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Access Plans High Risk Prescription List

This document is to help you as a broker find the most appropriate plan for your clients. It lists high-cost prescriptions whose use could potentially trigger a higher rate for Access plan members. While Access plans are guaranteed issue and all applicants are offered coverage, your clients who have a condition on this list may likely find an Affordable Care Act (ACA) plan to better suit their needs. BRAND NAME GENERIC NAME INDICATION Adempas Riociguat Pulmonary arterial hypertension (PAH) Afinitor Oncology - breast cancer, neuroendocrine tumors of gastrointestinal, lung or pancreatic origin, advanced renal cell , astrocytoma Alecensa Alectinib Oncology - small cell lung cancer Alunbrig Brigatinib Oncology - small cell lung cancer Ampyra Dalfampridine ER tablets Aralast NP Alpha-1-Proteinase Alpha-1 antitrypsin deficiency Inhibitor Atripla Efavirenz/ Human immunodeficiency virus (HIV) Emtricitabine/ Tenofovir Aubagio Multiple sclerosis Austedo Deutetrabenazine Huntington's disease Avonex Beta-1a Multiple sclerosis Avonex Pen Interferon Beta-1a Multiple sclerosis Benlysta Systemic lupus erthematosus (SLE) Betaseron Interferon beta - 1b Multiple sclerosis Bosulif Bosutinib oncology - chronic myelogenous leukemia (CML) Braftovi Encorafenib oncology - melanoma Buphenyl Sodium Urea cycle disorders Phenylbutyrate Cabometyx Cabozantinib Oncology - thyroid, and cancer Calquence Acalabrutinib Oncology - lymphoma Capecitabine Generic Xeloda Oncology - breast, colon and rectal Cancer Cayston Aztreonam Cystic fibrosis Cerdelga Eliglustat Gaucher disease Cimzia Prefilled Ankylosing spondylitis, Crohn's, psoriatic arthritis, (injection) rheumatoid arthritis Cimzia Starter Kit Certolizumab Pegol Ankylosing spondylitis, Crohn's, psoriatic arthritis, (injection) rheumatoid arthritis Cometriq Cabozantinib Oncology - thyroid, kidney and liver cancer Complera Emtricitabine/ Human immunodeficiency virus (HIV) Rilpivirine/ Tenofovir Disoproxil Fumarate tablets Copaxone Glatiramer Multiple sclerosis Cosentyx Secuklinumab Ankylosing spondylitis, psoriatic arthritis (injection) Cotellic Cobimetinib Oncology - melanoma Dupixent Dupilumab Asthma, eczema Enbrel Psoriatic arthritis, rheumatoid arthritis

© 2019 by Blue Cross of Idaho, an independent licensee of the Blue Cross and Blue Shield Association Access Plans High Risk Prescription List

Enbrel Sureclick Etanercept Rheumatoid arthritis Epclusa Sofosbuvir and Hepatitis C Velpatasir Erivedge Vismodegib Oncology - metastatic basal cell carcinoma (BCC) Erleada Apalutamide Oncology - prostate cancer Esbriet Idiopathic pulmonary fibrosis (IPF) Extavia Interferon Beta - 1b Multiple sclerosis Fasenra Benralizumab Asthma Firazyr Icatibant - Hereditary andioedema (HAE) subcutaneous (SC) injection FORTEO Teriparatide Bone fractures Gammagard S/D Less IgA Immune Globulin Immune system disorders Genotropin Somatropin Growth hormone Gilenya Multiple sclerosis Hydrochloride - oral Gilotrif Afatinib Oncology - metastatic non-small cell lung cancer Glatiramer Glatiramer Multiple sclerosis Glatopa Glatopa Multiple sclerosis Gleevec Imatinib Oncology - leukemias, myelodysplastic syndromes Haegarda Human C1- Esterase Hereditary andioedema (HAE) inhibitor Harvoni Sofosbuvir/Ledipasvir Hepatitis C Humate-P Antihemophilic Factor Hemophilia A Humatrope Somatropin Growth hormone Humira Ankylosing spondylitis, Crohn's, psoriatic arthritis, ulcerative colitis Humira Pen Adalimumab Ankylosing spondylitis, Crohn's, psoriatic arthritis, ulcerative colitis Humira Pen Adalimumab Ankylosing spondylitis, Crohn's, psoriatic arthritis, ulcerative colitis Ibrance Palbociclib Oncology - metastatic breast cancer Iclusig Ponatinib Oncology - chronic myelogenous leukemia (CML), acute lymphoblastic leukemia (ALL) Ilaris Monoclonal Autoinflammatory syndromes, Crohn's disease, rheumatoid arthritis Imatinib mesylate Imatinib mesylate Oncology - leukemias, myelodysplastic syndromes Ingrezza Valbenazine Tardive dyskinesia Invega Trinza Paliperidone Schizophrenia (given as injection every 3 months) Jadenu Deferasirox Transfusional iron overload, non transfusion-dependent thalassemia Jakafi Ruxolitinib Myelofibrosis, polycythemia vera Jynarque Tolvaptan Treat low sodium levels in blood Keveyis Dichlorphenamide Periodic paralysis (muscle weakness) Kevzara Sarilumab Rheumatoid arthritis Kineret Rheumatoid arthritis

© 2019 by Blue Cross of Idaho, an independent licensee of the Blue Cross and Blue Shield Association Access Plans High Risk Prescription List

Kisqali Ribociclib Oncology - breast cancer Kuvan Sapropterin Phenylketonuria (PKU) Lenvima Lenvatinib Oncology - endometrial, kidney, liver, thyroid cancer Lenvima Lenvatinib Oncology - thyroid, kidney cancer Letairis Ambrisentan Pulmonary arterial hypertension (PAH) Lonsurf Trifluridine Oncology - colon, rectal and stomach cancer Lupron Depot Leuprolide Oncology - prostate cancer, endometriosis, fibroids Lynparza Olaparib Oncology - ovarian cancer Mavyret Glecaprevir, Hepatitis C Pibrentasvir Mekinist Trametinib Oncology - melanoma, leukemia, breast, lung and renal cancers Mektovi Binimetinib Oncology - melanoma Nerlynx Neratinib Oncology - breast cancer Neulasta Pegfilgrastim Prevention of -induced NexAVAR Sorafenib Oncology - liver, kidney and thyroid cancer Ninlaro Oncology - Norditropin FlexPro Somatropin Growth hormone Nucala Asthma Nutropin AQ NuSpin 20 Somatropin Growth hormone Ocaliva Obeticholic Acid Primary biliary cholangitis, cirrhosis Odomzo Sonidegib Oncology - basal cell carcinoma Ominitrope Somatropin Growth hormone Opsumit Macitentan Pulmonary arterial hypertension (PAH) Orencia Psoriatic arthritis, rheumatoid arthritis, ulcerative colitis Orencia ClickJect Abatacept Psoriatic arthritis, rheumatoid arthritis Orkambi Lumacaftor or Cystic fibrosis Ivacaftor Otezla placque psoriasis, psoriatic arthritis Palynziq Pegvaliase PKU - phenylketonuria Phenoxybenzamine HCl Phenoxybenzamine Pheochromocytoma Pomalyst Oncology - multiple myeloma Pulmozyme Dornase Alfa Cystic fibrosis Rebif Interferon Beta-1a Multiple sclerosis Rebif Rebidose Interferon Beta - 1a Multiple sclerosis Remicade Ankylosing spondylitis, arthritis, Crohn's, plaque psoriasis, ulcerative colitis Renflexis Infliximab Ankylosing spondylitis, arthritis, Crohn's, plaque psoriasis, ulcerative colitis Revatio Sildenafil Pulmonary arterial hypertension (PAH) Revlimid Oncology - multiple myeloma, , myelodysplatic syndomes Reyataz Atazanavir Human immunodeficiency virus (HIV) Rubraca Rucaparib Oncology - ovarian cancer Saizen Click.Easy Somatropin Growth hormone Saizenprep Somatropin Growth hormone SandIMMUNE Cyclosporine Prevent rejection of transplanted organ/tissue

© 2019 by Blue Cross of Idaho, an independent licensee of the Blue Cross and Blue Shield Association Access Plans High Risk Prescription List

Siliq Brodalumab Psoriasis Simponi Ankylosing spondylitis, psoriatic arthritis, rhematoid arthritis, ulcerative colitis Somatuline Depot Lanreotide Acromegaly, carcinoid syndrome, neuroendocrine tumors Somavert Pegvisomant Acromegaly Sovaldi Sofosbuvir Hepatitis C Sprycel Dasatinib Oncology - chronic myeloid leukemia (CML), acute lymphoblastic leukemia (ALL) Stelara Plaque psoriasis and psoriatic arthritis, Crohn's disease Strensiq Asfotase Alfa Hypophosphatasia (HPP) Sucraid Sacrosidase Congenital sucrase-isomalase deficiency (CSID) Sutent Sunitinib Oncology - digestive GIST tumors, kidney cancer, neuroendocrine tumors Symdeko Tezacaftor/Ivacaftor Cystic fibrosis SymlinPen 120 Pramlintide Diabetes (Type 1 and Type 2) Tadalafil (PAH) Tadalafil Pulmonary arterial hypertension (PAH) Tafinlar Dabrafenib Oncology - melanoma, Tagrisso Osimertinib Oncology - non-small cell lung cancer Taltz Ixekizumab Ankylosing spondylitis, psoriasis, psoriatic arthritis Tarceva Erlotinib Oncology - non-small cell lung cancer, pancreatic cancer Tecfidera Multiple sclerosis Temozolomide Temozolomide Oncology - brain cancer Tetrabenazine Tetrabenazine Huntington's disease Thalomid Multiple myeloma Tracleer Bosentan Pulmonary hypertension Tremfya Guselkumab Plaque psoriasis Tykerb Lapatinib Oncology - breast cancer Tysabri Multiple sclerosis Tyvaso Starter Treprostinil Pulmonary arterial hypertension (PAH) Uptravi Selexipag Pulmonary arterial hypertension (PAH) Vemlidy Tenofovir Hepatitis B Alafenamide Venclexta Venetoclax Oncology - chronic lymphocytic leukemia, small lymphoctic lymphoma, acute myelogenous leukemia Verzenio Abemaciclib Oncology - breast cancer Vigabatrin Vigabatrin Epilepsy Vosevi Sofosbuvir, Hepatitis C Velpatasvir, Voxilaprvir Votrient Pazopanib Oncology - renal cancer, soft tissue sarcoma Xalkori Crizotnib Oncology - non-small cell lung cancer Xeljanz Psoriatic arthritis, rheumatoid arthritis, ulcerative colitis Xeljanz XR Tofacitinib Psoriatic arthritis, rheumatoid arthritis Xenazine Tetrabenazine Huntington's disease Xiaflex Collagenase Dupuytren's contracture Xolair Asthma, allergic, chronic hives

© 2019 by Blue Cross of Idaho, an independent licensee of the Blue Cross and Blue Shield Association Access Plans High Risk Prescription List

Xtandi Enzalutamide Oncology - prostate cancer, metastatic Xyrem Sodium Oxybate Narcolepsy Zegerid Omeprazole/ Erosive esophagitis, duodenal ulcers, gastric, GERD Sodium Bicarbonate Zejula Niraparib Oncology - ovarian cancer, fallopian tube cancer, peritoneal cancer Zelboraf Vemurafenib Oncology - melanoma Zepatier Elbasvir, Grazoprevir Hepatitis C Zileuton ER Zileuton Asthma

© 2019 by Blue Cross of Idaho, an independent licensee of the Blue Cross and Blue Shield Association