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Congenital Anomalies

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Congenital Anomalies 740 Anencephalus and similar anomalies 7400 Anencephalus and similar anomalies 74000 Absence of brain 74001 Acrania 74002 Anencephaly 74003 Hemlanencephaly 74008 Anencephalus - Other 7401 Craniorachischisis 7402 Iniencephaly 74020 Closed Iniencephaly 74021 Open Iniencephaly 74029 Iniencephaly - Unspecified 741 Spina bifida 7410 Spina bifida - With hydrocephalus 74100 Spina bifia aperta, any site, with hydrocephalus 74101 Spina bifida (cystica), any site, with Arnold Chiari malformation and hydrocephalus (Arnold Chiari malformation NOS) 74102 Spina bifida (cystica), any site, with stenosed aqueduct of Sylvius 74103 Spina bifida cystica, cervical, with unspecified hydrocephalus 74104 Spina bifida cystica, thoracic, with unspecified hydrocephalus 74105 Spina bifida - lumbar, with unspecified hydrocephalus 74106 Spina bifida cystica, sacral, with unspecified hydrocephalus 74107 Spina bifida of any site with hydrocephalus of late onset 74108 Spina bifida - With hydrocephalus - Other 74109 Spina bifida - With hydrocephalus - Unspecified 7419 Spina bifida - Without mention of hydrocephalus 74190 Spina bifida aperta - Without mention of hydrocephalus 74191 Spina bifida cystica, cervical - Without mention of hydrocephalus 74192 Spina bifida cystica, thoracic - Without mention of hydrocephalus 74193 Spina bifida cystica, lumbar - Without mention of hydrocephalus 74194 Spina bifida cystica, sacral - Without mention of hydrocephalus 74198 Spina bifida - Without mention of hydrocephalus - Other 74199 Spina bifida - Without mention of hydrocephalus - Unspecified 742 Other congenital anomalies of nervous system 7420 Encephalocele 74200 Encephalocele - Occipital 74208 Encephalocele - Other specified site 74209 Encephalocele - Unspecified 7421 Microcephalus 7422 Reduction deformities of brain 74220 Anomalies of cerebrum 74221 Anomalies of corpus callosum 74222 Anomalies of hypothalamus 74223 Anomalies of cerebellum 74224 Agyria and lissencephaly 74225 Microgyria 74226 Holoprosencephaly (Arhinencephaly) 74228 Other congenital anomalies of nervous system - Reduction deformities of brain - Other 74229 Reduction deformities of brain - Unspecified 7423 Congenital hydrocephalus (Exlcudes: Hydrocephalus with any condition in 7419 [7410]) 74230 Congenital hydrocephalus - Anomalies of aqueduct of Sylvius 74231 Congenital hydrocephalus - Atresia of foramina of Magendie and Luschka (Dandy-Walker syndrome) 74232 Hydranencephaly 74238 Congenital hydrocephalus - Other 74239 Congenital hydrocephalus - Unspecified 7424 Other specified anomalies of brain 74240 Enlarged brain (Megalencephaly, Macrocephaly) 74241 Porencephaly 74242 Multiple cerebral cysts 74248 Other specified anomalies of brain 7425 Other specified anomalies of spinal cord 74250 Other specified anomalies of spinal cord - Amyelia 74251 Hypoplasia and dysplasia of spinal cord (Atelomyelia, Myelodysplasia) 74252 Other specified anomalies of spinal cord - Diastematomyelia 74253 Other cauda equina anomalies 74254 Other specified anomalies of spinal cord - Hydromyelia (Hydrorhachis) 74258 Other specified anomalies of spinal cord and membranes 7428 Other specified anomalies of nervous system 74280 Jaw-winking syndrome (Marcus Gunn syndrome) 74281 Familial Dysautonomia (Riley-Day sundrome) 74288 Other specified anomalies of nervous system 7429 Unspecified anomalies of brain, spinal cord and nervous system 74290 Unspecified anomalies of brain 74291 Unspecified anomalies of spinal cord 74299 Unspecified anomalies of nervous system 743 Congenital anomalies of eye 7430 Anophthalmos (Agenesis of eye, Cryptophthalmos) 7431 Microphthalmos 7432 Buphthalmos 74320 Buphthalmos (Congenital glaucoma, Hydrophthalmos) 74321 Buphthalmos - Enlarged eye NOS 74322 Enlarged cornea (Congenital Keratoglobus, Megalocornea) 7433 Congenital cataract and lens anomalies 74330 Absence of lens (Congenital aphakia) 74331 Spherical lens (Spherophakia) 74332 Cataract 74333 Displaced lens 74334 Coloboma of lens 74339 Other and unspecified lens anomalies 7434 Coloboma and other anomalies of anterior segments 74340 Corneal opacity 74341 Other corneal anomalies 74342 Absence of iris (Aniridia) 74343 Coloboma of iris 74344 Other anomalies of iris (Polycoria, Ectopic pupil) 74345 Blue sclera 74348 Coloboma and other anomalies of anterior segments - Other (Reiger's anomaly) 74349 Coloboma and other anomalies of anterior segments - Unspecified 7435 Congenital anomalies of eye - Congenital anomalies of posterior segment 74350 Specified anomalies of vitreous humour 74351 Specified anomalies of retina (Congenital retinal aneurysm) 74352 Specified anomalies of optic disc (Coloboma of optic disc) 74353 Specified anomalies of chorold - eye malformation 74359 Eye - Congenital anomalies of posterior segment - Other and unspecified 7436 Congenital anomalies of eyelid, lacrimal system and orbit 74360 Blepharoptosis (Congenital ptosis) 74361 Eye - Ectropion 74362 Eye - Entropion 74363 Other anomalies of eyelids (Fused eyelids, Absence of cilie [eyelashes]) 74364 Absence of agenesis of lacrimal apparatus (Absence of punctum lacrimale) 74365 Stenosis or stricture of lacrimal duct 74366 Other anomalies of lacrimal apparatus 74367 Anomalies of orbit 7438 Other specified anomalies of eye 7439 Unspecified anomlies of eye 744 Congenital anomalies of ear, face and neck 7440 Anomalies of ear causing impairment of hearing 74400 Absence of stricture of auditory canal 74401 Absence of auricle (Absence of ear NOS) 74402 Anomaly of middle ear (Fusion of ossicles) 74403 Anomaly of inner ear (Congenital anomaly: Membranous labyrinth, Organ of Corti) 74409 Unspecified anomaly of ear with impairment of hearing 7441 Ear - Accessory auricle 74410 Accessory auricle (Polyotia) 74411 Preauricular appendage, tag or lobule 74412 Ear - Other appendage, tag or lobule 7442 Other specified anomalies of ear 74420 Macrotia 74421 Microtia 74422 Bat ear 74423 Other mis-shapen ear (Pointed ear) 74424 Misplaced ears (Low set ears) 74425 Absence of anomaly of Eustachian tube 74428 Other specified anomalies of ear (Darwin's tubercle) 7443 Unspecified anomalies of ear 7444 Branchial cleft, cyst or fistula; preauricular sinus 74440 Branchial cleft, sinus, fistula or cyst 74441 Preauricular sinus or cyst 74448 Other branchial cleft anomalies 7445 Webbing of neck B920 7448 Other specified anomalies of face and neck 74480 Macrostomia 74481 Microstomia 74482 Macrocheilia 74483 Microcheilia 74488 Other specified anomalies of face and neck - Other 7449 Unspecified anomalies of face and neck 74490 Congenital anomaly of neck NOS 74491 Congenital anomaly of face NOS 745 Bulbus cordis anomalies and anomalies of cardiac septal closure 7450 Common truncus 74500 Common truncus - Persistent truncus (arteriosus) 74501 Aortopulmonary window 7451 Transposition of great vessels 74510 Transposition of great vessels, complete 74511 Transposition of great vessels, incomplete (Taussig-Bing syndrome) 74512 Corrected transposition of great vessels 74518 Transposition of great vessels - Other specified 74519 Transposition of great vessels - Unspecified 7452 Tetralogy of Fallot 74520 Fallot's tetralogy 74521 Fallot's pentalogy (Fallot's tetralogy plus atrial septal defect) 7453 Common ventricle (Cor trilloculare biatriatum, Single ventricle) 7454 Ventricular septal defect 74540 Ventricular septal defect - Roger's disease 74541 Ventricular septal defect - Eisenmenger's syndrome 74542 Ventricular septal defect - Gerbode defect 74548 Other specified ventricular septal defect 74549 Unspecified ventricular septal defect 7455 Ostium secundum type atrial septal defect 74550 Nonclosure of foramen ovale NOS (Patent foramen ovale) 74551 Ostium secundum defect (ASD secundum) 74552 ASD secundum - Lutembacher's syndrome 74558 Other specified secundum atrial septal defect 74559 Unspecified secundum atrial septal defect (Auricular septal defect NOS) 7456 Endocardial cushion defects 74560 Ostium primum defects 74561 Single common atrium (Cor triloculare biventriculare) 74562 Common atrioventrucular canal-type ventricular septal defect 74563 Common atrioventricular canal 74568 Endocardial cushion defects - Other specified 74569 Únspecified endocardial cushion defect 7457 Cor biloculare 7458 Bulbus cordis anomalies and anomalies of cardiac septal closure - Other 7459 Bulbus cordis anomalies and anomalies of cardiac septal closure - Unspecified 746 Other congenital anomalies of heart 7460 Anomalies of pulmonary valve 74600 Atresia of pulmonary valve 74601 Stenosis of pulmonary valve 74602 Insufficiency of pulmonary valve 74608 Other specified anomalies of pulmonary valve 74609 Unspecified anomaly of pulmonary valve 7461 Tricuspid atresia and stenosis, congenital 7462 Ebstein's anomaly 7463 Congenital stenosis of aortic valve (Congenital aortic stenosis) 7464 Congenital insufficiency of aortic valve (Bicuspid aortic valve, Congenital aortic insufficiency) 7465 Congenital mitral stenosis 7466 Congenital mitral insufficience 7467 Hypoplastic left heart syndrome 7468 Other specified anomalies of heart 74680 Dextrocardia without situs inversus 74681 Levocardia 74682 Cor triatriatum 74683 Pulmonary infundibular stenosis 74684 Trilogy of Fallot 74685 Anomalies of pericardium 74686 Anomalies of myocardium (Congenital cardiomegaly NOS, Uhl's disease) 74687 Congenital heart block 74688 Other specified anomalies of heart 7469 Unspecified anomalies of heart 74690 Unspecified anomalies of heart valves 74691 Anomalous bands of heart 74692 Acyanotic congenital heart disease NOS 74693 Cyanotic congenital heart disease NOS
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