Published online: 2020-04-24 THIEME 136 Case Report | Relato de Caso Hemifacial Spasm Associated with Chiari Type I Malformation: Surgical Considerations and Case Report Espasmo Hemifacial Associado a Malformação de Chiari Tipo I: Considerações Cirúrgicas e Relato de Caso Carlos Augusto Ferreira Lobão1 Ulysses de Oliveira Sousa2 Diego Arthur Castro Cabral3 Fernanda Myllena Sousa Campos3 1 Division of Neurosurgery, Department of Neuroscience, Hospital Address for correspondence DiegoArthurCastroCabral,Medical Porto Dias, Belém, PA, Brazil oStudents, Universidade Federal do Pará, Belém, Pará, Brasil 2 Department of Neurosurgery, Hospital Saúde da Mulher, Belém, PA, Brazil (e-mail:
[email protected]). 3 Institute of Health Sciences, Faculdade de Medicina, Universidade Federal do Pará, Belém, PA, Brazil Arq Bras Neurocir 2020;39(2):136–141. Abstract Hemifacial spasm (HS) is a movement disorder characterized by paroxysmal and irregular contractions of the muscles innervated by the facial nerve. Chiari malforma- tion type I (CM I) is a congenital disease characterized by caudal migration of the cerebellar tonsils, and surgical decompression of foramen magnum structures has been used for treatment. The association of HS with CM I is rare, and its pathophysiol- ogy and therapeutics are speculative. There are only a few cases reported in the literature concerning this association. The decompression of the posterior fossa for the treatment of CM I has been reported to relieve the symptoms of HS, suggesting a relation between these diseases. However, the possible complications of posterior fossa surgery cannot be underrated. We report the case of a 66-year-old patient, in ambulatory follow-up due to right HS, no longer responding to botulinum toxin treatment.