American Thoracic Society International Conference

Where today’s science meets tomorrow’s careTM Rare Disease Guide

May 13-May 18, 2016 San Francisco, California conference.thoracic.org May 2016 Dear Colleagues: The scope of the American Thoracic Society is amazingly broad – covering pulmonary, critical care, and sleep medicine. Our challenge as we put the International Conference program together is that some clinical topics that may be of central importance to our members, conference attendees and patients may not be prominently featured in the program each year. This is the case with some of rare lung diseases. With each challenge though, comes opportunity. Because of the wealth of scientific and clinical information presented at ATS 2016, these diseases, though uncommon, will be the focus of many presentations over the next several days. The purpose of this Rare Lung Disease Guide is to help you more easily find these presentations. Zea Borok, MD In his chapter on rare lung diseases in “Breathing in America: Diseases, Progress, and Hope” (2010) Francis X. McCormack, MD noted that research on uncommon University of respiratory diseases has produced some of the most exciting discoveries in pulmonary medicine. “Insights gained from uncommon lung diseases often shed light on Southern California, the more common ones.” Los Angeles The definition of a rare disease by its prevalence varies by country. In the European Union, for instance, it is defined as a disease that affects fewer than 1 in 2,000 while in the United States it is a disease that affects fewer than 1 in 200,000. This guide was compiled by a small group of ATS Members who studied the ATS 2016 ATS 2016 abstracts – authors requested to be considered for inclusion. Many thanks to Dr. Frank McCormack, Dr. Lisa Young, Dr. Jonathan Kropski, Dr. Nishant Gupta and Mr. International Jack Kelly for their assistance with compiling this resource. Conference Chair There are a number of patient advocacy groups that are exhibiting at ATS 2016. In addition to attending the presentations noted within, I encourage you to visit with them to learn more about these rare conditions. Groups listed in BOLD are members of the ATS Public Advisory Roundtable and can all be found in PAR ROW, near the ATS Center in the Exhibit Hall. Learn more about this group and its many contributions to the Society and its work, here: http://www.thoracic.org/patients/par/. Alpha-1 Foundation – Booth 1028 NTM Info & Research, Inc. – Booth 1027 ARDS Foundation – Booth 506 Primary Ciliary Dyskinesia Foundation – Booth 1030 Children’s Interstitial Lung Disease Foundation (CHILD) – Booth 993 Foundation – Booth 2111 Foundation for Research – Booth 1026 Association – Booth 1128 The LAM Foundation – Booth 1032 Rare Lung Diseases Consortium – Booth 1343 Lung Transplant Foundation – Booth 927 Relapsing Polychondritis Awareness and Support Foundation, Inc. – Booth 1843 Lymphangiomatosis and Gorham’s Disease Alliance – Booth 1126 Scleroderma Foundation – Booth 1029 Sincerely,

Zea Borok, MD Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Acute Chest Syndrome in Patient with HB SE Sickle Cell Crisis Sunday, P572 9:00 am-4:15 pm; Use of V-V ECMO as a Novel Therapy for Severe Acute Chest Syndrome A54: Critical Care Case Reports: Acute Hypoxemic Area E, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm with Diffuse Alveolar Hemorrhage /ARDS Lower Level), Moscone Center

120 9:00 am-11:00 am; Acute Fibrinous and Organizing : A Newly Recognized, A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, Poster Viewing 9:00-9:45 am; but Poorly Understood Disease Lower Level), Moscone Center Poster Discussion 9:45-11:00 am

Alpha-1 Antitrypsin Deficiency Sunday, P1240 9:00 am-4:15 pm; Cardiovascular Risk and Lung Disease Severity in Alpha 1 Antitrypsin A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Deficiency Lower Level), Moscone Center

P1241 9:00 am-4:15 pm; Prevalence and Nature of Liver Involvement in Patients with PiZZ- A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Emphysema, Candidates for Lung Transplantation Lower Level), Moscone Center

P1242 9:00 am-4:15 pm; The Effect of Alpha-1 Proteinase Inhibitor (A1-PI) Therapy on Changes in A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Regional Lung Density: A Post-Hoc Analysis of the RAPID Trial Lower Level), Moscone Center

P1243 9:00 am-4:15 pm; The Relationship Between Changes in CT-Measured Lung Density and A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lung Volume in Severe Alpha-1 Antitrypsin Deficiency: Post-Hoc Analysis Lower Level), Moscone Center of the RAPID Trial P1244 9:00 am-4:15 pm; Rate of FEV1 Decline in Never-Smoking Alpha-1 Antitrypsin Deficiency A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Patients with and Without Small Airways Disease Lower Level), Moscone Center

P1245 9:00 am-4:15 pm; Health Status in Never-Smoking Alpha-1 Antitrypsin Deficiency Patients A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm With and Without Airflow Obstruction Lower Level), Moscone Center

P1247 9:00 am-4:15 pm; Serum Proteins Associated with Radiographic Emphysema and Its A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Progression in Severe Alpha-1 Antitrypsin Deficiency Lower Level), Moscone Center

P1248 9:00 am-4:15 pm; Serum Desmosine, Isodesmosine and Emphysema in Spirometrically Mild A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm PiZZ Alpha-1 Antitrypsin Deficiency Lower Level), Moscone Center P1249 9:00 am-4:15 pm; Impact of Augmentation Treatment in Alpha-1 Deficiency Patients on Lung A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Transplantation Result Lower Level), Moscone Center P1250 9:00 am-4:15 pm; Liver Fibrosis in Alpha 1 Antitrypsin Deficiency-Related Lung Disease A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center 1 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P1251 9:00 am-4:15 pm; Osteoporosis and Osteopenia in COPD Alpha-1 Antitrypsin Deficiency A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1252 9:00 am-4:15 pm; Demographics and Clinical Profile of Patients with Alpha-1 Antitrypsin A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Deficiency PiMS Genotype Started on Augmentation Therapy Lower Level), Moscone Center P1253 9:00 am-4:15 pm; Improving Survival Among ZZ Patients in the AlphaNet Program A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1254 9:00 am-4:15 pm; Differences Between ZZ and SZ Patients in the AlphaNet Program A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1255 9:00 am-4:15 pm; Gender Differences in Alpha-1-Antitrypsin Deficiency A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1256 9:00 am-4:15 pm; Rare Alpha-1 Antitrypsin Mutations Detected in Ireland A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1257 9:00 am-4:15 pm; The Irish Alpha-1 Antitrypsin Deficiency National Targeted Detection A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Programme Lower Level), Moscone Center P1258 9:00 am-4:15 pm; Alpha-1 Antitrypsin Deficiency in Romania - First Steps (Results of First A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Three Years of Screening) Lower Level), Moscone Center P1259 9:00 am-4:15 pm; Alpha-1 Antitrypsin Level Increase During an Inflammatory State: A A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Potential Cause of Missed Diagnosis in Alpha-1 Antitrypsin Deficiency Lower Level), Moscone Center P1260 9:00 am-4:15 pm; Alpha-1 Antitrypsin Deficiency - Do We Really Understand It? Case A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Presentations Lower Level), Moscone Center P1263 9:00 am-4:15 pm; Impact of AATD Patient Management Program on Health-Related A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Outcomes and Costs Lower Level), Moscone Center P1264 9:00 am-4:15 pm; Evaluation of Strategies for Comprehensive Diagnostic Testing for A1- A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Antitrypsin Deficiency that Include Quantitative Isoelectric Focusing and Lower Level), Moscone Center DNA Sequencing P1265 9:00 am-4:15 pm; The Elephant in the Room A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1266 9:00 am-4:15 pm; Generating a Novel Model of Alpha-1 Antitrypsin Deficiency Pathogenesis A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm by Deriving Type II Alveolar Cells from Pluripotent Stem Cells Lower Level), Moscone Center

2 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P1268 9:00 am-4:15 pm; Effects of Recombinant Alpha1-Antitrypsin IgG1 Fc-Fusion Protein (AAT-Fc) A43: Alpha-1-Antitrypsin Deficiency Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm in Experimental Emphysema Lower Level), Moscone Center P247 9:00 am-4:15 pm; A Web-Based Approach for Awareness and Management of Alpha1- A58: Epidemiology Of COPD And Lung Cancer Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Antitryspin Deficiency Lower Level), Moscone Center 309 2:15 pm-4:15 pm; Alpha-1 Clinical Demographics and Outcomes: Data from the Alpha-1 A102: Highlights In Patient-Centered Research: Methods Room 309 (South Building, Poster Viewing 2:15-3:00 pm; Therapy, Evaluation and Research (AL1TER) Patient Registry Program And Outcomes Esplanade Level), Moscone Poster Discussion 3:00-4:15 pm Center Monday, P140 9:00 am-4:15 pm; Overview of Multicenter Genomic Research in Alpha-1 Antitrypsin B31: Alpha-1 Antitrypsin Deficiency Area B, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Deficiency and Sarcoidosis (GRADS) and Biorepository Lower Level), Moscone Center P164 9:00 am-4:15 pm; Alveolar Macrophage-Mediated Efferocytosis in Alpha-1 Antitrypsin B32: Alveolar Macrophage Biology Area B, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Deficiency Lower Level), Moscone Center P1242 9:00 am-4:15 pm; Resolution of Sequential Mycobacterial Infections Associated with Alpha-1- B49: Non-Tuberculous Mycobacterial Disease And Case Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Antiprotease Therapy Reports Lower Level), Moscone Center P1017 9:00 am-4:15 pm; miR-199a-5p, miR-598 and miR-320a Are Regulated by NF?B and B59: Novel Genes And Gene Effects In Copd Area H, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Decreased in Monocytes of ZZ Individuals Receiving Alpha-1 Antitrypsin Lower Level), Moscone Center Augmentation Therapy P1007 9:00 am-4:15 pm; Molecular Characterization of Novel Rare Variants of SERPINA1 Gene in B59: Novel Genes And Gene Effects In COPD Area H, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Alpha-1 Antitrypsin Deficiency Patients from Spain Lower Level), Moscone Center 107 2:15 pm-4:15 pm; Rare SERPINA1 Variants in the Multi-Ethnic SPIROMICS Population B105: COPD: Epidemiology And Genetics Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm Tuesday, P635 9:00 am-4:15 pm; Exercise and Pulmonary Rehabilitation Participation Among Patients with C59: Topics On Self-Management And Supportive Care Area F, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Alpha-1 Antitrypsin Deficiency Across The Spectrum Of Chronic Respiratory Conditions Lower Level), Moscone Center P1295 9:00 am-4:15 pm; Alpha-1 Antitrypsin Decreases Pro-Inflammatory Monocyte-Endothelial C68: Immune Cell Interactions In COPD Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Cells Interactions Via Fractalkine Axis Lower Level), Moscone Center P1314 9:00 am-4:15 pm; In Vivo Imaging of Polymers in Alpha-1 Antitrypsin Deficiency C69: Here’s Looking At You: Imaging Studies In COPD Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center 522 2:15 pm-4:15 pm; Macrophages from Patients with Z Mutation in Antitrypsin Have Increased C107: Immunity, Exacerbation And Immune Cell Function Room 2014 (West Building, Poster Viewing 2:15-3:00 pm; Proteolytic Activity on Extracellular Matrix Through Matriptase-MMP-14 In COPD Level 2), Moscone Center Poster Discussion 3:00-4:15 pm

3 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Amyloidosis Sunday, P702 9:00 am-4:15 pm; Pulmonary AA Amyloidosis Presenting as Interstitial Infiltrates in A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Rheumatoid Arthritis Lower Level), Moscone Center P1457 9:00 am-4:15 pm; An Unusual Case of Severe Pulmonary Hypertension Due to Pulmonary A67: Case Reports In Pulmonary Vascular Disease Area M, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Amyloidosis Along with Cardiac Amyloidosis Presenting with Atypical Lower Level), Moscone Center Features in the Same Patient Monday, P396 9:00 am-4:15 pm; Localized Tracheobronchial Amyloidosis Presenting with Massive B37: Interventional Pulmonary Medicine: Cool Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Hemoptysis in an Intubated, Critically Ill Patient Lower Level), Moscone Center P296 9:00 am-4:15 pm; Pleural Involvement in Extensive Bilateral Primary Nodular Parenchymal B38: : Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Amyloidosis: An Incidentaloma Lower Level), Moscone Center P341 9:00 am-4:15 pm; An Elderly Man with : A Case of Primary Pulmonary B40: Dyspnea: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Amyloidosis Lower Level), Moscone Center P345 9:00 am-4:15 pm; A Rare Presentation of Isolated Pulmonary Amyloidosis Mimicking B40: Dyspnea: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Malignancy Lower Level), Moscone Center Tuesday, P452 9:00 am-4:15 pm; A Rare Case of Cystic Lung Disease C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Reports Lower Level), Moscone Center P282 9:00 am-4:15 pm; Nodular Pulmonary Amyloid Presenting with Hemoptysis C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Disease: Case Reports Lower Level), Moscone Center P286 9:00 am-4:15 pm; Immunoglobulin Light Chain Amyloidosis Presenting as Supraglottic Mass, C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm , and Cystic Lung Disease Disease: Case Reports Lower Level), Moscone Center P299 9:00 am-4:15 pm; Pulmonary Amyloidosis: A Rare Presentation of a Rare Disease C43: Pulmonary Alveolar Proteinosis And Other Rare Lung Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Disease: Case Reports Lower Level), Moscone Center 116 2:15 pm-4:15 pm; Pulmonary Amyloidosis: Clinicopathologic Correlation in an Autopsy Series C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; of Amyloidosis Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm ANCA Associated Vasculitis Sunday, P701 9:00 am-4:15 pm; Zebras Have Hooves Too: A Case of Granulomatosis with Polyangiitis A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P709 9:00 am-4:15 pm; The Important of Complete Evaluation of a Patient with Recurrent Diffuse A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Alveolar Hemorrhage: A Case Study Lower Level), Moscone Center 4 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P729 9:00 am-4:15 pm; Patients with Difficult to Control Eosinophilic Granulomatosis with A39: Eosinophilic Airways Disease Area G, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Polyangiitis of a Vasculitis Clinical Center in Sao Paulo, Brazil Lower Level), Moscone Center P1234 9:00 am-4:15 pm; HLA- Genotyping and Clinical Manifestation in Patients with A42: Autoimmune Myositis, Antisynthetase, Scleroderma, Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Granulomatosis with Polyangiitis And IPAF Lower Level), Moscone Center P1278 9:00 am-4:15 pm; Case-Control Study of HLA Region in Brazilian Carriers of Granulomatosis A44: Drug Induced And Rare Lung Disease Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm with Polyangiitis (Wegener’s) Lower Level), Moscone Center P126 9:00 am-4:15 pm; Nasal Disease, a Common Comorbidity in Patients with Chronic Severe A50: : Observational Studies Area A, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Asthma (CSA) and Eosinophilic Granulomatosis with Poliangiitis (EGPA) Lower Level), Moscone Center Monday, P335 9:00 am-4:15 pm; Rare Case of ANCA Vasculitis with Alveolar Hemorrhage in Non- Hodgkin B40: Dyspnea: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lymphoma Lower Level), Moscone Center P116 9:00 am-4:15 pm; Lung Perfusion Evaluation in Patients with Stable Granulomatosis with B55: Reason To Believe: Clinical PH Studies Area A, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Polyangiitis Lower Level), Moscone Center Anti-Synthetase Associated ILD Sunday, 106 9:00 am-11:00 am; Radiological Versus Histological Diagnosis in Antisynthetase - A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, May 15, 2016 Poster Viewing 9:00-9:45 am; Associated Interstitial Lung Disease Lower Level), Moscone Center Poster Discussion 9:45-11:00 am 107 9:00 am-11:00 am; Additional Clinical Signs and Symptoms Develop in Patients with A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, Poster Viewing 9:00-9:45 am; Antisynthetase Syndrome-Associated Interstitial Lung Disease Followed Lower Level), Moscone Center Poster Discussion 9:45-11:00 am Over 24 Months P711 9:00 am-4:15 pm; Rituximab - Respiratory Rescue; Salvage Therapy in Acute Antisynthetase A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Syndrome Lower Level), Moscone Center P1222 9:00 am-4:15 pm; Mycophenolate Mofetil (MMF) as Initial Treatment in Antisynthetase A42: Autoimmune Myositis, Antisynthetase, Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Syndrome - A Case Report Scleroderma, And IPAF Lower Level), Moscone Center P1223 9:00 am-4:15 pm; Retrospective Analysis of Twelve Patients with Anti-Synthetase Syndrome - A42: Autoimmune Myositis, Antisynthetase, Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Mayo Clinic Experience Scleroderma, And IPAF Lower Level), Moscone Center P1326 9:00 am-4:15 pm; A Curious Case of Acute Respiratory Failure - Anti-Synthetase Syndrome A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1328 9:00 am-4:15 pm; Flare of Anti-Synthetase Interstitial Lung Disease with Cessation of A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Immunosuppression Lower Level), Moscone Center

5 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P1329 9:00 am-4:15 pm; Infliximab for Treatment of Anti PL-12 Antisynthetase Syndrome: A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Misdiagnosis Led to New Potential Treatment for Rare Disease Lower Level), Moscone Center Tuesday, P207 9:00 am-4:15 pm; A Retrospective Cohort Analysis of Anti-Jo Associated Lung Disease C37: Pulmonary Fibrosis Area B, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Wednesday, 9:00 am-11:00 am; Azathioprine for Antisynthetase-Associated Interstitial Lung Disease D15: New Therapies In ILD Room 306/308 (South Building, May 18, 2016 Oral Presenation 10:00 am Esplanade Level), Moscone Center Arterio-Venous Malformations Monday, P109 9:00 am-4:15 pm; Clinical Significance of Detecting Pulmonary Arterio-Venous Malformations B55: Reason To Believe: Clinical PH Studies Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm with Chest Radiographs Lower Level), Moscone Center Tuesday, P586 9:00 am-4:15 pm; Diagnosis and Management of Sporadic Pulmonary Arteriovenous C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Malformation Not Associated with Hereditary Hemorrhagic Telangiectasia Lower Level), Moscone Center Wednesday, P994 9:00 am-3:30 pm; Pulmonary Arteriovenous Malformations in Non-Hereditary Hemorrhagic D53: The Promised Land: Clinical Studies In Pulmonary Area H, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Telangiectasia Patients: A 15-Year Retrospective Study Hypertension Lower Level), Moscone Center 522 1:30 pm-3:30 pm; Recurrent Hemoptysis in a Teen Boy with a Ciliary Motility Disorder and a D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, Poster Viewing 1:30-2:15 pm; Pulmonary Vascular Malformation Occult on Contrast Enhanced CT. Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Atypical Multifocal Pulmonary Carcinoid Tumor Wednesday, 301 1:30 pm-3:30 pm; Atypical Multifocal Pulmonary Carcinoid Tumor: A Case Report of a Very D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Rare Neoplasm Esplanade Level), Moscone Center Poster Discussion 2:15-3:30 pm Behcet’s Disease Sunday, P1464 9:00 am-4:15 pm; A Case of Behcet’s Disease Presenting with Right Atrial Thrombus and A67: Case Reports In Pulmonary Vascular Disease Area M, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Bilateral Synchronous Carcinoid Tumor of the Lung Wednesday, 302 1:30 pm-3:30 pm; Bilateral Synchronous Pulmonary Carcinoid Tumors Treated with Staged D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Segmentectomy Esplanade Level), Moscone Center Poster Discussion 2:15-3:30 pm

6 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Birt-Hogg-Dube Syndrome Tuesday, P256 9:00 am-4:15 pm; Concurrent Birt-Hogg-Dube Syndrome and Sarcoidosis C41: Sarcoidosis: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center 107 2:15 pm-4:15 pm; Lung Ultrasound Has Limited Diagnostic Value in Rare Cystic Lung C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Diseases Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 108 2:15 pm-4:15 pm; HRCT Screening for Diffuse Cystic Lung Diseases in Patients Presenting C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; with Spontaneous is Cost Effective Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 111 2:15 pm-4:15 pm; Total Covering Technique for Recurrent Pneumothorax in Patients of C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Birt-Hogg-Dube Syndrome Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm Bronchial Pulmonary Carcinoid Tumor Wednesday, P552 9:00 am-3:30 pm; A 17-Year-Old Male Presenting with Recurrent from a Primary D51: Pediatric Cases II Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Pulmonary Tumor Lower Level), Moscone Center Obliterans and Cryptogenic Organizing Pneumonias Sunday, 120 9:00 am-11:00 am; Acute Fibrinous and Organizing Pneumonia: A Newly Recognized, A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, May 15, 2016 Poster Viewing 9:00-9:45 am; but Poorly Understood Disease Lower Level), Moscone Center Poster Discussion 9:45-11:00 am P1313 9:00 am-4:15 pm; Unusual Presentation of Organizing Pneumonia in Primary Sjogren’s A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Syndrome Lower Level), Moscone Center Monday, P337 9:00 am-4:15 pm; Unexplained Dyspnea in a Non-Smoker: Think Outside the Box B40: Dyspnea: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Tuesday, P336 9:00 am-4:15 pm; A Diagnostic Dilemma with Crazy Paving Pattern C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P583 9:00 am-4:15 pm; A Delayed Diagnosis of Post Infectious Bronchiolitis Obliterans Associated C62: Pediatric Cases I Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm with RSV Lower Level), Moscone Center 113 2:15 pm-4:15 pm; Organizing Pneumonia in Myelodysplastic Syndrome: A Case Series C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm

7 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P545 9:00 am-3:30 pm; Pulmonary Complications of Stevens Johnson Syndrome: A Single Center D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Experience Lower Level), Moscone Center P557 9:00 am-3:30 pm; Bronchiolitis Obliterans Organizing Pneumonia Complicating Acute D51: Pediatric Cases II Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lymphoblastic Leukemia in Children Lower Level), Moscone Center Bronchogenic Cysts Monday, P392 9:00 am-4:15 pm; An Uncommon Congenital Anomaly Mimicking Mediastinal Carcinoma B37: Interventional Pulmonary Medicine: Cool Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Castleman Disease Tuesday, P245 9:00 am-4:15 pm; Castleman Disease Associated Diffuse Parenchymal Lung Disease: A C40: Sarcoidosis: Understanding This Multi-System Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Retrospective Analysis of 21 Cases in a Tertiary Chinese Hospital Disorder Lower Level), Moscone Center Tuesday, P328 9:00 am-4:15 pm; A Rare Case of Multicentric Castleman’s Disease Without Apparent C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Mediastinal Lymphadenopathy and a Review of the Japanese Literature Lower Level), Moscone Center Chronic Beryllium Disease Monday, 421 9:00 am-11:00 am; 5-ASA Treatment in Chronic Beryllium Disease B24: Occupational Medicine Room 2010/2012 (West Building, May 16, 2016 Poster Viewing 9:00-9:45 am; Level 2), Moscone Center Poster Discussion 9:45-11:00 am 422 9:00 am-11:00 am; The Role of JAK2 in Chronic Beryllium Disease B24: Occupational Medicine Room 2010/2012 (West Building, Poster Viewing 9:00-9:45 am; Level 2), Moscone Center Poster Discussion 9:45-11:00 am Chronic Cavitary Histoplasmosis Wednesday, P767 9:00 am-3:30 pm; Cancer Is Not Always the Answer D48: Lung Infection Case Reports I: Fungal Infections Area G, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Chronic Granulomatous Disease Monday, 919 2:15 pm-4:15 pm; Dendritic Cell-Mediated Lung Injury in Response to Aspergillus in Chronic B106: Cellular/Molecular Mechanisms And Translational Room 3014 (West Building, May 16, 2016 Poster Viewing 2:15-3:00 pm; Granulomatous Disease: Protective Role of Neutrophil-Derived Reactive Aspects Of Infections Level 3), Moscone Center Poster Discussion 3:00-4:15 pm Oxygen Species Monday, P306 9:00 am-4:15 pm; Chylothorax: The Milky Truth of Cirrhosis B38: Pleural Disease: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center

8 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P340 9:00 am-4:15 pm; A Rare Case of Massive Bilateral Chylothorax B40: Dyspnea: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Congenital Central Hypoventilation Syndrome Sunday, 805 9:00 am-11:00 am; Intelligent Volume-Assured Pressured Support (iVAPS) for the Treatment of A27: Advances In Pediatric Sleep Room 3011 (West Building, May 15, 2016 Poster Viewing 9:00-9:45 am; Pediatric Congenital Central Hypoventilation Syndrome Level 3), Moscone Center Poster Discussion 9:45-11:00 am Tuesday, 9:00 am-11:00 am; Does High Altitude Cause Hypoventilation in Patients with Congenital C19: From Genes To Motor Neurons: Advances In Control Room 2001/2003 (West Building, May 17, 2016 Oral Presentation 10:15 am Central Hypoventilation Syndrome? Of Breathing Level 2), Moscone Center P574 9:00 am-4:15 pm; Children Affected by Congenital Central Hypoventilation Syndrome: C62: Pediatric Cases I Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Decannulation and Non Invasive Ventilation Lower Level), Moscone Center Congenital Diaphragmatic Hernia Wednesday, 822 9:00 am-11:00 am; Poster Nutritional Follow-Up of Congenital Diaphragmatic Hernia Survivors - The D25: Neonatal Lung Diseases: From Bench To Babies Room 3011 (West Building, May 18, 2016 Viewing 9:00-9:45 am; Poster Sydney Children’s Hospital Experience Level 3), Moscone Center Discussion 9:45-11:00 am Congenital Myotonic Dystrophy Tuesday, P592 9:00 am-4:15 pm; Poster Successful Use of Non Invasive Ventilation in a Child Affected by Congenital C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Viewing 11:00 am-12:45 pm Myotonic Dystrophy Syndrome Lower Level), Moscone Center Congenital Pulmonary Adenomatous Malformations Wednesday, 309 1:30 pm-3:30 pm; Poster Congenital Pulmonary Airway Malformation (CPAM) with Malignant D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Viewing 1:30-2:15 pm; Poster Transformation Esplanade Level), Moscone Center Discussion 2:15-3:30 pm Cystic Lung Disease in Adult Dominant Polycystic Kidney Disease Tuesday, P444 9:00 am-4:15 pm; Cystic Lung Disease in Adult Polycystic Kidney Disease C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Reports Lower Level), Moscone Center Cystic Teratoma of the Pleura Monday, P319 9:00 am-4:15 pm; Intrapleural Benign Mature Cystic Teratoma B38: Pleural Disease: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Tuesday, P53 9:00 am-4:15 pm; Benign Metastasizing Leiomyoma C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center

9 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Diaphragmatic Flutter Wednesday, 513 1:30 pm-3:30 pm; Extreme Tachypnea in a Neonate - A Case of Diaphragmatic Flutter with D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; an Interesting Genetic Outcome Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia (DIPNECH) Monday, P478 9:00 am-4:15 pm; All that Wheezes Is Not Asthma but More so if Chest CT Shows Lung B45: : Interesting Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Nodules Lower Level), Moscone Center P564 9:00 am-4:15 pm; An Unsual Cause for Multiple Pulmonary Nodules B66: Lung Cancer Screening And Nodule Evaluation Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Tuesday, P283 9:00 am-4:15 pm; Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia Presenting C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm as Usual Interstitial Pneumonia Lung Disease: Case Reports Lower Level), Moscone Center P88 9:00 am-4:15 pm; DIPNECH a Rare Cause of Obstructive Airway Disease C81: Unusual Presentations Of Lung Cancer: Case Area A, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Reports Lower Level), Moscone Center Tuesday, P334 9:00 am-4:15 pm; Is Diffuse Panbronchiolitis Ionizing Radiation Related? C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Diffuse Pulmonary Meningotheliomatosis Tuesday, P330 9:00 am-4:15 pm; Miliary Pattern and No Complaints C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Sunday, P730 9:00 am-4:15 pm; Long-Term Outcome and Prognostic Factors of Chronic Eosinophilic A39: Eosinophilic Airways Disease Area G, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Pneumonia: Fujiyama Cohort Study Lower Level), Moscone Center P1297 9:00 am-4:15 pm; Sun Damage or Lung Damage: Heliocare? (Polypodium Leucotomas)- A46: Lung Disease Due To OTC And Illicits: Case Reports Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Induced Eosinophilic Lower Level), Moscone Center Tuesday, P327 9:00 am-4:15 pm; Wheezing with Yellow Eyes: A Case of Chronic Eosinophillic Pneumonia C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P331 9:00 am-4:15 pm; Atypical Presentation of Chronic Eosinophilic Pneumonia with Concomitant C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Mycobacterium Avium Infection Lower Level), Moscone Center

10 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P350 9:00 am-4:15 pm; Chronic Eosinophilic Pneumonia Complicated by Methicillin-Resistant C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Staphylococcus Aureus Lower Level), Moscone Center Wednesday, P569 9:00 am-3:30 pm; A Rare Case of Eosinophilic Pneumonia D51: Pediatric Cases II Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P574 9:00 am-3:30 pm; Chronic Eosinophilic Pneumonia in a 15-Year-Old Girl with Persistent D51: Pediatric Cases II Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Cough Lower Level), Moscone Center Epithelioid Hemangioepithelioma Monday, P560 9:00 am-4:15 pm; A Rare and Interesting Cause of Pulmonary Nodules: A Case of B66: Lung Cancer Screening And Nodule Evaluation Area E, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Epithelioid Hemangioendothelioma Lower Level), Moscone Center Epithelioid Trophoblastic Tumor Tuesday, P55 9:00 am-4:15 pm; Metastatic Epithelioid Trophoblastic Tumor to the C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Erasmus Syndrome Tuesday, P322 9:00 am-4:15 pm; Erasmus Syndrome in a Patient Evaluated for Pulmonary Hypertension C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Erdheim-Chester Disease Tuesday, P281 9:00 am-4:15 pm; Unusual Presentation of Erdheim-Chester Disease with Hemoptysis and C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Dyspnea as the Initial Chief Complaint Lung Disease: Case Reports Lower Level), Moscone Center Extramedullary Plasmacytoma Tuesday, P49 9:00 am-4:15 pm; Solitary Extramedullary Plasmacytoma of the : A Case Report and C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Review of the Literature Lower Level), Moscone Center Familial Dysautonomia Wednesday, P516 9:00 am-3:30 pm; Respiratory Characteristics in Patients with Familial Dysautonomia D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Fibrosing Wednesday, P773 9:00 am-3:30 pm; Healing and Hardening: Focal Fibrosing Mediastinitis Due to Histoplasmosis D48: Lung Infection Case Reports I: Fungal Infections Area G, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P774 9:00 am-3:30 pm; Fibrosing Mediastinitis D48: Lung Infection Case Reports I: Fungal Infections Area G, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center 11 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Follicular Bronchiolitis in Common Variable Immunodeficiency Monday, P186 9:00 am-4:15 pm; Ground Glass Nodules and Cough in an Individual with Common Variable B34: Case Report In Immunodeficiences And Allergy Area B, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Immunodeficiency Lower Level), Moscone Center Foreign Body Granulomatosis Sunday, P1309 9:00 am-4:15 pm; Don’t Blame the Birds A46: Lung Disease Due To OTC And Illicits: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Giant Cell Interstitial Pneumonia Sunday, P1356 9:00 am-4:15 pm; Giant Cell Interstitial Pneumonitis (GIP) as a Rare Manifestation of Chronic A48: Conventional Drug Associated Lung Disease Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Nitrofurantoin Lung Toxicity Lower Level), Moscone Center Wednesday, P136 9:00 am-3:30 pm; Giant Cell Interstitial Pneumonia in a Patient with World Trade Center Dust D46: Case Reports In Environmental And Occupational Area B, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Exposure Health Lower Level), Moscone Center Good Syndrome Monday, P185 9:00 am-4:15 pm; A Japanese Patient Diagnosed Good Syndrome with Prolonged Time B34: Case Report In Immunodeficiences And Allergy Area B, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm After Thymectomy Lower Level), Moscone Center P191 9:00 am-4:15 pm; Two Tumours, Neuropathy, Infections B34: Case Report In Immunodeficiences And Allergy Area B, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Granular Cell Tumor Tuesday, P73 9:00 am-4:15 pm; Granular Cell Tumor: A Case of a Rare Tumor with an Unusual Location and C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Presentation Lower Level), Moscone Center P102 9:00 am-4:15 pm; Coexistent Pulmonary Granular Cell Tumor and Adenocarcinoma of the C81: Unusual Presentations Of Lung Cancer: Case Area A, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lung with Pulmonary Tuberculosis Reports Lower Level), Moscone Center Granulomatous-Lymphocytic Interstitial Lung Disease Tuesday, P290 9:00 am-4:15 pm; Granulomatous-Lymphocytic Interstitial Lung Disease as an Early C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Manifestation of Common Variable Immunodeficiency: A Case Report Lung Disease: Case Reports Lower Level), Moscone Center Hereditary Hemorrhagic Telangiectasia (Osler-Weber-Rendu Syndrome) Sunday, A1460 9:00 am-4:15 pm; Two Rare Conditions Linked by an Activin Receptor-Like Kinase 1 (ALK-1) A67: Case Reports In Pulmonary Vascular Disease Area M, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Mutation Lower Level), Moscone Center Monday, P52 9:00 am-4:15 pm; Hereditary Hemorrhagic Telangiectasia (Rendu-Osler-Weber Syndrome): B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Unusual Presentation and Follow Up with CPET Lower Level), Moscone Center 12 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P582 9:00 am-4:15 pm; Worsening Hypoxemia in an 11-Year-Old with Hereditary Hemorrhagic C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Telangiectasia (HHT) Lower Level), Moscone Center Hermansky-Pudlak Syndrome Sunday, P420 9:00 am-4:15 pm; Epithelial Nox4 Contributes to Fibrotic Susceptibility in Hermansky-Pudlak A73: Lung Fibrosis: New Directions To Inform The Future Area D, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Syndrome Mice Lower Level), Moscone Center P423 9:00 am-4:15 pm; Chitinase 3-Like-1 and Its Receptors in Hermansky-Pudlak Syndrome- A73: Lung Fibrosis: New Directions To Inform The Future Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Associated Lung Disease Lower Level), Moscone Center P444 9:00 am-4:15 pm; Limp2 Mediates Prdx6 Delivery to Lamellar Bodies in AP3-Deficient Cell A73: Lung Fibrosis: New Directions To Inform The Future Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm and Mouse Models Lower Level), Moscone Center Tuesday, P316 9:00 am-4:15 pm; Clinical Dilemma in the Lung Transplant Clinic C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P332 9:00 am-4:15 pm; Unusual Usual Interstitial Pneumonia C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center High Grade Sarcoma Tuesday, P61 9:00 am-4:15 pm; Missed Case of Rare High-Grade Lung Sarcoma Presenting as Cavitary C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Pneumonia with Unusual Cutaneous Lesions Lower Level), Moscone Center Horseshoe Lung Wednesday, 507 1:30 pm-3:30 pm; An Unusual Cause of Tachypnea and Hypoxemia in an Infant D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Idiopathic Pleuroparenchymal Fibroelastosis Sunday, 124 9:00 am-11:00 am; Idiopathic Pleuroparenchymal Fibroelastosis and Its Mimickers A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, May 15, 2016 Poster Viewing 9:00-9:45 am; Lower Level), Moscone Center Poster Discussion 9:45-11:00 am IgG4-Related Disease Sunday, P696 9:00 am-4:15 pm; A Case Report of IgG4-Related Disease Masquerading as a 4.1 Centimeter A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Necrotic Pulmonary Mass with Bilateral Pulmonary Nodules Lower Level), Moscone Center P699 9:00 am-4:15 pm; IgG4 Related Disease in the Pleura Manifested as Weight Loss in an A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Immunocompromised Patient Lower Level), Moscone Center

13 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P708 9:00 am-4:15 pm; Do Not IGnore G4 A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1318 9:00 am-4:15 pm; Fatal Hemoptysis Secondary to Fibro-Inflammatory IgG4- Related Lung A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Disease: A Case Report Lower Level), Moscone Center P1323 9:00 am-4:15 pm; Sclerosing Mediastinitis: The Story Within A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Tuesday, P294 9:00 am-4:15 pm; Putting It All Together-A Challenging Diagnosis of Immunoglobulin G4- C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Related Lung Disease (IgG4RLD) Lung Disease: Case Reports Lower Level), Moscone Center 118 2:15 pm-4:15 pm; Respiratory Manifestations of IgG4 Related Disease: A Retrospective C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Analysis of 97 Cases in a Single Chinese Hospital Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm Immune Dysregulation Syndromes Wednesday, 504 1:30 pm-3:30 pm; Subpleural Cysts in a Patient with Immune Dysregulation, D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Polyendrocrinopathy, Enteropathy, X-Linked Syndrome Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Immunodeficiency, Severe Combined Wednesday, 517 1:30 pm-3:30 pm; Prolonged Tachypnea and Hypoxemia as Presentation of Bare Lymphocyte D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Syndrome, Type II Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Inflammatory Bowel Disease Sunday, P1360 9:00 am-4:15 pm; Ulcerative Colitis: Beyond the Bowel A48: Conventional Drug Associated Lung Disease Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Inflammatory Myofibroblastic Tumor of the Lung Tuesday, P51 9:00 am-4:15 pm; Inflammatory Myofibroblastic Tumor of the Lung: A Rare Case Report C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Sunday, 122 9:00 am-11:00 am; Radiographic and Physiologic Abnormalities in Subjects with Myositis- A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, May 15, 2016 Poster Viewing 9:00-9:45 am; Associated Interstitial Lung Disease Lower Level), Moscone Center Poster Discussion 9:45-11:00 am

14 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Interstitial Lung Disease Wednesday, P515 9:00 am-3:30 pm; Bombesein Staining May Be a Useful Marker in Idiopathic Interstitial D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Pneumonias Other Than NEHI Lower Level), Moscone Center Intralobar Bronchopulmonary Sequestration Tuesday, P98 9:00 am-4:15 pm; Synchronous Intralobar Pulmonary Sequestration and Poorly C81: Unusual Presentations Of Lung Cancer: Case Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Differentiated Adenocarcinoma in the Right Lower Lung Lobe Reports Lower Level), Moscone Center Kikuchi-Fujimoto Disease Tuesday, P312 9:00 am-4:15 pm; Kikuchi-Fujimoto Disease: A Refractory Case C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Langerhans Cell Histiocytosis Tuesday, P441 9:00 am-4:15 pm; Diffuse Cystic Lung Disease in A Heavy Smoker: A Rare Case of C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Pulmonary Langerhans Cell Histiocytosis Reports Lower Level), Moscone Center P276 9:00 am-4:15 pm; Atypical Langerhans Cell Histiocytosis Masquerading as Hidradenitis C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Suppurativa Lung Disease: Case Reports Lower Level), Moscone Center 107 2:15 pm-4:15 pm; Lung Ultrasound Has Limited Diagnostic Value in Rare Cystic Lung C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Diseases Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 108 2:15 pm-4:15 pm; HRCT Screening for Diffuse Cystic Lung Diseases in Patients Presenting C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; with Spontaneous Pneumothorax is Cost Effective Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm Wednesday, P544 9:00 am-3:30 pm; Langerhans Cell Histiocytosis and Pulmonary Involvement: Long Term D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Follow Up in 22 Pediatric Patients Having Pulmonary Function Tests Lower Level), Moscone Center P563 9:00 am-3:30 pm; Primary Pulmonary Langerhans Cell Hystiocytosis in a Three-Year-Old D51: Pediatric Cases II Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Patient Lower Level), Moscone Center P564 9:00 am-3:30 pm; Which Is the Better Treatment for Pulmonary Langerhans Cell D51: Pediatric Cases II Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Histiocytosis in Children? Lower Level), Moscone Center Large Cell Neuroendocrine Carcinoma of the Lung Tuesday, P10 9:00 am-4:15 pm; Large Cell Neuroendocrine Carcinoma of the Lung: A Rare Cancer by C79: Multimodality Approaches To Diagnosis And Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm EBUS Guided Core Needle Biopsy Treatment Of Lung Cancer Lower Level), Moscone Center

15 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Leiomyoma, Pulmonary Benign Metastasizing Tuesday, P53 9:00 am-4:15 pm; Benign Metastasizing Leiomyoma C:80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Wednesday, 306 1:30 pm-3:30 pm; Pulmonary Benign Metastasizing Leiomyoma: A Case Report D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center Leiomyosarcoma Arising from the Right Pulmonary Artery Wednesday, 307 1:30 pm-3:30 pm; Leiomyosarcoma Arising from the Right Pulmonary Artery as a Cause for D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Superior Vena Cava Syndrome: A Case of Dyspnea Not Entirely Explained Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm by Pulmonary Embolus Center Light Chain Deposition Disease (LCDD) Tuesday, 106 2:15 pm-4:15 pm; A Rare Cause of Nodular Cystic Disease: Report of Three Cases C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, May 17, 2016 Poster Viewing 2:15-3:00 pm; Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm Lung Neuroendocrine Tumor Wednesday, 303 1:30 pm-3:30 pm; Atypical Large Hydropneumothorax in the Setting of an Uncommon Lung D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Neuroendocrine Tumor Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center Lung Placental Transmogrification Monday, P480 9:00 am-4:15 pm; Lung Placental Transmogrification B45: Obstructive Lung Disease: Interesting Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Lymphatic Anomaly (Lymphangiomatosis), Lymphangiectasia, and Gorham-Stout Disease Tuesday, P309 9:00 am-4:15 pm; Kaposiform Lymphangiomatosis: An Unforeseen Cause of Spontaneous B38: Pleural Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm and Episodic Hemoptysis Lower Level), Moscone Center P683 9:00 am-4:15 pm; Rapamycin Reverses Lymphatic Abnormalities in a Transgenic Mouse B52: Neonatal Lung Disease: From Bench To Babies Area F, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Model of Pulmonary Lymphangiectasia Lower Level), Moscone Center P449 9:00 am-4:15 pm; Imatinib Treatment of Lymphangiomatosis C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Reports Lower Level), Moscone Center P579 9:00 am-4:15 pm; A Unique Case of Pulmonary Lymphangectasia in a Teenager C62: Pediatric Cases I Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center 16 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P598 9:00 am-4:15 pm; Gorham-Stout Disease in a Young Pregnant Female-A Management C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Dilemma Lower Level), Moscone Center P41 9:00 am-4:15 pm; Chyloptysis, Hemoptysis, and Chylothorax in a Fifty-Year-Old Woman C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Lymphangioleiomyomatosis (LAM) Sunday, P1320 9:00 am-4:15 pm; Case Report: Pulmonary Lymphangioleiomyomatosis in a A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Post-Menopausal Female Patient Lower Level), Moscone Center P1497 9:00 am-4:15 pm; High-Intensity Exercise to Treat a Patient with Tuberous Sclerosis A69: Pulmonary Rehabilitation In Pulmonary Area M, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Complex-Lymphangioleiomyomatosis (TSC-LAM) Hypertension, Interstitial Lung Disease, And Other Lower Level), Moscone Center Conditions: What’s New? P1498 9:00 am-4:15 pm; Exercise Training Improves Pulmonary Function and Bone Mineral A69: Pulmonary Rehabilitation In Pulmonary Area M, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Density in Women with Lymphangioleiomyomatosis (LAM) Hypertension, Interstitial Lung Disease, And Other Lower Level), Moscone Center Conditions: What’s New? P481 9:00 am-4:15 pm; Expression and Activity of Cathepsin K in Lymphangioleiomyomatosis A76: LAM: New Biology And New Insights Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm (LAM) Lower Level), Moscone Center P482 9:00 am-4:15 pm; Transcriptomic Differences Associated with TSC2 Gene Expression A76: LAM: New Biology And New Insights Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Loss in Lymphangioleiomyomatosis Lower Level), Moscone Center P483 9:00 am-4:15 pm; Pulmonary Lymphangioleiomyomatosis (LAM): Inflammatory Cell A76: LAM: New Biology And New Insights Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Infiltration in Human LAM Lung Lower Level), Moscone Center P484 9:00 am-4:15 pm; Myeloid Cell Recruitment in a TSC2-Null Mouse Model of A76: LAM: New Biology And New Insights Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lymphangioleiomyomatosis (LAM) Lower Level), Moscone Center P485 9:00 am-4:15 pm; Mesenchymal Tsc2 Deficiency Causes Retarded Lung Alveolarization A76: LAM: New Biology And New Insights Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm and Polycystic Kidney Lesion Lower Level), Moscone Center

P486 9:00 am-4:15 pm; Integrin β5 Implication in the Tumorigenic Potential of TSC-Deficient A76: LAM: New Biology And New Insights Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm LAM Cells Lower Level), Moscone Center Tuesday, P442 9:00 am-4:15 pm; A Case of Sporadic Lymphangioleiomyomatosis with Immune C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Thrombocytopenia Reports Lower Level), Moscone Center P445 9:00 am-4:15 pm; Sporadic Lymphangioleiomyomatosis and Pheochromocytoma: A Case C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm of Neural Crest Cells Gone Awry Reports Lower Level), Moscone Center

17 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P446 9:00 am-4:15 pm; A Case of Sporadic Lymphangioleiomyomatosis Confirmed by C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Thoracentesis Reports Lower Level), Moscone Center P451 9:00 am-4:15 pm; Placental Transmogrification of the Lung Mimicking C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lymphangioleiomyomatosis Reports Lower Level), Moscone Center P453 9:00 am-4:15 pm; Pulmonary Lymphangioleiomyomatosis in a Female with a Large C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Ovarian Cyst Reports Lower Level), Moscone Center 101 2:15 pm-4:15 pm; Early and Late Onset Adverse Events in LAM Patients Treated with C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Sirolimus for Two Years Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 102 2:15 pm-4:15 pm; Early Intervention with Sirolimus Benefits Mild C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Lymphangioleiomyomatosis-Related Lung Disease Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 103 2:15 pm-4:15 pm; Impact of Pleural Disease on Pulmonary Function Test Results in C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Patients with Lymphangioleiomyomatosis Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 104 2:15 pm-4:15 pm; Reproducibility of FEV1 Measurements in Patients with C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Lymphangioleiomyomatosis Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 107 2:15 pm-4:15 pm; Lung Ultrasound Has Limited Diagnostic Value in Rare Cystic Lung C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Diseases Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 108 2:15 pm-4:15 pm; HRCT Screening for Diffuse Cystic Lung Diseases in Patients Presenting C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; with Spontaneous Pneumothorax is Cost Effective Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 123 2:15 pm-4:15 pm; Proapototic Protein Bim Mediates Estrogen-Enhanced Survival in C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Lymphangioleiomyomatosis Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm 124 2:15 pm-4:15 pm; Cell-Cell Communication in Lymphangioleiomyomatosis: Microarray C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; Analysis Shows Induction of Chemokines and Fibroblast Growth Factors Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm in LAM Associated Fibroblasts

18 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, 125 2:15 pm-4:15 pm; CA-125 in Lymphangioleiomyomatosis Correlates with Disease C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, May 17, 2016 Poster Viewing 2:15-3:00 pm; Progression and Sirolimus Therapy Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm Wednesday, 9:00 am-11:00 am; Functional Improvement in Patients with Lymphangioleiomyomatosis D15: New Therapies In ILD Room 306/308 (South Building, May 18, 2016 Oral Presentation 10:15 am (LAM) After Sirolimus Esplanade Level), Moscone Center Lymphocytic Interstitial Pneumonia Monday, P184 9:00 am-4:15 pm; Interstitial Lung Disease Associated with HIV B34: Case Report In Immunodeficiences And Allergy Area B, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Tuesday, P310 9:00 am-4:15 pm; A Novel Use: Aspira Catheter Connected with Heimlich Valve to Manage C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Bronchopleural Fistula in Lymphocytic Interstitial Pneumonia Induced Lower Level), Moscone Center Recurrent Spontaneous Pneumothorax Lymphoma Sunday, P1462 9:00 am-4:15 pm; An Unusual Cause of Pulmonary Hypertension and Cor Pulmonale A67: Case Reports In Pulmonary Vascular Disease Area M, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Monday, P192 9:00 am-4:15 pm; Primary Effusion Lymphoma and Initiation of HAART in a Critically Ill B34: Case Report In Immunodeficiences And Allergy Area B, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Patient with AIDS Lower Level), Moscone Center P281 9:00 am-4:15 pm; An Unfortunate Manifestation of HHV-8 B38: Pleural Disease: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P335 9:00 am-4:15 pm; Rare Case of ANCA Vasculitis with Alveolar Hemorrhage in Non-Hodgkin B40: Dyspnea: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lymphoma Lower Level), Moscone Center P558 9:00 am-4:15 pm; Diffuse Pulmonary Nodules: A Tale of Two Diagnoses B66: Lung Cancer Screening And Nodule Evaluation Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Tuesday, P326 9:00 am-4:15 pm; Lymphoma and the Lung: A Case of Chronic Consolidation and Multiple C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Pneumatoceles in Lymphoplasmacytic Lymphoma Lower Level), Moscone Center P36 9:00 am-4:15 pm; A Case of Primary Pulmonary Extranodal Zone Lymphoma Mimicking C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Pneumonia Lower Level), Moscone Center P44 9:00 am-4:15 pm; Primary Pulmonary Anaplastic Large Cell Lymphoma Masquerading as C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Asthma in a Young Woman Lower Level), Moscone Center

19 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, P46 9:00 am-4:15 pm; An Unusual Way to Diagnose Intravascular Large B-Cell Lymphoma C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Wednesday, P553 9:00 am-3:30 pm; Hodgkin Lymphoma Presenting with Multiple Cavitary Pulmonary Lesions D51: Pediatric Cases II Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center 312 1:30 pm-3:30 pm; Tracheal Mucosa Associated Lymphoid Tissue Lymphoma as a Cause of D110: Unusual Tumors Of The Chest Room 309 (South Building, Poster Viewing 1:30-2:15 pm; Chronic Cough and Prandial Dyspnea Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center 314 1:30 pm-3:30 pm; Extranodal NK/T-Cell Lymphoma Masquerading as Limited Granulomatosis D110: Unusual Tumors Of The Chest Room 309 (South Building, Poster Viewing 1:30-2:15 pm; with Polyangiitis Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center Lymphomatoid Granulomatosis Tuesday, P37 9:00 am-4:15 pm; Lymphomatoid Granulomatosis Presenting as Multiple Lung Masses C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Malignant Peripheral Neural Sheath Tumors to Lungs Wednesday, 321 1:30 pm-3:30 pm; Pulmonary Metastasis from a Neurofibroma D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center Malignant Pleural Mesothelioma Tuesday, 320 2:15 pm-4:15 pm; Targeting EphA2 Using miR-302b Encapsulated-eprhin-A1 Conjugated C110: Mesothelioma And Malignant Pleural Disease: Room 309 (South Building, May 17, 2016 Poster Viewing 2:15-3:00 pm; Liposomal Nanoparticles Inhibits Malignant Pleural Mesothelioma From Bench To Bedside To Community Esplanade Level), Moscone Poster Discussion 3:00-4:15 pm Tumor Growth Center Marfan’s Associated Emphysema Monday, P359 9:00 am-4:15 pm; Making the ‘Connection’: A Case of Abnormal Connective Tissue B40: Dyspnea: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Mercury Inhalation Pneumonitis Sunday, P1300 9:00 am-4:15 pm; All That Glitters Is Not Gold: A Case of Mercury Pneumonitis A46: Lung Disease Due To OTC And Illicits: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center

20 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Microscopic Polyangiitis Sunday, P1325 9:00 am-4:15 pm; Microscopic Polyangiitis with an Unusual Pulmonary Manifestation and A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm No Renal Involvement Lower Level), Moscone Center Monophasic Pulmonary Synovial Sarcoma Tuesday, P22 9:00 am-4:15 pm; Successful Treatment of Early Stage Monophasic Pulmonary Synovial C79: Multimodality Approaches To Diagnosis And Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Sarcoma with Minimally Invasive Robotic Video-Assisted Lobectomy Treatment Of Lung Cancer Lower Level), Moscone Center Mounier-Kuhn Syndrome Monday, P344 9:00 am-4:15 pm; Mounier-Kuhn Syndrome: An Unusual Cause of Dyspnea B40: Dyspnea: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P497 9:00 am-4:15 pm; Mounier-Kuhn Syndrome and Coexist in the Same Patient B45: Obstructive Lung Disease: Interesting Cases Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm with Chronic Respiratory Failure Lower Level), Moscone Center P1237 9:00 am-4:15 pm; Mounier-Kuhn Syndrome Presenting with Dysphagia and Weight Loss B49: Non-Tuberculous Mycobacterial Disease And Case Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Reports Lower Level), Moscone Center Tuesday, P289 9:00 am-4:15 pm; Tracheobronchomegaly in Mounier-Kuhn Syndrome Mimicking the C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Cystic Lung Disease Seen in Lymphangioleiomyomatosis Lung Disease: Case Reports Lower Level), Moscone Center Wednesday, P556 9:00 am-3:30 pm; A Rare Case of Tracheobronchomegaly (Mounier-Kuhn) and Primary D51: Pediatric Cases II Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Ciliary Dyskinesia Lower Level), Moscone Center Mucoepidermoid Carcinoma of the Lung Wednesday, 304 1:30 pm-3:30 pm; A Rare Case of Mucoepidermoid Carcinoma of the Lung D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center Multifocal Micronodular Pneumocyte Hyperplasia Tuesday, P323 9:00 am-4:15 pm; Multifocal Micronodular Pneumocyte Hyperplasia in a Patient with C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Tuberous Sclerosis–Stable Chest CT Findings Over 9 Years of Follow Up Lower Level), Moscone Center Myositis-Associated ILD Sunday, P1327 9:00 am-4:15 pm; PM-DM Associated Interstitial Lung Disease A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center 111 9:00 am-11:00 am; Short-Term Efficacy of Treatment in Myositis-Associated ILD A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, Poster Viewing 9:00-9:45 am; Lower Level), Moscone Center Poster Discussion 9:45-11:00 am 21 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, 122 9:00 am-11:00 am; Radiographic and Physiologic Abnormalities in Subjects with A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, May 15, 2016 Poster Viewing 9:00-9:45 am; Myositis-Associated Interstitial Lung Disease Lower Level), Moscone Center Poster Discussion 9:45-11:00 am 2:15 pm-4:15 pm; Contribution of Mutations in Genes Encoding Proteins of the Surfactant A94: New Insights In IPF Room 306/308 (South Building, Oral Presentation 3:00 pm Metabolism to Idiopathic Interstitial Pneumonia and Idiopathic Pulmonary Esplanade Level), Moscone Fibrosis in a Cohort of 265 Families Center Necrotizing Granulomatous Pulmonary Nodules Sunday, P1317 9:00 am-4:15 pm; Necrobiotic Pulmonary Nodules Secondary to Crohn’s Disease A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Neuroendocrine Cell Hyperplasia of Infancy (NEHI) Monday, 9:00 am-11:00 am; Sleeping chILD: Neuroendocrine Cell Hyperplasia of Infancy and B19: Best Of Pediatrics Room 3006/3008 (West Building, May 16, 2016 Oral Presentation 9:45 am Polysomnography Level 3), Moscone Center Wednesday, 812 9:00 am-11:00 am; Quantitative Measures of Ground Glass Opacities Correlate with Use of D25: Neonatal Lung Diseases: From Bench To Babies Room 3011 (West Building, May 18, 2016 Poster Viewing 9:00-9:45 am; Daytime Oxygen in Neuroendocrine Cell Hyperplasia of Infancy Level 3), Moscone Center Poster Discussion 9:45-11:00 am P514 9:00 am-3:30 pm; Pulmonary Abnormalities in Adults with Familial Neuroendocrine Cell D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Hyperplasia of Infancy (NEHI) Lower Level), Moscone Center Neurofibromatosis Sunday, P1454 9:00 am-4:15 pm; A 45-Year-Old Woman with Neurofibromatosis Type-1-Associated A67: Case Reports In Pulmonary Vascular Disease Area M, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Pulmonary Arterial Hypertension Responsive to Epoprostenol Lower Level), Moscone Center Tuesday, P325 9:00 am-4:15 pm; Neurofibromatosis Related Interstitial Lung Disease: Is There a True C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Relationship? Lower Level), Moscone Center Non-Cystic Fibrosis Bronchiectasis Monday, 201 9:00 am-11:00 am; Healthcare Use and Costs Among Patients with Non-Cystic Fibrosis B22: Burden Of Pulmonary And Critical Care Medicine: Room 304 (South Building, May 16, 2016 Poster Viewing 9:00-9:45 am; Bronchiectasis in the US Cost And Utilization Esplanade Level), Moscone Poster Discussion 9:45-11:00 am Center Ornithine Carbamoyltransferase Deficiency Sunday, P1024 9:00 am-4:15 pm; Refractory Hyperammonemia: A Case Report of a Patient with Adult Onset A57: Critical Care Case Reports: Non-Pulmonary Area H, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Ornithine Carbamoyltransferase Deficiency Critical Care Lower Level), Moscone Center

22 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Pediatric Pulmonary Interstitial Lymphoid Hyperplasia Tuesday, P578 9:00 am-4:15 pm; Pulmonary Interstitial Lymphoid Hyperplasia and Autoimmune Hemolytic C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Anemia Successfully Responding to Steroid Sparing Agents in a 3-Year-Old Lower Level), Moscone Center Boy Peribronchial Sclerosing Hemangioma Tuesday, P77 9:00 am-4:15 pm; Peribronchial Sclerosing Hemangioma with 68Ga Uptakeof DOTATOC C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm PET-CT Lower Level), Moscone Center Placental Transmogrification of the Lung Tuesday, P451 9:00 am-4:15 pm; Placental Transmogrification of the Lung Mimicking C42: LAM, Cystic Lung Disease, And Mimics: Case Area D, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lymphangioleiomyomatosis Reports Lower Level), Moscone Center Plastic Sunday, P1451 9:00 am-4:15 pm; Atypical Plastic Bronchitis Two Decades After Tetralogy of Fallot Repair A67: Case Reports In Pulmonary Vascular Disease Area M, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Pleural Angiosarcoma Monday, P275 9:00 am-4:15 pm; Malignancy Unmasked - A Rare Primary Pleural Angiosarcoma Presenting B38: Pleural Disease: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm as a Complex Empyema Lower Level), Moscone Center Pleuroparenchymal Fibroelastosis (PPFE) Sunday, 113 9:00 am-11:00 am; Pleuroparenchymal Fibroelastosis (PPFE) Predicts Survival in Idiopathic A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, May 15, 2016 Poster Viewing 9:00-9:45 am; Pulmonary Fibrosis (IPF) Lower Level), Moscone Center Poster Discussion 9:45-11:00 am Tuesday, P315 9:00 am-4:15 pm; A Functional Respiratory Imaging View on Idiopathic Pleuroparenchymal C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Fibroelastosis Lower Level), Moscone Center Wednesday, P138 9:00 am-3:30 pm; Pleuroparynchemal Fibroelastosis Due to Long-Term Silica Exposure D46: Case Reports In Environmental And Occupational Area B, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Health Lower Level), Moscone Center Pleuropulmonary Synovial Sarcoma Tuesday, P8 9:00 am-4:15 pm; The Utility of Endobronchial Ultrasound in the Diagnosis of Recurrent C79: Multimodality Approaches To Diagnosis And Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Pleuropulmonary Synovial Sarcoma Treatment Of Lung Cancer Lower Level), Moscone Center

23 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Pompe Disease Tuesday, P463 9:00 am-4:15 pm; Progression from Respiratory Dysfunction to Failure in Late-Onset C45: Dyspnea: Takes Your Breath Away Area D, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Pompe Disease Lower Level), Moscone Center Primary Ciliary Dyskinesia (PCD) Sunday, P612 9:00 am-4:15 pm; The Effect of Inhaled Hypertonic Saline on Quality of Life in Primary A51: Bronchiectasis: Clinical And Epidemiologic Studies Area F, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Ciliary Dyskinesia Patients: A Double-Blind Randomized Controlled Lower Level), Moscone Center Cross-Over Trial P616 9:00 am-4:15 pm; Clinical Features and Associated Likelihood of Primary Ciliary Dyskinesia A51: Bronchiectasis: Clinical And Epidemiologic Studies Area F, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm in Adults Lower Level), Moscone Center P617 9:00 am-4:15 pm; Determinants of Respiratory Function in Adults Patients with Primary A51: Bronchiectasis: Clinical And Epidemiologic Studies Area F, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Ciliary Dyskinesia Lower Level), Moscone Center Monday, 9:00 am-11:00 am; Does Cardiopulmonary Fitness and Pulmonary Function Differ Between B19: Best Of Pediatrics Room 3006/3008 (West Building, May 16, 2016 Oral Presentation 9:00 am Age Matched Groups of Children with Primary Ciliary Dyskinesia (PCD) Level 3), Moscone Center and Cystic Fibrosis (CF) During One Year? P489 9:00 am-4:15 pm; Late Diagnosis of Primary Ciliary Dyskinesia in a Kuwaiti 38-Year-Old B45: Obstructive Lung Disease: Interesting Cases Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Male Lower Level), Moscone Center Tuesday, P581 9:00 am-4:15 pm; Probable Primary Ciliary Dyskinesia in the Presence of Complex C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Congenital Heart Disease and Juvenile Dermatomyositis Lower Level), Moscone Center P593 9:00 am-4:15 pm; Primary Ciliary Dyskinesia, Hypotrichosis and Macular Dystrophy: C62: Pediatric Cases I Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Coincidence or a Novel Syndrome? Lower Level), Moscone Center P966 9:00 am-4:15 pm; Deletion of Rsph1 in a Mouse Model of Primary Ciliary Dyskinesia Results C74: Models And Methods In Lung Biology Area H, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm in a Mild Phenotype Lower Level), Moscone Center Wednesday, 9:00 am-11:00 am; Respiratory Microbiology in Primary Ciliary Dyskinesia: Comparisons to D18: Cystic Fibrosis And Primary Ciliary Dyskinesia: Room 3007/3009 (West Building, May 18, 2016 Oral Presentation 9:00 am a Pediatric Cystic Fibrosis Cohort Two Sides Of The Same Coin? Level 3), Moscone Center 9:00 am-11:00 am; A Comparison of Anaerobic to Aerobic Power Ratio in Children with D18: Cystic Fibrosis And Primary Ciliary Dyskinesia: Room 3007/3009 (West Building, Oral Presentation 9:30 am Primary Ciliary Dyskinesia and Healthy Controls Two Sides Of The Same Coin? Level 3), Moscone Center

24 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Wednesday, P524 9:00 am-3:30 pm; HEATR2 Regulates Ciliogenesis and Distinguishes Subclasses of D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Preassembly Factors Mutated in Primary Ciliary Dyskinesia Lower Level), Moscone Center P525 9:00 am-3:30 pm; Cri-du-Chat Syndrome and Primary Ciliary Dyskinesia: A Genetic and D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Clinical Connection Lower Level), Moscone Center P526 9:00 am-3:30 pm; Toronto Database Registry Pilot Cohort Study: Effect of Proximity to D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm a PCD Center and Drug Insurance Coverage on Health Outcomes Lower Level), Moscone Center P527 9:00 am-3:30 pm; Development and Treatment of Chronic Rhinosinusitis in a Mouse Model D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm of Primary Ciliary Dyskinesia Lower Level), Moscone Center P528 9:00 am-3:30 pm; Nup153 Gene Mutation Leads to Heterotaxy Through Defective SMAD1/ D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm BMP Signaling Lower Level), Moscone Center P539 9:00 am-3:30 pm; Natural Evolution and Impact of Respiratory Tract Infections in Nasal D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Nitric Oxide Level During First 2 Years of Life - A Longitudinal Study Lower Level), Moscone Center P540 9:00 am-3:30 pm; Nasal Nitric Oxide in Primary Immunodeficiency: Helping to Distinguish D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Between Clinically Similar Diseases Lower Level), Moscone Center P542 9:00 am-3:30 pm; Ciliary Functional Biomarker Analysis in Pediatric Patients with Chronic D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Cough Lower Level), Moscone Center P543 9:00 am-3:30 pm; Mannose Binding Lectin and Its Impact on Patients with Primary Ciliary D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Dyskinesia Lower Level), Moscone Center P556 9:00 am-3:30 pm; A Rare Case of Tracheobronchomegaly (Mounier-Kuhn) and Primary D51: Pediatric Cases II Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Ciliary Dyskinesia Lower Level), Moscone Center Primary Pulmonary Amoebiasis Wednesday, P847 9:00 am-3:30 pm; A Case of Primary Pulmonary Amoebiasis D49: Lung Infection Case Reports II: Infections Other Area G, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Than Fungal Infections Lower Level), Moscone Center Primary Pulmonary Artery Sarcoma Wednesday, P1020 9:00 am-3:30 pm; Clinical Characteristics and Treatment Outcomes of Primary Pulmonary D54: Clinical Pulmonary Hypertension Area H, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Artery Sarcoma in Korea Lower Level), Moscone Center

25 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Primary Pulmonary Melanoma Wednesday, 322 1:30 pm-3:30 pm; A Rare Case of Primary Pulmonary Melanoma D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center Primary Pulmonary Synovial Sarcoma Tuesday, P59 9:00 am-4:15 pm; Primary Pulmonary Synovial Sarcoma- A Rare Aggressive Tumor and C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm a Diagnostic Challenge Lower Level), Moscone Center Prune-Belly Syndrome (Eagle-Barrett Syndrome) Tuesday, P571 9:00 am-4:15 pm; Pulmonary Function Tests in a 2-Year-Old Male with Prune-Belly C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Syndrome and Renal Failure Undergoing Peritoneal Dialysis Lower Level), Moscone Center Pulmonary Agenesis Monday, P63 9:00 am-4:15 pm; Pulmonary Hypertension Due to Unilateral Pulmonary Agenesis B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Pulmonary Alveolar Proteinosis (PAP) Sunday, 101 9:00 am-11:00 am; Increased Concentration of BAFF and APRIL in Patients with Autoimmune A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, May 15, 2016 Poster Viewing 9:00-9:45 am; Pulmonary Alveolar Proteinosis Lower Level), Moscone Center Poster Discussion 9:45-11:00 am 110 9:00 am-11:00 am; Clinical Information of Secondary Pulmonary Alveolar Proteinosis in A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, Poster Viewing 9:00-9:45 am; Japan: A Follow-Up Report (KAKEN26305028/AMED:H27-063) Lower Level), Moscone Center Poster Discussion 9:45-11:00 am 116 9:00 am-11:00 am; Whole Lung Lavage Therapy of Pulmonary Alveolar Proteinosis: A Global A24: Autoimmune Interstitial Lung Disease Room 133 (North Building, Poster Viewing 9:00-9:45 am; Survey of Current Practices and Procedures Lower Level), Moscone Center Poster Discussion 9:45-11:00 am P698 9:00 am-4:15 pm; Rare Association of Anti-Threonyl tRNA (PL-7) Antisynthetase Syndrome A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm and Pulmonary Alveolar Proteinosis Lower Level), Moscone Center P704 9:00 am-4:15 pm; Mycobacterium Avium Complex Secondary to Pulmonary Alveolar A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Proteinosis: A Case Report Lower Level), Moscone Center P1238 9:00 am-4:15 pm; Hepatic Steatosis Accompanies Pulmonary Alveolar Proteinosis A42: Autoimmune Myositis, Antisynthetase, Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Scleroderma, And IPAF Lower Level), Moscone Center

26 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Sunday, P1340 9:00 am-4:15 pm; Progressive Dyspnea in a Heart Transplant Recipient: Sirolimus-Induced A48: Conventional Drug Associated Lung Disease Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Pulmonary Alveolar Proteinosis Lower Level), Moscone Center P439 9:00 am-4:15 pm; Estimation of the True GM-CSF Autoantibody Concentration in the Sera A73: Lung Fibrosis: New Directions To Inform The Future Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm of Healthy Subjects Lower Level), Moscone Center Monday, P147 9:00 am-4:15 pm; Autoantibody Against GM-CSF Presented by MHC Class II in Autoimmune B32: Alveolar Macrophage Biology Area B, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Pulmonary Alveolar Proteinosis Lower Level), Moscone Center P371 9:00 am-4:15 pm; Utility of Therapeutic Lobar Lung Lavage in Four Patients of Pulmonary B37: Interventional Pulmonary Medicine: Cool Cases Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Alveolar Proteinosis Lower Level), Moscone Center P684 9:00 am-4:15 pm; Efficacy of Pulmonary Macrophage Transplantation (PMT) Therapy Is B52: Neonatal Lung Disease: From Bench To Babies Area F, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Mediated by Mature Macrophages Without Requirement of Myeloid Lower Level), Moscone Center Progenitor Expansion P1420 9:00 am-4:15 pm; Light Chain Genotype Analysis of GM-CSF Autoantibody in Autoimmune B57: Fibrosis Biology Area M, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Pulmonary Alveolar Proteinosis by Next Generation Sequencing Lower Level), Moscone Center P1503 9:00 am-4:15 pm; Elderly-Onset Hereditary Pulmonary Alveolar Proteinosis and CSF2RA B62: The Biology Of Scarring. Where Are We Now Area M, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Mutation Lower Level), Moscone Center Tuesday, P275 9:00 am-4:15 pm; Pulmonary Alveolar Proteinosis Co-Existing with Underlying Non Specific C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Interstitial Pneumonia Lung Disease: Case Reports Lower Level), Moscone Center P284 9:00 am-4:15 pm; Pathological Findings of Removal Lungs from a Patient with Refractory C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Fibrotic Autoimune Pulmonary Alveolar Proteinosis After Bilateral Lung Lung Disease: Case Reports Lower Level), Moscone Center Transplantation P291 9:00 am-4:15 pm; Autoimmune Pulmonary Alveolar Proteinosis with Progressive Fibrosis C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Refractory to Treatment with Whole Lung Lavage, Inhaled Granulocyte Lung Disease: Case Reports Lower Level), Moscone Center Macrophage Colony-Stimulating Factor and Rituximab P292 9:00 am-4:15 pm; A Case of Acquired Pulmonary Alveolar Proteinosis Successfully Treated C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm with Whole Lung Lavage Lung Disease: Case Reports Lower Level), Moscone Center P296 9:00 am-4:15 pm; Pulmonary Alveolar Proteinosis with Severe Hypoxemia: A Combined C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Therapeutic Strategy Lung Disease: Case Reports Lower Level), Moscone Center P298 9:00 am-4:15 pm; A Case of Autoimmune Pulmonary Alveolar Proteinosis with Fluctuating C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Disease Activity in Parallel with Tobacco Smoke Burden Lung Disease: Case Reports Lower Level), Moscone Center

27 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tuesday, 202 2:15 pm-4:15 pm; Establishment of a National Registry for Pulmonary Alveolar Proteinosis C102: Stategies To Understand ILD: Registries, Room 304 (South Building, May 17, 2016 Poster Viewing 2:15-3:00 pm; in the United States Prognostic Indicators And More Esplanade Level), Moscone Poster Discussion 3:00-4:15 pm Center 112 2:15 pm-4:15 pm; Pulmonary Alveolar Proteinosis: A Case Series from a Reference Center C104: Rare Interstitial Lung Disease: LAM, Cystic Lung Room 133 (North Building, Poster Viewing 2:15-3:00 pm; in Brazil Disease, And More Lower Level), Moscone Center Poster Discussion 3:00-4:15 pm Wednesday, 9:00 am-11:00 am; Whole Lung Lavage Followed by Inhaled Sargramostim as Therapy of D15: New Therapies In ILD Room 306/308 (South Building, May 18, 2016 Oral Presentation 10:30 am Autoimmune Pulmonary Alveolar Proteinosis Esplanade Level), Moscone Center 811 9:00 am-11:00 am; Determining the Dose-Response Curve Needed to Translate Pulmonary D25: Neonatal Lung Diseases: From Bench To Babies Room 3011 (West Building, Poster Viewing 9:00-9:45 am; Macrophage Transplantation (PMT) Therapy to Children with Hereditary Level 3), Moscone Center Poster Discussion 9:45-11:00 am Pulmonary Alveolar Proteinosis 506 9:00 am-11:00 am; Pulmonary Alveolar Proteinosis Is Driven by Reduced GM-CSF-Dependent D27: Macrophages: Resolvers, Responders Or Both? Room 2014 (West Building, Poster Viewing 9:00-9:45 am; Cholesterol Clearance by Alveolar Macrophages, Not an Inability to Level 2), Moscone Center Poster Discussion 9:45-11:00 am Catabolize Surfactant Phospholipids P761 9:00 am-3:30 pm; Invasive Pulmonary Aspergillosis Revealed After Whole Lung Lavage for D48: Lung Infection Case Reports I: Fungal Infections Area G, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Pulmonary Alveolar Proteinosis Lower Level), Moscone Center P513 9:00 am-3:30 pm; A Panel of Novel Blood Tests Based on GM-CSF Signaling Facilitates D50: Pediatric Rare Lung Diseases Area E, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm the Differential Diagnosis of PAP-Causing Diseases Lower Level), Moscone Center 510 1:30 pm-3:30 pm; Pulmonary Alveolar Proteinosis Associated with Secondary D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, Poster Viewing 1:30-2:15 pm; Hemophagocytic Lymphohistiocytosis: A Pediatric Case of Whole Lung Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Lavage Under Veno-Venous Extracorporeal Membrane Oxygenation Pulmonary Arterial Hypertension, Idiopathic Sunday, 907 2:15 pm-4:15 pm; Whole Genome Sequencing in Idiopathic and Heritable Pulmonary A107: Etiology Of PAH: Go Your Own Way Room 3014 (West Building, May 15, 2016 Poster Viewing 2:15-3:00 pm; Arterial Hypertension Level 3), Moscone Center Poster Discussion 3:00-4:15 pm Monday, 9:00 am-11:00 am; Utility of Deep Phenotyping in the Identification and Validation of Novel B20: Hooked On Ph’Omics Room 3003/3005 (West Building, May 16, 2016 Oral Presentation 9:00 am Causal Whole Genome Sequencing Variation in Patients with Pulmonary Level 3), Moscone Center Arterial Hypertension Pulmonary Artery Agenesis Monday, P79 9:00 am-4:15 pm; Pneumonectomy for the Management of Unilateral Pulmonary Artery B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Agenesis Lower Level), Moscone Center

28 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Pulmonary Artery Aneurysm, Idiopathic Monday, P73 9:00 am-4:15 pm; Idiopathic Pulmonary Artery Aneurysm B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Pulmonary Artery Sarcoma Tuesday, P57 9:00 am-4:15 pm; Pulmonary Artery Sarcoma: The Retrospective Study of Clinical C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Presentation and Course Lower Level), Moscone Center Pulmonary Bulla, Idiopathic Monday, P333 9:00 am-4:15 pm; Dangers of Flying High and Diving Low! An Unusual Case of Dyspnea B40: Dyspnea: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Pulmonary Calcification Sunday, P1359 9:00 am-4:15 pm; Metastatic Pulmonary Calcification Following Orthotopic Liver Transplant: A48: Conventional Drug Associated Lung Disease Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm A Bronchoscopic Diagnosis Lower Level), Moscone Center Tuesday, P280 9:00 am-4:15 pm; Calcium: Great for Bones, Not for Lungs C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lung Disease: Case Reports Lower Level), Moscone Center Monday, P288 9:00 am-4:15 pm; Pulmonary Alveolar Microlithiasis: A Case Report C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lung Disease: Case Reports Lower Level), Moscone Center Tuesday, P301 9:00 am-4:15 pm; Rare Case of Dendriform Pulmonary Ossification C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lung Disease: Case Reports Lower Level), Moscone Center P303 9:00 am-4:15 pm; Osteogenesis Imperfecta Associated with Dendriform Pulmonary C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Ossification and Emphysematous Change Lung Disease: Case Reports Lower Level), Moscone Center Monday, P347 9:00 am-4:15 pm; A Sandstorm Lung: A Case of Pulmonary Alveolar Microlithiasis C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P1422 9:00 am-4:15 pm; Revisiting Pulmonary Ossification B57: Fibrosis Biology Area M, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Tuesday, P1517 9:00 am-4:15 pm; Low Phosphate Diet Arrests and Reverses Stone Accumulation and C67: Acute Lung Injury Area M, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Acute Lung Injury in Mice with Pulmonary Alveolar Microlithiasis Lower Level), Moscone Center

29 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Pulmonary Capillaritis Sunday, P700 9:00 am-4:15 pm; A Case of Idiopathic Pauci Immune Pulmonary Capillaritis (IPIPC) A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Wednesday, 503 1:30 pm-3:30 pm; A Case of Concomitant Diffuse Alveor Hemorrhage and Pulmonary D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Embolism in Idiopathic Pulmonary Capillaritis Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Pulmonary Epithelioid Hemangioendothelioma Monday, P563 9:00 am-4:15 pm; Multiple Calcified Pulmonary Nodules: Not Always Granulomatous! B66: Lung Cancer Screening And Nodule Evaluation Area E, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Pulmonary Graft vs Host Disease Tuesday, 611 2:15 pm-4:15 pm; Changes in Peripheral Airway Function with Pulmonary Graft Vs. C108: Advances In Lung Function Assessment Room 2024 (West Building, May 17, 2016 Poster Viewing 2:15-3:00 pm; Host Disease in a Longitudinal Study of Paediatric Bone Marrow Level 2), Moscone Center Poster Discussion 3:00-4:15 pm Transplant Patients Pulmonary Hyalinizing Granuloma Tuesday, P277 9:00 am-4:15 pm; Hyalinizing Granuloma: A Rare Pulmonary Cavitary Pseudotumor, C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm a Case Report Lung Disease: Case Reports Lower Level), Moscone Center P278 9:00 am-4:15 pm; Pulmonary Hyalinising Granuloma with Sweet’s Syndrome C43: Pulmonary Alveolar Proteinosis And Other Rare Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lung Disease: Case Reports Lower Level), Moscone Center Pulmonary Interstitial Glycogenosis Tuesday, P573 9:00 am-4:15 pm; Severe BPD Complicated by PIG C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Pulmonary Leukemic Infiltration Wednesday, 313 1:30 pm-3:30 pm; Leukemic Infiltration in the Setting of Acute Respiratory Failure D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center Pulmonary Sarcoma Monday, P57 9:00 am-4:15 pm; A Rare Case of a Primary Sarcoma of the Pulmonary Artery in a 56 Year B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Old Female: A Case Report Lower Level), Moscone Center

30 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Pulmonary Sequestration Monday, P330 9:00 am-4:15 pm; Intra-Lobar Pulmonary Sequestration: A Unique and Potentially Fatal B40: Dyspnea: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Cause of Hemoptysis Lower Level), Moscone Center P348 9:00 am-4:15 pm; A Rare Case of Pulmonary Sequestration Presenting with Post Prandial B40: Dyspnea: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Epigastric Pain Lower Level), Moscone Center Pulmonary Vein Stenosis Monday, P61 9:00 am-4:15 pm; When Ventilation-Perfusion Scan Falters: A Rare Cause of Chronic B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Pleuritic Chest Pain, , and Pulmonary Hypertension Lower Level), Moscone Center Pulmonary Vein Varix Monday, P60 9:00 am-4:15 pm; Pulmonary Vein Varix: A Rare Incidental Finding B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Pulmonary Veno-Occlusive Disease (PVOD) Monday, P66 9:00 am-4:15 pm; Atypical Hemolytic Uremic Syndrome (HUS) and Pulmonary B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Veno-Occlusive Disease (PVOD) Lower Level), Moscone Center Tuesday, 1017 2:15 pm-4:15 pm; EIF2AK4 Mutation-Carriers with PVOD Present Distinct Features Within C106: Wrecking Ball: New Paradigms In Understanding Room 3024 (West Building, May 17, 2016 Poster Viewing 2:15-3:00 pm; the Remodeled Lung Vasculature And Treatment Of PH Level 3), Moscone Center Poster Discussion 3:00-4:15 pm Pulmonary Venous Thrombosis Monday, P76 9:00 am-4:15 pm; An Incidental Pulmonary Vein Thrombosis - Resolution with Watchful B54: Case Reports In The Pulmonary Circulation Area A, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Waiting Lower Level), Moscone Center Recurrent Respiratory Papillomatosis Monday, P464 9:00 am-4:15 pm; Recurrent Respiratory Papillomatosis Involving the Lower Airways Treated B39: Interventional Pulmonary Medicine: Recent Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm with Argon Plasma Coagulation and Cidofovir Intralesional Injection Advances Lower Level), Moscone Center Relapsing Polychondritis Sunday, P1602 9:00 am-4:15 pm; Reassess the Value of 18F-FDG PET/CT for Relapsing Polychondritis A79: Lung Imaging: CT And Beyond Area N, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Diagnose and Therapeutic Response Monitoring Lower Level), Moscone Center Monday, P450 9:00 am-4:15 pm; Quantitative CT Measurement of Tracheal Cross-Sectional Areas in B39: Interventional Pulmonary Medicine: Recent Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Relapsing Polychondritis: Correlations with Spirometric Values Advances Lower Level), Moscone Center

31 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Monday, P470 9:00 am-4:15 pm; A Rheumatologic Disorder Mimicking Asthma B45: Obstructive Lung Disease: Interesting Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Wednesday, 524 1:30 pm-3:30 pm; Presentation of Relapsing Polychondritis in an Adolescent D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Right Pulmonary Artery Atresia Wednesday, 505 1:30 pm-3:30 pm; Congenital Pulmonary Artery Atresia Masquerading as a Left Sided D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Anomaly Level 2), Moscone Center Poster Discussion 2:15-3:30 pm ROHHAD Syndrome Monday, P1577 9:00 am-4:15 pm; Successful Management of Breathing-Related Sleep Disorder Associated B65: Things That Go Bump In The Night: Sleep Case Area N, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm with an Orphan Syndrome, Rapid-Onset Obesity with Hypothalamic Studies And Non-OSA Sleep Lower Level), Moscone Center Dysfunction, Hypoventilation, and Autonomic Dysregulation (ROHHAD) Rosai Dorfman Disease Sunday, P692 9:00 am-4:15 pm; 37 Year Old Female with 7 Year History of Intermittent Dyspnea of Few A35: Case Reports In Autoimmune Lung Disease Area G, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Minutes Duration Lower Level), Moscone Center Sarcoidosis Monday, P140 9:00 am-4:15 pm; Overview of Multicenter Genomic Research in Alpha-1 Antitrypsin B31: Alpha-1 Antitrypsin Deficiency Area B, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Deficiency and Sarcoidosis (GRADS) and Biorepository Lower Level), Moscone Center Tuesday, P240 9:00 am-4:15 pm; Resolution of Cardiac Magnetic Resonance T2 Signal Following Immune C40: Sarcoidosis: Understanding This Multi-System Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Suppression for Cardiac Sarcoidosis: A Case Series Disorder Lower Level), Moscone Center P319 9:00 am-4:15 pm; A Case of Sarcoidosis and Sjogren’s Syndrome: Clues Suggesting C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Overlap Rather than Mimicry Lower Level), Moscone Center Sarcomatoid Carcinoma Tuesday, P116 9:00 am-4:15 pm; A Pathologic Rarity C81: Unusual Presentations Of Lung Cancer: Case Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Reports Lower Level), Moscone Center P129 9:00 am-4:15 pm; A Case of Sarcomatoid Carcinoma of the Lung in a Young Female C81: Unusual Presentations Of Lung Cancer: Case Area A, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Reports Lower Level), Moscone Center

32 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Scimitar Syndrome Sunday, P1463 9:00 am-4:15 pm; Scimitar Syndrome Presenting with Pulmonary Emboli and Right Heart A67: Case Reports In Pulmonary Vascular Disease Area M, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Failure Requiring ECMO Lower Level), Moscone Center Sclerosing Thymoma Monday, P362 9:00 am-4:15 pm; An “Ancient” Cause of an Anterior Mediastinal Mass B40: Dyspnea: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Short Telomere Syndrome and Idiopathic Pulmonary Fibrosis Tuesday, P311 9:00 am-4:15 pm; Short Telomere Syndrome a Rare Cause of Familial Idiopathic C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Pulmonary Fibrosis Lower Level), Moscone Center Shrinking Lung Syndrome Sunday, P1333 9:00 am-4:15 pm; Shrinking Lung Syndrome - An Unusual Cause of Dyspnea in Patients A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm with Systemic Lupus Erythematosus Lower Level), Moscone Center P1334 9:00 am-4:15 pm; Dyspnea in Systemic Lupus Erythematosus: A Case of Shrinking Lung A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Syndrome Lower Level), Moscone Center Shwachman-Diamond Syndrome Wednesday, 521 1:30 pm-3:30 pm; An Infant with Tachypnea and Progressive Respiratory Failure D108: Pediatric Cases: A Room Full Of Zebras Room 2014 (West Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Level 2), Moscone Center Poster Discussion 2:15-3:30 pm Sjogren’s Overlap Syndrome Tuesday, P319 9:00 am-4:15 pm; A Case of Sarcoidosis and Sjogren’s Syndrome: Clues Suggesting C44: Diffuse Parenchymal Lung Disease: Case Reports Area C, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Overlap Rather than Mimicry Lower Level), Moscone Center Solitary Fibrous Tumor Monday, P377 9:00 am-4:15 pm; Endobronchial Ultrasound Bronchoscopy in the Diagnosis of Mediastinal B37: Interventional Pulmonary Medicine: Cool Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Solitary Fibrous Tumor Lower Level), Moscone Center SP-C Related Interstitial Lung Disease Tuesday, 9:00 am-11:00 am; Expression of the Surfactant Protein C Mutant SP-CI73T in Mice Results C17: Fascinating Mechanisms In Lung Fibrosis Room 2020/2022 (West Building, May 17, 2016 Oral Presentation 9:15 am in Dose Dependent Disruption of Lung Development and Age Related Level 2), Moscone Center Diffuse Parenchymal Lung Remodeling In Adults

33 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Spindle Cell Carcinoma Tuesday, P84 9:00 am-4:15 pm; Appearances Are Deceptive: An Unusual Presentation of a Rare Primary C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lung Tumor!! Lower Level), Moscone Center Surfactant Protein-Associated Lung Disease Monday, P1538 9:00 am-4:15 pm; SFTPA1 Mutation in Familial Idiopathic Interstitial Pneumonia and Lung B62: The Biology Of Scarring. Where Are We Now Area M, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Cancer Lower Level), Moscone Center Tuesday, P596 9:00 am-4:15 pm; Successful Outcome of a Genetic Lethal Condition in a Term Newborn C62: Pediatric Cases I Area E, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Wednesday, 815 9:00 am-11:00 am; Multiplexed Direct Genomic Selection Identifies Exonic, Intronic, and D25: Neonatal Lung Diseases: From Bench To Babies Room 3011 (West Building, May 18, 2016 Poster Viewing 9:00-9:45 am; Copy Number Variation in Surfactant-Associated Genes Among Infants Level 3), Moscone Center Poster Discussion 9:45-11:00 am with Respiratory Distress Syndrome (RDS) and Children with Interstitial Lung Disease (chILD) Sweet’s Syndrome Tuesday, P856 9:00 am-4:15 pm; An Atypical Presentation of Acute Febrile Neutrophilic Dermatosis as C53: Critical Care Case Reports: Multisystem Organ Area G, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Drug-Induced Bullous Variant Sweet’s Syndrome Failure Lower Level), Moscone Center

Swyer-James Syndrome Sunday, P1446 9:00 am-4:15 pm; Unusual Clinical Presentation for Swyer-James-Macleod Syndrome A67: Case Reports In Pulmonary Vascular Disease Area M, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Monday, P487 9:00 am-4:15 pm; Swyer-James-MacLeod Syndrome Misdiagnosed as COPD B45: Obstructive Lung Disease: Interesting Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center P491 9:00 am-4:15 pm; New Diagnosis of Swyer-James-Macleod Syndrome in An Adult: B45: Obstructive Lung Disease: Interesting Cases Area D, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm A Case Report Lower Level), Moscone Center Wednesday, P578 9:00 am-3:30 pm; Unilateral Hyperlucent Lung in an Infant D51: Pediatric Cases II Area E, Hall D (North Building, May 18, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Thoracic Splenosis Monday, P293 9:00 am-4:15 pm; Malignancy Mimic: An Unexpected Consequence of an Abdominal Gun B38: Pleural Disease: Case Reports Area C, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Shot Wound Lower Level), Moscone Center P294 9:00 am-4:15 pm; Pleural Noduarity in a Vietnam Veteran B38: Pleural Disease: Case Reports Area C, Hall D (North Building, Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center

34 Rare Disease Term Date/Day Board Number/Time Abstract Title Session ID and Title Location Tracheal Fistula Sunday, P1322 9:00 am-4:15 pm; Flash Blood - An Unusual Case of Intermittent Massive Hemoptysis A47: Rare Interstitial Lung Disease: Case Reports Area L, Hall D (North Building, May 15, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Monday, P475 9:00 am-4:15 pm; Tracheobronchial-Esophageal Fistula in a 23 Year Old with “Asthma” B45: Obstructive Lung Disease: Interesting Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Tracheal Hamartoma Tuesday, P76 9:00 am-4:15 pm; A Rare Case of Tracheal Hamartoma C80: Thoracic Oncology: Case Reports Area A, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center Wednesday, 323 1:30 pm-3:30 pm; An Asymptomatic Case of Tracheal Hamartoma D110: Unusual Tumors Of The Chest Room 309 (South Building, May 18, 2016 Poster Viewing 1:30-2:15 pm; Esplanade Level), Moscone Poster Discussion 2:15-3:30 pm Center Very Long-Chain Acyl-CoA Dehydrogenase Deficiency Tuesday, P983 9:00 am-4:15 pm; Exercise Induced Respiratory Insufficiency in a Murine Model of Very C75: Improving And Assessing Respiratory Function Area H, Hall D (North Building, May 17, 2016 Poster Viewing 11:00 am-12:45 pm Long-Chain Acyl-CoA Dehydrogenase Deficiency Lower Level), Moscone Center Yellow Nail Syndrome Monday, P488 9:00 am-4:15 pm; Yellow Nail Syndrome B45: Obstructive Lung Disease: Interesting Cases Area D, Hall D (North Building, May 16, 2016 Poster Viewing 11:00 am-12:45 pm Lower Level), Moscone Center

35 B:11.25" T:11" S:10.5" B:6.25"

OFEV MEETS S:5.25" SAN FRANCISCO T:6" VISIT BOOTH #1003

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JOIN US FOR A NON-CME/CNE INFORMATIONAL PROGRAM Sponsored by Boehringer Ingelheim Pharmaceuticals, Inc.

Sunday, May 15, 2016 6:30 pm - 9:30 pm AND VISIT BOOTH #1003 Marriott Marquis, San Francisco

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An Industry-Organized Symposium at the ATS 2016 International Conference. All ATS 2016 International Conference attendees are invited to this non-CME/CNE educational program sponsored by Boehringer Ingelheim Pharmaceuticals, Inc.

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Copyright ©2016, Boehringer Ingelheim Pharmaceuticals, Inc. All rights reserved. (03/16) PC-OF-0361-PROF