An unusual presentation of Urachal Tumour

Ruth Reeve & Laura Durdle Advanced Practitioner Sonographers, Portsmouth Hospitals NHS Trust Background Anatomy There are only around 350 cases of Urachal described in The urachus is the fibrous remnant or the allantois, a canal that drains the medical literature to date, accounting for 0.2% of all bladder the of the fetus along with the umbilical cord. Failure . of the inside of the urachus to be filled leaves the urachus open. Urachal cancer is a rare type of cancer arising from the urachus There are four anatomical causes: or its remnants. It is often difficult to diagnose and requires a • Cyst multidisciplinary approach. • Fistula • Diverticulum Tumours generally present late with symptoms including: • Sinus -Haematuria The urachus is also subject to -Local pain/swelling neoplasic change -UTI’s -Umbilical discharge Patients who present with early confined disease have a good prognosis. Those with advanced disease have less promising outcomes. Case Report Role of Ultrasound for Management of Patient details: 40 year old Female with no previous Indeterminate Pelvic Masses imaging Clinical history: unprovoked right shoulder pain Differentials for pelvic masses. st 1 Investigation: Shoulder x-ray Leiomyoma (Fibroid) Ovarian Fibroma

Ectopic Pregnancy Findings: The humeral head and proximal humeral shaft shows Ovarian Malignancy patchy bone texture with periosteal reaction suggesting a diffuse permeative destructive process. Malignancy suspected

2nd investigation: CT Chest/Abdomen/Pelvis with Contrast Report: Applied to the urinary bladder is a well defined 5.5 cm mass with mixed density contents and a calcified rim - Possible Colon Carcinoma Bladder Malignancy dermoid although there is a possibility of malignant potential Colonic Mass considering bone . Recommend pelvic ultrasound

3rd investigation: Pelvic Ultrasound

Why use ultrasound?

• Inexpensive • Easily available

• Non ionising radiation • Well tolerated • Colour Doppler demonstrating vascularity. Findings: 5.6cm solid heterogeneous mass seen within • Can identify need for further imaging the midline pelvis extending into the right adnexa that is not related to either ovary and is closely applied to the bladder, abutting the abdominis muscle. Wide Learning points differential for US appearances including 1)urachal The umbilical region is often missed or overlooked on tumour 2) routine abdominal scanning. Further investigations following Ultrasound Urachal tumours often appear as a midline mass with PET – Multiple bony metastatic disease mixed echogenicity and foci of increased echogenicity. A MRI – Complex pelvic mass likely urachal tumour midline location is one of the key features that can Biopsy – Metastatic high grade carcinoma most likely distinguish urachal masses from other pelvic masses. urachal given the radiological Ultrasound is a good first line investigation to exclude other findings causes of pelvic masses