The 8Th Ann Mtg (2005) – International Symposium – the West Syndrome & Other Infantile Epileptic Encephalopathies
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The 8th Ann Mtg (2005) – International Symposium – The West Syndrome & Other Infantile Epileptic Encephalopathies Date April 29 – May 1, 2005 Venue The Yayoi Memorial Hall 8-1, Kawada-cho, Shinjuku-ku, Tokyo 162-8666, Japan Day 1 Friday, April 29 ☛ Day 2 ☛ Day 3 08:15-18:00 REGISTRATION 09:00 Opening Address Yukio FUKUYAMA Child Neurology Institute, Tokyo, Japan 09:10 ࠘Seizures in the Neonatal Period࠙ Chairpersons : Moshé SL (New York, USA) Watanabe K (Nagoya, Japan) 09:10-09:50 Classification of Neonatal Seizures: 1 A Fetal Neurology Perspective Mark S. SCHER Devision of Pediatric Neurology, Department of Pediatrics, Rainbow Babies and Children’s Hospital, Cleveland, OH, USA 09:50-10:20 Benign Familial and Non-Familial Neonatal Seizures 2 Perrine PLOUIN Clinical Neurophysiology Department, Hôpital Necker Enfants Malades, Paris, France Chairpersons : Nordli DR Jr (Chicago, USA) Eto Y (Tokyo, Japan) 10:20-11:00 Glut1 Deficiency: A Metabolic Model for Infantile Seizures 3 Darryl C. DE VIVO, Dong WANG, Juan M. PASCUAL The Colleen Giblin Research Laboratories for Pediatric Neurology, Neurological Institute, Columbia University Medical Center, New York, NY, USA 11:00-11:15 Clinical and Neurophysiological Manifestations of Glucose 4 Transporter-1 Deficiency Syndrome in Japan Keiko YANAGIHARA, Noriko KAMIO, Toshisaburo NAGAI, Yasuhiro SUZUKI, Hiroshi ARAI, Shihoko OHBA, Shin NABATAME, Takeshi OKINAGA, Keiichi OZONO, Minoru YAMADA, Itaru YANAGIHARA, Katsumi IMAI Research Institute and Divisionof Pediatric Neurology, Osaka Medical Center for Maternal and Child Health, Osaka, Japan Department of Pediatrics, and Allied Health Sciences, Osaka University Graduate School of Medicine, Osaka, Japan Department of Pediatric Neurology, Bobath Memorial Hospital, Osaka, Japan Chairpersons : Scher MS (Cleveland, USA) Iinuma K (Sendai, Japan) 11:15-11:45 Ohtahara Syndrome: With Special Reference to its Developmental 5 Aspects for Differentiating from the Early Myoclonic Encephalopathy Shunsuke OHTAHARA Department of Child Neurology, Okayama University Medical School, Okayama, Japan 11:45-12:15 Are Early Myoclonic Encephalopathy (EME) and the Ohtahara 6 Syndrome Independent of Each Other ? Solomon L.MOSHÉ, Aleksandra DJUKIC, Shlomo SHINNAR Department of Neurology, Neuroscience and Pediatrics, Albert Einstein Collegeof Medicine, Montefiore Medical Center, Bronx, New York, NY, USA 12:15-12:30 GENERAL DISCUSSION 7 12:30-13:30 LUNCH AND POSTER VISIT 12:40-13:20 Luncheon Seminar (1) Chairpersons : Yagi K (Shizuoka, Japan) Co-sponsored by Nikken Chemicals Co., Ltd, Japan 【Visual Sensitivity and Photosensitivity】 Kasteleijn-Nolst Trenité DGA (Utrecht, Netherlands) 13:30 【Epileptic Encephalopathies】 Chairpersons : Specchio N (Rome, Italy) Ohtahara S (Okayama, Japan) 13:30-14:05 Epileptic Encephalopathies - An Overview 8 Natalio FEJERMAN Honorary consultant. Service of Neurology. “Juan P Garrahan”Pediatric Hospital. Buenos Aires, Argentina 14:05-14:40 How Does Etiology Influence Ictal Semiology, Treatment Choice 9 and Long-Term Outcomes in Infantile Spasms and West Syndrome? Andrew L. LUX, John P. OSBORNE Department of Paediatric Neurology, British Royal Hospital for Children, Bristol, UK School for Health, University of Bath, UK Bath Unit for Research in Paediatrics, Royal United Hospital, Bath, UK ࠈ Chairpersons : Sankar R (Los Angeles, USA) Niijima S (Tokyo, Japan) ࠈࠈࠈࠈࠈ ࠈ ࠈࠈࠈࠈࠈࠈࠈࠈࠈࠈࠈ 14:40-15:00 Mutation Analysis of the ARX Gene in Patients with West 10 Syndrome Mitsuhiro KATO, Takashi SHIIHARA, Jun TOHYAMA, Noriyuki AKASAKA, Yasuhiro SUZUKI, Shinji FUJIMOTO, Kiyoshi HAYASAKA Department of Pediatrics, Yamagata University School of Medicine, Yamagata, Japan Epilepsy Center, Department of Pediatrics, Nishi-Niigata Chuo National Hospital, Niigata, Japan Division of Pediatric Neurology, Osaka Medical Center and Research Institute for Maternal and Child Health, Osaka, Japan Department of Pediatrics, Neonatalogy and Congenital Disorders, Nagoya City University Graduate School of Medical Sciences, Nagoya, Aichi, Japan 15:00-15:20 Migrating Partial Seizures in Infancy 11 PerrinePLOUIN, Olivier DULAC Clinical Neurophysiology Department, Hôpital Necker Enfants Malades, Paris, France Paediatric Neurology Department, Hôpital Necker Enfants Malades, Paris, France 15:20-15:40 Severe Epilepsy with Multiple Independent Spike Foci 12 Yasuko YAMATOGI, Shunsuke OHTAHARA Faculty of Health and Welfare Science, Okayama Prefectural University, Soja and Okayama, Japan Department of Child Neurology, Okayama University Medical School, Okayama, Japan 16:10 ࠘How to Classify ? ࠙ Chairpersons : Andermann F (Montreal, Canada) Chang K-P (Taipei, Taiwan) 16:10-16:30 Unclassified Infantile Epilepsies : Infants with Both Generalized 13 and Focal Features Douglas R. NORDLI, Jr.., Kent R. KELLEY, Linda LAUX, Joshua GOLDSTEIN, Christian M. KORFF, Laurel BUCHANAN, Pulio SILVA Children’s Memorial Epilepsy Center, Chicago, IL, USA 16:30-16:50 Diagnostic Issues of Cryptogenic or Symptomatic Generalized 14 Epilepsies Yoko OHTSUKA, Harumi YOSHINAGA, Katsuhiro KOBAYASHI, Tatsuya OGINO Department of Child Neurology, Okayama University Graduate School of Medicine and Dentistry, Okayama, Japan 16:50-17:10 Are Absences Truly Generalized Seizures? 15 Dana CRAIU, Sanda MAGUREANU Pediatric Neurology Clinic, National Reference Center Against Epilepsy, Alexandru Obregia Hospital, Bucharest, Romania ࠈࠈ Chairpersons : Lux A (Bristol, UK) Visudtibhan A (Bangkok, Thailand) 17:10-17:30 Benign Myoclonic Epilepsy: Is the Outcome so Benign? 16 Mary E. O’REGAN, Sameer M. ZUBERI Fraser of Allander Neuroscience Unit, Royal Hospital for Sick Children, Glasgow, UK 17:30-17:50 Electro-clinical Characterization of Infantile Seizures 17 Douglas R. NORDLI Jr., Christian M. KORFF Children’s Memorial Epilepsy Center, Chicago, IL, USA 17:50-18:00 ࠘General Discussion࠙ 18 18:30-22:00 WELCOME RECEPETION Venue: Restaurant “Kansui”, Rokubancho, Chiyoda-ku ☛ Day 1 ☛ Day 3 Day 2 Saturday, April 30 08:15- 18:00 REGISTRATION 08:30 ࠘Epilepsy Classification by ILAE Task Force࠙ Chairpersons : Engel J Jr (Los Angeles, USA) Seino M (Shizuoka, Japan) 08:30- 09:00 ILAE Classification of Epileptic Syndromes : Progress on Revising 19 the ILAE Classification of Seizures and Epilepsy Jerome ENGEL, Jr. Department of Neurology and Neurobiology, David Geffen School of Medicine at UCLA, Los Angeles, CA,USA 09:00- 09:30 Concepts in Classification and Their Relevance to Epilepsy 20 Anne T. BERG Department of Biology, Northern Illinois University, DeKalb, IL, USA 09:30- 10:00 Epileptic Seizures, Syndromes and Epilepsies - A Conceptual Issue 21 Masakazu SEINO National Epilepsy Center, Shizuoka Institute of Epilepsy and Neurological Disorders, Shizuoka, Japan 10:00- 10:30 The Classification of Idiopathic Generalized Epilepsies: Time for 22 Re-evaluation? Frederick ANDERMANN, Samuel F. BERKOVIC Department of Neurology and Pediatrics,McGill University; Epilepsy Service, Montreal Neurological Hospital and Institute, Montreal, Quebec, Canada Austin and Repatriation Medical Center, Epilepsy Research Institute, Melbourne, Victoria, Australia 10:30- 11:00 Basic Principles of the ILAE Syndrome Classification 23 Peter WOLF The Danish Epilepsy Centre, Dianalund, Denmark, and The National Hospitals Neurocentre, Copenhagen, Denmark 11:00- 12:00 GENERAL DISCUSSION 24 12:00- 13:05 LUNCH AND POSTER VISIT 12:15-12:55 Luncheon Seminar (2) ࠈ Chairperson: Takahashi T (Tokyo, Japan) ࠘Epilepsies in Developing Animals and Humans࠙ Solomon L. MOSHÉ ( New York, USA) 13:05 ࠘Epilepsy Prognosis in Children࠙ Chairpersons : Salonga AM (Manila, Philippines) Osawa M (Tokyo, Japan) 13:05- 13:40 The Prognosis of Childhood-Onset Epilepsy 25 Anne T. BERG Department of Biology,Northern Illinois University, DeKalb,IL, USA 13:40 ࠘Benign Infantile Seizures Complex - Part 1࠙ Chairpersons : Fejerman N (Buenos Aires, Argentina) Yamano T (Osaka, Japan) 13:40- 14:15 Benign Familial Infantile Seizures 26 Nicola SPECCHIO, Federico VIGEVANO Head of Neurology Division, Bambino Gesù Children Hospital, Rome, Italy 14:15- 14:40 Benign Partial Epilepsy in Infancy (Watanabe Syndrome) and its 27 Marginal Syndromes. Aspects from a Long-Term Follow-up Akihisa OKUMURA, Kazuyoshi WATANABE, Tamiko NEGORO, Fumio HAYAKAWA, Toru KATO, Kazuya ITOMI, Seiko ITOMI, Taketo IKUTA Department of Pediatrics, Nagoya University Graduate School of Medicine, Nagoya, Aichi, Japan Faculty of Medical Welfare,Aichi Shukutoku University, Nagakute, Aichi, Japan 14:40- 15:00 Benign Infantile Seizures in Japan : Clinical Manifestations and 28 Good Efficacy of Low Dose CBZ Keiko YANAGIHARA, Kazumasa OTANI, Katsumi IMAI, Collaborate Clinical Research Group for Pediatric Neurology, Osaka University Graduate School of Medicine Research Institute, Osaka Medical Center for Maternal and Child Health, Osaka, Japan Otani Clinic, Wakayama, Japan Department of Pediatrics, Osaka University Graduate School of Medicine, Osaka, Japan 15:00- 15:20 General Discussion 29 15:20- 15:50 INTERMISSION AND POSTER VISIT 15:50 ࠘Benign Infantile Seizures Complex - Part 2࠙ Chairpersons : Plouin P (Paris, France) Matsuishi T (Kurume, Japan) 15:50- 16:15 Benign Infantile Focal Epilepsy with Midline Spikes and Waves 30 During Sleep (BIMSE) Giuseppe CAPOVILLA Epilepsy Center, C. Poma Hospital, Mantova, Italy 16:15- 16:40 First Afebrile Seizures Associated with Non-CNS Infections 31 Comprise a Distinct Seizure Syndrome Wei-Ling LEE, Hian-Tat ONG Department of Neurology, National Neuroscience Institute, Singapore and Department of Paediatrics, National University