.2018.01141">[More Information] Information] Agarwal, S., Ahmed, R., DMello, N., Foxe, D., Kaizik, C., Henderson, R., Garton, F., Kiernan, M., Turner, M., Eisen, A. Kiernan, M., Halliday, G., Piguet, O., Hodges, J. (2019). (2019). Human cerebral evolution and the clinical syndrome of Predictors of survival and progression in behavioural variant amyotrophic lateral sclerosis. Journal of Neurology, frontotemporal dementia. European Journal of Neurology, Neurosurgery and Psychiatry, 90(5), 570-575. [More href="http://dx.doi.org/10.1111/ene.13887">[More Information] Information] Carroll, A., Burns, J., Nicholson, G., Kiernan, M., Vucic, S. Smyth, B., Krishnan, A., Gallagher, M., Kiernan, M., Snelling, (2019). Inherited Neuropathies. Seminars in Neurology, 39(5), P., Hawley, C., Fernando, M., Hand, S., Grimley, K., Burman, 620-639. [More Information] haemodiafiltration on uraemic neuropathy: FINESSE study Agarwal, S., Koch, G., Hillis, A., Huynh, W., Ward, N., Vucic, protocol. BMJ Open, 9(1), 1-8. [More transcranial magnetic stimulation: insights from Information] neurodegenerative disease and stroke. Journal of Neurology, Werry, E., Bright, F., Piguet, O., Ittner, L., Halliday, G., Neurosurgery and Psychiatry, 90(1), 47-57. [More Recent developments in TSPO PET imaging as a biomarker of Information] neuroinflammation in neurodegenerative disorders. Anderson, S., Kiernan, M., Ho, P. (2019). Lenalidomide-related International Journal of Molecular Sciences, 20(13), 3161. [More and Review of Drug-related Cases in Multiple Myeloma. Information] Clinical Lymphoma, Myeloma and Leukemia, 19(4), e169-e171. Menon, P., Yiannikas, C., Kiernan, M., Vucic, S. (2019). [More Regional motor cortex dysfunction in amyotrophic lateral Information] sclerosis. Annals of Clinical and Translational Neurology, 6(8), Kiernan, M., Goadsby, P., Burke, D. (2019). Marco Polo of 1373-1382. [More Psychiatry, 90(6), 627-628. href="http://dx.doi.org/10.1136/jnnp-2019-320989">[More Issar, T., Arnold, R., Kwai, N., Walker, S., Yan, A., Borire, A., Information] Poynten, A., Pussell, B., Endre, Z., Kiernan, M., et al (2019). McMackin, R., Muthuraman, M., Groppa, S., Babiloni, C., Relative contributions of diabetes and chronic kidney disease to Taylor, J., Kiernan, M., Nasseroleslami, B., Hardiman, O. neuropathy development in diabetic nephropathy patients. (2019). Measuring network disruption in neurodegenerative Clinical Neurophysiology, 130(11), 2088-2095. [More Neurology, Neurosurgery and Psychiatry, 90(9), 1011-1020. href="http://dx.doi.org/10.1136/jnnp-2018-319581">[More Gold, J., Rowe, D., Kiernan, M., Vucic, S., Mathers, S., Van Information] eijk, R., Nath, A., Montojo, M., Norato, G., Santamaria, U., et Kiernan, M. (2019). Milestones. Journal of Neurology, al (2019). Safety and tolerability of Triumeq in amyotrophic Neurosurgery and Psychiatry, 90(11), 1189. [More Sclerosis and Frontotemporal Degeneration, 20(7-Aug), 595- Information] 604. [Mor Higashihara, M., Menon, P., Geevasinga, N., van den Bos, M., e Information] Kiernan, M., Vucic, S. (2019). Motor neuron disease with malignancy: Clinical and pathophysiological insights. Clinical Yang, Y., Halliday, G., Kiernan, M., Tan, R. (2019). TDP-43 Neurophysiology, 130(9), 1557-1561. [More C9ORF72 or ATXN2 gene expansions. Neurology, 93(19), Information] e1748-e1755. [M Ahmed, R., Landin-Romero, R., Liang, C., Keogh, J., Henning, ore Information] E., Strikwerda Brown, C., Devenney, E., Hodges, J., Kiernan, M., Farooqi, I., Piguet, O. (2019). Neural networks associated Dharmadasa, T., Matamala, J., Howells, J., Simon, N., Vucic, with body composition in frontotemporal dementia. Annals of S., Kiernan, M. (2019). The effect of coil type and limb Clinical and Translational Neurology, 6(9), 1707-1717. [More excitability using TMS. Neuroscience Letters, 699, 84-90. [More Information] Information] Noto, Y., Garg, N., Li, T., Timmins, H., Park, S., Shibuya, K., Tan, R., Guennewig, B., Dobson-Stone, C., Kwok, J., Kril, J., Shahrizaila, N., Huynh, W., Matamala, J., Dharmadasa, T., Kiernan, M., Hodges, J., Piguet, O., Halliday, G. (2019). The Yiannikas, K., Vucic, S., Kiernan, M. (2018). Comparison of underacknowledged PPA-ALS: A unique clinicopathologic cross-sectional areas and distal-proximal nerve ratios in subtype with strong heritability. Neurology, 92(12), e1354- amyotrophic lateral sclerosis. Muscle and Nerve, 58(6), 777- e1366. [More href="http://dx.doi.org/10.1212/WNL.0000000000007146">[M Information] ore Information] Borire, A., Issar, T., Kwai, N., Visser, L., Simon, N., Poynten, Nathani, D., Barnett, M., Spies, J., Pollard, J., Wang, M., A., Kiernan, M., Krishnan, A. (2018). Correlation between Kiernan, M. (2019). Vasculitic neuropathy: Comparison of markers of peripheral nerve function and structure in type 1 clinical predictors with histopathological outcome. Muscle and diabetes. Diabetes - Metabolism: Research and Reviews, 34(7), Nerve, 59(6), 643-649. [More href="http://dx.doi.org/10.1002/mus.26431">[More Information] Information] Menon, P., Kiernan, M., Vucic, S. (2018). Cortical excitability 2018 varies across different muscles. Journal of Neurophysiology, 120(3), 1397-1403. [More Burke, D., Moalem-Taylor, G., Howells, J. (2018). A unified Information] model of the excitability of mouse sensory and motor axons. Noto, Y., Simon, N., Selby, A., Garg, N., Shibuya, K., Journal of the Peripheral Nervous System, 23(3), 159-173. [More Park, S., Vucic, S., Kiernan, M. (2018). Ectopic impulse Information] generation in peripheral nerve hyperexcitability syndromes and Baker, M., Dharmadasa, T., Jaiser, S., Kiernan, M. (2018). amyotrophic lateral sclerosis. Clinical Neurophysiology, 129(5), Amyotrophic lateral sclerosis � Time for beta testing? 974-980. [More href="http://dx.doi.org/10.1016/j.clinph.2018.04.613">[More Information] Information] Borire, A., Arnold, R., Pussell, B., Kwai, N., Visser, L., Simon, Garg, N., Park, S., Howells, J., Noto, Y., Vucic, S., Yiannikas, N., Kiernan, M., Krishnan, A. (2018). Effects of haemodialysis C., Tomlinson, S., Huynh, W., Simon, N., Mathey, E., Spies, J., on intraneural blood flow in end-stage kidney disease. Muscle Pollard, J., Kiernan, M., et al (2018). 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