American Thoracic Society International Conference

Where today’s science meets tomorrow’s careTM Rare Lung Disease Guide

May 18-May 23, 2018 San Diego, CA conference.thoracic.org

May 2018 Dear Colleagues: The scope of the American Thoracic Society is amazingly broad – covering pulmonary, critical care, and sleep medicine. The challenge that we face each year as we put the International Conference program together is that some clinical topics that may be of central importance to our members, conference attendees, and patients may not be prominently featured in the program. This is especially the case with some rare lung diseases. With each challenge though, comes opportunity. Because of the wealth of scientific and clinical information presented at ATS 2018, these diseases, though uncommon, will be the focus of many presentations over the next several days. The purpose of this Rare Lung Disease Guide is to help you more easily find these presentations.

Jess Mandel, MD In his chapter on rare lung diseases in “Breathing in America: Diseases, Progress, and Hope” (2010) Francis X. McCormack, MD noted that research on uncommon respiratory diseases Chair, ATS International has produced some of the most exciting discoveries in pulmonary medicine, stating that “Insights gained from uncommon lung diseases often shed light on the more common ones.” Conference Committee The definition of a rare disease by its prevalence varies by country. A disease or disorder is defined as rare in the United States when it affects fewer than 200,000 Americans at any given time. This guide was compiled by a small group of ATS Members who studied the ATS 2018 abstracts – authors requested to be considered for inclusion. Many thanks to Dr. Frank McCormack, Dr. Lisa Young, Dr. Jonathan Kropski, Dr. Nishant Gupta, and Mr. Jack Kelly for their assistance with this resource. There are a number of patient advocacy groups that are exhibiting at ATS 2018. In addition to attending the presentations noted within, I encourage you to visit with them to learn more about these rare conditions. Groups listed in bold are members of the ATS Public Advisory Roundtable and can all be found in PAR Path, near the ATS Center in the Exhibit Hall. Learn more about this group and its many contributions to the Society and its work at: http://www.thoracic.org/patients/par/. Sincerely, Jess Mandel, MD Chair, ATS International Conference Committee

Alpha-1 Foundation, Booth 536 LUNGevity Foundation, Booth 541 ARDS Foundation, Booth 439 Lymphangiomatosis and Gorham’s Disease Alliance (LGD), Booth 537 Asthma and Allergy Network, Booth 641 NTM Info & Research, Inc., Booth 539 Children’s Interstitial Lung Disease Foundation, Inc. (CHILD), Booth 740 Primary Ciliary Dyskinesia Foundation (PCD), Booth 636 Cystic Fibrosis Research, Inc., Booth 638 Pulmonary Fibrosis Foundation, Booth 722 Foundation for Sarcoidosis Research, Booth 639 Pulmonary Hypertension Association, Booth 1542 Hermansky-Pudlak Syndrome Network, Inc., Booth 637 Scleroderma Foundation, Booth 640 The LAM Foundation/Lymphangioleiomyomatosis, Booth 538 Tuberous Sclerosis Alliance, Booth 738 Lung Transplant Foundation, Booth 736 List Current as of 3/29/18

1 DISCLAIMER The purpose of this guide is to help the American Thoracic Society International Conference attendees navigate the viewing of posters for disorders that typically get less attention at the conference because of their rarity. During abstract submission, authors were instructed to check the box for consideration in the Rare Lung Disease Guide; the abstracts on that list were then further narrowed down. Conditions represented by less than 50 abstracts were considered for inclusion. We regret that not all rare diseases could be represented, and welcome suggestions for additional categories for listing in future editions. Please email us with any suggestions: [email protected]. Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location

ACD-MPV (ALVEOLAR CAPILLARY DYSPLASIA WITH MISALIGNMENT OF THE PULMONARY VEINS)

Tuesday, P1046 9:15 am-4:15 pm; A Novel Pathogenic Variant in FOXF1 Gene in an Infant with Severe C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Pulmonary Hypertension DISEASE San Diego Convention Center P1074 9:15 am-4:15 pm; Neonatal Severe Refractory Persistent Pulmonary Hypertension of C66: PEDIATRIC CASE REPORTS: CARDIOVASCULAR AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm the Newborn (PPHN), Rare and Perplexing Diagnosis CRITICAL CARE DISEASE San Diego Convention Center

ALPHA-1 ANTITRYPSIN DEFICIENCY

Sunday, P1387 9:15 am-4:15 pm; Alpha-1 Antitrypsin Deficiency Is Not a Risk Factor for Cancer: A46: TOPICS IN ALPHA-1-ANTITRYPSIN DEFICIENCY Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm A Cross-Sectional Study San Diego Convention Center P1396 9:15 am-4:15 pm; Alpha-1 Antitrypsin Therapy: A Satisfaction Survey of Individuals A46: TOPICS IN ALPHA-1-ANTITRYPSIN DEFICIENCY Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Self-Administering San Diego Convention Center P1397 9:15 am-4:15 pm; Alpha-1 Antitrypsin Deficiency Screening in Adults with A46: TOPICS IN ALPHA-1-ANTITRYPSIN DEFICIENCY Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Bronchiectasis Using Dry Blood Spot San Diego Convention Center P1388 9:15 am-4:15 pm; Results from a Large-Scale Screening Program for Alpha-1 A46: TOPICS IN ALPHA-1-ANTITRYPSIN DEFICIENCY Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Antitrypsin Deficiency: A History of Bronchiectasis Is Associated San Diego Convention Center with the ZZ Genotype P1391 9:15 am-4:15 pm; Smoking and SZ Alpha-1 Antitrypsin Deficiency (AATD): Exploring A46: TOPICS IN ALPHA-1-ANTITRYPSIN DEFICIENCY Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm the Relationship Between Smoke Exposure and Airflow Obstruction San Diego Convention Center P1393 9:15 am-4:15 pm; Analysis of Factors Associated with FEV1 Decline in Alpha-1 A46: TOPICS IN ALPHA-1-ANTITRYPSIN DEFICIENCY Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Antitrypsin Deficient Patients: A Comparison of Statistical San Diego Convention Center Approaches P1394 9:15 am-4:15 pm; Demographics and Patient Characteristics of the PI*MZ Allele A46: TOPICS IN ALPHA-1-ANTITRYPSIN DEFICIENCY Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Subgroup Identified in the US National Detection Program for Alpha- San Diego Convention Center 1-Antitrypsin Deficiency P1398 9:15 am-4:15 pm; Characteristics of Patients with Rare PI*F and PI*I Alleles from the A46: TOPICS IN ALPHA-1-ANTITRYPSIN DEFICIENCY Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm US National Detection Program for Alpha-1-Antitrypsin Deficiency San Diego Convention Center P42 9:15 am-4:15 pm; Modern Epidemiology of Alpha-1-Antitrypsin Deficiency (AATD) A55: ENVIRONMENTAL AND OCCUPATIONAL GENETICS, Area A (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm in the UK GENOMICS, AND EPIGENETICS San Diego Convention Center P41 9:15 am-4:15 pm; The Irish National Alpha-1 Antitrypsin Deficiency Targeted Detection A55: ENVIRONMENTAL AND OCCUPATIONAL GENETICS, Area A (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Programme GENOMICS, AND EPIGENETICS San Diego Convention Center

3 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P456 9:15 am-4:15 pm; Effects Of Recombinant Alpha1-Antitrypsin IgG1 Fc-fusion Protein A75: COPD: TARGETS, MODELS, AND CLINICAL STUDIES Area E (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm (AAT-Fc) In Experimental Emphysema San Diego Convention Center P476 9:15 am-4:15 pm; Effect Of N-glycosylation Of Recombinant Alpha-1 Antitrypsin A75: COPD: TARGETS, MODELS, AND CLINICAL STUDIES Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Therapeutic Protein Structure And Function: A Biophysical And San Diego Convention Center Molecular Dynamic Simulation Study Monday, P130 9:15 am-4:15 pm; Cardiovascular status and risk in Alpha 1 anti-trypsin Deficiency B54: CHRONIC DISORDERS: EVALUATION AND Area B (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm INTERVENTION San Diego Convention Center P1422 9:15 am-4:15 pm; Ventilation and Gas Transfer Distribution in Alpha-1 Antitrypsin B64: COPD: LUNG FUNCTION, IMAGING AND Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Deficiency After Replacement Therapy PATHOPHYSIOLOGY San Diego Convention Center P1440 9:15 am-4:15 pm; Proposal and Validation of a Minimal Clinically Important Difference B64: COPD: LUNG FUNCTION, IMAGING AND Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm (MCID) for Annual Pulmonary CT Density Decline PATHOPHYSIOLOGY San Diego Convention Center P1446 9:15 am-4:15 pm; Imaging Biomarkers of Emphysema in COPD and Alpha-1 B64: COPD: LUNG FUNCTION, IMAGING AND Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Antitrypsin Deficiency Patients using Accelerated 129Xe MRI PATHOPHYSIOLOGY San Diego Convention Center P1452 9:15 am-4:15 pm; Ventilation And Gas Transfer Measured By 129Xe MRI In Alpha-1 B64: COPD: LUNG FUNCTION, IMAGING AND Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Antitrypsin Heterozygotes: A Pilot Study PATHOPHYSIOLOGY San Diego Convention Center Oral Presentation 2:15 pm-4:15 pm Comprehensive Gene Resequencing of SERPINA1 in SPIROMICS Re- B96: GENETICS, EPIGENETICS, AND SMOKING Room 15 A-B (Mezzanine Level) veals Novel Rare Loci for 1-antitrypsin Deficiency and Emphysema San Diego Convention Center Tuesday, 622 9:15 am-11:15 am; Evaluation of the Safety and Effectiveness of the Spiration Valve C24: NEW TECHNOLOGIES FOR MANAGING COPD Room 30 C-E (Upper Level) May 22, 2018 Poster Viewing 9:15 am-9:45 am System for Single Lobe Treatment of Severe Emphysema in Patients San Diego Convention Center Poster Discussion 9:45 am-11:15 am with Alpha-1 Antitrypsin Deficiency 906 9:15 am-11:15 am; Measuring Endoplasmic Reticulum Viscosity in Cell Models of C28: ROLE OF CELLULAR CROSS TALK IN LUNG Pacific Ballroom 15-17 Poster Viewing 9:15 am-9:45 am 1-Antitrypsin Deficiency. HOMEOSTASIS AND AGING (North Tower, First Floor) Poster Discussion 9:45 am-11:15 am Marriott Marquis San Diego Marina 1016 9:15 am-11:15 am; A Systematic Analysis of Terminal Bronchiole Remodeling in COPD C29: LUNG STRUCTURE AND FUNCTION: NEW INSIGHTS Pacific Ballroom 24-26 Poster Viewing 9:15 am-10:00 am Patients with and without Alpha-1 Antitrypsin Deficiency FROM MEASUREMENT AND MODELING (North Tower, First Floor) Poster Discussion 10:00 am-11:15 am Marriott Marquis San Diego Marina P1338 9:15 am-4:15 pm; Aα-Val360 and Aα-Val541in Early Alpha-1 Antitrypsin Deficiency C34: COPD POTPOURRI Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1326 9:15 am-4:15 pm; Proteomic Profiling of Protein-Protein Interactions of Alpha-1 C34: COPD POTPOURRI Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Antitrypsin in Plasma San Diego Convention Center

4 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P1358 9:15 am-4:15 pm; Increased Neutrophil-Platelet Interactions in Alpha-1 Antitrypsin C34: COPD POTPOURRI Area L (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Deficient Individuals is Corrected Post Augmentation Therapy San Diego Convention Center P1414 9:15 am-4:15 pm; Predictors of Alpha-1 Antitrypsin Deficiency Among Medicare C42: CONTEMPORARY TOPICS IN COPD Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Beneficiaries with Chronic Obstructive Pulmonary Disease in the San Diego Convention Center United States P1415 9:15 am-4:15 pm; Predictors of Alpha-1 Antitrypsin Deficiency Among Commercially C42: CONTEMPORARY TOPICS IN COPD Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Insured Chronic Obstructive Pulmonary Disease Patients in the San Diego Convention Center United States P208 9:15 am-4:15 pm; Pulmonary Hypertension Characteristics in Alpha-1 Antitrypsin C70: WHO'S NEXT? NEW INSIGHTS INTO ATYPICAL WHO Area C (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Deficiency Patients Undergoing Lung Transplant Evaluation GROUP 1 AND GROUP 2-5 PH San Diego Convention Center P358 9:15 am-4:15 pm; Comparison of Pulmonary CT Density analysis between two leading C75: LUNG MEASUREMENT: NOVEL METHODS AND Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm software programs TECHNIQUES San Diego Convention Center Wednesday, P1336 9:15 am-4:15 pm; Recurrent Acute Pancreatitis Secondary to Alpha-1-Antitrypsin D40: COPD: CASE REPORTS Area L (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Deficiency San Diego Convention Center P1359 9:15 am-4:15 pm; A Comprehensive Repository Of Aatd Patient-specific Induced D53: OFF THE BEATEN PATH: NEW APPROACHES TO Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pluripotent Stem Cells With Detailed Clinical Phenotyping For COPD PATHOGENESIS San Diego Convention Center Translational Research P1345 9:15 am-4:15 pm; Alpha-1 Antitrypsin Antisense Oligonucleotide Modulates Protease- D53: OFF THE BEATEN PATH: NEW APPROACHES TO Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Antiprotease Imbalance without Further Aggravating Smoke- COPD PATHOGENESIS San Diego Convention Center induced Lung Injury P1363 9:15 am-4:15 pm; Lectin Complement Pathway Activation In Copd And Alpha-1 D53: OFF THE BEATEN PATH: NEW APPROACHES TO Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Antitrypsin (A1AT) Deficiency COPD PATHOGENESIS San Diego Convention Center P1380 9:15 am-4:15 pm; The Altered Abundance of Hydrogen Voltage-Gated Channel 1 D53: OFF THE BEATEN PATH: NEW APPROACHES TO Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm (HVCN1) in Neutrophils of Alpha-One Antitrypsin Deficient Patients COPD PATHOGENESIS San Diego Convention Center P1386 9:15 am-4:15 pm; Role for Cela1 in Postnatal Lung Remodeling and AAT-Deficient D53: OFF THE BEATEN PATH: NEW APPROACHES TO Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Emphysema COPD PATHOGENESIS San Diego Convention Center 606 1:30 pm-3:30 pm; Neutrophil Elastase and Proteinase 3 Activity in PiSZ Alpha-1 D101: MECHANISTIC AND TRANSLATIONAL STUDIES IN Room 30 C-E (Upper Level) Poster Viewing 1:30 pm-2:00 pm Antitrypsin Deficiency COPD San Diego Convention Center Poster Discussion 2:00 pm-3:30 pm

5 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, 612 1:30 pm-3:30 pm; Gene Co-expression Networks Analysis Reveals Novel Molecular D101: MECHANISTIC AND TRANSLATIONAL STUDIES IN Room 30 C-E (Upper Level) May 23, 2018 Poster Viewing 1:30 pm-2:00 pm Endotypes in Alpha-1 Antitrypsin Deficiency COPD San Diego Convention Center Poster Discussion 2:00 pm-3:30 pm 602 1:30 pm-3:30 pm; The Circulating Neutrophil Proteome is Altered in Alpha-1 D101: MECHANISTIC AND TRANSLATIONAL STUDIES IN Room 30 C-E (Upper Level) Poster Viewing 1:30 pm-2:00 pm Antitrypsin Deficiency and is Modified By Intravenous Augmentation COPD San Diego Convention Center Poster Discussion 2:00 pm-3:30 pm Therapy AMYLOIDOSIS Sunday, 206 2:15 pm-4:15 pm; Presentation, Survival and Factors of Survival in Respiratory Tract A103: ILD: OUTCOMES Room 6 D (Upper Level) May 20, 2018 Poster Viewing 2:15 pm-2:45 p Amyloidosis: A French Consecutive Case Series of 72 Patients San Diego Convention Center Poster Discussion 2:45 pm-4:15 pm Monday, P750 9:15 am-4:15 pm; Everything that Wheezes Is Not Asthma: Rare Case of Primary B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Endobronchial Amyloidoma San Diego Convention Center P256 9:15 am-4:15 pm; Endobronchial Obstruction by a Solitary Extramedullary B69: CASE REPORTS IN THORACIC ONCOLOGY I Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Plasmacytoma with Light Chain Amyloidosis San Diego Convention Center Wednesday, P893 9:15 am-4:15 pm; Pulmonary Amyloidosis — A Deadly Disease D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P703 9:15 am-4:15 pm; A Unique Case of Systemic Amyloidosis Presenting with Recurrent D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pleural Effusion San Diego Convention Center ANTI-GLOMERULAR BASEMENT MEMBRANE DISEASE Monday, P630 9:15 am-4:15 pm; Alveolar Hemorrhage in Anti-Basement Membrane Antibody Disease B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P669 9:15 am-4:15 pm; A Co-Occurrence of Good Pastures Disease and Graves Disease B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Wednesday, P881 9:15 am-4:15 pm; Relapsing Remitting Isolated Pulmonary Anti Glomerular Basement D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Membrane Disease San Diego Convention Center ARTERIOVENOUS MALFORMATION Monday, P757 9:15 am-4:15 pm; Bronchial Dieulafoy’s Disease and Mediastinal Arteriovenous B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Malformation San Diego Convention Center

6 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P1046 9:15 am-4:15 pm; Paradoxical Embolization and a Large Pulmonary Arteriovenous B58: WHO'S BAD: CASE REPORTS IN PULMONARY Area J (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Malformation VASCULAR MEDICINE I San Diego Convention Center P1047 9:15 am-4:15 pm; An Uncommon Cause of Hypoxia; Pulmonary Arteriovenous B58: WHO'S BAD: CASE REPORTS IN PULMONARY Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Malformations Successfully Treated with Embolization VASCULAR MEDICINE I San Diego Convention Center Wednesday, P446 9:15 am-4:15 pm; Successful Catheter Embolization of a Pulmonary Arteriovenous D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Malformation in a Patient with Hereditary Pulmonary Arterial VASCULAR MEDICINE II San Diego Convention Center Hypertension Due to BMPR2 Mutation P474 9:15 am-4:15 pm; A Case of a Massive Pulmonary Artery Aneurysm D50: CLOT ON THE ROCKS: CASE REPORTS OF PE AND Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm CTEPH San Diego Convention Center BENIGN ASBESTOS PLEURAL EFFUSION Monday, P782 9:15 am-4:15 pm; BAPE, A Rare Cause of Exudate Effusion B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center BENIGN METASTASIZING LEIOMYOMA Sunday, P1168 9:15 am-4:15 pm; Benign Metastasizing Leiomyoma Presenting with Lymphangitic A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Carcinomatosis San Diego Convention Center Monday, P318 9:15 am-4:15 pm; Benign Metastasizing Leiomyomas of the Lung in a Woman 12 B71: CASE REPORTS IN THORACIC ONCOLOGY III Area D (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Years After Hysterectomy for Uterine Fibroids San Diego Convention Center Wednesday, P638 9:15 am-4:15 pm; Not All Wheezes Are the Same: A Rare Presentation of Pulmonary D31: INTERVENTIONAL PULMONARY: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Benign Metastasizing Leiomyoma San Diego Convention Center BERYLLIUM ASSOCIATED LUNG DISEASE Sunday, P1151 9:15 am-4:15 pm; A Case of Fatal Community Acquired Chronic Beryllium Disease A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Surrounding a Beryllium Facility San Diego Convention Center P33 9:15 am-4:15 pm; DNA Methylation Changes in Bronchoalveolar Lavage Associated A55: ENVIRONMENTAL AND OCCUPATIONAL GENETICS, Area A (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm with Chronic Beryllium Disease GENOMICS, AND EPIGENETICS San Diego Convention Center BIRT-HOGG-DUBE SYNDROME Sunday, P1346 9:15 am-4:15 pm; Characterization of CT Scan in Birt-Hogg-Dube Syndrome (BHDs) A39: SARCOIDOSIS AND RARE LUNG DISEASE SCIENTIFIC Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Compared with Non-BHDs Diffuse Cysts Lung Diseases in Chinese ABSTRACTS San Diego Convention Center Patients

7 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P1166 9:15 am-4:15 pm; Strange Coincidences: A Case of Concurrent Sarcoidosis and Birt- A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Hogg-Dubé San Diego Convention Center P1446 9:15 am-4:15 pm; Secondary Pneumothorax in a Patient with Birt-Hogg-Dube A48: DYSPNEA: CASE REPORTS I Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Syndrome San Diego Convention Center Monday, P810 9:15 am-4:15 pm; Birt Hogg Dube Syndrome — A Rare Cause of Recurrent B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Pneumothorax San Diego Convention Center Wednesday, 201 1:30 pm-3:30 pm; Rethinking the Epidemiology of Birt-Hogg-Dubé: A Genetics-Based D103: TRANSPLANT AND ILD POTPOURRI Room 6 D (Upper Level) May 23, 2018 Poster Viewing 1:30 pm-2:00 pm Approach San Diego Convention Center Poster Discussion 2:00 pm-3:30 pm BLUE RUBBER BLEB NEVUS SYNDROME Wednesday, P568 9:15 am-4:15 pm; Blue Rubber Bleb Nevus Syndrome: A Rare Cause of Obstructive D59: CASE REPORTS IN SLEEP DISORDERS Area F (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Sleep Apnea San Diego Convention Center BRONCHIOLITIS OBLITERANS Sunday, 101 9:15 am-11:15 am; Study of the Etiology and Outcomes in Non-Transplant Related A23: ILD: DIAGNOSIS Room 5 A-B (Upper Level) May 20, 2018 Poster Viewing 9:15 am-9:45 am Small Airway Disease San Diego Convention Center Poster Discussion 9:45 am-11:15 am Monday, P1449 9:15 am-4:15 pm; Comparative Histological and Morphometrical Analysis of Small B64: COPD: LUNG FUNCTION, IMAGING AND Area L (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Conducting Airways in Constrictive Bronchiolitis and Chronic PATHOPHYSIOLOGY San Diego Convention Center Obstructive Pulmonary Disease Tuesday, 221 9:15 am-11:15 am Feasibility And Validity Of A Home-based Spirometry Program After C23: LUNG TRANSPLANT AND ACUTE ILD Room 6 D (Upper Level) May 22, 2018 Poster Viewing 9:15 am-9:45 am Hematopoietic Stem Cell Transplantation For The Early Detection Of San Diego Convention Center Poster Discussion 9:15 am-11:15 am Pulmonary Impairment P849 9:15 am-4:15 pm; Quantitative CT and Parametric Response Mapping Analysis for the C32: LUNG TRANSPLANTATION: CLINICAL STUDIES Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Assessment and Monitoring of Bronchiolitis Obliterans Syndrome San Diego Convention Center P1099 9:15 am-4:15 pm; Un-Even Steven: An Unusual Complication of Stevens-Johnson C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Syndrome DISEASE San Diego Convention Center 912 Flavoring-Related Lung Disease in a Worker at a Coffee Roasting C106: OCCUPATIONAL LUNG EPIDEMIOLOGY Pacific Ballroom 15-17 (North Tower, Poster Viewing 2:15 pm-2:45 pm; and Packaging Facility First Floor) Poster Discussion 2:45 pm-4:15 pm Marriott Marquis San Diego Marina

8 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, 918 2:15 pm-4:15 pm; Successful Treatment of Deployment-Related Constrictive C106: OCCUPATIONAL LUNG EPIDEMIOLOGY Pacific Ballroom 15-17 (North Tower, May 22, 2018 Poster Viewing 2:15 pm-2:45 pm Bronchiolitis with Azithromycin First Floor) Poster Discussion 2:45 pm-4:15 pm Marriott Marquis San Diego Marina Wednesday, 213 9:15 am-11:15 am; Pulmonary Screening of Pediatric Hematopoietic Stem Cell D25: ADVANCES IN RARE LUNG AND PULMONARY Room 6 D (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am Transplant Patients VASCULAR DISEASE IN CHILDREN San Diego Convention Center Poster Discussion 9:15 am-11:15 am P886 9:15 am-4:15 pm; Obliterative Bronchiolitis: A Rare Complication of Aspiration D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pneumonitis San Diego Convention Center P1033 9:15 am-4:15 pm; Every Dog Has Its Day: FIBOS Caused by Diacetyl Exposure from an D34: LUNG TRANSPLANT AND DRUG INDUCED LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Unusual Source DISEASE: CASE REPORTS San Diego Convention Center P731 9:15 am-4:15 pm; Obliterative Bronchitis and Bronchiolitis After Toxic Epidermal D37: CF AND NON-CF BRONCHIECTASIS AND IMMUNE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Necrolysis DEFICIENCIES: CASE REPORTS San Diego Convention Center P768 9:15 am-4:15 pm; Angry Airways: A Tale of Bronchocentric Granulomatosis D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P785 11:15 am-1:00 pm Inexplicable Dyspnea in a Soldier: Constrictive Bronchiolitis D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) San Diego Convention Center BRONCHOLITHIASIS Wednesday, P663 9:15 am-4:15 pm; Bronchoscopic Removal of Broncholiths D31: INTERVENTIONAL PULMONARY: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center CASTLEMAN DISEASE Monday, P671 9:15 am-4:15 pm; Bronchiolitis Obliterans from Paraneoplastic Pemphigus Associated B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm with Unicentric Castleman Disease San Diego Convention Center CONGENITAL CENTRAL HYPOVENTILATION SYNDROME Sunday, P541 9:15 am-4:15 pm; Mild Phenotype in Nonpolyalanine Repeat Mutations of PHOX2B in A59: PEDIATRIC SLEEP Area F (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Congenital Central Hypoventilation Syndrome San Diego Convention Center P542 9:15 am-4:15 pm; Congenital Central Hypoventilation Syndrome in Israel — a New A59: PEDIATRIC SLEEP Area F (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Nationwide Center San Diego Convention Center P563 9:15 am-4:15 pm; NIH Toolbox Cognition Battery Study: A Multi-Site Evaluation of A59: PEDIATRIC SLEEP Area F (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Neurocognition in Congenital Central Hypoventilation Syndrome San Diego Convention Center (CCHS) 9 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location CONNECTIVE TISSUE DISEASE ASSOCIATED ILD Sunday, P731 9:15 am-4:15 pm; The Common Gain-of-function MUC5B Promoter Variant A71: THE EPIGENOME, GENOME AND NON-CODING RNAs Area G (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm rs35705950 Contributes to the Risk of Developing Rheumatoid IN LUNG DISEASE San Diego Convention Center Arthritis Interstitial Lung Disease P1278 9:15 am-4:15 pm; The Incidence of Interstitial Pneumonia with Autoimmune Features A43: ILD SCIENTIFIC ABSTRACTS: GENERAL Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm in a Tertiary Referral Center Interstitial Lung Disease Clinic San Diego Convention Center 201 2:15 pm-4:15 pm; Survival Distinction in Interstitial Pneumonia with Autoimmune A103: ILD: OUTCOMES Room 6 D (Upper Level) Poster Viewing 2:15 pm-2:45 pm Features (IPAF) Patients: Results from a 5-Year Historical Cohort in San Diego Convention Center Poster Discussion 2:45 pm-4:15 pm an Interstitial Lung Diseases (ILD) Population Monday, P654 9:15 am-4:15 pm; Pulmonary 18F-FDG Up-Take Refines Current Risk Stratification in B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Non Specific Interstitial Pneumonitis (NSIP) San Diego Convention Center P732 9:15 am-4:15 pm; Autoantibodies associated with Connective Tissue Disease in B35: LUNG TRANSPLANT AND ILD SCIENTIFIC Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Interstitial Lung Disease — A Prospective Study ABSTRACTS: DRUG INDUCED LUNG DISEASE, San Diego Convention Center AUTOIMMUNE LUNG DISEASE CYSTIC AND BULLOUS LUNG DISEASE — OTHER Sunday, P1138 9:15 am-4:15 pm; Occam’s Razor: An Extremely Rare Presentation of a Very Rare A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Pulmonary Manifestation of Lupus San Diego Convention Center Tuesday, P1030 9:15 am-4:15 pm; Idiopathic Giant Bullous Emphysema in a Female Teenager C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm BRONCHOSCOPY San Diego Convention Center Wednesday, P1334 9:15 am-4:15 pm; The Cocktail Effect of Cigarettes and Marijuana in Giant Bullous D40: COPD: CASE REPORTS Area L (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Emphysema San Diego Convention Center CYSTIC FIBROSIS Sunday, 522 9:15 am-11:15 am; The ENaC Regulatory Peptide SPX-101 Is Resistant to Proteolytic A28: ADVANCES IN COPD AND ASTHMA Room 28 C-E (Upper Level) May 20, 2018 Poster Viewing 9:15 am-9:45 am Degradation in Diseased Sputum San Diego Convention Center Poster Discussion 9:45 am-11:15 am P521 9:15 am-4:15 pm; Attain Health - Integrating Telehealth and Integrative Health A67: PULMONARY REHABILITATION IN NON-COPD AND Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Coaching in Cystic Fibrosis Care LUNG TRANSPLANTATION San Diego Convention Center P747 9:15 am-4:15 pm; Distal Airway Oxygen Tension Is Low in Cystic Fibrosis: Noninvasive A72: WHAT'S NEW IN CYSTIC FIBROSIS, BPD AND OTHER Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Measurement Using a Novel, Fast-Response Oxygen Sensor CONGENITAL PEDIATRIC LUNG DISEASES San Diego Convention Center

10 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P749 9:15 am-4:15 pm; Lung Transplantation In Cystic Fibrosis Patients In Italy: A Single A72: WHAT'S NEW IN CYSTIC FIBROSIS, BPD AND OTHER Area G (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Center Experience Of 20 Years Follow-Up CONGENITAL PEDIATRIC LUNG DISEASES San Diego Convention Center P770 9:15 am-4:15 pm; Baseline Cystic Fibrosis Transmembrane Conductance Regulator A72: WHAT'S NEW IN CYSTIC FIBROSIS, BPD AND OTHER Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Protein Expression Predicts Subject Response to Lumacaftor- CONGENITAL PEDIATRIC LUNG DISEASES San Diego Convention Center Ivacaftor Treatment Monday, 205 9:15 am-11:15 am; Multi-Omics Profiling of Lumacaftor/Ivacaftor Response in Cystic B25: CHRONIC SUPPERATIVE LUNG DISEASE IN Room 6 D (Upper Level) May 21, 2018 Poster Viewing 9:15 am-9:45 am Fibrosis CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am 222 9:15 am-11:15 am; Biochemical and Biophysical Analysis of Direct Bronchial Mucus B25: CHRONIC SUPPURATIVE LUNG DISEASE IN Room 6 D (Upper Level) Poster Viewing 9:15 am-9:45 am from Preschool Aged Patients with CF CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am P566 9:15 am-4:15 pm; Increased Airway Mucus Rheology in Cystic Fibrosis Coincides with B56: CYSTIC FIBROSIS Area F (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Positive Microbial Culture in Bronchioalveolar Lavage Fluid San Diego Convention Center P578 9:15 am-4:15 pm; Characterization of Cystic Fibrosis Plasma Induced Innate Immune B56: CYSTIC FIBROSIS Area F (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Response and Its Clinical Implication San Diego Convention Center P967 9:15 am-4:15 pm; Proteostatic Network Gene Expression Is Decreased in Fdel508 B63: INFLAMMATION AND CELLULAR RESPONSES IN Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Homozygote Cystic Fibrosis Patients CYSTIC FIBROSIS San Diego Convention Center P970 9:15 am-4:15 pm; High-throughput Yeast Phenomics Identifies Genetic Modifiers That B63: INFLAMMATION AND CELLULAR RESPONSES IN Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Partially Rescue Human W1282X-CFTR CYSTIC FIBROSIS San Diego Convention Center P961 9:15 am-4:15 pm; CFTR-deficient Pigs Have Altered Bone Microarchitecture And B63: INFLAMMATION AND CELLULAR RESPONSES IN Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Elevated Closed Cortical Porosity At Birth CYSTIC FIBROSIS San Diego Convention Center P960 9:15 am-4:15 pm; Targeting ENaC With An Epithelial RNAi Trigger Delivery Platform For B63: INFLAMMATION AND CELLULAR RESPONSES IN Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm The Treatment Of Cystic Fibrosis CYSTIC FIBROSIS San Diego Convention Center P975 9:15 am-4:15 pm; Pharmacology ofα-7 nicotinic acetylcholine receptors (α-7 nAChR) B63: INFLAMMATION AND CELLULAR RESPONSES IN Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm agonists in Cystic Fibrosis CYSTIC FIBROSIS San Diego Convention Center P976 9:15 am-4:15 pm; Evaluation of Apremilast as a novel Therapeutic Agent in Cystic B63: INFLAMMATION AND CELLULAR RESPONSES IN Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Fibrosis CYSTIC FIBROSIS San Diego Convention Center P962 9:15 am-4:15 pm; Neutrophil Extracellular Traps Increase Proinflammatory Cytokine B63: INFLAMMATION AND CELLULAR RESPONSES IN Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Expression by Human Airway Epithelial Cells In Vitro CYSTIC FIBROSIS San Diego Convention Center

11 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P978 9:15 am-4:15 pm; Applying Epix™ Technology to Enable Ex Vivo Theratyping Using Air- B63: INFLAMMATION AND CELLULAR RESPONSES IN Area H (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm way Epithelial Cells Derived from Patients with Pulmonary Diseases CYSTIC FIBROSIS San Diego Convention Center Tuesday, P105 9:15 am-4:15 pm; Social Complexity: A Strong Influence on Outcomes in Adolescents C39: IDENTIFYING AND TREATING ANXIETY AND Area B (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm with Cystic Fibrosis DEPRESSION IN PULMONARY DISEASES San Diego Convention Center P166 9:15 am-4:15 pm; Differences in the Transition Towards Lung Transplantation for C41: HEALTH SERVICES RESEARCH IN PULMONARY Area B (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Cystic Fibrosis Between the United States and United Kingdom DISEASE San Diego Convention Center P135 9:15 am-4:15 pm; Non Concordance between Sputum and Pulmonary Explant C41: HEALTH SERVICES RESEARCH IN PULMONARY Area B (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Fragments Culture in Patients with Cystic Fibrosis after Lung DISEASE San Diego Convention Center Transplantation P1266 9:15 am-4:15 pm; Synergistic Activity of Colistin in Combination with N-Acetylcysteine C60: TRANSLATIONAL AND BASIC INVESTIGATIONS IN Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Against Colistin-Resistant Acinetobacter Baumannii Grown in Biofilms PULMONARY INFECTION San Diego Convention Center P1036 9:15 am-4:15 pm; Gotta Catch ‘Em All: Delayed Diagnosis of Cystic Fibrosis (CF) in C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm an Infant with a Novel CF Transmembrane Conductance Regulator BRONCHOSCOPY San Diego Convention Center (CFTR) Mutation P1037 9:15 am-4:15 pm; Fatal Outcome in a Patient with Cystic Fibrosis and Candia Blankii C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Infection: A Case Report BRONCHOSCOPY San Diego Convention Center Wednesday, 624 9:15 am-11:15 am; Routine Evaluation for Hypoxia, Hypercarbia, and Pulmonary D23: ADULT CF AND NON-CF BRONCHIECTASIS Room 30 C-E (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am Hypertension is Infrequent for Patients with Advanced Cystic San Diego Convention Center Poster Discussion 9:45 am-11:15 am Fibrosis Prior to Lung Transplant Referral P1019 9:15 am-4:15 pm; Regrets Over a Missed Opportunity to Have a Biological Child — D34: LUNG TRANSPLANT AND DRUG INDUCED LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm One Couple's Journey After Lung Transplantation for Cystic Fibrosis DISEASE: CASE REPORTS San Diego Convention Center P735 9:15 am-4:15 pm; Cystic Fibrosis and Twin Pregnancy, the Challenge of D37: CF AND NON-CF BRONCHIECTASIS AND IMMUNE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Multidisciplinary Care: A Case Report DEFICIENCIES: CASE REPORTS San Diego Convention Center 1006 1:30 pm-3:30 pm; hCFTR (human Cystic Fibrosis Transmembrane Conductance D110: EPITHELIAL FUNCTION IN HEALTH AND DISEASE Pacific Ballroom 24-26 (North Tower, Poster Viewing 1:30 pm-2:00 pm Regulator) mRNA Delivered Using a Novel Biodegradable First Floor) Poster Discussion 2:00 pm-3:30 pm Nanovector to CFTR Knock-out Rats Improves CFTR Expression and Marriott Marquis San Diego Marina Chloride Transport Across the Nasal Epithelium in vivo DERMATOMYOSITIS/ANTISYNTHETASE SYNDROME Sunday, 911 9:15 am-11:15 am; Long Term Pulmonary Function in a Cohort of Interstitial Lung A21: CLINICAL AND MECHANISTIC STUDIES OF LUNG Pacific Ballroom 15-17 May 20, 2018 Poster Viewing 9:15 am-9:45 am Disease Patients Positive to Antisynthetase Antibodies FIBROSIS (North Tower, First Floor) Poster Discussion 9:45 am-11:15 am Marriott Marquis San Diego Marina 12 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P1137 9:15 am-4:15 pm; Refractory Rapidly Progressive Interstitial Lung Disease in Anti- A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Melanoma Differentiation Antibody with Clinically Amyopathic San Diego Convention Center Dermatomyositis P1163 9:15 am-4:15 pm; MDA-5 Positive Dermatomyositis Complicated by A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pneumomediastinum San Diego Convention Center P1159 9:15 am-4:15 pm; Organizing Pneumonia as the Presenting Symptom of Anti-MDA5 A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Amyopathic Dermatomyositis San Diego Convention Center P1139 9:15 am-4:15 pm; Successful Application of Rituximab and ECMO in a Patient with A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Rapidly Progressive Interstitial Lung Disease Related to Anti-MDA-5 San Diego Convention Center Antibody Positive Amyopathic Dermatomyositis P1217 9:15 am-4:15 pm; Semi-Quantitative CT Chest Scoring System for Anti-Synthetase A41: ILD SCIENTIFIC ABSTRACTS: DIAGNOSIS, Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Syndrome Associated ILD OUTCOMES, AND PPFE San Diego Convention Center Monday, P625 9:15 am-4:15 pm; Recognizing the Pattern: Anti- MDA 5 Associated Clinically B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Amyopathic Dermatomyositis (CADM) with Rapidly Progressive San Diego Convention Center Interstitial Lung Disease (RP-ILD) Presenting as Multi-Focal Pneumonia P640 9:15 am-4:15 pm; A Pulmonary Prodrome of Anti-PL7 Positive Anti-Synthetase B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Syndrome San Diego Convention Center P678 9:15 am-4:15 pm; Triple the Trouble: A Case Report B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P677 9:15 am-4:15 pm; Why Won't this Pneumonia Go Away B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P656 9:15 am-4:15 pm; Rapidly Fatal Anti Synthetase Syndrome Presenting with Pneumonia B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P665 9:15 am-4:15 pm; A Catastrophic Presentation of Antisynthetase Syndrome with B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Rapidly Progressing Interstitial Lung Disease and Its Antibodies San Diego Convention Center P663 9:15 am-4:15 pm; Rapidly Progressive Interstitial Lung Disease in Amyopathic B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Dermatomyositis: When Skin Meets Lung San Diego Convention Center Wednesday, P862 9:15 am-4:15 pm; Synthesising the Correct Diagnosis in the Work-Up of Interstitial D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Lung Disease: Myositis Panel May Be Key San Diego Convention Center

13 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P866 9:15 am-4:15 pm; Management of Spontaneous Pneumomediastinum in D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Dermatomyositis with Cyclosporine San Diego Convention Center P887 9:15 am-4:15 pm; A Fatal Case of Anti-MDA5 Antibody Positive Clinically Amyopathic D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Dermatomyositis (CADM) Associated with Rapidly Progressive San Diego Convention Center Interstitial Lung Disease P941 9:15 am-4:15 pm; Myositis Associated ILD in a Patient with Autoantibody to PMScl D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center 1:30 pm-3:30 pm; Polymyositis and Dermatomyositis in Lung Transplantation: The D93: LUNG TRANSPLANT: CLINICAL RESEARCH Room 32 A-B (Upper Level) Oral Presentation 2:45 pm-3:00 pm National U.S. Experience San Diego Convention Center DIFFUSE ALVEOLAR HEMORRHAGE Sunday, P1142 9:15 am-4:15 pm; Asymmetric Migrating Diffuse Alveolar Hemorrhage A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Monday, P641 9:15 am-4:15 pm; Sometimes It Can Be Lupus: Diffuse Alveolar Hemorrhage (DAH) in B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm SLE San Diego Convention Center P1145 9:15 am-4:15 pm; Diffuse Alveolar Hemorrhage After a Nephrectomy... What's the B45: CRITICAL CARE CASE REPORTS: ACID-BASE, Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Association? ELECTROLYTES, ENDOCRINE, METABOLIC, AND RENAL San Diego Convention Center ABNORMALITIES P99 9:15 am-4:15 pm; Diffuse Alveolar Hemorrhage Induced by Vaping B51: CIGARETTES, E-CIGARETTES, AND HOOKAHS Area B (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Tuesday, P1109 9:15 am-4:15 pm; A Novel Presentation of Pulmonary Hemorrhage in Infancy C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm DISEASE San Diego Convention Center P1090 9:15 am-4:15 pm; Diffuse Alveolar Hemorrhage Following Generalized Tonic Clonic C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Seizure in a 14 Year-Old Boy DISEASE San Diego Convention Center P1106 9:15 am-4:15 pm; Goodpasture Syndrome in a 15 Month Old Presenting with Anemia C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm and Pulmonary Infiltrates DISEASE San Diego Convention Center P1105 9:15 am-4:15 pm; Double-Positive Goodpasture's Syndrome in a Child: Use of C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Rituximab DISEASE San Diego Convention Center Wednesday, P908 9:15 am-4:15 pm; Pulmonary Renal Syndrome: Diffuse Alveolar Hemorrhage in D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 11:15 am-1:00 pm Association with ANCA Negative Pauci-Immune Glomerulonephritis San Diego Convention Center

14 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P1092 9:15 am-4:15 pm; Amiodarone and Fluconazole: A Deadly Combination D35: DRUG INDUCED LUNG DISEASE: CASE REPORTS Area J (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center DIFFUSE IDIOPATHIC NEUROENDOCRINE CELL HYPERPLASIA Sunday, P1353 9:15 am-4:15 pm; Diffuse Idiopathic Pulmonary Neuroendocrine Cell A39: SARCOIDOSIS AND RARE LUNG DISEASE SCIENTIFIC Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Hyperplasia(DIPNECH): Our Institutional Experience with ABSTRACTS San Diego Convention Center Somatostatin Analog Therapy Monday, P779 9:15 am-4:15 pm; A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Hyperplasia Diagnosed with Transbronchial Lung Cryobiopsy San Diego Convention Center Wednesday, P900 9:15 am-4:15 pm; DIPNECH: A Lung Lined by Tumor D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P760 9:15 am-4:15 pm; Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia D38: COUGH: CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm (DIPNECH), An Under Recognized Clinical Entity San Diego Convention Center P348 9:15 am-4:15 pm; Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia D62: TYPES, GENOTYPES, AND PHENOTYPES: THE THREE Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm (DIPNECH): What Is It And What Should You Know? "T's" OF THORACIC ONCOLOGY San Diego Convention Center DUCHENNE MUSCULAR DYSTROPHY Sunday, P1406 9:15 am-4:15 pm; Comparison of Longitudinal Changes in Expiratory Respiratory A47: NEUROMUSCULAR DISEASE AND RESPIRATION Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Function Endpoints and Inspiratory Flow Reserve (IFR) in Patients San Diego Convention Center with Duchenne Muscular Dystrophy (DMD) Tuesday, P374 9:15 am-4:15 pm; The Natural History of Declining Pulmonary Function in Children C76: CHEST WALL, RESPIRATORY MUSCLES: NEURAL Area D (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm with Duchenne Muscular Dystrophy AND VENTILATORY CONTROL San Diego Convention Center P380 9:15 am-4:15 pm; Diagnostic Differences in Work of Breathing (WOB) Indices And C76: CHEST WALL, RESPIRATORY MUSCLES: NEURAL Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Respiratory Breathing Patterns in Healthy And Duchenne Muscular AND VENTILATORY CONTROL San Diego Convention Center Dystrophy (DMD) Children P370 9:15 am-4:15 pm; Effect of idebenone on respiratory function across various C76: CHEST WALL, RESPIRATORY MUSCLES: NEURAL Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm subgroups in patients with Duchenne Muscular Dystrophy (DMD) AND VENTILATORY CONTROL San Diego Convention Center P379 9:15 am-4:15 pm; Reliability Of Inspiratory Flow Reserve (IFR) Endpoints And Robustness C76: CHEST WALL, RESPIRATORY MUSCLES: NEURAL Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Of Longitudinal Analyses Assessing The Effect Of Idebenone On Ifr In AND VENTILATORY CONTROL San Diego Convention Center Patients With Duchenne Muscular Dystrophy (DMD)

15 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location EOSINOPHILIC DISORDERS — PULMONARY Sunday, P1280 9:15 am-4:15 pm; Retrospective Case Series of Thirty-Two Patients with Biopsy- A43: ILD SCIENTIFIC ABSTRACTS: GENERAL Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Proven Chronic Eosinophilic Pneumonia San Diego Convention Center Monday, P634 9:15 am-4:15 pm; Idiopathic Hyper-Eosinophilic Syndrome Presenting with a Cavitary, B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Eosinophilic Lung Abscess San Diego Convention Center P102 9:15 am-4:15 pm; Up In Smoke: A Case of Eosinophilic Pneumonia After Hookah Use B51: CIGARETTES, E-CIGARETTES, AND HOOKAHS Area B (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Tuesday, P867 9:15 am-4:15 pm; Acute Eosinophilic Pneumonia in the Setting of C35: CLINICAL STUDIES IN IMMUNODEFICIENCY Area H (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Hypogammaglobulinemia San Diego Convention Center P685 9:15 am-4:15 pm; The Jamaican Shuffle C51: CRITICAL CARE CASE REPORTS: YOU GIVE ME Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm FEVER — INFECTION AND SEPSIS San Diego Convention Center P1019 9:15 am-4:15 pm; Treatment of Childhood Hypereosinophilic Syndrome with C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Mepolizumab BRONCHOSCOPY San Diego Convention Center Wednesday, P932 9:15 am-4:15 pm; An Unusual Presentation of Chronic Eosinophilic Pneumonia D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1082 9:15 am-4:15 pm; A Case of Dapsone Induced Eosinophilic Pneumonia D35: DRUG INDUCED LUNG DISEASE: CASE REPORTS Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center EXPOSURE-RELATED IDIOPATHIC INTERSTITIAL PNEUMONIA Sunday, P1146 9:15 am-4:15 pm; Idiopathic Pulmonary Fibrosis in a Rail Yard Worker A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P4 9:15 am-4:15 pm; Domestic and Non-Occupational Exposures in Developing Countries: A54: INDOOR AND OUTDOOR AIR POLLUTION Area A (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm A Case of Desert Lung Syndrome San Diego Convention Center P30 9:15 am-4:15 pm; Cocaine and Hard Metals: Partners in Crime or Guilty by A54: INDOOR AND OUTDOOR AIR POLLUTION Area A (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Association? San Diego Convention Center Monday, 513 9:15 am-11:15 am; Biomass Smoke-Associated Interstitial Lung Disease B24: AN UPDATE ON INDOOR AND OUTDOOR AIR Room 28 C-E (Upper Level) May 21, 2018 Poster Viewing 9:15 am-10:00 am POLLUTION San Diego Convention Center Poster Discussion 10:00 am-11:15 am P82 9:15 am-4:15 pm; Hard Metal Lung Disease Presenting in a Surface Coal Miner B49: OCCUPATIONAL EXPOSURES Area B (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center

16 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, 922 2:15 pm-4:15 pm; Drilling Down on Hard Metal Lung Disease: An Unusual Case of a C106: OCCUPATIONAL LUNG EPIDEMIOLOGY Pacific Ballroom 15-17 May 22, 2018 Poster Viewing 2:15 pm-2:45 pm Dental Lab Technician with Rapidly Progressive Interstitial Lung (North Tower, First Floor) Poster Discussion 2:45 pm-4:15 pm Disease Marriott Marquis San Diego Marina FAMILIAL INTERSTITIAL PNEUMONIA AND OTHER GENETIC ILD Sunday, 116 9:15 am-11:15 am; RTEL1 Mutations Are Associated with Heterogeneous Pulmonary A23: ILD: DIAGNOSIS Room 5 A-B (Upper Level) May 20, 2018 Poster Viewing 9:15 am-9:45 am and Extra-Pulmonary Phenotypes San Diego Convention Center Poster Discussion 9:45 am-11:15 pm P1135 9:15 am-4:15 pm; Surfactant Protein C Deficiency and Rheumatoid Arthritis Interstitial A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Lung Disease in Pregnancy — A Fatal Combination San Diego Convention Center P1302 9:15 am-4:15 pm; The MUC5B Promoter Variant Is an Independent Risk Factor of A43: ILD SCIENTIFIC ABSTRACTS: GENERAL Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Idiopathic Interstitial Pneumonitis (IIP) in Families with Multiple San Diego Convention Center Cases of IIP P656 9:15 am-4:15 pm; Understanding the Cellular Dysfunction Caused by Pathogenic A68: MOLECULAR DETERMINANTS OF REMODELING IN Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Surfactant Protein C Mutant I73T LUNG FIBROSIS San Diego Convention Center P806 9:15 am-4:15 pm; Assessing Pulmonary Fibrosis Progression in a Model of Surfactant A73: DIFFUSE PARENCHYMAL LUNG DISEASE: NOVEL Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Protein C Mutation with Ultra-Short Echo-Time Magnetic Resonance MECHANISMS, BIOMARKERS, AND THERAPEUTICS San Diego Convention Center Imaging P772 9:15 am-4:15 pm; Re-Organization Of Air Spaces In The Surfactant Protein C Aging A73: DIFFUSE PARENCHYMAL LUNG DISEASE: NOVEL Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Lung And Lipid Homeostasis MECHANISMS, BIOMARKERS, AND THERAPEUTICS San Diego Convention Center 224 2:15 pm-4:15 pm; Clinical Features and Outcomes Associated with Telomere Pathway A103: ILD: OUTCOMES Room 6 D (Upper Level) Poster Viewing 2:15 pm-2:45 pm Mutations in Familial Interstitial Pneumonia San Diego Convention Center Poster Discussion 2:45 pm-4:15 pm Monday, 922 2:15 pm-4:15 pm; Expression Of An Interstitial Lung Disease Associated Surfactant B107: MECHANISTIC ADVANCES IN PULMONARY Pacific Ballroom 15-17 (North Tower, May 21, 2018 Poster Viewing 2:15 pm-2:45 pm Protein C SFTPC) Mutation Produces Dynamic Alterations In The FIBROSIS First Floor) Poster Discussion 2:45 pm-4:15 pm Alveolar Type 2 Epithelial Cell Transcriptome And A Fibrotic Lung Marriott Marquis San Diego Marina Phenotype In Mice Tuesday, P1055 9:15 am-4:15 pm; Computed Tomography Images and Electron Microscopy: Clues for C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 111:15 am-1:00 pm an ABCA-3 Deficiency Case Report in Colombia DISEASE San Diego Convention Center P1087 9:15 am-4:15 pm; At the Opposite End of the Spectrum: Filamin A-Associated C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Interstitial Lung Disease DISEASE San Diego Convention Center

17 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P1086 9:15 am-4:15 pm; A Novel Mutation in the SFPTC Gene in a Newborn with Persistent C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Tachypnea DISEASE San Diego Convention Center P1088 9:15 am-4:15 pm; Heterozygous Surfactant Protein B Disease Leading to Respiratory C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Failure DISEASE San Diego Convention Center P1098 9:15 am-4:15 pm; Desquamative Interstitial Pneumonia in a Child: A Case Report C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm DISEASE San Diego Convention Center P1097 9:15 am-4:15 pm; ABCA3 Mutation Associated with Interstitial Lung Disease in a C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Newborn: Case Report DISEASE San Diego Convention Center Wednesday, 212 9:15 am-11:15 am; Multiplexed Direct Genomic Selection to Identify Non-coding and D25: ADVANCES IN RARE LUNG AND PULMONARY Room 6 D (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am Copy Number Variation in ABCA3 among Neonates with Respiratory VASCULAR DISEASE IN CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am Failure and Children with Interstitial lung Disease (chILD) with Monoallelic ABCA3 Variants 218 9:15 am-11:15 am; Abnormal Surfactant Protein Expression and Activation of Anti- D25: ADVANCES IN RARE LUNG AND PULMONARY Room 6 D (Upper Level) Poster Viewing 9:15 am-9:45 am Apoptotic Pathways in Severe Interstitial Lung Disease (ILD) in VASCULAR DISEASE IN CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am Rubinstein-Taybi Syndrome (RTS) P911 9:15 am-4:15 pm; Fibrosing Mediastinitis Due to Histoplasma: A Rare but Potentially D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Treatable Entity San Diego Convention Center P769 9:15 am-4:15 pm; Myhre Syndrome in Montana, A Case Report D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P458 9:15 am-4:15 pm; Silicosis-Associated Fibrosing Mediastinitis a Rare Cause of D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pulmonary Hypertension VASCULAR MEDICINE II San Diego Convention Center P450 9:15 am-4:15 pm; Is Venous Thromboembolism a Risk Factor for Pulmonary D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Hypertension in Fibrosing Mediastinitis? VASCULAR MEDICINE II San Diego Convention Center 207 1:30 pm-3:30 pm; Multidisciplinary Team Dedicated to Suspected Heritable Pulmonary D103: TRANSPLANT AND ILD POTPOURRI Room 6 D (Upper Level) Poster Viewing 1:30 pm-2:00 pm Fibrosis One Year Experience. San Diego Convention Center Poster Discussion 2:00 pm-3:30 pm FOLLICULAR BRONCHIOLITIS Wednesday, P890 9:15 am-4:15 pm; Follicular Bronchiolitis Mimicking Mycobacterial Infection: Case D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Report San Diego Convention Center

18 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P891 9:15 am-4:15 pm; Follicular Bronchiolitis Associated with Behcet's Disease D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center GLYCOGEN STORAGE AND METABOLIC DISORDERS Sunday, P1132 9:15 am-4:15 pm; Niemann-Pick Disease Presenting as Familial Interstitial Lung A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Disease: Report of 2 Adult Siblings San Diego Convention Center Tuesday, P801 9:15 am-4:15 pm; When the Phrenic Nerve Fails You C54: CRITICAL CARE CASE REPORTS: CAUSES AND Area G (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm COMPLICATIONS OF ACUTE RESPIRATORY FAILURE San Diego Convention Center HEMOGLOBINOPATHY Sunday, P1431 9:15 am-4:15 pm; Low Oxygen Affinity Hemoglobinopathy: A Rare Sixth Cause of A48: DYSPNEA: CASE REPORTS I Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Hypoxemia San Diego Convention Center HEPATOPULMONARY SYNDROME Monday, P1013 9:15 am-4:15 pm; A Rare Case of Idiopathic Noncirrhotic Portal Hypertension Causing B58: WHO'S BAD: CASE REPORTS IN PULMONARY Area J (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Hepatopulmonary Syndrome VASCULAR MEDICINE I San Diego Convention Center Tuesday, P627 9:15 am-4:15 pm; Epoprostenol for Worsening Hypoxemia of Hepatopulmonary C50: CRITICAL CARE CASE REPORTS: THE LIVER, Area G (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Syndrome After Lung Transplantation PANCREAS, AND INTESTINES San Diego Convention Center Wednesday, P779 9:15 am-4:15 pm; Pentoxifylline Reduces Intrapulmonary Shunt in a Patient with D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Hepatopulmonary Syndrome San Diego Convention Center P791 9:15 am-4:15 pm; Hepatopulmonary Syndrome Masquerading as Interstitial Lung D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Disease San Diego Convention Center HEREDITARY HEMORRHAGIC TELANGIECTASIS Wednesday, P634 9:15 am-4:15 pm; Long-Term Management of HHT-Related PAVM: Lessons Learned on D31: INTERVENTIONAL PULMONARY: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm the Need for More HHT Centres of Excellence San Diego Convention Center P440 9:15 am-4:15 pm; Hereditary Hemorrhagic Telangiectasia and a Recurrent Brain D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Abscess VASCULAR MEDICINE II San Diego Convention Center HERMANSKY-PUDLAK SYNDROME Sunday, P1296 9:15 am-4:15 pm; Platelet Delta Granule Evaluation in Lung Transplant Recipients with A43: ILD SCIENTIFIC ABSTRACTS: GENERAL Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm HPS-1 to Study Platelet Biogenesis San Diego Convention Center

19 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P280 9:15 am-4:15 pm; Galectin-3 Interacts with CHI3L1 Axis and Contributes to C72: PULMONARY FIBROSIS: MECHANISMS AND Area D (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Hermansky-Pudlak Syndrome Lung Disease MODELS San Diego Convention Center P284 9:15 am-4:15 pm; The Endocannabinoid/CB₁R System is Overactive in C72: PULMONARY FIBROSIS: MECHANISMS AND Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Bleomycin-induced Pulmonary Fibrosis in Pale Ear (HPS1) mice MODELS San Diego Convention Center P302 9:15 am-4:15 pm; Circulating Fibrocytes Predict Biomarkers Of Immune Dysregulation C72: PULMONARY FIBROSIS: MECHANISMS AND Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm And Fibrogenesis In A Genetic Interstitial Lung Disease MODELS San Diego Convention Center Wednesday, P888 9:15 am-4:15 pm; An Unusual Cause of Pulmonary Fibrosis D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center HYPERSENSITIVITY PNEUMONITIS Sunday, 907 9:15 am-11:15 am; Evidence for an Organizing Adaptive Immune Response in Explant A21: CLINICAL AND MECHANISTIC STUDIES OF LUNG Pacific Ballroom 15-17 (North Tower, May 20, 2018 Poster Viewing 9:15 am-9:45 am Lungs with Chronic Hypersensitivity Pneumonitis FIBROSIS First Floor) Poster Discussion 9:45 am-11:15 am Marriott Marquis San Diego Marina 113 9:15 am-11:15 am; Chronic Hypersensitivity Pneumonitis: A Prospective Cohort Analysis A23: ILD: DIAGNOSIS Room 5 A-B (Upper Level) Poster Viewing 9:15 am-9:45 am of an Under-Recognized Clinical Entity San Diego Convention Center Poster Discussion 9:45 am-11:15 am P1143 9:15 am-4:15 pm; Hypersensitivity Pneumonitis and Sarcoidosis A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P29 9:15 am-4:15 pm; Pet Groomers Survey Responses A54: INDOOR AND OUTDOOR AIR POLLUTION Area A (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Monday, P651 9:15 am-4:15 pm; Clinical Relevance Of Antinuclear Antibodies (ANA) In Patients With B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Hypersensitivity Pneumonitis (HP): A Single Centre Experience. San Diego Convention Center Tuesday, P1093 9:15 am-4:15 pm; The Little Farmer’s Lung: Hypersensitivity Pneumonitis Due to C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Multiple Fungal Triggers in a 6-Year-Old DISEASE San Diego Convention Center P1085 9:15 am-4:15 pm; The Moldy Birds: An Adolescent with Progressive Dyspnea C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm DISEASE San Diego Convention Center Wednesday, P851 9:15 am-4:15 pm; A Complex Case of Interstitial Lung Disease Related to D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Nontuberculous Mycobacteria and Hot Tub Exposure San Diego Convention Center P1096 9:15 am-4:15 pm; Fibrotic Hypersensitivity Pneumonitis Induced by Oxaliplatin: A D35: DRUG INDUCED LUNG DISEASE: CASE REPORTS Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Unexpected but Serious Side Effect in Treating Colorectal Cancer San Diego Convention Center

20 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P1290 9:15 am-4:15 pm; A Case of Ziprasidone-Induced Hypersensitivity Pneumonitis: A D46: CRITICAL CARE CASE REPORTS: TOXICOLOGY AND Area K (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Previously Unreported Side Effect of an Atypical Antipsychotic POISONINGS San Diego Convention Center IDIOPATHIC PULMONARY HEMOSIDEROSIS Wednesday, 211 9:15 am-11:15 am; A Recurrent Hemizygous Deletion at the MHC Region Impacting D25: ADVANCES IN RARE LUNG AND PULMONARY Room 6 D (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am MICA, LINC01149, HCP5, HCG26 Associates with Idiopathic VASCULAR DISEASE IN CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am Pulmonary Hemosiderosis IGG4-RELATED DISEASE Sunday, P1347 9:15 am-4:15 pm; Lung Involvement in Immunoglobulin G4 Related Disease A39: SARCOIDOSIS AND RARE LUNG DISEASE SCIENTIFIC Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm ABSTRACTS San Diego Convention Center Monday, P628 9:15 am-4:15 pm; IgG4 Related Lung Disease Found in a Patient with a Pancreatic B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Mass San Diego Convention Center P632 9:15 am-4:15 pm; Revealing the Mystery of a Previously Diagnosed Inflammatory B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pseudotumor of the Lung San Diego Convention Center P652 9:15 am-4:15 pm; Evaluation of Lung Lesions in LATY136F Mutant Mice B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P659 9:15 am-4:15 pm; A New Foe: IgG4-Related Disease Presenting as Isolated Pulmonary B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Nodules San Diego Convention Center P666 9:15 am-4:15 pm; Dual Manifestations of Immunoglobulin G4 Related Disease in B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Thorax San Diego Convention Center P673 9:15 am-4:15 pm; Unusual Presentation of IgG4 Related Disease B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center INTERSTITIAL LUNG DISEASES — CHILDHOOD OTHER Monday, 2:15 pm-4:15 pm; The National Registry for Childhood Interstitial and Diffuse Lung B97: IMPORTANCE OF LONGITUDINAL COHORT STUDIES Room 6 C/F (Upper Level) May 21, 2018 Oral Presentation 2:45 pm-3:00 pm Diseases: An Initial Report from the ChILD Research Network IN PEDIATRICS San Diego Convention Center Tuesday, P1052 9:15 am-4:15 pm; Recurrent Life Threatening Pneumothorax Associated with Diffuse C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Subpleural Cystic Lung Disease in a Trisomy 21 Infant with DISEASE San Diego Convention Center Congenital Heart Disease: A Unique Case Report! P1094 9:15 am-4:15 pm; Diagnosis and Treatment of Cryptogenic Organizing Pneumonia in a C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Child on Extracorporeal Membrane Oxygenation Support DISEASE San Diego Convention Center

21 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P1083 9:15 am-4:15 pm; Combined Heterozygous TBX4 Loss and Single ABCA3 Mutation in C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm the Pathogenesis of Childhood Interstitial Lung Disease DISEASE San Diego Convention Center P1104 9:15 am-4:15 pm; Tracheostomy Bleeding Unfolding into an Unusual Etiology C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm DISEASE San Diego Convention Center Wednesday, 214 9:15 am-11:15 am; Assessment of Late Pulmonary Outcomes and Exercise Capacity D25: ADVANCES IN RARE LUNG AND PULMONARY Room 6 D (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am among Pediatric Survivors of High-Risk Neuroblastoma VASCULAR DISEASE IN CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am 208 9:15 am-11:15 am; Childhood Interstitial Lung Disease in a Large Tertiary Care Center: D25: ADVANCES IN RARE LUNG AND PULMONARY Room 6 D (Upper Level) Poster Viewing 9:15 am-9:45 am Implications of a Family Needs Assessment Survey VASCULAR DISEASE IN CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am LIGHT CHAIN DEPOSITION DISEASE Sunday, P1176 9:15 am-4:15 pm; Pulmonary Only Light Chain Deposition Disease in a Young Healthy A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Male San Diego Convention Center P869 9:15 am-4:15 pm; Light-Chain Deposition Disease: A Rare Cause of Cystic Lung D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Disease San Diego Convention Center P919 9:15 am-4:15 pm; Cystic Lung Disease Due to Primary Light Chain Deposition D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center LIPOID PNEUMONIA Sunday, P1434 9:15 am-4:15 pm; Progressive Chronic Hypoxemia After Chronic Constipation: A Case A48: DYSPNEA: CASE REPORTS I Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Report San Diego Convention Center P789 9:15 am-4:15 pm; A Case of Lipoid Pneumonia with Exogenous Source A73: DIFFUSE PARENCHYMAL LUNG DISEASE: NOVEL Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm MECHANISMS, BIOMARKERS, AND THERAPEUTICS San Diego Convention Center Wednesday, P1048 9:15 am-4:15 pm; A Case of Exogenous Lipoid Pneumonia Caused by Sesame Oil D34: LUNG TRANSPLANT AND DRUG INDUCED LUNG Area J (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Pulling Successfully Treated with Whole Lung Lavage DISEASE: CASE REPORTS San Diego Convention Center P1099 9:15 am-4:15 pm; Lipoid Pneumonia, An Unexpected Diagnosis in a Healthy Middle- D35: DRUG INDUCED LUNG DISEASE: CASE REPORTS Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Aged Patient San Diego Convention Center LYMPHANGIOLEIOMYOMATOSIS Sunday, 922 9:15 am-11:15 am; Identification of Novel Biomarkers for Lymphangioleiomyomatosis A21: CLINICAL AND MECHANISTIC STUDIES OF LUNG Pacific Ballroom 15-17 (North Tower, May 20, 2018 Poster Viewing 9:15 am-9:45 am by Proteomics from Serum Exosomes FIBROSIS First Floor) Poster Discussion 9:45 am-11:15 am Marriott Marquis San Diego Marina 22 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, 925 9:15 am-11:15 am; Pseudoneutropenia in Lymphangioleiomyomatosis Patients A21: CLINICAL AND MECHANISTIC STUDIES OF LUNG Pacific Ballroom 15-17 (North Tower, May 20, 2018 Poster Viewing 9:15 am-9:45 am Receiving Sirolimus FIBROSIS First Floor) Poster Discussion 9:45 am-11:15 am Marriott Marquis San Diego Marina 109 9:15 am-11:15 am; Serum Levels of VEGF-C Are Elevated in Sporadic but Not Tuberous A23: ILD: DIAGNOSIS Room 5 A-B (Upper Level) Poster Viewing 9:15 am-9:45 am Sclerosis Associated-LAM, Correlate with the Need for Supplemen- San Diego Convention Center Poster Discussion 9:45 am-11:15 am tal Oxygen, and Impact Lung Function Response to Sirolimus P1342 9:15 am-4:15 pm; Clinical Characteristics in Lymphangioleiomyomatosis-Related A39: SARCOIDOSIS AND RARE LUNG DISEASE SCIENTIFIC Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pulmonary Hypertension: An Observational Study ABSTRACTS San Diego Convention Center P1298 9:15 am-4:15 pm; A Rare Combination of Lymphangioleiomyomatosis with A43: ILD SCIENTIFIC ABSTRACTS: GENERAL Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Hypersensitivity Pneumonia San Diego Convention Center P790 9:15 am-4:15 pm; Does Chest Computed Tomography Body Positioning Change the A73: DIFFUSE PARENCHYMAL LUNG DISEASE: NOVEL Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Cyst Score for Lymphangioleiomyomatosis (LAM)? MECHANISMS, BIOMARKERS, AND THERAPEUTICS San Diego Convention Center P794 9:15 am-4:15 pm; Effect of Model-Based Iterative Reconstruction in Chest Computed A73: DIFFUSE PARENCHYMAL LUNG DISEASE: NOVEL Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Tomography on Lymphangioleiomyomatosis (LAM) Cyst Score MECHANISMS, BIOMARKERS, AND THERAPEUTICS San Diego Convention Center Quantification P800 9:15 am-4:15 pm; Correlations between Lung Parenchymal Changes on Computed A73: DIFFUSE PARENCHYMAL LUNG DISEASE: NOVEL Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Tomographic Imaging and both Disease Progression and Response MECHANISMS, BIOMARKERS, AND THERAPEUTICS San Diego Convention Center to Sirolimus Therapy in Lymphangioleiomyomatosis 2:15 pm-4:15 pm; Single Cell RNAseq of Lymphangioleiomyomatosis (LAM) Lungs A96: THE STEM AND PROGENITOR CELL NICHES AS Grand Ballroom 5-6 Oral Presentation 2:15 pm-2:30 pm Reveals Unique Populations Consistent with LAM Cells and THERAPEUTIC TARGETS (North Tower, Lobby Level) Lymphatic Endothelial Cells Marriott Marquis San Diego Marina 905 2:15 pm-4:15 pm; Potential Serum Biomarkers in Lymphangioleiomyomatosis A109: NOVEL EXPERIMENTAL MODELS AND Pacific Ballroom 15-17 Poster Viewing 2:15 pm-2:45 pm APPROACHES IN LUNG BIOLOGY (North Tower, First Floor) Poster Discussion 2:45 pm-4:15 pm Marriott Marquis San Diego Marina Monday, 906 9:15 am-11:15 am; Lymphangioleiomyomatosis-Derived Smooth Muscle Cells B28: CELL AND MATRIX MICROENVIRONMENTS Pacific Ballroom 15-17 May 21, 2018 Poster Viewing 9:15 am-9:45 am (LAM-SMCs) Destabilize Endothelial Cell (EC) Networks While ECs MODULATE LUNG DISEASE (North Tower, First Floor) Poster Discussion 9:45 am-11:15 am Promote Growth of LAM-SMCs Marriott Marquis San Diego Marina 204 2:15 pm-4:15 pm; Lung Function Response And Changes Of Lung Cysts To B103: ILD: MANAGEMENT Room 6 D (Upper Level) Poster Viewing 2:15 pm-2:45 pm Rapamycin For Lymphangioleiomyomatosis: Long-term Follow-up San Diego Convention Center Poster Discussion 2:45 pm-4:15 pm Observational Study

23 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P148 9:15 am-4:15 pm; Hospitalization Patterns in Patients with Lymphangioleiomyomatosis C41: HEALTH SERVICES RESEARCH IN PULMONARY Area B (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm (LAM) in the United States DISEASE San Diego Convention Center 2:15 pm-4:15 pm; Quantification Of Cyst Ventilation Using Hyperpolarized C97: DIFFUSE PARENCHYMAL LUNG DISEASES: Grand Ballroom 5-6 Oral Presentation 2:45 pm-3:00 pm 129Xe MRI Correlates With Pulmonary Function Tests In EVALUATION, OUTCOMES, AND TRIALS (North Tower, Lobby Level) Patients With Lymphangioleiomyomatosis. Marriott Marquis San Diego Marina Wednesday, 9:15 am-11:15 am; The NHLBI Lymphangioleiomyomatosis Registry: Prognostic D14: ILD: CLINICAL RESEARCH Room 3 (Upper Level) May 23, 2018 Oral Presentation 10:00 am-10:15 am Radiologic and Physiologic Biomarkers Emerge from a 15-Year San Diego Convention Center Prospective Longitudinal Analysis P885 9:15 am-4:15 pm; Lymphangioleiomyomatosis (LAM) of the Uterus: Risk of Pulmonary D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm LAM? San Diego Convention Center P873 9:15 am-4:15 pm; A Rare Case of Cocaine User with Sporadic D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Lymphangioleiomyomatosis San Diego Convention Center P924 9:15 am-4:15 pm; Pneumothorax in a Woman with Tuberous Sclerosis — the Trigger D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm to Diagnosis of Lymphangioleiomyomatosis San Diego Convention Center P901 9:15 am-4:15 pm; Pulmonary Lymphangioleiomyomatosis: A Prime of Life Misfortune D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P289 9:15 am-4:15 pm; Genetic Features Of Metastatic Tsc2-null Cells: Relevance To D52: DECONSTRUCTING TUMORS AND MALIGNANCIES Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pulmonary LAM San Diego Convention Center P285 9:15 am-4:15 pm; IGF2 As A Potential Novel Therapeutic Target For Rapamycin- D52: DECONSTRUCTING TUMORS AND MALIGNANCIES Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm insensitive LAM Patients San Diego Convention Center P288 9:15 am-4:15 pm; Translationally Controlled Tumour Protein: A Novel Therapeutic D52: DECONSTRUCTING TUMORS AND MALIGNANCIES Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Target for Lymphangioleiomyomatosis? San Diego Convention Center P283 9:15 am-4:15 pm; PD-L1 As a Notential Therapeutic Target For Patients With Advanced D52: DECONSTRUCTING TUMORS AND MALIGNANCIES Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm or Refractory-to-Rapamycin Pulmonary lymphangioleiomyomatosis San Diego Convention Center (LAM) P284 9:15 am-4:15 pm; Targeted Serum Proteomic Analysis Identifies Novel Biomarkers in D52: DECONSTRUCTING TUMORS AND MALIGNANCIES Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm LAM San Diego Convention Center P290 9:15 am-4:15 pm; Tuberous Sclerosis and Lymphangioleiomyomatosis are D52: DECONSTRUCTING TUMORS AND MALIGNANCIES Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Neurocristopathies San Diego Convention Center

24 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location LYMPHATIC ANOMALIES: GENERALIZED LYMPHATIC ANOMALY (GLA), GORHAM-STOUT DISEASE (GSD) Sunday, P801 9:15 am-4:15 pm; Assessment of Alveolar-Airspace Dimensions in a Case of Pediatric A73: DIFFUSE PARENCHYMAL LUNG DISEASE: NOVEL Area G (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Generalized Lymphatic Anomaly MECHANISMS, BIOMARKERS, AND THERAPEUTICS San Diego Convention Center Tuesday, P1047 9:15 am-4:15 pm; Chylous Effusion in an Infant: Presenting Symptom of C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Lymphangiomatosis DISEASE San Diego Convention Center Wednesday, P915 9:15 am-4:15 pm; Lymphangiomatosis D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P757 9:15 am-4:15 pm; Plastic Bronchitis: A Tale of Lymphatic Anomalies D38: COUGH: CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P781 9:15 am-4:15 pm; Vanishing Bone Disease D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center LYMPHOVENOUS MALFORMATION Tuesday, P1053 9:15 am-4:15 pm; A Curious Bronchoscopic Finding in a Patient with Tracheal C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Submucosal Lymphovenous Malformation DISEASE San Diego Convention Center MARFAN’S SYNDROME Monday, P1123 9:15 am-4:15 pm; Sildenafil Ameliorates Airspace Widening And Early Pulmonary B66: WHAT'S NEW IN VASCULAR AND PLEURAL DISEASE Area J (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Artery Dilation In The Mouse Model Of Marfan Syndrome San Diego Convention Center Wednesday, P751 9:15 am-4:15 pm; Massive Hemoptysis in a Patient with Marfan’s Syndrome D38: COUGH: CASE REPORTS Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center MOUNIER-KUHN SYNDROME Sunday, P226 9:15 am-4:15 pm; Mounier-Kuhn Syndrome Complicated by Mycobacterium A56: NON-TUBERCULOUS MYCOBACTERIA: CASE Area C (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Abscessus Infection in an Active Duty Solider REPORTS San Diego Convention Center Wednesday, P726 9:15 am-4:15 pm; Tracheobroncomegaly "Mounier-Kuhn Syndrome" D37: CF AND NON-CF BRONCHIECTASIS AND IMMUNE Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm DEFICIENCIES: CASE REPORTS San Diego Convention Center P727 9:15 am-4:15 pm; A Large Airway Problem: A Case of an Elderly Female with D37: CF AND NON-CF BRONCHIECTASIS AND IMMUNE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Mounier-Kuhn Syndrome DEFICIENCIES: CASE REPORTS San Diego Convention Center P773 9:15 am-4:15 pm; Mounier Kuhn Syndrome; a Magnified Incidental Finding D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center

25 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location NEUROENDOCRINE CELL HYPERPLASIA OF INFANCY Wednesday, 210 9:15 am-11:15 am; Lung Shape From Chest Computed Tomography Scan Predicts D25: ADVANCES IN RARE LUNG AND PULMONARY Room 6 D (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am Diagnosis of Neuroendocrine Cell Hyperplasia of Infancy VASCULAR DISEASE IN CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am NEUROFIBROMATOSIS Monday, P332 9:15 am-4:15 pm; Neurofibromatosis 1 Presenting with a Large Mediastinal Mass B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P367 9:15 am-4:15 pm; A New Diagnosis of Neurofibromatosis Type 1 in a Young Adult Male B73: CASE REPORTS IN THORACIC ONCOLOGY V Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Presenting with Palpitations and Posterior Mediastinal Mass San Diego Convention Center NON-CF BRONCHIECTASIS Monday, 221 9:15 am-11:15 am; Characteristics of Alaska Native Children with Chronic Suppurative B25: CHRONIC SUPPERATIVE LUNG DISEASE IN Room 6 D (Upper Level) May 21, 2018 Poster Viewing 9:15 am-9:45 am Lung Disease: A Prospective 10-year Study CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am Wednesday, 617 9:15 am-11:15 am; Effect of Inhaled Liposomal Ciprofloxacin on Severe Pulmonary D23: ADULT CF AND NON-CF BRONCHIECTASIS Room 30 C-E (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am Exacerbations in Patients with Bronchiectasis and Chronic San Diego Convention Center Poster Discussion 9:45 am-11:15 am Pseudomonas aeruginosa Lung Infections 618 9:15 am-11:15 am; Safety and Tolerability of ARD-3150, Inhaled Liposomal D23: ADULT CF AND NON-CF BRONCHIECTASIS Room 30 C-E (Upper Level) Poster Viewing 9:15 am-9:45 am Ciprofloxacin, in Patients with Bronchiectasis and Chronic San Diego Convention Center Poster Discussion 9:45 am-11:15 am Pseudomonas aeruginosa Infection: Results from two Phase 3 trials NON-LANGERHANS HISTIOCYTOSES Monday, P767 9:15 am-4:15 pm; Interesting Case of Mediastinal Adenopathy B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1178 9:15 am-4:15 pm; Bilateral Pulmonary Nodules and Intravascular Pulmonary B46: CRITICAL CARE CASE REPORTS: HEMATOLOGY, Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Histiocytosis: A Rare Presentation of Hemophagocytic ONCOLOGY, RHEUMATOLOGY, AND IMMUNOLOGY San Diego Convention Center Lymphohistiocytosis Secondary to Epstein-Barr Virus Infection Wednesday, P453 9:15 am-4:15 pm; So It’s Not a Pulmonary Embolism? A Rare Case of Cardiac Rosai- D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Dorfman Disease VASCULAR MEDICINE II San Diego Convention Center NON-TUBERCULOUS MYCOBACTERIAL INFECTION — PULMONARY Sunday, P239 9:15 am-4:15 pm; In Vitro Determination of Inhaled NO Regimen for Treatment of A58: NON-TUBERCULOUS MYCOBACTERIA: OFF THE Area C (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Pulmonary Non-Tuberculous Mycobacteria Infection BEATEN TRACK San Diego Convention Center 26 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P241 9:15 am-4:15 pm; Patient-Reported Health Status Measured by St. George’s A58: NON-TUBERCULOUS MYCOBACTERIA: OFF THE Area C (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Respiratory Questionnaire Improved with Sputum Culture BEATEN TRACK San Diego Convention Center Conversion in Patients with Nontuberculous Mycobacterial (NTM) Lung Disease Caused by Mycobacterium Avium Complex (MAC) ORGANIZING PNEUMONIA Sunday, P1150 9:15 am-4:15 pm; Acute Fibrinous and Organizing Pneumonia After Allogeneic Stem A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Cell Transplant San Diego Convention Center P1155 9:15 am-4:15 pm; A Rare Radiographic Presentation of Cryptogenic Organizing A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pneumonia: A Diffuse Micronodular Pattern Mimicking Miliary Lung San Diego Convention Center Infiltration P1173 9:15 am-4:15 pm; Frankincense for Organizing Pneumonia: A Steroid-Sparing Gift? A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1174 9:15 am-4:15 pm; Recurrent Acute Fibrinous and Organizing Pneumonia in a 40-Year- A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Old Woman San Diego Convention Center Monday, P676 9:15 am-4:15 pm; A Case of Acute Interstitial Pneumonia with Autoimmune Features B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Presenting as Granulomatous Organizing Pneumonia San Diego Convention Center P692 9:15 am-4:15 pm; An Atypical Presentation of Cryptogenic Organizing Pneumonia B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P727 9:15 am-4:15 pm; Cocaine Associated Organizing Pneumonia: A Fatal Low to Getting B35: LUNG TRANSPLANT AND ILD SCIENTIFIC Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm High ABSTRACTS: DRUG INDUCED LUNG DISEASE, San Diego Convention Center AUTOIMMUNE LUNG DISEASE P400 9:15 am-4:15 pm; Cryptogenic Organizing Pneumonia as a Precursor of Primary B74: CASE REPORTS IN THORACIC ONCOLOGY VI Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Hodgkin's Disease: An Unreported Entity San Diego Convention Center Wednesday, P746 9:15 am-4:15 pm; Not so “Cryptogenic”: A Case of Organizing Pneumonia (OP) D37: CF AND NON-CF BRONCHIECTASIS AND IMMUNE Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Associated with Common Variable Immunodeficiency (CVID) DEFICIENCIES: CASE REPORTS San Diego Convention Center P882 9:15 am-4:15 pm; Focal Organizing Pneumonia in a Severe Hemophiliac: A Diagnostic D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Dilemma San Diego Convention Center P925 9:15 am-4:15 pm; Fatal Acute on Chronic Respiratory Failure Due to Cryptogenic D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Organizing Pneumonia in the Setting of Systemic Lupus San Diego Convention Center Erythematosus

27 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P939 9:15 am-4:15 pm; Cryptogenic Organizing Pneumonia After Allogeneic Hematopoietic D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Stem Cell Transplant, Difficult to Diagnose, Easy to Treat San Diego Convention Center P1021 9:15 am-4:15 pm; A Rare Case of Cocaine-Induced Organizing Pneumonia D34: LUNG TRANSPLANT AND DRUG INDUCED LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm DISEASE: CASE REPORTS San Diego Convention Center P1063 9:15 am-4:15 pm; Acute Fibrinous and Organizing Pneumonia (AFOP) Associated with D35: DRUG INDUCED LUNG DISEASE: CASE REPORTS Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Chemotherapy Drug Reaction: A Case Report San Diego Convention Center P1100 9:15 am-4:15 pm; Bortezomib Induced Organizing Pneumonia in a Patient with D35: DRUG INDUCED LUNG DISEASE: CASE REPORTS Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Underlying Interstitial Lung Disease: The (Im)Perfect Setup San Diego Convention Center OSSIFICATION AND CALCIFICATION — PULMONARY Sunday, P1157 9:15 am-4:15 pm; Pulmonary Alveolar Microlithiasis with Satisfactory Diagnosis by A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Bone Scintigraphy of the Lung San Diego Convention Center 914 2:15 pm-4:15 pm; Osteogenesis and Osteolysis in Pulmonary Alveolar Microlithiasis A109: NOVEL EXPERIMENTAL MODELS AND Pacific Ballroom 15-17 (North Tower, Poster Viewing 2:15 pm-2:45 pm APPROACHES IN LUNG BIOLOGY First Floor) Poster Discussion 2:45 pm-4:15 pm Marriott Marquis San Diego Marina 917 2:15 pm-4:15 pm; Mechanisms of Microlith Clearance Induced by Dietary Phosphate A109: NOVEL EXPERIMENTAL MODELS AND Pacific Ballroom 15-17 (North Tower, Poster Viewing 2:15 pm-2:45 pm Restriction in Pulmonary Alveolar Microlithiasis APPROACHES IN LUNG BIOLOGY First Floor) Poster Discussion 2:45 pm-4:15 pm Marriott Marquis San Diego Marina Monday, P764 9:15 am-4:15 pm; Pulmonary Ossification: Not a Bone of Contention B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Tuesday, P905 9:15 am-4:15 pm; EGTA Therapeutic Lung Lavage For Pulmonary Alveolar C43: TOPICS IN IN INTERVENTIONAL PULMONARY AND Area H (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Microlithiasis PLEURAL DISEASES San Diego Convention Center P705 9:15 am-4:15 pm; Ivory Lungs: A Rare Case of Pulmonary Alveolar Microlithiasis C52: CRITICAL CARE CASE REPORTS: GOOD VIBRATIONS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Bridged to Transplant by AV ECMO — MECHANICAL VENTILATION FROM NIV TO ECMO San Diego Convention Center P1089 9:15 am-4:15 pm; Pulmonary Alveolar Microlithiasis: A Case of an Early Presentation C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm DISEASE San Diego Convention Center Wednesday, P1010 9:15 am-4:15 pm; Primary Pulmonary Calciphylaxis Found Six-Months After D34: LUNG TRANSPLANT AND DRUG INDUCED LUNG Area J (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Simultaneous Liver-Kidney Transplantation DISEASE: CASE REPORTS San Diego Convention Center

28 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location PLACENTAL TRANSMOGRIFICATION Sunday, P1158 9:15 am-4:15 pm; Placental Transmogrification of the Lung in a Patient with Anti- A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Synthetase Syndrome San Diego Convention Center Tuesday, P1091 9:15 am-4:15 pm; Giant Cystic Lesions with a Rare Pulmonary Diagnosis C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm DISEASE San Diego Convention Center PLASTIC BRONCHITIS Sunday, P1418 9:15 am-4:15 pm; Rare Case of Idiopathic Plastic Bronchitis in Adult A48: DYSPNEA: CASE REPORTS I Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Monday, P774 9:15 am-4:15 pm; Idiopathic Plastic Bronchitis: A Rare Presentation B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P773 9:15 am-4:15 pm; A Case of Plastic Bronchitis B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Tuesday, P850 9:15 am-4:15 pm; Plastic Bronchitis in an Adult Lung Transplant Patient with C32: LUNG TRANSPLANTATION: CLINICAL STUDIES Area H (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Refractory Donor-Related Asthma San Diego Convention Center P1031 9:15 am-4:15 pm; Old Disease-New Perspectives: Plastic Bronchitis C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm BRONCHOSCOPY San Diego Convention Center Wednesday, 207 9:15 am-11:15 am; Characterizing Bronchoalveolar Lavages and Bronchial Casts in D25: ADVANCES IN RARE LUNG AND PULMONARY Room 6 D (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am Patients with Congenital Heart Disease and Plastic Bronchitis at VASCULAR DISEASE IN CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am Time of Percutaneous Lymphatic Intervention P754 9:15 am-4:15 pm; "Doctor, I Coughed Up My Lung!" D38: COUGH: CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P793 9:15 am-4:15 pm; “Casting” for a Diagnosis: A Case of Plastic Bronchitis in an Adult D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Patient Following Cardiopulmonary Bypass San Diego Convention Center PLEUROPARENCHYMAL FIBROELASTOSIS (PPFE) Sunday, P1136 9:15 am-4:15 pm; Pleuroparenchymal Fibroelastosis Following Autologous Bone A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Marrow Transplant San Diego Convention Center P1177 9:15 am-4:15 pm; What You Don’t Know Can Hurt You: A Rare Form of Pulmonary A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Fibrosis in the Setting of Chronic Cyclophosphamide San Diego Convention Center

29 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P1144 9:15 am-4:15 pm; Pleuroparenchymal Fibroelastosis a Case Report A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1222 9:15 am-4:15 pm; Usual Interstitial Pneumonia Pattern in the Lower Lung Lobes as a A41: ILD SCIENTIFIC ABSTRACTS: DIAGNOSIS, Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Prognostic Factor in Idiopathic Pleuroparenchymal Fibroelastosis OUTCOMES, AND PPFE San Diego Convention Center P1219 9:15 am-4:15 pm; Clinical Features and Prognosis of Pleuroparenchymal Fibroelastosis A41: ILD SCIENTIFIC ABSTRACTS: DIAGNOSIS, Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm in Korean OUTCOMES, AND PPFE San Diego Convention Center Wednesday, P926 9:15 am-4:15 pm; Familial Pleuroparenchymal Fibroelastosis D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1068 9:15 am-4:15 pm; Pleuroparenchymal Fibroelastosis (PPFE): A Rare Disease Entity, D35: DRUG INDUCED LUNG DISEASE: CASE REPORTS Area J (Hall A-B2, Ground Level) Poster Viewing11:15 am-1:00 pm Secondary to Methotrexate? San Diego Convention Center PRIMARY CILIARY DYSKINESIA Monday, 215 9:15 am-11:15 am; Neonatal Chest X-ray Findings in Patients with Primary Ciliary B25: CHRONIC SUPPERATIVE LUNG DISEASE IN Room 6 D (Upper Level) May 21, 2018 Poster Viewing 9:15 am-9:45 am Dyskinesia CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am 214 9:15 am-11:15 am; Where Is The NO In Primary Ciliary Dyskinesia (PCD)? Somatic Cell B25: CHRONIC SUPPERATIVE LUNG DISEASE IN Room 6 D (Upper Level) Poster Viewing 9:15 am-9:45 am Heme Oxidizes N0 in Ciliated Human Epithelial Cells Homozygous CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am For The PCD Mutation, DNAH5 216 9:15 am-11:15 am; Investigation of “Read-Through” of Nonsense Mutations as a B25: CHRONIC SUPPERATIVE LUNG DISEASE IN Room 6 D (Upper Level) Poster Viewing 9:15 am-9:45 am Treatment for Primary Ciliary Dyskinesia CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am 212 9:15 am-11:15 am; NIOX VERO® Nasal Measurement Mode Differentiates Individuals B25: CHRONIC SUPPERATIVE LUNG DISEASE IN Room 6 D (Upper Level) Poster Viewing 9:15 am-9:45 am with PCD from Healthy Individuals with Two Breathing Methods CHILDREN San Diego Convention Center Poster Discussion 9:45 am-11:15 am 2:15 pm-4:15 pm; Primary Ciliary Dyskinesia: Longitudinal Study of Lung Disease B97: IMPORTANCE OF LONGITUDINAL COHORT STUDIES Room 6 C/F (Upper Level) Oral Presentation 2:30 pm-2:45 pm Progression by Ultrastructural Defect and Genotype IN PEDIATRICS San Diego Convention Center Tuesday, 9:15 am-11:15 am; Different Mutations in Cilia Preassembly Gene HEATR2 Are C18: BEST OF PEDIATRICS Room 1 A-B (Upper Level) May 22, 2018 Oral Presentation 10:00 am-10:15 am Associated with Variable Clinical Phenotypes and Defects in San Diego Convention Center Proteostasis Wednesday, 613 9:15 am-11:15 am; The Clinical Features of Bronchiectasis Associated with Alpha-1 D23: ADULT CF AND NON-CF BRONCHIECTASIS Room 30 C-E (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am Antitrypsin Deficiency, Common Variable Immunodeficiency, and San Diego Convention Center Poster Discussion 9:45 am-11:15 am Primary Ciliary Dyskinesia 30 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, 619 9:15 am-11:15 am; Longitudinal Analysis of Pulmonary Exacerbations: Results from D23: ADULT CF AND NON-CF BRONCHIECTASIS Room 30 C-E (Upper Level) May 23, 2018 Poster Viewing 9:15 am-9:45 am ORBIT-3 and ORBIT-4 trials of ARD-3150 in Patients with Non Cystic San Diego Convention Center Poster Discussion 9:45 am-11:15 am Fibrosis Bronchiectasis and Chronic Infection with Pseudomonas aeruginosa 1025 1:30 pm-3:30 pm; Mutations in C11ORF70 Cause Primary Ciliary Dyskinesia with D110: EPITHELIAL FUNCTION IN HEALTH AND DISEASE Pacific Ballroom 24-26 (North Tower, Poster Viewing 1:30 pm-2:00 pm Randomization of Left-Right Body Asymmetry Due to Outer and First Floor) Poster Discussion 2:00 pm-3:30 pm Inner Dynein Arm Defects Marriott Marquis San Diego Marina PULMONARY ALVEOLAR PROTEINOSIS Sunday, 102 9:15 am-11:15 am; Differential Diagnosis of Pulmonary Alveolar Proteinosis: Lung A23: ILD: DIAGNOSIS Room 5 A-B (Upper Level) May 20, 2018 Poster Viewing 9:15 am-9:45 am Biopsy or Blood Test? San Diego Convention Center Poster Discussion 9:45 am-11:15 am P1161 9:15 am-4:15 pm; Secondary Pulmonary Alveolar Proteinosis Predominant in the A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Transplanted Left Lung in Patients with Idiopathic Interstitial San Diego Convention Center Pneumonia: An Autopsy Case P777 9:15 am-4:15 pm; Pulmonary Alveolar Proteinosis: A Compositional and Biophysical A73: DIFFUSE PARENCHYMAL LUNG DISEASE: NOVEL Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Functional Analysis of its Effects on Lung Surfactant MECHANISMS, BIOMARKERS, AND THERAPEUTICS San Diego Convention Center Monday, P642 9:15 am-4:15 pm; Generation of cDNA Library Encoding GM-CSF Autoantibody B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Sequences In Autoimmune Pulmonary Alveolar Proteinosis by Next San Diego Convention Center Generation Sequencing P643 9:15 am-4:15 pm; Nocardia Survival and Virulence in Pulmonary Alveolar Proteinosis B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P728 9:15 am-4:15 pm; A Formal Toxicology Study of Inhaled rhGM-CSF in Healthy, Non- B35: LUNG TRANSPLANT AND ILD SCIENTIFIC Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Human Primates ABSTRACTS: DRUG INDUCED LUNG DISEASE, San Diego Convention Center AUTOIMMUNE LUNG DISEASE P730 9:15 am-4:15 pm; Autoimmune Pulmonary Alveolar Proteinosis: Presentation, Clinical B35: LUNG TRANSPLANT AND ILD SCIENTIFIC Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Manifestations and Current Therapeutic Approaches ABSTRACTS: DRUG INDUCED LUNG DISEASE, San Diego Convention Center AUTOIMMUNE LUNG DISEASE 209 2:15 pm-4:15 pm; The Effect of Inhaled Granulocyte-macrophage colony stimulating B103: ILD: MANAGEMENT Room 6 D (Upper Level) Poster Viewing 2:15 pm-2:45 pm factor(GM-CSF) for Patients with Mild-to-moderate Autoimmune San Diego Convention Center Poster Discussion 2:45 pm-4:15 pm Pulmonary Alveolar Proteinosis (APAP) in China

31 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, 9:15 am-11:15 am; Long-term Evaluation of Pulmonary Macrophage Transplantation C18: BEST OF PEDIATRICS Room 1 A-B (Upper Level) May 22, 2018 Oral Presentation 9:30 am-9:45 am Therapy in Csf2ra Gene-Deficient Mice, a Clinically Relevant Model San Diego Convention Center of Hereditary Pulmonary Alveolar Proteinosis 921 9:15 am-11:15 am; Induction Of Antibody Against Granulocyte/macrophage Colony C28: ROLE OF CELLULAR CROSS TALK IN LUNG Pacific Ballroom 15-17 Poster Viewing 9:15 am-9:45 am Stimulating Factor (gm-csf) Through Repeated Inhalation Of HOMEOSTASIS AND AGING (North Tower, First Floor) Poster Discussion 9:45 am-11:15 am Recombinant Human Gm-csf In No Human Primates. Marriott Marquis San Diego Marina 923 9:15 am-11:15 am; Restoration Of Gm-csf Signaling And Pulmonary Macrophage Trans- C28: ROLE OF CELLULAR CROSS TALK IN LUNG Pacific Ballroom 15-17 Poster Viewing 9:15 am-9:45 am plantation Therapy Of Hereditary Pulmonary Alveolar Proteinosis Is HOMEOSTASIS AND AGING (North Tower, First Floor) Safe, Efficacious, And Durable In Csf2ra Deficient Mice Marriott Marquis San Diego Marina P864 9:15 am-4:15 pm; Non-Familial Pulmonary Alveolar Proteinosis in a Pregnancy C35: CLINICAL STUDIES IN IMMUNODEFICIENCY Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Complicated by Stenotrophomonas Maltophilia San Diego Convention Center P899 9:15 am-4:15 pm; Pulmonary Alveolar Proteinosis Single Center Case Series C43: TOPICS IN IN INTERVENTIONAL PULMONARY AND Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Experience PLEURAL DISEASES San Diego Convention Center Wednesday, P854 9:15 am-4:15 pm; Rare Cause of Secondary Pulmonary Alveolar Proteinosis D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P863 9:15 am-4:15 pm; Relapsing Pulmonary Alveolar Proteinosis Treated with GM-CSF D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P907 9:15 am-4:15 pm; Pulmonary Alveolar Proteinosis: A Rare Disease, First-Line D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Treatment Resulting in a Near-Fatal Complication San Diego Convention Center PULMONARY ARTERY ANEURYSM Sunday, P148 9:15 am-4:15 pm; Pulmonary Artery Aneurysm: A 10 Year Community Hospital A64: LET'S GO TRIPPIN': DIAGNOSTICS AND RISK Area B (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Experience ASSESSMENT IN PULMONARY HYPERTENSION San Diego Convention Center Wednesday, P438 9:15 am-4:15 pm; Giant Pulmonary Artery Aneurysms in a Patient with Pulmonary D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Arterial Hypertension VASCULAR MEDICINE II San Diego Convention Center PULMONARY INTERSTITIAL GLYCOGENOSIS Tuesday, P1096 9:15 am-4:15 pm; Acute Respiratory Failure and Pulmonary Hemorrhage in the C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Newborn Period: An Unusual Presentation of Pulmonary Interstitial DISEASE San Diego Convention Center Glycogenosis

32 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location PULMONARY LANGERHANS CELL HISTIOCYTOSIS Sunday, P853 9:15 am-4:15 pm; Pulmonary Langerhans Cell Histiocytosis in a Patient with DRESS A31: ALLERGY AND ASTHMA CASE REPORTS Area H (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Syndrome and Acute Respiratory Failure San Diego Convention Center P1343 9:15 am-4:15 pm; Pneumothorax in Adult Pulmonary Langerhans Cell Histiocytosis A39: SARCOIDOSIS AND RARE LUNG DISEASE SCIENTIFIC Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm ABSTRACTS San Diego Convention Center P1345 9:15 am-4:15 pm; Pulmonary Langerhans Cell Histiocytosis-Cladribine Treatment A39: SARCOIDOSIS AND RARE LUNG DISEASE SCIENTIFIC Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm ABSTRACTS San Diego Convention Center P1160 9:15 am-4:15 pm; Mystery of Waxing and Waning Lung Nodules A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1165 9:15 am-4:15 pm; Late Onset Pulmonary Langerhans Cell Histiocytosis (PCLH) and A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Concurrent Diagnosis of Lung Cancer San Diego Convention Center P1171 9:15 am-4:15 pm; Pulmonary Langerhans Cell Histiocytosis in a Heavy Marijuana A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Smoker San Diego Convention Center P738 9:15 am-4:15 pm; Genetic Alterations in Adult Pulmonary Langerhans Cell Histiocytosis A71: THE EPIGENOME, GENOME AND NON-CODING RNAs Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm IN LUNG DISEASE San Diego Convention Center Monday, P86 9:15 am-4:15 pm; Upper Lobe Cystic Lung Disease Mimicking Pulmonary Langerhans B49: OCCUPATIONAL EXPOSURES Area B (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Cell Histiocytosis in a Veteran with Burn Pit Exposure San Diego Convention Center Wednesday, P874 9:15 am-4:15 pm; A Lung Cyst in a Sea of Histiocytes: Systemic Langerhans Cell D32: ILD: CASE REPORTS II Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Histiocytosis Diagnosed Via EBUS San Diego Convention Center P940 9:15 am-4:15 pm; A Common Presentation of a Rare Disease: Pulmonary Langerhans D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Cell Histiocytosis San Diego Convention Center P943 9:15 am-4:15 pm; Pulmonary Langerhans Cell Histiocytosis(PLCH): A Rare Cause of D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Chronic Cough San Diego Convention Center P286 9:15 am-4:15 pm; Molecular and Cellular Mechanisms of Pulmonary Langerhans Cell D52: DECONSTRUCTING TUMORS AND MALIGNANCIES Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Histiocytosis San Diego Convention Center PULMONARY CAPILLARY HEMANGIOMATOSIS AND PULMONARY VENO-OCCLUSIVE DISEASE (PVOD) Monday, P1036 9:15 am-4:15 pm; Hypoxemia and Ground-Glass Opacities: A Case of Pulmonary B58: WHO'S BAD: CASE REPORTS IN PULMONARY Area J (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Capillary Hemangiomatosis VASCULAR MEDICINE I San Diego Convention Center

33 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P441 9:15 am-4:15 pm; Cardiac Tamponade: As a Manifestation of Pulmonary Veno- D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Occlusive Disease (PVOD) VASCULAR MEDICINE II San Diego Convention Center P454 9:15 am-4:15 pm; Pulmonary Capillary Hemangiomatosis: A Rare Cause of Pulmonary D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Hypertension VASCULAR MEDICINE II San Diego Convention Center P432 9:15 am - 4:15 pm; Extracorporal Membrane Oxygenation, an Effective Therapy for D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) 11:15 am - 1:00 pm Pulmonary Veno-Occlusive Disease and Pulmonary Capillary VASCULAR MEDICINE II San Diego Convention Center Hemangiomatosis P451 9:15 am-4:15 pm; Pulmonary Capillary Hemangiomatosis with Clinical Improvement D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm on AntiangiogenicTreatment with Doxycycline VASCULAR MEDICINE II San Diego Convention Center PULMONARY WALDENSTRÖM MACROGLOBULINEMIA Monday, P289 9:15 am-4:15 pm; Lung Consolidation as a Manifestation of Lymphoplasmacytic B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Lymphoma with Waldenström's Macroglobulinemia San Diego Convention Center RARE CONGENITAL ANOMALIES Sunday, P1438 9:15 am-4:15 pm; A Case of Unilateral Pulmonary Artery Hypoplasia in an Adult Patient A48: DYSPNEA: CASE REPORTS I Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1426 9:15 am-4:15 pm; Practically Living with One Lung: A Rare Adult Presentation of A48: DYSPNEA: CASE REPORTS I Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Congenital Pulmonary Airway Malformation San Diego Convention Center Monday, P13 9:15 am-4:15 pm; Intrapulmonary Sequestration: A Rare Congenital Accessory B52: BACTERIAL INFECTION CASE REPORTS Area A (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P2 9:15 am-4:15 pm; Recurrent Pneumonia in a Healthy Adult: A Rare Case of Congenital B52: BACTERIAL INFECTION CASE REPORTS Area A (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pulmonary Airway Malformation San Diego Convention Center P1042 9:15 am-4:15 pm; Living with One Lung B58: WHO'S BAD: CASE REPORTS IN PULMONARY Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm VASCULAR MEDICINE I San Diego Convention Center Tuesday, P1062 9:15 am-4:15 pm; An Incidentally Discovered Congenital Pulmonary Airway C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Malformation DISEASE San Diego Convention Center P1054 9:15 am-4:15 pm; Bilateral and Multilobar Congenital Pulmonary Airway Malformation C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Type 2: A Rare Case DISEASE San Diego Convention Center P1063 9:15 am-4:15 pm; Bronchial Atresia Associated with a Bronchogenic Cyst C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm DISEASE San Diego Convention Center

34 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P1059 9:15 am-4:15 pm; Charlotte’s Web (of Bowels in the Chest) C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm DISEASE San Diego Convention Center P1064 9:15 am-4:15 pm; Congenital Pulmonary Airway Malformation in a Female Infant —­ C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Management Challenges in a Developing Country DISEASE San Diego Convention Center P1068 9:15 am-4:15 pm; Do Not Miss the Nuances: Failure to Thrive and Wheezing. A Case of C66: PEDIATRIC CASE REPORTS: CARDIOVASCULAR AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Scimitar Syndrome CRITICAL CARE DISEASE San Diego Convention Center P176 9:15 am-4:15 pm; Partial Anomalous Pulmonary Venous Return: Different Management C69: USE YOUR ILLUSION: NOVEL THERAPEUTIC Area C (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Approaches APPROACHES IN PULMONARY HYPERTENSION San Diego Convention Center Wednesday, P436 9:15 am-4:15 pm; Right Side Aortic Arch with Aberrant Left Subclavian Artery D49: SURFING SAFARI: CASE REPORTS IN PULMONARY Area E (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm VASCULAR MEDICINE II San Diego Convention Center P469 9:15 am-4:15 pm; Severe Pulmonary Artery Hypertension in the Setting of Isolated D50: CLOT ON THE ROCKS: CASE REPORTS OF PE AND Area E (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Unilaterally Absent Pulmonary Artery CTEPH San Diego Convention Center RARE IDIOPATHIC INTERSTITIAL PNEUMONIAS — OTHER Sunday, P1133 9:15 am-4:15 pm; A Rare Case of Bronchiolocentric Interstitial Fibrosis A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1305 9:15 am-4:15 pm; Telomere Length and the MUC5B Promoter Polymorphism in A43: ILD SCIENTIFIC ABSTRACTS: GENERAL Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Patients with Unclassifiable Interstitial Lung Disease San Diego Convention Center Tuesday, P774 9:15 am-4:15 pm; An Unusual Presentation of CMV Pneumonitis C53: CRITICAL CARE CASE REPORTS: YOU GIVE ME Area G (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm (MORE) FEVER - INFECTION AND SEPSIS San Diego Convention Center Wednesday, P903 9:15 am-4:15 pm; Early Diagnosis and Treatment of Acute Interstitial Pneumonia D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P923 9:15 am-4:15 pm; Interstitial Lung Disease in a Patient with Quiescent Ulcerative D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Colitis San Diego Convention Center RARE PLEURAL DISEASE Sunday, P1428 9:15 am-4:15 pm; A Unusual Case of Dyspnea: A Pancreaticopleural Fistula A48: DYSPNEA: CASE REPORTS I Area L (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1425 9:15 am-4:15 pm; Pulmonary Extramedullary Hematopoiesis in a Patient with A48: DYSPNEA: CASE REPORTS I Area L (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Polycythemia Vera San Diego Convention Center

35 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P745 9:15 am-4:15 pm; A Novel Use of Intrapleural t-PA/DNase Therapy for Loculated B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Chylothorax San Diego Convention Center P748 9:15 am-4:15 pm; Multi-Modality Management of a Lone Mediastinal Silicosis B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Presenting as an Extremely Rare Case of Chylothorax San Diego Convention Center P838 9:15 am-4:15 pm; Chylous Pleural Effusion: A Rare Complication of Chronic B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Lymphocytic Leukemia San Diego Convention Center P804 9:15 am-4:15 pm; An Exudative Urinothorax with Low Creatinine and Low pH B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P826 9:15 am-4:15 pm; Fungus Among Us: A Rare Case of Infected Chylothorax B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P814 9:15 am-4:15 pm; Bilothorax: Rare Cause of Respiratory Failure After Percutaneous B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Liver Biopsy San Diego Convention Center P23 9:15 am-4:15 pm; New Onset Atrial Fibrillation Masking a Nephropleural Fistula B52: BACTERIAL INFECTION CASE REPORTS Area A (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P341 9:15 am-4:15 pm; An Extremely Rare Case of Transudate Chylothorax Secondary to B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Carcinoid Tumor San Diego Convention Center Tuesday, P644 9:15 am-4:15 pm; Chylothorax After Abdominal Surgery — A Fatal Outcome C50: CRITICAL CARE CASE REPORTS: THE LIVER, Area G (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm PANCREAS, AND INTESTINES San Diego Convention Center P796 9:15 am-4:15 pm; Coprothorax: A Feculent Pleura C54: CRITICAL CARE CASE REPORTS: CAUSES AND Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm COMPLICATIONS OF ACUTE RESPIRATORY FAILURE San Diego Convention Center P1051 9:15 am-4:15 pm; Tension Faecopneumothorax: A Rare Complication of Ruptured C65: PEDIATRIC CASE REPORTS: NEONATAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Morgagni Diaphragmatic Hernia: Case Report and Review of DISEASE San Diego Convention Center Literature Wednesday, P1067 9:15 am-4:15 pm; It’s Never Lupus: A Rare Case of Methimazole Induced Pleural D35: DRUG INDUCED LUNG DISEASE: CASE REPORTS Area J (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Effusion San Diego Convention Center P686 9:15 am-4:15 pm; Left Sided Catamenial Pneumothorax : A Rare Entity D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P685 9:15 am-4:15 pm; Talcoma: The Confounding of a Differential Diagnosis in a Patient D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm with a Pleural-Based Mass San Diego Convention Center

36 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P710 9:15 am-4:15 pm; Another Case of Pleural Based Malignancy or Perhaps Not: An D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Unusual Presentation of Gunshot Injury San Diego Convention Center P688 9:15 am-4:15 pm; Extramedullary Hematopoesis of the Pleura: A Rare Cause of D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Massive Hemothorax San Diego Convention Center P673 9:15 am-4:15 pm; Pancreaticopleural Fistulae; a Rare Pulmonary Complication of an D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Intra-Abdominal Disease San Diego Convention Center P721 9:15 am-4:15 pm; Chylothorax Due to Esophageal Duplication Cyst: Case Report D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P679 9:15 am-4:15 pm; Pyocholethorax: A Rare Complication of Percutaneous Transhepatic D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Biliary Drainage San Diego Convention Center P716 9:15 am-4:15 pm; A Case of Cryptogenic Bilateral Fibrosing Pleuritis, an Extremely D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Rare Form of Interstitial Lung Disease San Diego Convention Center P702 9:15 am-4:15 pm; Transudative Chylothorax: A Portal Hypertension Problem? D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P696 9:15 am-4:15 pm; Spontaneous Pneumomediastinum (Hamman’s Syndrome): A Case D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Report San Diego Convention Center RARE TUMORS — AIRWAY Monday, P777 9:15 am-4:15 pm; Long Term Efficacy of Radio Frequency Ablation for Superficial B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Lesions of the Tracheobronchial Tree San Diego Convention Center P296 9:15 am-4:15 pm; Incidental Finding of Endobronchial Schwannoma in Lung B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) 11:15 am-1:00 pm Transplant Candidate Undergoing Lung Nodule Evaluation San Diego Convention Center P299 9:15 am-4:15 pm; Abscopal Effect Following CT Guided Permanent Seed B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Brachytherapy for Metastatic Adenoid Cystic Carcinoma to Lung San Diego Convention Center P306 9:15 am-4:15 pm; An Atypical Bronchopulmonary Carcinoid Tumor Manifesting as B71: CASE REPORTS IN THORACIC ONCOLOGY III Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Abdominal Cramping San Diego Convention Center P311 9:15 am-4:15 pm; A Rare Cause of Hemoptysis: Inflammatory Myofibroblastic Tumor B71: CASE REPORTS IN THORACIC ONCOLOGY III Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm of the Trachea San Diego Convention Center P328 9:15 am-4:15 pm; Bilateral Primary Endobronchial Leiomyosarcoma B71: CASE REPORTS IN THORACIC ONCOLOGY III Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center

37 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P351 9:15 am-4:15 pm; Rare Presentation of Sclerosing Pneumocytoma Manifesting as an B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Endobronchial Lesion San Diego Convention Center P354 9:15 am-4:15 pm; Dual Primary Lung Cancers. Mucoepidermoid Carcinoma and B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Adenocarcinoma, a Rare Entity San Diego Convention Center P392 9:15 am-4:15 pm; Tracheobronchial Inflammatory Myofibroblastic Tumor in a Young B74: CASE REPORTS IN THORACIC ONCOLOGY VI Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Adult with Subsequent Sarcoidosis San Diego Convention Center P414 9:15 am-4:15 pm; Unusual Presentation of Pulmonary MALT-Lymphoma as an B75: CASE REPORTS IN THORACIC ONCOLOGY VII Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Occlusive Mainstem Endobronchial Mass San Diego Convention Center P418 9:15 am-4:15 pm; Obstructing Hyalinizing Clear Cell Primary Tracheal Carcinoma B75: CASE REPORTS IN THORACIC ONCOLOGY VII Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Presenting with a Non-Fixed Expiratory Spirogram San Diego Convention Center Tuesday, P1039 9:15 am-4:15 pm; Pediatric Endobronchial Tumor Leading to Recurrent Pneumonia C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm BRONCHOSCOPY San Diego Convention Center P1041 9:15 am-4:15 pm; Interesting Presentation of a Rare Endobronchial Lesion C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm BRONCHOSCOPY San Diego Convention Center P1026 9:15 am-4:15 pm; When Wheezing Isn’t Asthma: A Case of Mucoepidermoid C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Carcinoma of the Trachea BRONCHOSCOPY San Diego Convention Center P1115 9:15 am-4:15 pm; A Lump in His Throat: Refractory Recurrent Respiratory C68: PEDIATRIC CASE REPORTS: IMMUNODEFICIENCY Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Papillomatosis with Pulmonary Parenchymal Involvement Improved AND INFECTION San Diego Convention Center with Systemic Bevacizumab Wednesday, P640 9:15 am-4:15 pm; Use of Endotracheal Stent for Hemostasis of a Bleeding D31: INTERVENTIONAL PULMONARY: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Glomus Tumor San Diego Convention Center P641 9:15 am-4:15 pm; Endobronchial Liposuction: Excision of Endobronchial Lipoma in D31: INTERVENTIONAL PULMONARY: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Patient with Pulmonary Hamartoma San Diego Convention Center P630 9:15 am-4:15 pm; Extranodal NK/T-Cell Lymphoma of the Trachea Causing Airway D31: INTERVENTIONAL PULMONARY: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Compromise San Diego Convention Center P653 9:15 am-4:15 pm; Carcinoma Ex Pleomorphic Adenoma of the Airway and Parenchyma D31: INTERVENTIONAL PULMONARY: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center RARE TUMORS — PARENCHYMAL Sunday, P1148 9:15 am-4:15 pm; Benign Pulmonary Nodular Lymphoid Hyperplasia (NLH) in an HIV A40: ILD: CASE REPORTS I Area K (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm Infected Patient: A Diagnostic Dilemma San Diego Convention Center 38 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P672 9:15 am-4:15 pm; Pulmonary Nodular Lymphoid Hyperplasia Associated with Multiple B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Sclerosis San Diego Convention Center P702 9:15 am-4:15 pm; Pulmonary Inflammatory Myofibroblastic Tumor (IMT) with B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Remarkable Response to Corticosteroids San Diego Convention Center P763 9:15 am-4:15 pm; Using EBUS to Sample Pulmonary Artery Tumors B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P768 9:15 am-4:15 pm; Extranodal Natural Killer/T Cell Lymphoma, Nasal Type: A Rare B37: INTERVENTIONAL PULMONARY: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pulmonary Presentation San Diego Convention Center P1212 9:15 am-4:15 pm; A Case of Suspected Metastatic Choriocarcinoma Versus Ectopic B46: CRITICAL CARE CASE REPORTS: HEMATOLOGY, Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Beta-HCG Producing Adenocarcinoma Causing Acute Hypoxic ONCOLOGY, RHEUMATOLOGY, AND IMMUNOLOGY San Diego Convention Center Respiratory Distress and Thyroid Storm P259 9:15 am-4:15 pm; A Giant Pain in the Shoulder B69: CASE REPORTS IN THORACIC ONCOLOGY I Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P265 9:15 am-4:15 pm; A Unique Presentation of a Rare Primary Epithelial-Myoepithelial B69: CASE REPORTS IN THORACIC ONCOLOGY I Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Carcinoma of Lung San Diego Convention Center P266 9:15 am-4:15 pm; Primary Lung Diffuse Large B-Cell Lymphoma with Hepatic B69: CASE REPORTS IN THORACIC ONCOLOGY I Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Metastases: A Rare Neoplasm San Diego Convention Center P274 9:15 am-4:15 pm; Hemoptysis as a Presentation of Composite Hemangioendothelioma B69: CASE REPORTS IN THORACIC ONCOLOGY I Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P279 9:15 am-4:15 pm; Pulmonary Artery Sarcoma Presenting as a Pulmonary Embolism B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P281 9:15 am-4:15 pm; Unusual Presentation of an Uncommon Lung Tumor: A Case Report B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P283 9:15 am-4:15 pm; “Hepatoid Adenocarcinoma of the Lung with Normal Alpha- B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Fetoprotein Level” San Diego Convention Center P284 9:15 am-4:15 pm; Incidental Diagnosis of Primary Pulmonary Synovial Sarcoma B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm (PPSS) in an Elderly Patient with Pulmonary Fibrosis Complicated San Diego Convention Center by Radiation Pneumonitis P285 9:15 am-4:15 pm; Squamous Cell Carcinoma in a Young Patient with a Chronic B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Infectious Disease San Diego Convention Center

39 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P286 9:15 am-4:15 pm; Pulmonary Large Cell Neuro-Endocrine Cancer: A Diagnostic B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Difficulty and Therapeutic Dilemma San Diego Convention Center P291 9:15 am-4:15 pm; Biphasic Pulmonary Blastoma Invading the Mediastinum and B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pleura with Brain Metastasis in an Adult Female San Diego Convention Center P297 9:15 am-4:15 pm; Chronic Hemoptysis: Manifestation of a Rare, Obscure, and Fatal B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) 11:15 am-1:00 pm Diagnosis San Diego Convention Center P309 9:15 am-4:15 pm; The New Miliary Kid on the Block B71: CASE REPORTS IN THORACIC ONCOLOGY III Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P323 9:15 am-4:15 pm; Lung Inflammatory Pseudotumor in an Adult Smoker B71: CASE REPORTS IN THORACIC ONCOLOGY III Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P325 9:15 am-4:15 pm; An Undifferentiated Malignancy B71: CASE REPORTS IN THORACIC ONCOLOGY III Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P334 9:15 am-4:15 pm; Myelolipoma: A Rare Tumor in a Rare Location B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P335 9:15 am-4:15 pm; Brotherly Love: A Case of Pulmonary Plasma Cell Granuloma in B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Twin Brothers San Diego Convention Center P346 9:15 am-4:15 pm; A Nut-ty Case of Lung Cancer B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P347 9:15 am-4:15 pm; A Rare Malignancy of the Lung: A Case of Solitary Plasmacytoma B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P350 9:15 am-4:15 pm; Near Complete Right Lung Obliteration Due to Rare Pulmonary NUT B72: CASE REPORTS IN THORACIC ONCOLOGY IV Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Midline Carcinoma San Diego Convention Center P365 9:15 am-4:15 pm; Lung Cancer in Very Young Males B73: CASE REPORTS IN THORACIC ONCOLOGY V Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P359 9:15 am-4:15 pm; Pulmonary Artery Sarcoma Diagnosed by Endovascular Catheter- B73: CASE REPORTS IN THORACIC ONCOLOGY V Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Guided Biopsy: A Case Report San Diego Convention Center P375 9:15 am-4:15 pm; An Unusual Tumor with Unusual Metastasis B73: CASE REPORTS IN THORACIC ONCOLOGY V Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center

40 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P377 9:15 am-4:15 pm; Sleeping Beauty: A Case of a 15-Year-Old Pulmonary Epithelioid B73: CASE REPORTS IN THORACIC ONCOLOGY V Area D (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Hemangioendothelioma San Diego Convention Center P363 9:15 am-4:15 pm; Pneumocytoma: A Benign Cause of a Malignant Diagnosis B73: CASE REPORTS IN THORACIC ONCOLOGY V Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P372 9:15 am-4:15 pm; Primary Pulmonary Angiosarcoma: Rare and Deadly B73: CASE REPORTS IN THORACIC ONCOLOGY V Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P393 9:15 am-4:15 pm; Rapid Progressive Pulmonary Malignant Perivascular Epithelioid Cell B74: CASE REPORTS IN THORACIC ONCOLOGY VI Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Tumor: A Case Report and Literature Review San Diego Convention Center P405 9:15 am-4:15 pm; A Rare Entity of Primary Pulmonary Hodgkin Lymphoma with B74: CASE REPORTS IN THORACIC ONCOLOGY VI Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Cavitation San Diego Convention Center P385 9:15 am-4:15 pm; A Rare Case of Metastatic Choriocarcinoma Presenting One Week B74: CASE REPORTS IN THORACIC ONCOLOGY VI Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm After a Term Pregnancy San Diego Convention Center P413 9:15 am-4:15 pm; Pulmonary Sarcomatoid Carcinoma: An Often Missed Diagnosis B75: CASE REPORTS IN THORACIC ONCOLOGY VII Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm with Poor Prognosis San Diego Convention Center P420 9:15 am-4:15 pm; Expanding Lung Mass in a Patient with Chronic Myelomonocytic B75: CASE REPORTS IN THORACIC ONCOLOGY VII Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Leukemia San Diego Convention Center Tuesday, P787 9:15 am-4:15 pm; Metastatic Angiosarcoma Presenting as Diffuse Alveolar C54: CRITICAL CARE CASE REPORTS: CAUSES AND Area G (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Hemorrhage COMPLICATIONS OF ACUTE RESPIRATORY FAILURE San Diego Convention Center P1222 9:15 am-4:15 pm; Presentation of Pulmonary Kaposi Sarcoma in the Absence of C59: UNUSUAL PULMONARY INFECTIONS Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Cutaneous Manifestations: A Diagnostic Challenge for Physicians San Diego Convention Center P1042 9:15 am-4:15 pm; Recurrent Pneumonia—When to Think Outside the Box C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm BRONCHOSCOPY San Diego Convention Center P1113 9:15 am-4:15 pm; Pulmonary Alveolar Proteinosisand Pulmonary Kaposi Sarcoma in a C68: PEDIATRIC CASE REPORTS: IMMUNODEFICIENCY Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Young Adult with HIV AND INFECTION San Diego Convention Center Wednesday, P933 9:15 am-4:15 pm; Lymphocytic Interstitial Pneumonitis with Lung-Localised D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm MALT LymphomaPresenting as Infiltrates on Chest X-Ray in an San Diego Convention Center Asymptomatic Patient P745 9:15 am-4:15 pm; Endemic Kaposi Disease (KD) with Pulmonary Localization: A Case D37: CF AND NON-CF BRONCHIECTASIS AND IMMUNE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Report DEFICIENCIES: CASE REPORTS San Diego Convention Center

41 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location RARE TUMORS — PLEURAL Monday, P819 9:15 am-4:15 pm; Pleural Lipoma with Secondary Changes — A Diagnostic Challenge B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P301 9:15 am-4:15 pm; Primary Synovial Sarcoma of the Pleura: A Rare Cause of a Lung B70: CASE REPORTS IN THORACIC ONCOLOGY II Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Mass San Diego Convention Center P314 9:15 am-4:15 pm; An Autopsied Case of Neurofibromatosis Type 1(von Recklinghau- B71: CASE REPORTS IN THORACIC ONCOLOGY III Area D (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm sen's Disease) Associated Malignant Peripheral Nerve Sheath Tu- San Diego Convention Center mor Carcinomatous Pleurisy with Giant Intrathoracic Meningoceles Wednesday, P687 9:15 am-4:15 pm; Recurrence of Resected Solitary Fibrous Tumor D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P693 9:15 am-4:15 pm; A Case of Pleuropulmonary Nodular Lymphoid Hyperplasia D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Presenting with Recurrent Exudative Pleural Effusions San Diego Convention Center P697 9:15 am-4:15 pm; Deadly Imposter: A Rare Pleural Tumor Masquerading as Pulmonary D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Abscess San Diego Convention Center P704 9:15 am-4:15 pm; Malignant Pleural Effusion as the First Presentation of Thyroid D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Cancer San Diego Convention Center P720 9:15 am-4:15 pm; Doege Potter Syndrome: Solitary Fibrous Tumor of the Pleura D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Associated with Hypoglycemia San Diego Convention Center RELAPSING POLYCHONDRITIS Sunday, 204 2:15 pm-4:15 pm; Long-Term Outcome of Metallic Stenting for Airway Involvement in A103: ILD: OUTCOMES Room 6 D (Upper Level) May 20, 2018 Poster Viewing 2:15 pm-2:45 pm Relapsing Polychondritis San Diego Convention Center Poster Discussion 2:45 pm-4:15 pm Wednesday, P646 9:15 am-4:15 pm; Unrelenting Tracheobronchial Stenosis in Relapsing Polychondritis D31: INTERVENTIONAL PULMONARY: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center SCLERODERMA LUNG DISEASE Sunday, 908 9:15 am-11:15 am; Safety and Suitability of a Direct Thrombin Inhibitor, Dabigatran A21: CLINICAL AND MECHANISTIC STUDIES OF LUNG Pacific Ballroom 15-17 (North Tower, May 20, 2018 Poster Viewing 9:15 am-9:45 am Etexilate, in Scleroderma-Associated Interstitial Lung Disease FIBROSIS First Floor) Poster Discussion 9:45 am-11:15 am (SSc-ILD) Patients Marriott Marquis San Diego Marina

42 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, 609 9:15 am-11:15 am; Hemodynamics and Prognosis in Scleroderma-Associated PAH A27: YOU GOT ANOTHER THING COMING: DIAGNOSIS Room 30 C-E (Upper Level) May 20, 2018 Poster Viewing 9:15 am -10:00 am AND PROGNOSTICATION IN PULMONARY HYPERTENSION San Diego Convention Center Poster Discussion 10:00 am-11:15 am P660 9:15 am-4:15 pm; M10, a 10 Amino Acid Peptide, Regulates the Extracellular Matrix A68: MOLECULAR DETERMINANTS OF REMODELING IN Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Expression via a Dual Mechanism in Scleroderma Associated Lung LUNG FIBROSIS San Diego Convention Center Fibrosis Monday, P649 9:15 am-4:15 pm; Re-evaluation of The Parenchymal CT Features of Scleroderma B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Lung Disease Using Volumetric HRCT San Diego Convention Center P648 9:15 am-4:15 pm; Small Airway Disease a Potential Feature of Scleroderma B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm LungDisease San Diego Convention Center P182 9:15 am-4:15 pm; Patients With Scleroderma Are At Increased Risk For Sleep Disorder B67: RISK AND PREVALENCE OF SLEEP DISORDERED Area C (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Breathing (sdb) BREATHING San Diego Convention Center Tuesday, 907 9:15 am-11:15 am; Molecular Evidences for Antifibrotic Potentials of Nintedanib in C28: ROLE OF CELLULAR CROSS TALK IN LUNG Pacific Ballroom 15-17 (North Tower, May 22, 2018 Poster Viewing 9:15 am-9:45 am Interstitial Lung Disease Associated with Systemic Sclerosis HOMEOSTASIS AND AGING First Floor) Poster Discussion 9:45 am-11:15 am Marriott Marquis San Diego Marina Wednesday, 9:15 am-11:15 am; Predicting Mortality in Systemic Sclerosis-Related Interstitial Lung D14: ILD: CLINICAL RESEARCH Room 3 (Upper Level) May 23, 2018 Oral Presentation 9:30 am-9:45 am Disease in Two Independent Cohorts San Diego Convention Center SHRINKING LUNG SYNDROME Monday, P686 9:15 am-4:15 pm; The Other "Baby Lung": Shrinking Lung Syndrome in the Absence B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm of Confirmed Connective Tissue Disease San Diego Convention Center P703 9:15 am-4:15 pm; Rare Case of Systemic Lupus Erythematosus Shrinking Lung B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Syndrome in a Young Male Patient San Diego Convention Center P684 9:15 am-4:15 pm; Shrinking into Thin Air? A Case Report of Vanishing Lung Syndrome B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center SICKLE CELL DISEASE Sunday, P616 9:15 am-4:15 pm; Airway Inflammatory Patterns in Sickle Cell Disease A62: SICKLE CELL DISEASE Area F (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Monday, 9:15 am-11:15 am; Platelets shed extracellular vesicles to promote IL-1β Dependent B15: IMMUNE PATHWAYS IN LUNG INJURY AND REPAIR Pacific Ballroom 22 (North Tower, First May 21, 2018 Oral Presentation 9:15 am-9:30 am Lung Vaso-Occlusion in Sickle Cell Disease Floor) Marriott Marquis San Diego Marina

43 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location SILICOSIS Monday, 1003 9:15 am-11:15 am; Comparison of Decellularization between Normal and Silicotic B29: LUNG ECM ENVIRONMENT: NOVEL FINDINGS AND Pacific Ballroom 24-26 (North Tower, May 21, 2018 Poster Viewing 9:15 am-9:45 am Lungs on Lung Function and Extracellular Matrix Components MODELS IN FIBROSIS First Floor) Poster Discussion 9:45 am-11:15 am Marriott Marquis San Diego Marina P80 9:15 am-4:15 pm; Complicated Silicosis Mimicking Primary Lung Malignancy on B49: OCCUPATIONAL EXPOSURES Area B (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Imaging San Diego Convention Center SJOGREN’S SYNDROME Wednesday, P699 9:15 am-4:15 pm; An Unusual Cause of Pleural Effusion D36: PLEURAL DISEASE: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center 214 1:30 pm-3:30 pm; Primary Sjögren’s Syndrome-Associated Interstitial Lung D103: TRANSPLANT AND ILD POTPOURRI Room 6 D (Upper Level) Poster Viewing 1:30 pm-2:00 pm Disease—A Descriptive Study San Diego Convention Center Poster Discussion 2:00 pm-3:30 pm SWEET SYNDROME Monday, P277 9:15 am-4:15 pm; Sweet Syndrome with Pulmonary Involvement: High Index of B69: CASE REPORTS IN THORACIC ONCOLOGY I Area D (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Suspicion Important for Differentiation from Pneumonia and Timely San Diego Convention Center Treatment Wednesday, P780 9:15 am-4:15 pm; Acute Respiratory Failure: A Rare Manifestation of Sweet D39: DYSPNEA: CASE REPORTS II Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Hydrothorax San Diego Convention Center THORACIC ENDOMETRIOSIS/CATAMENIAL PNEUMOTHORAX Monday, P809 9:15 am-4:15 pm; A Rare Case of Thoracic Endometriosis Presenting with B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Hemopneumothorax San Diego Convention Center P811 9:15 am-4:15 pm; Catamenial Hemothorax a Rare Cause of Recurrent Pleural Effusion B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P837 9:15 am-4:15 pm; A Rare Case of Tension Hydropneumothorax from Disseminated B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Endometriosis San Diego Convention Center TRACHEOBRONCHOPATHIA OSTEOCHONDROPLASTICA Wednesday, P761 9:15 am-4:15 pm; Tracheobronchopathia Osteochondroplastica: Rare Cause of D38: COUGH: CASE REPORTS Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Dyspnea, Cough, and Bronchitis San Diego Convention Center

44 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location VASCULITIS —­ ANCA-ASSOCIATED Monday, P645 9:15 am-4:15 pm; Clinical Utility of Serial Measurements of Antineutrophil Cytoplasmic B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Antibodies Targeting Proteinase 3 by Automated Bead-Based Assay San Diego Convention Center Tuesday, P1101 9:15 am-4:15 pm; Prolidase Deficiency and ANCA-Associated Vasculitis in a 16-Month C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Old Boy DISEASE San Diego Convention Center VASCULITIS — EOSINOPHILIC GRANULOMATOSIS WITH POLYANGIITIS (EGPA) Sunday, P863 9:15 am-4:15 pm; Hypoxia and Eosinophilia in a Patient with 'Difficult Asthma' A31: ALLERGY AND ASTHMA CASE REPORTS Area H (Hall A-B2, Ground Level) May 20, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P868 9:15 am-4:15 pm; Glucocorticoid Sparing Effects of Reslizumab in the Treatment of A34: ASTHMA CLINICAL STUDIES I Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Eosinophilic Granulomatosis with Polyangiitis San Diego Convention Center P872 9:15 am-4:15 pm; Low Dose Mepolizumab in Eosinophilic Granulomatosis with A34: ASTHMA CLINICAL STUDIES I Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Polyangiitis San Diego Convention Center P878 9:15 am-4:15 pm; A Novel Tool to Measure Clinical Activity and Outcomes in A34: ASTHMA CLINICAL STUDIES I Area H (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Eosinophilic Granulomatosis with Polyangiitis San Diego Convention Center Monday, P644 9:15 am-4:15 pm; Eosinophilic Granulomatosis with Polyangiitis Patient Characteristics B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm and Clinical Response to Mepolizumab Compared to Placebo San Diego Convention Center P1244 9:15 am-4:15 pm; Immunosuppressive Therapy Ameliorates Severe Pulmonary B47: CRITICAL CARE CASE REPORTS: CARDIOVASCULAR Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Hypertension and Refractory Vasospastic Angina Due to Eosinophilic DISEASES AND ECHOCARDIOGRAPHY San Diego Convention Center Granulomatosis with Polyangiitis P1247 9:15 am-4:15 pm; Eosinophilic Granulomatosis with Polyangiitis Presenting with B47: CRITICAL CARE CASE REPORTS: CARDIOVASCULAR Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Cardiac Tamponade DISEASES AND ECHOCARDIOGRAPHY San Diego Convention Center Tuesday, P162 9:15 am-4:15 pm; Clinical and Economic Characteristics of Patients Diagnosed with C41: HEALTH SERVICES RESEARCH IN PULMONARY Area B (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Eosinophilic Granulomatosis with Polyangiitis (EGPA, formerly DISEASE San Diego Convention Center Churg-Strauss Syndrome) in the United States P1102 9:15 am-4:15 pm; ANCA-Negative Eosinophilic Granulomatosis with Polyangitis C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Presenting as Hemoptysis in a Pediatric Patient DISEASE San Diego Convention Center VASCULITIS — GRANULOMATOSIS WITH POLYANGIITIS (GPA) Monday, P627 9:15 am-4:15 pm; Diffuse Cobblestone Appearance of the Tracheobronchial Tree: A B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Rare Presentation of Granulomatosis with Polyangiitis San Diego Convention Center

45 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P636 9:15 am-4:15 pm; A Rare Case of Polyangiitis Overlap Syndrome: Granulomatosis with B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm Polyangiitis and Eosinophilic Granulomatosis with Polyangiitis San Diego Convention Center P680 9:15 am-4:15 pm; The Benefit of Plasmapheresis on Alveolar Hemorrhage in B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pulmonary-Renal Syndrome: A Case of Granulomatosis with San Diego Convention Center Polyangiitis (GPA) P691 9:15 am-4:15 pm; Auto-Pneumonectomy with Compensatory Lobar Hyper-Expansion B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm and Extreme Mediastinal Shift in Granulomatosis with Polyangiitis San Diego Convention Center P667 9:15 am-4:15 pm; A Case of Granulomatosis with Polyangiitis Masquerading as Fungal B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Pneumonia San Diego Convention Center P694 9:15 am-4:15 pm; Flu Vaccine Associated ANCA Vasculitis: A Rare Entity B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm San Diego Convention Center Tuesday, P707 9:15 am-4:15 pm; Massive Hemoptysis and Diffuse Alveolar Hemorrhage from C52: CRITICAL CARE CASE REPORTS: GOOD VIBRATIONS Area G (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Granulomatosis with Polyangiitis Successfully Rescued by — MECHANICAL VENTILATION FROM NIV TO ECMO San Diego Convention Center Extracorporeal Membrane Oxygenation P1103 9:15 am-4:15 pm; All that Wheezes Is Not Asthma: An Atypical Presentation of C67: PEDIATRIC CASE REPORTS: INTERSTITIAL LUNG Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Granulomatosis with Polyangiitis in an 8-Year-Old Female DISEASE San Diego Convention Center VASCULITIS — MICROSCOPIC POLYANGIITIS Monday, P637 9:15 am-4:15 pm; Bloody Lungs and Broken Kidneys Banded in One Blight B32: CLINICAL STUDIES IN AUTOIMMUNE LUNG DISEASE Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1201 9:15 am-4:15 pm; Microscopic Polyangiitis Complicated Due to Mucormycosis B46: CRITICAL CARE CASE REPORTS: HEMATOLOGY, Area K (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm ONCOLOGY, RHEUMATOLOGY, AND IMMUNOLOGY San Diego Convention Center Wednesday, P910 9:15 am-4:15 pm; Presentation of MPO-ANCA Positive Microscopic Polyangiitis with D33: ILD: CASE REPORTS III Area H (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm Usual Interstitial Pneumonia San Diego Convention Center VASCULITIS — OTHER Monday, P698 9:15 am-4:15 pm; Beware of the Rare: Fatal Hemoptysis in Hughes-Stovin Syndrome B34: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center P1017 9:15 am-4:15 pm; Hughes-Stovin Syndrome and Chronic Thromboembolic Pulmonary B58: WHO'S BAD: CASE REPORTS IN PULMONARY Area J (Hall A-B2, Ground Level) Poster Viewing 11:15 am-1:00 pm Hypertension: A Case Report VASCULAR MEDICINE I San Diego Convention Center

46 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P1024 9:15 am-4:15 pm; A Cough that Is More than Asthma: A Rare Case of Bronchiectasis C64: PEDIATRIC CASE REPORTS: AIRWAY DISEASES AND Area J (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm BRONCHOSCOPY San Diego Convention Center P1019 9:15 am-4:15 pm; Regrets Over a Missed Opportunity to Have a Biological Child — D34: LUNG TRANSPLANT AND DRUG INDUCED LUNG Area J (Hall A-B2, Ground Level) 11:15 am-1:00 pm One Couple’s Journey After Lung Transplantation for Cystic Fibrosis DISEASE: CASE REPORTS San Diego Convention Center Wednesday, P725 9:15 am-4:15 pm; Williams-Campbell Syndrome: An Elusive Cause of Bronchiectasis D37: CF AND NON-CF BRONCHIECTASIS AND IMMUNE Area G (Hall A-B2, Ground Level) May 23, 2018 Poster Viewing 11:15 am-1:00 pm DEFICIENCIES: CASE REPORTS San Diego Convention Center XIPHOIDYNIA Tuesday, P365 9:15 am-4:15 pm; Excision of the Xiphoid Process for Chronic Pain: Patient C76: CHEST WALL, RESPIRATORY MUSCLES: NEURAL Area D (Hall A-B2, Ground Level) May 22, 2018 Poster Viewing 11:15 am-1:00 pm Characteristics and Results AND VENTILATORY CONTROL San Diego Convention Center YELLOW NAIL SYNDROME Monday, P835 9:15 am-4:15 pm; Rare Presentation of a Rare Disease B39: PLEURAL DISEASE: CASE REPORTS I Area G (Hall A-B2, Ground Level) May 21, 2018 Poster Viewing 11:15 am-1:00 pm San Diego Convention Center

47 B:11.25” T:11” S:10.5” YOU’RE INVITED TO 2 BOEHRINGER INGELHEIM GURU BAR SESSIONS

INTRODUCING RAD ROUNDS—UIP TO IPF: CONCOMITANT IDIOPATHIC PULMONARY A Digital Application to Identify Usual Interstitial FIBROSIS AND EMPHYSEMA: Pneumonia on HRCT Strategies to Improve Patient Management May 20, 2018, 12:30 PM May 21, 2018, 12:30 PM GURU BAR 1, EXHIBIT HALL GURU BAR 3, EXHIBIT HALL B:6.25” S:5.5” T:6”

Join us to learn about the recently launched Rad Rounds —UIP to IPF mobile app. The app’s radiology content and usual interstitial pneumonia (UIP) diagnostic algorithm will be detailed by an expert pulmonologist and radiologist.

TO INSTALL THIS APP ON YOUR iPHONE OR ANDROID PHONE: Come learn about the presence of concomitant emphysema in some patients Text RADIPF to 313131 to receive a download link for your iPhone with IPF and discuss management strategies for patients with CPFE with an Text RADUIP to 313131 to receive a download link for your Android phone expert pulmonologist.

CPFE, combined pulmonary fi brosis and emphysema; HRCT, high-resolution computed tomography; IPF, idiopathic pulmonary fi brosis. Copyright ©2018, Boehringer Ingelheim Pharmaceuticals, Inc. All rights reserved. (02/18) PC-US-102966

10928814_ATS_RLD_Guide_Ad_UNBRND_M5.indd 1 PREPARED BY FCB 3/19/18 3:12 PM Releasing as: PDFx1a Production: Maureen Rodolfy Job #: 10928814 Colors: 4C AD: Kevin Thompson Client: BI Live Area: 10.5"w x 5.5"h AE: Ashley Massaroco Product: NINT Trim: 11"w x 6"h Producer: Odochi Ibe Client Code: PC-US-102966 Bleed: 11.25"w x 6.25"h QC: L.Powell Date: March 19, 2018 3:05 PM Note: Digital Artist: VA, VA, gw, gw, tp Add’l Info: Proof: M5 Fonts: Co Text, Gotham, Helvetica Neue LT Std, Minion Pro FR Spellcheck: M. Massey Path: PrePress:BI_P zer:NINTEDANIB:10928814:10928814_ATS_RLD_Guide_Ad_UNBRND_M5 4C ATS Rare Lung Guide: Unbranded B:11.25” T:11” S:10.5”

JOIN US FOR AN INDUSTRY-ORGANIZED SYMPOSIUM Sponsored by Boehringer Ingelheim Pharmaceuticals, Inc.

Sunday, May 20, 2018 6:30 PM Dinner/Symposium AND VISIT BOOTH #1915 Hilton San Diego Bayfront B:6.25” S:5.5” Indigo Ballroom D/H TO LEARN MORE ABOUT OFEV T:6” San Diego, CA

ADMISSION IS COMPLIMENTARY AND WILL BE ON A FIRST-COME, FIRST-SERVED BASIS. DINNER WILL BE PROVIDED.

An Industry-Organized Symposium at the ATS 2018 International Conference. All ATS 2018 International Conference attendees are invited to this non-CME/CNE educational program sponsored by Boehringer Ingelheim Pharmaceuticals, Inc.

Attendance is limited to healthcare professionals only. Aspects of this program may be reportable under the physician payments Sunshine Act.

CME, continuing medical education; CNE, continuing nursing education.

Copyright ©2018, Boehringer Ingelheim Pharmaceuticals, Inc. All rights reserved. (02/18) PC-US-102965

10928814_ATS_RLD_Guide_Ad_M4.indd 1 3/19/18 1:37 PM PREPARED BY FCB Releasing as: PDFx1a Production: Maureen Rodolfy Job #: 10928814 Colors: 4C Process AD: Kevin Thompson Client: BI Flat Size: AE: Ashley Massaroco Product: NINT Bleed: 11.25”w x 6.25”h Producer: Odochi Ibe Client Code: PC-US-102965 Trim: 11”w x 6”h QC: L.Powell Date: March 19, 2018 1:35 PM Safety: 10.5”w x 5.5”h Digital Artist: VA, tp, VA, tp Add’l Size Info: Proof: M4 Fonts: FR Spellcheck: M. Massey Path: PrePress:BI_P zer:NINTEDANIB:10928814:10928814_ATS_RLD_Guide_Ad_M4 4C ATS Rare Lung Guide: Branded