American Academy of Ophthalmic Executives® Neuro-Ophthalmology ICD-10-CM Quick Reference Guide Effective Oct. 1, 2020 Disorders of the Nervous System TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Amaurosis fugax X X X G45.3 X Arnold-chiari malformation X X X G93.5 X Benign intracranial hypertension X X X G93.2 X Blepharospasm X X X G24.5 X Clonic hemifacial spasm G51.31 G51.32 G51.33 X G51.39 Horner’s Syndrome X X X G90.2 X Multiple sclerosis X X X G35 X Myasthenia gravis with (acute) exacerbation X X X G70.01 X Myasthenia gravis without (acute) X X X G70.00 X exacerbation Ophthalmoplegic migraine, intractable X X X G43.B1 X Ophthalmoplegic migraine, not intractable X X X G43.B0 X Transient cerebral ischemic attack, X X X G45.9 X unspecified (eg. TIA) Disorders of Optic Nerve & Visual Pathways TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Cortical blindness H47.611 H47.612 X X H47.619 Disorders of optic chiasm X X X H47.49 X Disorders of optic chiasm associated with X X X H47.41 X inflammatory disorders Disorders of optic chiasm associated with X X X H47.42 X other neoplasms Disorders of optic chiasm associated with X X X H47.43 X vascular disorders Drusen of optic nerve H47.321 H47.322 H47.323 X H47.329 Glaucomatous optic atrophy H47.231 H47.232 H47.233 X H47.239 Hereditary optic atrophy X X X H47.22 X Ischemic optic neuropathy H47.011 H47.012 H47.013 X H47.019 Page 1 of 5 © American Academy of Ophthalmology Neuro-Ophthalmology ICD-10-CM Quick Reference Guide Effective Oct. 1, 2020 Disorders of Optic Nerve & Visual Pathways (cont.) TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Nutritional optic neuropathy X X X H46.2 X Optic papillitis H46.01 H46.02 H46.03 X H46.00 Other disorders of optic nerve, NOC (eg. H47.091 H47.092 H4.093 X H47.099 compression of optic nerve) Other optic neuritis X X X H46.8 X Primary optic atrophy H47.211 H47.212 H47.213 X H47.219 Pseudopapilledema of optic disc H47.331 H47.332 H47.333 X H47.339 Retrobulbar neuritis H46.11 H46.12 H46.13 X H46.10 Toxic optic neuropathy X X X H46.3 X Unspecified optic atrophy X X X H47.20 X Unspecified optic neuritis X X X H46.9 X Unspecified papilledema X X X H47.10 X Miscellaneous TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Anisocoria X X X H57.02 X Benign neoplasm of cerebral meninges X X X D32.0 X Benign neoplasm of pituitary gland X X X D35.2 X Benign neoplasm of unspecified site of orbit D31.61 D31.62 X X D31.60 Cerebral infarction, unspecified (eg. Stroke) X X X I63.9 X Convergence insufficiency X X X H51.11 X Conversion disorder with sensory symptom or X X X F44.6 X deficit Elevated erythrocyte sedimentation rate X X X R70.0 X Focal chorioretinal inflammation, H30.011 H30.012 H30.013 X H30.019 juxtapapillary Granuloma of orbit (eg. Pseudotumor H05.111 H05.112 H05.113 X H05.119 (inflammatory) of orbit) Headache with orthostatic component, not X X X R51.0 X elsewhere classified Headache, unspecified X X X R51.9 X Internuclear ophthalmoplegia H51.21 H51.22 H51.23 X H51.20 Malignant neoplasm of orbit C69.61 C69.62 X X C69.60 Mydriasis X X X H57.04 X Nonpyogenic thrombosis of intracranial X X X I67.6 X venous system Italicized codes = new codes as of Oct. 1, 2020 Page 2 of 5 © American Academy of Ophthalmology Neuro-Ophthalmology ICD-10-CM Quick Reference Guide Effective Oct. 1, 2020 Miscellaneous (cont.) TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Ocular pain H57.11 H57.12 H57.13 X H57.10 Other giant cell arteritis X X X M31.6 X Other specified disorders of binocular X X X H51.8 X movement (eg. Skew deviation) Other specified disorders of eye and adnexa X X X H57.89 X Palsy (spasm) of conjugate gaze, Bell's Palsy X X X G51.0 X Parkinson’s disease X X X G20 X Partial retinal atery occlusion (eg. H34.211 H34.212 H34.213 X H34.219 Hollenhorst’s plaque) Progressive external ophthalmoplegia H49.41 H49.42 H49.43 X H49.40 Postconcussion syndrome X X X F08.71 X Thyrotoxicosis with diffuse goiter with thyrotoxic crisis or storm (eg. Graves’ Disease, X X X E05.01 X Exophthalmic or toxic goiter NOS) Thyrotoxicosis with diffuse goiter without thyrotoxic crisis or storm (eg. Graves’ Disease, X X X E05.00 X Exophthalmic or toxic goiter NOS) Tonic pupil H57.051 H57.052 H57.053 X H57.059 Transient cerebral ischemic attack, X X G45.9 X X unspecified (eg. TIA) Visual hallucination agnosia X X X R48.3 X Nystagmus TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Congenital X X X H55.01 X Deficiency of Saccades X X X H55.81 X Dissociated X X X H55.04 X Latent X X X H55.02 X Other forms of Nystagmus X X X H55.09 X Other irregular eye movements X X X H55.89 X Page 3 of 5 © American Academy of Ophthalmology Neuro-Ophthalmology ICD-10-CM Quick Reference Guide Effective Oct. 1, 2020 Other Strabismus TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Degenerative myopia with choroidal H44.2A1 H44.2A2 H44.2A3 X H44.2A9 neovascularization Degenerative myopia with macular hole H44.2B1 H44.2B2 H44.2B3 X H44.2B9 Degenerative myopia with retinal H44.2C1 H44.2C2 H44.2C3 X H44.2C9 detachment Degenerative myopia with foveoschisis H44.2D1 H44.2D2 H44.2D3 X H44.2D9 Degenerative myopia with other H44.2E1 H44.2E2 H44.2E3 X H44.2E9 maculopathy Palsies TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Third ocular motor nerve H49.01 H49.02 H49.03 X H49.00 Fourth ocular motor nerve H49.11 H49.12 H49.13 X H49.10 Sixth ocular motor nerve H49.21 H49.22 H49.23 X H49.20 Ptosis TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Congenital X X X Q10.0 X Mechanical H02.411 H02.412 H02.413 X H02.419 Myogenic H02.421 H02.422 H02.423 X H02.429 Paralytic H02.431 H02.432 H02.433 X H02.439 Vertigo TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Dizziness (vertigo, NOS) X X X R42 X Benign paroxysmal H81.11 H81.12 H81.13 X H81.09 Other peripheral H81.391 H81.392 H81.393 X H81.399 Page 4 of 5 © American Academy of Ophthalmology Neuro-Ophthalmology ICD-10-CM Quick Reference Guide Effective Oct. 1, 2020 Visual Disturbances TYPE RT LT BOTH SINGLE CODE UNSPECIFIED Amblyopia refractive H53.021 H53.022 H53.023 X H53.029 Amblyopia strabsimic H53.031 H53.032 H53.033 X H53.039 Aquired color vision deficiency X X X H53.52 X Diplopia X X X H53.2 X Heteronymous bilateral field defects X X X H53.47 X Homonymous bilateral field defects H53.461 H53.462 X X H53.469 Other subjective visual disturbances (eg. X X X H53.19 X visual halos) Scotoma of blind spot H53.421 H53.422 H53.423 X H53.429 Transient visual loss (eg. scintillating H53.121 H53.122 H53.123 X H53.129 scotoma) Unspecified visual field defects X X X H53.40 X Disclaimer and Limitation of Liability: All information provided by the American Academy of Ophthalmology, its employees, agents, or representatives participating in the Academy’s coding service is as current and reliable as reasonably possible. The Academy does not provide legal or accounting services or advice. You should seek legal and/ or accounting advice if appropriate to your situation. Coding is a complicated process involving continually changing rules and the application of judgment to factual situations. The Academy does not guarantee or warrant that either public or private payers will agree with the Academy’s information or recommendations. 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