Q80 Congenital Excludes1: Refsum's disease (G60.1) Q80.0 Q80.1 X-linked ichthyosis Q80.2 Collodion baby Q80.3 Congenital bullous ichthyosiform erythroderma Q80.4 Harlequin fetus Q80.8 Other congenital ichthyosis Q80.9 Congenital ichthyosis, unspecified Q81 Q81.0 Epidermolysis bullosa simplex Excludes1: Cockayne's syndrome (Q87.1) Q81.1 Epidermolysis bullosa letalis Herlitz' syndrome Q81.2 Epidermolysis bullosa dystrophica Q81.8 Other epidermolysis bullosa Q81.9 Epidermolysis bullosa, unspecified

Q82 Other congenital malformations of Excludes1: acrodermatitis enteropathica (E83.2) congenital erythropoietic porphyria (E80.0) pilonidal cyst or sinus (L05.-) Sturge-Weber (-Dimitri) syndrome (Q85.8) Q82.0 Hereditary Q82.1 Q82.2 Excludes1: malignant mastocytosis (C96.2) Q82.3 Q82.4 (anhidrotic) Excludes1: Ellis-van Creveld syndrome (Q77.6) Q82.5 Congenital non-neoplastic NOS Flammeus Nevus Portwine Nevus Strawberry Angioma Sanguineous Nevus Strawberry Nevus Vascular Nevus NOS Verrucous Nevus Excludes2: Café au lait spots (L81.3) lentigo (L81.4) nevus NOS (D22.-) araneus nevus (I78.1) (D22.-) pigmented nevus (D22.-) spider nevus (I78.1) stellar nevus (I78.1) Q82.8 Other specified congenital malformations of skin Abnormal palmar creases Accessory skin tags Benign familial pemphigus [Hailey-Hailey] Congenital poikiloderma (hyperelastica) Dermatoglyphic anomalies Inherited keratosis palmaris et plantaris Keratosis follicularis [Darier-White] Excludes1: Ehlers-Danlos syndrome (Q79.6) Q82.9 Congenital malformation of skin, unspecified

The diagnoses that follow are all coded Q82.8

Applicable To • Abnormal palmar creases • Accessory skin tags • Benign familial pemphigus [Hailey-Hailey] • Congenital poikiloderma • Cutis laxa (hyperelastica) • Dermatoglyphic anomalies • Inherited keratosis palmaris et plantaris • Keratosis follicularis [Darier-White] • Description Synonyms • Abnl palmar creases • Abnormal dermatoglyphic pattern • Accessory skin tag, congenital • Acrokeratosis verruciformis • Acrokeratosis verruciforms • Anomaly of skin pigment, congenital • Aplasia cutis • • • Congenital accessory skin tag • Congenital anomaly of skin pigment • Congenital • Congenital • Congenital pigmentary skin anomalies • Congenital scar • Congenital skin contracture • Darier disease • Dariers disease • Familial benign pemphigus • Goltz Gorlin syndrome • Goltz syndrome • Goltz-Gorlin (dermal hypoplasia) syndrome • Hailey disease • Hailey Hailey disease • Hereditary benign acanthosis nigricans • Howel Evans syndrome • Howel-Evans' syndrome • Keratoderma, congenital • Keratosis follicularis • Keratosis pilaris, congenital • • Mongolian spot (blue/gray skin discoloration) • • Porokeratosis () • Porokeratosis of Mibelli • • Scar, congenital